574 results match your criteria Ebstein Anomaly Imaging


Tricuspid Valve Imaging and Intervention in Pediatric and Adult Patients With Congenital Heart Disease.

JACC Cardiovasc Imaging 2019 Apr;12(4):637-651

Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota; Division of Cardiovascular Diseases, Mayo Clinic, Rochester, Minnesota. Electronic address:

Tricuspid valve abnormalities in congenital heart disease comprise a wide spectrum, with the most common being Ebstein anomaly and tricuspid valve dysplasia. Tricuspid valve dysfunction may also be secondary to other types of congenital heart disease, including functional tricuspid regurgitation seen in right heart volume overload conditions, such as atrial septal defect and repaired tetralogy of Fallot with severe pulmonary valve regurgitation. Congenitally corrected transposition and Mustard and Senning procedures maintain the right ventricle as the systemic ventricle, and the tricuspid valve is subject to unique hemodynamic stress not typically seen in normal circulation. Read More

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http://dx.doi.org/10.1016/j.jcmg.2018.10.036DOI Listing
April 2019
2 Reads

Uhl Anomaly in Asymptomatic Adult Woman.

Circ Cardiovasc Imaging 2019 Feb;12(2):e008277

Dipartimento di Diagnostica per Immagini, Imaging Molecolare, Radiologia Interventistica e Radioterapia, University Tor Vergata, Rome, Italy (M.F., L.P., R.F., M.C.).

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http://dx.doi.org/10.1161/CIRCIMAGING.118.008277DOI Listing
February 2019

[Redo Valve Replacement of Wada-Cutter Prosthetic Valve at Tricuspid Valve Position 47 Years After Implantation;Report of a Case].

Kyobu Geka 2018 12;71(13):1118-1121

Department of Cardiovascular Surgery, Tokyo Metropolitan Hiroo Hospital, Tokyo, Japan.

We experienced an explantation of Wada-Cutter prosthetic tilting disk valve of 47 years after implantation. The patient was 53 years old female who underwent the 1st operation for Ebstein's anomaly, which included tricuspid valve replacement (TVR), closure of atrial septal defect (ASD) and posterior annulorrhaphy when she was 6 years old. She was doing well after the 1st operation without symptom,but dyspnea and systemic edema worsened recently though increased admission of diuretics. Read More

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December 2018
4 Reads

Treatment of fetal circular shunt with non-steroidal anti-inflammatory drugs.

Ultrasound Obstet Gynecol 2018 Oct 31. Epub 2018 Oct 31.

Fetal Cardiac, Labatt Family Heart Centre, Hospital for Sick Children, University of Toronto, Toronto, Canada.

A circular shunt (CS) is a life-threatening condition consisting of massive shunting of systemic arterial blood via the ductus arteriosus to the left ventricle without traversing the lungs. In the prenatal circulation, it mainly occurs in severe Ebstein anomaly (EA) from unrestricted ductal flow and significant pulmonary and tricuspid regurgitation. We aimed to improve the fetal hemodynamics and chances of survival of affected fetuses by inducing ductal constriction with transplacental non-steroidal anti-inflammatory drugs (NSAIDs). Read More

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http://doi.wiley.com/10.1002/uog.20169
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http://dx.doi.org/10.1002/uog.20169DOI Listing
October 2018
14 Reads

Percutaneous closure of paravalvular leak after Cone repair for Ebstein's anomaly.

Catheter Cardiovasc Interv 2019 Jan 2;93(1):E46-E48. Epub 2018 Oct 2.

Department of Pediatrics, Ghent University Hospital, Ghent, Belgium.

We report the use of an Amplatzer Vascular plug for percutaneous closure of a paravalvular leak after Cone repair in a 5-year-old boy with Ebstein's anomaly. A paravalvular leak of the tricuspid valve developed gradually after Cone repair-surgery. The combination of fluoroscopy, transesophageal and transthoracic imaging during general anesthesia was necessary for correct and safe positioning of the device by percutaneous approach. Read More

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http://dx.doi.org/10.1002/ccd.27790DOI Listing
January 2019
5 Reads

Cardiovascular magnetic resonance evidence of myocardial fibrosis and its clinical significance in adolescent and adult patients with Ebstein's anomaly.

J Cardiovasc Magn Reson 2018 09 27;20(1):69. Epub 2018 Sep 27.

Department of Cardiology, West China Hospital, Sichuan University, Chengdu, 610041, Sichuan Province, China.

