190 results match your criteria Dysplasia Epiphysealis Hemimelica


Juvenile Dysplasia Epiphysealis Hemimelica with Multiple Ankle Free Body.

Case Rep Orthop 2021 9;2021:5579684. Epub 2021 Apr 9.

Department of Orthopedic Surgery, Faculty of Medicine, The University of Tokyo, 7-3-1 Hongo Bunkyo-ku, Tokyo 113-8655, Japan.

Dysplasia epiphysealis hemimelica (DEH), also known as Trevor's disease, is a rare overgrowth of cartilage that commonly arises in the epiphyseal bone of children. We report a rare case of DEH originating from a talus accompanied by multiple intra-articular free bodies in a 7-year-old patient with ankle instability. After the primary surgery for free body removal and microfracture technique for the cartilage defects in the ankle joint, the free body recurred. Read More

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Dysplasia epiphysealis hemimelica of the radial head: a rare case report.

BMC Musculoskelet Disord 2021 Feb 5;22(1):151. Epub 2021 Feb 5.

Rasoul-e-Akram Hospital, Iran University of Medical Sciences, Tehran, Iran.

Background: Dysplasia epiphysealis hemimelica (DEH) is a rare benign overgrowth generally affecting the epiphyses and short bones of the lower limbs. DEH in the elbow joint is extremely rare, and to date, only three cases of DEH have been reported in the radial head.

Case Presentation: In this study, we report a case of DEH located in the radial head of the right elbow of a 10-year-old boy, which was presented with elbow pain and limited range of motion. Read More

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February 2021

Dysplasia Epiphysealis Hemimelica (Trevor Disease) of the Patella: A Case Report.

JBJS Case Connect 2020 Jul-Sep;10(3):e2000003

1Department of Orthopaedics, Government Medical College & Hospital, Chandigarh, India 2Department of Radiodiagnosis & Imaging, Government Medical College & Hospital, Chandigarh, India 3Department of Pathology, Government Medical College & Hospital, Chandigarh, India.

Case: We report a rare case of dysplasia epiphysealis hemimelica in an 11-year-old male child involving the patella. The patient noticed swelling in the right knee 6 months before presentation. On evaluation, there was a mass lesion originating from superior pole of the patella extending into the suprapatellar pouch. Read More

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Dysplasia Epiphysealis Hemimelica Can Be Controlled by Growth Modulation: A Case Report.

JBJS Case Connect 2020 Jan-Mar;10(1):e0353

Department of Orthopaedic Surgery, Bone and Joint Diseases Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.

Case: Dysplasia epiphysealis hemimelica (DEH), or Trevor disease, is an abnormal nonmalignant overgrowth of the epiphysis on one side of the body, often confined to one half of a joint of a limb. There is no known etiology or treatment for it. We are reporting the case of a 4. Read More

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January 2021

TKA in the treatment of bilateral dysplasia epiphysealis hemimelica (Trevor's Disease) of the knee in a 50-year-old man: a case report.

BMC Musculoskelet Disord 2020 Mar 14;21(1):167. Epub 2020 Mar 14.

Department of Orthopaedics, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, 430022, China.

Background: Dysplasia epiphysealis hemimelica (DEH), also known as Trevor's disease, is a rare skeletal developmental disorder affecting the epiphyses in pediatric patients. DEH is characterized by an asymmetric osteochondral overgrowth arising from either the medial or lateral portion of an epiphysis and usually occurs in the joints of lower limbs, most commonly in the knees and ankles. However, bilateral involvement in an adult is extremely rare, and total knee arthroplasty (TKA) for a patient with DEH has been reported only once before. Read More

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Trevor's disease of the distal radioulnar joint in two children with achondroplasia.

Am J Med Genet A 2020 05 29;182(5):1249-1254. Epub 2020 Feb 29.

Department of Orthopedics and Rehabilitation, University of Wisconsin School of Medicine and Public Health, Madison, Wisconsin.

