675 results match your criteria Imaging in Restrictive Cardiomyopathy


Indications and diagnostic yield of endomyocardial biopsies for unexplained cardiomyopathy, a single center experience.

Acta Cardiol 2019 Jan 16:1-9. Epub 2019 Jan 16.

a Department of Cardiology , Ziekenhuis Oost-Limburg , Genk , Belgium.

Background: Endomyocardial biopsies (EMBs) remain the golden standard to diagnose underlying pathophysiologic process in heart failure (HF), when potential therapeutic decisions cannot be made by non-invasive techniques. However, changes in the field of non-invasive diagnostic testing might have an impact on the need for performing an EMB in certain scenarios.

Methods: We performed a retrospective analysis of consecutive EMBs performed in a single, non-academic, tertiary-care centre. Read More

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http://dx.doi.org/10.1080/00015385.2018.1561597DOI Listing
January 2019
2 Reads

Noninvasive Multimodality Imaging for the Diagnosis of Constrictive Pericarditis.

Circ Cardiovasc Imaging 2018 Nov;11(11):e007878

Center for the Diagnosis and Treatment of Pericardial Diseases, Heart and Vascular Institute (B.X., V.M., A.K., P.C.C., A.L.K.), Cleveland Clinic, OH.

There is a need to review the multimodality imaging techniques, as well as the emerging role of the newer noninvasive imaging modalities in the field of constrictive pericarditis (CP). Therefore, the aim of this review is to summarize the current available techniques that are useful for the diagnosis and differentiation of CP from restrictive cardiomyopathy. Also, we provide illustrative images and videos of typical CP noninvasive imaging findings, as well as a diagnostic and management algorithm. Read More

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http://dx.doi.org/10.1161/CIRCIMAGING.118.007878DOI Listing
November 2018
10 Reads
5.316 Impact Factor

Role of cardiovascular imaging for the diagnosis and prognosis of cardiac amyloidosis.

Open Heart 2018 26;5(2):e000881. Epub 2018 Sep 26.

Cardiology Department, Division of Internal Medicine, University of Texas MD Anderson Cancer Center, Houston, Texas, USA.

Cardiac amyloidosis (CA) describes the pathological process of amyloid protein deposition in the extracellular space of the myocardium. Unfortunately, the diagnosis of CA is often made late and when the disease process is advanced. However, advances in cardiovascular imaging have allowed for better prognostication and establishing diagnostic pathways with high sensitivity and specificity. Read More

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http://dx.doi.org/10.1136/openhrt-2018-000881DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6173267PMC
September 2018
7 Reads

Diastolic dysfunction evaluated by cardiac magnetic resonance: the value of the combined assessment of atrial and ventricular function.

Eur Radiol 2019 Mar 20;29(3):1555-1564. Epub 2018 Aug 20.

Dipartimento di Medicina Clinica e Sperimentale, University of Messina, Messina, Italy.

Objectives: We sought to evaluate the role of cardiac magnetic resonance imaging (CMR) in the evaluation of diastolic function by a combined assessment of left ventricular (LV) and left atrial (LA) function in a cohort of subjects with various degrees of diastolic dysfunction (DD) detected by echocardiography.

Methods: Forty patients with different stages of DD and 18 healthy controls underwent CMR. Short-axis cine steady-state free precession images covering the entire LA and LV were acquired. Read More

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http://dx.doi.org/10.1007/s00330-018-5571-3DOI Listing
March 2019
14 Reads

Electrocardiogram and Imaging: An Integrated Approach to Arrhythmogenic Cardiomyopathies.

Card Electrophysiol Clin 2018 06;10(2):413-429

Multimodality Cardiac Imaging Section, Policlinico San Donato, San Donato Milanese, Piazza Edmondo Malan, 2, 20097 San Donato Milanese MI, Italy.

Cardiovascular imaging has radically changed the management of patients with arrhythmogenic cardiomyopathies. This article focuses on the role of echocardiography and MRI in the diagnosis of these structural diseases. Cardiomyopathies with hypertrophic pattern (hypertrophic cardiomyopathy, restrictive cardiomyopathies, amyloidosis, Anderson-Fabry disease, and sarcoidosis), cardiomyopathies with dilated pattern, inflammatory cardiac diseases, and right ventricular arrhythmogenic cardiomyopathy are analyzed. Read More

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http://dx.doi.org/10.1016/j.ccep.2018.02.011DOI Listing
June 2018
6 Reads

Creation of a restrictive atrial communication in heart failure with preserved and mid-range ejection fraction: effective palliation of left atrial hypertension and pulmonary congestion.

Clin Res Cardiol 2018 Sep 16;107(9):845-857. Epub 2018 Apr 16.

Hessen Pediatric Heart Center, Justus Liebig University Clinic Giessen, Giessen, Germany.

Background: Left atrial decompression is considered in patients with symptomatic heart failure with preserved ejection fraction (HFpEF). We aimed to evaluate the feasibility and efficacy of transcatheter generation of a restrictive atrial septum communication to manage HFpEF from infancy to adulthood with cardiomyopathy and congenital heart defect.