Background: Myocardial fibrosis is a common pathophysiological process that is related to ventricular remodeling in congenital heart disease. However, the presence, characteristics, and clinical significance of myocardial fibrosis in Ebstein's anomaly have not been fully investigated. This study aimed to evaluate myocardial fibrosis using cardiovascular magnetic resonance (CMR) late gadolinium enhancement (LGE) and T1 mapping techniques, and to explore the significance of myocardial fibrosis in adolescent and adult patients with Ebstein's anomaly. Read More

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http://dx.doi.org/10.1186/s12968-018-0488-1DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6158838PMC
September 2018
10 Reads

Ebstein's Anomaly: "The One and a Half Ventricle Heart".

Braz J Cardiovasc Surg 2018 Jul-Aug;33(4):353-361

Department of Research, U. N. Mehta Institute of Cardiology and Research Centre (affiliated to BJ medical college, Ahmedabad), Gujarat, India.

Objective: Ebstein's anomaly remains a relatively ignored disease. Lying in the 'No Man's land' between congenital and valve surgeons, it largely remains inadequately studied. We report our short-term results of treating it as a 'one and a half ventricle heart' and propose that the true tricuspid annulus (TTA) 'Z' score be used as an objective criterion for estimation of 'functional' right ventricle (RV). Read More

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http://dx.doi.org/10.21470/1678-9741-2018-0100DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6122759PMC
January 2019
43 Reads

Cavotricuspid isthmus ablation using multimodality imaging in Ebstein anomaly with a mechanical tricuspid valve replacement.

HeartRhythm Case Rep 2018 Aug 9;4(8):346-349. Epub 2018 May 9.

Division of Cardiology, Department of Internal Medicine, Pusan National University Yangsan Hospital, Pusan National University of Medicine, Yangsan, Republic of Korea.

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http://dx.doi.org/10.1016/j.hrcr.2018.04.012DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6092982PMC
August 2018
13 Reads

Right Heart-Pulmonary Circulation Unit in Congenital Heart Diseases.

Heart Fail Clin 2018 Jul;14(3):283-295

Royal Brompton and Harefield Trust, London, UK. Electronic address:

The right ventricle plays a major role in congenital heart disease. This article describes the right ventricular mechanics in some selected congenital heart diseases affecting the right ventricle in different ways: tetralogy of Fallot, Ebstein anomaly, and the systemic right ventricle. Read More

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http://dx.doi.org/10.1016/j.hfc.2018.02.005DOI Listing
July 2018
6 Reads

Impact of the cone operation on left ventricular size, function, and dyssynchrony in Ebstein anomaly: a cardiovascular magnetic resonance study.

J Cardiovasc Magn Reson 2018 05 21;20(1):32. Epub 2018 May 21.

Department of Cardiology, Boston Children's Hospital, Boston, MA, USA.

Background: In addition to tricuspid regurgitation (TR) and right ventricular (RV) enlargement, patients with Ebstein anomaly are at risk for left ventricular (LV) dysfunction and dyssynchrony. We studied the impact of the cone tricuspid valve reconstruction operation on LV size, function, and dyssynchrony.

Methods: All Ebstein anomaly patients who had both pre- and postoperative cardiovascular magnetic resonance (CMR) studies were retrospectively identified. Read More

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http://dx.doi.org/10.1186/s12968-018-0452-0DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5963144PMC
May 2018
13 Reads

Fetal and Postnatal Echocardiographic Diagnosis of Ebstein Anomaly of the Mitral Valve.

Pediatr Cardiol 2018 Aug 14;39(6):1276-1279. Epub 2018 May 14.

Rush Center for Congenital Heart Disease, Rush University Medical College, Chicago, IL, USA.

Ebstein anomaly of mitral valve (MV) is an extremely rare congenital heart disease. In the current report, we present a case of Ebstein of MV that was diagnosed prenatally. Fetal echocardiogram showed that the posterior leaflet of MV was tethered to the lateral wall of left ventricle (LV) with downward displacement into LV cavity. Read More

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http://dx.doi.org/10.1007/s00246-018-1903-yDOI Listing
August 2018
5 Reads

Intracardiac echocardiography to guide catheter ablation of an accessory pathway in Ebstein's anomaly. A case report.

Med Ultrason 2018 May;20(2):250-253

5th Department of Internal Medicine, Cardiology-Rehabilitation, "Iuliu Hatieganu" University of Medicine and Pharmacy Cluj-Napoca, Romania..