Two children with achondroplasia who developed an abnormal bony outgrowth at the distal radioulnar joint (DRUJ), indistinguishable from an osteochondroma on histology, but the radiographic appearance, location, and asymmetry suggested the rare diagnosis of dysplasia epiphysealis hemimelica (DEH or "Trevor's disease"). One child experienced symptomatic relief with surgical excision and one was observed clinically due to lack of significant symptoms. These are the first presented cases of DEH in achondroplasia, both affecting the DRUJ. Read More

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Dysplasia epiphysealis hemimelica combined with contralateral accessory scaphoid bone: A case report and literature review.

Medicine (Baltimore) 2019 Nov;98(45):e17887

Department of Pediatric Orthopedics, Hunan Provincial People's Hospital, the First Affiliated Hospital of Hunan Normal University, Changsha, Hunan, China.

Rationale: Dysplasia epiphysealis hemimelica (DEH), also known as Trevor disease, is a rare, developmental bone disorder of childhood.

Patient Concerns: A 9-year-old girl was admitted due to pain in front of the medial malleolus of her right foot after a long walk or distance movement, in which the pain could be relieved after rest, while it was repeated and lasted for several months.

Diagnosis: Dysplasia epiphysealis hemimelica INTERVENTIONS:: The patient underwent an open resection surgery. Read More

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November 2019

Dysplasia Epiphysealis Hemimelica/Trevor Disease: Report of a Lesion Solely Involving the Lunate Bone: A Case Report.

JBJS Case Connect 2019 Dec;9(4):e0511

Division of Orthopaedic Surgery, IWK Health Centre, Dalhousie University, Halifax, Nova Scotia, Canada.

Case: We describe the case of a dysplasia epiphysealis hemimelica (DEH) lesion affecting uniquely the lunate bone in a 16-year-old boy causing pain, stiffness, and decreased range of motion. Surgical excision was performed, leading to resolution of primary symptoms with residual limitations in terminal wrist extension.

Conclusions: From our review of the literature, we believe this case to be the first report of a DEH lesion affecting solely the lunate bone. Read More

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December 2019

Benign bone tumours of tibial tuberosity clinically mimicking Osgood-Schlatter disease: a case series.

Int Orthop 2019 11 11;43(11):2563-2568. Epub 2019 Sep 11.

Bone and Joint Reconstruction Research Center, Shafa Orthopedic Hospital, Iran University of Medical Sciences, Tehran, IR, Iran.

Introduction: Osgood-Schlatter disease (OSD) is a traction apophysitis of the tibial tubercle and a common cause of anterior knee pain in growing adolescents. A variety of benign neoplasms can also cause bony prominence over the tibial tubercle in adolescents that might clinically imitate OSD. Therefore, the differential diagnosis of tumours mimicking OSD is critical and considered the primary goal of this study. Read More

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November 2019

Combined Anterior and Posterior Ankle Arthroscopy for Dysplasia Epiphysealis Hemimelica of the Ankle in a Child: A Case Report.

J Orthop Case Rep 2019 Jan-Feb;9(1):90-93

Department of Orthopaedics and Traumatology, Sultan Qaboos Hospital, Salalah, Oman.

Introduction: Dysplasia Epiphysealis Hemimelica (DEH)is a rare developmental epiphyseal disease characterized by asymmetri cover growth of cartilage in the epiphysis, histologically mimics osteochondroma of the joints. The disease mainly involves ankle, knee and tarsal bones. Small number of cases is reported in literature particularly those managed arthroscopically. Read More

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Asymptomatic Dysplasia Epiphysealis Hemimelica of the Shoulder in a Skeletally Mature Patient with Normal Function.

Case Rep Radiol 2019 27;2019:5356246. Epub 2019 Mar 27.

Departamento de Radiologia, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil.

