Liver transplantation as definitive treatment of an unresectable mesenchymal hamartoma in a child with Beckwith-Wiedemann Syndrome.
- Evelyn T Pan,
- Dor Yoeli,
- Michael L Kueht,
- N Thao N Galvan,
- Ronald T Cotton,
- Christine A O'Mahony,
- Abbas Rana,
- John A Goss
J Surg Case Rep 2017 Aug 31;2017(8):rjx167. Epub 2017 Aug 31.
Michael E DeBakey Department of Surgery, Division of Abdominal Transplantation, Baylor College of Medicine and Texas Children's Hospital, Houston, TX, USA.
Mesenchymal liver hamartomas are benign tumors that can cause life-threatening abdominal distension and carry a risk for malignant transformation. In this case report, we describe a 13-month-old male with Beckwith-Wiedemann Syndrome (BWS) who presented with multiple mesenchymal liver hamartomas causing severe intra-abdominal mass effect. Imaging revealed six large multi-locular cystic lesions, ranging from 3. Read More