3,265 results match your criteria Retroperitoneal Fibrosis


Yellow Periorbital Plaque and Retroperitoneal Fibrosis.

JAMA Dermatol 2019 Feb 20. Epub 2019 Feb 20.

Department of Pathology, Microbiology and Immunology, Vanderbilt University Medical Center, Nashville, Tennessee.

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http://dx.doi.org/10.1001/jamadermatol.2018.5233DOI Listing
February 2019

Immunoglobulin G4 Inflammatory Aortic Aneurysm Mimicking Acute Aortic Syndrome.

Ann Thorac Surg 2019 Feb 13. Epub 2019 Feb 13.

Department of Orthopedics and Trauma - Surgery, Division of Trauma - Surgery, General Hospital of Vienna, Austria.

Immunoglobulin-G4-related disease (IgG4RD) is a novel clinical entity characterized by lymphoplasmacytic infiltrates presenting as an excessive fibrosis such as retroperitoneal inflammatory pseudotumor but rarely affecting the heart or the aorta. We describe a case of IgG4RD with multifocal aortic involvement presenting as an acute aortic syndrome. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2019.01.029DOI Listing
February 2019
1 Read

Endovascular treatment of duplicated inferior vena cava compression from retroperitoneal fibrosis.

J Vasc Surg Cases Innov Tech 2018 Dec 10;4(4):311-314. Epub 2018 Dec 10.

Section of Vascular Surgery, Department of Surgery, Yale University School of Medicine, New Haven, Conn.

A 68-year-old man with a history of retroperitoneal fibrosis was referred to our clinic because of disabling bilateral lower extremity swelling and venous claudication, worse on the right side than on the left. He was noted to have a duplicated inferior vena cava and an iliac vein obliteration from retroperitoneal fibrosis. The patient underwent bilateral iliac vein stenting and had complete relief of symptoms through follow-up of 46 months with no recurrence. Read More

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http://dx.doi.org/10.1016/j.jvscit.2018.07.002DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6298941PMC
December 2018
1 Read

Chylous Ascites due to Mantle Cell Lymphoma.

Eur J Case Rep Intern Med 2018 26;5(6):000871. Epub 2018 Jun 26.

Internal Medicine Department, Centro Hospitalar de Vila Nova de Gaia-Espinho, Portugal.

Chylous ascites is rare and results in accumulation of lymph in the abdominal cavity, due to several mechanisms. The ascitic liquid is milky because of the high concentration of triglycerides (>200 mg/dl). The higher incidence compared to the past is explained by increased survival of patients with cancer and more aggressive surgery. Read More

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http://dx.doi.org/10.12890/2018_000871DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6346885PMC
June 2018
1 Read

Retroperitoneal fibrosis in the era of immunoglobulin G4-related disease.

Kidney Res Clin Pract 2019 Feb 12. Epub 2019 Feb 12.

Department of Internal Medicine, Korea University Anam Hospital, Seoul, Korea.

Background: Retroperitoneal fibrosis (RPF) is a rare disease characterized by fibroinflammatory tissue in the periaortic or periiliac retroperitoneum, where it frequently encases ureters. There is emerging evidence that a subset of this disease is part of a spectrum of multisystemic autoimmune diseases collectively referred to as "immunoglobulin G4 (IgG4)-related disease".

Methods: We retrospectively analyzed 27 idiopathic RPF patients and identified a subset as IgG4-related RPF, which we categorized according to recently published comprehensive diagnostic criteria. Read More

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http://www.krcp-ksn.org/journal/view.html?doi=10.23876/j.krc
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http://dx.doi.org/10.23876/j.krcp.18.0052DOI Listing
February 2019
2 Reads

Urine retention in cattle putatively associated with injection of an ivermectin and closantel anthelmintic formulation into the ischiorectal fossa.

N Z Vet J 2019 Feb 11:1-19. Epub 2019 Feb 11.

a School of Veterinary Science , Massey University , Private Bag 11 222, Palmerston North , 4442 , New Zealand.

Case History: A group of 39, 19- to 22-month-old Friesian bulls were administered an ivermectin/closantel anthelmintic via intended S/C injection in the ischiorectal fossa on 15 June 2017 (Day 0). Over the next 50 days, 22 affected bulls presented various degrees of anorexia, abdominal pain and urine dribbling. Seventeen bulls were examined by transrectal ultrasonography which revealed urinary bladder distension in all 17, and peritoneal fluid accumulation in some. Read More

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http://dx.doi.org/10.1080/00480169.2019.1581112DOI Listing
February 2019
1 Read

Pediatric idiopathic retroperitoneal fibrosis.

Radiol Case Rep 2019 Apr 31;14(4):459-462. Epub 2019 Jan 31.

University of Iowa Hospitals and Clinics, Department of Radiology, 3889 JPP, 200 Hawkins Drive, Iowa City, IA 52242, US.