We present the case of a 17-year-old girl with Ebstein anomaly and repeated episodes of reentrant tachycardia due to a right posterior accessory pathway. Catheter ablation was performed using intracardiac echocardiography. A ViewFlex Xtra probe was inserted and showed an anormal tricuspid valve with elongated anterior leaflet and low insertion of the septal leaflet towards the apex. Read More

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http://dx.doi.org/10.11152/mu-1347DOI Listing
May 2018
10 Reads

Three-dimensional echocardiographic evaluation of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome.

Cardiol Young 2018 Jun 22;28(6):885-887. Epub 2018 Apr 22.

3Pediatric Cardiology,Children's Hospital Colorado,University of Colorado School of Medicine,Aurora,CO,USA.

We report three-dimensional imaging of a rare finding of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome, which has been previously reported only by two-dimensional echocardiography. A fetal echocardiogram was performed at 19 weeks that showed a moderately hypoplastic left ventricle, severely hypoplastic mitral valve, a severely hypoplastic aortic valve, and a dysplastic tricuspid valve. Post Caesarean delivery at 40 weeks of gestation, a transthoracic echocardiogram confirmed the findings seen on the fetal echocardiogram. Read More

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http://dx.doi.org/10.1017/S1047951118000367DOI Listing
June 2018
13 Reads

Editorial commentary: The caveats of cardiac imaging in Ebstein anomaly.

Trends Cardiovasc Med 2018 08 20;28(6):410-411. Epub 2018 Feb 20.

Cardiovascular Center Zurich, Klinik im Park, Switzerland. Electronic address:

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http://dx.doi.org/10.1016/j.tcm.2018.02.007DOI Listing
August 2018
8 Reads

Angiographic aspect of longstanding Starr-Edwards valve for type C Ebstein anomaly.

Asian Cardiovasc Thorac Ann 2018 May 27;26(4):326. Epub 2018 Mar 27.

Pediatric Cardiac Surgery and GUCH Unit, S. Orsola-Malpighi Hospital, 60273 University of Bologna, Bologna, Italy.

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http://dx.doi.org/10.1177/0218492318767793DOI Listing
May 2018
9 Reads

Clinical aspects of myocardial fibrosis in adults with Ebstein's anomaly.

Heart Vessels 2018 Sep 21;33(9):1076-1085. Epub 2018 Feb 21.

Department of Cardiology, University of Medical Sciences, ½ Dluga Street, 61-848, Poznan, Poland.

Heart failure and arrhythmia are common complications in adults with Ebstein's anomaly. They may result not only from hemodynamic alterations, but also from myocardial fibrosis. Late gadolinium enhancement (LGE) by CMR enables the evaluation of myocardial fibrosis. Read More

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http://dx.doi.org/10.1007/s00380-018-1141-5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6096744PMC
September 2018
7 Reads

Cardiac imaging in Ebstein anomaly.

Trends Cardiovasc Med 2018 08 12;28(6):403-409. Epub 2018 Jan 12.

Division of Cardiovascular Diseases, Mayo Clinic, Rochester, MN.

Ebstein anomaly is a congenital disorder of right ventricular myocardial development, which affects the tricuspid valve in addition to the right ventricular myocardium. Cardiac imaging by transthoracic echocardiography and cardiac magnetic resonance imaging are the key modalities used to assess timing and type of surgery. In this article, we review the current standards of echocardiographic and magnetic resonance imaging in Ebstein anomaly. Read More

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http://dx.doi.org/10.1016/j.tcm.2018.01.002DOI Listing
August 2018
13 Reads

Atrio-ventricular deformation and heart failure in Ebstein's Anomaly - A cardiovascular magnetic resonance study.

Int J Cardiol 2018 04 3;257:54-61. Epub 2018 Feb 3.

Department of Cardiology and Pneumology, University Medical Center, Georg-August-University Göttingen, Germany; DZHK, German Center for Heart Research, partner site Göttingen, Germany; Department of Cardiology, Royal North Shore Hospital, The Kolling Institute, Northern Clinical School, University of Sydney, Sydney, Australia. Electronic address:

Purpose: We aimed to quantify atrial and ventricular myocardial deformation in Ebstein's Anomaly (EA) in a case-control study with cardiovascular magnetic resonance (CMR) feature tracking and to correlate changes in cardiac performance with the severity of disease and clinical heart failure parameters.

