2,134 results match your criteria Ebstein Anomaly


Ebstein anomaly associated with cri du chat (cat's cry) syndrome and 20q duplication.

BMJ Case Rep 2020 Jun 1;13(6). Epub 2020 Jun 1.

Department of Pediatrics, Neonatology, Fundacion Santa Fe de Bogota Hospital Universitario, Bogota, Colombia.

Ebstein anomaly is a congenital heart defect with a low prevalence and high mortality in the early stages of life. In medical literature, there is no reported association between Ebstein anomaly and cri du chat syndrome. Here, we report the case of a full-term newborn with a low weight for his age and who had a prenatal diagnosis of Ebstein anomaly and a postnatal diagnosis of cri du chat syndrome and 20q duplication detected on array CGH. Read More

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http://dx.doi.org/10.1136/bcr-2019-233766DOI Listing

Ebstein anomaly combined with unique pulmonary venous abnormality in a 9-month-old child.

Cardiol Young 2020 Jun 2:1-3. Epub 2020 Jun 2.

Division of Pediatric Cardiology, Department of Pediatrics, University of Arkansas for Medical Sciences and Arkansas Children's Research Institute, Little Rock, AR, USA.

Ebstein anomaly is a rare CHD known for its wide spectrum of presentation with the age of diagnosis dependent on the malformation's severity. Here, the authors describe a case of delayed diagnosis of Ebstein anomaly, secondary to lack of medical attention, which resulted in severe tricuspid regurgitation and pulmonary hypertension. Furthermore, the case was complicated by a unique pulmonary venous abnormality. Read More

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http://dx.doi.org/10.1017/S1047951120001249DOI Listing

Heart failure in the adult Ebstein patient.

Heart Fail Rev 2020 May 29. Epub 2020 May 29.

Department of Medicine, Division of Cardiovascular Medicine, Stanford University School of Medicine, 870 Quarry Road - Falk CVRC, Stanford, CA, 94305-5406, USA.

Ebstein anomaly comprises approximately 1% of all congenital heart diseases. It occurs when the tricuspid valve fails to properly delaminate from the right ventricle, resulting in a clinical spectrum of abnormal tricuspid valve morphology and right ventricular dysfunction. Due to the anatomy of the tricuspid valve and right ventricle, as well as associated right- and left-sided pathology, patients are at risk for both right and left ventricular failure and the associated symptoms of each. Read More

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http://dx.doi.org/10.1007/s10741-020-09930-2DOI Listing

Rapid two-stage Starnes approach in high-risk neonates with Ebstein anomaly.

Eur J Cardiothorac Surg 2020 May 27. Epub 2020 May 27.

Department of Cardiology, Kanagawa Children's Medical Center, Yokohama, Japan.

Objectives: The purpose of this study is to review the short- and long-term outcomes of high-risk neonates with Ebstein anomaly treated with a newly developed rapid 2-stage Starnes procedure, which is aimed at reducing the size of the enlarged right side of the heart.

Methods: Fifty-two foetuses with Ebstein anomaly were analysed in this study and divided into 2 groups. The control group comprised 25 foetuses, referred to us before 2008, and the study group was composed of 27 foetuses, referred to us after 2009. Read More

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http://dx.doi.org/10.1093/ejcts/ezaa139DOI Listing

Diagnosis of Ebstein Anomaly with Atrial Septal Defect and Persistent Left Superior Vena Cava Using Cardiac Magnetic Resonance Imaging.

J Cardiovasc Imaging 2020 May 27. Epub 2020 May 27.

Department of Radiology, Soonchunhyang University Hospital, Seoul, Korea.

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http://dx.doi.org/10.4250/jcvi.2019.0132DOI Listing

Does addition of bi-directional cavo-pulmonary shunt to tricuspid repair in advanced cases of Ebstein anomaly result in better outcomes?

Gen Thorac Cardiovasc Surg 2020 May 20. Epub 2020 May 20.

Department of Cardiac Anesthesia, U. N. Mehta Institute of Cardiology and Research Center, Ahmedabad, India.

Objectives: Ebstein anomaly can be managed by single ventricular, bi-ventricular and one and a half ventricular repairs. We present midterm results of Comprehensive Tricuspid Valve repair (CTVR) with bi-directional cavo-pulmonary shunt (BCPS).

