674 results match your criteria Eosinophilic Fasciitis


A Histologically Proven Case of Autoimmune Hepatitis with Eosinophilic Fasciitis.

Intern Med 2018 Oct 17. Epub 2018 Oct 17.

Third department of Internal Medicine, Nara Medical University, Japan.

Both autoimmune hepatitis (AIH) and eosinophilic fasciitis (EF) are known to be complicated by other autoimmune diseases. However, AIH complicated by EF has never been reported. We experienced a 58-year-old man with AIH complicated by EF. Read More

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http://dx.doi.org/10.2169/internalmedicine.1299-18DOI Listing
October 2018
1 Read

Eosinophilic fasciitis: a case series with an emphasis on therapy and induction of remission.

Drugs Context 2018 2;7:212529. Epub 2018 Oct 2.

Department of Dermatology, Wake Forest University School of Medicine, Winston-Salem, NC, USA.

Eosinophilic fasciitis is an uncommon connective tissue disorder that affects patients of all ages, resulting in significant morbidity. Systemic corticosteroids can induce remission of disease. However, there is no universally accepted treatment ladder for eosinophilic fasciitis. Read More

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https://www.drugsincontext.com/eosinophilic-fasciitis-a-case
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http://dx.doi.org/10.7573/dic.212529DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6172017PMC
October 2018
3 Reads

[Mimetics of systemic sclerosis].

Z Rheumatol 2018 Sep 25. Epub 2018 Sep 25.

Klinik für Rheumatologie und klinische Immunologie, Universitätsklinikum Schleswig-Holstein, Campus Lübeck, Ratzeburger Allee 160, 23538, Lübeck, Deutschland.

Background: Systemic sclerosis (SSc) is characterized by heterogeneous clinical symptoms. Peripheral skin fibrosis can be a common symptom. Nevertheless, a variety of diseases with different etiologies are associated with a thickening of the skin and make the initial diagnosis of systemic sclerosis more difficult. Read More

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http://dx.doi.org/10.1007/s00393-018-0538-yDOI Listing
September 2018
10 Reads

Diagnostic ultrasonography in a child with eosinophilic fasciitis.

Clin Exp Dermatol 2019 01 30;44(1):85-86. Epub 2018 Aug 30.

Department of Dermatology, Hospital Universitario La Paz, Paseo de la Castellana 261, Madrid, 28046, Spain.

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http://dx.doi.org/10.1111/ced.13714DOI Listing
January 2019
2 Reads

Granulomatous fasciitis followed by morphea profunda: Is granulomatous fasciitis part of a spectrum of deep morphea? A case report and review of the literature.

Clin Case Rep 2018 Aug 4;6(8):1412-1417. Epub 2018 Jun 4.

Department of Rheumatology School of Medicine University of California, San Diego La Jolla CA USA.

Although eosinophilic fasciitis is known to be part of the deep morphea spectrum, this first report of the coexistence of granulomatous fasciitis and morphea profunda suggests that granulomatous fasciitis may also be a part of the spectrum of deep morphea. Read More

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http://dx.doi.org/10.1002/ccr3.1608DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6098999PMC
August 2018
2 Reads

Eosinophilic fasciitis: Current concepts.

Clin Dermatol 2018 Jul - Aug;36(4):487-497. Epub 2018 Apr 10.

Department of Dermatology, Oregon Health and Science University, Portland, Oregon, USA.

Eosinophilic fasciitis (EF) is an uncommon connective tissue disease characterized by abrupt onset of edema, followed by progressive induration of primarily the distal extremities. Patients may exhibit inflammatory arthritis, joint contractures, decreased mobility, and nerve entrapment. Almost half of patients with EF may have coexisting morphea plaques. Read More

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http://dx.doi.org/10.1016/j.clindermatol.2018.04.006DOI Listing
December 2018
24 Reads

Generalized morphea/eosinophilic fasciitis overlap after epoxy exposure.

