1,228 results match your criteria Retroperitoneal Fibrosis Imaging

Retroperitoneal fibrosis as a postoperative complication following renal transplantation in cats.

J Feline Med Surg 2021 May 21:1098612X211018976. Epub 2021 May 21.

Department of Surgical Sciences, University of Wisconsin-Madison, Madison, WI, USA.

Objectives: The aim of this report was to describe the clinical signs, diagnostic imaging findings, surgical management, histopathological findings, outcome and possible risk factors for cats that developed retroperitoneal fibrosis (RPF) following renal transplantation.

Methods: Medical records of cats that underwent renal transplantation and developed clinically significant RPF between 1995 and 2019 were reviewed.

Results: Eighty-one cats underwent 83 renal transplantations. Read More

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Imaging of ureter: a primer for the emergency radiologist.

Emerg Radiol 2021 Apr 13. Epub 2021 Apr 13.

Department of Radiology, University of Texas Health, San Antonio, TX, USA.

In this review article, we will discuss the gamut of abnormalities involving the ureters. In the emergency department, ureterolithiasis is the most common indication for imaging abdomen and pelvis. However, spectrum of ureteral abnormalities including congenital, infectious and inflammatory, primary and secondary ureteral malignancies, retroperitoneal fibrosis rare described in this article may be encountered. Read More

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[A total replacement of the both ureters and urinary bladder by ileal conduit in a woman with contracted bladder and Ormonds disease].

Urologiia 2021 Mar(1):107-111

Department of urology of North-Western State Medical University named after I.I. Mechnikov, Saint Petersburg, Russia.

A description of the successful surgical treatment of a patient with irreversible changes in both ureters and bladder resulting from a severe form of Ormond's disease and interstitial cystitis, resulting in contracted bladder, is presented. For the first time in clinical practice, a one-stage cystectomy, a bilateral ureterectomy with complete replacement of both ureters and the bladder with two isoperistaltic small bowel segment was performed. The postoperative course was uneventful. Read More

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A case of idiopathic retroperitoneal fibrosis presenting as gallbladder carcinoma.

BMC Surg 2021 Mar 25;21(1):162. Epub 2021 Mar 25.

Department of Surgery, Changxing People's Hospital, No. 66, Taihu Road, Changxing, Huzhou, 313100, Zhejiang, China.

Background: Retroperitoneal fibrosis (RPF) is a rare disease with a poor prognosis characterized by systemic inflammation and fibroinflammatory tissue. Idiopathic RPF (IRPF) accounts for approximately two-thirds of RPF cases.

Case Presentation: A 56-year-old female patient with abdominal distension was admitted to Changxing Hospital. Read More

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Oncology and complications.

Arch Ital Urol Androl 2021 Mar 19;93(1):71-76. Epub 2021 Mar 19.

Urology Department, General Hospital of Athens "G. Gennimatas", Athens.

This collection of cases describes some unusual urological tumors and complications related to urological tumors and their treatment. Case 1: A case of uretero-arterial fistula in a patient with long-term ureteral stenting for ureteral oncological stricture and a second case associated to retroperitoneal fibrosis were described. Abdominal CT, pyelography, cystoscopy were useful to show the origin of the bleeding. Read More

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A rare case of a cystic renal mass with heterotopic ossification and a mini literature review.

J Xray Sci Technol 2021 ;29(3):541-549

Wake Forest Institute for Regenerative Medicine, Wake Forest University School of Medicine, Winston-Salem, NC, USA.

Introduction: It is a challenge to make accurate pre-surgical diagnosis for renal tumors. This study is to report the findings, management, and outcome of one rare case of ossification in a cystic renal mass. We present and discuss the pathological characteristics, radiologic features, and treatment alternatives of the patient. Read More

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January 2021

An enigmatic case of IgG4-related nephropathy and an updated review of the literature.

Clin Exp Med 2021 Mar 8. Epub 2021 Mar 8.

Division of Nephrology, Dialysis and Renal Transplantation, ASST Grande Ospedale Metropolitano Niguarda, 20162, Milan, Italy.

IgG4-related disease (IgG4-RD) is still an underestimated disorder which affects multiple organs, and its recognition as a distinct clinical disease has been only proved in the recent decades. The renal involvement has been documented in approximately 15% of patients with IgG4-RD, and the typical manifestation is a tubulo-interstitial nephritis. The main histological findings in IgG4-RD are typically a dense tissue infiltration of IgG4-positive plasma cells, storiform fibrosis, obliterative phlebitis, and frequently elevated IgG4 serum levels. Read More

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Into Clinical Practice: Diagnosis and Therapy of Retroperitoneal Fibrosis.

