1,346 results match your criteria Congenital Heart Disease[Journal]


Comparison of creatinine and cystatin C for estimation of glomerular filtration rate in pediatric patients after Fontan operation.

Congenit Heart Dis 2019 Apr 16. Epub 2019 Apr 16.

Section of Pediatric Cardiology, Department of Pediatrics, University of Colorado, Children's Hospital Colorado, Aurora, Colorado.

Background: There are several limitations when using creatinine to estimate glomerular filtration rate, especially in children with chronic medical conditions who are at high risk of kidney dysfunction. Cystatin C has been the recent focus of research as a replacement biomarker for creatinine. Our objective was to compare the 2 biomarkers in pediatric single-ventricle heart disease patients who have undergone the Fontan operation. Read More

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http://dx.doi.org/10.1111/chd.12776DOI Listing
April 2019
1 Read

Serial assessment of postoperative ventricular mechanics in young children with tetralogy of Fallot: Comparison of transannular patch and valve-sparing repair.

Congenit Heart Dis 2019 Apr 15. Epub 2019 Apr 15.

Division of Pediatric Cardiothoracic Surgery, Betty Irene Moore Heart Center Clinical and Translational Research Program, Lucile Packard Children's Hospital, Stanford University Medical Center, Palo Alto, California.

Background: Little is known about the early time course of biventricular function and mechanics after tetralogy of Fallot (TOF) repair. We sought to evaluate and describe the evolution of the right ventricle (RV) after TOF repair in young infants and children using conventional echocardiographic parameters and global longitudinal strain (GLS).

Methods: A retrospective review was performed of all patients with TOF and pulmonary stenosis who underwent repair from January 2002 to September 2015 and had at least 3 serial postsurgical echocardiograms spanning from infancy to early childhood (<8 years). Read More

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http://dx.doi.org/10.1111/chd.12772DOI Listing
April 2019
1 Read

Hand-held echocardiography in children with hypoplastic left heart syndrome.

Congenit Heart Dis 2019 Apr 11. Epub 2019 Apr 11.

Section of Pediatric Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas.

Background: When performed by cardiologists, hand-held echocardiography (HHE) can assess ventricular systolic function and valve disease in adults, but its accuracy and utility in congenital heart disease is unknown. In hypoplastic left heart syndrome (HLHS), the echocardiographic detection of depressed right ventricular (RV) systolic function and higher grade tricuspid regurgitation (TR) can identify patients who are at increased risk of morbidity and mortality and who may benefit from additional imaging or medical therapies.

Methods: Children with HLHS after Stage I or II surgical palliation (Norwood or Glenn procedures) were prospectively enrolled. Read More

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http://dx.doi.org/10.1111/chd.12774DOI Listing
April 2019
1 Read

Right ventricular and pulmonary vascular function indices for risk stratification of patients with pulmonary regurgitation.

Congenit Heart Dis 2019 Apr 8. Epub 2019 Apr 8.

Department of Cardiovascular Medicine, Mayo Clinic Rochester, Rochester, Minnesota.

Background: We hypothesized that echocardiographic indices of right ventricular to pulmonary artery (RV-PA) coupling were comparable to cardiac magnetic resonance imaging (CMRI)-derived RV volumetric indices in predicting disease severity in chronic pulmonary regurgitation (PR).

Methods: Patients with ≥ moderate PR (2003-2015) with and without prior CMRI scans were enrolled into the study cohort and validation cohort, respectively. Endpoint was to determine the association between noninvasive RV-PA coupling indices (tricuspid annular plane systolic excursion/right ventricular systolic pressure [TAPSE/RVSP] and fractional area change [FAC]/RVSP ratio) and markers of disease severity, and compared this association to that of CMRI-derived RV volumetric indices and markers of disease severity (peak oxygen consumption [VO ], NT-proBNP and atrial and/or ventricular arrhythmias). Read More

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http://dx.doi.org/10.1111/chd.12768DOI Listing
April 2019
7 Reads
1.202 Impact Factor

Initiating a Fontan multidisciplinary clinic: Decreasing care variability, improving surveillance, and subsequent treatment of Fontan survivors.

Congenit Heart Dis 2019 Apr 8. Epub 2019 Apr 8.

Heart Institute, Section of Pediatric Cardiology, Department of Pediatrics, University of Colorado School of Medicine, Children's Hospital Colorado, Aurora, CO.

Background: Children with single ventricle (SV) heart disease who undergo Fontan operation are at risk for developing multiorgan dysfunction. Although survival has improved, significant comorbidities involving multiple organ systems may develop, requiring evaluation and management by many subspecialists. Using data from an internal survey, we documented high care variability for our Fontan population. Read More

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http://dx.doi.org/10.1111/chd.12769DOI Listing
April 2019
1 Read

Do we have the ACHD physician resources we need to care for the burgeoning ACHD population?

