1,820 results match your criteria Lymphangiectasia


[Primary intestinal lymphangiectasia: Could propranolol be an effective alternative treatment?]

An Pediatr (Barc) 2018 Oct 25. Epub 2018 Oct 25.

Servicio de Gastroenterología y Nutrición, Hospital Materno Infantil, Badajoz, España.

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http://dx.doi.org/10.1016/j.anpedi.2018.09.006DOI Listing
October 2018

Novel Magnified Single-Balloon Enteroscopy Enables Observation of Jejunal White Spots Associated with Lymphangiectasia.

Dig Dis 2018 Nov 22:1-5. Epub 2018 Nov 22.

A 59-year-old woman was diagnosed with primary intestinal lymphangiectasia (PIL), with characteristic findings on capsule enteroscopy and confirmation by histopathological examination of biopsy specimens. We viewed the abnormal jejunal mucosa using a newly developed magnifying single-balloon enteroscope (SIF-Y0007). Conventional observation showed leakage of chyle. Read More

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http://dx.doi.org/10.1159/000493578DOI Listing
November 2018

An additional case of Hennekam lymphangiectasia-lymphedema syndrome caused by loss-of-function mutation in ADAMTS3.

Am J Med Genet A 2018 Nov 18. Epub 2018 Nov 18.

Ambry Genetics, Aliso Viejo, California, USA.

Hennekam lymphangiectasia-lymphedema syndrome (HKLLS) is a genetically heterogeneous lymphatic dysplasia with characteristic of facial dysmorphism, neurocognitive impairments, and abnormalities of the pericardium, intestinal tract, and extremities. It is an autosomal recessive condition caused by biallelic mutations in CCBE1 (collagen- and calcium-binding epidermal growth factor domain-containing protein 1) (HKLLS1; OMIM 235510) or FAT4 (HKLLS2; OMIM 616006). CCBE1 acts via ADAMTS3 (a disintegrin and metalloprotease with thrombospondin motifs-3 protease) to enhance vascular endothelial growth factor C signaling. Read More

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http://doi.wiley.com/10.1002/ajmg.a.40633
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http://dx.doi.org/10.1002/ajmg.a.40633DOI Listing
November 2018
4 Reads

Milky Mesentery: Acute Abdomen with Chylous Ascites.

Indian Pediatr 2018 Oct;55(10):909-910

Department of Surgery, University College of Medical Sciences and Guru Teg Bahadur Hospital, Shahdara, Delhi, India.

Background: Clinical presentations of intestinal lymphangiectasia include pitting edema, chylous ascites, pleural effusion, diarrhea, malabsorption and intestinal obstruction.

Case Characteristics: An 8-year-old male child presented to the emergency department with clinical features of peritonitis, raising suspicion of appendicular or small bowel perforation.

Intervention/outcome: Diagnosis of chylous ascites with primary intestinal lymphangiectasia made on laparotomy. Read More

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October 2018
4 Reads

Eculizumab Is Safe and Effective as a Long-term Treatment for Protein-losing Enteropathy Due to CD55 Deficiency.

J Pediatr Gastroenterol Nutr 2018 Nov 8. Epub 2018 Nov 8.

The Genetics Institute, Rambam Health Care Campus.

Objectives: Loss of the complement inhibitor CD55 leads to a syndrome of early-onset protein-losing enteropathy (PLE), associated with intestinal lymphangiectasia and susceptibility to large-vein thrombosis. The in vitro and short-term treatment benefits of eculizumab (C5-inhibitor) therapy for CD55-deficiency have been previously demonstrated. Here we present the 18-months treatment outcomes for 3 CD55-deficiency patients with sustained therapeutic response. Read More

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http://Insights.ovid.com/crossref?an=00005176-900000000-9663
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http://dx.doi.org/10.1097/MPG.0000000000002198DOI Listing
November 2018
4 Reads

Acquired Lymphangiectasia of the Scrotum.

Skinmed 2018 9;16(5):337-339. Epub 2018 Nov 9.

West Bengal Skineplex, Center of Dermatology, Burdwan, West Bengal, India.

A 56-year-old man presented with multiple, skin-colored, raised eruptions of the scrotum that had been present for 2 years. Their onset had been gradual, and they had been increasing in size, resulting in cosmetic disfigurement. A year previously, he had been operated on for a bilateral vaginal hydrocele with partial excision and eversion of the sac (Jabouley method). Read More

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November 2018
6 Reads

Primary Intestinal Lymphangiectasia (Waldmann's disease).

