429 results match your criteria Truncus Arteriosus Imaging


Congenital hypothyroidism, cardiac defects, and pancreatic agenesis in an infant with GATA6 mutation.

Am J Med Genet A 2020 Mar 24. Epub 2020 Mar 24.

Division of Clinical and Metabolic Genetics, The Hospital for Sickkids, University of Toronto, Toronto, Ontario, Canada.

GATA6 pathogenic variants primarily manifest a phenotype with pancreatic agenesis and cardiac malformations. However, additional congenital malformations affecting the biliary system, congenital diaphragmatic hernia and developmental delay have been reported. We report a newborn, prenatally diagnosed with truncus arteriosus and intrauterine growth restriction, who was postnatally found to have pancreatic agenesis associated with neonatal diabetes and hepatobiliary abnormalities. Read More

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http://dx.doi.org/10.1002/ajmg.a.61569DOI Listing

Characterization of size, shape and pattern of flow in the neo-aorta and pulmonary artery in a patient following an innovative technique of repair for truncus arteriosus.

Glob Cardiol Sci Pract 2019 Sep 20;2019(2):e201918. Epub 2019 Sep 20.

Department of Surgery, Aswan Heart Centre, Magdi Yacoub Heart Foundation, Egypt.

Truncus arteriosus (TA) caries a very poor prognosis. In the absence of early correction, only 12 percent of patients born with this anomaly survive beyond one year. There is no agreement about the best method of surgical correction of this anomaly. Read More

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http://dx.doi.org/10.21542/gcsp.2019.18DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6865202PMC
September 2019

Characteristics of Cardiovascular Magnetic Resonance Imaging and Outcomes in Adults With Repaired Truncus Arteriosus.

Am J Cardiol 2019 11 22;124(10):1636-1642. Epub 2019 Aug 22.

Joint Department of Medical Imaging, University Health Network, Toronto General Hospital, Toronto, Ontario, Canada; Peter Munk Cardiac Centre, University Health Network, Toronto General Hospital, Toronto, Ontario, Canada. Electronic address:

The cardiovascular magnetic resonance imaging (CMR) features of adults with repaired truncus arteriosus (rTA) are largely undefined. We sought to explore CMR characteristics in rTA and to identify associations between imaging findings and cardiovascular outcomes. Adults with rTA and CMR were identified and anatomic subtypes (1-4) were assigned (Collett and Edwards classification). Read More

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http://dx.doi.org/10.1016/j.amjcard.2019.08.007DOI Listing
November 2019
2 Reads

Tricuspid Atresia With Truncus Arteriosus: Off-Pump Stage I Palliation.

World J Pediatr Congenit Heart Surg 2019 09;10(5):635-637

Department of Pediatric Cardiac Sciences, Sir Ganga Ram Hospital, New Delhi, Delhi, India.

Coexistence of tricuspid atresia and truncus arteriosus (common arterial trunk) is an extremely rare combination of anomalies and requires staged palliation. Initial palliation involves disconnection of the pulmonary arteries from the common trunk and creation of a systemic-to-pulmonary artery shunt. This has generally been accomplished with the use of cardiopulmonary bypass. Read More

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http://dx.doi.org/10.1177/2150135119847607DOI Listing
September 2019
2 Reads

Atypical variant of truncus arteriosus: sinusal origin of pulmonary artery segment with non-confluent branch pulmonary arteries.

BMJ Case Rep 2019 Apr 24;12(4). Epub 2019 Apr 24.

Cardiovascular Radiology and Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India.

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http://dx.doi.org/10.1136/bcr-2019-229547DOI Listing

Anomalous origin of left vertebral artery from ascending aorta associated with interrupted aortic arch and persistent truncus arteriosus.

Cardiol Young 2019 Mar 4;29(3):414-415. Epub 2019 Feb 4.

Department of Cardiovascular Radiology and Endovascular Interventions,All India Institute of Medical Sciences,New Delhi-110029,India.

We present a case of a 3-week-old boy with persistent truncus arteriosus associated with interrupted right aortic arch having an anomalous origin of the left vertebral artery from the ascending aorta. Read More

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http://dx.doi.org/10.1017/S1047951118002494DOI Listing
March 2019
5 Reads

Truncus Arteriosus With Major Aortopulmonary Collateral Arteries.

Ann Thorac Surg 2019 08 30;108(2):e105-e106. Epub 2019 Jan 30.

Department of Pediatric Cardiology, Hyogo Prefectural Amagasaki General Medical Center, Hyogo, Japan.