Congenit Heart Dis 2019 Apr 4. Epub 2019 Apr 4.

Indiana University School of Medicine, Krannert Institute of Cardiology and Section of Pediatric Cardiology, Indianapolis, Indiana.

Background: Delivery of care to the adult congenital heart disease (ACHD) population has been limited by a shortage in the ACHD physician resources. There is limited data regarding the adequacy of the ACHD physician resources in the United States and our population estimates are extrapolated from Canadian data. Therefore, we proposed to evaluate the adequacy of ACHD physician: patient ratios in the United States at both national and regional levels. Read More

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http://dx.doi.org/10.1111/chd.12771DOI Listing
April 2019
1 Read

Reflections on mentoring.

Authors:
Jane W Newburger

Congenit Heart Dis 2019 Mar;14(2):126-127

Department of Cardiology, Boston Children's Hospital, Boston, Massachusetts.

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http://dx.doi.org/10.1111/chd.12773DOI Listing

Anticipatory perioperative management for patent ductus arteriosus surgery: Understanding postligation cardiac syndrome.

Congenit Heart Dis 2019 Mar;14(2):311-316

Department of Pediatrics, University of Iowa, Iowa City, Iowa.

Ligation of a hemodynamically significant ductus arteriosus results in significant changes in loading conditions which have predictable consequences. Postligation cardiac syndrome, defined as hypotension requiring inotropic support and failure of oxygenation and ventilation, may occur 6-12 hours following ligation due to left ventricular systolic and diastolic failure, respectively. Afterload is the primary driver of this decompensation. Read More

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https://onlinelibrary.wiley.com/doi/abs/10.1111/chd.12738
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http://dx.doi.org/10.1111/chd.12738DOI Listing
March 2019
8 Reads

Optimum age for performing Fontan operation in patients with univentricular heart.

Congenit Heart Dis 2019 Mar;14(2):138-139

Department of Cardiovascular Medicine, Mayo Clinic, Rochester, Minnesota.

The purpose of this study was to determine the optimal age for performing Fontan operation using data from the National Inpatient Sample. Our results showed that although the Fontan operation was most commonly performed at age 2 in the United States, age 3 is the optimum age for this procedure as evident by lower rate of in-hospital mortality, procedure-related complications, and rate of nonroutine home discharge when procedure is performed at age 3 years. Read More

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http://dx.doi.org/10.1111/chd.12690DOI Listing
March 2019
2 Reads
1.202 Impact Factor

Cognitive dysfunction is associated with abnormal responses in cerebral blood flow in patients with single ventricular physiology: Novel insights from transcranial Doppler ultrasound.

Congenit Heart Dis 2019 Mar 25. Epub 2019 Mar 25.

Department of Medicine, John Hunter Hospital, New Lambton, Australia.

Objectives: Improvements in the management of complex congenital heart disease, including those with single ventricle physiology, have resulted in increased survival. As this population ages, the recognition of cognitive impairment is increasingly important. At present, little is known about the potential mechanisms of cognitive dysfunction. Read More

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http://dx.doi.org/10.1111/chd.12763DOI Listing

Long-term follow-up of adult patients with congenital heart disease and an implantable cardioverter defibrillator.

Congenit Heart Dis 2019 Mar 19. Epub 2019 Mar 19.

Cardiology Department, Hospital de Santa Marta, Centro Hospitalar Universitário de Lisboa Central, Lisbon, Portugal.

Objective: Sudden cardiac death is common in the adult congenital heart disease (ACHD) population. Knowledge and experience about the use of implantable cardioverter defibrillators (ICD) in ACHD patients is very limited. We aimed to characterize a cohort of patients with ACHD and ICDs. Read More

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https://onlinelibrary.wiley.com/doi/abs/10.1111/chd.12767
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http://dx.doi.org/10.1111/chd.12767DOI Listing
March 2019
6 Reads

Pacemaker treatment after Fontan surgery-A Swedish national study.

Congenit Heart Dis 2019 Mar 18. Epub 2019 Mar 18.

Department of Clinical Sciences, Umeå University, Umeå, Sweden.

Objective: Fontan surgery is performed in children with univentricular heart defects. Previous data regarding permanent pacemaker implantation frequency and indications in Fontan patients are limited and conflicting. We examined the prevalence of and risk factors for pacemaker treatment in a consecutive national cohort of patients after Fontan surgery in Sweden. Read More

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http://dx.doi.org/10.1111/chd.12766DOI Listing
March 2019
1 Read

Midterm outcomes of right ventricular outflow tract reconstruction using the Freestyle xenograft.

