5,371 results match your criteria Pediatric Cardiology[Journal]


Whole-Exome Sequencing Reveals Novel Genetic Variation for Dilated Cardiomyopathy in Pediatric Chinese Patients.

Pediatr Cardiol 2019 Apr 16. Epub 2019 Apr 16.

Department of Cardiology, Children's Hospital of Nanjing Medical University, 72 Guangzhou Road, Nanjing, 210008, China.

Dilated cardiomyopathy (DCM) is characterized by left or bilateral ventricular dilation and systolic dysfunction without rational conditions, which can lead to progressive heart failure and sudden cardiac death. Most of the pathogenic genes have been reported in adult population by locus mapping in familial cases and animal model studies. However, it still remains challenging to decipher the role of genetics in the etiology of pediatric DCM. Read More

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http://dx.doi.org/10.1007/s00246-019-02096-1DOI Listing

Usefulness of 4D-Flow MRI in Mapping Flow Distribution Through Failing Fontan Circulation Prior to Cardiac Intervention.

Pediatr Cardiol 2019 Apr 13. Epub 2019 Apr 13.

Division of Cardiology, Heart Institute, Children's Hospital Colorado, University of Colorado Denver, Anschutz Medical Campus, 13123 E 16th Ave, Aurora, CO, 80045-2560, USA.

We report a case of a 23-year-old male with failing Fontan circulation who was taken to the catheterization lab to better evaluate the Fontan circulation and hemodynamics. Catheterization revealed arteriovenous malformations exclusively present in the right lung leading to the consideration of placing stents to direct the inferior vena cava flow through the Fontan circuit to the right pulmonary artery (RPA), thus increasing the RPA concentration of the hepatic factor. However, comprehensive 4D-Flow MRI analyses indicated sufficient distribution of the hepatic flow between branch pulmonary arteries, and consequently no further invasive intervention to redirect hepatic flow was performed. Read More

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http://dx.doi.org/10.1007/s00246-019-02101-7DOI Listing
April 2019
1 Read

Reverse Remodeling of Pulmonary Arterioles After Pulmonary Artery Banding in Patients ≥ 2 Years Old with Severe Pulmonary Arterial Hypertension and Congenital Heart Disease.

Pediatr Cardiol 2019 Apr 13. Epub 2019 Apr 13.

Department of Pediatric Cardiology, Beijing Anzhen Hospital, Capital Medical University, Beijing, China.

The purpose of this study was to evaluate the pathological changes of the pulmonary arterioles in patients ≥ 2 years of age who first underwent a pulmonary artery banding (PAB) procedure, followed by bidirectional Glenn or Fontan according to their specific conditions. This was a prospective study of 15 children diagnosed and treated with PAB at the Department of Cardiothoracic Surgery of Anzhen Hospital between January 2009 and December 2012. The percentage of media area (%MS) of pulmonary arteriole, the percentage of media thickness (%MT), and pulmonary arterial density (APSC) were calculated from lung tissue sections. Read More

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http://dx.doi.org/10.1007/s00246-019-02097-0DOI Listing

Morbidity During Adult Congenital Heart Surgery Admissions.

Pediatr Cardiol 2019 Apr 11. Epub 2019 Apr 11.

Division of Pediatric-Congenital Cardiology, Department of Pediatric, MassGeneral Hospital for Children, Massachusetts General Hospital, Harvard Medical School, 175 Cambridge Street, Suite 510, Boston, MA, 02114, USA.

The frequency of complications during Adult Congenital Heart Disease (ACHD) surgery admissions and their association to patient outcome is not well known. Our study objectives are to (1) define the frequency of complications during ACHD surgery admissions, (2) identify their risk factors, and (3) explore their association with death and resource use. We identified ACHD surgery admissions ages 18 to 49 during the years 2005-2009 from the Nationwide Inpatient Sample database. Read More

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http://dx.doi.org/10.1007/s00246-019-02103-5DOI Listing
April 2019
1 Read

Readmissions Following Congenital Heart Surgery in Infants and Children.

Pediatr Cardiol 2019 Apr 11. Epub 2019 Apr 11.

Division of Pediatric-Congenital Cardiology, Department of Pediatric, MassGeneral Hospital for Children, Massachusetts General Hospital, Harvard Medical School, 175 Cambridge Street, Suite 510, Boston, MA, 02114, USA.

Thirty-day readmission after congenital heart surgery (CHS) is an important outcome given the vulnerability of pediatric patients. We hypothesized that readmissions after pediatric CHS are common and identifiable risk factors exist. We obtained State Inpatient Databases for Washington, New York, Florida, and California and selected CHS admissions age < 19 years. Read More

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http://dx.doi.org/10.1007/s00246-019-02104-4DOI Listing

Left and Right Atrial Function and Remodeling in Beta-Thalassaemia Major.

Pediatr Cardiol 2019 Apr 10. Epub 2019 Apr 10.

Department of Paediatrics and Adolescent Medicine, Queen Mary Hospital, The University of Hong Kong, Hong Kong, China.