Truncus arteriosus with the absence of one branching pulmonary artery and presence of major aortopulmonary collateral arteries is rare. A small patient, with a birth weight of 2,219 g, was successfully repaired by a staged approach, after banding of the left pulmonary artery and unifocalization of major aortopulmonary collateral arteries. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2018.12.051DOI Listing
August 2019
2 Reads

Persistent truncus arteriosus with absent semilunar valve in first trimester.

J Med Ultrason (2001) 2019 Apr 14;46(2):273-275. Epub 2019 Jan 14.

Department of Obstetrics, The Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China.

Persistent truncus arteriosus (PTA) is a relatively uncommon congenital heart disease, accounting for approximately 0.7-1.4% of all congenital cardiac abnormalities worldwide. Read More

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http://dx.doi.org/10.1007/s10396-018-00926-yDOI Listing
April 2019
7 Reads

Common Arterial Trunk: Physiology, Imaging, and Management.

Semin Cardiothorac Vasc Anesth 2019 Jun 29;23(2):225-236. Epub 2018 Dec 29.

3 Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Common arterial trunk (CAT), or truncus arteriosus, is a rare form of cyanotic congenital heart disease and is highly associated with DiGeorge syndrome (microdeletion 22q11.2). Prenatal diagnosis is highly feasible, allowing proper delivery planning and postnatal management. Read More

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http://journals.sagepub.com/doi/10.1177/1089253218821382
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http://dx.doi.org/10.1177/1089253218821382DOI Listing
June 2019
51 Reads

Neonatal quadricuspid truncal valve repair with left coronary artery unroofing.

J Thorac Cardiovasc Surg 2019 02 5;157(2):710-711. Epub 2018 Oct 5.

Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Victoria, Australia; Heart Research Group, Murdoch Children's Research Institute, Melbourne, Victoria, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Victoria, Australia; Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine, Melbourne, Victoria, Australia.

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https://linkinghub.elsevier.com/retrieve/pii/S00225223183255
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http://dx.doi.org/10.1016/j.jtcvs.2018.09.046DOI Listing
February 2019
34 Reads

Prenatal detection of critical cardiac outflow tract anomalies remains suboptimal despite revised obstetrical imaging guidelines.

Congenit Heart Dis 2018 Sep 18;13(5):748-756. Epub 2018 Jul 18.

Division of Pediatric Cardiology, Department of Pediatrics, Rady Children's Hospital, University of California, San Diego, California.

Background: Fetal echocardiography can accurately diagnose critical congenital heart disease prenatally, but relies on referrals from abnormalities identified on routine obstetrical ultrasounds. Critical congenital heart disease that is frequently missed due to inadequate outflow tract imaging includes anomalies such as truncus arteriosus, double outlet right ventricle, transposition of the great arteries, tetralogy of Fallot, pulmonary stenosis, and aortic stenosis.

Objective: This study evaluated the prenatal detection rate of critical outflow tract anomalies in a single urban pediatric hospital before and after "AIUM Practice Guideline for the Performance of Obstetric Ultrasound Examinations," which incorporated outflow tract imaging. Read More

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http://dx.doi.org/10.1111/chd.12648DOI Listing
September 2018
10 Reads

Double semilunar valve replacement in complex congenital heart disease using decellularized homografts.

Interact Cardiovasc Thorac Surg 2019 01;28(1):151-157

Department of Cardiothoracic, Transplantation and Vascular Surgery, Hannover Medical School, Hannover, Germany.

Objectives: Patients with complex congenital heart disease often require multiple reoperations, resulting in increased rates of operative morbidity and mortality. Decellularized heart valves (DHVs) have led to reduced reoperation rates compared with current other valve substitutes when used for pulmonary valve replacement and have also shown very auspicious early results in aortic valve replacement. The aim of the work was to analyse the outcome of a single-stage decellularized valve implantation in the aortic and pulmonary position. Read More

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http://dx.doi.org/10.1093/icvts/ivy212DOI Listing
January 2019
11 Reads

Type B Interrupted Right Aortic Arch: Diagnostic and Surgical Approaches.

Ann Thorac Surg 2019 01;107(1):e41-e43

Department of Cardiology and Pediatrics, Boston Children's Hospital, Boston, Massachusetts. Electronic address:

Interrupted right aortic arch is a rare congenital cardiovascular anomaly typically associated with other forms of congenital heart disease. We report two cases of interrupted right aortic arch associated with isolated left pulmonary artery and bilateral ductus arteriosus in the first case and with truncus arteriosus in the second case. Computed tomography was complementary to echocardiography in delineating the anatomic details in both cases, informing surgical repair with reconstruction of a left aortic arch in the first case and right arch in the second case. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2018.05.098DOI Listing
January 2019
33 Reads

: report of three cases and review of literature.

