239 results match your criteria Steatocystoma Multiplex


Eruptive Vellus Hair Cyst: An Uncommon and Underdiagnosed Entity.

Int J Trichology 2018 Jan-Feb;10(1):31-33

Department of Dermatology, Hindu Rao Hospital and NDMC Medical College, NewDelhi, India.

Eruptive vellus hair cyst (EVHC) is a rare follicular developmental abnormality of the vellus hair follicles. They are usually seen in children, adolescents, or young adults and manifest as reddish-brown smooth papules most commonly involving the chest, limbs, and abdomen. An 18-year-old male presented with asymptomatic papules on the trunk and flexor aspect of both forearms for the past 2 years. Read More

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February 2018

Cutaneous Cysts with Nail Dystrophy in a Young Female: A Classical Association.

Indian J Dermatol 2017 Nov-Dec;62(6):661-664

Department of Dermatology, Venereology and Leprosy, School of Tropical Medicine, Kolkata, West Bengal, India.

Pachyonychia Congenita (PC) refers to a group of autosomal dominant disorders with variable clinical presentations. While nail dystrophy and plantar keratoderma are the most consistent features in all the variants, a myriad of other manifestations has been observed. This report highlights a case of young female presenting with multiple asymptomatic cutaneous cysts associated with plantar kearatoderma and nail dystrophy. Read More

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December 2017
6 Reads

A recurrent mutation in the KRT17 gene responsible for severe steatocystoma multiplex in a large Chinese family.

Clin Exp Dermatol 2018 Mar 8;43(2):205-208. Epub 2017 Dec 8.

Department of Dermatology, Xinhua Hospital, Shanghai Jiaotong University School of Medicine, 1665 Kongjiang Road, Shanghai, 200092, China.

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March 2018
5 Reads

Co-occurrence of steatocystoma multiplex, eruptive vellus hair cysts, and trichofolliculomas.

Cutis 2017 Jul;100(1):E23-E26

Department of Dermatology and the Department of Laboratory Medicine, Mayo Clinic, Rochester, Minnesota, USA.

An association between steatocystoma multiplex (SCM) and eruptive vellus hair cysts (EVHCs) has been recognized. Steatocystoma multiplex and EVHC have similar clinical features but distinctive histologic features. Rare cases of co-occurrence of these conditions have been known to occur on the trunk and the forehead. Read More

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July 2017
4 Reads

Case Series: A Kindred With Eruptive Vellus Hair Cysts and Systemic Features.

J Cutan Med Surg 2017 Nov/Dec;21(6):564-567. Epub 2017 Jun 28.

1 Department of Dermatology and Skin Science, University of British Columbia, Vancouver, British Columbia, Canada.

Eruptive vellus hair cysts (EVHCs) often occur on the trunk and limbs. Facial involvement is uncommon. Autosomal dominant inheritance has been described, but associated extracutaneous anomalies have not. Read More

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June 2017
2 Reads

A Tale of Two Cysts: Steatocystoma Multiplex and Eruptive Vellus Hair Cysts-Two Case Reports and a Review of the Literature.

Case Rep Dermatol Med 2017 5;2017:3861972. Epub 2017 Apr 5.

College of Medicine, University of Illinois-Chicago, Urbana Campus, 506 South Mathews Ave., 190 Medical Sciences Building, MC-714, Urbana, IL 61801, USA.

. Steatocystoma multiplex (SM) and eruptive vellus hair cysts (EVHC) are uncommon benign tumors of the pilosebaceous unit. Both SM and EVHC are characterized by smooth, asymptomatic papules or nodules, most commonly presenting on the chest, limbs, and abdomen. Read More

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April 2017
3 Reads

Steatocystoma multiplex suppurativa: case report of a rare condition.

An Bras Dermatol 2016 Sep-Oct;91(5 suppl 1):51-53

Universidade do Estado do Rio de Janeiro (UERJ) - Rio de Janeiro (RJ), Brazil.

Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. Read More

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July 2017
5 Reads

Pachyonychia congenita with late onset (PC tarda).