This study aimed to assess left (LA) and right atrial (RA) function in patients with beta-thalassaemia major. Thirty-eight patients (19 males) aged 34.5 ± 10. Read More

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http://dx.doi.org/10.1007/s00246-019-02105-3DOI Listing
April 2019
1 Read

A Novel Somatic Variant in HEY2 Unveils an Alternative Splicing Isoform Linked to Ventricular Septal Defect.

Pediatr Cardiol 2019 Apr 6. Epub 2019 Apr 6.

Department of Pediatrics and Adolescent Medicine, American University of Beirut, Beirut, Lebanon.

Congenital heart defects (CHDs) are the leading cause of death in infants under 1 year of age. Aberrations in the expression and function of cardiac transcription factors (TFs) are a major contributor to CHDs. Despite the numerous studies undertaken to functionally characterize these TFs, their exact role in different stages of cardiogenesis is still not fully elucidated. Read More

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http://dx.doi.org/10.1007/s00246-019-02099-yDOI Listing
April 2019
2 Reads

Screening Echocardiography and Brain Natriuretic Peptide Levels Predict Late Pulmonary Hypertension in Infants with Bronchopulmonary Dysplasia.

Pediatr Cardiol 2019 Apr 1. Epub 2019 Apr 1.

Division of Cardiology, Department of Pediatrics, University of Virginia Children's Hospital, Charlottesville, VA, USA.

Through this study, we aimed to assess the ability of routine neonatal screening at time of bronchopulmonary dysplasia (BPD) diagnosis to predict the development of late pulmonary hypertension (PHTN). This is a retrospective longitudinal cohort study of 37 premature infants with BPD assessing the utility of screening serum brain natriuretic peptide (BNP) and echocardiograms performed at the time of BPD diagnosis ('early PHTN') to predict 'late PHTN' at the last follow-up. Screening evaluation demonstrated early PHTN in 9/37 patients. Read More

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http://dx.doi.org/10.1007/s00246-019-02100-8DOI Listing

Ambulatory Arrhythmia Detection with ZIO® XT Patch in Pediatric Patients: A Comparison of Devices.

Pediatr Cardiol 2019 Apr 1. Epub 2019 Apr 1.

The Congenital Heart Collaborative, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, 44106, USA.

Ambulatory electrocardiogram monitoring devices can be used for 24-72 h to detect arrhythmias. A new device, the ZIO® XT Patch has cardiac monitoring capabilities that can be utilized for up to 14 days. The purpose of this study is to describe duration of ZIO use by age, and to compare its time to arrhythmia detection with the Holter monitor in a pediatric population. Read More

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http://dx.doi.org/10.1007/s00246-019-02089-0DOI Listing
April 2019
1 Read
1.550 Impact Factor

Postoperative heart failure after stage 1 palliative surgery for single ventricle cardiac disease.

Pediatr Cardiol 2019 Apr 1. Epub 2019 Apr 1.

Division of Cardiology, Children's Hospital Los Angeles, MS#34 4650 W. Sunset Blvd, Los Angeles, CA, 90027, USA.

Outcomes for patients with single ventricle congenital heart disease (SV-CHD) continue to improve over time. However, the prognosis for patients who develop heart failure immediately after surgery is poorly understood. We conducted a single-center, retrospective cohort study of patients with SV-CHD, who suffered postoperative heart failure. Read More

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http://dx.doi.org/10.1007/s00246-019-02093-4DOI Listing
April 2019
1 Read

Outcomes of Reinterventions for Children with Postoperative Pulmonary Venous Restenosis.

Pediatr Cardiol 2019 Apr 1. Epub 2019 Apr 1.

Department of Cardiothoracic Surgery, School of Medicine, Heart Center, Shanghai Children's Medical Center, Shanghai Jiaotong University, Dongfang Road 1678, Shanghai, China.

This report aims to summarize and evaluate the efficacy and experience of reintervention for children with postoperative pulmonary venous restenosis. Clinical data from 61 patients with postoperative pulmonary venous restenosis who underwent reintervention at Shanghai Children's Medical Center (SCMC) from September 2009 to June 2018 were retrospectively analyzed. The patients comprised 38 boys and 23 girls, with a mean age of 15. Read More

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http://link.springer.com/10.1007/s00246-019-02098-z
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http://dx.doi.org/10.1007/s00246-019-02098-zDOI Listing
April 2019
2 Reads

Umbilical Vein Catheter Protruding Through a Pulmonary Vein in a Patient with an Infracardiac Type Total Abnormal Pulmonary Venous Drainage.

Pediatr Cardiol 2019 04 30;40(4):878-879. Epub 2019 Mar 30.

Department of Paediatric Cardiology, Leiden University Medical Center, Albinusdreef 2, 2333 ZA, Leiden, The Netherlands.

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http://dx.doi.org/10.1007/s00246-019-02094-3DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6451718PMC
April 2019
1 Read

Cardiovascular Collapse with Intravenous Amiodarone in Children: A Multi-Center Retrospective Cohort Study.