Afr Health Sci 2018 Mar;18(1):147-156

Department of Fetopathology, CHU Pellegrin, place Amélie Raba, 33076 Bordeaux cedex France.

Background: (TAC) is a congenital heart defect in which the physiologic arterial common trunk was not divided into aorta and pulmonary artery trunk.

Objectives: In this paper, we report on three observed cases from which we looked for (in conjunction with literature review) the different causes of TAC many of which have genetic origins.

Methods: We collected three clinical files of fetuses having a TAC. Read More

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http://dx.doi.org/10.4314/ahs.v18i1.19DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6016971PMC
March 2018
39 Reads

Aortopulmonary window with pumonary atresia with ventricular septal defect with D-transposition of great arteries: extremely rare anomaly.

BMJ Case Rep 2018 Jun 13;2018. Epub 2018 Jun 13.

Department of Anaesthesia, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India.

Aortopulmonary window (APW) is rare a congenital heart disease accounting for 0.1%-0.2% of all congenital heart defects. Read More

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http://dx.doi.org/10.1136/bcr-2018-224401DOI Listing
June 2018
6 Reads

Antenatal Diagnosis of Fetal Retinoid Syndrome at 20 Weeks of Gestation: A Case Report.

Fetal Pediatr Pathol 2018 Aug 29;37(4):282-286. Epub 2018 May 29.

a Istanbul University Cerrahpasa Medical Faculty , Obstetrics and Gynecology Division of Perinatology , Istanbul , Turkey.

Introduction: Isotretinoin, a synthetic derivative of vitamin A, is one of the most potent human teratogens, and is mainly utilized for the treatment of severe recalcitrant nodular acne. Retinoic acid embryopathy is well defined in the literature.

Case Report: The mother was referred for a fetal posterior fossa abnormality, first detected at 20 weeks of gestation. Read More

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http://dx.doi.org/10.1080/15513815.2018.1472354DOI Listing
August 2018
13 Reads

Repair of Ductus or Hemi-Truncus to One Lung and Major Aortopulmonary Collaterals to the Other Lung.

Ann Thorac Surg 2018 08 21;106(2):568-574. Epub 2018 Apr 21.

Division of Pediatric Cardiac Surgery, Stanford University School of Medicine, Lucile Packard Children's Hospital, Stanford, Stanford, California.

Background: There are patients born with pulmonary atresia and a ductus arteriosus or hemi-truncus to one lung and major aortopulmonary collateral arteries (MAPCAs) to the contralateral lung. The purpose of this study was to review our surgical results for this relatively rare subset of patients.

Methods: This was a retrospective review of 35 patients with ductus/hemi-truncus in association with pulmonary atresia with ventricular septal defect and MAPCAs. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2018.03.041DOI Listing
August 2018
18 Reads

Impact of truncal valve surgery on the outcomes of the truncus arteriosus repair.

Eur J Cardiothorac Surg 2018 09;54(3):524-531

Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, VIC, Australia.

Objectives: Preoperative moderate or greater truncal valve (TV) insufficiency is one of the most important factors influencing mortality in children with truncus arteriosus. We therefore sought to determine the impact of TV insufficiency and concomitant TV surgery on children who underwent truncus arteriosus repair at a single institution.

Methods: We reviewed 180 patients who underwent truncus arteriosus repair between 1979 and 2016. Read More

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http://dx.doi.org/10.1093/ejcts/ezy080DOI Listing
September 2018
12 Reads

Polytetrafluoroethylene conduits versus homografts for right ventricular outflow tract reconstruction in infants and young children: An institutional experience.

J Thorac Cardiovasc Surg 2018 05 31;155(5):2082-2091.e1. Epub 2018 Jan 31.

Cardiothoracic Surgery, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pa.

Objective: Our institution uses a valved polytetrafluoroethylene conduit as an alternative to homografts. The objective of this study was to investigate the performance of bicuspid valved polytetrafluoroethylene conduits used for right ventricular outflow tract reconstruction in children aged less than 2 years and to evaluate risk factors for earlier conduit explant.

Methods: We performed an Institutional Review Board-approved retrospective chart review of all patients aged less than 2 years who underwent surgical right ventricular outflow tract reconstruction with a bicuspid valved polytetrafluoroethylene conduit or homograft conduit from July 2004 to December 2014. Read More

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http://dx.doi.org/10.1016/j.jtcvs.2017.11.107DOI Listing
May 2018
20 Reads

Long-Term Outcome of Interrupted Arch Repair With Direct Anastomosis and Homograft Augmentation Patch.