Congenit Heart Dis 2019 Mar 12. Epub 2019 Mar 12.

Department of Cardiothoracic Surgery, Cook Children's Medical Center, Fort Worth, Texas.

Objective: Various options exist for right ventricular outflow tract (RVOT) reconstruction in congenital heart disease. The Freestyle porcine aortic root may be used but its longevity is not well defined.

Design: We performed a retrospective review of all non-Ross RVOT reconstructions using the Freestyle root in our institution. Read More

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http://dx.doi.org/10.1111/chd.12765DOI Listing
March 2019
1 Read

Echocardiographic parameters of severe pulmonary regurgitation after surgical repair of tetralogy of Fallot.

Congenit Heart Dis 2019 Mar 7. Epub 2019 Mar 7.

Department of Cardiology, Erasmus Medical Center, Rotterdam, The Netherlands.

Aims: Reliable evaluation of the severity and consequences of pulmonary regurgitation (PR) in patients with repaired tetralogy of Fallot (TOF) is crucial to timely identify the need for pulmonary valve intervention. We aimed to identify the accuracy of echocardiographic parameters to differentiate between moderate and severe PR, using phase contrast cardiac magnetic resonance imaging (CMR) as gold standard.

Methods And Results: In this cross-sectional study, 45 TOF patients with both echocardiographic and CMR measurements of PR were enrolled. Read More

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http://dx.doi.org/10.1111/chd.12762DOI Listing
March 2019
1 Read

Predictors of extracorporeal membrane oxygenation support after surgery for adult congenital heart disease in children's hospitals.

Congenit Heart Dis 2019 Mar 5. Epub 2019 Mar 5.

Division of Cardiology, Seattle Children's Hospital, Seattle, Washington.

Objective: Adult congenital heart disease (ACHD) patients who undergo cardiac surgery are at risk for poor outcomes, including extracorporeal membrane oxygenation support (ECMO) and death. Prior studies have demonstrated risk factors for mortality, but have not fully examined risk factors for ECMO or death without ECMO (DWE). We sought to identify risk factors for ECMO and DWE in adults undergoing congenital heart surgery in tertiary care children's hospitals. Read More

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http://dx.doi.org/10.1111/chd.12758DOI Listing

Electronic health record associated stress: A survey study of adult congenital heart disease specialists.

Congenit Heart Dis 2019 Mar 1. Epub 2019 Mar 1.

Congenital Heart Center, Spectrum Health Helen DeVos Children's Hospital, Grand Rapids, Michigan.

Background: Physician burnout has many undesirable consequences, including negative impact on patient care delivery and physician career satisfaction. Electronic health records (EHRs) may exacerbate burnout by increasing physician workload.

Objective: To determine burnout in adult congenital heart disease (ACHD) specialists by assessing stress associated with EHRs. Read More

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http://dx.doi.org/10.1111/chd.12745DOI Listing
March 2019
1 Read

Exploration of the Notch3-HES5 signal pathway in monocrotaline-induced pulmonary hypertension using rat model.

Congenit Heart Dis 2019 Feb 27. Epub 2019 Feb 27.

Department of Cardiothoracic Surgery, Xiangya Hospital Central South University, Changsha, P.R. China.

Objective: This study explores the role of the Notch3-HES5 signal pathway in monocrotaline-induced pulmonary hypertension (PH) using rat models.

Method: Sprague Dawley rats (n = 45) were randomly grouped into normal group, control group, and model group. Rats in the model group were used to establish the PH rat model. Read More

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http://dx.doi.org/10.1111/chd.12733DOI Listing
February 2019

Surgical management of patent ductus arteriosus.

Congenit Heart Dis 2019 Jan;14(1):57-59

Department of Pediatric Cardiothoracic Surgery, Le Bonheur Children's Hospital, University of Tennessee Health Science Center, Memphis, Tennessee.

Surgical ligation of patent ductus arteriosus can be performed safely by following standard steps of operation. Familiarity of the anatomical landmarks and simple precautions result in high degree of safety. The technique of surgical ligation varies with the age of the patient. Read More

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http://dx.doi.org/10.1111/chd.12699DOI Listing
January 2019
1 Read
1.202 Impact Factor

Practice variation in the management of patent ductus arteriosus in extremely low birth weight infants in the United States: Survey results among cardiologists and neonatologists.

Congenit Heart Dis 2019 Jan;14(1):6-14

The Lillie Frank Abercrombie Section of Cardiology, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas.