Pediatr Cardiol 2019 Mar 30. Epub 2019 Mar 30.

Children's Heart Centre, University of British Columbia, Vancouver, BC, Canada.

Objective: To determine the incidence of cardiovascular collapse in children receiving intravenous (IV) amiodarone and to identify the population at risk.

Design: A multicenter study of patients ≤ 18 years of age who received intravenous amiodarone between January 2005 and December 2015. A retrospective analysis was performed to identify patients who developed cardiovascular collapse (bradycardia and/or hypotension). Read More

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http://dx.doi.org/10.1007/s00246-019-02090-7DOI Listing
March 2019
1 Read

Sinus node dysfunction in patients with Fontan circulation: could heart rate variability be a predictor for pacemaker implantation?

Pediatr Cardiol 2019 Apr 27;40(4):685-693. Epub 2019 Mar 27.

Department of Clinical Sciences, Pediatrics, Umeå University, 901 85, Umeå, Sweden.

Sinus node dysfunction (SND) causes significant morbidity in patients after Fontan surgery. Heart rate variability (HRV) reflects the autonomic regulation of the heart, and changes in HRV have been associated with SND in adults. We aimed to study whether changes in HRV could be detected in 24-h electrocardiographic (ECG) recordings in Fontan patients with SND. Read More

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http://dx.doi.org/10.1007/s00246-019-02092-5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6451711PMC
April 2019
1 Read

Right Ventricular Mechanical Dyssynchrony in Hypoplastic Left Heart Syndrome: Correlation with Systolic Function and QRS Duration.

Pediatr Cardiol 2019 Mar 20. Epub 2019 Mar 20.

Department of Pediatric Cardiology, Advocate Children's Hospital, Advocate Children's Heart Institute, 4440 W95th St, Oak Lawn, IL, 60453, USA.

The single right ventricle (RV) in hypoplastic left heart syndrome (HLHS) often develops systolic dysfunction with time and this affects prognosis. Mechanical dyssynchrony has been reported in HLHS but has not consistently correlated with systolic function or electrical dyssynchrony. The aims of this study were to assess the relationship between RV mechanical dyssynchrony, RV systolic function, and QRS duration on surface electrocardiography. Read More

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http://link.springer.com/10.1007/s00246-019-02091-6
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http://dx.doi.org/10.1007/s00246-019-02091-6DOI Listing
March 2019
6 Reads

Outcomes of Prosthetic Valved Conduits for Right Ventricular Outflow Tract Reconstruction.

Pediatr Cardiol 2019 Apr 18;40(4):848-856. Epub 2019 Mar 18.

Department of Cardio-thoracic Surgery, Heart Center, Shanghai Children's Medical Center, School of Medicine, Shanghai Jiao Tong University, 1678 Dongfang Road, Pudong New District, Shanghai, China.

There are limited data regarding the implantation of prosthetic valved conduits for right outflow tract reconstruction in pediatric patients in China. A retrospective review of 128 patients undergoing conduits implantation with a median follow-up of 33.3 months (range, 3. Read More

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http://dx.doi.org/10.1007/s00246-019-02081-8DOI Listing
April 2019
1 Read

Feasibility and Normal Ranges of Arterial Intima-Media Thickness and Stiffness in 2-Year-Old Children: A Pilot Study.

Pediatr Cardiol 2019 Mar 16. Epub 2019 Mar 16.

Menzies Institute for Medical Research, University of Tasmania, 17 Liverpool St, Hobart, TAS, 7000, Australia.

Introduction: In adults, noninvasive assessments of vascular function have been established. However, little is known about the applicability and reference values of these techniques among children < 6 years old and none ≤ 2. We aimed to determine the feasibility of conducting noninvasive vascular assessments in 2-year-old children and the normal range of results in this age group. Read More

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http://dx.doi.org/10.1007/s00246-019-02088-1DOI Listing

The Significance of Left Axis Deviation in the Pediatric Population: A Meta-Analysis.

Pediatr Cardiol 2019 Apr 16;40(4):677-684. Epub 2019 Mar 16.

Section of Pediatrics and Section of Cardiology, Department of Medicine, Lakes Region General Hospital, Laconia, NH, USA.

Left axis deviation (LAD) in children is rare but may be associated with structural heart disease. The aim of this study is to systematically assess the significance of LAD in the pediatric population. We included studies listed in PubMed, EMBASE, Web of Science, Cochrane databases, and Google Scholar before May 31, 2018 and their reference lists. Read More

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http://dx.doi.org/10.1007/s00246-019-02086-3DOI Listing

Cardiac Rhythm Disturbances in Heterotaxy Syndrome.

Pediatr Cardiol 2019 Mar 14. Epub 2019 Mar 14.

Department of Pediatrics, University of Tokyo Hospital, Tokyo, Japan.