Retroperitoneal fibrosis (RPF) is a very rare disease that is even more rare in the pediatric population. Even less common are idiopathic pediatric cases of retroperitoneal fibrosis, with a majority of reported pediatric retroperitoneal fibrosis cases being associated with secondary etiologies. We present an 11-year-old Caucasian female that was diagnosed with idiopathic retroperitoneal fibrosis using magnetic resonance imaging (MRI) to work-up severe bilateral hydronephrosis that was identified with retroperitoneal ultrasound. Read More

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http://dx.doi.org/10.1016/j.radcr.2019.01.006DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6357545PMC
April 2019
1 Read

Endovascular Repair of Inflammatory Aortic Aneurysms: Experience in a Single Center.

Ann Vasc Surg 2019 Feb 5. Epub 2019 Feb 5.

Vascular and Thoracic surgeon, Department of General, Vascular and Thoracic Surgery, Centre Hospitaliere Regional du Val de Sambre, Sambreville, Belgium.

Objective: Inflammatory aortic abdominal aneurysm (IAAA) remained a rare cause of aneurysmal aortic disease with incidences between 5-10%. The current treatment of IAAA consists of open surgical repair (OSR) and endovascular aneurysm repair (EVAR). Avoiding an inflamed, fibrotic retroperitoneum is the driving force behind the desire to repair IAAA endovascularly. Read More

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http://dx.doi.org/10.1016/j.avsg.2018.10.046DOI Listing
February 2019
5 Reads

Consideration concerning similarities and differences between ANCA-associated vasculitis and IgG-4-related diseases: case series and review of literature.

Immunol Res 2019 Feb 8. Epub 2019 Feb 8.

Department of Rheumatology and Allergy, Japanese Red Cross Society Narita Hospital, 90-1, Iida-cho, Narita-shi, Chiba, 286-8523, Japan.

Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) and immunoglobulin G4-related diseases (IgG4-RD) are regarded as entirely different disease types with different etiological mechanisms. However, we experienced two cases that had clinical features of both AAV and IgG4-RD. The first case is an 81-year-old woman who showed periaortitis and retroperitoneal fibrosis and periarteritis with elevation of myeloperoxidase-anti-neutrophil cytoplasmic antibody and IgG4 levels. Read More

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http://dx.doi.org/10.1007/s12026-019-9070-7DOI Listing
February 2019
1 Read
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Persistent FDG/PET CT uptake in idiopathic retroperitoneal fibrosis helps identifying patients at a higher risk for relapse.

Eur J Intern Med 2019 Jan 31. Epub 2019 Jan 31.

Département de Médecine Interne, Hôpital Bichat, PRES Sorbonne Paris Cité, Assistance Publique Hôpitaux de Paris, Université Paris Diderot, Paris, France; Département Hospitalo-Universitaire FIRE (Fibrosis, Inflammation and Remodelling in Renal and Respiratory Diseases), Paris, France; INSERM U1149, Paris, France. Electronic address:

Background: The aim of this study was to evaluate the prognostic value of persistent retroperitoneal fibrosis FDG uptake using FDG/PET CT in patients with idiopathic retroperitoneal fibrosis (IRF).

Methods: In this monocentric retrospective cohort study, all patients admitted for IRF from January 2009 to December 2017 underwent a FDG/PET CT at diagnosis and during follow up. Metabolic activity of IRF was assessed by retroperitoneal fibrosis FDG uptake measured as maximal standardized uptake value (SUVmax). Read More

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http://dx.doi.org/10.1016/j.ejim.2019.01.019DOI Listing
January 2019
1 Read

IgG4-related disease: what a hematologist needs to know.

Haematologica 2019 Jan 31. Epub 2019 Jan 31.

Division of Rheumatology, Department of Medicine, University of British Columbia, Vancouver, Canada.

IgG4-related disease is a fibroinflammatory condition that can affect nearly any organ system. Common presentations include major salivary and lacrimal gland enlargement, orbital disease, autoimmune pancreatitis, retroperitoneal fibrosis and tubulointerstitial nephritis. This review focuses on the hematological manifestations of IgG4-related disease, including lymphadenopathy, eosinophilia, and polyclonal hypergammaglobulinemia. Read More

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http://dx.doi.org/10.3324/haematol.2018.205526DOI Listing
January 2019
2 Reads

Disease associated with immunoglobulin g.

Authors:
A G Chuchalin

Ter Arkh 2018 Apr;90(3):4-9

Scientific research Institute pulmonology Federal medical and biological Agency, Moscow, Russia.

Diseases associated with disorders of immunoglobulin g synthesis and its subclasses are described. The analysis of the role of both deficiency and its increased production in the diagnosis and treatment of a number of diseases in humans. Read More

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http://dx.doi.org/10.26442/terarkh20189034-9DOI Listing
April 2018
1 Read

Relapse patterns and predictors of IgG4-related diseases involved with autoimmune pancreatitis: A single-center retrospective study of 115 patients.