Methods: In this prospective observational study (Jan2012-July2018), 69 patients underwent surgery for Ebstein anomaly. Read More

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http://dx.doi.org/10.1007/s11748-020-01379-2DOI Listing

Perioperative Risk Factors for Mortality in Patients Undergoing Surgery for Ebstein's Anomaly at a Single Institution: A Retrospective Analysis.

Heart Surg Forum 2020 04 3;23(2):E193-E199. Epub 2020 Apr 3.

Department of Anesthesiology, University Hospitals of Leuven, Leuven, Belgium.

Background: Mortality after cardiac surgery for Ebstein's anomaly ranges from 2.5% to 31%. Independent predictors for mortality and morbidity remain poorly defined because of the low incidence of this congenital anomaly. Read More

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http://dx.doi.org/10.1532/hsf.2755DOI Listing

An ontology-based classification of Ebstein's anomaly and its implications in clinical adverse outcomes.

Int J Cardiol 2020 Apr 26. Epub 2020 Apr 26.

Department of Laboratory Medicine, State Key Laboratory of Cardiovascular Disease, Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing 100037, China. Electronic address:

Background: Ebstein's anomaly (EA) is a rare congenital heart disease with significantly phenotypic heterogeneity, accompanied with multiple associated phenotypes. The classification of cases with EA based on a standardized vocabulary of phenotypic abnormalities from Human Phenotype Ontology (HPO) and its association with adverse clinical outcomes has yet to be investigated.

Methods: We developed a deep phenotyping algorithm for Chinese electronic medical records (EMRs) from the Chinese National Cardiovascular Center at the Fuwai Hospital to ascertain EA cases. Read More

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http://dx.doi.org/10.1016/j.ijcard.2020.04.073DOI Listing

Dynamic Slow-Motion Display in the Diagnosis of Functional Pulmonary Atresia in Fetal Ebstein Anomaly.

Authors:
Noboru Inamura

CASE (Phila) 2020 Apr 24;4(2):57-58. Epub 2019 Oct 24.

Department of Pediatrics, Kindai University Faculty of Medicine, Osakasayama, Japan.

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http://dx.doi.org/10.1016/j.case.2019.07.009DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7175753PMC

Right Ventricular Systolic Function After the Cone Procedure for Ebstein's Anomaly: Comparison Between Echocardiography and Cardiac Magnetic Resonance.

Pediatr Cardiol 2020 Apr 25. Epub 2020 Apr 25.

Echocardiography Laboratory, Hospital Israelita Albert Einstein, Av. Albert Einstein, 627/701, Morumbi, São Paulo, SP, 05652-900, Brazil.

Although the Cone procedure has improved outcomes for patients with Ebstein´s anomaly (EA), neither RV systolic function recovery in long-term follow-up nor the best echocardiographic parameters to assess RV function are well established. Thus, we evaluated RV performance after the Cone procedure comparing two-dimensional (2DEcho) and three-dimensional (3DEcho) echocardiography to cardiac magnetic resonance (CMR). We assessed 27 EA patients after the Cone procedure (53% female, median age of 20 years at the procedure, median post-operative follow-up duration of 8 years). Read More

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http://dx.doi.org/10.1007/s00246-020-02347-6DOI Listing

Right Ventricular Failure and Congenital Heart Disease.

Cardiol Clin 2020 May;38(2):239-242

Division of Cardiovascular Medicine, Duke University Medical Center, Box 2819, Durham, NC 27710, USA.

Survivorship into adulthood of patients with congenital heart disease is due to improvements in prenatal detection, novel surgeries, and specialized adult congenital heart disease care. As patients survive further into adulthood, long-term complications of congenital and repaired physiology have been more clearly elucidated. The overall mortality of patients with adult congenital heart disease with heart failure is around 4%. Read More

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http://dx.doi.org/10.1016/j.ccl.2020.02.002DOI Listing

Surgical outcomes in complex adult congenital heart disease: a brief review.

J Thorac Dis 2020 Mar;12(3):1224-1234

Mount Sinai Adult Congenital Heart Disease Center, Mount Sinai Heart, Icahn School of Medicine at Mount Sinai, New York, NY, USA.