Dysplasia epiphysealis hemimelica is a rare osteocartilaginous overgrowth syndrome of bone epiphysis, mostly encountered in the lower limbs of immature skeleton patients. We report a case of proximal humerus presentation in an adult male, with neither articular involvement nor clinical dysfunction. This case highlights the importance of stratification into intra- and extra-articular lesions, as this distinction ultimately influences both symptoms and treatment outcome. Read More

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Watching and waiting in chronic hip pain.

Lancet 2019 04 4;393(10179):e36. Epub 2019 Apr 4.

Prince of Wales Clinical School, Department of Orthopaedics, Prince of Wales Hospital, University of New South Wales, Sydney, NSW, Australia; Department of Orthopaedics, Prince of Wales Private Hospital, Sydney, NSW, Australia.

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An unusual presentation of Trevor's disease at the ankle joint: Involvement of both medial and lateral epiphyses.

Foot (Edinb) 2018 Sep 31;36:55-58. Epub 2018 Jan 31.

İstanbul Medeniyet University Goztepe Training and Research Hospital, Orthopaedics and Traumatology Department, Turkey. Electronic address:

Introduction: Trevor's disease, also known as dyplasia epiphysealis hemimelica, is characterised by osteochondromas arising from epiphyses. The disease typically affects one side of an epiphysis (usually the medial side).

Case Presentation: A case in whom both the medial and lateral sides of the epiphysis were involved is described. Read More

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September 2018

More Than Epiphyseal Osteochondromas: Updated Understanding of Imaging Findings in Dysplasia Epiphysealis Hemimelica (Trevor Disease).

AJR Am J Roentgenol 2018 10 30;211(4):910-919. Epub 2018 Aug 30.

1 Department of Radiology, The Children's Hospital of Philadelphia, 3NW39, 3401 Civic Center Blvd, Philadelphia, PA 19104.

Objective: The purpose of this article is to discuss approaches to imaging dysplasia epiphysealis hemimelica in the context of recent advances in the understanding of the underlying pathophysiologic profile of this entity, which may result in pain, growth disturbance, and early development of osteoarthritis.

Conclusion: Dysplasia epiphysealis hemimelica was first characterized as a skeletal disorder with osteochondromas characteristically involving epiphyses on one side of the same lower extremity. Upper extremity involvement was subsequently recognized. Read More

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October 2018

Arthroscopic treatment of intra-articular dysplasia epiphysealis hemimelica of the knee.

SAGE Open Med Case Rep 2018 26;6:2050313X18790166. Epub 2018 Jul 26.

Department of Orthopaedic Surgery and Sports Medicine, Tsukuba University Hospital Mito Clinical Education and Training Center, Mito Kyodo General Hospital, University of Tsukuba, Mito, Japan.

Dysplasia epiphysealis hemimelica, also known as Trevor Fairbank disease, is characterized by asymmetrical osteochondral overgrowth of the epiphyseal cartilage. The clinical presentation of dysplasia epiphysealis hemimelica is wide and variable, depending on the site of the lesion. Herein, we describe the physical examination of a 9-year-old boy with intra-articular dysplasia epiphysealis hemimelica, in whom the symptoms were elicited on "reverse Wilson's sign": bending the knee from 70° to 120° against resistance while externally rotating the tibia. Read More

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A child with painless left wrist swelling.

Skeletal Radiol 2018 04;47(4):547-548

Department of Diagnostic and Interventional Radiology, Kwong Wah Hospital, 25 Waterloo Road, Yau Ma Tei, Hong Kong.

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The Natural History of the Development of Trevor Disease of the Hip and Subsequent Arthroplasty: A Case Report.

JBJS Case Connect 2017 Jul-Sep;7(3):e67

1Department of Orthopaedic Surgery, Bone and Joint Diseases Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.

Case: Trevor disease (dysplasia epiphysealis hemimelica [DEH]) is a rare, intra-articular anomaly of cartilaginous overgrowth of the epiphysis. The usual presentation is on 1 side of the body and on 1 side of the epiphysis. The natural history of this disease is not clear because the lesions often are treated during childhood. Read More

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Dysplasia epiphysealis hemimelica: a histological comparative study with osteochondromas.