Objective: Heterotaxy syndrome is associated with complex cardiac malformations and cardiac conduction system abnormalities. Those with right atrial isomerism (RAI) have dual sinus nodes and dual atrioventricular nodes predisposing them to supraventricular tachycardia (SVT). Those with left atrial isomerism (LAI) lack a normal sinus node and are at risk of sinus node dysfunction (SND) and atrioventricular block (AV block). Read More

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http://dx.doi.org/10.1007/s00246-019-02087-2DOI Listing
March 2019
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Rare Copy Number Variations Might Not be Involved in the Molecular Pathogenesis of PA-IVS in an Unselected Chinese Cohort.

Pediatr Cardiol 2019 Apr 13;40(4):762-767. Epub 2019 Mar 13.

Department of Pediatric Cardiothoracic Surgery, Shanghai Children's Medical Center, Shanghai Jiao Tong University School of Medicine, 1678 Dongfang Road, Shanghai, 200127, China.

Congenital heart defect (CHD) is one of the most common birth defects in China, while pulmonary atresia with intact ventricular septum (PA-IVS) is the life-threatening form of CHD. Numerous previous studies revealed that rare copy number variants (CNVs) play important roles in CHD, but little is known about the prevalence and role of rare CNVs in PA-IVS. In this study, we conducted a genome-wide scanning of rare CNVs in an unselected cohort consisted of 54 Chinese patients with PA-IVS and 20 patients with pulmonary atresia with ventricular septal defect (PA-VSD). Read More

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http://dx.doi.org/10.1007/s00246-019-02062-xDOI Listing
April 2019
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Identifying Subclinical Coronary Abnormalities and Silent Myocardial Ischemia After Arterial Switch Operation.

Pediatr Cardiol 2019 Mar 9. Epub 2019 Mar 9.

Nemours Cardiac Center, Nemours/Alfred I. duPont Hospital for Children, 1600 Rockland Rd, Wilmington, DE, 19803, USA.

The incidence of late coronary complications is reported around 8% after arterial switch operation (ASO) for d-transposition of the great arteries, but the affected patients are usually asymptomatic. Exercise stress test (EST) and myocardial perfusion imaging (MPI) are common non-invasive modalities to screen for silent myocardial ischemia, but their diagnostic reliability in children after ASO is unclear. We retrospectively reviewed asymptomatic patients following ASO with EST, MPI, and coronary imaging studies (CIS) and examined the reliability of each test in identifying abnormal coronary lesions responsible for myocardial ischemia. Read More

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http://dx.doi.org/10.1007/s00246-019-02085-4DOI Listing

Correlation Between Cardiopulmonary Exercise Test, Spirometry, and Congenital Heart Disease Severity in Pediatric Population.

Pediatr Cardiol 2019 Apr 8;40(4):871-877. Epub 2019 Mar 8.

Service de Cardiologie Pédiatrique, Cliniques Universitaires Saint-Luc, Bruxelles, Belgium.

Congenital heart disease (CHD) is a common chronic disease. This study aimed to verify the relationship between spirometry and exercise capacity in children, considering the CHD severity. All cardiopulmonary exercise testing (CPET) and Spirometry from CHD children (5-18 years) were retrospectively reviewed during three years. Read More

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http://dx.doi.org/10.1007/s00246-019-02084-5DOI Listing

Computational Identification of Ventricular Arrhythmia Risk in Pediatric Myocarditis.

Pediatr Cardiol 2019 Apr 6;40(4):857-864. Epub 2019 Mar 6.

Institute for Computational Medicine and Department of Biomedical Engineering, Johns Hopkins University, Baltimore, MD, USA.

Children with myocarditis have increased risk of ventricular tachycardia (VT) due to myocardial inflammation and remodeling. There is currently no accepted method for VT risk stratification in this population. We hypothesized that personalized models developed from cardiac late gadolinium enhancement magnetic resonance imaging (LGE-MRI) could determine VT risk in patients with myocarditis using a previously-validated protocol. Read More

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http://dx.doi.org/10.1007/s00246-019-02082-7DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6451890PMC
April 2019
2 Reads

Standardization of a Continuous Ramp Ergometer Protocol for Clinical Exercise Testing in Children.

Pediatr Cardiol 2019 Apr 5;40(4):834-840. Epub 2019 Mar 5.

Nemours Cardiac Center, Nemours/Alfred I. duPont Hospital for Children, P.O. Box 269, Wilmington, DE, 19899, USA.

Developing a standardized protocol for pediatric exercise laboratories is challenging. Our objective was to report normal pediatric values for a continuous non-steady state cycle ergometer ramp protocol to achieve 8-10 min of exercise based on sex and weight. One hundred seventeen patients (117) [mean age 13 ± 2. Read More

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http://dx.doi.org/10.1007/s00246-019-02079-2DOI Listing
April 2019
1 Read

Catheterization Performed in the Early Postoperative Period After Congenital Heart Surgery in Children.

Pediatr Cardiol 2019 Apr 4;40(4):827-833. Epub 2019 Mar 4.

Universidad Pontificia Bolivariana, Medellín, Colombia.

