Curr Opin Pulm Med 2021 Jul 6. Epub 2021 Jul 6.
Interstitial Lung Disease Unit, Royal Brompton Hospital National Heart and Lung Institute, Imperial College, London, United Kingdom Department of Medicine, National Jewish Health, Denver, CO, USA National Reference Center for Rare Pulmonary Diseases, Louis Pradel Hospital, Hospices Civils de Lyon, Claude Bernard University Lyon 1, University of Lyon, INRAE, IVPC, UMR754, member of ERN-LUNG, Lyon, France.
Purpose Of Review: The progressive fibrotic phenotype (PFP), a term that covers large sub-groups of patients with fibrotic lung diseases that clinically progress despite appropriate usual management, is now an everyday problem for patients and clinicians alike. This review covers recent data that are relevant to major clinical uncertainties.
Recent Findings: The clinical relevance of the PFP is covered by a brief review of data from which this entity was constructed. Read More