695 results match your criteria Ebstein Anomaly Imaging


Comprehensive Evaluation of Pediatric Patients with Ebstein Anomaly Requires Both Echocardiography and Cardiac Magnetic Resonance Imaging.

Pediatr Cardiol 2022 Jun 21. Epub 2022 Jun 21.

Department of Pediatric Cardiology, Amalia Children's Hospital, University Medical Center Nijmegen, Nijmegen, 6525GA, The Netherlands.

With the trend towards childhood surgery in patients with Ebstein anomaly (EA), thorough imaging is crucial for patient selection. This study aimed to assess biventricular function by echocardiography and cardiac magnetic resonance (CMR) and compare EA severity classifications. Twenty-three patients (8-17 years) underwent echocardiography and CMR. Read More

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Ebstein Anomaly-Of Veils and Visions.

JAMA 2022 06;327(22):2173-2174

Department of Cardiovascular Surgery, Mayo Clinic, Rochester, Minnesota.

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Editorial: Left, but not right, ventricular status determines heart failure in adults with Ebstein anomaly - A case-control study based on magnetic resonance.

Int J Cardiol 2022 Aug 20;361:38-39. Epub 2022 May 20.

The Center for Ultrasound Molecular Imaging and Therapeutics, Department of Medicine, The University of Pittsburgh, 15213, PA, United States of America. Electronic address:

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Moyamoya Disease Complicating Ebstein's Anomaly.

Intern Med 2022 May 14. Epub 2022 May 14.

Department of Cardiology and Nephrology, Mie University Graduate School of Medicine, Japan.

Ebstein's anomaly is an uncommon congenital disorder affecting the tricuspid valve. We herein report a 38-year-old woman who experienced consciousness and sensory disturbance during treatment for heart failure caused by Ebstein's anomaly. Urgent magnetic resonance imaging and cerebral angiography demonstrated acute cerebral infarction and internal carotid artery obstruction with the development of collateral arteries. Read More

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Left, but not right, ventricular status determines heart failure in adults with Ebstein anomaly - A case-control study based on magnetic resonance.

Int J Cardiol 2022 Jul 26;358:39-44. Epub 2022 Apr 26.

1(st) Department of Cardiology, University of Medical Sciences, Poznan, Poland; 1-2 Dluga Street, 61-848 Poznan, Poland.

Background: Ebstein anomaly (EA) is a congenital heart defect affecting the right heart. Heart failure (HF) is a significant complication in adults with EA. It may result not only from the right ventricle (RV), but also from the left ventricle (LV) abnormalities. Read More

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[Successful Surgical Repair for Adult Ebstein Disease Using Cone Reconstruction Combined with One and a Half Ventricle Repair].

Kyobu Geka 2022 Feb;75(2):92-97

Second Department of Surgery, Yamagata University Faculty of Medicine, Yamagata, Japan.

A 67-year-old woman presented with dyspnea on effort and cyanosis due to massive tricuspid regurgitation and an atrial septal defect with right to left shunt. She was diagnosed with Ebstein disease at the age of 53 when she underwent surgery for varicose veins. Echocardiography showed the severe apical displacement of the septal and posterior leaflet. Read More

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February 2022

The Mid-Term Outcomes of Cone Repair or Replacement of Tricuspid Valve in Patients with Ebstein's Anomaly: Our Experience.

Heart Surg Forum 2022 Jan 17;25(1):E030-E036. Epub 2022 Jan 17.

Department of Cardiac Surgery, National Heart Foundation Hospital and Research Institute, Mirpur, Dhaka-1216, Bangladesh.

Background: Cone repair of the tricuspid valve (TV) is a contemporary reproducible technique for surgical reconstruction of Ebstein's anomaly. Different authorities have shown that this technique restores excellent tricuspid valve function. In Bangladesh, this technique still is unfamiliar to many. Read More

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January 2022

Accuracy of Deep Learning Echocardiographic View Classification in Patients with Congenital or Structural Heart Disease: Importance of Specific Datasets.

J Clin Med 2022 Jan 28;11(3). Epub 2022 Jan 28.

Department of Cardiology III-Adult Congenital and Valvular Heart Disease, University Hospital Muenster, Albert-Schweitzer-Campus 1, 48149 Muenster, Germany.