Life expectancy of patients with congenital heart disease (CHD) continues to increase dramatically over the last few decades, primarily due to significant medical and surgical advancements in the field. Adult congenital heart disease (ACHD) patients are now living longer but continue to face morbidity and reduced long-term survival when compared to the general population. We briefly describe the growth of ACHD with a focus on surgical procedures and outcomes in the more complex lesions including Tetralogy of Fallot, Ebsteins Anomaly of the tricuspid valve, Coarctation of the Aorta, Transposition of the Great Arteries and single ventricle lesions. Read More

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http://dx.doi.org/10.21037/jtd.2019.12.136DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7139079PMC

Clinical Spectrum and Long-term Outcome of 183 Cases of Ebstein's Anomaly, Experience of Mexican Population.

Arch Med Res 2020 Apr 3. Epub 2020 Apr 3.

Consulta externa, Instituto Nacional de Cardiología, Ignacio Chavez, Ciudad de México, México.

Background: Ebstein's anomaly (EA) is a myopathy of the right ventricle that causes a variable spectrum of tricuspid valve delamination failure with diverse clinical and anatomical presentation. We reviewed our data of EA to establish an association between clinical and echocardiographic findings with mortality.

Methods: We divided patients in infants, Children/adolescents (Ch/A), and adults, according to age of presentation. Read More

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http://dx.doi.org/10.1016/j.arcmed.2020.03.008DOI Listing

Successful catheter ablation for ventricular tachycardia after cone procedure in Ebstein anomaly.

HeartRhythm Case Rep 2020 Feb 18;6(2):106-109. Epub 2019 Nov 18.

Department of Pediatrics, Seoul National University Children's Hospital, Seoul, South Korea.

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http://dx.doi.org/10.1016/j.hrcr.2019.11.002DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7026556PMC
February 2020

Indian Guidelines for Indications and Timing of Intervention for Common Congenital Heart Diseases: Revised and Updated Consensus Statement of the Working Group on Management of Congenital Heart Diseases. Abridged Secondary Publication.

Indian Pediatr 2020 02;57(2):143-157

GKNM Hospital, Coimbatore, Tamil Nadu, India.

Justification: A number of guidelines are available for management of congenital heart diseases from infancy to adult life. However, these guidelines are for patients living in high income countries. Separate guidelines, applicable to Indian children, are required when recommending an intervention for congenital heart diseases, as often these patients present late in the course of the disease and may have co-existing morbidities and malnutrition. Read More

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February 2020
1.014 Impact Factor

Novel KLHL26 variant associated with a familial case of Ebstein's anomaly and left ventricular noncompaction.

Mol Genet Genomic Med 2020 Apr 27;8(4):e1152. Epub 2020 Jan 27.

Department of Surgery, Division of Cardiothoracic Surgery, Medical College of Wisconsin, Milwaukee, WI, USA.

Background: Ebstein's anomaly (EA) is a rare congenital heart disease of the tricuspid valve and right ventricle. Patients with EA often manifest with left ventricular noncompaction (LVNC), a cardiomyopathy. Despite implication of cardiac sarcomere genes in some cases, very little is understood regarding the genetic etiology of EA/LVNC. Read More

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http://dx.doi.org/10.1002/mgg3.1152DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7196453PMC

Examination of pathologic features of the right atrioventricular groove in hearts with Ebstein anomaly and correlation with arrhythmias.

Heart Rhythm 2020 Jan 22. Epub 2020 Jan 22.

Department of Cardiology, Boston Children's Hospital, Boston, Massachusetts; Department of Pediatrics, Harvard Medical School, Boston, Massachusetts. Electronic address:

Background: Catheter ablation of accessory pathways (APs) in patients with Ebstein anomaly (EA) has a higher recurrence rate than in subjects with normal hearts. Anatomic features could account for suboptimal ablation outcomes.

Objective: The purpose of this study was to examine the right atrioventricular (AV) groove in autopsy hearts with EA, correlate with clinical data, and identify features relevant for catheter ablation. Read More

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http://dx.doi.org/10.1016/j.hrthm.2020.01.013DOI Listing
January 2020

Unusual Location of a Ventricular Tachycardia: Let the Cat Out of the Bag.

JACC Clin Electrophysiol 2020 Jan;6(1):127-128

Department of Cardiology (Division D), University Hospital Southampton, Southampton, United Kingdom.

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http://dx.doi.org/10.1016/j.jacep.2019.10.018DOI Listing
January 2020

Enlarged coronary sinus thrombosis after repair of Ebstein's anomaly.