JAAD Case Rep 2018 Mar 4;4(2):175-178. Epub 2018 Feb 4.

Department of Dermatology, The University of Texas MD Anderson Cancer Center, Houston, Texas.

Generalized morphea is associated with epoxy resin vapors and is characterized by the development of lesions shortly after exposure. Morphea presenting along with eosinophilic fasciitis (EF), or morphea/EF overlap, is rare and an indicator of poor prognosis and resistance to treatment. Here we present a case of generalized morphea/EF overlap linked to epoxy exposure. Read More

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http://dx.doi.org/10.1016/j.jdcr.2017.09.006DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5993554PMC
March 2018
5 Reads

Eosinophilic fasciitis and lichen sclerosus in a patient treated with nivolumab.

Australas J Dermatol 2018 Nov 24;59(4):e302-e304. Epub 2018 May 24.

Department of Dermatology, Hospital 12 de Octubre and Institute i+12, Medical School, Universidad Complutense, Madrid, Spain.

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http://dx.doi.org/10.1111/ajd.12836DOI Listing
November 2018
26 Reads

bacteremia mimicking eosinophilic fasciitis in a patient with X-linked agammaglobulinemia.

JAAD Case Rep 2018 May 31;4(4):327-329. Epub 2018 Mar 31.

Department of Allergy and Immunology, Centre Hospitalier de l'Université de Montréal (CHUM), Montreal, Canada.

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http://dx.doi.org/10.1016/j.jdcr.2017.11.016DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5911815PMC
May 2018
5 Reads

Neuromuscular ultrasound findings in eosinophilic fasciitis: A case series and literature review.

Muscle Nerve 2018 Aug 24;58(2):E15-E18. Epub 2018 May 24.

Department of Neurology, Wake Forest School of Medicine, Winston-Salem, North Carolina, USA.

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http://dx.doi.org/10.1002/mus.26150DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6105431PMC
August 2018
5 Reads

Eosinophilic Fasciitis in Association With Hypereosinophilic Syndrome in an HIV-Infected Patient With Severe Multiorgan Involvement.

J Investig Allergol Clin Immunol 2018 Apr;28(2):126-128

Department of Dermatology, Hospital Universitari Germans Trias i Pujol, Badalona, Universitat Autònoma de Barcelona, Spain.

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http://dx.doi.org/10.18176/jiaci.0216DOI Listing
April 2018
4 Reads

Skin ultrasound is a useful tool for evaluating and monitoring eosinophilic fasciitis.

Int J Dermatol 2018 06 6;57(6):743-745. Epub 2018 Apr 6.

Departament of Dermatology, University Hospital Complex of Santiago de Compostela, A Coruña, Spain.

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http://dx.doi.org/10.1111/ijd.13986DOI Listing
June 2018
7 Reads

Population-based prevalence of eosinophilic fasciitis (Shulman syndrome): a capture-recapture study.

Br J Dermatol 2018 Aug 7;179(2):516-517. Epub 2018 Jun 7.

Service de rhumatologie, Centre National de Référence des Maladies Systémiques et Auto-immunes rares, Université de Strasbourg, Strasbourg, France.

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http://dx.doi.org/10.1111/bjd.16535DOI Listing
August 2018
10 Reads

Ultrasonographic images of the hand in a case with early eosinophilic fasciitis.

J Med Ultrason (2001) 2018 Oct 20;45(4):641-645. Epub 2018 Feb 20.

Department of Physical Medicine and Rehabilitation, National Taiwan University Hospital and National Taiwan University College of Medicine, Taipei, Taiwan, ROC.

Eosinophilic fasciitis (EF), a rare rheumatic disease, usually affects the limbs symmetrically and generally spares the hands and feet. Cases of unilateral hand involvement are rarely reported. Here, we report such a rare case. Read More

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http://dx.doi.org/10.1007/s10396-018-0872-3DOI Listing
October 2018
5 Reads

Rituximab as a therapeutic consideration for refractory eosinophilic fasciitis.