Indian Dermatol Online J 2016 Jul-Aug;7(4):278-80

Department of Dermatology, Maharajah's Institute of Medical Sciences, Nellimarla, Andhra Pradesh, India.

Pachyonychia congenita is a rare type of ectodermal dysplasia further classified into 4 types. Cutaneous manifestations seen in most of the cases of Pachyonychia congenita include palmoplantar keratoderma, follicular hyperkeratosis, wedge shaped nails, oral leukokeratosis and woolly hair. A 25-year-old male presented to us with thickened nails and scanty scalp hair. Read More

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August 2016
4 Reads

Fractionated ablative carbon dioxide laser treatment of steatocystoma multiplex.

J Cosmet Laser Ther 2016 Nov 19;18(7):364-366. Epub 2016 Jul 19.

b Department of Dermatology , University of California Irvine , Irvine , CA , USA.

Steatocystoma multiplex is a well-recognized condition in which subjects develop dermal cysts generally inherited in an autosomal dominant fashion, though these can occur sporadically. This case report describes the successful treatment of a 51-year-old woman with steatocystomata limited to the face, who after two treatments with a fractionated ablative carbon dioxide laser remained free of cysts for three years. We conclude that this treatment should be considered as an efficient and effective treatment option for patients with steatocystoma multiplex. Read More

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November 2016
27 Reads

Steatocystoma simplex in penile foreskin: a case report.

J Med Case Rep 2016 Mar 8;10:49. Epub 2016 Mar 8.

Biodiversity Research Center, Federal University of Roraima (CBio/UFRR), Boa Vista - RR, Brazil.

Background: Steatocystoma simplex is an uncommon skin lesion with a histological pattern that is identical to that of steatocystoma multiplex. We are reporting this case of steatocystoma simplex for its uncommon location in the penile foreskin, and its occurrence in a Wapishana man.

Case Presentation: A 56-year-old man of Wapishana ethnicity presented with complaints of referred penile discomfort and pain during sexual intercourse for 5 years. Read More

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March 2016
8 Reads

Clinical Misdiagnosis of Steatocystoma Simplex of Eyebrow in a Pediatric Patient.

Chin Med J (Engl) 2016 Feb;129(3):377-8

Institute of Plastic and Craniofacial Surgery, SOBRAPAR Hospital, Campinas, São Paulo, Brazil.

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February 2016
2 Reads

Steatocystoma multiplex is associated with the R94C mutation in the KRTl7 gene.

Mol Med Rep 2015 Oct 8;12(4):5072-6. Epub 2015 Jul 8.

Department of Dermatology, Hainan Provincial Hospital of Skin Disease, Haikou, Hainan 570206, P.R. China.

Steatocystoma multiplex (SM) is an uncommon disorder, characterized by numerous skin‑colored subcutaneous cysts. A number of SM pedigrees have been identified with mutations in the keratin 17 (KRT17) gene. The present study examined a four‑generation Chinese pedigree with an autosomal dominant mode of inheritance and examined its genetic basis. Read More

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October 2015
19 Reads

Timed exposure 10,600 nm CO2 laser drilling in various benign dermal tumours.

Eur J Dermatol 2015 Jul-Aug;25(4):358-9

Netherlands Institute for Pigment Disorders (SNIP),, Department of Dermatology, Academic Medical Center, Meibergdreef 9, 1105AZ, Amsterdam, the Netherlands.

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June 2016
2 Reads

Association of copeptin and cortisol in newly diagnosed multiple sclerosis patients.

J Neuroimmunol 2015 May 11;282:21-4. Epub 2015 Mar 11.

Department of Neuroendocrinology, Centre of Postgraduate Medical Education, Marymoncka 99/103, 01-813 Warsaw, Poland. Electronic address:

Multiple sclerosis (MS) is a chronic autoimmune disease of the central nervous system. Obesity may increase the risk of developing MS. The aim of this study was to evaluate copeptin and cortisol plasma levels in newly diagnosed untreated MS patients and to determine whether copeptin and cortisol are related to the patients' clinical statuses. Read More

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Steatocystoma multiplex with hair shaft abnormalities.

