2,035 results match your criteria Ebstein Anomaly


Cardiopulmonary Exercise Testing-A Valuable Tool, Not Gatekeeper When Referring Patients With ACHD for Transplant Evaluation.

World J Pediatr Congenit Heart Surg 2019 Mar 4:2150135118825263. Epub 2019 Mar 4.

2 Division of Cardiology, Hospital of the University of Pennsylvania, Philadelphia, PA, USA.

Introduction:: Treatment of patients with adult congenital heart disease (ACHD) with advanced therapies including heart transplant (HT) is often delayed due to paucity of objective prognostic markers for the severity of heart failure (HF). While the utility of Cardiopulmonary Exercise Testing (CPET) in non-ACHD patients has been well-defined as it relates to prognosis, CPET for this purpose in ACHD is still under investigation.

Methods:: We performed a retrospective cohort study of 20 consecutive patients with ACHD who underwent HT between March 2010 and February 2016. Read More

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http://dx.doi.org/10.1177/2150135118825263DOI Listing
March 2019
1 Read

Contemporary outcomes and mortality risks of Ebstein anomaly: A single-center experience in Thailand.

Congenit Heart Dis 2019 Feb 21. Epub 2019 Feb 21.

Department of Pediatrics, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Background: The increasing number of patients with Ebstein anomaly (EA) surviving into adulthood implies improvements in the treatments for the complex lesion. We revisited the clinical outcomes of patients with EA to demonstrate their "real world" survival.

Objectives: To identify the survival and predictors of mortality in patients with EA who underwent medical or surgical management in the present era. Read More

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http://dx.doi.org/10.1111/chd.12759DOI Listing
February 2019
1 Read

Expanding the genetic and clinical spectrum of the NONO-associated X-linked intellectual disability syndrome.

Am J Med Genet A 2019 Feb 17. Epub 2019 Feb 17.

Division of Medical Genetics, University of Utah, Salt Lake City, Utah.

The NONO gene encodes a nuclear protein involved in RNA metabolism. Hemizygous loss-of-function NONO variants have been associated with syndromic intellectual disability and with left ventricular noncompaction (LVNC). A two-year-old boy presented to the University of Utah's Penelope Undiagnosed Disease Program with developmental delay, nonfamilial features, relative macrocephaly, and dilated cardiomyopathy with LVNC and Ebstein anomaly. Read More

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http://dx.doi.org/10.1002/ajmg.a.61091DOI Listing
February 2019
4 Reads

External Plication of the Atrialized Right Ventricle in the Repair of Ebstein's Anomaly.

Semin Thorac Cardiovasc Surg 2019 Feb 5. Epub 2019 Feb 5.

Department of Pediatrics, Artemis Hospital, Delhi, India.

We describe a change in our technique for plication of the atrialized right ventricle during a Cone repair. The plication was performed from the "Outside"-on a beating heart. Advantages expected from this change are-all major coronaries are better seen when full of blood and can be avoided, if a major vessel is compromised-electrocardiography changes should point it out immediately, there is a small but significant saving in terms of arrest time and if the plication needs to be taken down because of an adverse coronary event-this can be done without the need of another cardioplegia. Read More

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http://dx.doi.org/10.1053/j.semtcvs.2019.02.004DOI Listing
February 2019
1 Read

Reconstructive surgery for Ebstein anomaly: three decades of experience.

Eur J Cardiothorac Surg 2019 Feb 5. Epub 2019 Feb 5.

Department of Cardiothoracic Surgery, Erasmus MC, Rotterdam, Netherlands.

Objectives: Since 1988, our centre employs vertical plication repair with deattachment and reattachment of the tricuspid valve for Ebstein anomaly. This study describes the characteristics and long-term outcomes of our single-centre cohort.

Methods: Data from all patients operated on between 1988 and 2016 were retrospectively collected. Read More

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http://dx.doi.org/10.1093/ejcts/ezz022DOI Listing
February 2019
3 Reads

Exercise Capacity After Repair of Ebstein Anomaly in Adults.

Pediatr Cardiol 2019 Jan 30. Epub 2019 Jan 30.

