1,279 results match your criteria Congenital Cystic Adenomatoid Malformation


Thoracoscopic lobectomy for a 4-day-old neonate with a large congenital pulmonary airway malformation: a case report.

J Cardiothorac Surg 2020 Jul 1;15(1):159. Epub 2020 Jul 1.

Department of Cadiothoracic Surgery, Fujian Children's Hospital, 18 daoshan Road, Fuzhou City, Fujian Province, China.

Background: Congenital pulmonary airway malformation is a rare congenital lung lesion. Infants with large Congenital pulmonary airway malformation can present with a series of serious symptoms. Surgery is still the main treatment. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1186/s13019-020-01174-3DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7331191PMC
July 2020
1.018 Impact Factor

Two's Company: Multiple Thoracic Lesions on Prenatal US and MRI.

Fetal Diagn Ther 2020 Jun 29:1-11. Epub 2020 Jun 29.

Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, USA.

Background: Congenital pulmonary airway malformations (CPAM), bronchopulmonary sequestrations (BPS), and CPAM-BPS hybrid lesions are most commonly solitary; however, >1 lung congenital lung lesion may occur.

Objectives: To assess the frequency of multiple congenital thoracic anomalies at a high-volume referral center; determine prenatal ultrasound (US) and magnetic resonance imaging (MRI) features of these multifocal congenital lung lesions that may allow prenatal detection; and determine the most common distribution or site of origin.

Methods: Database searches were performed from August 2008 to May 2019 for prenatally evaluated cases that had a final postnatal surgical diagnosis of >1 congenital lung lesion or a lung lesion associated with foregut duplication cyst (FDC). Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1159/000507783DOI Listing

Neonatal pulmonary sequestration (PS) with rhabdomyomas-like hyperplasia: A case report.

Medicine (Baltimore) 2020 May;99(20):e20052

Children's Hospital of Capital Medical University, Beijing, China.

Introduction: Pulmonary sequestration (PS) is a rare pulmonary congenital malformation characterized by disconnection with the tracheobronchial tree or the pulmonary arterial blood supply thus impeding the connection to the arterial blood supply from systemic circulation, ultimately resulting in a non-functional lung.

Patient Concerns: A 73-day-old boy with rhabdomyomatoid hyperplasia was hospitalized for cough and fever 2 months after birth.

Diagnoses: Routine B-ultrasound revealed a cystic malformation in the right lung. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1097/MD.0000000000020052DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7313550PMC

Comparison of the Prognostic Factors of Fetuses With Congenital Pulmonary Airway Malformations According to Type.

J Ultrasound Med 2020 May 18. Epub 2020 May 18.

Departments of Obstetrics and Gynecology, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea.

Objectives: To compare the prognostic factors of fetuses with microcystic and macrocystic congenital pulmonary airway malformations (CPAMs).

Methods: We retrospectively evaluated fetuses with CPAMs at Asan Medical Center. The CPAM size, mass effect, and maximum cyst size in macrocystic CPAMs were evaluated prenatally. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/jum.15335DOI Listing

Perinatal Outcomes in Fetuses Prenatally Diagnosed with Congenital Diaphragmatic Hernia and Concomitant Lung Lesions: A 10-Year Review.

Fetal Diagn Ther 2020 May 7:1-6. Epub 2020 May 7.

Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, USA.

Aim: To describe perinatal outcomes of fetuses with a prenatal diagnosis of a concomitant lung lesion in the setting of congenital diaphragmatic hernia (CDH) and to compare outcomes with an isolated CDH control group without a lung lesion, matched by ultrasound-based prognostic markers including presence of liver herniation and lung measurements.

Material And Methods: This was a retrospective case-control study, wherein all pregnancies diagnosed with CDH and concomitant lung lesions were identified between July 1, 2008, and December 31, 2018. For each case, 2 controls with isolated CDH from the same study period were selected after matching for the presence of liver herniation into the thoracic cavity and ultrasound-based lung measurements either observed over expected lung-to-head ratio (LHR) or absolute LHR with their corresponding gestational age. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1159/000507481DOI Listing

Thoracoscopic Resection in the Treatment of Spontaneous Pneumothorax.

Sisli Etfal Hastan Tip Bul 2020 25;54(1):94-97. Epub 2020 Mar 25.

Department of Pediatric Surgery, Sisli Hamidiye Etfal Training and Research Hospital, Istanbul, Turkey.

Objectives: We retrospectively evaluated the patients with primer spontaneous pneumothorax (PSP) who were treated with thoracoscopic resection.

Methods: We retrospectively collected the data of the patients with a spontaneous pneumothorax who were operated with video-assisted thoracoscopic surgery (VATS) between 2010 and 2016.