Methods And Results: From June 2009 to December 2016, 24 patients (50% with an age less than 16 years) with HFpEF were palliated; NYHA-/Ross class IV (n = 10); median systemic ventricular ejection fraction 64 (range 35-78) %. Read More

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http://dx.doi.org/10.1007/s00392-018-1255-xDOI Listing
September 2018
35 Reads

Incremental Value of the Tissue Motion of Annular Displacement Derived From Speckle-Tracking Echocardiography for Differentiating Chronic Constrictive Pericarditis From Restrictive Cardiomyopathy.

J Ultrasound Med 2018 Nov 30;37(11):2637-2645. Epub 2018 Mar 30.

Department of Cardiovascular Ultrasound, First Hospital of China Medical University, Shenyang, China.

Objectives: The tissue motion of annular displacement provides an accurate and rapid assessment of left ventricular (LV) systolic function. However, it has rarely been used in patients with chronic constrictive pericarditis and restrictive cardiomyopathy. This study aimed to assess the differences in LV systolic function in patients with constrictive pericarditis and restrictive cardiomyopathy using tissue motion of annular displacement derived from speckle-tracking echocardiography. Read More

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http://dx.doi.org/10.1002/jum.14625DOI Listing
November 2018
3 Reads

Loeffler endocarditis as a rare cause of heart failure with preserved ejection fraction: A case report and review of literature.

Medicine (Baltimore) 2018 Mar;97(11):e0079

Department of Cardiology, The First Hospital of Jilin University, Changchun, China.

Rationale: Hypereosinophilic syndrome (HES) is a rare disease characterized by hypereosinophilia and its ensuing organ damage. Cardiac involvement is divided into 3 chronological stages: an acute necrotic stage; a thrombus formation stage; and a fibrotic stage. Infiltration of the myocardium by eosinophilic cells followed by endomyocardial fibrosis is known as "Loeffler endocarditis. Read More

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http://dx.doi.org/10.1097/MD.0000000000010079DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5882404PMC
March 2018
13 Reads

Assessment of cerebral microbleeds by susceptibility-weighted imaging at 3T in patients with end-stage organ failure.

Radiol Med 2018 Jun 17;123(6):441-448. Epub 2018 Feb 17.

Department of Diagnostic and Therapeutic Services, IRCCS-ISMETT (Mediterranean Institute for Transplantation and Advanced Specialized Therapies), Palermo, Italy.

Purpose: Cerebral microbleeds (CMBs) are small rounded lesions representing cerebral hemosiderin deposits surrounded by macrophages that results from previous microhemorrhages. The aim of this study was to review the distribution of cerebral microbleeds in patients with end-stage organ failure and their association with specific end-stage organ failure risk factors.

Materials And Methods: Between August 2015 and June 2017, we evaluated 15 patients, 9 males, and 6 females, (mean age 65. Read More

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http://dx.doi.org/10.1007/s11547-018-0863-xDOI Listing
June 2018
4 Reads

The Cardiomyopathy Registry of the EURObservational Research Programme of the European Society of Cardiology: baseline data and contemporary management of adult patients with cardiomyopathies.

Eur Heart J 2018 May;39(20):1784-1793

EURObservational Research Programme, European Society of Cardiology, 2035 Route des colles, CS 80179 Biot, 06903 Sophia-Antipolis Cedex, France.

Aims: The Cardiomyopathy Registry of the EURObservational Research Programme is a prospective, observational, and multinational registry of consecutive patients with four cardiomyopathy subtypes: hypertrophic cardiomyopathy (HCM), dilated cardiomyopathy (DCM), arrhythmogenic right ventricular cardiomyopathy (ARVC), and restrictive cardiomyopathy (RCM). We report the baseline characteristics and management of adults enrolled in the registry.

Methods And Results: A total of 3208 patients were enrolled by 69 centres in 18 countries [HCM (n = 1739); DCM (n = 1260); ARVC (n = 143); and RCM (n = 66)]. Read More

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http://dx.doi.org/10.1093/eurheartj/ehx819DOI Listing
May 2018
22 Reads

Hydroxychloroquine-induced restrictive cardiomyopathy: a case report.

Postgrad Med J 2018 03 20;94(1109):185-186. Epub 2018 Jan 20.

Department of Medicine, Division of Cardiology, Bronx-Lebanon Hospital Center, Bronx, New York, USA.

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http://dx.doi.org/10.1136/postgradmedj-2017-135236DOI Listing
March 2018
6 Reads

Dysregulated autophagy in restrictive cardiomyopathy due to Pro209Leu mutation in BAG3.

Mol Genet Metab 2018 03 6;123(3):388-399. Epub 2018 Jan 6.

Department of Child Neurology, Justus Liebig University Giessen, 35392 Giessen, Germany.