Background: Patent ductus arteriosus (PDA) is highly prevalent in extremely low birth weight (ELBW), preterm infants. There are diverse management approaches for the PDA in ELBW infants. The objectives of this research were to identify current PDA management practices among cardiologists and neonatologists in the United States, describe any significant differences in management, and describe areas where practices align. Read More

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http://dx.doi.org/10.1111/chd.12729DOI Listing
January 2019
1 Read

Blalock-Taussig shunt versus patent ductus arteriosus stent as first palliation for ductal-dependent pulmonary circulation lesions: A review of the literature.

Congenit Heart Dis 2019 Jan;14(1):105-109

The Cardiac Center at the Children's Hospital of Philadelphia, University of Pennsylvania School of Medicine, Philadelphia, Pennsylvania.

Background: Infants with ductal-dependent pulmonary blood flow (PBF) often undergo a palliative procedure to provide a stable source of PBF prior to definitive palliation or repair. In the current era, a surgical shunt or ductal stent is used to provide PBF. We aimed to review the current literature comparing ductal stents to surgical shunts. Read More

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http://dx.doi.org/10.1111/chd.12707DOI Listing
January 2019
2 Reads

Echocardiographic guidance for transcatheter patent ductus arteriosus closure in extremely low birth weight infants.

Congenit Heart Dis 2019 Jan;14(1):74-78

Division of Pediatric Cardiology, University of Tennessee Health Science Center, Le Bonheur Children's Hospital, Memphis, Tennessee.

Echocardiographic imaging provides real-time guidance during transcatheter patent ductus arteriosus (PDA) closure in extremely low birth weight (ELBW) infants. Transthoracic echocardiogram provides detailed assessment of the PDA and surrounding structures prior to, during, and after transcatheter closure. This article aims to review the different echocardiographic techniques and concepts utilized during transcatheter PDA closure in ELBW infants. Read More

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http://dx.doi.org/10.1111/chd.12725DOI Listing
January 2019
1 Read

Echocardiography of the patent ductus arteriosus in premature infant.

Congenit Heart Dis 2019 Jan;14(1):42-45

Pediatric Cardiology, University of Tennessee Health Science Center, Le Bonheur Children's Hospital, Memphis, Tennessee.

Management of the patent ductus arteriosus (PDA) in the premature infant has been a point of controversy for decades as smaller and earlier gestational age infants have been surviving. Increasing experience with catheter-based device closure has generated a new wave of interest in this subject. In this era, echocardiography plays a central role for collaboration within a multispecialty team. Read More

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http://dx.doi.org/10.1111/chd.12703DOI Listing
January 2019
2 Reads

Live broadcast of transcatheter PDA closure in a 700 grams ELBW infant during the International PDA Symposium.

Congenit Heart Dis 2019 Jan;14(1):85-89

University of Tennessee Health Science Center, LeBonheur Children's Hospital, Memphis, Tennessee.

Objective: The objective of this article is to describe a live case transmission of transcatheter closure of a patent ductus arteriosus (PDA) in an extremely low birth weight (ELBW) infant during the first International PDA Symposium conducted in Memphis, Tennessee.

Setting: A multidisciplinary team approach including audiovisual specialists, information technology specialists, physicians, nurses, and other health care specialists was required to perform the transcatheter PDA closure (TCPC) in an ELBW infant at LeBonheur Children's Hospital and the procedure was broadcast live to the attendees at the International PDA Symposium allowing for a two-way audiovisual discussion during the procedure.

Patient: The patient was a 14 days old 24-week premature ELBW infant, who weighed 700 g at the time of the procedure. Read More

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http://doi.wiley.com/10.1111/chd.12710
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http://dx.doi.org/10.1111/chd.12710DOI Listing
January 2019
7 Reads

PDA: To treat or not to treat.

Congenit Heart Dis 2019 Jan;14(1):46-51

Division of Neonatal and Developmental Medicine, Stanford University School of Medicine, Palo Alto, California.

Management of patent ductus arteriosus in extremely preterm infants remains a topic of debate. Treatment to produce ductal closure was widely practiced until the past decade, despite lack of evidence that it decreases morbidities or mortality. Meta-analyses of trials using nonsteroidal anti-inflammatory drugs have shown effectiveness in accelerating ductal closure, but no reduction in neonatal morbidities, regardless of agent used, indication, timing, gestational age, or route of administration. Read More

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http://dx.doi.org/10.1111/chd.12708DOI Listing
January 2019
1 Read

Percutaneous closure of the patent ductus arteriosus: opportunities moving forward.

Congenit Heart Dis 2019 Jan;14(1):95-99

Center for Perinatal Research, The Research Institute at Nationwide Children's Hospital, Columbus, Ohio.