J Child Orthop 2017 Jun;11(3):160-168

Department of Orthopaedic Surgery, Research School CAPHRI, Maastricht University Medical Centre, Maastricht, The Netherlands.

Purpose: Dysplasia epiphysealis hemimelica (DEH) is a rare developmental disorder resulting in epiphyseal overgrowth. Based on histological appearance, it is often described as an osteochondroma or osteochondroma-like lesion, although clinical differences exist between DEH and osteochondromas. The aim of this study was to test whether DEH and osteochondromas are histologically identical diseases. Read More

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Arthroscopic Treatment of 2 Consecutive Cases of Dysplasia Epiphysealis Hemimelica of the Ankle: A 5-Year Follow-Up Report.

Case Rep Orthop 2017 30;2017:3175765. Epub 2017 May 30.

Orthopaedic and Traumatology Department, S. Andrea Hospital, Faculty of Medicine and Psychology, "Sapienza" University of Rome, Rome, Italy.

The dysplasia epiphysealis hemimelica (DEH) is a rare disease of unknown etiology consisting in an abnormal osteocartilaginous growth at the epiphysis, usually hemimelic with histological findings similar to benign osteochondroma. In this case series, we described the results of the arthroscopic treatment of 2 consecutive cases of intra-articular ankle localization of DEH in 2 patients aged 9 and 10 years. The good result obtained, persistent at the 5-year follow-up, leads us to consider the arthroscopic approach as a reliable treatment in patient affected by intra-articular ankle DEH. Read More

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Novel case of Trevor's disease: Adult onset and later recurrence.

World J Orthop 2017 Jan 18;8(1):77-81. Epub 2017 Jan 18.

Amrit S Khalsa, Neil S Kumar, Matthew A Chin, the Department of Orthopaedic Surgery, Hahnemann University Hospital, Philadelphia, PA 19102, United States.

Dysplasia epiphysealis hemimelica (DEH), or Trevor's disease, is an osteocartilaginous epiphyseal overgrowth typically occurring in children. The literature reports 6 adult cases and none describe recurrence requiring additional procedures. We present a new-onset proximal tibial DEH in an adult recurring approximately 3 years after open excision. Read More

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January 2017

Dysplasia epiphysealis hemimelica of the lower limb.

Skeletal Radiol 2017 Jan 14;46(1):111-115. Epub 2016 Oct 14.

School of Medicine, Pathology Department, Gaziosmanpasa University, Tokat, Turkey.

Dysplasia epiphysealis hemimelica (DEH) is a rare developmental disorder characterized by osteocartilaginous overgrowth in one or more epiphyses. The disease usually involves a single limb or is hemimelic (lateral or medial compartment), and lower extremities are more frequently affected than upper extremities. Here we present clinical and radiological findings for a male DEH patient at 1. Read More

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January 2017

[An eight-year-old boy with painful flat feet].

Radiologe 2016 Oct;56(10):917-920

Abteilung für Diagnostische und Interventionelle Radiologie, Radiologische Klinik, Universitätsklinikum Heidelberg, Im Neuenheimer Feld 110, 69120, Heidelberg, Deutschland.

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October 2016

Trevor's Disease: Management Difficulties and Proposed Classification.

Authors:
Daine O Clarke

Orthopedics 2016 Sep 1;39(5):e967-9. Epub 2016 Jun 1.

Dysplasia epiphysealis hemimelica, also known as Trevor's disease, is a rare developmental disorder with osteocartilagenous overgrowth of the epiphysis or epiphyseal equivalent. The condition bears similarities to osteochondroma in terms of its radiographic appearance, but differs in its pathobiology and geographic occurrence. Unlike the metaphyseal occurrence of osteochondromata, it arises from the epiphysis. Read More

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September 2016

Dysplasia epiphysealis hemimelica (Trevor disease) in the ankle.