Myofibrillary myopathies (MFM) are hereditary myopathies histologically characterized by degeneration of myofibrils and aggregation of proteins in striated muscle. Cardiomyopathy is common in MFM but the pathophysiological mechanisms are not well understood. The BAG3-Pro209Leu mutation is associated with early onset MFM and severe restrictive cardiomyopathy (RCM), often necessitating heart transplantation during childhood. Read More

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http://dx.doi.org/10.1016/j.ymgme.2018.01.001DOI Listing
March 2018
2 Reads

Restrictive Mitral Annuloplasty With or Without Papillary Muscle Approximation for Functional Mitral Regurgitation.

J Heart Valve Dis 2017 07;26(4):447-455

Department of Cardiovascular Surgery, Osaka University Graduate School of Medicine, Suita City, Osaka, Japan.

Background And Aim Of The Study: The impact of adding papillary muscle approximation (PMA) to restrictive mitral annuloplasty (RMA) on postoperative left ventricular (LV) function is unknown. Changes in LV function parameters and clinical outcome were evaluated following RMA with and without PMA in patients with clinically relevant functional mitral regurgitation (FMR).

Methods: A total of 176 patients with advanced cardiomyopathy underwent RMA either with (n = 59) or without (n = 117) PMA. Read More

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July 2017
12 Reads

Restrictive Cardiomyopathies: The Importance of Noninvasive Cardiac Imaging Modalities in Diagnosis and Treatment-A Systematic Review.

Radiol Res Pract 2017 15;2017:2874902. Epub 2017 Nov 15.

Department of Cardiology, Chatzikosta General Hospital, Ioannina, Greece.

Restrictive cardiomyopathy (RCM) is the least common among cardiomyopathies. It can be idiopathic, familial, or secondary to systematic disorders. Marked increase in left and/or right ventricular filling pressures causes symptoms and signs of congestive heart failure. Read More

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http://dx.doi.org/10.1155/2017/2874902DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5705874PMC
November 2017
6 Reads

Discordant Findings on 18F-NaF and 99mTc-HDP Bone Scans in a Patient With ATTR Cardiac Amyloidosis.

Clin Nucl Med 2018 Mar;43(3):e89-e92

Cardiac amyloidosis is an important cause of restrictive cardiomyopathy and congestive heart failure. Bone scintigraphy with [Tc]hydroxymethylene diphosphonate (Tc-HDP) and [F]sodium fluoride (F-NaF) have been investigated in the noninvasive diagnosis of transthyretin (ATTR)-related cardiac amyloidosis. We present a case of a 76-year-old man with metastatic prostate cancer who underwent Tc-HDP bone scintigraphy with an incidental finding of diffuse left ventricular abnormal uptake suggesting ATTR cardiac amyloidosis. Read More

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http://dx.doi.org/10.1097/RLU.0000000000001933DOI Listing
March 2018
8 Reads

Restrictive Cardiomyopathy or Constrictive Pericarditis: An Unresolved Conundrum.

World J Pediatr Congenit Heart Surg 2018 05 27;9(3):360-363. Epub 2017 Feb 27.

2 Department of Paediatric Cardiac Surgery, Cardiopulmonary Transplant Unit, Freeman Hospital, Newcastle Upon Tyne NE7 7DN, United Kingdom.

Cardiomyopathy may have a variety of causes and may lead to significant morbidity. Often, there is no "perfect" treatment. New investigative techniques may add insight but retain the possibility of uncertainty. Read More

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http://dx.doi.org/10.1177/2150135116678415DOI Listing
May 2018
7 Reads

Left Ventricle Relative Apical Sparing in Cardiac Amyloidosis.

J Cardiovasc Echogr 2017 Oct-Dec;27(4):141-142

Non Invasive Cardiology Unit, Emergency Department, University Hospital of Ferrara, Ferrara, Italy.

Amyloidosis is a disease characterized by the extracellular deposition of the protein amyloid. It is a multiorgan disease, and cardiac involvement is not uncommon, generally in the form of a restrictive cardiomyopathy. Typical aspects of cardiac amyloidosis have been described at echocardiography and magnetic resonance imaging (MRI). Read More

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http://dx.doi.org/10.4103/jcecho.jcecho_22_17DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5672686PMC
November 2017
9 Reads

CMR assessment and clinical outcomes of hypertrophic cardiomyopathy with or without ventricular remodeling in the end-stage phase.

Int J Cardiovasc Imaging 2018 Apr 25;34(4):597-605. Epub 2017 Oct 25.

Department of Cardiac MR, Fuwai Hospital, National Center for Cardiovascular Diseases of China, Chinese Academy of Medical Sciences and Peking Union Medical College, No. 167 Beilishi Road, Beijing, 100037, People's Republic of China.

End-stage phase of hypertrophic cardiomyopathy (ES-HCM) is a recognized part of HCM disease spectrum. Information on cardiac magnetic resonance (CMR) studies for ES-HCM especially for those without ventricular remodeling has been limited. We aimed to evaluate the morpho-functional and tissue features of ES-HCM with or without ventricular remodeling and to explore CMR prognostic value in these patients. Read More

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http://link.springer.com/10.1007/s10554-017-1263-3
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http://dx.doi.org/10.1007/s10554-017-1263-3DOI Listing
April 2018
14 Reads

Myocardial biopsy: techniques and indications.