Department of Pediatric Cardiology, Mayo Clinic, 200 1st St SW, Rochester, MN, 55905, USA.

Repair of Ebstein anomaly has evolved over the last decade, and timing of repair remains variable. There have been no studies of exercise or functional capacity in patients who have had tricuspid valve surgery for Ebstein anomaly in adulthood. We aimed to compare exercise capacity before and after tricuspid valve repair or replacement for Ebstein anomaly in adults at Mayo Clinic. Read More

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http://dx.doi.org/10.1007/s00246-019-02056-9DOI Listing
January 2019
1 Read

Uhl Anomaly in Asymptomatic Adult Woman.

Circ Cardiovasc Imaging 2019 Feb;12(2):e008277

Dipartimento di Diagnostica per Immagini, Imaging Molecolare, Radiologia Interventistica e Radioterapia, University Tor Vergata, Rome, Italy (M.F., L.P., R.F., M.C.).

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http://dx.doi.org/10.1161/CIRCIMAGING.118.008277DOI Listing
February 2019

Prognostic value of echocardiographic parameters in pediatric patients with Ebstein's anomaly.

Int J Cardiol 2019 Mar 14;278:76-83. Epub 2018 Oct 14.

Paediatric Cardiology, Royal Brompton Hospital, London, United Kingdom.

Background: Accurate risk stratification of patients with Ebstein's anomaly (EA) is crucial. Aim of the study was to assess the prognostic value of echocardiography, including 2D speckle tracking (STE) derived myocardial deformation indices, for predicting outcome in pediatric and young adult unrepaired EA patients.

Methods: Fifty consecutive EA patients (1 day-18 years, 52% males) underwent echocardiography and were followed for a mean follow-up of 60 ± 41 months for clinical outcome (ventricular tachyarrhythmia, heart failure, need for surgery and/or death). Read More

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http://dx.doi.org/10.1016/j.ijcard.2018.10.046DOI Listing
March 2019
1 Read

Ischemia Begets Right Ventricular Dysfunction After Cone Repair for Ebstein's Anomaly.

J Cardiothorac Vasc Anesth 2019 01 25;33(1):261-262. Epub 2018 Sep 25.

Department of Cardiac Anaesthesia, Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India.

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http://dx.doi.org/10.1053/j.jvca.2018.09.026DOI Listing
January 2019

The first known use of the double-orifice valve technique for Ebstein anomaly, performed 30 years ago.

J Thorac Cardiovasc Surg 2019 Feb 26;157(2):e47-e49. Epub 2018 Oct 26.

Department of Cardiothoracic and Vascular Surgery Cardio Centrum Berlin, Berlin, Germany.

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http://dx.doi.org/10.1016/j.jtcvs.2018.10.077DOI Listing
February 2019
2 Reads

Ebstein's anomaly with imperforate tricuspid valve: An extremely rare congenital anomaly.

J Cardiovasc Comput Tomogr 2018 Nov 10. Epub 2018 Nov 10.

Department of Cardiovascular Radiology and Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India.

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http://dx.doi.org/10.1016/j.jcct.2018.10.029DOI Listing
November 2018
14 Reads

[Anesthetic management for patient with severe cyanosis following bioprosthetic valve stenosis].

Authors:
Jun Zeng Wei Wei

Rev Bras Anestesiol 2018 Nov 13. Epub 2018 Nov 13.

Sichuan University, West China Hospital, Department of Anesthesiology, Chengdu, China. Electronic address:

We presented a 39-year-old female patient with life-threatening hypoxemia after tricuspid valve replacement because of Ebstein's anomaly. And the severe cyanosis is due to bioprosthetic valve stenosis and atrial septal defect. Anesthetic management of a patient with severe obstructive prosthetic valve dysfunction can be challenging. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S00347094183003
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http://dx.doi.org/10.1016/j.bjan.2018.06.010DOI Listing
November 2018
13 Reads

Treatment of fetal circular shunt with non-steroidal anti-inflammatory drugs.

Ultrasound Obstet Gynecol 2018 Oct 31. Epub 2018 Oct 31.

Fetal Cardiac, Labatt Family Heart Centre, Hospital for Sick Children, University of Toronto, Toronto, Canada.