Int J Dermatol 2018 05 15;57(5):614-615. Epub 2018 Feb 15.

Department of Dermatology, Henry Ford Hospital, Detroit, MI, USA.

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http://dx.doi.org/10.1111/ijd.13940DOI Listing
May 2018
9 Reads

Eosinophilic Fasciitis: A Single Center Experience of Seven Patients.

Isr Med Assoc J 2018 Feb;20(2):95-99

Department of Medicine, Hadassah-Hebrew University Medical Center, Ein Kerem Campus, Jerusalem, Israel.

Background: Eosinophilic fasciitis (EF) is a rare disease characterized by scleroderma-like skin, inflammation of deep muscle fascia, hypergammaglobulinemia, peripheral eosinophilia, and elevated erythrocyte sedimentation rate.

Objectives: To present our experience in diagnosis and treatment of seven biopsy-proven EF patients in a large tertiary medical center.

Methods: We screened all patients who were admitted to our tertiary medical center and diagnosed with EF by tissue biopsies from January 2000 to January 2016. Read More

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February 2018
9 Reads

Rheumatic manifestations among cancer patients treated with immune checkpoint inhibitors.

Autoimmun Rev 2018 Mar 16;17(3):284-289. Epub 2018 Jan 16.

Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel; Ella Lemelbaum Institute for Immuno-Oncology, Sheba Medical Center, Israel. Electronic address:

Background: The use of immune checkpoint inhibitors (ICI) has grown incessantly since they were first approved in 2014. These monoclonal antibodies inhibit T cell activation, yielding a dramatic tumor response with improved survival. However, immunotherapy is frequently hampered by immune adverse events (iAE) such as hypophysitis, colitis, hepatitis, pneumonitis and rash. Read More

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http://dx.doi.org/10.1016/j.autrev.2018.01.003DOI Listing
March 2018
10 Reads

[EOSINOPHILIC FASCIITIS (EF)].

Harefuah 2017 Dec;156(12):786-790

Sackler Faculty of Medicine, Tel Aviv University.

Introduction: Eosinophilic fasciitis (EF) is a rare connective tissue disease characterized by erythema, edema and myalgia with induration and thickening of the skin and soft tissue, especially subcutaneous fascia. Laboratory findings usually show peripheral eosinophilia, and full-thickness wedge biopsy is essential to establish the diagnosis. Corticosteroids are effective and remain the standard therapy for EF, although some patients may improve spontaneously. Read More

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December 2017
14 Reads

Morphoea profunda and its relationship to eosinophilic fasciitis.

Clin Exp Dermatol 2018 Apr 26;43(3):306-310. Epub 2017 Dec 26.

Royal United Hospital Bath, Bath, Avon, UK.

In this small case series, all eight patients were women in their fifth and sixth decades. This is similar to the female predominance in morphoea and less in keeping with eosinophilic fasciitis (EF). All cases had diffuse induration of their limbs with both proximal and distal patterns of distribution, and five of the patients exhibited peau d'orange skin. Read More

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http://dx.doi.org/10.1111/ced.13353DOI Listing
April 2018
8 Reads

Eosinophilic fasciitis during pregnancy: case report and review of literature.

Rheumatol Int 2018 Mar 15;38(3):525-529. Epub 2017 Dec 15.

Division of Rheumatology, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, São Paulo, SP, Brazil.

The authors describe the case of a 23-year-old woman who was referred to the rheumatologist due to symmetrical and progressive stiffness, induration, and swelling of arms and thighs at the 12th week of her first gestation. The characteristic clinical aspect of 'peau d'orange', associated to the histopathologic results of the deep biopsy of the skin confirmed the diagnosis of eosinophilic fasciitis. Treatment with oral prednisone, at an initial dose of 1 mg/kg/day, was effective and rapidly tapered to 10 mg/day till the birth of a healthy newborn. Read More

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http://dx.doi.org/10.1007/s00296-017-3908-xDOI Listing
March 2018
21 Reads

Diagnostic criteria, severity classification and guidelines of eosinophilic fasciitis.