J Card Surg 2020 Mar 16;35(3):675-678. Epub 2020 Jan 16.

Department of Cardiovascular Surgery, Kumamoto University Hospital, Kumamoto, Japan.

A 58-year-old woman was referred to our hospital with progressively increasing breathlessness. She reported a history of bioprosthetic valve implantation for tricuspid valve replacement and direct closure of an atrial septal defect for Ebstein's anomaly, 31 years before presentation. Transthoracic echocardiography revealed prosthetic valve failure, an enlarged coronary sinus, and severe mitral regurgitation. Read More

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http://dx.doi.org/10.1111/jocs.14414DOI Listing

Anterior Tricuspid Leaflet Cleft in an Adult Male: An Autopsy Case Report.

Am J Forensic Med Pathol 2020 Mar;41(1):40-41

From the Division of Legal Medicine, Department of Community Medicine and Social Healthcare Science, Kobe University Graduate School of Medicine.

The deceased was a 44-year-old male who was treated for a suspected Ebstein's anomaly observed using transthoracic echocardiogram. He was found dead in his bed at home. Autopsy revealed that the septal tricuspid leaflet was intact; however, a large anterior tricuspid leaflet cleft and right atrioventricular cavity dilation were observed. Read More

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http://dx.doi.org/10.1097/PAF.0000000000000525DOI Listing

[Ebstein's anomaly : from fetal diagnosis to surgical treatment].

Rev Med Liege 2020 Jan;75(1):43-48

Département de Pédiatrie, Cardiologie Pédiatrique, CHU Liège, Belgique.

Ebstein's anomaly is a rare and complex congenital heart disease involving abnormal embryological development of the tricuspid valve. Its exact prevalence remains unknown given the under-diagnosis of minor forms and the broad clinical spectrum of this pathology resulting from the highly variable tricuspid morphology. Echocardiography plays an important role in diagnosis, assessment and prognostic evaluation of this condition. Read More

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January 2020

Ebstein's anomaly with 'reversible' functional pulmonary atresia.

BMJ Case Rep 2019 Dec 29;12(12). Epub 2019 Dec 29.

Pediatric Cardiology, Hospital Santa Cruz, Carnaxide, Portugal.

We present the case of an infant with prenatal diagnosis, at 32 weeks gestation, of Ebstein's anomaly without anterograde flow from right ventricular to pulmonary atresia (PA)-functional PA with flow reversal in the ductus arteriosus. Prostaglandin E1 was started after birth. Chest X-ray showed severe cardiomegaly and echocardiogram confirmed Ebstein's anomaly with a thickened non-opening pulmonary valve without anterograde flow but with mild regurgitation. Read More

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http://dx.doi.org/10.1136/bcr-2019-229809DOI Listing
December 2019

Heart failure with reduced and preserved ejection fraction in adult congenital heart disease.

Heart Fail Rev 2019 Dec 24. Epub 2019 Dec 24.

Department of Medicine, Division of Cardiovascular Medicine, Stanford University School of Medicine, Palo Alto, CA, USA.

Heart failure with reduced ejection fraction (HFrEF) is common in patients with adult congenital heart disease. Many of the most common congenital defects have a high prevalence of HFrEF, including left-sided obstructive lesions (aortic stenosis, coarctation of the aorta, Shone complex), tetralogy of Fallot, Ebstein anomaly, lesions in which there is a systemic right ventricle, and lesions palliated with a Fontan circulation. However, heart failure with preserved ejection fraction (HFpEF) is also prevalent in all these lesions. Read More

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http://dx.doi.org/10.1007/s10741-019-09904-zDOI Listing
December 2019

[Application of cream formula in treatment of severe heart failure].

Zhongguo Zhong Yao Za Zhi 2019 Sep;44(18):3903-3907

Affiliated Hospital of Integrated Traditional Chinese and Western Medicine Nanjing 210028,China.

Cream formula has been mostly used to treat deficiency syndrome. Currently,it has been used to recuperate the body,promote health against aging,and prevent and treat chronic disease. In modern medicine,there are only treatment concepts and methods of diseases,but lack of concepts of " deficiency syndrome" and " restoring deficiency". Read More

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http://dx.doi.org/10.19540/j.cnki.cjcmm.20190403.503DOI Listing
September 2019

Pseudopolycystic Atrialized Right Ventricle in Ebstein's Anomaly.