Am J Gastroenterol 2018 Nov 8. Epub 2018 Nov 8.

Department of Pediatric Gastroenterology and Nutrition, School of Medicine, Pontificia Universidad Católica de Chile, Santiago, Chile.

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http://dx.doi.org/10.1038/s41395-018-0413-0DOI Listing
November 2018
7 Reads

Primary intestinal lymphangiectasia and a review of the current literature.

Turk J Gastroenterol 2018 11;29(6):714-716

Department of Internal Medicine, Health Sciences University, İzmir Tepecik Health Practice and Research Center, İzmir, Turkey.

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http://dx.doi.org/10.5152/tjg.2018.18596DOI Listing
November 2018

Cutaneous Lymphangiectasia of Genitalia: A Rare Occurrence.

J Assoc Physicians India 2018 Apr;66(4):60

Senior Resident, Department of Respiratory Medicine, Government Medical College, Kota, Rajasthan.

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Acquired widespread lymphangiectasia mimicking immunobullous disease: A case report.

SAGE Open Med Case Rep 2018 9;6:2050313X18802137. Epub 2018 Oct 9.

Department of Dermatology, MetroHealth Medical Center, Case Western Reserve University, Cleveland, OH, USA.

A 76-year-old Caucasian woman presented with a 3-year history of a recurrent pruritic eruption on the hips, thighs, and under the breasts associated with intermittent lesions resembling vesicles and bullae that failed to respond to topical corticosteroids. She had a history of severe lichen sclerosis et atrophicus, leading to invasive squamous cell carcinoma of the vulva for which she underwent radical vulvectomy and bilateral inguino-femoral lymph node dissection. On physical examination, involving the inframammary breasts, abdomen, hips, and proximal thighs there were multiple erosions with hemorrhagic crust and multiple clustered translucent papules. Read More

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http://journals.sagepub.com/doi/10.1177/2050313X18802137
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http://dx.doi.org/10.1177/2050313X18802137DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6178371PMC
October 2018
2 Reads

Lymphaticovenous anastomosis and resection for genital acquired lymphangiectasia (GAL).

Authors:
H Hara M Mihara

J Plast Reconstr Aesthet Surg 2018 Nov 8;71(11):1625-1630. Epub 2018 Jun 8.

Department of Lymphatic and Reconstructive Surgery, JR Tokyo General Hospital, 2-1-3 Yoyogi, Shibuya-ku, Tokyo, 151-8528, Japan. Electronic address:

The purpose of this paper is to report on the relationship between lymphoscintigraphic findings and the operative results of lymphaticovenous anastomosis (LVA) as well as the resection of genital acquired lymphangiectasia (GAL). Seventeen patients with GAL who underwent lymphoscintigraphy between April 2012 and June 2016 were included in this retrospective study. LVA and GAL resections were performed for 14 patients. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S17486815183016
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http://dx.doi.org/10.1016/j.bjps.2018.05.015DOI Listing
November 2018
3 Reads

Intestinal lymphangiectasia: a rare cause of intussusception in an adolescent.

Ann R Coll Surg Engl 2018 Oct 16:e1-e2. Epub 2018 Oct 16.

Department of Surgical Gastroenterology, Jawaharlal Institute of Post Graduate Medical Education and Research, Pondicherry , Puducherry , India.

Intussusception in adolescents is usually idiopathic in nature. A 17-year-old woman with diffuse large B cell lymphoma presented with signs of intestinal obstruction after initiation of induction chemotherapy. On evaluation, the patient was diagnosed to have ileoileal intussusception with intestinal lymphangiectasia as the lead point. Read More

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https://publishing.rcseng.ac.uk/doi/10.1308/rcsann.2018.0182
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http://dx.doi.org/10.1308/rcsann.2018.0182DOI Listing
October 2018
8 Reads

Magnified single-balloon enteroscopy in the diagnosis of intestinal follicular lymphoma: a case series.

Intest Res 2018 Oct 10;16(4):628-634. Epub 2018 Oct 10.

Department of Medicine, Shiga University of Medical Science, Otsu, Japan.