A circular shunt (CS) is a life-threatening condition consisting of massive shunting of systemic arterial blood via the ductus arteriosus to the left ventricle without traversing the lungs. In the prenatal circulation, it mainly occurs in severe Ebstein anomaly (EA) from unrestricted ductal flow and significant pulmonary and tricuspid regurgitation. We aimed to improve the fetal hemodynamics and chances of survival of affected fetuses by inducing ductal constriction with transplacental non-steroidal anti-inflammatory drugs (NSAIDs). Read More

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http://doi.wiley.com/10.1002/uog.20169
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http://dx.doi.org/10.1002/uog.20169DOI Listing
October 2018
9 Reads

Characteristics and Outcomes of Pediatric Patients Who Undergo Placement of Implantable Cardioverter Defibrillators.

Circ Arrhythm Electrophysiol 2018 Sep;11(9):e006542

The Heart Institute, Cincinnati Children's Hospital Medical Center, OH (S.B., D.S.S., R.J.C.).

Background Implantable cardioverter defibrillators (ICDs) are an important part of therapy for many patients, yet there is little data on population characteristics, complications, or system survival in pediatric patients. Methods A retrospective review of ICD recipients in the National Cardiovascular Data Registry ICD Registry was performed from 2010 to 2016. Patient characteristics and complications between pediatric (≤21 years) and adult populations (>21 years) were compared. Read More

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https://www.ahajournals.org/doi/10.1161/CIRCEP.118.006542
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http://dx.doi.org/10.1161/CIRCEP.118.006542DOI Listing
September 2018
9 Reads

Successful pregnancy in a patient with Ebstein's anomaly; a case report from a developing country.

J Pak Med Assoc 2018 Sep;68(9):1391-1393

Liaquat National Hospital and Medical College, Karachi.

Ebstein anomaly is a rare malformation of the tricuspid valve of the heart. The malformed tricuspid valve may be incompetent, stenotic, or rarely, imperforate. Pregnant patients with Ebstein anomaly become a challenge for the physician in terms of management. Read More

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September 2018
5 Reads
0.403 Impact Factor

Percutaneous closure of paravalvular leak after Cone repair for Ebstein's anomaly.

Catheter Cardiovasc Interv 2019 Jan 2;93(1):E46-E48. Epub 2018 Oct 2.

Department of Pediatrics, Ghent University Hospital, Ghent, Belgium.

We report the use of an Amplatzer Vascular plug for percutaneous closure of a paravalvular leak after Cone repair in a 5-year-old boy with Ebstein's anomaly. A paravalvular leak of the tricuspid valve developed gradually after Cone repair-surgery. The combination of fluoroscopy, transesophageal and transthoracic imaging during general anesthesia was necessary for correct and safe positioning of the device by percutaneous approach. Read More

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http://dx.doi.org/10.1002/ccd.27790DOI Listing
January 2019
4 Reads

Cardiovascular magnetic resonance evidence of myocardial fibrosis and its clinical significance in adolescent and adult patients with Ebstein's anomaly.

J Cardiovasc Magn Reson 2018 09 27;20(1):69. Epub 2018 Sep 27.

Department of Cardiology, West China Hospital, Sichuan University, Chengdu, 610041, Sichuan Province, China.

Background: Myocardial fibrosis is a common pathophysiological process that is related to ventricular remodeling in congenital heart disease. However, the presence, characteristics, and clinical significance of myocardial fibrosis in Ebstein's anomaly have not been fully investigated. This study aimed to evaluate myocardial fibrosis using cardiovascular magnetic resonance (CMR) late gadolinium enhancement (LGE) and T1 mapping techniques, and to explore the significance of myocardial fibrosis in adolescent and adult patients with Ebstein's anomaly. Read More

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http://dx.doi.org/10.1186/s12968-018-0488-1DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6158838PMC
September 2018
9 Reads

Ebstein's Anomaly: "The One and a Half Ventricle Heart".

Braz J Cardiovasc Surg 2018 Jul-Aug;33(4):353-361

Department of Research, U. N. Mehta Institute of Cardiology and Research Centre (affiliated to BJ medical college, Ahmedabad), Gujarat, India.

