1,972 results match your criteria Lymphangiectasia

Conjunctival Chemosis and Annular Ciliochoroidal Detachments Detected by Anterior-Segment Optical Coherence Tomography in a Case of Systemic Lupus Erythematosus.

Case Rep Ophthalmol 2021 Jan-Apr;12(1):154-158. Epub 2021 Apr 12.

Department of Ophthalmology, Shimane University Faculty of Medicine, Izumo, Japan.

A 61-year-old Japanese woman presented to our hospital for treatment of systemic serositis associated with systemic lupus erythematosus (SLE). At the initial ophthalmologic examination, her best-corrected visual acuity was 1.2 and 0. Read More

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Case Report: A Relatively Mild Presentation of Unilateral Congenital Pulmonary Lymphangiectasia.

Front Pediatr 2021 22;9:657473. Epub 2021 Apr 22.

Department of Pediatrics, CS Mott Children's Hospital, Michigan Medicine, Ann Arbor, MI, United States.

Pulmonary lymphangiectasia (PL) is a rare congenital disorder of pulmonary lymphatic development. Although it was traditionally a fatal disorder of infancy, some cases in later childhood have been reported, suggesting a spectrum of severity. We present an unusual case of unilateral, congenital pulmonary lymphangiectasia. Read More

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Lip swelling with lymphangiectasia.

JAAD Case Rep 2021 May 26;11:93-95. Epub 2021 Mar 26.

Department of Dermatology, Tulane University, New Orleans, Louisiana.

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Therapeutic Lymphatic Embolization in Pediatric Primary Intestinal Lymphangiectasia.

Yonsei Med J 2021 May;62(5):470-473

Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.

Primary intestinal lymphangiectasia (IL) can cause leakage of lymphatic fluids into the gastrointestinal tract, eventually leading to protein-losing enteropathy. A 15-year-old male patient, whose disease began at the age of 8 years, recently felt worsening general weakness. After diagnosing abnormal lymphatic lesions in the duodenum through endoscopy with biopsy and contrast-enhanced magnetic resonance lymphangiography, glue embolization of the leaking duodenal lymphatic channel was successfully performed. Read More

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Refractory lymphatic ascites following laparoscopic management of renal lymphangiectasia: An unusual presentation.

J Minim Access Surg 2021 Apr 8. Epub 2021 Apr 8.

Department of Urology, All India Institute of Medical Sciences, New Delhi, India.

Renal lymphangiectasia characterised by either unilocular or multilocular cystic lesion in and around the kidney is an uncommon condition. Presentation of these lesions is quite varied, which along with its uncommon occurrence adds to the challenges in the management of this condition. Most of these cases are managed conservatively and very rarely need any intervention. Read More

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Non-immune hydrops fetalis secondary to congenital chylothorax with diffuse interstitial lung disease: a diagnostic conundrum.

BMJ Case Rep 2021 Apr 16;14(4). Epub 2021 Apr 16.

Department of Neonatal and Developmental Medicine, Singapore General Hospital, Singapore.

A Chinese male infant was born at 35 weeks weighing 2935 g to a mother with polyhydramnios and prenatal hydrops fetalis. He developed marked respiratory distress secondary to bilateral congenital chylothorax and required pleural drainage, high frequency oscillation and inhaled nitric oxide therapy. He was extubated to non-invasive ventilation by day 14. Read More

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Prognostic value of the nutmeg lung pattern/lymphangiectasia on fetal magnetic resonance imaging.

Pediatr Radiol 2021 Apr 15. Epub 2021 Apr 15.

Department of Radiology, Children's Hospital of Philadelphia, 3401 Civic Center Blvd., Philadelphia, PA, 19104, USA.

Background: A nutmeg lung pattern on magnetic resonance imaging (MRI) is an imaging finding associated with pulmonary lymphangiectasia. However, the prognostic value of the nutmeg lung pattern is unknown.

Objective: To evaluate the clinical associations of nutmeg lung indicating lymphangiectasia on fetal lung MRI and its relationship with early mortality in fetuses with primary and secondary lymphangiectasia. Read More

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Unilateral congenital pulmonary lymphangiectasis presenting with pneumothorax and an NRAS variant.

Pediatr Pulmonol 2021 Apr 14. Epub 2021 Apr 14.

Department of Pathology and Laboratory Medicine, Alberta Children's Hospital and University of Calgary, Calgary, Alberta, Canada.

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A Four-Week-Old Infant With Respiratory Distress: An Emergency Department Case Presentation of Congenital Lobar Emphysema.

Cureus 2021 Mar 10;13(3):e13814. Epub 2021 Mar 10.