J Dermatol 2015 May 21;42(5):521-3. Epub 2015 Mar 21.

Department of Dermatology, Venereology and Pediatric Dermatology, Medical University of Lublin, Lublin, Poland.

Steatocystoma multiplex (SM) is an unusual benign disorder of the pilosebaceous duct characterized by multiple cysts with little or no nail and hair involvement. We report a 30-year-old woman with multiple cystic nodules located on the neck, axillae and forearms as well as patchy scalp alopecia. Histopathological examination of the lesions was diagnostic of SM. Read More

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May 2015
2 Reads

Polycystic kidney disease with steatocystoma multiplex: evidences for a disruptive effect of mutated polycystin-1 on keratin 17 polymerisation.

Acta Derm Venereol 2015 Mar;95(3):353-4

Department of Dermatology, Faculty of Medicine, Kagawa University, 1750-1 Ikenobe, Kita-gun Miki-cho, 761-0793 Kagawa, Japan.

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March 2015
4 Reads

Facial steatocystoma multiplex combined with eruptive vellus hair cysts: a hybrid?

J Eur Acad Dermatol Venereol 2015 Oct 30;29(10):2051-3. Epub 2014 Jul 30.

Department of Dermatology und Venereology, Otto-von-Guericke University Magdeburg, Magdeburg, Germany.

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October 2015
4 Reads

On Steatocystoma, Sebaceous Duct Cyst, Isthmic-Anagenic Cyst, and CK19.

Am J Dermatopathol 2015 Sep;37(9):733-4

Department of Cellular Pathology, Hospital El Bierzo, Ponferrada, Spain.

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September 2015
4 Reads

Cutaneous keratocyst and steatocystoma unified as sebaceous duct cyst, a hamartoma resembling the sebaceous duct.

Authors:
Mani Makhija

Am J Dermatopathol 2015 Nov;37(11):871-3

Department of Histopathology, National Reference Laboratory, Dr Lal Pathlabs, Delhi, India.

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November 2015
2 Reads

Carbon dioxide laser perforation and extirpation of steatocystoma multiplex.

Dermatol Surg 2014 Jun;40(6):658-62

*Both the authors are affiliated with the Manchester Laser Unit, Dermatology Centre, Salford Royal NHS Foundation Trust, Manchester, United Kingdom.

Background: Steatocystoma multiplex (SM) is a rare condition that presents as multiple dermal cysts, the appearance of which can have a significant impact on the patients' quality of life. Treatment options for SM are limited to surgical excision.

Objective: To present our experience of treating 8 SM cases using a novel approach that uses the carbon dioxide (CO2) laser and to explore patients' views about the treatment. Read More

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June 2014
3 Reads

Familial pachyonychia congenita with steatocystoma multiplex and multiple abscesses of the scalp due to the p.Asn92Ser mutation in keratin 17.

Br J Dermatol 2014 Dec 2;171(6):1565-7. Epub 2014 Nov 2.

Department of Dermatology, Montauban Hospital, Montauban, France.

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December 2014
3 Reads

Recurring axillary, abdominal and genitofemoral nodules and abscesses. Hereditary steatocystoma multiplex.

Acta Derm Venereol 2015 Jan;95(1):121-3

Department of Dermatology, Roskilde Hospital, Health Sciences Faculty, University of Copenhagen, Køgevej 7-13, DK-4000 Roskilde, Denmark.

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January 2015
6 Reads

Steatocystoma multiplex associated with bilateral preauricular sinuses.

J Cutan Pathol 2014 Aug 19;41(8):677-9. Epub 2014 Mar 19.

Department of Cellular Pathology, Hospital El Bierzo, Ponferrada, Spain.

Steatocystoma multiplex is characterized by the development of numerous steatocystomas. The condition has occasionally been related to congenital bilateral preauricular sinuses. Herein, we present the third case of such an association, a 34-year-old male who was born with bilateral preauricular sinuses that were surgically repaired. Read More

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August 2014
9 Reads

Steatocystoma multiplex as initial impression of non-small cell lung cancer with complete response to gefitinib.