Results: During the study period, 10 patients applied to our hospital with spontaneous pneumothorax. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.14744/SEMB.2018.88310DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7192249PMC

Surgical treatment of pulmonary sequestration in adults and children: long-term results.

Interact Cardiovasc Thorac Surg 2020 Jul;31(1):71-77

Department of Thoracic Surgery, Sant'Andrea Hospital, Sapienza University, Rome, Italy.

Objectives: Few experiences comparing paediatric and adult patients treated for pulmonary sequestration (PS) have been reported. Surgical treatment is considered the best choice, but the time of surgery is still controversial. We present our experience in this setting, comparing characteristics, histological results and outcome of paediatric and adult patients undergoing PS resection. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1093/icvts/ivaa054DOI Listing

Computed tomography features can distinguish type 4 congenital pulmonary airway malformation from other cystic congenital pulmonary airway malformations.

Eur J Radiol 2020 May 19;126:108964. Epub 2020 Mar 19.

Department of Radiology, Guangzhou Women and Children's Medical Center, Guangzhou Medical University, Guangzhou 510623, China.

Purpose: We aimed to identify clinical and computed tomography (CT) features that distinguish among cystic congenital pulmonary airway malformations (CPAMs) and offer new management strategies.

Methods: We retrieved data on 145 children (85 male, 60 female; median age, 14 months) with pathologically confirmed cystic CPAMs from 2008 to 2018 and retrospectively analyzed the clinical and CT characteristics.

Results: Of the 145 patients, 54 had type 1, 72 had type 2, and 19 had type 4 cystic CPAMs. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.ejrad.2020.108964DOI Listing

Variability of presentation and surgical approach in Congenital Cystic Lesions of Lung: A retrospective study in children presenting in Mayo Hospital.

J Pak Med Assoc 2019 Jul;69(7):1035-1038

Department of Plastic surgery, King Edward medical university, Lahore.

The objective was to study the clinical presentation and surgical outcome in children with congenital cystic lesions of the lung. The medical records of 11 patients operated in the department of paediatric surgery, from January 2014 to December 2017, were evaluated retrospectively. Median age was 18 months (1-108). Read More

View Article

Download full-text PDF

Source

[Clinical analysis of 96 cases of congenital cystic lung lesions in children].

Zhonghua Er Ke Za Zhi 2020 Jan;58(1):19-24

Department of Pathology, Tianjin Children's Hospital, Tianjin 300134, China.

To summarize the diagnosis, clinical manifestations, treatment and prognosis of congenital cystic lung lesions. A retrospective study described the clinical course of 96 patients (46 female and 50 male) diagnosed with congenital cystic lung lesions treated at the Tianjin Children's Hospital from January 2010 to March 2019. The clinical findings, imaging examinations, pathological findings, treatment and follow-up were analyzed. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.3760/cma.j.issn.0578-1310.2020.01.006DOI Listing
January 2020

Fetal mediastinal teratoma: Misinterpretation as congenital cystic lesions of the lung on prenatal ultrasound.

J Clin Ultrasound 2020 Jun 20;48(5):287-290. Epub 2019 Dec 20.

University of Tunis El Manar, Tunis, Tunisia.

Congenital mediastinal teratoma can lead to development of hydrops fetalis and may be misinterpreted on ultrasound. In this case report, ultrasound revealed severe fetoplacental hydrops, moderate posthemorrhagic hydrocephalus, and multiple pulmonary cysts suggesting cystic adenomatoid malformation and displacement of the heart to the left side. Autopsy of the hydropic 24-weeks male fetus showed a large cystic-solid mediastinal mass that was consistent with nonmetastatic immature teratoma. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/jcu.22808DOI Listing

Congenital Cystic Adenomatoid Malformation of the Lung Tipe II: Three Cases Report.

Transl Med UniSa 2019 Jul-Dec;20:4-8. Epub 2019 Jan 12.

Department of Advanced Biomedical Sciences, Pathology Unit, University of Naples Federico II.

Congenital cystic adenomatoid malformation (CCAM) is a rare congenital lung lesion. It may appear since birth (30-35%) with difficulty breathing or may have a late onset (60-65%) with recurring pulmonary infections or growth failure; in a small percentage of cases, the lesion can be completely asymptomatic. Fetal or post-natal surgery can be used as surgical treatment of these lesions. Read More

View Article

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6910145PMC
January 2019

Outcomes of Cases of Prenatally-Diagnosed Congenital Pulmonary Airway Malformation.

Rev Bras Ginecol Obstet 2019 Nov 19;41(11):654-659. Epub 2019 Nov 19.