J Dig Dis 2019 Jan 31. Epub 2019 Jan 31.

Department of Medicine and Bioregulatory Science, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Objective: Autoimmune pancreatitis (AIP) was autoimmune disorder accompanied by clinicopathological manifestation whose concept was established as IgG4-related disease (IgG4-RD). Other IgG4-RDs are often involved with autoimmune pancreatitis, sometimes relapsing despite the favorable response to a steroid therapy. This study aimed to clarify patterns and risk factors for extrapancreatic relapse. Read More

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http://dx.doi.org/10.1111/1751-2980.12708DOI Listing
January 2019
2 Reads

Early administration of systemic chemotherapy should be considered for scirrhous gastric cancer: A case report.

Mol Clin Oncol 2019 Jan 16;10(1):113-117. Epub 2018 Nov 16.

Keio Cancer Center, Keio University School of Medicine, Tokyo 160-8582, Japan.

Scirrhous gastric cancer tends to disseminate to the peritoneum and retroperitoneum, where it induces fibrosis. Retroperitoneal fibrosis (RPF) frequently causes acute renal failure due to ureteral obstruction and it tends to make many of physicians hesitate to initiate systemic chemotherapy. The present study reported the case of a 68-year-old man who was diagnosed with scirrhous gastric cancer with peritoneal and retroperitoneal dissemination, causing acute renal failure due to RPF. Read More

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http://dx.doi.org/10.3892/mco.2018.1767DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6313955PMC
January 2019
1 Read

Applying Radiomics to Predict Pathology of Postchemotherapy Retroperitoneal Nodal Masses in Germ Cell Tumors.

JCO Clin Cancer Inform 2018 12;2:1-12

Jeremy Lewin, Padraig Warde, Peter Chung, Lynn Anson Cartwright, Joan Sweet, Aaron R. Hansen, and Philippe L. Bedard, Princess Margaret Cancer Centre; Michael A.S. Jewett, Robert J. Hamilton, Madhur Nayan, Ricardo Leão, Aaron R. Hansen, and Philippe L. Bedard, University of Toronto; Paul Dufort, Jaydeep Halankar, Martin O'Malley, and Ur Metser, University Health Network; and Abha Gupta, Armando Lorenzo, and Jeffrey Traubici, Hospital for Sick Children, Toronto, Ontario, Canada.

Purpose: After chemotherapy, approximately 50% of patients with metastatic testicular germ cell tumors (GCTs) who undergo retroperitoneal lymph node dissections (RPNLDs) for residual masses have fibrosis. Radiomics uses image processing techniques to extract quantitative textures/features from regions of interest (ROIs) to train a classifier that predicts outcomes. We hypothesized that radiomics would identify patients with a high likelihood of fibrosis who may avoid RPLND. Read More

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http://dx.doi.org/10.1200/CCI.18.00004DOI Listing
December 2018
1 Read

Multifocal gastrointestinal varices: a rare manifestation of immunoglobulin G4-related disease.

Postgrad Med 2019 Jan 11:1-6. Epub 2019 Jan 11.

a Department of Internal Medicine, National Cheng Kung University Hospital, College of Medicine , National Cheng Kung University , Tainan , Taiwan.

Multifocal gastrointestinal varices are uncommon and often associated with liver cirrhosis. They consist of varices at the gastroesophageal region and the other sites (i.e. Read More

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https://www.tandfonline.com/doi/full/10.1080/00325481.2019.1
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http://dx.doi.org/10.1080/00325481.2019.1568018DOI Listing
January 2019
6 Reads

Clinical phenotypes of IgG4-related disease: an analysis of two international cross-sectional cohorts.

Ann Rheum Dis 2019 Mar 5;78(3):406-412. Epub 2019 Jan 5.

Rheumatology Unit, Division of Rheumatology, Allergy, and Immunology, Massachusetts General Hospital, Boston, Massachusetts, USA.

Objective: IgG4-related disease (IgG4-RD) is a heterogeneous, multiorgan condition of unclear aetiology that can cause organ failure. Difficulty recognising IgG4-RD contributes to diagnostic delays. We sought to identify key IgG4-RD phenotypes. Read More

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http://dx.doi.org/10.1136/annrheumdis-2018-214603DOI Listing
March 2019
3 Reads

Clinical Manifestations and Long-term Outcomes of IgG4-Related Kidney and Retroperitoneal Involvement in a United Kingdom IgG4-Related Disease Cohort.

Kidney Int Rep 2019 Jan 1;4(1):48-58. Epub 2018 Sep 1.

Translational Gastroenterology Unit, John Radcliffe Hospital, and Nuffield Department of Medicine, University of Oxford, Oxford, UK.

Introduction: IgG4-related disease (IgG4-RD) is a relapsing multisystem fibro-inflammatory disease, which may involve the kidney (IgG4-related kidney disease [IgG4-RKD]) and retroperitoneum (IgG4-related retroperitoneal fibrosis [IgG4-RPF]). The aim of this study was to describe IgG4-RKD and IgG4-RPF in the United Kingdom.