Objective: Ebstein's anomaly remains a relatively ignored disease. Lying in the 'No Man's land' between congenital and valve surgeons, it largely remains inadequately studied. We report our short-term results of treating it as a 'one and a half ventricle heart' and propose that the true tricuspid annulus (TTA) 'Z' score be used as an objective criterion for estimation of 'functional' right ventricle (RV). Read More

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http://dx.doi.org/10.21470/1678-9741-2018-0100DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6122759PMC
January 2019
34 Reads

Ventricular arrhythmias and sudden death in patients with Ebstein anomaly: insights from a retrospective cohort study.

J Thorac Dis 2018 Jul;10(Suppl 18):S2172-S2175

Electrophysiology Service and Adult Congenital Heart Disease Centre, Montreal Heart Institute, Université de Montréal, Montreal, Quebec, Canada.

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http://dx.doi.org/10.21037/jtd.2018.06.74DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6072962PMC
July 2018
8 Reads

Cavotricuspid isthmus ablation using multimodality imaging in Ebstein anomaly with a mechanical tricuspid valve replacement.

HeartRhythm Case Rep 2018 Aug 9;4(8):346-349. Epub 2018 May 9.

Division of Cardiology, Department of Internal Medicine, Pusan National University Yangsan Hospital, Pusan National University of Medicine, Yangsan, Republic of Korea.

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http://dx.doi.org/10.1016/j.hrcr.2018.04.012DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6092982PMC
August 2018
13 Reads

Electro-vectorcardiographic and electrophysiological aspects of Ebstein's anomaly.

Ann Noninvasive Electrocardiol 2018 Aug 14:e12590. Epub 2018 Aug 14.

Heart Center, Faculty of Medicine and Life Sciences, Tampere University Hospital, University of Tampere, Tampere, Finland.

Ebstein's anomaly is a congenital heart disease where the most important anatomic feature is the inferior displacement of the tricuspid valve leaflets. Vectorcardiographic features are mainly forgotten and electrocardiographic features may be unrecognized by cardiologists handling adult patients. Read More

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http://dx.doi.org/10.1111/anec.12590DOI Listing
August 2018
7 Reads

Diastolic paradoxical septal motion in Ebstein anomaly.

Anatol J Cardiol 2018 Aug;20(2):E3

Department of Cardiology, Ümraniye Training and Research Hospital; İstanbul-Turkey.

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http://dx.doi.org/10.14744/AnatolJCardiol.2018.79026DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6237949PMC
August 2018
4 Reads

A rare case of Ebstein's anomaly with left ventricular noncompaction.

Asian Cardiovasc Thorac Ann 2019 Mar 6;27(3):208-209. Epub 2018 Aug 6.

1 St. Luke's Hospital, Thessaloniki, Greece.

Ebstein's anomaly is a rare congenital cardiac disease characterized by apical displacement of the tricuspid valve with decreased right ventricular function. Left ventricular noncompaction is a cardiomyopathy characterized by the presence of numerous and prominent trabeculations together with deep intertrabecular recesses in a portion of the ventricular wall, principally at the lateral and apical level. We describe the very rare case of a patient living for 78 years with a benign form of Ebstein's anomaly and left ventricular noncompaction cardiomyopathy with slightly reduced systolic function. Read More

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http://dx.doi.org/10.1177/0218492318791421DOI Listing
March 2019
6 Reads

Postablation Right Atrial Dissection in Ebstein's Anomaly.

CASE (Phila) 2018 Feb 15;2(1):16-19. Epub 2017 Nov 15.

Division of Cardiology, Department of Pediatrics, University of California, San Francisco, San Francisco, California.

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http://dx.doi.org/10.1016/j.case.2017.08.004DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6058392PMC
February 2018
2 Reads

Live-Born Major Congenital Heart Disease in Denmark: Incidence, Detection Rate, and Termination of Pregnancy Rate From 1996 to 2013.

JAMA Cardiol 2018 Sep;3(9):829-837

Department of Cardiology, Copenhagen University Hospital Rigshospitalet, Copenhagen, Denmark.