World J Pediatr Congenit Heart Surg 2020 Jan;11(1):110-111

Department of Cardiac Surgery, Ghent University Hospital, Belgium.

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http://dx.doi.org/10.1177/2150135119884915DOI Listing
January 2020

Severity Scores for Ebstein Anomaly: Credibility and Usefulness of Echocardiographic vs Magnetic Resonance Assessments of the Celermajer Index.

Can J Cardiol 2019 Dec 14;35(12):1834-1841. Epub 2019 Aug 14.

1st Department of Cardiology, Poznan University of Medical Sciences, Poznań, Poland; Cardiac Magnetic Resonance Unit at 1st Department of Cardiology, Poznan University of Medical Sciences, Poznań, Poland.

Background: The severity score of Ebstein anomaly (EA) that corresponds to clinical status is still under research, with the Celermajer index (Cel-ind) being one of those. The agreement between echocardiographic and cardiac magnetic resonance (CMR) assessment of Cel-ind is not known. We determined the agreement between echocardiography- and CMR-derived Cel-ind and its relationship with heart failure markers. Read More

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http://dx.doi.org/10.1016/j.cjca.2019.08.003DOI Listing
December 2019

Arrhythmias in Adults With Congenital Heart Disease: What the Practicing Cardiologist Needs to Know.

Authors:
Paul Khairy

Can J Cardiol 2019 Dec 16;35(12):1698-1707. Epub 2019 Jul 16.

Electrophysiology Service and Adult Congenital Heart Disease Center, Montreal Heart Institute, Université de Montréal, Montreal, Québec, Canada. Electronic address:

The expanding population of adults with congenital heart disease (CHD) combined with the pervasiveness of arrhythmias has resulted in the rapid growth of a dedicated sector of cardiology at the intersection between 2 subspecialties: electrophysiology and adult CHD. Herein, practical considerations are offered regarding urgent referral for catheter ablation of atrial arrhythmias, anticoagulation, and primary prevention implantable cardioverter-defibrillators (ICDs). Patients with Ebstein anomaly and ventricular pre-excitation should be referred promptly due to the high prevalence of multiple accessory pathways and increased incidence of atrial tachyarrhythmias, which may be poorly tolerated. Read More

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http://dx.doi.org/10.1016/j.cjca.2019.07.009DOI Listing
December 2019

Case 5/2019 - Naturally Evolving Ebstein's Anomaly of Discrete Repercussion in 24-Year-old Asymptomatic Adult.

Arq Bras Cardiol 2019 10 10;113(3):435-437. Epub 2019 Oct 10.

Instituto do Coração do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, São Paulo, SP - Brazil.

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http://dx.doi.org/10.5935/abc.20190158DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6882404PMC
October 2019

Which One Predominates in Ebstein Anomaly: Tricuspid Regurgitation or Right Ventricular Dysfunction?

Ann Thorac Surg 2020 05 3;109(5):1626. Epub 2019 Oct 3.

Department of Cardiovascular Surgery, Izmir Ataturk Education and Research Hospital, Basin Sitesi, 35360 Izmir, Turkey.

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http://dx.doi.org/10.1016/j.athoracsur.2019.08.086DOI Listing
May 2020
1 Read

Right Ventricular Diastolic Function and Right Atrial Function and Their Relation With Exercise Capacity in Ebstein Anomaly.

Can J Cardiol 2019 Dec 12;35(12):1824-1833. Epub 2019 Jun 12.

Division of Cardiology, The Labatt Family Heart Centre, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada. Electronic address:

Background: Right ventricular (RV) diastolic function and right atrial (RA) function are poorly characterized in patients with Ebstein anomaly (EA) but may influence functional capacity. We aimed to evaluate RV diastolic function and RA function in EA and study their relationship with biventricular systolic function and exercise capacity.

Methods: Seventy-two patients with EA and 69 controls prospectively underwent echocardiography, cardiovascular magnetic resonance imaging, and cardiopulmonary exercise testing to investigate RV systolic and diastolic function, RA function, and exercise capacity. Read More

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http://dx.doi.org/10.1016/j.cjca.2019.05.036DOI Listing
December 2019
12 Reads

Mirror Syndrome with Severe Postpartum Presentation following Stillbirth and Shoulder Dystocia.