Chin J Cancer Res 2014 Feb;26(1):E5-9

1 Department of Internal Medicine, 2 Department of Dermatology, 3 Department of Pathology, Chung Shan Medical University Hospital and School of Medicine, Chung Shan Medical University, Taichung 402, Taiwan, China.

Cutaneous metastases are rare and seldom present at the time of first diagnosis of cancer. Data from various studies show that 1-12% of lung cancer patients experience tumor spread to the skin. The scalp, chest, and abdomen are favored sites of skin metastases from lung cancers, but metastases to multiple skin sites in a single patient are rarely reported. Read More

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February 2014
2 Reads

Late onset localized steatocystoma multiplex of the vulva.

Indian J Dermatol Venereol Leprol 2014 Jan-Feb;80(1):89-90

Department of Dermatology, Chonbuk National University Medical School; Research Institute of Clinical Medicine of Chonbuk National University Biomedical Research Institute of Chonbuk National University Hospital, Jeonju, South Korea.

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April 2016
4 Reads

A novel missense mutation of keratin 17 gene in a chinese family with steatocystoma multiplex.

Ann Dermatol 2013 Nov 30;25(4):508-10. Epub 2013 Nov 30.

Institute of Dermatology, Anhui Medical University, Hefei, Anhui, China. ; The MOE Key Laboratory of Dermatology, Hefei, Anhui, China. ; Department of Dermatology and Venereology, the First Affiliated Hospital, Anhui Medical University, Hefei, Anhui, China.

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November 2013
2 Reads

Steatocystoma.

Dermatol Online J 2013 Dec 16;19(12):20721. Epub 2013 Dec 16.

New York University School of Medicine.

Steatocystoma multiplex is a rare condition that is characterized by cutaneous cysts and may be inherited in an autosomal dominant manner or may occur sporadically. The pathogenesis is hypothesized to involve mutations in the keratin 17 gene. There are no internal manifestations. Read More

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December 2013
4 Reads

Multiple cystic disease: K17 dysfunction?

Skinmed 2013 Sep-Oct;11(5):301-3

Dermatology Department, Hospital Nacional Profesor Alejandro Posadas, Buenos Aires, Argentina.

Our patient is a 29-year-old woman without any previous disease who presented with different kinds of lesions on her face, neck, and chest. She first noticed the lesions 10 years ago and, since that time, they have become more numerous. She has no affected relatives. Read More

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January 2014
6 Reads

Increased FDG uptake in scrotal steatocystoma multiplex with calcification.

Clin Nucl Med 2014 Sep;39(9):822-4

From the Departments of *Nuclear Medicine, †Pathology, and ‡Respiratory Medicine, Changhai Hospital, Second Military Medical University, Shanghai, China.

Steatocystoma multiplex is a rare, benign, sporadic or familial disorder. Steatocystoma multiplex with extensive calcification is extremely rare. A 57-year-old man presented fever and cough with expectoration for 3 weeks. Read More

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September 2014
3 Reads

A rare case of facial steatocystoma multiplex.

Acta Dermatovenerol Croat 2013 ;21(3):205-6

Derya Uçmak, MD, Department of Dermatology, Dicle University Faculty of Medicine, Diyarbakir, Turkey;

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August 2014
7 Reads

Nodular-cystic lesions on a congenital alopecic plaque.

Actas Dermosifiliogr 2014 Jan-Feb;105(1):85-6. Epub 2013 Oct 16.

Servicio de Dermatología, Hospital Gregorio Marañón, Madrid, España.

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April 2015
1 Read

Diseases associated with hidranitis suppurativa: part 2 of a series on hidradenitis.

Authors:
Noah Scheinfeld

Dermatol Online J 2013 Jun 15;19(6):18558. Epub 2013 Jun 15.

Weill Cornell Medical College, New York, NY, USA.