Introduction: Automated echocardiography image interpretation has the potential to transform clinical practice. However, neural networks developed in general cohorts may underperform in the setting of altered cardiac anatomy.

Methods: Consecutive echocardiographic studies of patients with congenital or structural heart disease (C/SHD) were used to validate an existing convolutional neural network trained on 14,035 echocardiograms for automated view classification. Read More

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January 2022

Left Ventricular Dysfunction in Neonatal Ebstein's Anomaly and Tricuspid Valve Dysplasia.

J Am Soc Echocardiogr 2022 May 31;35(5):503-512.e3. Epub 2022 Jan 31.

Fetal & Neonatal Cardiology Program, Division of Cardiology, Department of Pediatrics, Women & Children Health Research Institute, University of Alberta, Edmonton, Alberta, Canada.

Background: The mechanisms and prognostic importance of left ventricular (LV) dysfunction in neonatal Ebstein's anomaly (EA) and tricuspid valve dysplasia (TVD) are not well understood. The authors recently demonstrated reduced cardiac output and dyssynchrony to be common in fetal EA/TVD and therefore hypothesized that LV dysfunction may be associated with worse outcomes in neonatal EA/TVD.

Methods: A multicenter retrospective case-control study was conducted among neonatal patients with EA/TVD (n = 32) and a healthy control cohort (n = 17) encountered from 2004 to 2019. Read More

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Impact of fetal haemodynamics on surgical and neurodevelopmental outcomes in patients with Ebstein anomaly and tricuspid valve dysplasia.

Cardiol Young 2022 Jan 6:1-12. Epub 2022 Jan 6.

Division of Pediatric Cardiology, Department of Pediatrics, The Hospital for Sick Children, University of Toronto, ON, Canada, Toronto.

Objectives: To evaluate the impact of fetal haemodynamics on surgical and neurodevelopmental outcomes in severe Ebstein anomaly and tricuspid valve dysplasia.

Methods: Thirty-four fetuses with Ebstein anomaly/tricuspid valve dysplasia were referred from 2013 to 2019 for fetal echocardiography and clinical management. Nineteen fetuses with Ebstein anomaly/tricuspid valve dysplasia and 30 controls underwent cardiovascular magnetic resonance to quantify the fetal blood flow and to calculate cerebral oxygen delivery (cDO2) and consumption (cVO2). Read More

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January 2022

A case of redo tricuspid valve repair after neonatal cone operation for Ebstein's anomaly.

Gen Thorac Cardiovasc Surg 2022 Mar 29;70(3):289-291. Epub 2021 Nov 29.

Department of Cardiovascular Surgery, Kyoto Prefectural University of Medicine, Kyoto, Japan.

Cone reconstruction for Ebstein's anomaly, although effective, is challenging in neonatal cases. Very few reports have discussed recurrent regurgitation. Herein, we report a successful redo tricuspid valve repair for recurrent regurgitation 5 years after cone reconstruction. Read More

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Ebstein Anomaly and Right Aortic Arch in Patient with Charge Syndrome.

Medicina (Kaunas) 2021 Nov 13;57(11). Epub 2021 Nov 13.

Department of Pediatrics, Riga Stradins University, LV-1007 Riga, Latvia.

Ebstein anomaly is a rare congenital heart disease characterized by a varying degree of anatomical and functional abnormalities of tricuspid valve and right ventricle. It often coexists with other congenital cardiac malformations. Up to 79-89% of patients with Ebstein anomaly have interatrial communication in the form of patent oval foramen or atrial septal defect and more than one-third has other types of cardiac malformations. Read More

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November 2021

Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy.

Am J Case Rep 2021 Nov 24;22:e933677. Epub 2021 Nov 24.

Department of Congenital Heart Diseases, A.N. Bakoulev National Medical Research Center of Cardiovascular Surgery, Moscow, Russian Federation.

BACKGROUND The cardiotoxic effects of chemotherapy in cancer treatment can damage cardiomyocytes. A common link in the pathogenesis is the proliferation of fibroblasts and the increase of collagen synthesis, leading to development of common endomyocardial fibrosis. The walls of ventricles become rigid and their inability to relax prevents them from carrying the required amount of blood. Read More

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November 2021

Imaging for Transcatheter Edge-to-Edge Repair for Tricuspid Regurgitation in Ebstein Anomaly.