Ann Thorac Surg 2018 06 13;105(6):1819-1826. Epub 2018 Feb 13.

Department of Cardiac Surgery, Birmingham Children's Hospital, Birmingham, United Kingdom. Electronic address:

Background: This study analyzed outcomes of interrupted aortic arch (IAA) repair using a standardized technique to interpret the role of the arch repair on late outcomes in a complex and heterogeneous group of patients.

Methods: This single institution study covered the period from 1988 to 2015. A total of 120 cases of IAA were divided into four groups: IAA with ventricular septal defect (VSD) (n = 38), IAA with a Norwood or Damus-Kaye-Stansel procedure (n = 41), IAA with truncus arteriosus (n = 24), and a miscellaneous group (n = 17). Read More

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http://dx.doi.org/10.1016/j.athoracsur.2018.01.035DOI Listing
June 2018
8 Reads

Modified Repair of Type I and II Truncus Arteriosus Limits Early Right Ventricular Outflow Tract Reoperation.

Semin Thorac Cardiovasc Surg 2018 8;30(2):199-204. Epub 2018 Feb 8.

Department of Surgery, University of Rochester Medical Center, Rochester, New York; Department of Pediatrics, University of Rochester Medical Center, Rochester, New York; Pediatric Cardiac Consortium of Upstate New York. Electronic address:

Repair of truncus arteriosus often requires early right ventricular outflow tract (RVOT) reoperation. Using a modified repair, the branch pulmonary arteries are left in situ, which may avoid earlier RVOT reoperation. We hypothesized that our modified repair for type I and II truncus arteriosus would extend the time to RVOT reoperation. Read More

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http://dx.doi.org/10.1053/j.semtcvs.2018.02.003DOI Listing
November 2018
11 Reads

Prenatal diagnosis of the fetal common arterial trunk. A case series.

Med Ultrason 2018 Feb;1(1):100-104

Gynecology Department, University of Medicine and Pharmacy Victor Babeș Timișoara, Romania.

Fetal common arterial trunk is an anomaly represented by a unique arterial trunk that arouses from the base of the heart, and gives birth to systemic branches, both pulmonary and coronary, frequently associated with a ventricular septal defect (VSD) and has a poor prognosis. We present a series of 17 cases diagnosed in our tertiary center with different types of fetal common arterial trunk, its associated disorders, the evolution of the pregnancies, and of the neonates. We concluded that our cases support the fact that a complete intrauterine evaluation of each case of the common arterial trunk is impossible. Read More

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http://dx.doi.org/10.11152/mu-1084DOI Listing
February 2018
9 Reads

Role of virtual reality in congenital heart disease.

Congenit Heart Dis 2018 May 5;13(3):357-361. Epub 2018 Feb 5.

Division of Pediatric Cardiology, Johns Hopkins Hospital, Baltimore, MD, USA.

Objective: New platforms for patient imaging present opportunities for improved surgical planning in complex congenital heart disease (CHD). Virtual reality (VR) allows for interactive manipulation of high-resolution representations of patient-specific imaging data, as a supplement to traditional 2D visualizations and 3D printed heart models.

Design: We present the novel use of VR for the presurgical planning of cardiac surgery in two infants with complex CHD to demonstrate interactive real-time views of complex intra and extracardiac anatomy. Read More

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http://dx.doi.org/10.1111/chd.12587DOI Listing
May 2018
16 Reads
1.202 Impact Factor

Truncus arteriosus with double aortic arch: A rare association.

Turk J Pediatr 2017 ;59(2):221-223

Department of Pediatric, Cardiology, Eskisehir Osmangazi University Medical Faculty, Eskisehir, Turkey.

Yıldırım SV, Yıldırım A. Truncus arteriosus with double aortic arch: A rare association. Turk J Pediatr 2017; 59: 221-223. Read More

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http://dx.doi.org/10.24953/turkjped.2017.02.020DOI Listing
November 2018
18 Reads

Outcomes of Right Ventricular Outflow Tract Reconstruction for Children with Persistent Truncus Arteriosus: A 10-Year Single-Center Experience.

Pediatr Cardiol 2018 Mar 19;39(3):565-574. Epub 2017 Dec 19.

Department of Cardiothoracic Surgery, Shanghai Children's Medical Center, Heart Center, School of Medicine, Shanghai Jiaotong University, Dongfang Road 1678, Shanghai, China.