Heart 2018 06 14;104(11):950-958. Epub 2017 Oct 14.

Transplant Unit, Papworth Hospital, Cambridge, UK.

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http://heart.bmj.com/lookup/doi/10.1136/heartjnl-2017-311382
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http://dx.doi.org/10.1136/heartjnl-2017-311382DOI Listing
June 2018
1 Read

High validity of cardiomyopathy diagnoses in western Sweden (1989-2009).

ESC Heart Fail 2018 04 11;5(2):233-240. Epub 2017 Oct 11.

Section of Emergency and Cardiovascular Medicine, Department of Molecular and Clinical Medicine, Institute of Medicine, Sahlgrenska Academy, University of Gothenburg, Sahlgrenska University Hospital/Östra, Gothenburg, Sweden.

Aim: Hospital discharges with a diagnosis of cardiomyopathy have more than doubled in Sweden since 1987. We validated the cardiomyopathy diagnoses over this time period to investigate that the increase was real and not a result of improved recognition of the diagnosis and better diagnostic methods.

Methods And Results: Every fifth year from 1989 to 2009, records for all patients with a cardiomyopathy diagnosis were identified by searching the local registers in three hospitals in Västra Götaland, Sweden. Read More

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http://dx.doi.org/10.1002/ehf2.12224DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5880670PMC
April 2018
24 Reads

Endomyocardial fibrosis in a context of peritonitis.

Eur Heart J Cardiovasc Imaging 2017 11;18(11):1297

CHU de Bordeaux, Hôpital Cardiologique du Haut-Lévêque, Avenue de Magellan, 33604, Bordeaux-Pessac, France.

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http://dx.doi.org/10.1093/ehjci/jex145DOI Listing
November 2017
25 Reads

Pediatric Cardiomyopathies.

Circ Res 2017 Sep;121(7):855-873

From the Department of Pediatrics, Columbia University Medical Center, New York, NY (T.M.L., W.K.C., L.J.A.); Department of Pediatrics, Albert Einstein College of Medicine, The Children's Hospital at Montefiore, Bronx, NY (D.T.H., J.M.L.); Department of Pediatrics, Stollery Children's Hospital, University of Alberta, Edmonton, Canada (P.K.); Department of Pediatrics, The Heart Institute, Le Bonheur Children's Hospital, Memphis, TN (J.A.T.); Indiana University School of Medicine, Indianapolis (S.M.W.); Department of Cardiology, Boston Children's Hospital, MA (S.D.C.); Department of Pediatrics, Cincinnati Children's Hospital Medical Center, OH (J.L.J., E.M.M.); Department of Pediatrics, Children's Hospital of Philadelphia, PA (J.W.R.); Department of Pediatrics, Washington University School of Medicine, St. Louis, MO (C.D.C.); Department of Pediatrics, Primary Children's Hospital, Salt Lake City, UT (A.K.L.); Department of Pediatrics, Ann and Robert H. Lurie Children's Hospital, Chicago, IL (P.T.T.); and Department of Pediatrics, Wayne State University School of Medicine and Children's Hospital of Michigan, Detroit (J.D.C., H.R., A.H., S.E.L.).

Pediatric cardiomyopathies are rare diseases with an annual incidence of 1.1 to 1.5 per 100 000. Read More

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http://dx.doi.org/10.1161/CIRCRESAHA.116.309386DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5657298PMC
September 2017
37 Reads

Restrictive Cardiomyopathy: Genetics, Pathogenesis, Clinical Manifestations, Diagnosis, and Therapy.

Circ Res 2017 Sep;121(7):819-837

From the Division of Hematology (E.M., M.A.G.) and Department of Cardiovascular Medicine (L.A.B.), Mayo Clinic, Rochester, MN.

Restrictive cardiomyopathy (RCM) is characterized by nondilated left or right ventricle with diastolic dysfunction. The restrictive cardiomyopathies are a heterogenous group of myocardial diseases that vary according to pathogenesis, clinical presentation, diagnostic evaluation and criteria, treatment, and prognosis. In this review, an overview of RCMs will be presented followed by a detailed discussion on 3 major causes of RCM, for which tailored interventions are available: cardiac amyloidosis, cardiac sarcoidosis, and cardiac hemochromatosis. Read More

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http://dx.doi.org/10.1161/CIRCRESAHA.117.310982DOI Listing
September 2017
6 Reads

Endomyocardial fibrosis in Sudan: clinical and echocardiographic features.

Cardiovasc J Afr 2017 Jul/Aug;28(4):208-214

Academy Teaching Hospital, Khartoum, Sudan.