Importance: The occurrence of major congenital heart disease (CHD) is affected by several variables. Determining the development of the true incidence is critical to the establishment of proper treatment of these patients.

Objective: To evaluate time trends in incidence, detection rate, and termination of pregnancy (TOP) rate of major CHD in fetuses in Denmark and assess the influence of the introduction of general prenatal screening in 2004. Read More

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http://dx.doi.org/10.1001/jamacardio.2018.2009DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6233653PMC
September 2018
15 Reads

Anatomy of the ventricular septal defect in congenital heart defects: a random association?

Orphanet J Rare Dis 2018 07 18;13(1):118. Epub 2018 Jul 18.

Université Paris Descartes, Sorbonne Paris Cité, 149 rue de Sevres, 75004, Paris, France.

Background: A ventricular septal defect (VSD) is an integral part of most congenital heart defects (CHD). To determine the prevalence of VSD in various types of CHD and the distribution of their anatomic types.

Methods: We reviewed 1178 heart specimens with CHD from the anatomic collection of the French Reference Centre for Complex Congenital Heart Defects. Read More

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http://dx.doi.org/10.1186/s13023-018-0861-zDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6052685PMC
July 2018
17 Reads

Ebstein Anomaly with Pregnancy: A Rare Case.

J Reprod Infertil 2018 Apr-Jun;19(2):119-122

Department of Cardiology, North Eastern Indira Gandhi Regional Institute of Health and Medical Sciences, Shillong, India.

Background: Ebstein anomaly is an uncommon, complex congenital malformation of the heart with prevalence of 0.3-0.5%. Read More

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6010821PMC
July 2018
5 Reads

Wide QRS complex supraventricular tachycardia with negative precordial concordance: Electrocardiographic clues for Mahaim pathway with Ebstein anomaly.

J Electrocardiol 2018 Jul - Aug;51(4):663-666. Epub 2018 Apr 12.

Health Science University, Turkiye Yuksek Ihtisas Training and Research Hospital, Department of Electrophysiology, Ankara, Turkey.

Ebstein's anomaly is often accompanied by either Wolff-Parkinson-White syndrome or atriofascicular Mahaim. These bypass tracts give rise to antidromic atrioventricular (AV) re-entrant tachycardias, in which the bypass tract serves as the anterograde limb of the circuit and the AV node as the retrograde limb of the reentrant circuit. Since the antidromic AV reentrant tachycardia over a Mahaim fibre has a typically left bundle braunch block (LBBB) morphology, it is easy to make a misdiagnosis of supraventricular tachycardia with functional LBBB or even of ventricular tachycardia particularly in the presence of negative concordance. Read More

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http://dx.doi.org/10.1016/j.jelectrocard.2018.04.003DOI Listing
April 2018
4 Reads

Right Heart-Pulmonary Circulation Unit in Congenital Heart Diseases.

Heart Fail Clin 2018 Jul;14(3):283-295

Royal Brompton and Harefield Trust, London, UK. Electronic address:

The right ventricle plays a major role in congenital heart disease. This article describes the right ventricular mechanics in some selected congenital heart diseases affecting the right ventricle in different ways: tetralogy of Fallot, Ebstein anomaly, and the systemic right ventricle. Read More

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http://dx.doi.org/10.1016/j.hfc.2018.02.005DOI Listing
July 2018
6 Reads

Identification of a New Candidate Locus for Ebstein Anomaly in 1p36.2.

Mol Syndromol 2018 May 28;9(3):164-169. Epub 2018 Apr 28.

Laboratorio de Biología Molecular y Pruebas Diagnósticas de Alta Complejidad, Bogotá, Colombia.

Ebstein anomaly (EA) is a rare congenital heart defect (CHD) with a poorly characterized genetic etiology. However, some EA patients carry deletions in 1p36, all of which have been reported to carry distal deletions and share loss of the gene, which is currently considered the most likely candidate for EA development in this region. Here, we report a patient with an 11. Read More

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http://dx.doi.org/10.1159/000488820DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6006643PMC
May 2018
25 Reads

Cor-Triatriatum Dexter with Associated Cyanosis in a 3-Month-Old Girl.