The purpose of this report is to assess the mid- and long-term outcomes of right ventricular outflow tract (RVOT) reconstruction for children with persistent truncus arteriosus. Between September 2006 and 2016, 105 patients with persistent truncus arteriosus (PTA) received surgical treatment at Shanghai Children's Medical Center. Direct right ventricle-pulmonary artery anastomosis (pulmonary artery pull-down) was performed in 51 patients; a left auricle or pericardial conduit was inserted between the RVOT and pulmonary artery as a connection in 17 patients; heterograft (bovine jugular vein or Gore-tex) conduits and homograft conduits were used in 30 and 7 cases, respectively, to connect the distal pulmonary and right ventricle outflow tract; and pulmonary valve reconstruction was performed in 38 patients using a Gore-tex monocusp. Read More

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http://dx.doi.org/10.1007/s00246-017-1789-0DOI Listing
March 2018
15 Reads

Repair of a quadricuspid truncal valve by tricuspidization and reconstruction of right ventricular outflow tract with the excised truncal cusp.

J Thorac Cardiovasc Surg 2018 03 16;155(3):1186-1189. Epub 2017 Nov 16.

Department of Surgery, National Taiwan University Hospital, National Taiwan University College of Medicine, Taipei, Taiwan. Electronic address:

Objective: Quadricuspid truncal valves are susceptible to regurgitation, and tricuspid configuration is considered more durable after repairing the truncal valve. We report a new method by excising the excessive truncal cuspid to reconstruct a new competent aortic valve.

Methods: Bilateral pulmonary banding failed to stabilize a 4-month-old baby with type I truncus arteriosus and quadricuspid truncal valve with severe regurgitation, so surgery was performed. Read More

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http://dx.doi.org/10.1016/j.jtcvs.2017.09.148DOI Listing
March 2018
11 Reads

Pregnancy in Women With Repaired Truncus Arteriosus: A Case Series.

Can J Cardiol 2017 12 6;33(12):1737.e1-1737.e3. Epub 2017 Oct 6.

Department of Medicine, Obstetric Medicine and Pregnancy and Heart Disease Programs, Mount Sinai Hospital and University Health Network, University of Toronto, Toronto, Ontario, Canada. Electronic address:

Pregnancy in women with repaired truncus arteriosus (TA) is rare. We report the outcomes of 8 pregnancies in 4 women with surgically repaired TA. None of the women had adverse cardiac events during pregnancy. Read More

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http://dx.doi.org/10.1016/j.cjca.2017.09.018DOI Listing
December 2017
14 Reads

Role of computed tomography angiography in the differentiation of feline truncus arteriosus communis from pulmonary atresia with ventricular septal defect.

J Vet Cardiol 2017 Dec 27;19(6):514-522. Epub 2017 Oct 27.

Department of Clinical Sciences, Colorado State University, Campus Delivery 1678, Fort Collins, CO 80523-1678, USA.

Two domestic shorthair cats, a 6-month-old castrated male and a 7-month-old intact female, were diagnosed with complex congenital heart disease. Transthoracic echocardiography in both cats revealed a dilated arterial trunk overriding the interventricular septum with a large ventricular septal defect. The pulmonary trunk and branch pulmonary arteries were not visible using standard echocardiographic views in either cat. Read More

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http://dx.doi.org/10.1016/j.jvc.2017.09.004DOI Listing
December 2017
7 Reads

A rare mechanism of aortic regurgitation in a young patient.

Echocardiography 2017 12 29;34(12):1948-1949. Epub 2017 Oct 29.

Department of Cardiology, University of Health Sciences, Division of Kosuyolu Heart & Research Hospital, Istanbul, Turkey.

A 19-year-old male patient was admitted to our institute with dyspnea. His medical history had no rheumatic fever or infective endocarditis. Physical examination revealed a diastolic murmur over the aortic area, rales of bilateral lungs. Read More

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http://dx.doi.org/10.1111/echo.13741DOI Listing
December 2017
9 Reads

Ex utero intrapartum treatment-to-extracorporeal membrane oxygenation followed by cardiac operation for truncus arteriosus communis.

Interact Cardiovasc Thorac Surg 2018 02;26(2):353-354

Department of Cardiovascular and Thoracic Surgery, Hokkaido University Hospital, Sapporo, Japan.

Extracorporeal membrane oxygenation has been recently indicated as an ex utero intrapartum treatment procedure for placental support in patients with a large thoracic mass. In our case, a foetus with truncus arteriosus communis and hydrops with ventricular failure due to severe truncal valve stenosis was delivered under ex utero intrapartum treatment-to-extracorporeal membrane oxygenation at 34 weeks of gestation. The neonate underwent truncal valve plasty. Read More

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http://dx.doi.org/10.1093/icvts/ivx303DOI Listing
February 2018
7 Reads

Prenatal diagnosis of truncus arteriosus in the first trimester with a high frequency curved transducer.