Objective: Endomyocardial fibrosis (EMF) is a rare disease and is often an underdiagnosed and forgotten cardiomyopathy. The objective of this study was to document the current frequency of EMF in Sudan by defining and selecting cases from patients attending the echocardiography laboratory. Additionally we aimed to create an EMF registry for Sudan. Read More

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http://dx.doi.org/10.5830/CVJA-2016-079DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5642024PMC
June 2018
10 Reads

Safety and efficacy of a TTR specific antisense oligonucleotide in patients with transthyretin amyloid cardiomyopathy.

Amyloid 2017 Dec 14;24(4):219-225. Epub 2017 Sep 14.

c Department of Cardiology , Indiana University School of Medicine , Indianapolis , IN , USA.

Objectives: Cardiomyopathy is a major cause of death in both the hereditary form of transthyretin (TTR) amyloidosis and the sporadic late-age-onset transthyretin amyloidosis (ATTR wild-type (ATTR)). Clinically disease progression from time of diagnosis to death is usually quoted as 5- to 15-years. In prior studies, significant progression of cardiac parameters in patients with moderate to severe cardiomyopathy has been noted within a 12-month time span. Read More

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http://dx.doi.org/10.1080/13506129.2017.1374946DOI Listing
December 2017
11 Reads

Imaging cardiac innervation in amyloidosis.

J Nucl Cardiol 2019 Feb 8;26(1):174-187. Epub 2017 Sep 8.

Department of Nuclear Medicine and Molecular Imaging (EB50), Medical Imaging Center, University Medical Center Groningen, University of Groningen, Hanzeplein 1, P.O. Box 30.001, 9700 RB, Groningen, The Netherlands.

Cardiac amyloidosis is a form of restrictive cardiomyopathy resulting in heart failure and potential risk on arrhythmia, due to amyloid infiltration of the nerve conduction system and the myocardial tissue. The prognosis in this progressive disease is poor, probably due the development of cardiac arrhythmias. Early detection of cardiac sympathetic innervation disturbances has become of major clinical interest, because its occurrence and severity limits the choice of treatment. Read More

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http://dx.doi.org/10.1007/s12350-017-1059-9DOI Listing
February 2019
21 Reads

Clinical features of idiopathic restrictive cardiomyopathy: A retrospective multicenter cohort study over 2 decades.

Medicine (Baltimore) 2017 Sep;96(36):e7886

aDepartment of Cardiology, Asan Medical Center, University of Ulsan College of Medicine bDepartment of Internal Medicine, Seoul National University Hospital cDepartment of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul dDepartment of Cardiology, Translational Research Center on Aging, Chonnam National University Hospital, Gwangju eDepartment of Internal Medicine, Wonju College of Medicine,Yonsei University, Wonju fDepartment of Internal Medicine, Kangbuk Samsung Hospital, Seoul gDepartment of Internal Medicine, CHA Bundang Medical Center, CHA University school of Medicine, Bundang hDepartment of Cardiology, Sejong General Hospital iDepartment of Cardiovascular Medicine, Gachon University Gil Medical Center, Incheon jDepartment of Internal Medicine, Chungbuk National University School of Medicine, Cheongju, Korea.

Idiopathic restrictive cardiomyopathy (RCMP) has not been fully understood because this disease is difficult to diagnose. The present study aimed to assess the clinical profile and outcome of idiopathic RCMP from a multicenter cohort.This investigation is a retrospective study of consecutive patients with idiopathic RCMP at 10 centers in Korea between 1990 and 2010. Read More

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http://dx.doi.org/10.1097/MD.0000000000007886DOI Listing
September 2017
18 Reads

Cardiac amyloidosis: An update on pathophysiology, diagnosis, and treatment.

Trends Cardiovasc Med 2018 01 13;28(1):10-21. Epub 2017 Jul 13.

Section of Cardiovascular Medicine, Department of Medicine, Boston University School of Medicine, Boston Medical Center, 88 East Newton Street, Boston, MA; Amyloidosis Center, Boston University School of Medicine, Boston Medical Center, Boston, MA; Department of Radiology, Boston University School of Medicine, Boston Medical Center, Boston, MA. Electronic address:

The amyloidoses are a group of systemic diseases characterized by organ deposition of misfolded protein fragments of diverse origins. The natural history of the disease, involvement of other organs, and treatment options vary significantly based on the protein of origin. In AL amyloidosis, amyloid protein is derived from immunoglobulin light chains, and most often involves the kidneys and the heart. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S10501738173010
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http://dx.doi.org/10.1016/j.tcm.2017.07.004DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5741539PMC
January 2018
21 Reads

Restrictive cardiomyopathy due to novel desmin gene mutation.

Kardiol Pol 2017 ;75(7):723

Department of Cardiomyopathy, Institute of Cardiology, Warsaw, Poland, Poland.

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http://dx.doi.org/10.5603/KP.2017.0129DOI Listing
January 2018
11 Reads

Combined myocardial deformation to predict cardiac resynchronization therapy response in nonischemic cardiomyopathy.

Pacing Clin Electrophysiol 2017 Sep;40(9):986-994

Department of Cardiology, The First Affiliated Hospital of Harbin Medical University, Harbin, Heilongjiang, P. R. China.