Division of Neonatology, Department of Pediatrics, Hacettepe University, Ankara, Turkey.

Objective:  To evaluate the outcomes of cases of prenatally-diagnosed congenital pulmonary airway malformation (CPAM).

Methods:  We retrospectively evaluated cases of prenatally-diagnosed CPAM between 2004 and 2018. Ultrasonographic features such as visualization of a fetal lung mass and heterogeneous pulmonary parenchyma were used for CPAM diagnosis. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1055/s-0039-1697983DOI Listing
November 2019

Congenital pulmonary airway malformation: A case report of a rare cause of neonatal respiratory distress and review of the literature.

Niger J Clin Pract 2019 Nov;22(11):1621-1625

Department of Surgery, Lagos State University College of Medicine, Ikeja, Lagos, Nigeria.

Congenital pulmonary airway malformation (CPAM), formerly known as congenital cystic adenomatoid malformation (CCAM), is a rare developmental dysplastic lesion of the fetal tracheobronchial tree. CPAM is a rare cause of neonatal respiratory distress; however, its presence may span fetal to adult period. In two previous case-reports from Nigeria, CPAM was present in post-neonatal infants. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.4103/njcp.njcp_20_19DOI Listing
November 2019

Bronchopulmonary and vascular anomalies are frequent in children with oesophageal atresia.

Acta Paediatr 2020 Jun 11;109(6):1221-1228. Epub 2019 Dec 11.

Pediatric Pulmonology and Allergy Department, Pole Enfant, Jeanne de Flandre Hospital, CHU Lille, Univ. Lille, Lille, France.

Aim: Oesophageal atresia is frequently associated with other malformations, and our aim was to use computed tomography (CT) to explore intrathoracic malformations in patients with this condition.

Method: This was retrospective study of children aged 0-16 with oesophageal atresia who were born in 1996-2013 and followed up at the French reference centre for rare oesophageal diseases at the University of Lille. Computed tomography scans were available for 48 of the 234 patients during follow-up visits, and these were reviewed by a thoracic radiologist. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/apa.15086DOI Listing

Type I pleuropulmonary blastoma presenting as congenital pulmonary airway malformation: A report of two cases.

Indian J Pathol Microbiol 2019 Oct-Dec;62(4):595-598

Department of Pathology, All India Institute of Medical Sciences, New Delhi, India.

Pleuropulmonary blastoma (PPB) is a rare aggressive intrathoracic tumor which is believed to originate from embryonic uncommitted lung mesenchymal cells, which are important for developing the lung. Type I PPB is cystic, type II is cystic and solid, while type III is predominantly solid. Diagnosing type 1 PPB is a challenge for both radiologists as well as pathologists. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.4103/IJPM.IJPM_713_18DOI Listing
February 2020
1 Read
0.642 Impact Factor

Prenatal diagnosis of submicroscopic chromosomal aberrations in fetuses with congenital cystic adenomatoid malformation by chromosomal microarray analysis.

J Matern Fetal Neonatal Med 2019 Oct 3:1-7. Epub 2019 Oct 3.

Department of Prenatal Diagnostic Center, Guangzhou Women and Children's Medical Center, Guangzhou Medical University , Guangdong , China.

To explore the copy number variations (CNVs) of fetal congenital cystic adenomatoid malformation (CCAM). Fetuses with CCAM were investigated by karyotypes and chromosomal microarray analysis (CMA). The cases were classified as isolated or CCAM with additional structural anomalies. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/14767058.2019.1670793DOI Listing
October 2019
1 Read

Congenital pulmonary airway malformation associated with mosaic Klinefelter syndrome.

J Clin Ultrasound 2020 Feb 30;48(2):121-124. Epub 2019 Sep 30.

Department of Obstetrics and Gynecology, West Virginia University, Charleston, West Virginia.

A 26-year-old female, G4 P2012 presented for an anatomy scan at 18 weeks. Multiple macrocysts were seen in the left fetal lung, which lead to a diagnosis of congenital pulmonary airway malformation (CPAM) type II. A fetal MRI examination performed at 24 weeks of gestation confirmed the diagnosis of CPAM type II. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/jcu.22777DOI Listing
February 2020
1 Read

Pneumomediastinum Mimicking Congenital Pulmonary Airway Malformation.

Authors:
Ranjit I Kylat

Children (Basel) 2019 Sep 17;6(9). Epub 2019 Sep 17.

Department of Pediatrics, College of Medicine, University of Arizona, PO BOX 245073, 1501 N Campbell Avenue, Tucson, AZ 85724, USA.