Materials And Methods: Atrial and ventricular deformation was measured using CMR feature tracking in 30 EA and 20 healthy control subjects. Atrial performance was characterized using longitudinal strain and strain rate parameters for reservoir function, conduit function and booster pump function. Read More

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http://dx.doi.org/10.1016/j.ijcard.2017.11.097DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5856281PMC
April 2018
11 Reads

Going beyond morphology in Ebstein's anomaly.

Int J Cardiol 2018 04;257:75

Multimodality Cardiac Imaging Section, I.R.C.C.S. Policlinico San Donato, San Donato Milanese, Milan, Italy; Department of Pediatric Cardiology and Adult Congenital Heart Disease, I.R.C.C.S. Policlinico San Donato, San Donato Milanese, Milan, Italy.

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http://dx.doi.org/10.1016/j.ijcard.2018.01.027DOI Listing
April 2018
2 Reads

Direct assessment of tricuspid regurgitation by 4D flow cardiovascular magnetic resonance in a patient with Ebstein's anomaly.

Eur Heart J Cardiovasc Imaging 2018 05;19(5):587-588

Division of Pediatric Cardiology, Department of Pediatrics, Leiden University Medical Center, Albinusdreef 2, 2333 ZA, Leiden, The Netherlands.

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http://dx.doi.org/10.1093/ehjci/jey008DOI Listing
May 2018
8 Reads

A "congenitally corrected" variant of Ebstein's anomaly.

Cardiol Young 2018 Apr 10;28(4):608-610. Epub 2018 Jan 10.

1Department of Cardiology,Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital,Istanbul,Turkey.

Ebstein's anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein's anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function. Read More

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http://dx.doi.org/10.1017/S1047951117002712DOI Listing
April 2018
5 Reads

Left ventricular synchrony, torsion, and recoil mechanics in Ebstein's anomaly: insights from cardiovascular magnetic resonance.

J Cardiovasc Magn Reson 2017 Dec 14;19(1):101. Epub 2017 Dec 14.

Department of Cardiology and Pneumology, Georg-August-University Göttingen, University Medical Center, Robert-Koch-Str. 40, D-37099, Götttingen, Germany.

Background: Disease progression and heart failure development in Ebstein's Anomaly (EA) of the tricuspid valve is characterized by both right and left ventricular (LV) deterioration. The mechanisms underlying LV dysfunction and their role in heart failure development are incompletely understood. We hypothesized that LV dyssynchrony and impaired torsion and recoil mechanics induced by paradoxical movement of the basal septum may play a role in heart failure development. Read More

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http://dx.doi.org/10.1186/s12968-017-0414-yDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5729283PMC
December 2017
22 Reads

Radiofrequency Ablation of Atrial Fibrillation in Patients with Ebstein's Anomaly: A Two-Case Report.

Cardiology 2018;139(1):33-36. Epub 2017 Nov 29.

Department of Electrophysiology, Heart Center Duisburg, Duisburg, Germany.

Ebstein's anomaly (EA) is a rare congenital heart disease characterized by "atrialization" of the right ventricle, due to apical displacement of the tricuspid leaflets into the right ventricle. Patients with EA may develop all kinds of supraventricular arrhythmias requiring radiofrequency ablation. Atrial fibrillation (Afib) is a common arrhythmia in EA patients, and results in debilitating symptoms that often require surgical treatment. Read More

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http://dx.doi.org/10.1159/000484039DOI Listing
September 2018
4 Reads

Assessing the borderline ventricle in a term infant: combining imaging and physiology to establish the right course.

Authors:
Meryl S Cohen

Curr Opin Cardiol 2018 Jan;33(1):95-100

Division of Cardiology, The Children's Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, USA.

Purpose Of Review: The purpose of this review is to describe the challenges associated with the diagnosis and treatment of children with borderline ventricles. A borderline ventricle is one in which there is concern that it will not be able to support its circulation. If a biventricular repair is attempted and fails, outcome is often poor. Read More

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http://dx.doi.org/10.1097/HCO.0000000000000466DOI Listing
January 2018
18 Reads

Effect of cone reconstruction on right ventricular function in patients with Ebstein's anomaly: a meta-analysis.

Interact Cardiovasc Thorac Surg 2018 02;26(2):301-306

Department of Cardiovascular Surgery, West China Hospital, Sichuan University, Sichuan, China.

Objectives: Cone reconstruction (CR) is a novel technique for surgically treating the tricuspid valve and right ventricle (RV) in patients with Ebstein's anomaly. However, precise changes in the RV function after CR remain unclear. This study aimed to evaluate the RV size and New York Heart Association (NYHA) functional class by conducting a meta-analysis of reported data. Read More

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http://dx.doi.org/10.1093/icvts/ivx312DOI Listing
February 2018
12 Reads

Cardiac Resynchronization Therapy in Patients with Ebstein's Anomaly.