Background: 20-30% of patients do not benefit from cardiac resynchronization therapy (CRT) when the established selection criteria were applied. We hypothesized that a combined assessment of mechanical dyssynchrony, myocardial deformation, and diastolic function would identify patients who would benefit most from CRT.

Method: In 36 CRT patients, clinical evaluation and echocardiography were performed before and after CRT. Read More

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http://dx.doi.org/10.1111/pace.13151DOI Listing
September 2017
20 Reads

Hypertrophic restrictive cardiomyopathy with apical thinning: a peculiar case of genotype-phenotype correlation.

J Cardiovasc Med (Hagerstown) 2017 10;18(10):835-836

Cardiovascular Department, Azienda Sanitaria Universitaria Integrata of Trieste 'ASUITS', Trieste, Italy.

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http://dx.doi.org/10.2459/JCM.0000000000000538DOI Listing
October 2017
6 Reads

Restrictive Arteriopathy in Late-Onset Pompe Disease: Case Report and Review of the Literature.

J Stroke Cerebrovasc Dis 2017 Aug 21;26(8):e172-e175. Epub 2017 Jun 21.

Neurovascular Imaging Research Core, University of California, Los Angeles, California.

Late-onset Pompe disease (LOPD) is an adult type of classical Pompe disease and presents without cardiomyopathy. Neuroimaging in LOPD is typically limited to posterior circulation and involves dilative arteriopathy, especially dolichoectasia and intracranial aneurysms. We report an interesting case of an established diagnosis of asymptomatic LOPD in a young man with a restrictive-variant pattern in posterior vasculature. Read More

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http://dx.doi.org/10.1016/j.jstrokecerebrovasdis.2017.05.032DOI Listing
August 2017
11 Reads

Hypereosinophilic cardiac disease.

Acta Cardiol 2017 Feb;72(1):9-18

a Centre Hospitalier Universitaire de Nancy, Service de Cardiologie, Institut Lorrain du Cœur et des Vaisseaux , Vandœuvre-lès-Nancy , France.

Hypereosinophilia may be due to several aetiologies. Cardiac complications are not uncommon, whatever the causes. Clinical presentations of hypereosinophilic cardiac diseases may vary widely from asymptomatic form to fatal necrotic myocarditis or irreversible restrictive cardiomyopathy. Read More

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http://dx.doi.org/10.1080/00015385.2017.1281546DOI Listing
February 2017
12 Reads

Eosinophilic myocarditis presenting as acute coronary syndrome.

Turk Kardiyol Dern Ars 2017 Jun;45(4):358-361

Department of Cardiology, Ege University Faculty of Medicine, İzmir, Turkey.

Eosinophilic myocarditis (EM) is a rare condition that may result from several heterogeneous eosinophilic diseases, including parasite infection, hypersensitivity reaction, vasculitis, and hypereosinophilic syndrome. Regardless of etiology, the disease may present with various cardiac conditions, such as acute coronary syndrome, heart failure, or arrhythmia. Irreversible endomyocardial fibrosis, which causes restrictive cardiomyopathy, occurs in the late phase of the disease. Read More

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http://dx.doi.org/10.5543/tkda.2016.49392DOI Listing
June 2017
7 Reads

Progressive mitral regurgitation in a patient with tropical endomyocardial fibrosis.

Eur Heart J Cardiovasc Imaging 2017 Sep;18(9):1071

First Department of Internal Medicine, Nara Medical University, 840 Shijo, Kashihara, Nara 634-8522, Japan.

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http://dx.doi.org/10.1093/ehjci/jex132DOI Listing
September 2017
11 Reads

Discovery of a new mutation in the desmin gene in a young patient with cardiomyopathy and muscular weakness.

Rom J Morphol Embryol 2017 ;58(1):225-230

Department of Cardiology, "Prof. Dr. C. C. Iliescu" Institute of Emergency for Cardiovascular Diseases, "Carol Davila" University of Medicine and Pharmacy, Bucharest, Romania;

A 25-year-old woman with a five years history of syncope, mild left ventricular hypertrophy and moderately enlarged atria, was diagnosed with third degree atrioventricular heart block alternating with atrioventricular heart block 2:1, and received a dual chamber pacemaker. After three years of evolution, she developed atrial fibrillation, marked biatrial enlargement, severely depressed longitudinal myocardial velocities, associated with mild girdle weakness and slight increase in creatine kinase level. The diagnosis of restrictive cardiomyopathy with mild skeletal myopathy imposed the screening for a common etiology. Read More

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March 2018
30 Reads

Amyloidosis - a rare cause of refractory heart failure in a young female.