J Cardiovasc Echogr 2018 Apr-Jun;28(2):143-145

Department of Nursing, Aminu Kano Teaching Hospital, Kano, Nigeria.

Cor-triatriatum is uncommon and cor-triatriatum dexter is rarer, and patients may remain asymptomatic in isolated cases especially if the partitioning is mild and nonobstructing. There may be other cardiac defects associated with it which are mostly right-sided cardiac defects such as atrial septal defect, Ebstein anomaly, and pulmonary stenosis. However, left-sided heart anomaly such as aortic regurgitation has been associated with it, but its association with transposition of the great vessels has not been documented before now. Read More

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http://dx.doi.org/10.4103/jcecho.jcecho_11_17DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5989550PMC
June 2018
22 Reads

[The experience of surgical treatment for Ebstein anomaly in 141 children].

Zhonghua Wai Ke Za Zhi 2018 Jun;56(6):422-426

Department of Pediatric Cardiothoracic Surgery, Shanghai Children's Medical Center, School of Medicine, Shanghai Jiaotong University, Shanghai 200127, China.

To explore the surgical strategy for Ebstein anomaly in children. From January 2003 to December 2015, a total of 141 cases of Ebstein anomaly were treated at Department of Pediatric Cardiothoracic Surgery, Shanghai Children's Medical Center, School of Medicine, Shanghai Jiaotong University. There were 65 male and 76 female patients, with age of (6. Read More

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http://dx.doi.org/10.3760/cma.j.issn.0529-5815.2018.06.007DOI Listing
June 2018
9 Reads

[The outcomes of operation for 237 patients with Ebstein anomaly].

Zhonghua Wai Ke Za Zhi 2018 Jun;56(6):418-421

Department of Cardiac Surgery, First Hospital of Tsinghua University, Beijing 100016, China.

To evaluate the early and long-term outcomes cardiac surgery of patients with Ebstein anomaly. The clinic data of 237 patients with Ebstein anomaly received surgical procedures from March 2004 to December 2017 at Department of Cardiac Surgery, First Hospital of Tsinghua University was analyzed retrospectively. There were 105 male and 132 female patients with age of (19. Read More

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http://dx.doi.org/10.3760/cma.j.issn.0529-5815.2018.06.006DOI Listing
June 2018
17 Reads

Impact of the cone operation on left ventricular size, function, and dyssynchrony in Ebstein anomaly: a cardiovascular magnetic resonance study.

J Cardiovasc Magn Reson 2018 05 21;20(1):32. Epub 2018 May 21.

Department of Cardiology, Boston Children's Hospital, Boston, MA, USA.

Background: In addition to tricuspid regurgitation (TR) and right ventricular (RV) enlargement, patients with Ebstein anomaly are at risk for left ventricular (LV) dysfunction and dyssynchrony. We studied the impact of the cone tricuspid valve reconstruction operation on LV size, function, and dyssynchrony.

Methods: All Ebstein anomaly patients who had both pre- and postoperative cardiovascular magnetic resonance (CMR) studies were retrospectively identified. Read More

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http://dx.doi.org/10.1186/s12968-018-0452-0DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5963144PMC
May 2018
9 Reads

Surgical Management and Outcomes of Ebstein Anomaly in Neonates and Infants: A Society of Thoracic Surgeons Congenital Heart Surgery Database Analysis.

Ann Thorac Surg 2018 Sep 16;106(3):785-791. Epub 2018 May 16.

Division of Cardiac Surgery, Department of Surgery, Johns Hopkins University School of Medicine, Baltimore, Maryland.

Background: Ebstein anomaly (EA) encompasses a broad spectrum of morphology and clinical presentation. Those who are symptomatic early in infancy are generally at highest risk, but there are limited data regarding multicentric practice patterns and outcomes. We analyzed multiinstitutional data concerning operations and outcomes in neonates and infants with EA. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2018.04.049DOI Listing
September 2018
8 Reads

Influence of pregnancy on cardiac function and hemodynamics in women with Ebstein's anomaly.

Acta Obstet Gynecol Scand 2018 May 16. Epub 2018 May 16.

Department of Pediatric Cardiology, Division of Adult Congenital Heart Disease Pathophysiology and Life-long Care, Tokyo Women's Medical University, Tokyo, Japan.

