108 results match your criteria Lown-Ganong-Levine Syndrome


Perioperative management of patients with pre-excitation syndromes.

Rom J Anaesth Intensive Care 2018 Oct;25(2):131-147

Department of Anaesthesiology, 401 Military Hospital, Athens, Greece.

Patients with pre-excitation abnormalities are at a high risk for life-threatening perioperative arrhythmias. In Wolff-Parkinson-White syndrome, the anaesthetics used for invasive diagnostic testing/ablation, should not affect cardiac electrophysiology; propofol, sevoflurane, fentanyl, sufentanil, alfentanil are suitable. In non-ablative surgery, propofol, sevoflurane, isoflurane, fentanyl, alfentanil, sufentanil have been used safely. Read More

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October 2018

A Case of Lown-Ganong-Levine Syndrome: Due to an Accessory Pathway of James Fibers or Enhanced Atrioventricular Nodal Conduction (EAVNC)?

Am J Case Rep 2018 Mar 18;19:309-313. Epub 2018 Mar 18.

Heart Institute, Joe DiMaggio Children's Hospital, Hollywood, FL, USA.

BACKGROUND Lown-Ganong-Levine syndrome, includes a short PR interval, normal QRS complex, and paroxysmal tachycardia. The pathophysiology of this syndrome includes an accessory pathway connecting the atria and the atrioventricular (AV) node (James fiber), or between the atria and the His bundle (Brechenmacher fiber). Similar features are seen in enhanced atrioventricular nodal conduction (EAVNC), with the underlying pathophysiology due to a fast pathway to the AV node, and with the diagnosis requiring specific electrophysiologic criteria. Read More

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[53-year-old woman with paroxysmal tachycardia].

Dtsch Med Wochenschr 2013 Jan 8;138(3):89-90. Epub 2013 Jan 8.

Klinik III für Innere Medizin, Herzzentrum der Universität zu Köln.

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January 2013

A novel gain-of-function KCNJ2 mutation associated with short-QT syndrome impairs inward rectification of Kir2.1 currents.

Cardiovasc Res 2012 Mar 8;93(4):666-73. Epub 2011 Dec 8.

Department of Cardiovascular Medicine, Kyoto University Graduate School of Medicine, 54 Shogoin Kawahara-cho, Sakyo-ku, Kyoto 606-8507, Japan.

Aims: Short-QT syndrome (SQTS) is a recently recognized disorder associated with atrial fibrillation (AF) and sudden death due to ventricular arrhythmias. Mutations in several ion channel genes have been linked to SQTS; however, the mechanism remains unclear. This study describes a novel heterozygous gain-of-function mutation in the inward rectifier potassium channel gene, KCNJ2, identified in SQTS. Read More

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Country cardiograms case 41.

Can J Rural Med 2011 ;16(4):133, answer pg 141-2

Department of Medicine, Dalhousie University, Halifax, NS. brent .mcgrath

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January 2012

Anaesthetic management of a patient with Lown Ganong Levine syndrome-a case report.

Authors:
M K Sharma S Misra

Med J Armed Forces India 2011 Jul 7;67(3):285-7. Epub 2011 Aug 7.

Senior Advisor (Anaesthesiology), MH, Meerut Cantt.

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Lown-Ganong-Levine syndrome in a 3-month-old infant with isolated left ventricular noncompaction.

Pediatr Cardiol 2010 Feb 27;31(2):274-6. Epub 2009 Oct 27.

Division of Cardiology, Department of Pediatrics, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

This report describes a 3-month-old boy with isolated left ventricular noncompaction admitted to a medical facility due to heart failure and dysrhythmia. His electrocardiogram showed a short PR interval and a normal QRS complex after abortion of supraventricular tachycardia in favor of Lown-Ganong-Levine syndrome or enhanced atrioventricular nodal conduction. Read More

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February 2010

Electrocardiographic changes in patients with spontaneous pneumothorax.

J Physiol Pharmacol 2008 Dec;59 Suppl 6:361-73

Department of Internal Medicine, Pneumology and Allergology, Warsaw Medical University, Warsaw, Poland.

The aim of the study was to evaluate the prevalence of electrocardiography (ECG) abnormalities in subjects with spontaneous pneumothorax. Forty consecutive patients (mean age 43.7 +/-19. Read More

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December 2008

Ablation therapy of supraventricular tachycardia in elderly persons.

Am J Geriatr Cardiol 2005 Jan-Feb;14(1):20-5

Department of Cardiovascular Disease, Florida Hospital, Orlando, FL,USA.