J Dermatol 2018 Aug 13;45(8):881-890. Epub 2017 Dec 13.

Department of Dermatology and Plastic Surgery, Faculty of Life Sciences, Kumamoto University, Kumamoto, Japan.

We established diagnostic criteria and severity classification of eosinophilic fasciitis because there is no established diagnostic criteria or widely accepted severity classification of the disease. Also, there has been no clinical guideline for eosinophilic fasciitis, so we established its clinical guideline ahead of all over the world. In particular, the clinical guideline was established by clinical questions based on evidence-based medicine according to the New Minds Clinical Practice Guideline Creation Manual (version 1. Read More

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http://dx.doi.org/10.1111/1346-8138.14160DOI Listing
August 2018
11 Reads

Eosinophilic Fasciitis: an Updated Review on Diagnosis and Treatment.

Curr Rheumatol Rep 2017 Nov 4;19(12):74. Epub 2017 Nov 4.

Department of Dermatology, Brigham and Women's Hospital, Boston, MA, USA.

Purpose Of Review: First recognized in 1974, eosinophilic fasciitis (EF) is a fibrosing disorder of the fascia with characteristic cutaneous and hematologic manifestations. This review discusses recent trends in the diagnosis and treatment of EF.

Recent Findings: Although fascial biopsy has classically been considered the gold standard for making a diagnosis of EF, radiologic imaging, particularly magnetic resonance imaging, has been increasingly used for both diagnosis and monitoring of treatment response. Read More

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http://dx.doi.org/10.1007/s11926-017-0700-6DOI Listing
November 2017
10 Reads

[F] FDG PET/CT may be a useful adjunct in diagnosis of eosinophilic fasciitis.

Reumatol Clin 2017 Oct 23. Epub 2017 Oct 23.

Department of Rheumatology, Hospital Universitario de Bellvitge-IDIBELL, Barcelona, Spain.

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http://dx.doi.org/10.1016/j.reuma.2017.09.004DOI Listing
October 2017
11 Reads

[Sarcoid-like granulomatosis associated with eosinophilic fasciitis].

Ann Dermatol Venereol 2018 Jan 28;145(1):37-42. Epub 2017 Sep 28.

Service de dermatologie, hôpital Saint-Louis, 1, avenue Claude-Vellefaux, 75010 Paris, France; Université Paris-Diderot, Paris VII, 75010 Paris, France. Electronic address:

Background: Eosinophilic fasciitis (EF) is a rare condition characterized by swelling of the extremities, sclerodermatous evolution and frequent hypereosinophilia. Hematological disorders, including aplastic anemia, solid tumors and autoimmune diseases, may be associated with EF. EF is usually not associated with granulomatous diseases. Read More

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http://dx.doi.org/10.1016/j.annder.2017.08.012DOI Listing
January 2018
6 Reads

Positive prayer sign in eosinophilic fasciitis.

Authors:
José Pardos-Gea

Rheumatology (Oxford) 2017 Apr;56(4):628

Department of Internal Medicine, Autoimmune Diseases Unit, Vall d´Hebrón University Hospital, Barcelona, Spain.

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http://dx.doi.org/10.1093/rheumatology/kew415DOI Listing
April 2017
7 Reads

[Eosinophilia heralding the diagnosis of eosinophilic fasciitis (Shulman's disease)].

Rev Med Interne 2017 Dec 1;38(12):840-843. Epub 2017 Sep 1.

Service de médecine interne, hôpital Nord, Aix-Marseille université, Assistance publique-Hôpitaux de Marseille (AP-HM), chemin des Bourrely, 13915 Marseille cedex 15, France. Electronic address:

Introduction: Eosinophilic fasciitis or Shulman's disease is characterized, in its typical form, by palpable thickening of the skin and soft tissues, blood hypereosinophilia and fascia lesions. We hereby report a case of eosinophilic fasciitis in which hypereosinophilia preceded for several months the clinical signs of fasciitis.