Fetal Pediatr Pathol 2019 Sep 27:1-5. Epub 2019 Sep 27.

2nd Department of Obstetrics and Gynecology, Medical University of Warsaw , Warsaw , Poland.

Mirror syndrome (MS) is a pregnancy-related condition characterized by fetal, placental and maternal edema. We report a case of MS with severe postpartum presentation following stillbirth, shoulder dystocia, McRoberts maneuver, anterior shoulder disimpaction and manual posterior shoulder delivery together with serum soluble fms-like tyrosine kinase 1 (sFlt-1)/placental growth factor (PlGF) ratio results. A 33-year-old patient G3P0A2 at 34 weeks gestation was referred with fetal Ebstein anomaly and fetal hydrops. Read More

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http://dx.doi.org/10.1080/15513815.2019.1658246DOI Listing
September 2019
3 Reads

Quantitative Assessment of Left Ventricular Dysfunction in Fetal Ebstein's Anomaly and Tricuspid Valve Dysplasia.

J Am Soc Echocardiogr 2019 12 21;32(12):1598-1607. Epub 2019 Sep 21.

Division of Cardiology, Department of Pediatrics, Fetal and Neonatal Cardiology Program, Women's and Children Health Research Institute, University of Alberta, Edmonton, Alberta, Canada. Electronic address:

Background: Fetal Ebstein's anomaly and tricuspid valve dysplasia (EA/TVD) are associated with high perinatal mortality relative to pulmonary atresia with intact ventricular septum (PAIVS), despite both requiring redistribution of the cardiac output (CO) to the left ventricle (LV). LV dysfunction is suspected to contribute to adverse outcomes in EA/TVD.

Objective: We sought to examine global and segmental LV function in fetal EA/TVD with comparison to normal controls and PAIVS. Read More

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http://dx.doi.org/10.1016/j.echo.2019.07.008DOI Listing
December 2019
3 Reads

Permanent Pacing in a Patient With Fontan Circulation: Use All You Have at Your Discretion.

Heart Lung Circ 2020 Jan 14;29(1):e17-e18. Epub 2019 Sep 14.

St Boniface Hospital, University of Manitoba, Winnipeg, Canada.

Patients with Fontan circulation post significant technical challenges at the time of permanent pacemaker implantation, as majority of them are treated with surgically implanted epicardial pacemakers. However, transvenous pacemaker implantation is technically feasible, and the treating physician should be aware of each individual's anatomy and available treatment options. Read More

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http://dx.doi.org/10.1016/j.hlc.2019.08.013DOI Listing
January 2020

Modified underlying cardiac disease severity in twin-twin transfusion syndrome.

Ann Pediatr Cardiol 2019 Sep-Dec;12(3):336-338

Department of Pediatric Cardiology, Saitama Medical Center, Saitama Medical University, Saitama, Japan.

Twin-twin transfusion syndrome or related conditions affect fetal loading. We report monochorionic-diamniotic twins. Twin 1 had Ebstein anomaly with mild tricuspid regurgitation (TR) and slightly thickened tricuspid valve leaflets with plastering. Read More

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http://www.annalspc.com/text.asp?2019/12/3/336/263600
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http://dx.doi.org/10.4103/apc.APC_112_18DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6716300PMC
September 2019
5 Reads

Spontaneous closure of arterio-venous pulmonary fistulas by redirection of hepatic venous blood 9 years after Glenn anastomosis in a 12-year-old girl.

Cardiol Young 2019 Oct;29(10):1287-1289

Department of Pediatric Cardiology and Congenital Heart Disease, German Heart Center Munich, Technische Universität München, Germany.

We report on a 12-year-old girl with Ebstein's anomaly after a unidirectional Glenn procedure with surgical ligation of the proximal right pulmonary artery, who suffered from significant central cyanosis caused by multiple arterio-venous fistulas in the right lung. The continuity between the right pulmonary artery and the pulmonary trunk was restored with the use of radiofrequency perforation and consecutive covered stent implantation. Read More

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http://dx.doi.org/10.1017/S1047951119000465DOI Listing
October 2019

Cerebral abscess following the self-extraction of teeth in patient with Ebstein's anomaly: a case report.

BMC Oral Health 2019 08 30;19(1):200. Epub 2019 Aug 30.

Department of Special Care Dentistry, Matsumoto Dental University, Nagano, Japan.