Ther Clin Risk Manag 2016 6;12:545-7. Epub 2016 Apr 6.

Department of Orthopedics and Traumatology, Kayseri Training and Research Hospital, Kayseri, Turkey.

Dysplasia epiphysealis hemimelica, also termed Trevor disease, is a rare disorder that, although benign in nature, can be locally aggressive, particularly when affecting the ankle joint, which is the joint most frequently affected, followed by the knee. The female:male ratio is 1:3, and it is generally diagnosed between 2 and 14 years of age. Surgical treatment with complete resection is recommended before irreversible joint damage and deformity occurs. Read More

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Trevor's disease: up-to-date review of the literature with case series.

J Pediatr Orthop B 2017 Nov;26(6):532-545

Departments of aOrthopaedics and Trauma bRadiodiagnostic, Antalya Memorial Hospital cOrthopaedics and Trauma Department, Akdeniz University School of Medicine, Antalya dOrthopaedics and Trauma Department, Ozel Bahar Hospital, Bursa, Turkey.

Trevor's disease, also known as dysplasia epiphysealis hemimelica, is a rare nonhereditary skeletal development disorder that affects epiphyses. This type of dysplastic lesion was first reported by Mouchet and Berlot in 1926 under the name 'tarsomegaly'. The main aim of this study is to raise awareness of Trevor's disease among orthopedic surgeons and underline some important aspects of treatment by a detailed presentation of four different possible manifestations of the disease. Read More

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November 2017

Dysplasia epiphysealis hemimelica of the ankle: a fracture-like rare developmental disorder.

BMJ Case Rep 2015 Sep 30;2015. Epub 2015 Sep 30.

Athens Children's Hospital Aghia Sophia, Athens, Greece.

Dysplasia epiphysealis hemimelica is a rare developmental disorder which affects the epiphyses. We report a case of the disease located in the ankle joint, referred to our clinic with the initial misdiagnosis of a Salter-Harris 3 type fracture of the distal epiphysis of the tibia. After correct diagnosis, the patient was treated surgically with the excision of the cartilaginous masses. Read More

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September 2015

Dysplasia Epiphysealis Hemimelica Treated with Osteochondral Allograft: A Case Report.

Iowa Orthop J 2015 ;35:42-8

The Department of Orthopaedic Surgery and Rehabilitation, University of Iowa Hospitals and Clinics , 200 Hawkins Drive, 01008 JPP, Iowa City, IA 52242 , USA.

Background: Dysplasia epiphysealis hemimelica (DEH), or Trevor's disease, is a developmental disorder of the pediatric skeleton characterized by asymmetric osteochondral overgrowth.

Methods: We present the case of a five year old boy with a two year history of right knee pain and evidence of DEH on imaging who underwent initial arthroscopic resection of his lesion with subsequent recurrence. The patient then underwent osteochondral allograft revision surgery and was asymptomatic at two year follow-up with a congruent joint surface. Read More

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Response to Comment on the article 'Dysplasia epiphysealis hemimelica of the knee: an unusual presentation with intra-articular loose bodies and literature review' by Wheeldon and Altiok. J Pediatr Orthop B 2015:377-378.

J Pediatr Orthop B 2015 Sep;24(5):479-81

aCollege of Human Medicine, Michigan State University, East Lansing, Michigan bShriners Hospitals for Children, Chicago, Illinois, USA.

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September 2015

Comment on the article 'Dysplasia epiphysealis hemimelica of the knee: an unusual presentation with intra-articular loose bodies and literature review' by Wheeldon and Altiok.

J Pediatr Orthop B 2015 Jul;24(4):377-8

aDeparment of Orthopaedics and Trauma, Ozel Antalya Memorial Hospital, Antalya bDepartment of Orthopedics and Trauma, Bursa Ozel Bahar Hospital, Bursa, Turkey.

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