Introduction: We examined the perinatal outcomes and right ventricular function before pregnancy, during pregnancy, and after delivery in women with Ebstein's anomaly.

Material And Methods: We retrospectively investigated the clinical course and mode of delivery and monitored hemodynamic parameters throughout pregnancy in 17 women with Ebstein's anomaly who delivered at our institution during the period of 1995-2015.

Results: Eight women, including nine pregnancies, underwent elective cesarean section, and nine women, including 14 pregnancies, underwent vaginal delivery. Read More

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http://dx.doi.org/10.1111/aogs.13373DOI Listing
May 2018
4 Reads

Fetal and Postnatal Echocardiographic Diagnosis of Ebstein Anomaly of the Mitral Valve.

Pediatr Cardiol 2018 Aug 14;39(6):1276-1279. Epub 2018 May 14.

Rush Center for Congenital Heart Disease, Rush University Medical College, Chicago, IL, USA.

Ebstein anomaly of mitral valve (MV) is an extremely rare congenital heart disease. In the current report, we present a case of Ebstein of MV that was diagnosed prenatally. Fetal echocardiogram showed that the posterior leaflet of MV was tethered to the lateral wall of left ventricle (LV) with downward displacement into LV cavity. Read More

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http://dx.doi.org/10.1007/s00246-018-1903-yDOI Listing
August 2018
5 Reads

Intracardiac echocardiography to guide catheter ablation of an accessory pathway in Ebstein's anomaly. A case report.

Med Ultrason 2018 May;20(2):250-253

5th Department of Internal Medicine, Cardiology-Rehabilitation, "Iuliu Hatieganu" University of Medicine and Pharmacy Cluj-Napoca, Romania..

We present the case of a 17-year-old girl with Ebstein anomaly and repeated episodes of reentrant tachycardia due to a right posterior accessory pathway. Catheter ablation was performed using intracardiac echocardiography. A ViewFlex Xtra probe was inserted and showed an anormal tricuspid valve with elongated anterior leaflet and low insertion of the septal leaflet towards the apex. Read More

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http://dx.doi.org/10.11152/mu-1347DOI Listing
May 2018
9 Reads

Wide complex tachycardia in a patient with Ebstein's anomaly.

J Cardiovasc Electrophysiol 2018 Sep 18;29(9):1321-1324. Epub 2018 May 18.

Cardiovascular Division, Electrophysiology Section, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, PA, USA.

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http://dx.doi.org/10.1111/jce.13624DOI Listing
September 2018
4 Reads

Outcomes of Ebstein's Anomaly Patients Treated with Tricuspid Valvuloplasty or Tricuspid Valve Replacement: Experience of a Single Center.

Chin Med J (Engl) 2018 May;131(9):1067-1074

Department of Cardiac Surgery, State Key Laboratory of Cardiovascular Disease, National Center for Cardiovascular Disease, Fuwai Hospital, Chinese Academy of Medical Sciences, Peking Union Medical College, Beijing 100037, China.

Background: The incidence of Ebstein's anomaly is extremely low, and except for the Mayo Clinic, no cardiac center has reported on a sufficient number of patients. The aim of our study was to report the outcomes of Ebstein's anomaly patients treated with tricuspid valvuloplasty (TVP) or tricuspid valve replacement (TVR).

Methods: TVP or TVR was performed in 245 patients from July 2006 to April 2016. Read More

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http://dx.doi.org/10.4103/0366-6999.230731DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5937315PMC
May 2018
15 Reads

Three-dimensional echocardiographic evaluation of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome.

Cardiol Young 2018 Jun 22;28(6):885-887. Epub 2018 Apr 22.

3Pediatric Cardiology,Children's Hospital Colorado,University of Colorado School of Medicine,Aurora,CO,USA.