Methods: We conducted a retrospective observational study of patients with IgG4-RKD and IgG4-RPF in a multicenter IgG4-RD cohort. Read More

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http://dx.doi.org/10.1016/j.ekir.2018.08.011DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6308386PMC
January 2019
8 Reads

Retroperitoneal fibrosis. Steroid treatment response seems to depend on its association to IgG4 related disease.

Med Hypotheses 2019 Jan 15;122:120-123. Epub 2018 Nov 15.

Research Division-School of Medicine Universidad Nacional Autónoma de Méxcio, Department of Gastroenterology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico. Electronic address:

Retroperitoneal fibrosis (RF) is part of a rare fibrosclerotic disorder. Oral steroids are the initial treatment. Steroid combination with other immunosupressants is used in refractory cases. Read More

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http://dx.doi.org/10.1016/j.mehy.2018.11.005DOI Listing
January 2019
8 Reads

[Retroperitoneal fibrosis in adults: Diagnostic approach based on a retrospective multicenter study on 32 cases].

Prog Urol 2018 Dec 19. Epub 2018 Dec 19.

Service de médecine interne, hôpital Sahloul, Sousse, Tunisie.

Introduction: Retroperitoneal fibrosis is a rare disease, typically with an insidious and various clinical course. The peak incidence is seen in patients 40 to 60 years of age and mostly in man. The characteristic finding in this disease is a periaortic fibrous mass that often surrounds the ureters. Read More

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http://dx.doi.org/10.1016/j.purol.2018.10.006DOI Listing
December 2018
7 Reads

Sex disparities in clinical characteristics and prognosis of immunoglobulin G4-related disease: a prospective study of 403 patients.

Rheumatology (Oxford) 2018 Dec 17. Epub 2018 Dec 17.

Department of Rheumatology, Peking Union Medical College Hospital, Chinese Academy of Medical Science & Peking Union Medical College, Beijing.

Objectives: To study the impact of sex on the clinical presentation of IgG4-related disease (IgG4-RD).

Methods: We prospectively enrolled 403 newly diagnosed IgG4-RD patients. We compared the demographic features, clinical manifestations, organ involvement, laboratory tests and treatment outcomes between female and male patients. Read More

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http://dx.doi.org/10.1093/rheumatology/key397DOI Listing
December 2018
3 Reads

Inferior vena cava syndrome caused by retroperitoneal fibrosis after pelvic irradiation: A case report.

Gynecol Oncol Rep 2019 Feb 4;27:19-21. Epub 2018 Dec 4.

Department of Radiation Oncology, National Cancer Center Hospital, 5-1-1 Tsukiji, Chuo-ku, Tokyo 104-0045, Japan.

In this case report, we share our experience of a case with inferior vena cava (IVC) syndrome caused by secondary retroperitoneal fibrosis related to prior pelvic irradiation. A 60 year-old-female who has history of pelvic irradiation developed severe leg edema. Radiological examination revealed obstruction of IVC. Read More

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http://dx.doi.org/10.1016/j.gore.2018.12.002DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6289939PMC
February 2019
2 Reads

Association of serum levels of fibrosis-related biomarkers with disease activity in patients with IgG4-related disease.

Arthritis Res Ther 2018 Dec 14;20(1):277. Epub 2018 Dec 14.

Immunology and Rheumatology, Nagasaki University Graduate School of Biomedical Sciences, Nagasaki, Japan.

Background: The aim of this study was to identify fibrosis-related serological surrogate outcome measures in patients with immunoglobulin G4-related disease (IgG4-RD).

Methods: This was a clinical observational study of 72 patients with untreated IgG4-RD from four institutions in Japan. The serum concentrations of growth differentiation factor 15 (GDF-15), CCL2, hyaluronic acid (HA), amino-terminal propeptide of type III procollagen (PIIINP), and tissue inhibitor of metalloproteinases 1 (TIMP-1) were measured by enzyme-linked immunosorbent assays. Read More

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http://dx.doi.org/10.1186/s13075-018-1777-7DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6293522PMC
December 2018
1 Read

IgG4-Related Disease, the Malignancy Mimicker: Case Series from Bahrain.

Case Rep Rheumatol 2018 28;2018:4057024. Epub 2018 Oct 28.

Consultant Diagnostic Radiologist, Radiology Unit, Salmaniya Medical Hospital, Manama, Bahrain.

IgG4-related disease is an evolving immune-mediated condition. The hallmark of this condition is IgG4(+) plasma cells infiltration of the affected organs accompanied by a variable degree of fibrosis and occasionally elevated serum IgG4 level. It links many conditions that were once recognized as isolated unrelated idiopathic single organ disorders (e. Read More

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https://www.hindawi.com/journals/crirh/2018/4057024/
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http://dx.doi.org/10.1155/2018/4057024DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6230411PMC
October 2018
9 Reads

IgG4-related kidney disease and retroperitoneal fibrosis: An update.