Pneumomediastinum is the collection of free air in the mediastinum. Its incidence is higher in preterm infants and those on positive airway pressure support or on mechanical ventilation. But it has decreased dramatically after the introduction of surfactant and synchronized, non-invasive mechanical ventilation. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.3390/children6090104DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6770375PMC
September 2019
1 Read

[Congenitial Pulmonary Airway Malformation in an Adult with Pneumonia].

Kyobu Geka 2019 Sep;72(9):664-667

Department of Thoracic Surgery, Shin Koga Hospital, Kurume, Japan.

Congenitial pulmonary airway malformation (CPAM) most commonly present respiratory distress in the prenatal or neonatal period, but may rarely be asymptomatic and is incidentally found in adult patients with acute or recurrent pneumonia. Herein, we report a case of a 26-year-old asymptomatic adult male patient with pneumonia of the right lower lobe. He was also found to have multiple cystic lesions in the same lobe which was suspected to be CPAM, and the right lower lobectomy was performed. Read More

View Article

Download full-text PDF

Source
September 2019
1 Read

Congenital lung lesions.

Semin Pediatr Surg 2019 Aug 18;28(4):150821. Epub 2019 Jul 18.

Fetal Treatment Center, Department of Surgery, University of California, San Francisco. Electronic address:

Diagnosis and management of congenital lung malformations has evolved dramatically over the past several decades. Advancement in imaging technology has enabled earlier, more definitive diagnoses and, consequently, more timely intervention in utero or after birth, when indicated. These advancements have increased overall survival rates to around 95% from historical rates of 60%. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1053/j.sempedsurg.2019.07.004DOI Listing
August 2019
2 Reads

Angeborene Lungenerkrankungen – welche Diagnostik ist wann sinnvoll?

Rofo 2019 Sep 20;191(S 02):S119-S121. Epub 2019 Aug 20.

Universitätsklinikum Jena, Sektion Pädiatrische Radiologie, Institut für Diagnostische und Interventionelle Radiologie.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1055/a-0943-1293DOI Listing
September 2019

Pränatale sonografische Diagnostik von Lungenfehlbildungen.

Authors:
Michael Bolz

Rofo 2019 Sep 20;191(S 02):S106-S109. Epub 2019 Aug 20.

Universitätsfrauenklinik und Poliklinik Rostock.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1055/a-0943-1068DOI Listing
September 2019

Whole exome sequencing to uncover genetic variants underlying congenital cystic adenomatoid malformations.

Authors:
P K Tam

Hong Kong Med J 2019 08;25 Suppl 5(4):36-38

Department of Surgery, The University of Hong Kong.

View Article

Download full-text PDF

Source

Current Management of Pleuropulmonary Blastoma: A Surgical Perspective.

Children (Basel) 2019 Jul 25;6(8). Epub 2019 Jul 25.

Department of Surgery, St. Jude Children's Research Hospital, Memphis, TN 38105, USA.

Pleuropulmonary blastomas (PPB) are pediatric, embryonal cancers of the lung parenchyma and pleural surfaces and are among the most common DICER1-related disorders. These tumors undergo evolution through several forms, allowing division into types I, Ir, II, and III, with correlates to the age of diagnosis and prognosis. We sought to provide a comprehensive review of the relevant literature describing the characteristics of these tumors and their multidisciplinary treatment, with an emphasis on surgical management. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.3390/children6080086DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6721434PMC

Congenital Cystic Adenomatoid Malformation Volume Ratio in Prenatal Assessment of Prognosis of Fetal Pulmonary Sequestrations.

Curr Med Sci 2019 Aug 25;39(4):658-662. Epub 2019 Jul 25.

Department of Medical Imaging, Xiangyang No. 1 People's Hospital Affiliated to Hubei University of Medicine, Xiangyang, 441000, China.

This study aimed to evaluate the prognosis of pulmonary sequestration (PS) by measuring congenital cystic adenomatoid malformation volume ratio (CVR) value in fetal congenital PS. The fetal CVR in 49 cases of fetal PS diagnosed by prenatal ultrasound in Xiangyang No. 1 People's Hospital from March 2010 to June 2017 were measured, and the clinical outcomes were observed. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s11596-019-2088-1DOI Listing
August 2019
3 Reads

 A Young Adult with Tracheal Bronchus and Congenital Cystic Adenomatoid Malformation.

J Assoc Physicians India 2019 Apr;67(4):74-75

Professor, Department of Pulmonary Medicine, Government Medical College and Hospital, Chandigarh.

View Article

Download full-text PDF

Source
April 2019
6 Reads

Invasive mucinous adenocarcinoma of the lung arising in a type 1 congenital pulmonary airway malformation in a 68-year-old patient: a case report.