Case Report: A 64-year-old woman, with a history of Little's syndrome with motor disability, was admitted in internal medicine for eosinophilia. Read More

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http://dx.doi.org/10.1016/j.revmed.2017.07.010DOI Listing
December 2017
7 Reads

Clinicopathologic and immunophenotypic features of eosinophilic fasciitis and morphea profunda: A comparative study of 27 cases.

J Am Acad Dermatol 2018 Jan 31;78(1):121-128. Epub 2017 Aug 31.

Department of Dermatology, Mayo School of Graduate Medical Education, Mayo Clinic, Rochester, Minnesota; Department of Laboratory Medicine and Pathology, Mayo School of Graduate Medical Education, Mayo Clinic, Rochester, Minnesota. Electronic address:

Background: Eosinophilic fasciitis (EF) and morphea profunda (MP) are inflammatory and sclerosing disorders of the subcutis that can exhibit clinical and pathologic presentations that overlap.

Objective: To identify clinicopathologic features that can be used to distinguish EF from MP.

Methods: We performed a retrospective review of 16 patients with EF and 11 patients with MP. Read More

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http://dx.doi.org/10.1016/j.jaad.2017.06.148DOI Listing
January 2018
18 Reads

[Extensive connective tissue nevus in children].

Ann Dermatol Venereol 2017 Nov 29;144(11):700-704. Epub 2017 Jul 29.

Service de dermatologie, CHU de Caen, avenue de la Côte-de-Nacre, CS 30001, 14033 Caen cedex 9, France.

Background: Connective tissue nevus (CTN) is a rare condition of the extracellular matrix components that generally presents as papulae of normal skin colour. This condition may be syndromic or sporadic.

Patients And Methods: We report herein two isolated cases of extensive and infiltrative CTN in children at risk for subsequent joint stiffening. Read More

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http://dx.doi.org/10.1016/j.annder.2017.06.006DOI Listing
November 2017
5 Reads

Long-term outcome of eosinophilic fasciitis: A cross-sectional evaluation of 35 patients.

J Am Acad Dermatol 2017 Sep 19;77(3):512-517.e5. Epub 2017 Jul 19.

Department of Dermatology, Radboud University, Nijmegen, The Netherlands; Radboud University Medical Centre, Radboud University, Nijmegen, The Netherlands.

Background: Eosinophilic fasciitis (EF) is a connective tissue disease with an unknown long-term course.

Objective: To evaluate presence and determinants of residual disease damage in patients with EF after long-term follow-up.

Methods: Patients with biopsy-proven EF were included for this cross-sectional study. Read More

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http://dx.doi.org/10.1016/j.jaad.2017.05.018DOI Listing
September 2017
32 Reads

Cutaneous Manifestations of Scleroderma and Scleroderma-Like Disorders: a Comprehensive Review.

Clin Rev Allergy Immunol 2017 Dec;53(3):306-336

Section of Dermatology, Department of Medical Sciences and Public Health, University of Cagliari, Cagliari, Italy.

Scleroderma refers to an autoimmune connective tissue fibrosing disease, including three different subsets: localized scleroderma, limited cutaneous systemic sclerosis, and diffuse cutaneous systemic sclerosis with divergent patterns of organ involvement, autoantibody profiles, management, and prognostic implications. Although systemic sclerosis is considered the disease prototype that causes cutaneous sclerosis, there are many other conditions that can mimic and be confused with SSc. They can be classified into immune-mediated/inflammatory, immune-mediated/inflammatory with abnormal deposit (mucinoses), genetic, drug-induced and toxic, metabolic, panniculitis/vascular, and (para)neoplastic disorders according to clinico-pathological and pathogenetic correlations. Read More

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http://dx.doi.org/10.1007/s12016-017-8625-4DOI Listing
December 2017
22 Reads

Scleroderma-like Disorders.