The objective of this study was to evaluate the magnified endoscopic findings in the diagnosis of follicular lymphoma in the small intestine in comparison with those of intestinal follicular lymphoma and lymphangiectasia. Four patients with follicular lymphoma and 3 with lymphangiectasia in the small intestine were retrospectively analyzed. A prototype magnifying singleballoon enteroscope was used. Read More

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http://irjournal.org/journal/view.php?doi=10.5217/ir.2018.00
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http://dx.doi.org/10.5217/ir.2018.00003DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6223446PMC
October 2018
5 Reads

Acquired Cutaneous Lymphangiectasia Secondary to Cervical Cancer Treatment.

Am J Dermatopathol 2018 Oct 4. Epub 2018 Oct 4.

Department of Dermatology, Chung-Ang University College of Medicine, Seoul, Korea.

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http://dx.doi.org/10.1097/DAD.0000000000001127DOI Listing
October 2018

Pulmonary cysts in smoking-related interstitial fibrosis: a form of pseudocyst secondary to pulmonary interstitial emphysema.

Rev Esp Patol 2018 Oct - Dec;51(4):257-261. Epub 2018 Mar 14.

From the Department of Pneumology, University General Hospital, Valencia, Spain; From the Departement of Medicine. Valencia University, Valencia, Spain.

Smoking-related interstitial fibrosis is a distinct form of fibrosis, found in smokers, which has striking histopathological features. We present a case of pulmonary interstitial fibrosis with cysts in a 58-year-old woman who was a significant active smoker, presenting with a 7 month history of progressive dyspnea. TAC revealed thin-walled pulmonary cysts. Read More

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http://dx.doi.org/10.1016/j.patol.2018.01.005DOI Listing
March 2018
1 Read

Gross and histopathologic findings in sheep with plastic bags in the rumen.

Int J Vet Sci Med 2017 Dec 9;5(2):152-158. Epub 2017 Nov 9.

Department of Public Health, Pharmacology and Toxicology, Faculty of Veterinary Medicine, University of Nairobi, Kenya.

The objective of this study was to evaluate the gross and histo-pathological lesions caused by plastic bags in the rumen of sheep. Sixteen (16) castrated, one-year old Dorper sheep were used for the study. The animals were divided into 4 groups each consisting of 4 sheep. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S23144599173007
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http://dx.doi.org/10.1016/j.ijvsm.2017.08.005DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6137837PMC
December 2017
6 Reads

Atypical Clinical Presentation of Crohn's Disease with Superior Mesenteric Vein Obstruction and Protein-losing Enteropathy.

Intern Med 2018 Sep 12. Epub 2018 Sep 12.

Department of Internal Medicine, National Defense Medical College, Japan.

We herein report a 44-year-old man suffering from systemic edema due to protein-losing enteropathy (PLE) with superior mesenteric vein (SMV) obstruction and development of collateral veins, which subsequently proved to be a chronic result of thrombosis and a complication of Crohn's disease (CD). PLE was supposedly induced by both intestinal erosion and thrombosis-related lymphangiectasia, which was histologically proven in his surgically-resected ileal stenosis. Elemental diet and anti-TNFα agent improved his hypoalbuminemia after surgery. Read More

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http://dx.doi.org/10.2169/internalmedicine.1192-18DOI Listing
September 2018
2 Reads

[Conjunctival lymphangiectasia: Appearance on confocal microscopy and OCT].

J Fr Ophtalmol 2018 Jun 14;41(6):e271-e273. Epub 2018 Jun 14.

Service de dermatologie, hôpital universitaire de Saint-Étienne, 42055 Saint-Étienne cedex 2, France. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S01815512183020
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http://dx.doi.org/10.1016/j.jfo.2017.09.025DOI Listing
June 2018
2 Reads

CT Lymphangiography (CTL) in Primary Intestinal Lymphangiectasia (PIL): A Comparative Study with Intraoperative Enteroscopy (IOE).

Acad Radiol 2018 Jun 6. Epub 2018 Jun 6.

Department of Radiology, Beijing Shijitan Hospital, Capital Medical University, No. 10 Tieyi St, Haidian District, Beijing 100038, China. Electronic address:

Rationale And Objectives: To investigate the clinical feasibility of CT lymphangiography (CTL) in primary intestinal lymphangiectasia (PIL) by comparison with intraoperative enteroscopy (IOE) during exploratory laparotomy.

Materials And Methods: Eleven PIL patients (F/M, two/nine, age range 10-37 years) were recruited in this study, and they were performed IOE during exploratory laparotomy for suspected serious lymphatic-intestinal leakages. All the patients were performed CTL before surgery, and the imaging data were reviewed by two radiologists separately. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S10766332183023
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http://dx.doi.org/10.1016/j.acra.2018.04.023DOI Listing
June 2018
15 Reads

Lymphatic Endothelial Cell in Endemic Bancroftian Filariasis: A Focus on the Lymphatics of the Tunica Vaginalis Testis.