Hidradenitis suppurativa (HS), a pathologic follicular disease, impacts patients' lives profoundly and usually occurs in isolation. The diseases with the strongest association are obesity, depression, and pain. HS is associated with many diseases including acne conglobata (AC), dissecting cellulitis, pilonidal cysts, and obesity. Read More

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June 2013
4 Reads

Eruptive vellus hair cyst presenting as asymptomatic follicular papules on extremities.

Indian Dermatol Online J 2013 Jul;4(3):213-5

Department of Dermatology, K. J. Somaiya Medical College, Mumbai, Maharashtra, India.

Eruptive vellus hair cysts were first described in 1977. They usually appear as yellow to reddish-brown papules on the chest. Usual onset is between ages 17 and 24 years, but they may be congenital. Read More

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July 2013
7 Reads

Acral steatocystoma multiplex.

Indian Dermatol Online J 2013 Apr;4(2):156-7

Department of Pathology, Lady Hardinge Medical College and Smt. Sucheta Kriplani Hospital, New Delhi, India.

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April 2013
4 Reads

Facial papules in an adolescent with a history of natal teeth.

Pediatr Dermatol 2013 May-Jun;30(3):387-8

School of Medicine, University of Missouri, Kansas City, Missouri, USA.

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January 2014
2 Reads

Sebaceous and sweat gland disorders.

Authors:
Nigel Stollery

Practitioner 2013 Jan;257(1757):32-3

Leicester Royal Infirmary, Leicester, UK.

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January 2013
4 Reads

Steatocystoma multiplex-a rare genetic disorder: a case report and review of the literature.

J Clin Diagn Res 2013 Jan 1;7(1):166-8. Epub 2013 Jan 1.

Assistant Professor, Government Medical College , Latur, Maharashtra, India .

A 17 years old female presented with multiple asymptomatic cutaneous cysts all over body, sparing the head and neck region. The microscopic examination of the cysts showed the features of steatocystoma multiplex. This disorder, although it is asymptomatic, is a cosmetic threat to the patient. Read More

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January 2013
3 Reads

Eruptive vellus hair cysts.

Dermatol Online J 2012 Dec 15;18(12). Epub 2012 Dec 15.

The Ronald O. Perelman Department of Dermatology, New York University School of Medicine, USA.

Eruptive vellus hair cyst (EVHC), described initially in 1977, is a benign dermatologic condition that is characterized by the sudden appearance of monomorphic, follicular, asymptomatic, small papules in children and young adults. The diagnosis is based on the histopathologic findings of stratified-squamous epithelium with a granular layer that surrounds a cystic space filled with laminated keratin and a variable number of vellus hair cysts. EVHC can be associated with steatocystoma multiplex. Read More

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December 2012
11 Reads

Mammographic and sonographic findings of steatocystoma multiplex presenting as breast lumps.

Singapore Med J 2012 Dec;53(12):e261-3

National Cancer Centre, Singapore.

Steatocystoma multiplex (SM) is an uncommon cutaneous disorder characterised by multiple intradermal cysts distributed over the trunk and proximal extremities. This condition affects both genders and is often inherited as an autosomal dominant trait, although sporadic cases have been described. This report describes the mammographic and sonographic features of the cysts, which presented as breast lumps, for evaluation. Read More

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December 2012
5 Reads

Steatocystoma multiplex--an uncommon lesion with special emphasis on cytological features and cyto-histological correlation.

J Postgrad Med 2012 Jul-Sep;58(3):210-1

Department of Pathology, Subharti Medical College, NH-58, Delhi Haridwar Bypass, Meerut, Uttar Pradesh, India.

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January 2013
3 Reads

Acral subcutaneous steatocystoma multiplex: a distinct subtype of the disease?

Australas J Dermatol 2012 Aug 2;53(3):198-201. Epub 2012 Jul 2.

Dipartimento di Anestesiologia, Terapia Intensiva e Scienze Dermatologiche, Università degli Studi di Milano, U.O. Dermatologia, Fondazione IRCCS Ca' Granda-Ospedale Maggiore Policlinico, Milan, Italy.