Authors:
Amit Sharma

Curr Rheumatol Rev 2018 Apr;14(1):22-27

Fortis Escorts Hospital, Jaipur, Rajasthan, India.

Background: Scleroderma is a term used to describe diseases that involve hardening and tightening of the skin and the underlying subcutaneous connective tissue. It could be localized to skin and subcutaneous tissue, or may involve the internal organs too in systemic sclerosis.

Objective: There are disorders that can cause hardening and tightening of skin and mimic scleroderma but are rarely associated with Raynaud phenomenon, sclerodactyly, and autoantibodies in the serum, features specific to scleroderma/systemic sclerosis. Read More

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http://dx.doi.org/10.2174/1573397113666170612091419DOI Listing
April 2018
19 Reads

Eosinophilic Fasciitis: A Firm Warning.

Authors:
Warren R Heymann

Skinmed 2017 1;15(2):139-140. Epub 2017 Apr 1.

Division of Dermatology, Departments of Medicine and Pediatrics, Cooper Medical School of Rowan University, Marlton, NJ;

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April 2017
10 Reads

Scleroderma Mimickers.

Curr Treatm Opt Rheumatol 2016 Mar 5;2(1):69-84. Epub 2016 Feb 5.

Division of Rheumatology, Johns Hopkins University School of Medicine, Baltimore, MD, USA.

Cutaneous fibrosing disorders encompass a diverse array of diseases united by the presence of varying degrees of dermal sclerosis. The quality and distribution of skin involvement, presence or absence of systemic complications and unique associated laboratory abnormalities often help to distinguish between these diseases. It is imperative that an effort is made to accurately differentiate between scleroderma and its mimics, in order to guide long-term management and facilitate implementation of the appropriate treatment modality where indicated. Read More

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http://dx.doi.org/10.1007/s40674-016-0038-7DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5412724PMC
March 2016
15 Reads

Hypereosinophilic syndrome: endomyocardial biopsy versus echocardiography to diagnose cardiac involvement.

Postgrad Med 2017 Jun 25;129(5):517-523. Epub 2017 Apr 25.

a Division of Allergic Diseases, and Mayo Clinic Program for Mast Cell and Eosinophilic Disorders , Mayo Clinic , Rochester , MN , USA.

Objective: To compare echocardiograms and endomyocardial biopsies to diagnose cardiac involvement in hypereosinophilic syndrome.

Methods: We examined the agreement between echocardiography and endomyocardial biopsies to detect cardiac involvement in hypereosinophilic syndrome by reviewing cases identified as hypereosinophilia or hypereosinophilic syndrome in Mayo Clinic databases from January 1978 through June 2009. Single-organ cases of eosinophilia such as eosinophilic fasciitis and eosinophilic gastroenteritis were excluded. Read More

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http://dx.doi.org/10.1080/00325481.2017.1317215DOI Listing
June 2017
15 Reads

Th1- and Th17-polarized immune infiltrates in eosinophilic fasciitis-A potential marker for histopathologic distinction from morphea.

J Cutan Pathol 2017 Jun;44(6):548-552

Pathology Service, Massachusetts General Hospital and Harvard Medical School, Boston, Massachusetts.

Background: Morphea (localized scleroderma) and eosinophilic fasciitis (EF) are rare fibrosing disorders which may present a diagnostic challenge. While histopathologic features are often distinct, in some cases there may be overlap. T-cells contribute to etiopathogenesis of both autoimmune conditions. Read More

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http://dx.doi.org/10.1111/cup.12947DOI Listing
June 2017
25 Reads

Diagnostic utility of Magnetic Ressonance Imaging in Eosinophilic Fasciitis.

Acta Reumatol Port 2017 Jul-Sep;42(3):271-272

Centro Hospitalar e Universitário de Coimbra.

