450 results match your criteria Truncus Arteriosus Imaging


Diagnostic quality of 3Tesla postmortem magnetic resonance imaging in fetuses with and without congenital heart disease.

Am J Obstet Gynecol 2021 Mar 1. Epub 2021 Mar 1.

Department of Biomedical Imaging and Image-Guided Therapy, Medical University of Vienna, Vienna, Austria.

Background: Postmortem confirmation of prenatally diagnosed congenital heart disease after termination of pregnancy and evaluation of potential cardiac defects after spontaneous fetal or neonatal death are essential. Conventional autopsy rates are decreasing, and 1.5Tesla magnetic resonance imaging has demonstrated limited diagnostic accuracy for postmortem cardiovascular assessment. Read More

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A case of computed tomography diagnosis of truncus arteriosus type IV.

Oxf Med Case Reports 2021 Feb 15;2021(2):omaa144. Epub 2021 Feb 15.

Department of Radiology, Kilimanjaro Christian Medical Centre, Moshi, Tanzania.

Persistent truncus arteriosus is a rare congenital heart disease with four variants, and the last being the rarest. The prognosis without surgical intervention is poor. In such cases, an echocardiography is not sufficient hence computed tomography (CT) imaging is required. Read More

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February 2021

Multimodality imaging before persistent truncus arteriosus repair in a 36-year-old woman.

Eur Heart J Case Rep 2020 Dec 9;4(6):1-2. Epub 2020 Nov 9.

Université de Paris, Hôpital Européen Georges Pompidou, 20-40 Rue Leblanc, 75908 Paris, France.

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December 2020

Increased Aortic Stiffness and Left Ventricular Dysfunction Exist After Truncus Arteriosus Repair.

Ann Thorac Surg 2020 Dec 8. Epub 2020 Dec 8.

Division of Pediatric Cardiothoracic Surgery, University of Colorado School of Medicine, Children's Hospital Colorado.

Background: The purpose of this study was to determine if aortic biomechanical properties are abnormal in children with repaired truncus arteriosus (TA) and to concurrently evaluate left ventricular function post-repair utilizing a novel platform for regional ventricular function.

Methods: Cardiac magnetic resonance (CMR) studies from 26 children (mean age: 15.6±7. Read More

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December 2020

Unilateral Branch Pulmonary Artery Origin From a Solitary Arterial Trunk With Major Aortopulmonary Collaterals to the Contralateral Lung: Anatomic and Developmental Considerations.

Semin Thorac Cardiovasc Surg 2020 Nov 9. Epub 2020 Nov 9.

Department of Pediatrics, Division of Pediatric Cardiology, Stanford University School of Medicine, Palo Alto, California.

In both truncus arteriosus communis (TAC) and tetralogy of Fallot (TOF), there is a rare phenotype that includes a single branch pulmonary artery (PA) arising from a solitary great artery and major aortopulmonary collaterals (MAPCAs) supplying the contralateral lung. We describe the intracardiac and great vessel anatomy of infants with this phenotype, consider rationale for classifying patients as TOF vs TAC, and describe surgical outcomes. Our institution's surgical database was reviewed for patients with a single branch PA from a solitary arterial trunk and contralateral MAPCAs from 2007 to 2019. Read More

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November 2020

CABG With Internal Thoracic Artery in Children With Congenital Heart Defects: A Good Option When It Is the Only One.

World J Pediatr Congenit Heart Surg 2020 Nov;11(6):748-752

Division of Cardiovascular Surgery, 218809Hospital Universitario Austral. Pilar, Buenos Aires, Argentina.

Objective: Coronary complications may present during or after repair of congenital heart defects. We report coronary artery bypass grafting (CABG) by internal thoracic artery (ITA) grafts to either coronary artery in children with congenital anomalies.

Methods: Four cases who underwent CABG with ITA grafts from March 2016 to March 2020 were retrospectively reviewed. Read More

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November 2020

Pattern of congenital heart disease among children presenting to the Uganda Heart Institute, Mulago Hospital: a 7-year review.

Afr Health Sci 2020 Jun;20(2):745-752

Uganda Heart Institute.

Background: Congenital heart disease (CHD) is the most common congenital anomaly in children. Over half of the deaths due to CHD occur in the neonatal period. Most children with unrepaired complex heart lesions do not live to celebrate their first birthday. Read More

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Segmental Pulmonary Hypertension in Children with Congenital Heart Disease.