Mod Rheumatol 2018 Nov 30:1-24. Epub 2018 Nov 30.

c Division of Nephrology and Rheumatology, Department of Internal Medicine, Faculty of Medicine , Fukuoka University , Fukuoka , Japan.

The most representative kidney lesion of IgG4-related disease (IgG4-RD) is plasma cell-rich tubulointerstitial nephritis (TIN) with distinctive imaging findings including multiple low-density lesions on contrast-enhanced computed tomography. In addition, membranous glomerulonephritis is a representative glomerular lesion of this disease. Recent advances have clarified that inflammation with IgG4-positive plasma cell infiltrates is not restricted to the renal parenchyma, but can be seen in outside the renal capsule, around medium-sized arteries such as lobar arteries, around nerves, and in the renal pelvis and periureter. Read More

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http://dx.doi.org/10.1080/14397595.2018.1554321DOI Listing
November 2018
13 Reads

Retroperitoneal Liposarcoma Masquerading as an Impending Rupture of Inflammatory Abdominal Aortic Aneurysm.

Ann Vasc Surg 2018 Nov 26. Epub 2018 Nov 26.

5th Department of Surgery, Medical School, Aristotle University of Thessaloniki, Hippocratio Hospital, Thessaloniki, Greece.

Background: We present a unique case scenario of a periaortic liposarcoma masquerading as an impending rupture of an inflammatory abdominal aortic aneurysm (AAA).

Methods And Results: A 57-year-old man was referred to our unit for an emergency endovascular repair of "an inflammatory AAA with computed tomography (CT) features of impending rupture." He underwent an uneventful endovascular repair with a bifurcated endograft (C3; Gore, Flagstaff, AZ). Read More

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http://dx.doi.org/10.1016/j.avsg.2018.08.103DOI Listing
November 2018
16 Reads

Comparison of two subsets of Chinese patients with retroperitoneal fibrosis in terms of IgG4 immunohistochemical staining.

Rheumatology (Oxford) 2018 Nov 21. Epub 2018 Nov 21.

Department of Rheumatology, Chinese PLA General Hospital, Chinese PLA Institute of Nephrology, State Key Laboratory of Kidney Diseases, National Clinical Research Center for Kidney Diseases, Beijing, China.

Objective: To identify clinical and pathological differences between IgG4-related retroperitoneal fibrosis (IgG4-RPF) and idiopathic RPF (iRPF) in a Chinese population.

Method: Clinical and pathological data of 50 RPF patients from 2006 to 2016 were retrospectively analysed. The presence of at least one characteristic histopathological feature, >30 IgG4+ plasma cells per high power field, and an IgG4+/IgG+ plasma cells ratio cutoff of >40% were used to define IgG4-RPF. Read More

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https://academic.oup.com/rheumatology/advance-article/doi/10
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http://dx.doi.org/10.1093/rheumatology/key324DOI Listing
November 2018
12 Reads

Xanthogranulomatous pyelonephritis in adults: clinical, biological, radiological and therapeutic main findings in diffuse and focal forms. About 42 cases.

Tunis Med 2018 Aug - Sep;96(8-09):495-500

Introduction: Xanthogranulomatous pyelonephritis (XGPN) is a particular form of chronic renal suppuration characterized by the destruction of renal parenchyma and its replacement by a granulomatous tissue containing xanthomatous cells.

Objective: To report and describe the main clinical, biological, radiological and therapeutic aspects of xanthogranulomatous pyelonephritis in adults in focal and diffuse forms.

Methods: This was a monocentric retrospective study involving 42 cases of XGPN operated and histologically confirmed between 2005 and 2015. Read More

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November 2018
20 Reads

[Erdheim-Chester disease : An important differential diagnosis and its main symptoms].

Z Rheumatol 2019 Feb;78(1):66-71

Medizinische Klinik 3 - Rheumatologie und Immunologie, Universitätsklinikum Erlangen, Friedrich-Alexander-Universität Erlangen-Nürnberg (FAU), Ulmenweg 18, 91054, Erlangen, Deutschland.

Background: During the last 3 years 4 patients were admitted to this hospital with a wide variety of different symptoms, in whom Erdheim-Chester disease (ECD) was diagnosed via different diagnostic pathways.

Objective: Based on four clinical cases of ECD and using additional information from the literature, this article presents the symptoms of ECD. Furthermore, similarities and differences in comparison to important rheumatological differential diagnoses are presented. Read More

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http://dx.doi.org/10.1007/s00393-018-0566-7DOI Listing
February 2019
1 Read

RUG technique: replacement of the ureter with gonadal vein. A cadaveric study.

Minerva Urol Nefrol 2019 Feb 7;71(1):85-91. Epub 2018 Nov 7.