Circ Cardiovasc Imaging 2021 11 11;14(11):e013327. Epub 2021 Nov 11.

Li Ka Shing Institute of Health Science, The Chinese University of Hong Kong, Hong Kong SAR, China (K.K., K.S., A.P.-W.L.).

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November 2021

The Association of Pulmonary Flow Characteristics With Cardiac Function in Tricuspid Valve Malformation Fetuses: Study With Two-Dimensional Speckle Tracking Echocardiography.

J Ultrasound Med 2022 Jul 2;41(7):1791-1805. Epub 2021 Nov 2.

Department of Ultrasound Medicine, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China.

Objectives: To explore the relationship between cardiac function and pulmonary flow characteristics in tricuspid valve malformation (TVM) fetuses by conventional and speckle tracking echocardiography.

Methods: Eighty-eight TVM fetuses were retrospectively included and compared with 80 normal controls. TVM fetuses in each trimester were divided into two subgroups according to pulmonary flow characteristics: those with normal pulmonary flow (TVM-N) and those with reduced or absent pulmonary flow (TVM-R/A). Read More

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Improved Tricuspid Valve Function, Preload Recruitment and Ventricular Efficiency During Submaximal Exercise in Patients with Unoperated Ebstein's Anomaly: An MRI Study.

J Magn Reson Imaging 2022 06 15;55(6):1843-1850. Epub 2021 Oct 15.

Congenital Heart Disease and Pediatric Cardiology, German Heart Center Munich, Technical University of Munich, Munich, Germany.

Background: Adolescents and adults with native Ebstein's anomaly (EA) are at the benign part of the Ebstein spectrum, having survived infancy without surgery. In this population, surgical indication and timing remain objects of controversy and depend, among other factors, on exercise capacity.

Purpose: To better understand the pathophysiology of exercise adaptation in native EA. Read More

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Cone Reconstruction for Ebstein Anomaly: Ventricular Remodeling and Preliminary Impact of Stem Cell Therapy.

Mayo Clin Proc 2021 12 1;96(12):3053-3061. Epub 2021 Sep 1.

Wanek Family Program for Hypoplastic Left Heart Syndrome, Mayo Clinic, Rochester, MN; Department of Cardiovascular Surgery, Mayo Clinic, Rochester, MN.

Objective: To define the impact of tricuspid valve cone reconstruction (CR) on ventricular performance in Ebstein anomaly, both independently and after stem cell therapy.

Patients And Methods: The control group included 257 patients who had CR between June 2007 and December 2019. Ten subjects of a phase I stem cell therapy trial (May 2017 - March 2019) were compared with the controls to assess the echocardiographic impact on ventricular remodeling. Read More

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December 2021

Ebstein's Anomaly: Review of Arrhythmia Types and Morphogenesis of the Anomaly.

JACC Clin Electrophysiol 2021 09 25;7(9):1198-1206. Epub 2021 Aug 25.

Cardiology, Section of Cardiac Electrophysiology, University of California-San Francisco, San Francisco, California, USA.

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September 2021

Intraparenchymal Brain Abscess in an Adult Male With Underlying Ebstein Anomaly and Cor Triatriatum Dexter.

JACC Case Rep 2021 Feb 27;3(2):194-197. Epub 2021 Jan 27.

Department of Critical Care Medicine, Inova Fairfax Medical Campus, Falls Church, Virginia, USA.

A 21-year-old man presented with new-onset seizures and brain abscess. Echocardiography and cardiac magnetic resonance imaging revealed underlying Ebstein anomaly, secundum atrial septal defect, and cor triatriatum dexter. The elevated right heart pressures shunting through the septal defect and transient bacteremia were the likely mechanisms for his presentation. Read More

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February 2021

A simplified repair method for adult Ebstein's anomaly.

J Card Surg 2021 Sep 14;36(9):3368-3370. Epub 2021 Jun 14.

Department of Cardiovascular and Thoracic Surgery, The Affiliated Drum Tower Hospital of Nanjing University Medical School, Nanjing, Jiangsu, China.