Rom J Morphol Embryol 2017 ;58(1):201-206

Department of Ophthalmology, "Grigore T. Popa" University of Medicine and Pharmacy, Iasi, Romania;

Cardiac amyloidosis may occur in any type of systemic amyloidosis. The clinical picture is often characterized by restrictive cardiomyopathy. We report the case of a 41-year-old female patient admitted to the Department of Cardiology with clinical signs of right heart failure: congested jugular veins, hepatomegaly, peripheral edema, ascites associated with atrial fibrillation, low values of arterial blood pressure and oliguria. Read More

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March 2018
22 Reads

Multimodality Imaging in Restrictive Cardiomyopathies: An EACVI expert consensus document In collaboration with the "Working Group on myocardial and pericardial diseases" of the European Society of Cardiology Endorsed by The Indian Academy of Echocardiography.

Eur Heart J Cardiovasc Imaging 2017 Oct;18(10):1090-1121

University Hospital Ramon y Cajal Carretera de Colmenar Km 9,100, 28034 Madrid, Spain.

Restrictive cardiomyopathies (RCMs) are a diverse group of myocardial diseases with a wide range of aetiologies, including familial, genetic and acquired diseases and ranging from very rare to relatively frequent cardiac disorders. In all these diseases, imaging techniques play a central role. Advanced imaging techniques provide important novel data on the diagnostic and prognostic assessment of RCMs. Read More

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https://academic.oup.com/ehjcimaging/article/18/10/1090/3828
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http://dx.doi.org/10.1093/ehjci/jex034DOI Listing
October 2017
61 Reads

The novel αB-crystallin (CRYAB) mutation p.D109G causes restrictive cardiomyopathy.

Hum Mutat 2017 08 21;38(8):947-952. Epub 2017 Jun 21.

Department of Thoracic and Cardiovascular Surgery, Heart and Diabetes Centre NRW, University Hospital of the Ruhr-University Bochum, Erich and Hanna Klessmann Institute for Cardiovascular Research & Development (EHKI), Bad Oeynhausen, Germany.

Restrictive cardiomyopathy (RCM) is a rare heart disease characterized by diastolic dysfunction and atrial enlargement. The genetic etiology of RCM is not completely known. We identified by a next-generation sequencing panel the novel CRYAB missense mutation c. Read More

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http://dx.doi.org/10.1002/humu.23248DOI Listing
August 2017
27 Reads

Surgical Treatment of Constrictive Pericarditis.

Tex Heart Inst J 2017 Apr 1;44(2):101-106. Epub 2017 Apr 1.

Constrictive pericarditis is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. Transthoracic echocardiography, computed tomography, and cardiac magnetic resonance imaging each can reveal severe diastolic dysfunction and increased pericardial thickness. Cardiac catheterization can help to confirm a diagnosis of diastolic dysfunction secondary to pericardial constriction, and to exclude restrictive cardiomyopathy. Read More

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http://dx.doi.org/10.14503/THIJ-16-5772DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5408622PMC
April 2017
22 Reads

Late onset cardiomyopathy as presenting sign of ATTR A45G amyloidosis caused by a novel TTR mutation (p.A65G).

Cardiovasc Pathol 2017 Jul - Aug;29:19-22. Epub 2017 Apr 18.

Department of Rheumatology & Clinical Immunology, University of Groningen, University Medical Center Groningen, The Netherlands.

Objective: The clinical description of a novel TTR gene mutation characterized by a late onset amyloid cardiomyopathy.

Methods And Results: A 78-year-old man of Dutch origin with recent surgery for bilateral carpal tunnel syndrome (CTS) was admitted to our hospital because of heart failure with preserved ejection fraction (55%). Cardiac ultrasound showed thickened biventricular walls, and cardiac magnetic resonance imaging also showed late gadolinium enhancement. Read More

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http://dx.doi.org/10.1016/j.carpath.2017.04.002DOI Listing
August 2018
18 Reads

Hypereosinophilic syndrome: endomyocardial biopsy versus echocardiography to diagnose cardiac involvement.

Postgrad Med 2017 Jun 25;129(5):517-523. Epub 2017 Apr 25.

a Division of Allergic Diseases, and Mayo Clinic Program for Mast Cell and Eosinophilic Disorders , Mayo Clinic , Rochester , MN , USA.

Objective: To compare echocardiograms and endomyocardial biopsies to diagnose cardiac involvement in hypereosinophilic syndrome.

Methods: We examined the agreement between echocardiography and endomyocardial biopsies to detect cardiac involvement in hypereosinophilic syndrome by reviewing cases identified as hypereosinophilia or hypereosinophilic syndrome in Mayo Clinic databases from January 1978 through June 2009. Single-organ cases of eosinophilia such as eosinophilic fasciitis and eosinophilic gastroenteritis were excluded. Read More

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http://dx.doi.org/10.1080/00325481.2017.1317215DOI Listing
June 2017
18 Reads

Familial amyloid cardiomyopathy masquerading as chronic Guillain-Barre syndrome: things are not always what they seem.

Front Med 2017 Jun 19;11(2):293-296. Epub 2017 Apr 19.

Department of Cardiovascular Medicine, the Second Xiangya Hospital, Central South University, Changsha, 410011, China.