Background: Antibiotic prophylaxis before invasive treatments, including dental extractions, is still recommended for patients at high risk of infective endocarditis. However, the risk from self-extraction of teeth in daily life of patients with intellectual disabilities is uncertain.

Case Presentation: A 6-year-old patient with Ebstein's anomaly developed cerebral abscess, which appeared associated with infective endocarditis of dental origin. Read More

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http://dx.doi.org/10.1186/s12903-019-0893-3DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6717324PMC
August 2019
2 Reads

A Young Woman With Recurrent Palpitations: A Case of Ebstein Anomaly With Mahaim Fiber Tachycardia.

CASE (Phila) 2019 Aug 31;3(4):145-148. Epub 2019 May 31.

Division of Cardiology, Department of Medicine, Einstein Medical Center, Philadelphia, Pennsylvania.

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http://dx.doi.org/10.1016/j.case.2019.03.006DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6710817PMC
August 2019
2 Reads

Prenatal detection of 1p36 deletion syndrome: ultrasound findings and microarray testing results.

J Matern Fetal Neonatal Med 2019 Aug 25:1-121. Epub 2019 Aug 25.

Prenatal Diagnostic Center, Guangzhou Women and Children's Medical Center affiliated to Guangzhou Medical University , Guangzhou , China.

Only a small number of reports have been made on the prenatal ultrasound findings observed in 1p36 deletion syndrome. We explored prenatal diagnosis of 1p36 deletion by ultrasound as well as chromosomal microarray (CMA), and delineated the fetal presentation of this syndrome. This was a retrospective analysis of ten new prenatal cases of 1p36 deletion identified by CMA at a single Chinese medical center. Read More

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http://dx.doi.org/10.1080/14767058.2019.1660764DOI Listing
August 2019
3 Reads

Radiofrequency catheter ablation of accessory pathways at the site of prior valve surgery.

J Arrhythm 2019 Aug 8;35(4):645-653. Epub 2019 Jul 8.

Division of Cardiology, Department of Internal Medicine, Severance Hospital Yonsei University College of Medicine Seoul Republic of Korea.

Background: Radiofrequency catheter ablation (RFCA) for accessory pathways (APs) at the site of prior valve surgery (VS) remains challenging. We aimed to clarify the factors associated with successful RFCA for such APs.

Methods: Upon reviewing a RFCA registry and previous case reports, we included nine patients who underwent RFCA of APs at the site of prior VS (total-VS group; age, 34. Read More

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http://dx.doi.org/10.1002/joa3.12213DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6686296PMC
August 2019
5 Reads

Fusobacterial brain abscess caused by paradoxical embolization associated with Ebstein's anomaly in an adult patient: A case report.

Anaerobe 2020 Feb 6;61:102084. Epub 2019 Aug 6.

Department of Cardiology Post Graduate Institute of Medical Education and Research, Chandigarh, India.

Brain abscess remains a life-threatening condition. Here, we are reporting a case of brain abscess due to Fusobacterium nucleatum in a previously known case of Ebstein anomaly. A 44-year-old male presented with the complaints of headache, and fever. Read More

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http://dx.doi.org/10.1016/j.anaerobe.2019.102084DOI Listing
February 2020
5 Reads

Surgical Repair of Ebstein's Anomaly Using a Bicuspidization Approach.

Ann Thorac Surg 2019 12 5;108(6):1875-1882. Epub 2019 Aug 5.

Division of Pediatric Cardiac Surgery, Lucile Packard Children's Hospital Stanford, Stanford University School of Medicine, Stanford, California.

Background: Ebstein's anomaly of the tricuspid valve is a rare and heterogeneous form of congenital heart defect. The purpose of this study was to review the surgical experience with Ebstein's anomaly at a single institution.

Methods: This was a retrospective review of 47 patients with Ebstein's anomaly who were previously unrepaired and underwent surgical repair of the tricuspid valve. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2019.06.026DOI Listing
December 2019
2 Reads

Postoperative persistent diastolic dyssynchronous expansion in patients with Ebstein's anomaly.

PLoS One 2019 8;14(8):e0220890. Epub 2019 Aug 8.

Department of Internal Medicine, Cardiovascular Center, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Korea.