Department of Neurosciences, Institute of Anatomy, University of Padua, Padua, Italy.

Background: Ureteral defect lesions may result from retroperitoneal fibrosis, radiation damage, tumors, or surgical procedures; the management of long-segment ureteral defects is a challenge for urologists. Total or partial replacement of the ureter is sometimes required, with consequent ileal interposition, but this technique may lead to several complications, such as severe urinary infections. In a few cases, nephrectomy may be required. Read More

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https://www.minervamedica.it/index2.php?show=R19Y9999N00A181
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http://dx.doi.org/10.23736/S0393-2249.18.03261-7DOI Listing
February 2019
22 Reads

Serum and histological IgG4-negative type 1 autoimmune pancreatitis.

Clin J Gastroenterol 2018 Nov 10. Epub 2018 Nov 10.

Division of Gastroenterology, Department of Internal Medicine, Showa University Fujigaoka Hospital, 1-30 Fujigaoka, Aoba-ku, Yokohama-shi, Kanagawa, 227-8501, Japan.

A 66-year-old man who was on oral medication for type 2 diabetes experienced a rapid decline in glycemic control (increase in glycosylated hemoglobin level from 7.7 to 10.2% over 3 months). Read More

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http://link.springer.com/10.1007/s12328-018-0919-4
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http://dx.doi.org/10.1007/s12328-018-0919-4DOI Listing
November 2018
18 Reads

Molecular Imaging for Evaluation of Viable Testicular Cancer Nodal Metastases.

Curr Urol Rep 2018 Nov 9;19(12):110. Epub 2018 Nov 9.

The James Buchanan Brady Urological Institute and Department of Urology, Johns Hopkins University School of Medicine, 600 North Wolfe Street, Marburg 144, Baltimore, MD, 21287, USA.

Purpose Of Review: Determining the metastatic viability of suspicious retroperitoneal nodes in testicular cancer with conventional imaging is challenging. The aim of this report is to review recent evidence in the utilization of novel imaging modalities to assess viable testicular cancer nodal metastases.

Recent Evidence: Testicular germ cell tumors (TCGTs) follow a predictable lymphatic metastatic spread to the retroperitoneum. Read More

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http://link.springer.com/10.1007/s11934-018-0863-3
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http://dx.doi.org/10.1007/s11934-018-0863-3DOI Listing
November 2018
13 Reads

Chronic Periaortitis: an Update.

Curr Rheumatol Rep 2018 Nov 5;20(12):80. Epub 2018 Nov 5.

Nephrology Unit, Parma University Hospital, Parma, Italy.

Purpose Of Review: We aim to review traditional concepts and recent developments on the nosology, pathophysiology, clinical phenotypes and treatment of chronic periaortitis (CP).

Recent Findings: CP is a rare disorder hallmarked by a periaortic fibro-inflammatory tissue. It can present as an isolated disease, but it can also be associated with other autoimmune and fibro-inflammatory lesions (e. Read More

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http://link.springer.com/10.1007/s11926-018-0789-2
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http://dx.doi.org/10.1007/s11926-018-0789-2DOI Listing
November 2018
8 Reads

Rituximab for idiopathic and IgG4-related retroperitoneal fibrosis.

Medicine (Baltimore) 2018 Oct;97(42):e12631

Department of Medicine.

Retroperitoneal fibrosis (RPF) refers to a fibro-inflammatory lesion in the retroperitoneum, often anterolateral to the aorta. Most cases are due to IgG4-related disease (IgG4-RD) or are idiopathic. RPF can lead to severe morbidity. Read More

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http://dx.doi.org/10.1097/MD.0000000000012631DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6211888PMC
October 2018
28 Reads

Clinical Questions and an Inquiring Mind for Patients with IgG4-related Disease.

Intern Med 2019 Feb 17;58(4):469-470. Epub 2018 Oct 17.

Department of Rheumatology and Clinical Immunology, Sapporo Medical University School of Medicine, Japan.

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http://dx.doi.org/10.2169/internalmedicine.1765-18DOI Listing
February 2019
2 Reads

Retroperitoneal Fibrosis Diagnosed as IgG4-related Disease after 35 Years.

Intern Med 2019 Feb 17;58(4):609-613. Epub 2018 Oct 17.

Director Emeritus KKR Sapporo Medical Center, Japan.

In 1982, we reported a case of retroperitoneal fibrosis (RPF) exhibiting various clinical manifestations. Our current understanding of immunoglobulin G4 (IgG4)-related disease led us to consider it as a possible diagnosis because all of the patient's clinical features could be explained by this disease entity. To confirm our hypothesis, were investigated the histopathological findings of resected specimens that had been stored for 35 years postoperatively. Read More

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http://dx.doi.org/10.2169/internalmedicine.1241-18DOI Listing
February 2019
2 Reads

Association of a polymorphism of the Fcγ-receptor 2A (FCGR2A) gene with chronic periaortitis.