The optimal treatment method for infants with a patent ductus arteriosus (PDA) necessitating closure remains a subject of controversy and debate. While the risks associated with surgical PDA ligation are well described, the available evidence base for alternative management strategies during infancy, including percutaneous closure or conservative (nonintervention) management, are not well explored. Among infants, the goals of this review are to: (a) use rigorous systematic review methodology to assess the quality and quantity of published reports on percutaneous closure vs surgical ligation; (b) compare outcomes of percutaneous closure vs conservative management; and (c) based on recommendations from the International PDA symposium, to elucidate needs and opportunities for future research and interdisciplinary collaboration. Read More

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http://dx.doi.org/10.1111/chd.12704DOI Listing
January 2019
1 Read

Comparative case studies: PDAs treated with medication, surgical ligation, and transcatheter device closure.

Congenit Heart Dis 2019 Jan;14(1):65-68

Le Bonheur Children's Hospital, Memphis, Tennessee.

The ductus arteriosus is a lifeline for the developing fetus prior to delivery, allowing the circulation of oxygen-rich blood from the placenta to bypass the lungs and perfuse the body. However, when the ductus fails to close after birth, the pressures can cause blood to shunt from the aorta back into the lungs, causing pulmonary edema. This is called a left-to-right shunt. Read More

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http://dx.doi.org/10.1111/chd.12711DOI Listing
January 2019

Can transcatheter PDA closure be performed in neonates ≤1000 grams? The Memphis experience.

Congenit Heart Dis 2019 Jan;14(1):79-84

University of Tennessee Health Science Center, LeBonheur Children's Hospital, Memphis, Tennessee.

Objective: Advancements in transcatheter technology have now made it possible to safely close patent ductus arteriosus (PDA) in extremely low birth weight (ELBW) infants. The objective of this article is to describe our technique for transcatheter PDA closure (TCPC) in ELBW infants.

Design: The techniques employed are very specific to this population and are drastically different when compared to the procedure performed in patients weighing >5 kg. Read More

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http://dx.doi.org/10.1111/chd.12700DOI Listing
January 2019
1 Read

Stenting of the ductus arteriosus for ductal-dependent pulmonary blood flow-current techniques and procedural considerations.

Congenit Heart Dis 2019 Jan;14(1):110-115

The Lillie Frank Abercrombie Section of Cardiology, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas.

The use of prostaglandin-E1 immediately after birth and subsequent surgical creation of the modified Blalock-Taussig shunt (BTS) shunt have remarkably improved the prognosis and survival of children with congenital heart disease and ductal-dependent pulmonary blood flow (PBF). Despite the advancement in surgical techniques, bypass strategies, and postoperative management, significant morbidity and mortality after BTS still remain. Patent ductus arteriosus stenting has been shown to be as an acceptable alternative to BTS placement in select infants with ductal-dependent PBF. Read More

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http://doi.wiley.com/10.1111/chd.12709
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http://dx.doi.org/10.1111/chd.12709DOI Listing
January 2019
5 Reads

A comprehensive program for preterm infants with patent ductus arteriosus.

Congenit Heart Dis 2019 Jan;14(1):90-94

Department of Pediatric Cardiology, University of Tennessee Health Science Center, LeBonheur Children's Hospital, Memphis, Tennessee.

Objectives: Patent ductus arteriosus (PDA) is a common finding in preterm infants. A hemodynamically significant PDA may require intervention for closure. This article aims to describe a transcatheter PDA closure (TCPC) program for preterm infants and the components of a comprehensive outpatient follow-up strategy. Read More

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http://dx.doi.org/10.1111/chd.12705DOI Listing
January 2019
1 Read

Overview of transcatheter patent ductus arteriosus closure in preterm infants.

Congenit Heart Dis 2019 Jan;14(1):60-64

Guerin Family Congenital Heart Program, Smidt Heart Institute, Los Angeles, California.

Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeutic options have their advantages and limitations. Read More

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http://dx.doi.org/10.1111/chd.12712DOI Listing
January 2019
1 Read

Effect of patent ductus arteriosus on the heart in preterm infants.

Congenit Heart Dis 2019 Jan;14(1):33-36

Division of Pediatric Cardiology, University of Tennessee Health Science Center, Le Bonheur Children's Hospital, Memphis, Tennessee.

There continues to be controversy on the long-term effects of a patent ductus arteriosus (PDA) and its management. However, the hemodynamic effects of a large PDA in a preterm infant are well known. This article aims to provide insight into the adaptive changes and remodeling effects of a PDA on the myocardium in preterm infants. Read More

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http://dx.doi.org/10.1111/chd.12701DOI Listing
January 2019
3 Reads

Transport of extremely low birth weight neonates for persistent ductus arteriosus closure in the catheterization lab.