J Trop Med 2018 16;2018:5134670. Epub 2018 May 16.

Núcleo de Ensino, Pesquisa e Assistência em Filariose (NEPAF), Hospital das Clínicas, Universidade Federal de Pernambuco, Recife, PE, Brazil.

Background: In endemic areas, lymphangiectasia is the fundamental alteration to live adult worms which, in adult males, are usually found in the lymphatic vessels of the spermatic cord; accordingly, hydrocele/filaricele is the most common clinical manifestation of bancroftian filariasis. The pathogenic role of the lymphatic endothelial cells (LECs) and the status of mesothelial cells (MCs) samples of the parietal layer (PL) of the tunica vaginalis testis were examined.

Methods: The PL of thirty-two patients, excised for different reasons, was examined by histology and immunohistochemistry using the D2-40 monoclonal antibody for identification of LECs and CK-7 antibody for recognition of mesothelial cells (MCs). Read More

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http://dx.doi.org/10.1155/2018/5134670DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5976995PMC
May 2018
9 Reads

Unique Case of Postural Acquired Lymphangiectasia of the Scrotum Exacerbated by an Erect Position.

Ann Dermatol 2018 Jun 23;30(3):378-379. Epub 2018 Apr 23.

Department of Dermatology, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea.

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https://synapse.koreamed.org/DOIx.php?id=10.5021/ad.2018.30.
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http://dx.doi.org/10.5021/ad.2018.30.3.378DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5929965PMC
June 2018
6 Reads

Cutis Marmorata Telangiectatica Congenita Presenting as a Fetal Hemothorax.

Fetal Diagn Ther 2018 May 23:1-4. Epub 2018 May 23.

Division of Maternal Fetal Medicine, Department of Obstetrics and Gynecology, University of Michigan, Ann Arbor, Michigan, USA.

We report a case of a fetus diagnosed at 28 weeks' gestation with a spontaneous prenatal hemothorax. Fetal intervention consisted of 2 thoracenteses with analysis of the pleural effusion. The pregnancy was further complicated by recurrence of the hemothorax, with subsequent mediastinal shift, hydrops, and nonreassuring antenatal testing requiring delivery at 31 weeks' gestation. Read More

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http://dx.doi.org/10.1159/000488487DOI Listing
May 2018
1 Read

Removal of Peritnoeo-venous-atrial shunt thrombus without cardiopulmonary bypass.

Asian Cardiovasc Thorac Ann 2018 Jun 7;26(5):387-389. Epub 2018 May 7.

5 Department of Interventional Radiology, Sir Charles Gairdner Hospital, Nedlands, Australia.

Thrombus formation is not uncommon in longstanding intracardiac catheters, but formation of a thrombus at the tip of a Peritnoeo-venous-atrial shunt, causing obstruction of the tricuspid valve, is a rare complication and frequently unrecognized. A large intracardiac thrombus causing valve obstruction requires surgical removal with the support of cardiopulmonary bypass which is associated with significant morbidity. We successfully removed a thrombus attached to the tip of peritoneovenous shunt without cardiopulmonary bypass in a 25-year-old man. Read More

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http://journals.sagepub.com/doi/10.1177/0218492318776878
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http://dx.doi.org/10.1177/0218492318776878DOI Listing
June 2018
8 Reads

Successful management of extremely high-output refractory congenital chylothorax with chemical pleurodesis using 4% povidone-iodine and propranolol: a case report.

Clin Case Rep 2018 04 27;6(4):702-708. Epub 2018 Feb 27.

Pediatrics University of Nebraska Medical Center Omaha Nebraska.

First-line therapy for congenital chylothorax is conservative treatment. However, surgical intervention or chemical pleurodesis is required for refractory cases. With all the concerns regarding its complications, povidone-iodin provided a successful management for a high-output congenital chylothorax. Read More

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http://dx.doi.org/10.1002/ccr3.1449DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5889237PMC

[The colonoscopic characteristics of colorectal endometriosis: a single-centered retrospective study].

Zhonghua Nei Ke Za Zhi 2018 Apr;57(4):275-278

Department of Gastroenterology, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medicine Sciences, Beijing 100730, China.