Ebstein's anomaly (EA) is a rare but difficult to manage congenital heart disease with a wide spectrum of clinical manifestations. We present a simplified repair method which combines the plication of the atrialized right ventricle, tricuspid leaflet repair and ring annuloplasty. This method is suitable for older adult EA patients with progressive right heart dysfunction symptoms. Read More

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September 2021

MRI characterization of hemodynamic patterns of human fetuses with cyanotic congenital heart disease.

Ultrasound Obstet Gynecol 2021 Dec;58(6):824-836

Division of Paediatric Cardiology, Department of Paediatrics, Hospital for Sick Children, University of Toronto, Toronto, Canada.

Objectives: To characterize, using magnetic resonance imaging (MRI), the distribution of blood flow and oxygen transport in human fetuses with subtypes of congenital heart disease (CHD) that present with neonatal cyanosis.

Methods: Blood flow was measured in the major vessels of 152 late-gestation human fetuses with CHD and 40 gestational-age-matched normal fetuses, using cine phase-contrast MRI. Oxygen saturation (SaO ) was measured in the major vessels of 57 fetuses with CHD and 40 controls. Read More

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December 2021

Surgical treatment of Ebstein anomaly in pediatric patients: A 10-year single-center study.

J Card Surg 2021 Sep 30;36(9):3138-3145. Epub 2021 May 30.

Department of Pediatric Cardiovascular Surgery, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Education and Research Hospital, Istanbul, Turkey.

Objective: We report the early and long-term results of the strategies and surgical methods used in our center to treat pediatric patients who underwent surgical intervention to correct Ebstein anomaly (EA) in our center.

Materials And Methods: In our study, a consecutive sample of 29 patients who underwent surgery for EA between February 2011 and February 2020 in our center were evaluated retrospectively.

Results: The 29 patients underwent a total of 40 operations. Read More

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September 2021

Repair of Ebstein's anomaly-The devils in the fine print.

J Card Surg 2021 Sep 30;36(9):3146. Epub 2021 May 30.

University of Tennessee Health Sciences Center and Le Bonheur Children's Hospital, Memphis, Tennessee, USA.

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September 2021

Commentary: Ebstein Anomaly - Still So Many Unanswered Questions.

Semin Thorac Cardiovasc Surg 2022 15;34(1):213-214. Epub 2021 May 15.

Department of Cardiovascular Surgery, Mayo Clinic, Rochester, Minnesota. Electronic address:

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The Association of Age and Repair Modification with Outcome after Cone Repair for Ebstein's Malformation.

Semin Thorac Cardiovasc Surg 2022 7;34(1):205-212. Epub 2021 May 7.

Department of Cardiac Surgery, Boston Children's Hospital, Boston, Massachusetts; Harvard Medical School, Boston, Massachusetts. Electronic address:

Cone repair (CR) uses native tissue for tricuspid valve (TV) repair and provides potential for growth. Results after CR were investigated in different age groups including several surgical modifications. Single institution retrospective analysis of all CR excluding neonatal procedures. Read More

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COVID-19-Positive Patient and Hypoxemia: Are Lungs Always to Be Blamed?

JACC Cardiovasc Interv 2021 05 14;14(9):e101-e102. Epub 2021 Apr 14.

Section of Cardiology, Cardiac Sciences Program, St Boniface Hospital, University of Manitoba, Winnipeg, Manitoba, Canada. Electronic address:

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Uncommon mitral valve anomalies associated with Ebstein anomaly.

Rev Esp Cardiol (Engl Ed) 2021 08 27;74(8):717-719. Epub 2021 Mar 27.

Departamento de Ecocardiografía Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, Mexico City, Mexico. Electronic address:

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Myocardial Fibrosis in Pediatric Patients With Ebstein's Anomaly.

Circ Cardiovasc Imaging 2021 03 16;14(3):e011136. Epub 2021 Mar 16.

Division of Cardiology, Department of Paediatrics (S.A., M.S., L.G.-W.), The Hospital for Sick Children, University of Toronto, Ontario, Canada.

Background: Left ventricular dysfunction in Ebstein's anomaly (EA) is associated with higher mortality. The health of the left ventricular myocardium in children and adolescents with EA has not been investigated in detail.

Methods: Patients with unrepaired EA who had undergone cardiac magnetic resonance imaging including T1 mapping were retrospectively reviewed. Read More

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