Congenit Heart Dis 2019 Jan;14(1):69-73

LeBonheur Children's Hospital, Memphis, Tennessee.

Objective: The objective of this article is to describe the elements involved with transporting extremely low birth weight (ELBW) infants from referring centers to our center's neonatal intensive care unit (NICU) and then from the NICU to the catheterization lab for transcatheter closure of patent ductus arteriosus (PDA).

Setting: Several referring centers are over 300 miles away. ELBW infants are transferred in to our NICU safely for the procedure and transferred back following the procedure. Read More

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http://dx.doi.org/10.1111/chd.12706DOI Listing
January 2019
1 Read

Effect of patent ductus arteriosus on pulmonary vascular disease.

Congenit Heart Dis 2019 Jan;14(1):37-41

Division of Pediatric Cardiology, University of Tennessee Health Science Center, Le Bonheur Children's Hospital, Memphis, Tennessee.

The hemodynamic effects of a patent ductus arteriosus (PDA) are well known including systemic hypoperfusion and volume overload on the left ventricle. This article aims to provide a review of the long-standing effect of a hemodynamically significant PDA on the pulmonary vasculature and the role of cardiac catheterization in preterm infants with a PDA and pulmonary hypertension. Read More

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http://dx.doi.org/10.1111/chd.12702DOI Listing
January 2019
2 Reads

Fate of the Fontan connection: Mechanisms of stenosis and management.

Congenit Heart Dis 2019 Feb 25. Epub 2019 Feb 25.

Division of Pediatric Cardiology, Department of Pediatric and Adolescent Medicine, Mayo Clinic College of Medicine, Rochester, Minnesota.

Background: Stenosis of the venous connections and conduits is a well-known late complication of the Fontan procedure. Currently, data on the outcomes of percutaneous intervention for the treatment of extra- or intracardiac conduits and lateral tunnel baffles obstruction are limited. In an attempt to better define the nature and severity of the stenosis and the results of catheter interventional management, we reviewed Fontan patients with obstructed extra- or intracardiac conduits and lateral tunnel baffles. Read More

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http://dx.doi.org/10.1111/chd.12757DOI Listing
February 2019
2 Reads

Contemporary outcomes and mortality risks of Ebstein anomaly: A single-center experience in Thailand.

Congenit Heart Dis 2019 Feb 21. Epub 2019 Feb 21.

Department of Pediatrics, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Background: The increasing number of patients with Ebstein anomaly (EA) surviving into adulthood implies improvements in the treatments for the complex lesion. We revisited the clinical outcomes of patients with EA to demonstrate their "real world" survival.

Objectives: To identify the survival and predictors of mortality in patients with EA who underwent medical or surgical management in the present era. Read More

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http://dx.doi.org/10.1111/chd.12759DOI Listing
February 2019
1 Read

Accuracy of risk prediction scores in pregnant women with congenital heart disease.

Congenit Heart Dis 2019 Feb 6. Epub 2019 Feb 6.

Maternal and Child Health Research Center, Department of Obstetrics and Gynecology, University of Pennsylvania Perelman School of Medicine Philadelphia, Pennsylvania.

Objective: To assess performance of risk stratification schemes in predicting adverse cardiac outcomes in pregnant women with congenital heart disease (CHD) and to compare these schemes to clinical factors alone.

Design: Single-center retrospective study.

Setting: Tertiary care academic hospital. Read More

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http://dx.doi.org/10.1111/chd.12750DOI Listing
February 2019
5 Reads

Strategy of treating secundum atrial septal defect not referred to percutaneous closure.

Congenit Heart Dis 2019 Feb 4. Epub 2019 Feb 4.

Department of Cardiovascular Surgery, the Second Xiangya Hospital, Central South University, Changsha, P.R. China.

Objective: To evaluate safety and effectiveness of intraoperative device closure for secundum atrial septal defect (ASD) not referred to percutaneous closure.

Design And Patients: From April 2010 to December 2018, 231 secundum ASD children (≤14 years) directly recommended to surgical repair were enrolled in this study. These patients were divided into two groups according to the parents' choice based on surgeons' recommendation. Read More

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http://dx.doi.org/10.1111/chd.12753DOI Listing
February 2019
3 Reads

Education as important predictor for successful employment in adults with congenital heart disease worldwide.

Congenit Heart Dis 2019 Feb 4. Epub 2019 Feb 4.

Amsterdam UMC, Department of Cardiology, University of Amsterdam, Amsterdam, The Netherlands.