The aim of this study was to describe pediatric patients who underwent early postoperative cardiac catheterization after congenital heart surgery, their clinical indications, findings, interventions, and complications in a cardiovascular center. A descriptive retrospective study was performed. All catheterizations performed within 6 weeks after congenital heart surgery between January 2004 and December 2014 were reviewed. Read More

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http://link.springer.com/10.1007/s00246-019-02078-3
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http://dx.doi.org/10.1007/s00246-019-02078-3DOI Listing
April 2019
9 Reads

Recurrent Congenital Heart Diseases Among Neonates Born to Mothers with Congenital Heart Diseases.

Pediatr Cardiol 2019 Apr 4;40(4):865-870. Epub 2019 Mar 4.

Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.

The frequency of newborns with congenital heart disease (CHD) is approximately 1% in the general population; however, the recurrence rate of CHD in mothers with CHD differs in ethnicity and reports. We therefore aimed to determine the prevalence of CHD among neonates born to mothers with CHD in our institute in Japan. We reviewed the medical charts of 803 neonates delivered by 529 women with CHD at the National Cerebral and Cardiovascular Center from 1982 to 2016. Read More

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http://dx.doi.org/10.1007/s00246-019-02083-6DOI Listing
April 2019
2 Reads
1.550 Impact Factor

Relationship Between Pulmonary Arterial Resistance and Compliance in Patients with Down Syndrome.

Pediatr Cardiol 2019 Apr 4;40(4):841-847. Epub 2019 Mar 4.

Division of Pediatric Cardiology, Department of Cardiovascular Surgery, Japan Community Healthcare Organization, Kyushu Hospital, 1-8-1, Kishinoura, Yahatanishiku, Kitakyushu, Fukuoka, 806-8501, Japan.

This study aimed to clarify the characteristics of pulmonary arterial resistance (Rp)-compliance (Cp) coupling in individuals with Down syndrome (DS), who have increased risks of pulmonary arterial hypertension (PAH). We performed cardiac catheterization before and after corrective surgery in 85 DS infants and 85 controls with congenital heart disease and PAH. We retrospectively collected hemodynamic data and compared Rp and Cp between the groups. Read More

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http://dx.doi.org/10.1007/s00246-019-02080-9DOI Listing
April 2019
3 Reads

Usefulness of Red Cell Width Distribution (RDW) in the Assessment of Children with Pulmonary Arterial Hypertension (PAH).

Pediatr Cardiol 2019 Apr 4;40(4):820-826. Epub 2019 Mar 4.

Department of Cardiology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20, 04-730, Warsaw, Poland.

Red cell width distribution (RDW) is known to be a prognostic marker in adults with pulmonary hypertension. The value of this test in the pulmonary arterial hypertension (PAH) pediatric population was not yet established. The aim of the study was to evaluate the prognostic value of RDW in children with PAH and utility of this parameter in the management. Read More

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http://dx.doi.org/10.1007/s00246-019-02077-4DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6451723PMC
April 2019
2 Reads

Levosimendan as Rescue Therapy for Acute Heart Failure in a Patient with Duchenne Muscular Dystrophy.

Pediatr Cardiol 2019 Mar 22;40(3):668-670. Epub 2019 Feb 22.

Pediatric Intensive Care Unit, Hôpital Raymond-Poincaré, APHP, 92380, Garches, France.

The longer survival of patients with Duchenne muscular dystrophy due to advances in clinical care has increased the incidence of Duchenne muscular dystrophy-associated cardiomyopathy, a nearly consistent feature in the third decade of life. A 26-year-old patient with Duchenne muscular dystrophy experienced severe acute heart failure triggered by pneumonia. Levosimendan was effective in improving heart function. Read More

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http://link.springer.com/10.1007/s00246-019-02072-9
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http://dx.doi.org/10.1007/s00246-019-02072-9DOI Listing
March 2019
9 Reads

Does Coronary Reimplantation After Neoaortic Reconstruction Increase Aortic Regurgitation?

Pediatr Cardiol 2019 Apr 19;40(4):813-819. Epub 2019 Feb 19.

Department of Pediatrics, Dong-A University Hospital, Busan, South Korea.

Coronary reimplantation after neoaortic reconstruction (CRANR) in the arterial switch operation (ASO) allows easy selection of accurate coronary transfer sites in the distended neoaorta. However, neoaortic valve injury may occur during coronary reimplantation. We determined whether the CRANR procedure increased the incidence of aortic valve regurgitation (AR) after ASO. Read More

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http://dx.doi.org/10.1007/s00246-019-02075-6DOI Listing
April 2019
1 Read

Arterial Stiffness and Its Relationship to Cardiorespiratory Fitness in Children and Young Adults with a Fontan Circulation.

Pediatr Cardiol 2019 Apr 15;40(4):784-791. Epub 2019 Feb 15.

Child Development and Exercise Center, Wilhelmina Children's Hospital, P.O. Box 85090, 3508 AB, Utrecht, The Netherlands.