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November 2018
12 Reads

Morphea and Eosinophilic Fasciitis: An Update.

Am J Clin Dermatol 2017 Aug;18(4):491-512

Department of Dermatology, Radboud University Medical Centre, Nijmegen, The Netherlands.

Morphea, also known as localized scleroderma, encompasses a group of idiopathic sclerotic skin diseases. The spectrum ranges from relatively mild phenotypes, which generally cause few problems besides local discomfort and visible disfigurement, to subtypes with severe complications such as joint contractures and limb length discrepancies. Eosinophilic fasciitis (EF, Shulman syndrome) is often regarded as belonging to the severe end of the morphea spectrum. Read More

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http://dx.doi.org/10.1007/s40257-017-0269-xDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5506513PMC
August 2017
14 Reads

Eosinophilic fasciitis.

An Bras Dermatol 2016 Sep-Oct;91(5 suppl 1):57-59

Escola Superior de Ciências da Saúde (ESCS) - Brasília (DF), Brazil.

Eosinophilic fasciitis is a rare sclerodermiform syndrome of unknown etiology. It is characterized by the thickening of the muscular fascia and subcutaneous tissue, with a variable infiltration of eosinophils. Peripheral eosinophilia, poly or monoclonal hypergammaglobulinemia and increased erythrocyte sedimentation rate can be seen. Read More

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http://dx.doi.org/10.1590/abd1806-4841.20164683DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5324994PMC
July 2017
9 Reads

Groove Sign of Eosinophilic Fasciitis.

J Clin Rheumatol 2017 Apr;23(3):169

From The Ronald O. Perelman Department of Dermatology, New York University Langone Medical Center, New York, NY.

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http://dx.doi.org/10.1097/RHU.0000000000000524DOI Listing
April 2017
35 Reads

A case of eosinophilic fasciitis associated with pyoderma gangrenosum.

J Eur Acad Dermatol Venereol 2017 Aug 27;31(8):e356-e358. Epub 2017 Feb 27.

Department of Dermatology, Henry Ford Hospital, Detroit, MI, 48202, USA.

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http://dx.doi.org/10.1111/jdv.14148DOI Listing
August 2017
10 Reads

Basidiobolomycosis complicated by hydronephrosis and a perinephric abscess presenting as a hypertensive emergency in a 7-year-old boy.

Paediatr Int Child Health 2018 05 23;38(2):146-149. Epub 2017 Jan 23.

a Department of Pediatrics , Jawaharlal Institute of Postgraduate Medical Education and Research (JIPMER) , Pondicherry 605006 , India.

A 7-year-old boy presented with a chronic, indurated, tender left thigh swelling in association with a hypertensive emergency. He had a bilateral moderate degree of hydronephrosis and a left perinephric abscess, and MRI features of posterior reversible encephalopathy syndrome. Histopathological examination of the biopsy specimen demonstrated eosinophilic fasciitis with filamentous fungi. Read More

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http://dx.doi.org/10.1080/20469047.2016.1162392DOI Listing
May 2018
26 Reads
0.871 Impact Factor

Eosinophilic fasciitis with subjacent myositis.

Muscle Nerve 2017 09 27;56(3):525-529. Epub 2017 Mar 27.

Department of Neurology, Mayo Clinic, 4500 San Pablo Road, Jacksonville, Florida, 32224, USA.

Introduction: Eosinophilic fasciitis (EF) is a rare disorder that can present with muscle symptoms that mimic other neuromuscular diseases.

Methods: We report the case of a 43-year-old woman with chronic muscle aches, tightness, and stiffness with hypertrophied, well-defined muscles despite physical inactivity, and thickened skin with reduced elasticity and discoloration.

Results: Except for mild peripheral eosinophilia, laboratory studies, including blood count, electrolytes, paraneoplastic panel, muscle enzymes, thyroid function, and serum protein electrophoresis, were normal. Read More

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http://dx.doi.org/10.1002/mus.25492DOI Listing
September 2017
12 Reads

A Literature Review of Eosinophilic Fasciitis with an Illustrative Case.