Background: Conflicting results have been reported regarding employment status and work ability in adults with congenital heart disease (CHD). Since this is an important determinant for quality of life, we assessed this in a large international adult CHD cohort.

Methods: Data from 4028 adults with CHD (53% women) from 15 different countries were collected by a uniform survey in the cross-sectional APPROACH International Study. Read More

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http://dx.doi.org/10.1111/chd.12747DOI Listing
February 2019
4 Reads

Two-year evolution of latent rheumatic heart disease in Malawi.

Congenit Heart Dis 2019 Jan 31. Epub 2019 Jan 31.

Department of Pediatrics, Baylor College of Medicine Clinical Center of Excellence, Lilongwe, Malawi.

Background: In asymptomatic children, screening echocardiography has been used to attempt to diagnose rheumatic heart disease (RHD) at an early stage (latent RHD). World Heart Federation guidelines have standardized categorization of "definite," "borderline," or no RHD by echo findings. The progression of RHD diagnosed through echo screening is not known. Read More

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http://dx.doi.org/10.1111/chd.12756DOI Listing
January 2019
2 Reads

Obesity trends in children, adolescents, and young adults with congenital heart disease.

Congenit Heart Dis 2019 Jan 30. Epub 2019 Jan 30.

Cleveland Clinic Children's, Cleveland, Ohio.

Objectives: To determine the prevalence, age of onset, and risk factors for overweight and obesity in children with congenital heart disease (CHD).

Study Design: Children with CHD who were seen at our institution from 1996 to 2017 were studied. Patients were full-time residents of the United States and were receiving all cardiac care at our institution. Read More

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http://doi.wiley.com/10.1111/chd.12754
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http://dx.doi.org/10.1111/chd.12754DOI Listing
January 2019
19 Reads

Systolic/diastolic ratio correlates with end diastolic pressures in pediatric patients with single right ventricles.

Congenit Heart Dis 2019 Jan 30. Epub 2019 Jan 30.

Pediatric Cardiology, Lucille Packard Children's Hospital, Palo Alto, California.

Background: Increased ventricular end-diastolic pressure (VEDP) is a known risk factor for morbidity and mortality in patients with single right ventricle (RV) physiology. Previous studies have shown mixed results correlating echocardiographic measurements with catheter-derived VEDP in this population. Goal of this study was to evaluate if echocardiographic systolic/diastolic ratio (S/D) correlated with VEDP. Read More

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http://dx.doi.org/10.1111/chd.12755DOI Listing
January 2019

Opportunities for training to advance the care for adults with congenital heart disease with advanced circulatory failure.

Congenit Heart Dis 2019 Jan 25. Epub 2019 Jan 25.

Department of Pediatrics, Section of Pediatric and Adult Congenital Cardiology, Texas Children's Hospital, Baylor College of Medicine, Houston, Texas.

Heart failure is an emerging issue with important implications in adult patients with congenital heart disease. Practitioners with expertise in both adult congenital heart disease and heart failure are needed to manage this growing and often complex population. In the United States, the optimal training pathway to enable practitioners to best care for these patients is ill-defined. Read More

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http://dx.doi.org/10.1111/chd.12748DOI Listing
January 2019

Safety of contraceptive use among women with congenital heart disease: A systematic review.

Congenit Heart Dis 2019 Jan 25. Epub 2019 Jan 25.

Division of Congenital and Developmental Disorders, National Center on Birth Defects and Developmental Disabilities, Centers for Disease Control and Prevention, Atlanta, Georgia.

Objective: Women with congenital heart disease (CHD) are at increased risk of pregnancy complications and need information on safe, effective contraceptive methods to avoid unintended pregnancy. This systematic review examines evidence regarding safety of contraceptive use among women with CHD.

Methods: The PubMed database was searched for any peer-reviewed articles published through April 2018 that included safety outcomes associated with reversible contraceptive methods among women with CHD. Read More

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http://dx.doi.org/10.1111/chd.12752DOI Listing
January 2019
2 Reads

Body mass index in adults with congenital heart disease.

Congenit Heart Dis 2019 Jan 25. Epub 2019 Jan 25.

Department of Pediatric Cardiology, Ghent University Hospital, Ghent, Belgium.

Objective: To investigate the status of body mass index (BMI) in adult people with congenital heart disease (ACHD).

Methods: Five hundred thirty-nine adults with CHD (53.8% men) were seen in the outpatient clinic from 2013 to 2015 and compared to a reference population (n = 1737). Read More

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http://dx.doi.org/10.1111/chd.12751DOI Listing
January 2019
3 Reads

A better approach for left ventricular training in transposition of the great arteries and intact interventricular septum: Bidirectional cavopulmonary anastomosis and pulmonary artery banding.