To reinforce the awareness of colorectal endometriosis (EM) in colonoscopy examination. Patients diagnosed as colorectal EM at Peking Union Medical College Hospital between February 2002 and February 2017 were enrolled in this study. The clinical characteristics and endoscopic features of EM lesions were summarized and compared between pathologically positive group and negative group. Read More

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http://dx.doi.org/10.3760/cma.j.issn.0578-1426.2018.04.009DOI Listing

Hennekam Syndrome: A Case Report.

Ann Rehabil Med 2018 Feb 28;42(1):184-188. Epub 2018 Feb 28.

Department of Rehabilitation Medicine, Hanyang University College of Medicine, Seoul, Korea.

Hennekam syndrome is a rare autosomal recessive disorder resulting from malformation of the lymphatic system. The characteristic signs of Hennekam syndrome are lymphangiectasia, lymph edema, facial anomalies, and mental retardation. This is a case in which a patient presented with left-arm lymphedema, facial-feature anomalies, and multiple organ lymphangiectasia consistent with symptoms of Hennekam syndrome. Read More

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http://dx.doi.org/10.5535/arm.2018.42.1.184DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5852224PMC
February 2018

The application value of capsule endoscopy in diagnosing small intestinal carcinoma.

J Cancer Res Ther 2018 Jan;14(1):57-60

Department of Endoscopy, Xinxiang Central Hospital, Henan Province, PR China.

Objective: The aim of this study was to explore the clinical value of capsule endoscopy in the diagnosis of small intestine neoplastic lesions.

Materials And Methods: A retrospective analysis was conducted on the clinical data of 108 patients who underwent capsule endoscopic examination in the Endoscopy Center of Xinxiang Central Hospital from February 2010 to January 2014. The characteristics of different small bowel diseases were observed, and the prevalence rates of different small bowel lesions were calculated. Read More

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http://dx.doi.org/10.4103/jcrt.JCRT_584_17DOI Listing
January 2018
1 Read

Case report of primary intestinal lymphangiectasia diagnosed in an octogenarian by ileal intubation and by push enteroscopy after missed diagnosis by standard colonoscopy and EGD.

Medicine (Baltimore) 2018 Jan;97(3):e9649

Department of Pathology, William Beaumont Hospital.

Rationale: Primary intestinal lymphangiectasia (PIL) is a rare, presumably congenital lesion that is usually diagnosed in patients < 3 years old, is rarely first diagnosed in adulthood, and when first diagnosed in adulthood typically presents with symptoms for many years. Although PIL is often identified by endoscopic abnormalities, it must be emphasized that the jejunoileum/distal duodenum must be intubated for diagnosis because the lesions are present in these regions. This work demonstrates that 1)-PIL can occur in an octogenarian; 2)-shows that the characteristic endoscopic findings are not found at colonoscopy without terminal ileal intubation; and 3)-may be missed at standard EGD without distal duodenal intubation. Read More

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http://Insights.ovid.com/crossref?an=00005792-201801190-0003
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http://dx.doi.org/10.1097/MD.0000000000009649DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5779771PMC
January 2018
12 Reads

Anterior segment and external ocular disorders associated with HIV infections in the era of HAART in Chiang Mai University Hospital, a prospective descriptive cross sectional study.

PLoS One 2018 21;13(2):e0193161. Epub 2018 Feb 21.

Ophthalmology department, Chiang Mai University Hospital, Chiang Mai, Thailand.

Human immunodeficiency virus (HIV) causes impairment to the human immune system which leads to immunocompromised conditions, including ocular complications. Several important HIV-associated disorders may involve the anterior segment, ocular surface, and adnexae organ such as dry eye, blepharitis which reduce quality of life of patients. In present, potent antiretroviral therapies HAART (highly active antiretroviral therapy) has improved the length and quality of life which may lead to an increased prevalence of anterior segment ocular disorders. Read More

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http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0193161PLOS
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5821368PMC
May 2018
12 Reads

Hyperplasia of Lymphoid Follicles and Lymphangiectasia in the Parietal Pleura in Bucillamine-induced Yellow Nail Syndrome.

Intern Med 2018 Jul 9;57(13):1887-1892. Epub 2018 Feb 9.

Department of Pulmonary Medicine and Clinical Immunology, Dokkyo Medical University, Japan.