Curr Rheumatol Rev 2017 ;13(2):113-120

Consultant Neurologist, Salford Royal NHS Foundation Trust, United Kingdom.

Eosinophilic fasciitis (EF), a rare connective tissue disorder, was first reported by Lawrence Shulman in 1974. Since then over 300 cases have been reported worldwide. EF has variable clinical presentations and currently does not have internationally accepted diagnostic criteria. Read More

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http://www.eurekaselect.com/146170/article
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http://dx.doi.org/10.2174/1573397112666161007154703DOI Listing
May 2018
40 Reads

A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus.

Indian Dermatol Online J 2016 Sep-Oct;7(5):386-389

Department of Dermatology, Indian Naval Hospital Ship Asvini, Mumbai, Maharashtra, India.

Eosinophilic fasciitis, also known as Shulman's syndrome, is a fibrosing scleroderma-like syndrome, which is a distinct entity. A 55-year-old man, presented with progressive skin darkening, thickening, and tightening over the left lower limb since 6 months. Dermatological examination revealed a hyperpigmented indurated area on the left thigh, extending to the anterior aspect of the left leg. Read More

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http://dx.doi.org/10.4103/2229-5178.190516DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5038099PMC
October 2016
19 Reads

Progressive Contractures due to Eosinophilic Fasciitis in a 17 year old Male.

Ir Med J 2016 Apr 11;109(4):399. Epub 2016 Apr 11.

Neurology Department, Cork University Hospital, Wilton, Cork.

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April 2016
10 Reads

Shulman disease (eosinophilic fasciitis) in X-linked agammaglobulinemia.

Pol J Pathol 2016 Jun;67(2):183-8

Prof. Anna Pituch-Noworolska MD, Department of Clinical Immunology, Polish-American Institute of Pediatrics, Medical College, Jagiellonian University, Wielicka 265, 30-663 Krakow, Poland, tel./fax +48 12 658 17 56, e-mail:

X-linked agammaglobulinemia (XLA) diagnosed in the first year of life is an immunodeficiency with a life-long indication for substitution of immunoglobulins, due to lack of B lymphocytes in the periphery. The decrease of bacterial infection frequency and severity is an effect of immunoglobulin replacement. However, in the majority of patients bronchiectasis and chronic sinusitis with an overgrown mucous membrane develop despite regular substitution. Read More

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June 2016
12 Reads

High-Dose Intravenous Pulse Methotrexate in Patients With Eosinophilic Fasciitis.

JAMA Dermatol 2016 11;152(11):1262-1265

Department of Dermatology, Radboud University Medical Centre, Nijmegen, the Netherlands.

Importance: Eosinophilic fasciitis (EF) is a connective tissue disorder in which conventional treatment leads to disappointing results in a proportion of patients. Therefore, we investigated high-dose intravenous (IV) pulse methotrexate (MTX) as a treatment for EF.

Objective: To examine safety and effects of monthly high-dose IV pulse MTX in EF. Read More

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http://dx.doi.org/10.1001/jamadermatol.2016.2873DOI Listing
November 2016
13 Reads

Successful treatment of aplastic anemia-paroxysmal nocturnal hemoglobinuria associated with eosinophilic fasciitis with matched unrelated donor allogeneic peripheral blood stem cell transplantation.

Clin Case Rep 2016 Aug 6;4(8):765-7. Epub 2016 Jul 6.

Department of Leukemia The University of Texas MD Anderson Cancer Center Houston Texas USA.

We report the first patient case of successful treatment intervention for both eosinophilic fasciitis and aplastic anemia with allogeneic peripheral blood stem cell transplantation from a matched unrelated donor after multiple immunosuppressant failure. Read More

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http://dx.doi.org/10.1002/ccr3.613DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4974424PMC
August 2016
14 Reads