Int Heart J 2017 Oct 30;58(5):816-819. Epub 2017 Sep 30.

Department of Cardiovascular Medicine, Graduate School of Medicine, The University of Tokyo.

Ebstein's anomaly is a rare congenital heart disease characterized by apical displacement of the septal and posterior tricuspid valve leaflets. It is often complicated with left ventricular (LV) dysfunction as well as right-sided abnormalities. On the other hand, in the presence of LV dysfunction, right ventricular pacing is likely to aggravate the diseased LV function, which is termed pacemaker-induced cardiomyopathy. Read More

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http://dx.doi.org/10.1536/ihj.16-580DOI Listing
October 2017
24 Reads
1.130 Impact Factor

Neonatal Ebstein Anomaly.

Semin Thorac Cardiovasc Surg 2017 25;29(3):331-337. Epub 2017 Sep 25.

Surgery and Chief of Pediatric Cardiothoracic Surgery, University of Tennessee Health Sciences Center and Le Bonheur Children's Hospital, Memphis, Tennessee. Electronic address:

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http://dx.doi.org/10.1053/j.semtcvs.2017.09.006DOI Listing
October 2018
12 Reads

Change in biventricular function after cone reconstruction of Ebstein's anomaly: an echocardiographic study.

Eur Heart J Cardiovasc Imaging 2018 07;19(7):808-815

Great Ormond Street Hospital for Children, Great Ormond Street, London, UK.

Aims: The Cone reconstruction in Ebstein's anomaly (EA) aims to reduce tricuspid valve regurgitation (TR) and reposition the valve to the anatomic annulus, but post-operative progress of ventricular function is poorly understood. This study evaluated biventricular function after Cone reconstruction using echocardiographic techniques.

Methods And Results: A retrospective study assessing longitudinal change was conducted from 2009 to 2014. Read More

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http://dx.doi.org/10.1093/ehjci/jex186DOI Listing
July 2018
9 Reads

Coexistence of a Double-Chambered Right Ventricle With Ebstein-Like Anomaly and Right Ventricular Apical Hypoplasia - Usefulness of Multimodality Imaging.

Circ J 2018 03 1;82(4):1215-1217. Epub 2017 Sep 1.

Department of Cardiovascular Medicine, National Cerebral and Cardiovascular Center.

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http://dx.doi.org/10.1253/circj.CJ-17-0288DOI Listing
March 2018
20 Reads
3.940 Impact Factor

The Two Anomalies of Wilhelm Ebstein.

Tex Heart Inst J 2017 Jun 1;44(3):198-201. Epub 2017 Jun 1.

The year 2016 was the 180th anniversary of Wilhelm Ebstein's birth and the 150th anniversary of his description of the congenital tricuspid valve malformation that came to be known as Ebstein anomaly. We present a brief history of the life and work of Dr. Wilhelm Ebstein. Read More

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http://dx.doi.org/10.14503/THIJ-16-6063DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5505398PMC
June 2017
10 Reads

Prenatal Maternal Hyperoxygenation Testing and Implications for Critical Care Delivery Planning among Fetuses with Congenital Heart Disease: Early Experience.

Am J Perinatol 2018 Jan 26;35(1):16-23. Epub 2017 Jul 26.

Children's National Heart Institute, Children's National Health System, Washington, District of Columbia.

Background:  Maternal hyperoxygenation (MH) during fetal ultrasound can characterize fetal pulmonary vasoreactivity (PVr) and its associations with postnatal physiology.

Objective:  We explored MH testing to facilitate perinatal risk stratification for fetuses with congenital heart disease (CHD).

Methods:  MH was performed in 12 fetuses: 2 with Ebstein anomaly, 2 with total anomalous pulmonary venous connection (TAPVC), 4 with hypoplastic left heart syndrome (HLHS) with (a) restrictive atrial septum (RAS) or (b) intact atrial septum (IAS) with decompressing vertical vein (VV), and 4 with D-loop transposition of the great arteries (TGA). Read More

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http://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1603991
Publisher Site
http://dx.doi.org/10.1055/s-0037-1603991DOI Listing
January 2018
11 Reads

Major adverse events and atrial tachycardia in Ebstein's anomaly predicted by cardiovascular magnetic resonance.

Heart 2018 01 6;104(1):37-44. Epub 2017 Jul 6.