J Obstet Gynaecol 2018 Apr 19;38(3):419-420. Epub 2017 Oct 19.

a Department of Ultrasound , Shenzhen People's Hospital, Jinan University , Shenzhen , Guangdong , China.

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http://dx.doi.org/10.1080/01443615.2017.1360848DOI Listing
April 2018
15 Reads

The Perception of a Three-Dimensional-Printed Heart Model from the Perspective of Different Stakeholders: A Complex Case of Truncus Arteriosus.

Front Pediatr 2017 28;5:209. Epub 2017 Sep 28.

School of Clinical Sciences, Bristol Heart Institute, University of Bristol, Bristol, United Kingdom.

The case of an 11-year-old male patient with truncus arteriosus is presented. The patient has a right aortic arch, a repaired truncus arteriosus, pulmonary artery stenosis, as well as conduit stenosis, with a complex surgical plan being discussed. In order to gather additional insight into the patient's anatomy prior to the surgery and to facilitate communication with the patient's parents, a three-dimensional (3D) model of his heart and main vessels was created from computed tomography data. Read More

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http://dx.doi.org/10.3389/fped.2017.00209DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5626947PMC
September 2017
9 Reads

An Unusual Combination of Truncus Arteriosus, Interrupted Aortic Arch, and Hypoplastic Left Ventricle.

World J Pediatr Congenit Heart Surg 2018 11 19;9(6):714-717. Epub 2017 Sep 19.

1 Heart Centre for Children, The Children's Hospital at Westmead, Westmead, New South Wales, Australia.

Truncus arteriosus (common arterial trunk) is known to be associated with interrupted aortic arch in 10% to 15% of cases. However, the association of either of these lesions with a hypoplastic left ventricle is rare. The combination of all three of these lesions along with an intact interventricular septum is virtually unknown with only two cases reported in the literature. Read More

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http://dx.doi.org/10.1177/2150135117716886DOI Listing
November 2018
9 Reads

Cardio-cephalic neural crest syndrome: A novel hypothesis of vascular neurocristopathy.

Authors:
M Komiyama

Interv Neuroradiol 2017 Dec 16;23(6):572-576. Epub 2017 Aug 16.

Department of Neuro-Intervention, Osaka City General Hospital, Osaka, Japan.

A novel hypothesis proposes that "cardio-cephalic neural crest (NC) syndrome," i.e. cephalic NC including cardiac NC, contributes to the concurrent occurrence of vascular diseases in the cardio- and cerebrovascular regions. Read More

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http://dx.doi.org/10.1177/1591019917726093DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5814071PMC
December 2017
9 Reads

Role of Transesophageal Echocardiography in Surgery for Hemitruncus Arteriosus.

Anesth Analg 2017 Oct;125(4):1153-1155

From the *Department of Anesthesiology and †Department of Cardiovascular and Thoracic Surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, Kerala, India.

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http://dx.doi.org/10.1213/ANE.0000000000002306DOI Listing
October 2017
5 Reads

Prenatal screening of fetal ventriculoarterial connections: benefits of 4D technique in fetal heart imaging.

Cardiovasc Ultrasound 2017 Jun 23;15(1):17. Epub 2017 Jun 23.

Department of Sonography, Shengjing Hospital of China Medical University, Heping District, Shenyang, China.

Background: Identification of prenatal ventriculoarterial connections in fetuses with conotruncal anomalies (CTA) remains one of the greatest challenges for sonographers performing screening examinations. Herein, we propose a novel protocol of 4D volume analysis that identifies ventriculoarterial connections and evaluate its clinical utility in routine screenings.

Methods: Twenty-nine cases of transposition of the great arteries (TGA), 22 cases of double-outlet right ventricle (DORV), 36 cases of tetralogy of Fallot (TOF), 14 cases of truncus arteriosus (TCA), and randomly selected 70 normal fetuses were reviewed in this study. Read More

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http://dx.doi.org/10.1186/s12947-017-0108-5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5481875PMC
June 2017
53 Reads

Perventricular Implantation of Melody Valve in Child With Pulmonary Hypertension After a Potts Shunt.

Ann Thorac Surg 2017 Jul;104(1):e67-e69

Department of Pediatric Cardiac Surgery, Jagiellonian University, Krakow, Poland.