Familial amyloid cardiomyopathy is a challenging condition that mimics many other diseases, particularly in patients with pronounced neurological presentations and unexplained or equivocal cardiac abnormalities. In this case, a 57-year-old man was admitted for outpatient cardiological evaluation of progressive right heart failure and limb paraesthesias. The patient presented with hypertension, chronic Guillain-Barre syndrome, and sick sinus syndrome. Read More

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http://dx.doi.org/10.1007/s11684-017-0516-9DOI Listing
June 2017
4 Reads

Septal artery diastolic flow profile in hypertrophic restrictive cardiomyopathy: Doppler square root sign!

Eur Heart J Cardiovasc Imaging 2017 Sep;18(9):1067

Aurora Cardiovascular Services, Aurora Sinai/Aurora St. Luke's Medical Centers, University of Wisconsin School of Medicine and Public Health, 2801 W. Kinnickinnic River Parkway, Milwaukee, WI 53215, USA.

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http://dx.doi.org/10.1093/ehjci/jex061DOI Listing
September 2017
6 Reads

New Cardiac Imaging Algorithms to Diagnose Constrictive Pericarditis Versus Restrictive Cardiomyopathy.

Curr Cardiol Rep 2017 05;19(5):43

Heart and Vascular Institute, West Virginia University, 1 Medical Center Drive, Morgantown, WV, 26506, USA.

Purpose Of Review: Echocardiography is the mainstay in the diagnostic evaluation of constrictive pericarditis (CP) and restrictive cardiomyopathy (RCM), but no single echocardiographic parameter is sufficiently robust to accurately distinguish between the two conditions. The present review summarizes the recent advances in echocardiography that promise to improve its diagnostic performance for this purpose. The role of other imaging modalities such as cardiac computed tomography, magnetic resonance imaging, and invasive hemodynamic assessment in the overall diagnostic approach is also discussed briefly. Read More

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http://dx.doi.org/10.1007/s11886-017-0851-0DOI Listing
May 2017
6 Reads

Effect of preoperative left ventricular diastolic dysfunction on mid-term outcomes after surgical ventricular restoration for ischemic cardiomyopathy.

Gen Thorac Cardiovasc Surg 2017 Jul 4;65(7):381-387. Epub 2017 Apr 4.

Department of Cardiovascular Surgery, Faculty of Medicine, University of Miyazaki, 5200 Kiyotakecho Kihara, Miyazaki-city, Miyazaki, 889-1692, Japan.

Objectives: The impact of surgical ventricular restoration (SVR) on survival and major adverse cardiac events (MACEs) is still controversial. The purposes of this study were to analyze our surgical experience with SVR for ischemic cardiomyopathy and to determine the effect of preoperative left ventricular diastolic dysfunction on mid-term outcomes after SVR.

Methods And Results: Between April 2010 and May 2016, 19 patients underwent SVR. Read More

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http://dx.doi.org/10.1007/s11748-017-0773-1DOI Listing
July 2017
3 Reads

Magnetic resonance imaging for characterizing myocardial diseases.

Int J Cardiovasc Imaging 2017 Sep 31;33(9):1395-1414. Epub 2017 Mar 31.

Department of Radiology and Biomedical Imaging, School of Medicine, University of California San Francisco, 185 Berry Street, Suite 350, Campus Box 0946, San Francisco, CA, 94107-5705, USA.

The National Institute of Health defined cardiomyopathy as diseases of the heart muscle. These myocardial diseases have different etiology, structure and treatment. This review highlights the key imaging features of different myocardial diseases. Read More

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http://dx.doi.org/10.1007/s10554-017-1127-xDOI Listing
September 2017
11 Reads

Mycoplasma hominis periaortic abscess following heart-lung transplantation.

Transpl Infect Dis 2017 Jun 3;19(3). Epub 2017 May 3.

Department of Infection Control and Prevention, Osaka University Graduate School of Medicine, Osaka, Japan.

We report the first case of Mycoplasma hominis periaortic abscess after heart-lung transplantation. The absence of sternal wound infection delayed the diagnosis, but the patient successfully recovered with debridement surgeries and long-term antibiotic therapy. Owing to the difficulty in detection and the intrinsic resistance to beta-lactams, M. Read More

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http://dx.doi.org/10.1111/tid.12697DOI Listing
June 2017
5 Reads

Multiparametric cardiac magnetic resonance imaging (CMR) for the diagnosis of Loeffler's endocarditis: a case report.

BMC Cardiovasc Disord 2017 03 11;17(1):74. Epub 2017 Mar 11.

Department of Cardiology, Pulmonology and Vascular Medicine, Heinrich-Heine University Düsseldorf, Düsseldorf, Germany.

Background: Endocarditis parietalis fibroplastica Löfflein (EPF) is a rare form of primary restrictive cardiomyopathy with poor prognosis. It is generally caused by hypereosinophilic syndrome with eosinophilic penetration of the heart. This leads to congestive heart failure in three different stages. Read More

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http://dx.doi.org/10.1186/s12872-017-0492-7DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5346256PMC
March 2017
2 Reads