Emergency Medicine, Stanford University, Stanford, USA.

Congenital lobar emphysema (CLE) and congenital pulmonary lymphangiectasis (CPL) are rare conditions that are most often identified with prenatal ultrasonography. Occasionally, this disease process is first identified in the emergency department (ED), where the physician should avoid common pitfalls in order to prevent acute decompensation. To the best of our knowledge, there are no prior reports in the emergency medicine literature of CLE or CPL presenting to the ED as undifferentiated respiratory distress in an infant. Read More

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Refractory primary intestinal lymphangiectasia effectively managed with subcutaneous octreotide.

BMJ Case Rep 2021 Apr 9;14(4). Epub 2021 Apr 9.

General Surgery, Highgate Private Hospital, London, Highgate, UK.

This case report describes a young man with a history of lymphoedema and long-standing gastrointestinal symptoms since childhood. After undergoing extensive investigations, he was diagnosed with primary intestinal lymphangiectasia (IL). The patient's condition was refractory to conventional medium-chain triglyceride diet but responded well to treatment with subcutaneous octreotide. Read More

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J Wildl Dis 2021 Apr;57(2):321-326

Programa de Ganadería, Campus Montecillo, Colegio de Postgraduados (ColPos), Km 36.5 Carretera México-Texcoco, Montecillo, Texcoco, Mexico, 56230.

Paratuberculosis (PTB) is a disease that affects cattle (Bos taurus), goats (Capra aegagrus hircus), sheep (Ovis aries), and wild animals, such as white-tailed deer (Odocoileus virginianus), since all ruminants are susceptible. The causal agent is Mycobacterium avium subsp. paratuberculosis (MAP). Read More

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Lymphatic dysfunction in advanced cirrhosis: Contextual perspective and clinical implications.

World J Hepatol 2021 Mar;13(3):300-314

Department of Radiodiagnosis, All India Institute of Medical Sciences, Patna 801507, Bihar, India.

The lymphatic system plays a very important role in body fluid homeostasis, adaptive immunity, and the transportation of lipid and waste products. In patients with liver cirrhosis, capillary filtration markedly increases, primarily due to a rise in hydrostatic pressure, leading to enhanced production of lymph. Initially, lymphatic vasculature expansion helps to prevent fluid from accumulating by returning it back to the systemic circulation. Read More

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Vulval lymphangiectasia in pregnancy-a rare case report.

J Obstet Gynaecol Res 2021 Mar 28. Epub 2021 Mar 28.

Department of Obstetrics and Gynecology, Sri Manakula Vinayagar Medical College and Hospital, Puducherry, India.

Difficulty in arriving at a diagnosis of vulval lesions of women presenting in labor leads to a dilemma in deciding the delivery route. Here we present a case of large vulval lesion extending from mons pubis to anterior half of perineum presenting in labor in a 27-year-old second gravida with term pregnancy. History revealed an onset of vulval swelling within 3 months of starting antituberculosis treatment for cervical tuberculous lymphadenopathy at the age of 25 years. Read More

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Hennekam lymphangiectasia syndrome: A rare case of primary lymphedema.

Indian J Dermatol Venereol Leprol 2021 Mar-Apr;87(2):240-244

Department of Dermatology and STD, Lady Hardinge Medical College and Associated Hospitals, New Delhi, India.

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[Intestinal lymphangiectasia in a patient with Sanfilippo B syndrome].

Arch Argent Pediatr 2021 04;119(2):e138-e141

Servicio de Anatomía Patológica, Hospital Clínico Universitario Lozano Blesa. Zaragoza, España.

Mucopolysaccharidosis type IIIB is a lysosomal storage disease caused by a deficiency of the N-acetyl-alpha-d-glucosaminidase enzyme involved in the catabolism of heparan sulfate, causing its accumulation in various tissues. We present an 8-year-old patient with mucopolysaccharidosis type IIIB, with a history of chronic diarrhea and endoscopic and histological findings compatible with intestinal lymphangiectasia. After a dietary treatment with a low-fat diet supplemented with mediumchain triglyceride, our patient presents clinical improvement until today. Read More

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The diagnostic value of capsule endoscopy in children with intestinal lymphangiectasia.

Rev Esp Enferm Dig 2021 Mar 18. Epub 2021 Mar 18.

Gastroenterology, Children's Hospital of Fudan University, China.

Background: Intestinal lymphangiectasia is an unusual cause of protein-losing enteropathy due to either congenital malformation or the obstruction of the intestinal lymphatics. However, few reports have investigated the use of video capsule endoscopy in children with intestinal lymphangiectasia. This study was performed to evaluate the diagnostic value of video capsule endoscopy for paediatric intestinal lymphangiectasia. Read More

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Lymphangioma Formation Following Hyaluronic Acid Injection for Lip Augmentation.