In Ebstein's anomaly, maximal expansion in the atrialized right ventricle (RV) occurs during early diastole, whereas that of the functional RV occurs in late diastole, resulting in diastolic dyssynchronous expansion (DSE). We quantitatively assessed DSE and identified preoperative factors correlated with persistent DSE after surgery. Seventeen patients diagnosed with Ebstein's anomaly in whom transthoracic echocardiography (TTE) and cardiac magnetic resonance (CMR) images available were retrospectively analyzed for quantitative DSE assessment and 10 patients who underwent surgery and postoperative TTE available were additionally analyzed for postoperative DSE. Read More

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http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0220890PLOS
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6687137PMC
March 2020
2 Reads

Echocardiographic and pathomorphological features in fetuses with ductal-dependent congenital heart diseases.

Echocardiography 2019 09 7;36(9):1736-1743. Epub 2019 Aug 7.

Department of Ultrasound, Xinqiao Hospital, Army Medical University, Chongqing, China.

Objective: To individually analyze echocardiographic features in fetuses with ductal-dependent congenital heart diseases (DDCHD) and to verify the anatomical characteristics corresponding to the echocardiogram scan views.

Background: Ductal-dependent congenital heart diseases depends on the ductus arteriosus (DA) remaining open to maintain suitable pulmonary or systemic circulation after birth. An accurate diagnosis using prenatal echocardiography has important clinical significance in evaluating disease prognosis and ensuring timely treatment. Read More

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http://dx.doi.org/10.1111/echo.14452DOI Listing
September 2019
10 Reads

Ebstein's Anomaly.

Methodist Debakey Cardiovasc J 2019 Apr-Jun;15(2):138-144

MAYO CLINIC, ROCHESTER, MINNESOTA.

Ebstein's anomaly is a malformation of the tricuspid valve with myopathy of the right ventricle (RV) that presents with variable anatomic and pathophysiologic characteristics, leading to equally variable clinical scenarios. Medical management and observation is often recommended for asymptomatic patients and may be successful for many years. Tricuspid valve repair is the goal of operative intervention; repair also typically includes RV plication, right atrial reduction, and atrial septal closure or subtotal closure. Read More

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http://dx.doi.org/10.14797/mdcj-15-2-138DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6668741PMC
August 2019
10 Reads

Early and Long-Term Outcomes of Surgical Treatment of Ebstein's Anomaly.

Braz J Cardiovasc Surg 2019 12 1;34(5):511-516. Epub 2019 Dec 1.

Universidade de São Paulo Faculdade de Medicina Hospital das Clínicas São Paulo SP Brazil Instituto do Coração do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (InCor-HCFMUSP), São Paulo, SP, Brazil.

Objective: This study aimed to evaluate Ebstein's anomaly surgical correction and its early and long-term outcomes.

Methods: A retrospective analysis of 62 consecutive patients who underwent surgical repair of Ebstein's anomaly in our institution from January 2000 to July 2016. The following long-term outcomes were evaluated: survival, reoperations, tricuspid regurgitation, and postoperative right ventricular dysfunction. Read More

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http://dx.doi.org/10.21470/1678-9741-2018-0333DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6852467PMC
December 2019
1 Read

Denoising and artefact removal for transthoracic echocardiographic imaging in congenital heart disease: utility of diagnosis specific deep learning algorithms.

Int J Cardiovasc Imaging 2019 Dec 19;35(12):2189-2196. Epub 2019 Jul 19.

Department of Cardiology III - Adult Congenital and Valvular Heart Disease, University Hospital Muenster, Albert-Schweitzer-Campus 1, 48149, Münster, Germany.

Deep learning (DL) algorithms are increasingly used in cardiac imaging. We aimed to investigate the utility of DL algorithms in de-noising transthoracic echocardiographic images and removing acoustic shadowing artefacts specifically in patients with congenital heart disease (CHD). In addition, the performance of DL algorithms trained on CHD samples was compared to models trained entirely on structurally normal hearts. Read More

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http://dx.doi.org/10.1007/s10554-019-01671-0DOI Listing
December 2019
7 Reads
2.322 Impact Factor

Tuberculosis of the Sternoclavicular Joint: Report of Three cases.

J Assoc Physicians India 2018 Oct;66(10):96

Senior Specialist, Tata Main Hospital, Jamshedpur, Jharkhand.

Ebstein's anomaly accounts for 0.3% to 0.7% of all cases of congenital heart disease. Read More

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October 2018
4 Reads