Curr Rheumatol Rep 2021 Feb 10;23(3):18. Epub 2021 Feb 10.

Department of Biomedical, Experimental and Clinical Sciences "Mario Serio", University of Firenze, Florence, Italy.

Purpose Of The Review: We aim to review the most relevant diagnostic features and treatment options of retroperitoneal fibrosis, in order to provide a useful guide for clinical practice.

Recent Findings: The recent literature highlights the role of imaging studies such as computed tomography, magnetic resonance imaging and positron emission tomography as useful tools for the diagnosis of retroperitoneal fibrosis, with retroperitoneal biopsy being reserved to atypical cases. The treatment approach is mainly conservative and is based on the use of medical therapies plus urological interventions. Read More

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February 2021

Outcomes of ureterolysis for primary retroperitoneal fibrosis: A single-center experience.

Int J Urol 2021 05 21;28(5):520-525. Epub 2021 Jan 21.

Department of Urology, Hacettepe University School of Medicine, Ankara, Turkey.

Objective: To report our experience with ureterolysis for the management of retroperitoneal fibrosis.

Methods: The data of 25 patients who underwent ureterolysis due to primary retroperitoneal fibrosis between 2002 and 2017 were reviewed retrospectively. Initial symptoms, laterality, renal function status (initial/final), operation complications and serum creatinine levels (diagnosis/preoperative/6 months, 12 months postoperatively) were recorded. Read More

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Periureteral Marginal Zone Lymphoma Resulting in Hydronephrosis and Flank Pain in the Absence of Disseminated Disease: Case Report of Two Patients Presenting with Rare But Important Differential.

J Endourol Case Rep 2020 29;6(4):519-522. Epub 2020 Dec 29.

Department of Urology, University of Kansas, Kansas City, Kansas, USA.

Extrinsic compression of the ureter can result from multiple different malignancies, typically in the presence of known or disseminated disease. Rarely, hydroureteronephrosis and flank pain can occur as the presenting sign and symptom of lymphoma. In this study, we present two cases of primary ureteral obstruction in patients without a prior diagnosis of lymphoma and without bulky retroperitoneal lymphadenopathy. Read More

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December 2020

IgG4 related disease as a cause of isolated retroperitoneal fibrosis with no other organ involvement; Case report.

Ann Med Surg (Lond) 2021 Jan 23;61:69-72. Epub 2020 Dec 23.

Department of Internal Medicine, Hamad Medical Corporation, P.O 3050, Doha, Qatar.

Introduction And Importance: Retroperitoneal fibrosis (RPF) is a rare disease characterized by the replacement of normal tissue with fibrosis and inflammation. We present the case of a 40-years-old gentleman with RPF whose presenting complaints were bilateral flank pain and weight loss and was found to have IgG4 related disease. To the best of our knowledge, IgG4-related disease with isolated retroperitoneal involvement is a very rare occurrence. Read More

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January 2021

Validation of the diagnostic criteria for IgG4-related kidney disease (IgG4-RKD) 2011, and proposal of a new 2020 version.

Clin Exp Nephrol 2021 Feb 4;25(2):99-109. Epub 2021 Jan 4.

Division of Nephrology and Rheumatology, Department of Internal Medicine, Faculty of Medicine, Fukuoka University, 7-45-1 Nanakuma, Jonan-ku, Fukuoka, 814-0180, Japan.

Background: In 2011, the IgG4-related kidney disease (IgG4-RKD) working group of the Japanese Society of Nephrology proposed diagnostic criteria for IgG4-RKD. The aim of the present study was to validate those criteria and develop a revised version.

Methods: Between April 2012 and May 2019, we retrospectively collected Japanese patients with kidney disease, for whom data on serum IgG4 values and/or immunohistological staining for IgG4 in renal biopsy samples were available. Read More

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February 2021

Value of adjuvant chemotherapy and informed microscopic examination for occult gynecologic cancer detected upon risk-reducing salpingo-oophorectomy after chemotherapy for BRCA1/2-associated breast cancer: a case report.

Jpn J Clin Oncol 2021 Mar;51(3):492-497

Department of Obstetrics and Gynecology, St. Marianna University School of Medicine, Kawasaki-shi, Japan.