NIHR Cardiovascular Biomedical Research Unit, Royal Brompton Hospital, London, England.

Objectives: Patients with Ebstein's anomaly of the tricuspid valve (EA) are at risk of tachyarrhythmia, congestive heart failure and sudden cardiac death. We sought to determine the value of cardiovascular magnetic resonance (CMR) for predicting these outcomes.

Methods: Seventy-nine consecutive adult patients (aged 37±15 years) with unrepaired EA underwent CMR and were followed prospectively for a median 3. Read More

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http://dx.doi.org/10.1136/heartjnl-2017-311274DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5749347PMC
January 2018
36 Reads

Intraoperative Transesophageal Echocardiography in the Operation of Ebstein's Anomaly: A Retrospective Study.

Chin Med J (Engl) 2017 Jul;130(13):1540-1543

Heart Center, First Hospital of Tsinghua University, Beijing 100016, China.

Background: Ebstein's anomaly (EA) has various spectrums in clinical and anatomic features. This study aimed to report the experience of two-dimensional intraoperative transesophageal echocardiography (2D-ITEE) during the EA surgery and to analyze the characteristics of the tricuspid valve (TV) by comparing the data from 2D-ITEE with the results from the surgery.

Methods: 2D-ITEE data of 164 patients with EA who were operated in the First Hospital of Tsinghua University between July 2004 and April 2014 were retrospectively analyzed in this study. Read More

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http://dx.doi.org/10.4103/0366-6999.208233DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5494916PMC
July 2017
9 Reads

Surgical Correction for a Neonate With Ebstein's Anomaly Associated With Tetralogy of Fallot.

Ann Thorac Surg 2017 Jul;104(1):e79-e81

Department of Surgery, National Taiwan University Hospital and Medical College, National Taiwan University, Taipei, Taiwan. Electronic address:

Ebstein's anomaly in combination with tetralogy of Fallot (TOF) is rare. We report a male infant with these combined anomalies who presented with severe cyanosis, heart failure, and respiratory distress after birth. Biventricular repair was successfully performed with 1-stage correction of his ventricular septal defect (VSD), right ventricular outflow tract (RVOT) obstruction, and tricuspid regurgitation. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2017.01.082DOI Listing
July 2017
7 Reads

Ebstein's anomaly in adults: Modified cone reconstruction of the tricuspid valve is associated with promising outcomes.

Arch Cardiovasc Dis 2017 May 26;110(5):325-333. Epub 2017 May 26.

Marie-Lannelongue Hospital, Department of Pediatric and Congenital Heart Disease, 92330 Le Plessis Robinson, France.

Background: Ebstein's anomaly is a complex malformation. Justification of a procedure in mildly symptomatic adults is debatable: repair techniques are demanding and valve replacement is associated with poorer outcome.

Objectives: We report our initial experience with the cone procedure versus medical follow-up. Read More

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http://dx.doi.org/10.1016/j.acvd.2017.03.003DOI Listing
May 2017
18 Reads

The Cone Technique for Ebstein Repair. First Cases.

Rev Esp Cardiol (Engl Ed) 2018 Jun 18;71(6):490-491. Epub 2017 May 18.

Instituto de Investigación Sanitaria Gregorio Marañón, Madrid, Spain; Servicio de Cardiología Pediátrica, Hospital Universitario Gregorio Marañón, Madrid, Spain.

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http://dx.doi.org/10.1016/j.rec.2017.04.019DOI Listing
June 2018
4 Reads

Surgical Strategy Toward Biventricular Repair for Severe Ebstein Anomaly in Neonates and Infancy.

Ann Thorac Surg 2017 Sep 21;104(3):917-925. Epub 2017 Apr 21.

Department of Surgery, National Taiwan University Hospital, National Taiwan University College of Medicine, Taipei, Taiwan.

Background: Neonates with severe forms of Ebstein anomaly present a surgical challenge, and the Starnes operation as single ventricle palliation is highly advocated. Cone reconstruction for tricuspid valvuloplasty (TVP) has become a widely accepted technique, although very few cases of TVP have been reported in neonates. This report describes a surgical strategy for neonatal Ebstein anomaly, with an aim toward biventricular repair. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2017.01.081DOI Listing
September 2017
41 Reads

Right Atrial Dysfunction in the Fetus with Severely Regurgitant Tricuspid Valve Disease: A Potential Source of Cardiovascular Compromise.

J Am Soc Echocardiogr 2017 Jun 11;30(6):579-588. Epub 2017 Apr 11.