Medicina (Kaunas) 2020 Sep 24;56(10). Epub 2020 Sep 24.

Department of Pediatric Cardiology, University of Colorado Health Science Center, Children's Hospital of Colorado, Denver, CO 80045, USA.

Segmental pulmonary hypertension is a complex condition in children that encompasses many congenital heart diseases including pulmonary atresia with ventricular septal defect, hemitruncus/truncus arteriosus with branch pulmonary artery stenosis, unilateral absent pulmonary artery, and several post-tricuspid shunt lesions. Multimodality imaging is required to confirm and assess pulmonary vascular disease in subjects with major aorto-pulmonary collaterals. We describe 3 children with complex congenital heart defects who have a variable degree of segmental pulmonary hypertension and discuss management strategies and the role of interventional and/or pulmonary hypertension targeted therapies. Read More

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September 2020

First Trimester Prenatal Diagnosis of a Conotruncal Anomaly Using Spatiotemporal Image Correlation Imaging Confirmed by Conventional Autopsy.

Fetal Pediatr Pathol 2020 Aug 20:1-5. Epub 2020 Aug 20.

Department of Fetal medicine, Annai Velankanni Multispeciality Hospital, Tirunelveli, Tamil Nadu, India.

Background: Fetal echocardiography continues to be the first line investigation for detecting congenital heart diseases (CHD). As accurate and complete diagnosis of complex heart disease is often difficult in the first trimester due to small size of the fetal heart, confirmation/expanded description by fetopsy provides the best information for accurate counseling for future pregnancies. Although non invasive fetal autopsy alternatives have been investigated with favorable results, conventional autopsy remains the gold standard procedure used to confirm the fetal abnormalities. Read More

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Rare Association of an Intramural Coronary Artery and Truncus Arteriosus.

Heart Lung Circ 2020 Nov 7;29(11):e263-e264. Epub 2020 Jul 7.

Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Heart Research Group, Murdoch Children's Research Institute, Melbourne, Vic, Australia; Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine, Melbourne, Vic, Australia. Electronic address:

The association of truncus arteriosus (TA) and an intramural coronary artery is rare. Seven (7) patients had TA and an intramural coronary artery at the Royal Children's Hospital, Melbourne between 1996 and 2018. Four (4) patients underwent concomitant unroofing of their intramural coronary artery. Read More

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November 2020

Truncus Arteriosus With Double Aortic Arch.

World J Pediatr Congenit Heart Surg 2020 07;11(4):507-508

Department of Cardiovascular and Thoracic Surgery, U. N. Mehta Institute of Cardiology and Research Center (Affiliated to B. J. Medical College, Ahmedabad), New Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India.

Truncus arteriosus (TA) or common arterial trunk is a congenital cardiac anomaly having high association with arch anomalies such as right aortic arch or aortic arch interruption. However, TA with double aortic arch (DAA) is a rare occurrence. We report a case of TA with DAA where the diagnosis of DAA was missed initially. Read More

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Hemitruncus Arteriosus in a 10-Day-Old Neonate with Patent Ductus Arteriosus and Thrombocytopenia.

Vasc Health Risk Manag 2020 1;16:99-101. Epub 2020 Apr 1.

Student Research Committee, Urmia University of Medical Sciences, Urmia, Iran.

Hemitruncus arteriosus refers to an uncommon congenital cardiovascular abnormality. It usually presents in infancy and leads to the development of pulmonary hypertension, heart failure, and in severe cases maybe death. Herein, we reported hemitruncus arteriosus in a 10-day-old neonate with respiratory distress, patent ductus arteriosus, and thrombocytopenia. Read More

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Congenital hypothyroidism, cardiac defects, and pancreatic agenesis in an infant with GATA6 mutation.

Am J Med Genet A 2020 06 24;182(6):1496-1499. Epub 2020 Mar 24.

Division of Clinical and Metabolic Genetics, The Hospital for Sickkids, University of Toronto, Toronto, Ontario, Canada.

GATA6 pathogenic variants primarily manifest a phenotype with pancreatic agenesis and cardiac malformations. However, additional congenital malformations affecting the biliary system, congenital diaphragmatic hernia and developmental delay have been reported. We report a newborn, prenatally diagnosed with truncus arteriosus and intrauterine growth restriction, who was postnatally found to have pancreatic agenesis associated with neonatal diabetes and hepatobiliary abnormalities. Read More

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Surgical Repair of Peripheral Pulmonary Artery Stenosis in Patients Without Williams or Alagille Syndromes.