Congenit Heart Dis 2019 Jan 25. Epub 2019 Jan 25.

Department of Pediatric Cardiology, Florence Nightingale Hospital, Istanbul, Turkey.

Objective: Management of the patients with transposition of the great arteries and intact ventricular septum may be challenging beyond the newborn period. Herein, we would like to present our alternative strategy for training the left ventricle in these patients.

Methods: Six patients with transposition of the great arteries and intact ventricular septum were evaluated in our clinic. Read More

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http://dx.doi.org/10.1111/chd.12749DOI Listing
January 2019

Creatinine-based estimation of glomerular filtration rate in patients with a Fontan circulation.

Congenit Heart Dis 2019 Jan 21. Epub 2019 Jan 21.

Heart Research Group, Murdoch Childrens Research Institute, Melbourne, Victoria, Australia.

Background: Patients with a Fontan circulation are at risk of renal dysfunction. We analyzed cross-sectional data in pediatric and adult Fontan patients in order to assess the accuracy of commonly used serum creatinine-based methods in estimating glomerular filtration rate (GFR).

Methods: A total of 124 Fontan patients (58 children, 66 adults) were enrolled across three study centers. Read More

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http://dx.doi.org/10.1111/chd.12746DOI Listing
January 2019
9 Reads

Circulating biomarkers of left ventricular hypertrophy in pediatric coarctation of the aorta.

Congenit Heart Dis 2019 Jan 16. Epub 2019 Jan 16.

Division of Cardiology, Department of Pediatrics, University of Colorado Denver, Aurora, Colorado.

Objective: Patients undergoing surgical repair of aortic coarctation have a 50% risk of pathologic left ventricular remodeling (increased left ventricular mass or relative wall thickness). Endothelin 1, ST2, galectin 3, norepinephrine and B-natriuretic peptide are biomarkers that have been associated with pathologic LV change in adult populations but their predictive value following pediatric coarctation repair are not known.

Hypothesis: Biomarker levels at coarctation repair will predict persistent left ventricular remodeling at 1-year follow up. Read More

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http://doi.wiley.com/10.1111/chd.12744
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http://dx.doi.org/10.1111/chd.12744DOI Listing
January 2019
14 Reads

Feeding methods for infants with single ventricle physiology are associated with length of stay during stage 2 surgery hospitalization.

Congenit Heart Dis 2019 Jan 12. Epub 2019 Jan 12.

Department of Pediatrics, Otolaryngology, Physical Medicine and Rehabilitation, Johns Hopkins University School of Medicine, Baltimore, Maryland.

Background: Tube feedings are often needed to achieve the growth and nutrition goals associated with decreased morbidity and mortality in patients with single ventricle anatomy. Variability in feeding method through the interstage period has been previously described, however, comparable information following stage 2 palliation is lacking.

Objectives: To identify types of feeding methods following stage 2 palliation and their influence on length of stay. Read More

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http://doi.wiley.com/10.1111/chd.12742
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http://dx.doi.org/10.1111/chd.12742DOI Listing
January 2019
26 Reads

Pulmonary artery interventions after the arterial switch operation: Unique and significant risks.

Congenit Heart Dis 2019 Mar 8;14(2):288-296. Epub 2019 Jan 8.

Department of Pediatric Cardiology, Rady Children's Hospital, University of California San Diego, San Diego, California.

Background: In the modern era, results of the arterial switch operation (ASO) for transposition of the great arteries are excellent. However, because of the LeCompte maneuver, there may be a propensity for development of pulmonary artery stenosis. We encountered atypical complications of pulmonary artery stenting in patients after the ASO, including aorto-pulmonary fistula and coronary compression. Read More

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http://dx.doi.org/10.1111/chd.12726DOI Listing
March 2019
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Extended cardiac ambulatory rhythm monitoring in adults with congenital heart disease: Arrhythmia detection and impact of extended monitoring.

Congenit Heart Dis 2019 Jan 3. Epub 2019 Jan 3.

Department of Pediatrics, Division of Cardiology, Stanford University School of Medicine, Lucile Packard Children's Hospital, Stanford, California.

Background: Arrhythmias are a leading cause of death in adults with congenital heart disease (ACHD). While 24-48-hour monitors are often used to assess arrhythmia burden, extended continuous ambulatory rhythm monitors (ECAM) can record 2 weeks of data. The utility of this device and the arrhythmia burden identified beyond 48-hour monitoring have not been evaluated in the ACHD population. Read More

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http://dx.doi.org/10.1111/chd.12736DOI Listing
January 2019
2 Reads