Int J Clin Exp Pathol 2015 1;8(1):260-74. Epub 2015 Jan 1.
Department of Pathology, University of Oklahoma Health Sciences Center Oklahoma City, OK 73104, USA ; Department of Pathology, Oklahoma City Veterans Administration Medical Center Oklahoma City, OK 73104, USA.
Pediatric primary "small round blue cell" tumors in the CNS represent several entities, some more common than others. Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/pPNET) is rare and must be distinguished from other tumors such as medulloblastoma [1, 2], atypical rhabdoid/teratoid tumor, ependymomal tumors, metastatic sarcomas, hematologic malignancies, and other mimics. Although therapy for ES/pPNET is effective, it brings severe side effects, including cardiac toxicity, making correct recognition important . Read More