Clin Exp Rheumatol 2018 09 17. Epub 2018 Sep 17.

Unit of Medical Genetics, University Hospital of Parma, Italy.

Objectives: Chronic periaortitis (CP) is an inflammatory disease associated in 20-60% of the cases with IgG4 related disease. Current evidence supports an autoimmune nature for CP. Fc gamma receptors (FcγRs) are involved in several immune system activities and are associated with autoimmunity in general. Read More

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September 2018
12 Reads

Aphthous Stomatitis and Laryngitis, Another Form of Presentation of an IgG4-Related Disease?

Reumatol Clin 2018 Oct 5. Epub 2018 Oct 5.

Servicio de Medicina Interna, Unidad de Enfermedades Autoinmunes Sistémicas (UEAS), Hospital Universitario Central de Asturias, Oviedo, Asturias, España.

IgG4-related disease is characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis and obliterative phlebitis. It can present as parotid gland enlargement, tubulointerstitial nephritis, retroperitoneal fibrosis or pancreatitis, although nearly any organ can be affected. We report the case of a 37-year-old woman who presented with severe dysphonia and recurrent painful aphthous ulcers, with histopathological findings at the level of the larynx that revealed a lymphoplasmacytic infiltrate and IgG4 positivity. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S1699258X183019
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http://dx.doi.org/10.1016/j.reuma.2018.08.011DOI Listing
October 2018
8 Reads

Surgical Management of Patients with Advanced Germ Cell Tumors Following Salvage Chemotherapy: Memorial Sloan Kettering Cancer Center (MSKCC) Experience.

Urology 2019 Feb 6;124:174-178. Epub 2018 Oct 6.

Urology Service, Department of Surgery, Sidney Kimmel Center for Prostate and Urological Cancers, Memorial Sloan Kettering Cancer Center, New York, NY.

Objective: To characterize clinical and pathologic outcomes of cisplatin-refractory or relapsed germ cell tumor (GCT) patients who underwent retroperitoneal lymph node dissection (RPLND) following salvage chemotherapy with either conventional or high dose regimens.

Methods: Data were reviewed to identify all patients treated with TIP or TICE salvage chemotherapy between 1994 and 2011(n = 184) at our institution. We report clinicopathologic and outcomes data on 131 patients who were further managed with surgical resection. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S00904295183106
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http://dx.doi.org/10.1016/j.urology.2018.09.024DOI Listing
February 2019
19 Reads

Long-term outcomes and predictors of a large cohort of idiopathic retroperitoneal fibrosis patients: a retrospective study.

Authors:
J Zhao J Li Z Zhang

Scand J Rheumatol 2018 Sep 30:1-7. Epub 2018 Sep 30.

a Department of Rheumatology and Clinical Immunology , Peking University First Hospital , Beijing , China.

Objectives: Idiopathic retroperitoneal fibrosis (iRPF) is an uncommon disease with inflammatory features. Most patients have good prognosis but some may relapse or even progress to chronic renal failure. The aims of the study were to investigate the prognosis of a large cohort of iRPF patients and explore the risk factors for poor outcomes. Read More

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http://dx.doi.org/10.1080/03009742.2018.1497700DOI Listing
September 2018
9 Reads

Pancreatitis.

Surg Clin North Am 2018 Oct 17;98(5):895-913. Epub 2018 Jul 17.

Department of Surgery, Allegheny General Hospital, 320 East North Avenue, Pittsburgh, PA 15212, USA. Electronic address:

Acute pancreatitis is an inflammation of the glandular parenchyma of the retroperitoneal organ that leads to injury with or without subsequent destruction of the pancreatic acini. This inflammatory process can either result in a self-limited disease or involve life-threatening multiorgan complications. Chronic pancreatitis consists of endocrine and exocrine gland dysfunction that develops secondary to progressive inflammation and chronic fibrosis of the pancreatic acini with permanent structural damage. Read More

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http://dx.doi.org/10.1016/j.suc.2018.06.001DOI Listing
October 2018
3 Reads

Idiopathic retroperitoneal fibrosis presenting as spastic paraparesis.

Neurol India 2018 Sep-Oct;66(5):1481-1482

Department of Radiodiagnosis, Global Hospitals, Hyderabad, Telangana, India.

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http://dx.doi.org/10.4103/0028-3886.241348DOI Listing
September 2018
3 Reads

Immunoglobulin G4 Sclerosing Cholangitis: An Unusual Cause of Obstructive Jaundice-Case Report and Literature Review.

Case Rep Rheumatol 2018 23;2018:9602373. Epub 2018 Aug 23.

Department of Medicine, Reading Hospital-Tower Health System, West Reading, PA 19611, USA.