Yellow nail syndrome (YNS) pleurisy is often difficult to control, and pathological examinations have rarely been reported. We herein report a case of bucillamine-induced YNS in which histopathology of the parietal pleura revealed hyperplasia of the lymphoid follicles and lymphangiectasia. Even after the discontinuation of bucillamine, the pleurisy and lymphedema showed no change. Read More

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https://www.jstage.jst.go.jp/article/internalmedicine/57/13/
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http://dx.doi.org/10.2169/internalmedicine.9679-17DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6064696PMC
July 2018
21 Reads

Unilateral pedal lymphangiography plus computed tomography angiography for location of persistent idiopathic chyle leakage not detectable by ordinary contrast computed tomography.

BMC Urol 2018 Feb 6;18(1). Epub 2018 Feb 6.

Department of Urology, Shanghai Jiao Tong University Medical School Affiliated Ruijin Hospital, 197 Ruijin Er Road, Shanghai, 200025, People's Republic of China.

Background: To identify the value of unilateral pedal lymphangiography (LPG) plus computed tomography angiography (CTA) in accurate depiction of persistent idiopathic chyluria undetectable by ordinary contrast CT.

Methods: Eighteen patients 44-63 years of age with persistent idiopathic chyluria who failed conservative management were included. Ordinary CT had not revealed a chyle leak. Read More

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http://dx.doi.org/10.1186/s12894-018-0323-xDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5801799PMC
February 2018
7 Reads

Nutritional therapy and effect assessment of infants with primary intestinal lymphangiectasia: Case reports.

Medicine (Baltimore) 2017 Dec;96(51):e9240

Department of Nuclear Medicine, Beijing Shijitan Hospital, Capital Medical University, Beijing, China.

Rationale: Intestinal lymphangiectasia (IL) is a rare enteropathy involving the expansion and rupture of intestinal lymphatic channels. Although several reports have studied cases of primary IL (PIL), this condition is very rare, and is even less commonly encountered in infants. This study aimed to investigate the nutritional therapy and effect assessment of chylous reflux disorder caused by PIL in infants. Read More

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http://dx.doi.org/10.1097/MD.0000000000009240DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5758182PMC
December 2017
9 Reads

Surgical Management of Chyloptysis.

Ann Thorac Surg 2018 Feb;105(2):e79-e81

Division of Thoracic Surgery, Mayo Clinic, Rochester, Minnesota.

Chyloptysis is a rare clinical presentation. Diagnosis is challenging and requires recognition of milky-sputum or bronchial casts. We describe a case of chyloptysis secondary to thoracic lymphangiectasia that necessitated surgical ligation of the main thoracic duct and accessory branches. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2017.09.017DOI Listing
February 2018

Acute small intestinal inflammation results in persistent lymphatic alterations.

Am J Physiol Gastrointest Liver Physiol 2018 Mar 14;314(3):G408-G417. Epub 2017 Dec 14.

Inflammation Research Network and Smooth Muscle Research Group, Snyder Institute for Chronic Diseases, Department of Physiology and Pharmacology, Cumming School of Medicine, University of Calgary , Calgary, Alberta , Canada.

Inflammatory bowel disease (IBD) has a complex pathophysiology with limited treatments. Structural and functional changes in the intestinal lymphatic system have been associated with the disease, with increased risk of IBD occurrence linked to a history of acute intestinal injury. To examine the potential role of the lymphatic system in inflammation recurrence, we evaluated morphological and functional changes in mouse mucosal and mesenteric lymphatic vessels, and within the mesenteric lymph nodes during acute ileitis caused by a 7-day treatment with dextran sodium sulfate (DSS). Read More

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http://dx.doi.org/10.1152/ajpgi.00340.2017DOI Listing
March 2018
3 Reads

Vulvar vesicles in an elderly female: cutaneous manifestation of a past malignancy.

Am J Obstet Gynecol 2018 Apr 23;218(4):455-456. Epub 2017 Dec 23.

Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.

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http://dx.doi.org/10.1016/j.ajog.2017.12.212DOI Listing
April 2018
4 Reads
4.700 Impact Factor

[Clinical analysis of intestinal lymphangiectasia in 47 children].

Zhonghua Er Ke Za Zhi 2017 Dec;55(12):937-941

Department of Gastroenterology, Beijing Children's Hospital Affiliated to Capital Medical University, Beijing 100045, China.