There are no previous studies on arterial stiffness and its associations with cardiorespiratory fitness in young Fontan patients. Therefore, we examined the arterial stiffness and its relationship to cardiorespiratory fitness in children and young adults with a Fontan circulation. Altogether, 17 Fontan patients and 26 healthy controls (16 females and 27 males aged 8-40 years) participated in this cross-sectional study. Read More

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http://dx.doi.org/10.1007/s00246-019-02065-8DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6451712PMC
April 2019
2 Reads

Modifiable Clinical Correlates of Vascular Health in Children and Adolescents with Dyslipidemia.

Pediatr Cardiol 2019 Apr 13;40(4):805-812. Epub 2019 Feb 13.

The Ward Family Heart Center, Children's Mercy Hospital, 2401 Gillham Rd, Kansas City, MO, 64108, USA.

Atherosclerosis promoting cardiovascular disease risk factors (CVDrf) are highly prevalent among youth in the U.S. Determining which standard modifiable clinical measures (SMCMs) has the greatest impact on vascular structure and function is valuable for the health care provider to help identify children at highest risk. Read More

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http://dx.doi.org/10.1007/s00246-019-02071-wDOI Listing
April 2019
3 Reads

Variable Treatment Approaches for Extracorporeal Membrane Oxygenation Complications in Neonates: A Case Series.

Pediatr Cardiol 2019 Mar 13;40(3):664-667. Epub 2019 Feb 13.

Division of Pediatric Cardiology, Children's Hospital of Georgia, Augusta University, 1120 15th Street BA 8300, Augusta, GA, 30912, USA.

Extracorporeal membrane oxygenation complications involving vascular injury or intracardiac thrombosis in neonates are rare. We present a series of unique complications and describe their variable treatments. Read More

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http://dx.doi.org/10.1007/s00246-019-02070-xDOI Listing
March 2019
1 Read

In Utero Aortic Arch Thrombosis Masquerading as Interrupted Aortic Arch: A Case Report and Review of the Literature.

Pediatr Cardiol 2019 Mar 8;40(3):658-663. Epub 2019 Feb 8.

Lillie Frank Abercrombie Section of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, 6621 Fannin St, Legacy Tower, E1920, Houston, TX, 77030, USA.

Aortic arch thrombosis is an extremely rare but life-threatening diagnosis that is often misdiagnosed in the neonatal period. Strategies including surgical intervention, systemic anticoagulation, and thrombolysis have been previously described in the treatment of these neonates. We describe the case of a neonate who presented with concern for interrupted aortic arch and was diagnosed with an in utero aortic arch thrombosis. Read More

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http://dx.doi.org/10.1007/s00246-019-02068-5DOI Listing

Size and Stiffness of the Pulmonary Autograft after the Ross Procedure in Children.

Pediatr Cardiol 2019 Apr 7;40(4):776-783. Epub 2019 Feb 7.

Department of Cardiovascular Surgery, Japan Community Health Care Organization Kyushu Hospital, 1-8-1 Kishinoura, Yahatanishi-ku, Kitakyushu, 806-8501, Japan.

Progressive dilatation of the pulmonary autograft is one of the greatest concerns after the Ross procedure. Increased stress in the arterial wall may cause changes in the elastic properties of the pulmonary autograft, and thus lead to pathological dilatation. The present study aimed to investigate the changes in the autograft diameter and stiffness during follow-up after the Ross procedure. Read More

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http://dx.doi.org/10.1007/s00246-019-02064-9DOI Listing

Transseptal Puncture for Catheter Ablation in Children.

Pediatr Cardiol 2019 Apr 7;40(4):799-804. Epub 2019 Feb 7.

Department of Pediatric Cardiology/Electrophysiology, Istanbul Medipol University Hospital, Istanbul, Turkey.

Transseptal puncture (TP) is used in pediatric patients to access the left atrium in left-sided arrhythmia catheter ablation. Performing this procedure can be difficult and risky, especially in small children. In this study, we aimed to evaluate the safety and feasibility of TPs in children ≤ 30 kg. Read More

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http://link.springer.com/10.1007/s00246-019-02069-4
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http://dx.doi.org/10.1007/s00246-019-02069-4DOI Listing
April 2019
8 Reads

Characteristics and Outcomes of Heart Transplantation in DiGeorge Syndrome.

Pediatr Cardiol 2019 Apr 7;40(4):768-775. Epub 2019 Feb 7.

Pediatric Cardiology, Monroe Carell Jr. Children's Hospital, Nashville, TN, USA.

DiGeorge syndrome (DGS) is commonly associated with both congenital heart disease (CHD) and immunologic abnormalities. While CHD may prompt consideration for heart transplantation (HTx), little is known about HTx management or outcomes in this group. The aim of this study was to describe the spectrum of patients with DGS who undergo HTx and report post-HTx outcomes. Read More

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http://dx.doi.org/10.1007/s00246-019-02063-wDOI Listing
April 2019
2 Reads

Non-invasive Hemodynamic CMR Parameters Predicting Maximal Exercise Capacity in 54 Patients with Ebstein's Anomaly.