Cureus 2021 Jan 27;13(1):e12929. Epub 2021 Jan 27.

Oral and Maxillofacial Surgery, Rotherham National Health Service Foundation Trust, Rotherham, GBR.

Administration of hyaluronic acid (HA) filler for aesthetic lip augmentation is a routine and common procedure with a low rate of adverse reactions. This case report documents an extremely rare complication of lip augmentation with HA leading to the development of lymphangiomas. Lymphangiomas are uncommon hamartomas of the lymphatic system. Read More

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January 2021

Long-term endoscopic findings in pediatric primary intestinal lymphangiectasia.

Clin Case Rep 2021 Feb 5;9(2):1029-1030. Epub 2020 Dec 5.

Division of Gastroenterology, Department of Internal Medicine, Faculty of Medicine Saga University Saga Japan.

This is the first case report comparing endoscopic images of primary intestinal lymphangiectasia (PIL) over 10 years. Regular endoscopic examination is essential in PIL because endoscopic findings do not correlate well with clinical manifestations. Read More

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February 2021


Rev Esp Enferm Dig 2021 Feb 11. Epub 2021 Feb 11.

Gastroenterology, Portuguese Oncology Institute of Coimbra.

A 41-year-old caucasian female, with past medical history of pituitary adenoma medicated with cabergoline, presented with worsening dyspepsia and unintentional weight loss of 5%. Physical exam and laboratory results were unremarkable for pathological findings. Esophagogastroduodenoscopy revealed an oedematous and exuberant lymphangiectasia appearance in the duodenum, with no ulceration or suspected infiltration component (figure 1 - A/B). Read More

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February 2021

Intestinal Lymphangiectasia Associated With Refractory Ascites in a Cirrhosis Patient.

Cureus 2021 Jan 7;13(1):e12567. Epub 2021 Jan 7.

Radiology, All India Institute of Medical Sciences Patna, Patna, IND.

Lymphatic systems play a very important role in the body fluid homeostasis by interstitial fluid reabsorption. Lymphatic dysfunctions are common in patients with advanced cirrhosis, contributing to ascites and lymphedema. An unusual manifestation of lymphatic dysfunction in patients with cirrhosis is intestinal lymphangiectasia. Read More

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January 2021

Capsule Retention Caused by Cryptogenic Multifocal Ulcerous Stenosing Enteritis.

Rev Esp Enferm Dig 2021 Feb 10. Epub 2021 Feb 10.

Gastroenterology, Beijing Shijitan Hospital. Capital Medical University.

Introduction: Cryptogenic multifocal ulcerous stenosing enteritis (CMUSE) is a rare illness, and capsule retention (CR) has been reported in a few cases of CMUSE.

Methods: We present four cases of CMUSE with CR. None of the patients showed any symptoms or signs of small bowel obstruction before a capsule endoscopy (CE) and denied a history of any non-steroidal anti-inflammatory drugs intake, radiotherapy treatment, or abdominal surgery. Read More

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February 2021

Dermatochalasis Through Decades: A Histopathologic Study.

Ann Plast Surg 2021 03;86(3):340-344

Eye Research Center, The Five Senses Institute.

Objectives: Three prior studies (2008, 2011, 2018) histopathologically compared the eyelid specimens of patients with dermatochalasis (DC, undergoing blepharoplasty) with a control group and proposed that DC may begin with subclinical inflammation leading to elastolysis and lymphostasis. With growing number of younger patients consulting for blepharoplasty, the unanswered question is whether histopathologic changes of DC differ between the younger and the older.

Patients And Methods: In this prospective case series, 20 right upper eyelid skin of 20 nonsmoker, class 3 Fitzpatrik skin type women (30-68 years old) were histopathologically examined. Read More

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Primary intestinal lymphangiectasia in an adult patient: A case report and review of literature.

World J Gastroenterol 2020 Dec 8;26(48):7707-7718. Epub 2020 Dec 8.

Department of Internal Medicine, General Hospital Oberndorf, Teaching Hospital of the Paracelsus Medical University Salzburg, Oberndorf 5110, Austria.

Background: Primary intestinal lymphangiectasia (PIL), first described in 1961, is a rare disorder of unknown etiology resulting in protein-losing enteropathy. The disease is characterized by dilatation and leakage of intestinal lymph vessels leading to hypoalbuminemia, hypogammaglobulinemia, and lymphopenia. Since the severity and location of lymph vessels being affected can vary considerably, the range of associated symptoms is wide from mild lower-limb edema to generalized edema, abdominal and/or pleural effusion, and recurrent diarrhea, among others. Read More

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December 2020

Acquired lymphangiectasia: a rare mimic of genital warts.