Fetal & Neonatal Cardiology Program, Division of Cardiology, Department of Pediatrics, Women & Children's Health Research Institute and Mazankowski Alberta Heart Institute, University of Alberta, Edmonton, Alberta, Canada; Department of Obstetrics & Gynecology, Women & Children's Health Research Institute and Mazankowski Alberta Heart Institute, University of Alberta, Edmonton, Alberta, Canada. Electronic address:

Background: In severe right heart obstruction (RHO), redistribution of cardiac output to the left ventricle (LV) is well tolerated by the fetal circulation. Although the same should be true of severely regurgitant tricuspid valve disease (rTVD) with reduced or no output from the right ventricle, affected fetuses more frequently develop hydrops or suffer intrauterine demise. We hypothesized that right atrium (RA) function is altered in rTVD but not in RHO, which could contribute to differences in outcomes. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S08947317173000
Publisher Site
http://dx.doi.org/10.1016/j.echo.2017.01.002DOI Listing
June 2017
15 Reads

Assessment of left ventricular deformation in patients with Ebstein's anomaly by cardiac magnetic resonance tissue tracking.

Eur J Radiol 2017 Apr 18;89:20-26. Epub 2017 Jan 18.

Department of Radiology, West China Second University Hospital, Sichuan University, 20# Section 3 South Renmin Road, Chengdu, Sichuan 610041, China.

Purpose: The aim of this study was to clarify the feasibility of myocardial strain using cardiovascular magnetic resonance (CMR) for the evaluation of left ventricular (LV) deformation in patients with Ebstein's anomaly (EA).

Materials And Methods: We recruited 32 patients with EA and 30 controls for CMR examination and measured LV function, dimension and tissue tracking parameters (the global and regional radial, circumferential and longitudinal peak strain), together with the right ventricle (RV) dimension. LV strain parameters were compared among the controls, patients with preserved LV ejection fraction (LVEF; ≥55%), and patients with reduced LVEF (<55%). Read More

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http://dx.doi.org/10.1016/j.ejrad.2017.01.013DOI Listing
April 2017
18 Reads

Modified Cone Reconstruction of the Tricuspid Valve for Ebstein Anomaly as Performed in Siberia.

Tex Heart Inst J 2017 Feb 1;44(1):39-42. Epub 2017 Feb 1.

The cone reconstruction technique, first described by da Silva and modified by Dearani and by others, has become the repair method of choice in patients with Ebstein anomaly of the tricuspid valve. This report details the outcome of the modified cone reconstruction technique in 6 children who underwent surgical correction of Ebstein anomaly at the Tomsk Institute of Cardiology in Siberia. From 2012 through 2015, 4 boys and 2 girls (age range, 11 mo-12 yr) underwent surgery to correct Ebstein anomaly. Read More

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http://dx.doi.org/10.14503/THIJ-16-5832DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5317358PMC
February 2017
9 Reads

[Ebstein's anomaly revealed by fetal-placental anasarca. Original case study].

Pan Afr Med J 2016 28;24:279. Epub 2016 Jul 28.

Equipe de Recherche en Santé et Nutrition du Couple Mère Enfant, Service de Médecine et de Réanimation Néonatale à l'Hôpital d'Enfant de Rabat, Faculté de Médecine et de Pharmacie, Université Mohammed V, Rabat, Maroc.

Ebstein's anomaly is a congenital heart defect rarely revealed by fetal-placental anasarca. Our study reports an original case of Ebstein's anomaly diagnosed during fetal-placental anasarca assessment, revealed by antenatal ultrasound, objectifying hydramnios, ascites and pericardial effusion. Echocardiography allowed the identification of Ebstein's disease with significant tricuspid insufficiency, mitral regurgitation (grade 3) and patent ductus arteriosus. Read More

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http://dx.doi.org/10.11604/pamj.2016.24.279.9970DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5267876PMC
March 2017
3 Reads

Prevention preferable to treatment: 3 case reports of patients experiencing right-sided heart failure after Ebstein anomaly correction.

Medicine (Baltimore) 2017 Jan;96(1):e5627

Department of Anesthesiology and Translational Neuroscience Center, West China Hospital, Sichuan University, Chengdu, China.

Rationale: Ebstein anomaly is a common congenital heart disease that may induce severe tricuspid regurgitation and dilation of the "atrialized" portion of the right ventricle. Patients who undergo surgery to correct Ebstein anomaly are at high risk of postoperative right-sided heart failure, yet little is known about what pre-, peri-, or postoperative procedures may help reduce this risk.