Pediatr Cardiol 2019 Apr 6;40(4):792-798. Epub 2019 Feb 6.

Pediatric Cardiology and Congenital Heart Disease, Deutsches Herzzentrum München, Technical University of Munich, Lazarettstrasse 36, 80636, Munich, Germany.

Background: Exercise capacity is a well-defined marker of outcome in congenital heart disease. We analyzed seventeen cardiovascular magnetic resonance (CMR) derived parameters and their correlation to exercise capacity in patients with Ebstein's anomaly (EA).

Methods: Fifty-four surgery free patients, age 5 to 69 years (median 30 years) prospectively underwent CMR examination and cardiopulmonary exercise testing (CPET). Read More

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http://dx.doi.org/10.1007/s00246-019-02066-7DOI Listing
April 2019
1 Read

Analysis of Inflammatory Cytokines in Postoperative Fontan Pleural Drainage.

Pediatr Cardiol 2019 Apr 1;40(4):744-752. Epub 2019 Feb 1.

University of Michigan Congenital Heart Center, 1540 E. Hospital Dr, Ann Arbor, MI, 48109, USA.

Prolonged pleural drainage is a common complication in patients after Fontan palliation and is associated with short- and long- term morbidities. Among many potential etiologies, prolonged drainage has an inflammatory component, but there are no descriptions of cytokines in Fontan pleural drainage to date. This study aimed to examine the inflammatory make-up of Fontan pleural drainage. Read More

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http://dx.doi.org/10.1007/s00246-019-02059-6DOI Listing

Diagnostic Effect of the Single BP Cut-Offs for Identifying Elevated BP and Hypertension in Adolescents Aged 13-17 Years.

Pediatr Cardiol 2019 Apr 1;40(4):738-743. Epub 2019 Feb 1.

Department of Epidemiology, School of Public Health, Shandong University, Jinan, 250012, China.

In contrast to the percentile-based definitions of elevated blood pressure (BP) and hypertension for children and adolescents of all ages in the 2004 fourth report, the 2017 American Academy of Pediatrics (AAP) BP guideline recommends a change to single BP cut-offs for clinical diagnosis (120/< 80-129/< 80 mmHg for elevated BP and ≥ 130/80 mmHg for hypertension) in adolescents aged 13 years and older, and it also recommends researchers using the percentile-based definitions for more precise BP classification. The aim of our study was to assess the diagnostic effect of the single BP cut-offs for identifying adolescent abnormal BP as compared to the 2017 AAP percentile table by sex, age, and height. Data were from 8287 adolescents aged 13-17 years in NHANES 1999-2016 and 1659 adolescents aged 13-17 years in NHANES III (1988-1994). Read More

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http://dx.doi.org/10.1007/s00246-019-02058-7DOI Listing
April 2019
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Exercise Capacity After Repair of Ebstein Anomaly in Adults.

Pediatr Cardiol 2019 Apr 30;40(4):726-732. Epub 2019 Jan 30.

Department of Pediatric Cardiology, Mayo Clinic, 200 1st St SW, Rochester, MN, 55905, USA.

Repair of Ebstein anomaly has evolved over the last decade, and timing of repair remains variable. There have been no studies of exercise or functional capacity in patients who have had tricuspid valve surgery for Ebstein anomaly in adulthood. We aimed to compare exercise capacity before and after tricuspid valve repair or replacement for Ebstein anomaly in adults at Mayo Clinic. Read More

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http://dx.doi.org/10.1007/s00246-019-02056-9DOI Listing
April 2019
2 Reads

Complications of Transthoracic Intracardiac and Central Venous Lines in Neonates Undergoing Cardiac Surgery.

Pediatr Cardiol 2019 Apr 30;40(4):733-737. Epub 2019 Jan 30.

Department of Anesthesiology, Critical Care and Pain Medicine, Division of Cardiac Anesthesia, Boston Children's Hospital, 300 Longwood Ave, Boston, MA, 02115, USA.

Neonates undergoing congenital heart surgery require central venous access for diagnostic information and medication administration. There are multiple options for central access including peripherally inserted central catheters, umbilical, central venous, and transthoracic intracardiac lines. We retrospectively identified all patients younger than 30 days who underwent cardiac surgery in a 1-year period. Read More

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http://dx.doi.org/10.1007/s00246-019-02057-8DOI Listing
April 2019
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Three-Dimensional Rotational Angiography in Pediatric Patients with Congenital Heart Disease: A Literature Review.

Pediatr Cardiol 2019 Feb 24;40(2):257-264. Epub 2019 Jan 24.

Department of Pediatric Cardiology, Wilhelmina Children's Hospital, University Medical Center Utrecht, Lundlaan 6, P.O. Box 85090, 3508 AB, Utrecht, the Netherlands.