Dermatol Online J 2020 Dec 15;26(12). Epub 2020 Dec 15.

University Clinic for Dermatology, Faculty of Medicine, Ss. Cyril and Methodius University-Skopje, Skopje.

Acquired lymphangiectasia of the vulva is very uncommon. Owing to the non-specific papillomatous manifestation and the vast array of possible differential diagnoses, lymphangioma circumscriptum (LC) still presents a diagnostic challenge. In this report, we present a very rare form of acquired vulvar LC in a 71-year-old patient with a longstanding history of asymptomatic lesions over the labia majora that had been previously treated as genital warts. Read More

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December 2020

Individual approach for treatment of primary intestinal lymphangiectasia in children: single-center experience and review of the literature.

BMC Pediatr 2021 Jan 7;21(1):21. Epub 2021 Jan 7.

Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine, 81 Irwon-ro, Gangnam-gu, Seoul, 06351, South Korea.

Background: Intestinal lymphangiectasia is a rare disease. Thus, prospective studies are impossible, and therapy is still controversial. Several medicines are suggested for treatment but there are no existing indications for drug choice and treatment guidelines. Read More

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January 2021

Scrotal Lymphangiectasia with Penile Elephantiasis in Underlying Lymphatic Filariasis-Challenging the Diagnostic Mind! A Case Report.

Dermatopathology (Basel) 2021 Jan 1;8(1):10-16. Epub 2021 Jan 1.

Dermatology Unit, Skin Saga Centre for Dermatology, Mumbai 400053, India.

Background: A plethora of diseases manifest as acquired genital lymphangiectasias which clinically manifest as superficial vesicles. They range from infections such as tuberculosis to connective tissue diseases such as scleroderma and even malignancy. Amongst infectious etiologies, lymphatic filariasis leads as the cause for lymphatic obstruction. Read More

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January 2021

Retroperitoneal Lymphangioma in Adult: A Case Report.

Mymensingh Med J 2021 Jan;30(1):224-227

Dr Md Manir Hossain Khan, Associate Professor, Department of Surgery, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh; E-mail:

Lymphangioma is a rare, benign tumour occurring due to congenital malformation of the lymphatic channels. It occurs due to obstruction in the lymphatic channel and results in lymphangiectasia. The tumour is most commonly encountered in the head and neck regions and almost 90% are in the children below the age of 2 years. Read More

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January 2021

Pleural effusion and ascites in extrarenal lymphangiectasia caused by post-biopsy hematoma: A case report.

World J Clin Cases 2020 Dec;8(24):6330-6336

Department of Nephrology, The First Hospital of Hebei Medical University, Shijiazhuang 050000, Hebei Province, China.

Background: The renal system has a specific pleural effusion associated with it in the form of "urothorax", a condition where obstructive uropathy or occlusion of the lymphatic ducts leads to extravasated fluids (urine or lymph) crossing the diaphragm innate perforations or lymphatic channels. As a rare disorder that may cause pleural effusion, renal lymphangiectasia is a congenital or acquired abnormality of the lymphatic system of the kidneys. As vaguely mentioned in a report from the American Journal of Kidney Diseases, this disorder can be caused by extrinsic compression of the kidney secondary to hemorrhage. Read More

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December 2020

Posttransplant Renal Lymphangiectasia Presents Differently From Native Kidneys and Warrants Attention.

Prog Transplant 2021 Mar 15;31(1):95-96. Epub 2020 Dec 15.

Division of Diagnostic and Interventional Ultrasound in Transplantations, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

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A case of "misplaced" Tritrichomonas foetus infection in a dog in Northern Italy.

Vet Parasitol Reg Stud Reports 2020 12 19;22:100451. Epub 2020 Aug 19.

Città di Pavia Veterinary Hospital, 179 Cremona road, 27100 Pavia, Italy. Electronic address:

An 8-year-old, spayed female Rottweiler dog, under immunosuppressant treatment for protein-losing enteropathy (PLE) and intestinal lymphangiectasia, was presented for anorexia, poor general conditions and episodes of diarrhea. A subcutaneous mass between the caudal abdominal mammary glands was found. A fine-needle aspiration cytology was performed and revealed the presence of inflammatory cells mixed with pear- or round-shaped microorganisms with cytomorphological features of flagellated protozoan trophozoites, belonging to Trichomonadida order. Read More

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December 2020