To analyze the clinical manifestations, diagnosis, treatment and prognosis of intestinal lymphangiectasia (IL) in children in order to improve the skills of diagnosis and treatment of IL. Clinical manifestations, laboratory findings, gastroscopic findings, histopathological examinations and lymphatic radionuclide imaging assessments were analyzed retrospectively among 47 IL patients who were hospitalized in the Gastroenterology Department of Beijing Children's Hospital Affiliated to Capital Medical University from June 2007 to December 2015. All patients were followed up by telephone. Read More

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http://dx.doi.org/10.3760/cma.j.issn.0578-1310.2017.12.014DOI Listing
December 2017
37 Reads

Lymphangiomatosis involving the pulmonary and extrapulmonary lymph nodes and surrounding soft tissue: A rare case report.

Medicine (Baltimore) 2017 Dec;96(49):e9032

aDepartment of ENT, Children's Medical Center, Shanghai Jiao Tong University, ShanghaibDepartment of Pathology, Shanghai Tongji Hospital, Tongji Hospital Affiliated to Tongji University, ShanghaicDepartment of Pathology, Chongqing Medical University, ChongqingdDepartment of Pathology, Shanghai Pulmonary Hospital, Tongji University School of Medicine, Shanghai, China.

Background: Diffuse pulmonary lymphangiomatosis (DPL) mainly affects the lung and pleura. There are very few pathological reports of lung damage accompanied by diffuse involvement of the extrapulmonary lymph nodes and surrounding soft tissue. The clinicopathological significance of coexistence of pulmonary and extrapulmonary lesions is unknown. Read More

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http://dx.doi.org/10.1097/MD.0000000000009032DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5728910PMC
December 2017
6 Reads

Lymphangiectasia.

Clin Exp Optom 2018 May 12;101(3):418-419. Epub 2017 Dec 12.

School of Optometry and Vision Science, Queensland University of Technology, Brisbane, Queensland, Australia.

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http://doi.wiley.com/10.1111/cxo.12647
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http://dx.doi.org/10.1111/cxo.12647DOI Listing
May 2018
12 Reads

Benign mesothelial nodules reflux within acquired cutaneous lymphangiectasia associated with huge ovarian clear cell carcinoma.

Pathol Int 2018 01 8;68(1):53-55. Epub 2017 Dec 8.

Department of Pathology and Laboratory Medicine, Kanazawa Medical University, Ishikawa.

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http://dx.doi.org/10.1111/pin.12619DOI Listing
January 2018
5 Reads

An approach to familial lymphoedema.

Clin Med (Lond) 2017 Dec;17(6):552-557

Department of Clinical Genetics, St Georges Hospital and St George's, University of London, London, UK.

Lymphoedema is the build-up of lymphatic fluid leading to swelling in the tissues. Most commonly it affects the peripheries. Diagnosis is based on clinical assessment and imaging with lymphoscintigraphy. Read More

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http://www.clinmed.rcpjournal.org/lookup/doi/10.7861/clinmed
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http://dx.doi.org/10.7861/clinmedicine.17-6-552DOI Listing
December 2017
7 Reads

[Primary intestinal lymphangiectasia associated with follicular lymphoma: one case report].

Authors:
Y Y Wu X Lai

Zhonghua Xue Ye Xue Za Zhi 2017 Oct;38(10):900-901

Department of Hematology. The First People's Hospital of Yunnan, Kunming 650032, China.

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http://dx.doi.org/10.3760/cma.j.issn.0253-2727.2017.10.016DOI Listing
October 2017
1 Read

Transmission electron microscopy helpfulness in Whipple's disease masked by immunosuppressant therapy for arthritis.

APMIS 2018 Jan 20;126(1):92-96. Epub 2017 Nov 20.

Section of Pathology, Department of Emergency and Organ Transplantation, University 'Aldo Moro' of Bari, Bari, Italy.

A 61-year-old woman received a diagnosis of undifferentiated non-erosive arthritis in 2010 and assumed methotrexate and steroids in 2014. After 1 year, she experienced watery diarrhea, vomiting, fever, weight loss, and severe hypoalbuminemia, thus being admitted into our Unit. Esophagogastroduodenoscopy showed duodenal lymphangiectasia and duodenal biopsy samples several foamy PAS-positive macrophages and villous subtotal atrophy. Read More

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http://dx.doi.org/10.1111/apm.12782DOI Listing
January 2018
24 Reads

Correlation between the FCEAI and diagnostic parameters in chronic enteropathies in 147 cats (2006-2012).

Tierarztl Prax Ausg K Kleintiere Heimtiere 2017 Nov 3;45(6). Epub 2017 Nov 3.