Semin Thorac Cardiovasc Surg 2020 Winter;32(4):973-979. Epub 2020 Jan 17.

Division of Pediatric Cardiac Surgery, Stanford University School of Medicine, Lucile Packard Children's Hospital, Stanford, California.

Peripheral pulmonary artery stenosis is a relatively rare form of congenital heart disease typically associated with genetic syndromes, such as Williams or Alagille syndromes. However, some patients present with severe stenosis without associated syndromes. The purpose of the study was to review our surgical experience in such patients. Read More

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Characterization of size, shape and pattern of flow in the neo-aorta and pulmonary artery in a patient following an innovative technique of repair for truncus arteriosus.

Glob Cardiol Sci Pract 2019 Sep 20;2019(2):e201918. Epub 2019 Sep 20.

Department of Surgery, Aswan Heart Centre, Magdi Yacoub Heart Foundation, Egypt.

Truncus arteriosus (TA) caries a very poor prognosis. In the absence of early correction, only 12 percent of patients born with this anomaly survive beyond one year. There is no agreement about the best method of surgical correction of this anomaly. Read More

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September 2019

From an innocent heart murmur to pulmonary arterial hypertension.

Bol Med Hosp Infant Mex 2019 ;76(6):287-293

Cardiología Pediátrica, Instituto Nacional de Pediatría, Ciudad de México, México.

Background: The detection of congenital heart disease in newborns, based on a heart murmur or cyanosis is not effective. Critical congenital heart diseases, such as truncus arteriosus (TA), cause most of neonatal deaths due to congenital malformations. The screening for pulse oximetry in newborns detects up to 70% of these heart diseases. Read More

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Utilization of inhaled nitric oxide after surgical repair of truncus arteriosus: A multicenter analysis.

Congenit Heart Dis 2019 Nov 11;14(6):1078-1086. Epub 2019 Nov 11.

Department of Pediatrics, Division of Critical Care Medicine, University of Utah School of Medicine, Primary Children's Hospital, Salt Lake City, Utah.

Background: Elevated pulmonary vascular resistance (PVR) is common following repair of truncus arteriosus. Inhaled nitric oxide (iNO) is an effective yet costly therapy that is frequently implemented postoperatively to manage elevated PVR.

Objectives: We aimed to describe practice patterns of iNO use in a multicenter cohort of patients who underwent repair of truncus arteriosus, a lesion in which recovery is often complicated by elevated PVR. Read More

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November 2019

Quadricuspid Neoaortic Valve in Truncus Arteriosus Type II.

Radiol Cardiothorac Imaging 2019 Oct 31;1(4):e190074. Epub 2019 Oct 31.

Departments of Radiology and Nuclear Medicine (M.E.F., R.P.J.B.), Pediatric Cardiology (M.D.), and Cardiothoracic Surgery (A.J.J.C.B.), Erasmus Medical Center, Rotterdam, the Netherlands; and Department of Radiology, AZ Monica, Deurne, Belgium (M.E.F.).

Supplemental material is available for this article. Read More

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October 2019

Type A3 truncus arteriosus with infracardiac total anomalous pulmonary venous return and single ventricle physiology: A triad of tribulations.

J Cardiovasc Comput Tomogr 2020 Nov - Dec;14(6):e137-e138. Epub 2019 Sep 23.

Department of Cardiovascular Radiology & Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, 110029, India. Electronic address:

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February 2021

Characteristics of Cardiovascular Magnetic Resonance Imaging and Outcomes in Adults With Repaired Truncus Arteriosus.

Am J Cardiol 2019 11 22;124(10):1636-1642. Epub 2019 Aug 22.

Joint Department of Medical Imaging, University Health Network, Toronto General Hospital, Toronto, Ontario, Canada; Peter Munk Cardiac Centre, University Health Network, Toronto General Hospital, Toronto, Ontario, Canada. Electronic address:

The cardiovascular magnetic resonance imaging (CMR) features of adults with repaired truncus arteriosus (rTA) are largely undefined. We sought to explore CMR characteristics in rTA and to identify associations between imaging findings and cardiovascular outcomes. Adults with rTA and CMR were identified and anatomic subtypes (1-4) were assigned (Collett and Edwards classification). Read More

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November 2019

Tricuspid Atresia With Truncus Arteriosus: Off-Pump Stage I Palliation.