Patient Concerns: Here, we describe 3 cases of adults with Ebstein anomaly who underwent corrective surgery and in whom right-sided heart failure occurred with severe tricuspid regurgitation detected by transesophageal echocardiography. Read More

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http://dx.doi.org/10.1097/MD.0000000000005627DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5228659PMC
January 2017
13 Reads

[Congenital heart disease: Recent technical advances in three-dimensional echocardiography].

Presse Med 2017 May 4;46(5):482-489. Epub 2017 Jan 4.

CHU de Toulouse, Children Hospital, Paediatric Cardiology Unit, 31000 Toulouse, France.

The recent technical advances allow the use in practice of three-dimensional echocardiography in children especially through the new high frequency matrix probe. It is difficult or even impossible to hold breathing during children' acquisition so to avoid motion full volume artifact, one beat and live 3D modes are suitable. 3D echocardiography is more accurate than 2D to assess the size, location, and relationship with surrounding structures of atrial and ventricular septal defects and thus helps in the therapeutic decision. Read More

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http://dx.doi.org/10.1016/j.lpm.2016.11.016DOI Listing
May 2017
29 Reads

Assessment of Progressive Pathophysiology After Early Prenatal Diagnosis of the Ebstein Anomaly or Tricuspid Valve Dysplasia.

Am J Cardiol 2017 Jan 29;119(1):106-111. Epub 2016 Sep 29.

Division of Cardiology, Department of Pediatrics, University of California, San Francisco, San Francisco, California.

In fetuses with Ebstein anomaly or tricuspid valve dysplasia (EA/TVD), poor hemodynamic status is associated with worse neonatal outcome. It is not known whether EA/TVD fetuses with more favorable physiology earlier in gestation progress to more severe disease in the third trimester. We evaluated if echocardiographic indexes in EA/TVD fetuses presenting <24 weeks of gestation are reliable indicators of physiologic status later in pregnancy. Read More

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http://dx.doi.org/10.1016/j.amjcard.2016.09.022DOI Listing
January 2017
30 Reads

Unguarded tricuspid orifice---a rare cause of fetal right atrial dilatation with characteristic color doppler sign: Case report with review of literature.

J Clin Ultrasound 2017 Jul 18;45(6):370-374. Epub 2016 Oct 18.

Feto-Maternal Medicine, Centre for Infertility and Assisted Reproduction, Edappal Hospitals Private Limited, Edappal, Kerala, India, 679576.

The anatomic causes for fetal right atrial dilatation with tricuspid regurgitation include Ebstein anomaly, tricuspid dysplasia, unguarded tricuspid orifice, and Uhl anomaly. Unguarded tricuspid orifice is characterized by complete or partial agenesis of the tricuspid valvular and subvalvular structures. It is commonly associated with pulmonary atresia. Read More

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http://dx.doi.org/10.1002/jcu.22416DOI Listing
July 2017
22 Reads
0.801 Impact Factor

Ebstein's Anomaly with Various Unexplained Arrhythmias in a 57-Year Old Man.

J Assoc Physicians India 2016 02;64(2):74-76

Junior Resident.

There are very few congenital cardiac disease which may remain asymptomatic up to adulthood, Ebstein's anomaly is one of them. With rapid advancement in the field of echocardiography many new cases identified in day-to-day practice. Timely surgical intervention in these cases may distinct survival advantage. Read More

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February 2016

Natural Course of Adult Ebstein Anomaly When Treated according to Current Recommendation.

J Korean Med Sci 2016 Nov;31(11):1749-1754

Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.

The objectives of this study were to assess the clinical outcomes of adults with Ebstein Anomaly (EA) according to their treatment modalities. All adult EA patients diagnosed between October 1994 and October 2014 were retrospectively evaluated by medical record review. Total 60 patients were categorized into 3 groups according to their treatment strategy, i. Read More

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http://dx.doi.org/10.3346/jkms.2016.31.11.1749DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5056206PMC
November 2016
14 Reads

Atypical And Severe Enlargement Of Right Atrium.

Acta Biomed 2016 09 13;87(2):191-3. Epub 2016 Sep 13.

Parma University Hospital, Parma, Italy.

A 76 year-old woman was admitted to the Emergency Department for recent-onset dyspnea and cough. The electrocardiogram was considered inconclusive. A thoracic X-ray showed global cardiac profile enlargement. Read More

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September 2016
9 Reads