The Potts operation is a surgical option for the treatment of children with suprasystemic pulmonary arterial hypertension (PAH). Its positive hemodynamic effect may be obliterated by pulmonary valvar insufficiency. We describe a case in which the Potts shunt was followed by perventricular Melody valve implantation in the pulmonary position in a 12-kg child with a previously repaired truncus arteriosus communis (TAC) in whom PAH developed. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2017.01.084DOI Listing
July 2017
8 Reads

Dyspnoea on exertion in a 53-year-old woman.

Heart 2017 09 10;103(17):1390-1391. Epub 2017 Jun 10.

Division of Interventional Cardiology, Onassis Cardiac Surgery Center, Athens, Greece.

Clinical Introduction: A 53-year-old woman with no previous medical history complained of easy fatigue over the last 6 months. She had a positive family history for coronary artery disease but no other risk factors. On physical examination, a 3/6 pansystolic murmur was heard over the apex, and the lung auscultation was unremarkable. Read More

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http://dx.doi.org/10.1136/heartjnl-2017-311256DOI Listing
September 2017
8 Reads

Cyanotic Congenital Heart Disease: Essential Primer for the Practicing Radiologist.

Radiol Clin North Am 2017 Jul 6;55(4):693-716. Epub 2017 Apr 6.

Department of Radiology, Boston Children's Hospital and Harvard Medical School, 300 Longwood Avenue, Boston, MA 02115, USA.

The cyanotic congenital heart diseases are a rare and heterogeneous group of disorders, often requiring urgent neonatal management. Although echocardiography is the mainstay for imaging, continued technological advances have expanded the role for computed tomography and magnetic resonance imaging, helping to limit invasive cardiac catheterization. In this article, the authors review the broad spectrum of cyanotic congenital heart disease, focusing on the utility of advanced noninvasive imaging modalities while highlighting key clinical features and management considerations. Read More

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http://dx.doi.org/10.1016/j.rcl.2017.02.009DOI Listing
July 2017
7 Reads

Thrombus formation in the interrupted segment of the aorta.

Echocardiography 2017 Jun 7;34(6):945-946. Epub 2017 Apr 7.

Department of Cardiology, Hitit University Çorum Training and Research Hospital, Çorum, Turkey.

Interrupted aorta is a very rare heart defect in which there is a gap between the ascending and the descending thoracic aorta. It is usually associated with other cardiac anomalies, including ventricular septal defect, ductus arteriosus, and truncus arteriosus. Severe cases present with serious complications such as hypertension, heart failure, or intracranial hemorrhage. Read More

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http://dx.doi.org/10.1111/echo.13536DOI Listing
June 2017
12 Reads

Hemolytic Anemia due to Right Ventricular to Pulmonary Artery Conduit Stenosis.

J Pediatr Hematol Oncol 2017 07;39(5):e290-e292

Departments of *Pediatrics, Division of Pediatric Hematology-Oncology-Transplantation †Pediatrics, Division of Pediatric Cardiology ‡Pathology and Laboratory Medicine §Medical Imaging Administration, Ann & Robert H. Lurie Children's Hospital of Chicago, Northwestern University Feinberg School of Medicine.

Hemolytic anemia is a well-recognized complication in patients with left-sided mechanical heart valves. It is rare to see hemolysis with a bioprosthetic valve in the right ventricular outflow tract. We report a 4-year-old-girl with history of truncus arteriosus status-post repair who developed hemolytic anemia as a result of a calcified and obstructed bioprosthetic right ventricular to pulmonary artery-valved conduit. Read More

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http://dx.doi.org/10.1097/MPH.0000000000000801DOI Listing
July 2017
13 Reads

Transseptal Anchored Vascular Plug Closure of Mitral Valve Perforation.

JACC Cardiovasc Interv 2017 03 15;10(5):e45-e46. Epub 2017 Feb 15.

Division of Pediatric Cardiology, Children's Healthcare of Atlanta, Atlanta, Georgia; Department of Pediatrics, Emory University School of Medicine, Atlanta, Georgia.

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http://dx.doi.org/10.1016/j.jcin.2016.12.004DOI Listing
March 2017
27 Reads

Temporally Distinct Six2-Positive Second Heart Field Progenitors Regulate Mammalian Heart Development and Disease.

Cell Rep 2017 01;18(4):1019-1032

Departments of Urology and Surgery, Boston Children's Hospital and Harvard Medical School, 300 Longwood Avenue, Boston, MA 02115, USA. Electronic address:

The embryonic process of forming a complex structure such as the heart remains poorly understood. Here, we show that Six2 marks a dynamic subset of second heart field progenitors. Six2-positive (Six2) progenitors are rapidly recruited and assigned, and their descendants are allocated successively to regions of the heart from the right ventricle (RV) to the pulmonary trunk. Read More

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http://dx.doi.org/10.1016/j.celrep.2017.01.002DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7032615PMC
January 2017
90 Reads

Intramural Coronary Artery in Truncus Arteriosus: Importance of Preoperative Echocardiographic Diagnosis and Impact on Surgical Planning.