Cardiac catheterization is a commonly used form of imaging and treatment in pediatric patients with congenital heart disease. Traditionally, two-dimensional conventional angiography was the method used, but since 2000 three-dimensional rotational angiography (3DRA) is increasingly used in the field of cardiology in both adult and pediatric patients. To investigate the use and applications of 3DRA in pediatric congenital cardiology, literature was systematically reviewed and 29 eligible articles were found. Read More

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http://dx.doi.org/10.1007/s00246-019-02052-zDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6399168PMC
February 2019
2 Reads

Worldwide Variability of Antithrombotic Therapy During Cardiac Catheter Ablation in Children: A Survey from 50 Centers Around the World.

Pediatr Cardiol 2019 Feb 23;40(2):456-458. Epub 2019 Jan 23.

Arrhythmia Unit, Cardiology Department, Hospital Sant Joan de Déu, Universitat de Barcelona, Barcelona, Spain.

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http://dx.doi.org/10.1007/s00246-019-02053-yDOI Listing
February 2019

Pulmonary Artery Banding in Post-tricuspid Congenital Cardiac Shunting Defects with High Pulmonary Vascular Resistance.

Pediatr Cardiol 2019 Apr 23;40(4):719-725. Epub 2019 Jan 23.

Division of Cardiac Critical Care, and the Pulmonary Hypertension Program, Department of Cardiology, Boston Children's Hospital, 300 Longwood Ave, Boston, MA, 02115, USA.

Reports of "treat and repair" of cardiac shunting lesions with inoperably high pulmonary vascular resistance (PVR) mostly concern pre-tricuspid defects; post-tricuspid lesions are different. We report our experience with pulmonary artery (PA) banding ± targeted pulmonary hypertension medications in five patients with a large VSD and inoperably high PVR, and review previous reports of PA banding with post-tricuspid defects. Three of our 5 patients had mean PAP > 50 mmHg after banding and no or only a transient fall in PVR. Read More

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http://dx.doi.org/10.1007/s00246-019-02054-xDOI Listing
April 2019
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Anomalous Origin of Right Coronary Artery from the Non-coronary Cusp Demonstrated by Echocardiography and CT Angiography.

Pediatr Cardiol 2019 Feb 23;40(2):454-455. Epub 2019 Jan 23.

Department of Pediatric Cardiology, Cleveland Clinic, Cleveland, OH, USA.

Certain coronary anomalies have been associated with sudden cardiac death. Anomalous origin of the right coronary artery (RCA) from the posterior non-coronary aortic cusp is exceedingly rare. Through multimodality imaging, we present a young female with an anomalous RCA arising from the non-coronary cusp. Read More

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http://dx.doi.org/10.1007/s00246-019-02055-wDOI Listing
February 2019
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Timing of Fontan Completion in Children with Functionally Univentricular Hearts and Isomerism: The Impact of Age, Weight, and Pre-Fontan Arterial Oxygen Saturation.

Pediatr Cardiol 2019 Apr 22;40(4):753-761. Epub 2019 Jan 22.

Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Isomerism, or heterotaxy, impacts morbidity and mortality after various stages of univentricular palliation. Timing of Fontan completing in these patients based on preoperative factors has not been investigated previously. The aim of this study was to determine the impact of preoperative factors on various outcomes including length of hospital stay and duration of chest tubes. Read More

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http://dx.doi.org/10.1007/s00246-019-02060-zDOI Listing

Usefulness of Electroanatomical Mapping with Contact Force Monitoring for Accessory Pathways Ablation in Pediatric Population.

Pediatr Cardiol 2019 Apr 21;40(4):713-718. Epub 2019 Jan 21.

Arrhythmia Unit and Electrophysiology Laboratories, San Raffaele Scientific Institute, Milan, Italy.

The current approach for catheter ablation (CA) of accessory pathways (AP) includes the use of standard catheters under fluoroscopic visualization. We hypothesize that use of contact force (CF) irrigated tip catheters might increase procedural safety in pediatric patients compared to standard irrigated tip catheters, by decreasing the number of radiofrequency (RF) pulses required to obtain AP elimination. Seventy-one pediatric patients (13. Read More

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http://dx.doi.org/10.1007/s00246-019-02051-0DOI Listing
April 2019
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Impact of Time Interval Between Glenn and Fontan Procedures on Fontan Operative and Long-Term Follow-up Results.

Pediatr Cardiol 2019 Apr 16;40(4):705-712. Epub 2019 Jan 16.

Department of Congenital Heart Disease, State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, No. 167 North Lishi Road, Xicheng District, Beijing, China.

Objective: The bidirectional cavopulmonary shunt (BCPS) is an effective palliative procedure which has been widely used to boost outcome of the Fontan procedure. However, there is no standard duration time between these two procedures. Therefore, we investigated whether different time intervals between BCPS and Fontan procedure affects morbidity and mortality of Fontan patients. Read More

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http://link.springer.com/10.1007/s00246-018-2049-7
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http://dx.doi.org/10.1007/s00246-018-2049-7DOI Listing
April 2019
15 Reads