Ablation of supraventricular tachycardia in elderly persons presents a challenging problem to electrophysiologists. Friable cardiac structures, prone to catheter perforation, comorbid cardiovascular disease, and the propensity to develop atrial fibrillation and thromboembolic complications, place these patients at high risk. Newer techniques for cardiac mapping and ablation, the establishment of precise ablation lines, and safer approaches to the ablation mechanism (particularly for atrial fibrillation) are presented in this review. Read More

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Lown-Ganong-Levine syndrome in pregnancy.

Obstet Gynecol 2003 Dec;102(6):1393-5

Department of Obstetrics and Gynecology, St. Mary's Health Center, Saint Louis University School of Medicine, St. Louis, Missouri 63117, USA.

Background: Lown-Ganong-Levine syndrome is characterized by paroxysmal supraventricular tachycardia, a short PR interval, and normal QRS.

Case: A gravida 3, para 2 was diagnosed with Lown-Ganong-Levine syndrome at 16 weeks' gestation after an episode of chest pain and shortness of breath. She was hospitalized and treated with digoxin, and her symptoms subsided. Read More

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December 2003

[Atypical symptoms of Fabry's disease: sudden bilateral deafness, lymphoedema and Lown-Ganong-Levine syndrome].

Pol Arch Med Wewn 2002 Nov;108(5):1085-90

II Katedra Chorób Wewnetrznych, Collegium Medicum UJ Kraków.

A 40-year-old man with Fabry disease, confirmed by decreased leukocyte alpha-galactosidase A activity in 2001, complained of sudden bilateral deafness, as evidenced by clinical history and audiometry. Magnetic resonance of the brain revealed features typical of Fabry disease. Other clinical manifestations of the disease included: angiokeratoma, mild proteinuria with normal renal function, lymphoedema of the lower limbs, pre-excitation syndrome, myocardial hypertrophy. Read More

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November 2002

[Ventricular pre-excitation: electrophysiopathology, criteria for interpretation and clinical diagnosis. References for geriatrics].

Minerva Cardioangiol 2001 Feb;49(1):47-73

Istituto di Clinica Medica Generale e Terapia Medica, Università degli Studi, Trieste, Italy.

The authors review the state-of-the-art on ventricular pre-excitation in medical and arrhythmological literature in order to facilitate the recognition of the various clinical forms, like classic and occult Wolff Parkinson withe syndrome and Lown Ganong Levine syndrome. A historical introduction reviews our electrophysiopathological knowledge of the electrical activation and conduction of ventricular pre-excitation compared to normal, starting from the anatomic discovery of conduction pathways to the possible use of transesophageal electrostimulation and endocavity mapping to study electric potentials. Avantgarde technologies have also been developed to eliminate anomalous pathways firstly by using a direct current dirscharge and secondly radiofrequency. Read More

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February 2001

Ventricular preexcitation in children and young adults: atrial myocarditis as a possible trigger of sudden death.

Circulation 2001 Jan;103(2):269-75

Department of Pathology, University of Padua Medical School, Padua, Italy.

Background: Sudden death (SD) in ventricular preexcitation (VP) syndrome is believed to be the result of atrial fibrillation with rapid ventricular response over the accessory pathway. Previous reports are anecdotal and often lack autopsy validation.

Methods And Results: Prevalence and clinicopathological features of VP were investigated in a series of 273 SDs in children and young adults (aged Read More

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January 2001

Continuous vectorcardiographic monitoring of ischemia during coronary angioplasty in patients with bundle-branch block.

Coron Artery Dis 1999 Oct;10(7):501-7

Clinical Experimental Research Laboratory, Sahlgrenska University Hospital, Ostra, Sweden.

Background: Patients with the combination of bundle-branch block and ischemic heart disease have a poor outcome. There is no established criterion for detection of transient ischemia when bundle-branch block is present.

Objective: To elucidate vectorcardiographic changes during coronary angioplasty of patients with bundle-branch block. Read More

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October 1999

High incidence of pre-excitation syndrome in Japanese families with Leber's hereditary optic neuropathy.

Clin Genet 1996 Dec;50(6):535-7

Department of Ophthalmology, Keio University School of Medicine, Tokyo, Japan.

Cardiac conduction abnormalities have been reported in families with Leber's hereditary optic neuropathy (LHON). The pre-excitation syndrome Wolff-Parkinson-White syndrome or Lown-Ganong-Levine syndrome, is reportedly common in Finns with LHON, being seen in 14 (9%) of the 163 individuals with mitochondrial DNA (mtDNA) mutations. While this syndrome is thought to be rare in other ethnic groups with LHON, the present study of 35 Japanese LHON families confirmed that it is also relatively common among Japanese families, being seen in 5 (8%) of the 63 individuals with mtDNA mutations. Read More

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December 1996

Clinical and evolutive aspects in ventricular preexcitation syndromes in child.