World J Pediatr Congenit Heart Surg 2018 05 25;9(3):368-370. Epub 2017 Jan 25.

1 Division of Cardiology, Department of Pediatrics, Oklahoma University Children Hospital, Oklahoma University Health Sciences Center, Oklahoma City, OK, USA.

Coronary artery anomalies are known to be associated with truncus arteriosus (common arterial trunk). Delineation of coronary anatomy preoperatively is important to avoid complications intraoperatively and postoperatively. We report the case of a 12-year-old boy with repaired truncus arteriosus who presented with moderate to severe truncal valve regurgitation and severe conduit stenosis. Read More

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http://dx.doi.org/10.1177/2150135116682453DOI Listing
May 2018
7 Reads

Bicuspization of a quadricuspid truncal valve.

Multimed Man Cardiothorac Surg 2017 01 16;2017. Epub 2017 Jan 16.

Though relatively rare, quadricuspid truncal valves are associated with significant valve regurgitation that often necessitates surgical correction. We present the repair of a quadricuspid truncal valve using a bicuspidization technique. Read More

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http://dx.doi.org/10.1510/mmcts.2017.002DOI Listing
January 2017
7 Reads

Fetal trisomy 8 mosaicism associated with truncus arteriosus Type I.

Ultrasound Obstet Gynecol 2017 10 5;50(4):541-542. Epub 2017 Sep 5.

Division of Maternal Fetal Medicine, Department of Obstetrics and Gynecology, State University of New York (SUNY), Downstate Medical Center, 450 Clarkson Avenue, Box 24, Brooklyn, NY, USA.

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http://doi.wiley.com/10.1002/uog.17411
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http://dx.doi.org/10.1002/uog.17411DOI Listing
October 2017
4 Reads

Initial Experience with Elective Perventricular Melody Valve Placement in Small Patients.

Pediatr Cardiol 2017 Mar 20;38(3):575-581. Epub 2016 Dec 20.

Children's Hospital of Georgia, Augusta University, 1120 15th Street BA 8300, Augusta, GA, 30912, USA.

Perventricular Melody valve placement has been described as a bailout approach or alternative RVOT approach in patients >30 kg. We present three patients <20 kg and two patients with limited venous access, where we electively performed the perventricular approach. Retrospective analysis of patients <30 kg and vascular access limitation undergoing elective hybrid pulmonary valve replacement were reviewed. Read More

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http://dx.doi.org/10.1007/s00246-016-1550-0DOI Listing
March 2017
19 Reads

Intra- and inter-reader reproducibility of blood flow measurements on the ascending aorta and pulmonary artery using cardiac magnetic resonance.

Radiol Med 2017 Mar 22;122(3):179-185. Epub 2016 Nov 22.

Radiology Unit, Research Hospital Policlinico San Donato, Via Morandi 30, 20097, San Donato Milanese, Italy.

The aim of our study was to estimate the intra- and inter-reader reproducibility of blood flow measurements in the ascending aorta and main pulmonary artery using cardiac magnetic resonance (CMR) and a semi-automated segmentation method. The ethics committee approved this retrospective study. A total of 50 consecutive patients (35 males and 15 females; mean age±standard deviation 27±13 years) affected by congenital heart disease were reviewed. Read More

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http://dx.doi.org/10.1007/s11547-016-0706-6DOI Listing
March 2017
31 Reads

Percutaneous closure of isolated ostium secundum-type atrial septal defect in a patient with Mayer-Rokitansky-Küster-Hauser syndrome.

Rev Port Cardiol 2016 Dec 16;35(12):701.e1-701.e3. Epub 2016 Nov 16.

Department of Radiology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey.

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized by complete or partial aplasia of the uterus and the upper part of the vagina. It is reported to be associated with cardiovascular disorders including atrial septal defect, anomalous pulmonary venous return, aortopulmonary window, pulmonary valve stenosis, mitral valve prolapse, tetralogy of Fallot, truncus arteriosus, and patent ductus arteriosus. Herein, for the first time in the medical literature, we present percutaneous closure of an isolated ostium secundum atrial septal defect in this syndrome. Read More

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http://dx.doi.org/10.1016/j.repc.2016.02.008DOI Listing
December 2016
24 Reads