Steatocystoma multiplex (SM) is a hamartomatous malformation of the pilosebaceous duct consisting of dermal cysts filled with a sebum-like material. SM lesions are typically located in areas with sebaceous follicles, although atypical presentations involving sites lacking sebaceous follicles have exceptionally been described. We reviewed retrospectively a series of 32 histologically diagnosed SM observed in our department in the period 2006-2010, evaluating the kinds of lesions and their locations, and family history of SM and associated disorders, to focus on the clinical features of the acral subcutaneous variety of SM and to estimate its prevalence. Read More

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August 2012
5 Reads

Multiple large infected scrotal sebaceous cysts masking Fournier's gangrene in a 32-year-old man.

BMJ Case Rep 2012 May 30;2012. Epub 2012 May 30.

Department of Urological Surgery, University Hospital Aintree, Liverpool, UK.

Extensive large sebaceous cysts on the scotum are rare and present a problem only when infected or when cosmesis is deemed unacceptable by the patient. Fournier's gangrene is an infective condition with a high death rate. We describe a case of Fournier's gangrene in a patient masked by multiple large infected scrotal sebaceous cysts. Read More

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May 2012
4 Reads

Syringoma masquerading as steatocystoma multiplex.

Indian J Dermatol Venereol Leprol 2012 May-Jun;78(3):365-6

Department of Dermatology, Sri Dharmasthala Manjunatheshwara College of Medical Sciences and Hospital, Sattur, Dharwad, Karnataka, India.

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September 2012
4 Reads

1,450-nm diode laser in combination with the 1550-nm fractionated erbium-doped fiber laser for the treatment of steatocystoma multiplex: a case report.

Dermatol Surg 2012 Jul 9;38(7 Pt 1):1104-6. Epub 2012 Apr 9.

Derm Surgery Associates, Houston, Texas, USA.

Steatocystoma multiplex (SM) is a rare condition characterized by multiple, small, asymptomatic dermal cysts. Treatment options are limited, with varying degrees of success; these include oral isotretinoin, surgical excision or drainage, and liquid nitrogen cryotherapy. The most effective method is excision, but cosmetic considerations, time, overall cost, and pain must be considered, because patients tend to have multiple cysts. Read More

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July 2012
5 Reads

Atypical steatocystoma multiplex with calcification.

ISRN Dermatol 2011 12;2011:381901. Epub 2011 Jul 12.

Cosmoderma Skin Cure Center 96/G, Nirmalabas, Sheora Road, Mymensingh 2200, Bangladesh.

A 60-year-old male reported to us with an atypical case of giant steatocystoma multiplex in the scrotum with calcification. There was no family history of similar lesions. Yellowish, creamy material was expressed from a nodule during punch biopsy. Read More

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August 2012
1 Read

Do you know this syndrome? Pachyonychia congenita.

An Bras Dermatol 2011 Nov-Dec;86(6):1222-7

Federal University of Bahia, Salvador, Brazil.

Pachyonychia Congenita is a rare genodermatosis of keratinization, first described in 1906 by Jadassohn and Lewandowsky. Besides not being well known, phenotypic variability and oligosymptomatic subtypes make the diagnosis difficult. We report a family with three generations affected, until recently not diagnosed. Read More

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September 2012
2 Reads

Steatocystoma multiplex confined to the scalp with concurrent alopecia.

Ann Dermatol 2011 Oct 31;23(Suppl 2):S258-60. Epub 2011 Oct 31.

Department of Dermatology, Busan Paik Hospital, College of Medicine, Inje University, Busan, Korea.

Steatocystoma multiplex (SM) is an uncommon disorder of the pilosebaceous unit characterized by the development of numerous sebum-containing dermal cysts which rarely involves the scalp. Here, we report a case of a 50-year-old man with multiple cystic nodules and alopecic patches on his scalp. On histopathological examination, the folded cyst was found to be lined by stratified squamous epithelium, while flattened sebaceous gland cells were identified in the cystic wall. Read More

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October 2011
2 Reads