Am J Dermatopathol 2021 Feb 16. Epub 2021 Feb 16.
Department of Dermatology, Georgetown University School of Medicine, Washington, DC; Department of Dermatology, MedStar Washington Hospital Center, Georgetown University Hospital, Washington, DC; Aurora Diagnostics/MidAtlantic Pathology Services, Sterling, VA; and Children's National Medical Center, Washington, DC.
Abstract: Although not a diagnostic criterion for basal cell nevus syndrome (BCNS, OMIM#109400), cutaneous cysts, particularly epidermoid cysts, are common in this condition. Cutaneous keratocysts, on the other hand, are extremely rare in general and have been identified in only 5 patients with BCNS. Here, we describe a BCNS patient with a cutaneous keratocyst that demonstrated D2-40 (podoplanin) immunoreactivity, which has been detected in odontogenic keratocysts but not cutaneous keratocysts. Read More