BRCA1/2 mutation carriers are at high risk for type II ovarian, fallopian tube or peritoneal cancer. Although risk-reducing salpingo-oophorectomy plays an important role in the prevention of these BRCA1/2-associated gynecological cancers, occult ovarian, fallopian tube, or peritoneal cancer is discovered upon risk-reducing salpingo-oophorectomy in 1-4% of BRCA1/2 mutation carriers. Notably, around 30% of BRCA1/2 mutation carriers who undergo risk-reducing salpingo-oophorectomy have undergone adjuvant chemotherapy for breast cancer. Read More

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[Clinical features of hydronephrosis induced by retroperitoneal fibrosis: 17 cases reports].

Beijing Da Xue Xue Bao Yi Xue Ban 2020 Dec;52(6):1069-1074

Department of Rheumatology and Immunology, Peking University People's Hospital, Beijing 100044, China.

Objective: To investigate the clinical features and outcome of hydronephrosis induced by retroperitoneal fibrosis (RPF), and to evaluate the effect of corticosteroid based therapy combined with surgical intervention of ureteral obstruction.

Methods: A total of 17 RPF patients with hydronephrosis hospitalized in Peking University International Hospital from May 2016 to December 2019 were analyzed retrospectively.

Results: The median age was 56 (53, 65) years, the male to female ratio was 2. Read More

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December 2020

Idiopathic Retroperitoneal Fibrosis With Intense Uptake of 68Ga-Fibroblast Activation Protein Inhibitor and 18F-FDG.

Clin Nucl Med 2021 Feb;46(2):175-176

Department of Rheumatology, Chinese Academy of Medical Sciences and Peking Union Medical College Hospital, Beijing, People's Republic of China.

Abstract: A 26-year-old man presented with a retroperitoneal mass with left urinary tract obstruction and hydronephrosis recently. 18F-FDG PET/CT showed the retroperitoneal mass had intense and homogeneous FDG avidity. In 68Ga-FAPI PET/CT, the retroperitoneal mass showed intense radioactivity without other organ involvements. Read More

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February 2021

Overview of IgG4-related aortitis and periaortitis. A decade since their first description.

Autoimmun Rev 2020 Dec 22;19(12):102694. Epub 2020 Oct 22.

First Department of Propaedeutic and Internal Medicine, "Laiko" Hospital, Athens, Greece; Institute of Infection, Immunity and Inflammation, University of Glasgow, Glasgow, United Kingdom. Electronic address:

Aortic involvement is relatively common in the context of IgG4-related disease (IgG4-RD). It includes IgG4-aortitis, and IgG4-(chronic) periaortitis (IgG4-CP). The latter overlaps with IgG4-retroperitoneal fibrosis (IgG4-RPF). Read More

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December 2020

Retroperitoneal fibrosis: A rare mimicker of a perirenal hematoma.

Radiol Case Rep 2020 Dec 6;15(12):2530-2534. Epub 2020 Oct 6.

Department of Radiology, AZ Delta campus Rumbeke, Deltalaan 1, 8800 Roeselare, Belgium.

Retroperitoneal fibrosis (RPF) is a relatively rare entity, characterized by chronic inflammation and fibrosis in the retroperitoneal periaortic tissues. Due to this rarity, the diagnosis might be delayed or challenging, especially with atypical presentations of RPF. We report the imaging findings of an incidental finding of active RPF in an asymptomatic 84-year-old male patient. Read More

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December 2020

[Diagnosis and treatment of radiation intestinal injury: current status and perspectives].

Y S Li

Zhonghua Wei Chang Wai Ke Za Zhi 2020 Aug;23(8):723-727

Department of General Surgery, Shanghai Ninth People's Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 200011, China.

Radiation intestinal injury (RII) refers to the intestinal complication resulting from radiation therapy of pelvic, abdominal or retroperitoneal tumor, which involves the small intestine, colon and rectum. Although the advances in radiotherapy technology have decreased the injury of adjacent tissues, 90% of the patients receiving radiotherapy have acute symptoms, the quality of life is affected due to gastrointestinal symptoms in 50% of patients, and 20%-40% of patients have moderate to severe symptoms. Based on the pathological stage, characteristics and clinical manifestations, RII can be divided into acute and chronic types, generally 3 to 6 months as the cutoff in clinical history. Read More

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Clinical features of IgG4-related retroperitoneal fibrosis among 407 patients with IgG4-related disease: a retrospective study.

Rheumatology (Oxford) 2021 02;60(2):767-772

Department of Rheumatology and Immunology, Peking University People's Hospital, Beijing, China.