Rev Med Chir Soc Med Nat Iasi 1996 Jul-Dec;100(3-4):95-8

1st Clinic of Pediatrics, University of Medicine and Pharmacy, Iaşi.

Ventricular preexcitation syndromes (VPS) are very important between cardiac rhythm disturbances in childhood, because their presence can change the clinical and ECG picture and thus the treatment can be very difficult. The authors studied 58 cases of VPS in children (2 weeks-15 years old) admitted in a period of 3 years. The surface ECG showed VPS aspects: in 30% of cases we noticed WPW syndrome type B and the rest presented VPS with Mahaim pathways and Lown-Ganong-Levine syndrome. Read More

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[Lown-Ganong-Levine syndrome].

Authors:
N Toshida K Hirao

Ryoikibetsu Shokogun Shirizu 1996 (12):196-8

First Department of Internal Medicine, Tokyo Medical and Dental University.

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[Use-dependence of propafenone. Clinical demonstration of the hypothesis of modulated receptors].

Medicina (B Aires) 1995 ;55(1):33-8

División Cardiología, Hospital Municipal Dr. Cosme Argerich, Buenos Aires, Argentina.

Unlabelled: The aim of this study was to assess use-dependence in patients with ventricular premature contractions (VPC's) treated with propafenone, by means of the increase in heart rate using transesophageal atrial pacing. It was also analyzed whether this phenomenon was related to the antiarrhythmic effect. Fifteen patients with more than 30 symptomatic VPC's/sour were evaluated. Read More

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October 1995

Enhanced A-V nodal conduction (Lown-Ganong-Levine syndrome) by congenitally hypoplastic A-V node.

Eur Heart J 1992 Nov;13(11):1579-84

Department of Cardiology, City Hospital, Vicenza, Italy.

The basic anatomical substrate of enhanced A-V nodal conduction, manifesting or not as Lown-Ganong-Levine syndrome, is still a controversial issue. We describe the case of a 34-year-old man who presented episodes of ventricular fibrillation. Electrophysiological studies showed that the AH interval was 55 ms, and increased by only 20 ms at paced cycle lengths of 300 ms; atrial pacing induced atrial fibrillation, with a shortest RR interval of 240 ms. Read More

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November 1992

The preexcitation syndrome: epidemiological and genetic study.

Int J Cardiol 1992 May;35(2):181-6

Department of Internal Medicine, University Hospital, Rebro Medical Faculty, University of Zagreb, Croatia, Yugoslavia.

A sample of 4210 subjects of both sexes aged 35-54 years was examined, chosen at random from six regions of Croatia. An electrocardiogram at rest was performed in all subjects and changes analyzed by the Minnesota code. A short P-R interval together with a widening QRS complex and a delta wave was found in 0. Read More

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Pulmonary developmental anomaly associated with Klippel-Feil syndrome and anomalous atrioventricular conduction.

Chest 1992 Apr;101(4):1157-8

Clinical Research Centre, University of Delhi, India.

We report the findings in a patient with Klippel-Feil syndrome and associated agenesis of right upper and middle lobes, hypoplasia of the right lower lobe of the lung, and Lown-Ganong-Levine syndrome. To our knowledge, such an association has not been previously described. Read More

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[Disorders of cardiac rhythm in combined ventricular pre-excitation syndrome and primary mitral valve prolapse].

Ter Arkh 1990 ;62(4):38-43

Primary prolapse of the mitral valve was diagnosed in 27 (11.7%) out of 230 patients with preexcitation syndrome: 10 of them presented with Wolff-Parkinson-White syndrome, 15 with Clerc-Lévy-Critesco syndrome, and two patients with combination of both syndromes. Preexcitation syndrome combined with mitral valve prolapse manifested itself by different disorders of the cardiac rhythm, mainly by the supraventricular forms: by PST in 17, nonparoxysmal tachycardia in 1, atrial fibrillation paroxysms in 7, sinus tachycardia in 2, supraventricular extrasystole in 3, pacemaker migration in the atria in 1 patient. Read More

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October 1990

[The inheritance of the ventricular pre-excitation syndrome].

Authors:
I G Fomina

Ter Arkh 1990 ;62(10):84-8

Medico-genetic studies including preparation of the family pedigree, interviews, examinations, electro- and echocardiography were carried out in the families of 75 patients with pre-excitation syndrome (PES). Of these, 35 patients presented with Wolff-Parkinson-White (WPW) syndrome and 40 with Clerc-Lévy-Cristesco (CLC) syndrome. The studies made in possible to define the autosomal-dominant type of the syndrome or PES inheritance and to diagnose for the first time WPW syndrome in 3, PES in 1, CLC syndrome in 32 and CLC phenomenon in 89 persons out of 233 relatives of the first and second degree kinship. Read More

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