Pediatric Malignant Atrophic Papulosis.
- Authors:
- Yung-Chieh Huang,
- Jiaan-Der Wang,
- Fang-Yi Lee,
- Lin-Shien Fu
Pediatrics 2018 Apr;141(Suppl 5):S481-S484
Departments of Pediatrics and
Malignant atrophic papulosis (MAP), also known as Degos disease, is an extremely rare disease that is characterized by its unique skin presentation (namely, central, porcelain-white atrophic lesions with a telangiectatic rim). MAP has the following 2 variants: cutaneous MAP is manifested in the skin alone, whereas systemic MAP affects the gastrointestinal tract, central nervous system, lungs, and other internal organs. Some patients who presented with only cutaneous symptoms at first may develop systemic symptoms several years later. Read More