Objectives: IgG4-related disease (IgG4-RD) is recently recognized as a fibro-inflammatory condition featured by tumefactive lesions in multiple organs, and the retroperitoneum is one of the common involved sites. We undertook this study to compare detailed demographic, clinical and laboratory characteristics of IgG4-RD patients with retroperitoneum lesion (IgG4-RD RPF+) and retroperitoneum free IgG4-RD (IgG4-RD RPF-) in a large cohort.

Methods: We carried out a retrospective review of the medical records of 407 cases of IgG4-RD diagnosed at Peking University People's Hospital between March 2009 and May 2019. Read More

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February 2021

Use of rituximab in idiopathic retroperitoneal fibrosis.

BMC Rheumatol 2020 6;4:40. Epub 2020 Aug 6.

Arthritis Research Canada, 5591 No. 3 Road, Richmond, BC V6X 2C7 Canada.

Background: Retroperitoneal fibrosis (RPF) is characterized by the proliferation of fibrous tissue in the retroperitoneum. The majority of RPF cases are due to idiopathic or IgG4-related disease. Recent studies on IgG4-related disease have shown rituximab to be an effective treatment. Read More

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Filariasis an Unusual Cause of Retroperitoneal Fibrosis, Hydronephrosis, and Infertility in a Young Adult Male.

J Endourol Case Rep 2019 30;5(3):113-116. Epub 2019 Aug 30.

Department of Urology, London North West University Healthcare NHS Trust, Ealing and Northwick Park Hospital, London, United Kingdom.

Filariasis is a tropical disease caused by infection with nematode parasites of the Filarioidea family. Filariasis is an endemic disease in parts of India, Sub-Saharan Africa, and Southeast Asia. Filariasis is a progressive disease predominantly affecting the lymphoreticular system, which can result in genitourinary complications (hydrocele, scrotal pain, and infertility), lymphedema, and elephantitis. Read More

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Metallic ureteral stent in restoring kidney function: Nine case reports.

World J Clin Cases 2020 Jul;8(13):2841-2848

Department of Urology, Xuanwu Hospital, Capital Medical University, Beijing 100053, China.

Background: Retroperitoneal fibrosis is an exceptionally rare disease characterized by proliferation of fibrous tissue and inflammation in the retroperitoneum. It features many symptoms in the kidneys and in other organs and usually leads to ureteral obstruction.

Case Summary: Here we present 9 consecutive cases of idiopathic retroperitoneal fibrosis (IRPF) in patients who presented to the Department of Nephrology or Department of Rheumatology, Xuanwu Hospital, Capital Medical University, Beijing, China, between January 2012 and June 2017 with ureteral obstruction due to external compression of the ureter that led to hydronephrosis and kidney dysfunction. Read More

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La fibrose rétropéritonéale idiopathique.

Rev Med Interne 2020 Dec 27;41(12):822-828. Epub 2020 Jul 27.

Department of Internal Medicine and Clinical Immunology, AP-HP, Groupe Hospitalier Pitié-Salpêtrière, 75013 Paris, France; Sorbonne Université, UPMC Université Paris 06, UMR 7211, Inflammation-Immunopathology-Biotherapy Department (DHU i2B), 75005 Paris, France.

Retroperitoneal fibrosis (RPF) is a rare disease characterized by the presence of fibro-inflammatory tissue around the aorta entrapping the adjacent structures. RPF can be idiopathic or secondary to many disorders. The physiopathology is unknown but can be part of the spectrum of IgG4 related diseases. Read More

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December 2020

Primary and secondary diseases of the perinephric space: an approach to imaging diagnosis with emphasis on MRI.

Clin Radiol 2021 01 22;76(1):75.e13-75.e26. Epub 2020 Jul 22.

Department of Medical Imaging, The Ottawa Hospital, 501 Smyth Road, Ottawa, ON, K1H 8L6, Canada.

The perinephric space is the middle compartment of the retroperitoneum, containing the kidneys and adrenal glands. Differential considerations for diseases involving primarily the perinephric space differ from those arising from the kidney itself, show variant imaging features, and require identification and characterisation by interpreting radiologists-an imaging diagnosis can be suggested in many cases. Lymphangiomas are congenital cystic lesions that may contain lipid-laden chyle, which may be detectable on magnetic resonance imaging (MRI). Read More

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January 2021

Retroperitoneal Fibrosis and its Differential Diagnoses: The Role of Radiological Imaging.

Rofo 2020 Oct 22;192(10):929-936. Epub 2020 Jul 22.