World J Pediatr Congenit Heart Surg 2019 09;10(5):635-637

Department of Pediatric Cardiac Sciences, Sir Ganga Ram Hospital, New Delhi, Delhi, India.

Coexistence of tricuspid atresia and truncus arteriosus (common arterial trunk) is an extremely rare combination of anomalies and requires staged palliation. Initial palliation involves disconnection of the pulmonary arteries from the common trunk and creation of a systemic-to-pulmonary artery shunt. This has generally been accomplished with the use of cardiopulmonary bypass. Read More

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September 2019

GATA6 mutations: Characterization of two novel patients and a comprehensive overview of the GATA6 genotypic and phenotypic spectrum.

Am J Med Genet A 2019 09 12;179(9):1836-1845. Epub 2019 Jul 12.

Department of Clinical Genetics, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.

The first human mutations in GATA6 were described in a cohort of patients with persistent truncus arteriosus, and the phenotypic spectrum has expanded since then. This study underscores the broad phenotypic spectrum by presenting two patients with de novo GATA6 mutations, both exhibiting complex cardiac defects, pancreatic, and other abnormalities. Furthermore, we provided a detailed overview of all published human genetic variation in/near GATA6 published to date and the associated phenotypes (n = 78). Read More

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September 2019

Truncus arteriosus communis associated with interrupted aortic arch - Type B and right aberrant subclavian artery: A rare entity.

J Cardiovasc Comput Tomogr 2020 Sep - Oct;14(5):e73-e74. Epub 2019 Apr 19.

Department of Pediatric Cardiology, Faculty of Medicine, Comenius University, Bratislava, Slovakia; Cardiac Department, Pediatric Cardiac Center, National Institute of Cardiovascular Diseases, Bratislava, Slovakia.

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October 2020

Atypical variant of truncus arteriosus: sinusal origin of pulmonary artery segment with non-confluent branch pulmonary arteries.

BMJ Case Rep 2019 Apr 24;12(4). Epub 2019 Apr 24.

Cardiovascular Radiology and Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India.

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Anomalous origin of left vertebral artery from ascending aorta associated with interrupted aortic arch and persistent truncus arteriosus.

Cardiol Young 2019 Mar 4;29(3):414-415. Epub 2019 Feb 4.

Department of Cardiovascular Radiology and Endovascular Interventions,All India Institute of Medical Sciences,New Delhi-110029,India.

We present a case of a 3-week-old boy with persistent truncus arteriosus associated with interrupted right aortic arch having an anomalous origin of the left vertebral artery from the ascending aorta. Read More

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Truncus Arteriosus With Major Aortopulmonary Collateral Arteries.

Ann Thorac Surg 2019 08 30;108(2):e105-e106. Epub 2019 Jan 30.

Department of Pediatric Cardiology, Hyogo Prefectural Amagasaki General Medical Center, Hyogo, Japan.

Truncus arteriosus with the absence of one branching pulmonary artery and presence of major aortopulmonary collateral arteries is rare. A small patient, with a birth weight of 2,219 g, was successfully repaired by a staged approach, after banding of the left pulmonary artery and unifocalization of major aortopulmonary collateral arteries. Read More

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Persistent truncus arteriosus with absent semilunar valve in first trimester.

J Med Ultrason (2001) 2019 Apr 14;46(2):273-275. Epub 2019 Jan 14.

Department of Obstetrics, The Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China.

Persistent truncus arteriosus (PTA) is a relatively uncommon congenital heart disease, accounting for approximately 0.7-1.4% of all congenital cardiac abnormalities worldwide. Read More

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Common Arterial Trunk: Physiology, Imaging, and Management.

Semin Cardiothorac Vasc Anesth 2019 Jun 29;23(2):225-236. Epub 2018 Dec 29.

3 Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Common arterial trunk (CAT), or truncus arteriosus, is a rare form of cyanotic congenital heart disease and is highly associated with DiGeorge syndrome (microdeletion 22q11.2). Prenatal diagnosis is highly feasible, allowing proper delivery planning and postnatal management. Read More

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Neonatal quadricuspid truncal valve repair with left coronary artery unroofing.

J Thorac Cardiovasc Surg 2019 02 5;157(2):710-711. Epub 2018 Oct 5.

Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Victoria, Australia; Heart Research Group, Murdoch Children's Research Institute, Melbourne, Victoria, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Victoria, Australia; Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine, Melbourne, Victoria, Australia.

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February 2019