Dr. Stefanie Mitze, Tierklinik Haar, Keferloher Strasse 25, 85540 Haar, Email:

Objective: The Feline Chronic Enteropathy Activity Index (FCEAI) has been established as a quantitative index for disease activity in chronic enteropathies in cats. A definite diagnosis is aimed at histology with initial exclusion of extraintestinal causes by laboratory examinations, diagnostic imaging and endoscopy. The study aimed to examine diagnostic parameters and FCEAI in chronic gastroenteropathies. Read More

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http://dx.doi.org/10.15654/TPK-170089DOI Listing
November 2017
17 Reads

Evaluation of lymphatic vessel dilatations by anterior segment swept-source optical coherence tomography: case report.

BMC Ophthalmol 2017 Oct 23;17(1):194. Epub 2017 Oct 23.

Faculty of Medicine Department of Ophthalmology, Semmelweis University, Budapest, Hungary.

Background: Conjunctival lymphangiectasia is a rare condition presumably caused by the obstruction of lymphatic channels or by an abnormal connection between conjunctival lymphatic and blood vessels. Diagnosis is based on clinical appearance and histology. We report a case of conjunctival lymphangiectasia in which anterior segment optical coherence tomography (OCT) was used to assist the diagnosis and the planning of the biopsy location. Read More

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http://dx.doi.org/10.1186/s12886-017-0588-yDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5654095PMC
October 2017
13 Reads

Loss of ADAMTS3 activity causes Hennekam lymphangiectasia-lymphedema syndrome 3.

Hum Mol Genet 2017 11;26(21):4095-4104

Human Molecular Genetics, de Duve Institute, University of Louvain, 1200 Brussels, Belgium.

Primary lymphedema is due to developmental and/or functional defects in the lymphatic system. It may affect any part of the body, with predominance for the lower extremities. Twenty-seven genes have already been linked to primary lymphedema, either isolated, or as part of a syndrome. Read More

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http://dx.doi.org/10.1093/hmg/ddx297DOI Listing
November 2017
35 Reads

Primary Intestinal Lymphangiectasia (Waldmann's Disease) Presenting with Chylous Effusions in a 15-Year-Old.

J Clin Diagn Res 2017 Aug 1;11(8):OD17-OD18. Epub 2017 Aug 1.

Professor, Department of Medicine, JIPMER, Puducherry, India.

Primary Intestinal Lymphangiectasia (PIL) is a rare disease of unknown aetiology which presents in the paediatric age group with anasarca, diarrhoea, hypoproteinaemia, lymphoedema and chylous effusions. Tuberculosis, filariasis, chest trauma, malignancies and haematological disorders usually contribute to most cases of secondary lymphangiectasia and chylous effusions. We hereby describe a case of PIL presenting with chylous effusions which remained undiagnosed for eight years. Read More

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http://dx.doi.org/10.7860/JCDR/2017/29055.10522DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5620829PMC
August 2017
8 Reads

[Diagnostic and therapeutic approach to chronic inflammatory enteropathies in dogs].

Tierarztl Prax Ausg K Kleintiere Heimtiere 2017 10 21;45(5):317-327. Epub 2017 Sep 21.

Carolin Erdmann, Klinik für Kleintiere, der Universität Leipzig, An den Tierkliniken 23, 04103 Leipzig, E-Mail:

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http://dx.doi.org/10.15654/TPK-170366DOI Listing
October 2017
21 Reads

Cutaneous alternariosis in an immunocompromised dog successfully treated with cold plasma and cessation of immunosuppressive medication.

Tierarztl Prax Ausg K Kleintiere Heimtiere 2017 Oct 13;45(5):337-343. Epub 2017 Sep 13.

Janine Classen, Clinic of Small Animal Medicine, Centre for Clinical Veterinary Medicine, Ludwig-Maximilians University, Veterinärstraße 13, 80539 Munich, Germany, Email:

A cutaneous infection with Alternaria spp. was diagnosed in a 2-year-old male intact Irish setter dog, presenting with multifocal papules, plaques and ulcerations involving all four distal limbs, shoulder blades, scrotum, pinnae and nasal mucous membranes. The dog had been treated for inflammatory bowel disease and lymphangiectasia with immunosuppressive doses of cyclosporine and prednisolone for approximately 3 months. Read More

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http://dx.doi.org/10.15654/TPK-160851DOI Listing
October 2017
14 Reads