Department of Diagnostic and Interventional Radiology, Eberhard Karls University Tübingen, Tübingen, Germany.

Background:  Retroperitoneal fibrosis is a rare disease with an incidence of 0-1/100 000 inhabitants per year and is associated with chronic inflammatory fibrosis of the retroperitoneum and the abdominal aorta. This article sheds light on the role of radiological imaging in retroperitoneal fibrosis, names various differential diagnoses and provides an overview of drug and surgical treatment options.

Methods:  A literature search for the keywords "retroperitoneal fibrosis" and "Ormond's disease" was carried out in the PubMed database between January 1, 1995 and December 31, 2019 (n = 1806). Read More

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October 2020

Intimal angiosarcoma masquerading as retroperitoneal fibrosis.

Vasa 2021 Apr 13;50(3):240-243. Epub 2020 Jul 13.

Department of Internal Medicine, Albert Schweitzer Hospital, Dordrecht, The Netherlands.

We present a rare case of intimal angiosarcoma arising from the iliac artery with unusual symptoms and signs mimicking retroperitoneal fibrosis (RPF). This 84-year-old male presented with constitutional symptoms, abdominal pain, increased acute-phase reactant levels, impaired renal function and a CT-documented left-sided parailiac soft-tissue mass with unilateral extrinsic ureteric obstruction. Whole-body F-fluorodeoxyglucose positron emission tomography scan showed highly increased FDG-uptake in a horseshoe-like pattern surrounding the left common iliac artery, but no pathologic activity elsewhere. Read More

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Erdheim-Chester disease: a rapidly evolving disease model.

Leukemia 2020 11 26;34(11):2840-2857. Epub 2020 Jun 26.

Department of Biomedical, Experimental and Clinical Sciences "Mario Serio", University of Firenze, and Nephrology and Dialysis Unit, Meyer Children's Hospital, Firenze, Italy.

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis with a putative neoplastic and inflammatory nature. The disease is driven by mutations in proto-oncogenes such as BRAF and MEK, while immune-mediated mechanisms contribute to disease development and progression. The clinical presentation of ECD is highly heterogeneous, ranging from smouldering unifocal forms to multiorgan life-threatening disease. Read More

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November 2020

European Guideline on IgG4-related digestive disease - UEG and SGF evidence-based recommendations.

United European Gastroenterol J 2020 07 18;8(6):637-666. Epub 2020 Jun 18.

Département de Médicine Interne Timone, Assistance Publique-Hôpitaux de Marseille, Aix-Marseille Université, Marseille, France.

The overall objective of these guidelines is to provide evidence-based recommendations for the diagnosis and management of immunoglobulin G4 (IgG4)-related digestive disease in adults and children. IgG4-related digestive disease can be diagnosed only with a comprehensive work-up that includes histology, organ morphology at imaging, serology, search for other organ involvement, and response to glucocorticoid treatment. Indications for treatment are symptomatic patients with obstructive jaundice, abdominal pain, posterior pancreatic pain, and involvement of extra-pancreatic digestive organs, including IgG4-related cholangitis. Read More

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Retroperitoneal Sclerosing Lipogranuloma in an Adolescent With Congenital Atresia of the Inferior Vena Cava: Case Report and Literature Review.

J Pediatr Hematol Oncol 2021 05;43(4):e525-e528

Hematology/Oncology, John R. Oishei Children's Hospital.

Sclerosing lipogranuloma (SLG) in children is a rare, benign disease of unknown etiology suspected to be due to abnormal fatty tissue reaction. A 13-year-old girl presented with progressively worsening back pain. Cross-sectional imaging identified a retroperitoneal mass compressing the left ureter as well as infrarenal inferior vena cava atresia with extensive venous collaterals and chronic partially occlusive thromboses of the iliac veins. Read More

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Case report: IgG4-related renal disease co-existing with retroperitoneal fibrosis.

Transl Androl Urol 2020 Apr;9(2):794-799

Department of Internal Medicine, Chonnam National University Medical School, Gwangju, South Korea.

A 51-year-old woman visited our clinic for orthopnea, chest discomfort, and facial and leg edema. Acute kidney injury and pleural effusion were diagnosed and she received hemodialysis. This is a rare case of IgG4-related disease diagnosed by renal biopsy in the patient with retroperitoneal fibrosis and severe acute kidney injury, which progressed rapidly and required hemodialysis without markedly elevated serum IgG4 level and urinary tract obstruction. Read More

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