We report three-dimensional imaging of a rare finding of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome, which has been previously reported only by two-dimensional echocardiography. A fetal echocardiogram was performed at 19 weeks that showed a moderately hypoplastic left ventricle, severely hypoplastic mitral valve, a severely hypoplastic aortic valve, and a dysplastic tricuspid valve. Post Caesarean delivery at 40 weeks of gestation, a transthoracic echocardiogram confirmed the findings seen on the fetal echocardiogram. Read More

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http://dx.doi.org/10.1017/S1047951118000367DOI Listing
June 2018
12 Reads

Editorial commentary: The caveats of cardiac imaging in Ebstein anomaly.

Trends Cardiovasc Med 2018 08 20;28(6):410-411. Epub 2018 Feb 20.

Cardiovascular Center Zurich, Klinik im Park, Switzerland. Electronic address:

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http://dx.doi.org/10.1016/j.tcm.2018.02.007DOI Listing
August 2018
6 Reads

Angiographic aspect of longstanding Starr-Edwards valve for type C Ebstein anomaly.

Asian Cardiovasc Thorac Ann 2018 May 27;26(4):326. Epub 2018 Mar 27.

Pediatric Cardiac Surgery and GUCH Unit, S. Orsola-Malpighi Hospital, 60273 University of Bologna, Bologna, Italy.

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http://dx.doi.org/10.1177/0218492318767793DOI Listing
May 2018
7 Reads

Identification of clinically relevant phenotypes in patients with Ebstein anomaly.

Clin Cardiol 2018 Mar 22;41(3):343-348. Epub 2018 Mar 22.

Departamento de Investigaciones, Fundación Cardioinfantil-Instituto de Cardiología, Bogotá, Colombia.

Background: Ebstein anomaly (EA) is a heterogeneous congenital heart defect (CHD), frequently accompanied by diverse cardiac and extracardiac comorbidities, resulting in a wide range of clinical outcomes.

Hypothesis: Phenotypic characterization of EA patients has the potential to identify variables that influence prognosis and subgroups with distinct contributing factors.

Methods: A comprehensive cross-sectional phenotypic characterization of 147 EA patients from one of the main referral institutions for CHD in Colombia was carried out. Read More

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http://dx.doi.org/10.1002/clc.22870DOI Listing
March 2018
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Clinical aspects of myocardial fibrosis in adults with Ebstein's anomaly.

Heart Vessels 2018 Sep 21;33(9):1076-1085. Epub 2018 Feb 21.

Department of Cardiology, University of Medical Sciences, ½ Dluga Street, 61-848, Poznan, Poland.

Heart failure and arrhythmia are common complications in adults with Ebstein's anomaly. They may result not only from hemodynamic alterations, but also from myocardial fibrosis. Late gadolinium enhancement (LGE) by CMR enables the evaluation of myocardial fibrosis. Read More

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http://dx.doi.org/10.1007/s00380-018-1141-5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6096744PMC
September 2018
4 Reads

Recurrent venous thrombosis in a patient with Ebstein's anomaly.

Saudi Med J 2018 Feb;39(2):209-212

College of Medicine, Alfaisal University, Riyadh, Kingdom of Saudi Arabia. E-mail.

Herein, we report a case of a 27-year-old man with Ebstein's anomaly and a history of unexplained recurrent venous thrombosis despite adequate anticoagulation. After surgical correction of the Ebstein's anomaly, the venous thromboembolic events did not recur. This case demonstrates the possible etiopathogenesis of Ebstein's anomaly in causing recurrent venous thromboembolism, which is likely caused through impedance of venous blood flow. Read More

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http://dx.doi.org/10.15537/smj.2018.2.21317DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5885100PMC
February 2018
5 Reads

Cardiac imaging in Ebstein anomaly.

Trends Cardiovasc Med 2018 08 12;28(6):403-409. Epub 2018 Jan 12.

Division of Cardiovascular Diseases, Mayo Clinic, Rochester, MN.

Ebstein anomaly is a congenital disorder of right ventricular myocardial development, which affects the tricuspid valve in addition to the right ventricular myocardium. Cardiac imaging by transthoracic echocardiography and cardiac magnetic resonance imaging are the key modalities used to assess timing and type of surgery. In this article, we review the current standards of echocardiographic and magnetic resonance imaging in Ebstein anomaly. Read More

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http://dx.doi.org/10.1016/j.tcm.2018.01.002DOI Listing
August 2018
13 Reads