IgG4-related sclerosing cholangitis (IgG4-SC) is one of the most common extra-pancreatic manifestation of IgG4-related disease (IgG4-RD) and is clinically distinct from primary sclerosing cholangitis (PSC). IgG4-RD is an increasingly recognized immune-mediated fibroinflammatory systemic disease, mostly affecting middle-aged and older male populations that can affect multiple organs. The presence of extra-biliary clinical manifestations of IgG4-RD, such as parotid and lacrimal swelling, lymphadenopathy, autoimmune pancreatitis, and retroperitoneal fibrosis, if present could provide important clues to diagnosis. Read More

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http://dx.doi.org/10.1155/2018/9602373DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6126084PMC
August 2018
3 Reads

Retroperitoneal fibrosis secondary to non-urology carcinomas: a clinical and outcome analysis of 97 cases.

Clin Transl Oncol 2019 Mar 4;21(3):373-379. Epub 2018 Sep 4.

Department of Urology, Shandong Provincial Hospital Affiliated to Shandong University, Jinan, 250021, Shandong, People's Republic of China.

Purpose: Accumulated evidences have reminded us that since the prognosis of retroperitoneal fibrosis (RPF) secondary to non-urology carcinoma is poor it is essential to distinguish this condition from others. The objective of this study is to investigate the clinical features and outcomes of this infrequent but life-threatening disease.

Methods: A total of 97 patients diagnosed with RPF secondary to non-urology carcinoma were enrolled in this retrospective study. Read More

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http://dx.doi.org/10.1007/s12094-018-1936-yDOI Listing
March 2019
2 Reads

Autoimmune pancreatitis associated with retroperitoneal fibrosis mimicking cholangiocarcinoma.

Oxf Med Case Reports 2018 Sep 25;2018(9):omy056. Epub 2018 Aug 25.

Surgical Anatomy, Faculty of Medicine, National and Kapodistrian University of Athens, Athens, Greece.

Autoimmune pancreatitis (AIP) is a rare systematic autoimmune disease that causes chronic pancreatitis. Type 1-AIP (IgG4-related disease) may involve other organs as well. In this report we are presenting a case of a 74-year-old man with obstructive abdominal pain jaundice, mild and a history of retroperitoneal fibrosis and hydronephrosis. Read More

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http://dx.doi.org/10.1093/omcr/omy056DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6109199PMC
September 2018
15 Reads

A Case of Aortic Stenosis with Serum IgG4 Elevation, and IgG4-Positive Plasmacytic Infiltration in the Aortic Valve, Epicardium, and Aortic Adventitia.

Int Heart J 2018 Sep 11;59(5):1149-1154. Epub 2018 Aug 11.

Department of Cardiology, Osaka Medical College.

A 74-year-old man was admitted for preoperative screening of aortic stenosis. Five months before this admission, he was found to have elevated serum immunoglobulin G4 (IgG4; 2,010 mg/dL). Computed tomography (CT) showed a soft tissue mass surrounding the abdominal aorta, suggestive of IgG4-related periaortitis. Read More

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https://www.jstage.jst.go.jp/article/ihj/59/5/59_17-567/_art
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http://dx.doi.org/10.1536/ihj.17-567DOI Listing
September 2018
5 Reads

Mediastinal and retroperitoneal fibrosis as a manifestation of breast cancer metastasis: A case report and literature review.

Medicine (Baltimore) 2018 Aug;97(32):e11842

Department of Pathology, Soonchunhyang University Seoul Hospital, Soonchunhyang University College of Medicine, Seoul, Republic of Korea.

Rationale: Mediastinal and retroperitoneal fibrosis as a manifestation of metastasis from malignancies is rare disease and particularly, cases of mediastinal fibrosis have been rarely reported.

Patient Concerns: A 60-year-old woman presented with dyspnea and bilateral flank pain. The patient had no previous history of malignancy. Read More

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http://dx.doi.org/10.1097/MD.0000000000011842DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6133628PMC
August 2018
12 Reads

Acquired generalised lipodystrophy and type 1 diabetes mellitus in a child: a rare and implacable association.

BMJ Case Rep 2018 Aug 3;2018. Epub 2018 Aug 3.

Department of Paediatrics, Post Graduate Institude of Medical Education and Research, Chandigarh, India.

Lipodystrophy syndromes are frequently associated with marked degree of insulin resistance and lipoatrophic diabetes. Although acquired generalised lipodystrophy (AGL) has been known to be associated with various autoimmune disorders, type 1 diabetes mellitus (T1DM) is very rarely reported to occur with AGL. Combination of AGL and T1DM can lead to a totally different phenotype with very difficult-to-treat diabetes and progressive complications of both the conditions. Read More

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http://dx.doi.org/10.1136/bcr-2018-225553DOI Listing
August 2018
3 Reads

Renal allotransplantation in retroperitoneal fibrosis: technical aspects

Ceylon Med J 2018 06;63(2):86-87

Consultant Vascular and Transplant Surgeon, National Hospital, Sri Lanka.

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http://dx.doi.org/10.4038/cmj.v63i2.8688DOI Listing
June 2018
2 Reads