Acta Chir Belg 2019 Jul 2:1-6. Epub 2019 Jul 2.

a Department of Thoracic Surgery , University Hospitals Leuven , Leuven , Belgium.

Congenital pulmonary airway malformation (CPAM), previously described as congenital cystic adenomatoid malformation (CCAM), is a congenital disorder of lung parenchyma. The association with the presence of a malignant transformation like rhabdomyosarcoma, pleuropulmonary blastoma, and most common invasive mucinous adenocarcinoma (IMA) is a rare development described in patients with CPAM. Here, we report the case of a 68-year-old male patient who underwent a right lower lobectomy for a mass in the right pulmonary lobe. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/00015458.2019.1634926DOI Listing
July 2019
5 Reads

Congenital Lung Malformations: Unresolved Issues and Unanswered Questions.

Front Pediatr 2019 13;7:239. Epub 2019 Jun 13.

Division of Paediatrics, Department of Translational Medical Sciences, Federico II University, Naples, Italy.

Advances in prenatal and postnatal diagnosis, perioperative management, and postoperative care have dramatically increased the number of scientific reports on congenital thoracic malformations (CTM). Nearly all CTM are detected prior to birth, generally by antenatal ultrasound. After delivery, most infants do well and remain asymptomatic for a long time. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.3389/fped.2019.00239DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6584787PMC
June 2019
8 Reads

Adenocarcinoma in situ in type I congenital pulmonary airway malformation.

Asian Cardiovasc Thorac Ann 2019 Sep 21;27(7):606-608. Epub 2019 Jun 21.

2 Apollo Hospitals, Chennai, India.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1177/0218492319860346DOI Listing
September 2019
18 Reads

[EXIT: Experiences from Karolinska University Hopsital].

Lakartidningen 2019 May 15;116. Epub 2019 May 15.

Karolinska Universitetssjukhuset - Centrum för Fostermedicin Stockholm, Sweden Karolinska Universitetssjukhuset - Centrum för Fostermedicin Stockholm, Sweden.

The main, but not sole, indication for an Ex-utero Intrapartum Treatment (EXIT) delivery is an airway obstruction due to either laryngeal atresia or tumors in the head and neck region. Here we present our Institution's experience with eleven cases: three teratomas, four lymphatic malformations, two laryngeal atresias and two dermoid cysts. The EXIT procedure was used to secure the fetal airway while maintaining uteroplacental gas exchange and fetal hemodynamic stability through the umbilical circulation. Read More

View Article

Download full-text PDF

Source
May 2019
9 Reads

Establishment of a biobank for human lung tissues of congenital diaphragmatic hernia and congenital pulmonary airway malformation.

J Pediatr Surg 2019 Nov 11;54(11):2439-2442. Epub 2019 May 11.

Department of Surgery, Division of Pediatric Surgery, University of Manitoba and Children's Hospital Research Institute of Manitoba, Biology of Breathing Theme, Winnipeg, Manitoba, Canada; Department of Pediatrics & Child Health and Physiology & Pathophysiology (Adjunct), University of Manitoba and Children's Hospital Research Institute of Manitoba, Biology of Breathing Theme, Winnipeg, Manitoba, Canada. Electronic address:

Background: Human tissue samples are an invaluable and little available source of information for translational studies of congenital lung diseases such as Congenital Diaphragmatic Hernia (CDH) or Congenital Pulmonary Airway Malformation (CPAM).

Purpose: We aimed to establish a human lung tissue biobank of CDH and CPAM patients together with age-matched controls, coupled with a clinical database.

Methods: Pathology records from autopsies or surgical specimens for CDH and CPAM cases between 1980 and 2017 were reviewed. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpedsurg.2019.05.003DOI Listing
November 2019
4 Reads

A rare disease; congenital pulmonary airway malformation in an adult.

Tuberk Toraks 2019 Mar;67(1):71-76

Department of Chest Diseases, Faculty of Medicine, Recep Tayyip Erdogan University, Rize, Turkey.

Congenital pulmonary airway malformation (CPAM), is a rare disease known as a developmental abnormality of the lower respiratory tract. It may occur in the neonatal period due to respiratory distress and patients usually die in the first few months of life. Rarely, it may remain asymptomatic until adulthood. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.5578/tt.68095DOI Listing
March 2019
11 Reads

Congenital Pulmonary Airway Malformation - 19-Year Experience from a Tertiary Care Center in India.

Fetal Pediatr Pathol 2019 Dec 14;38(6):449-459. Epub 2019 May 14.

Kasturba Medical College Mangalore, Manipal Academy of Higher Education, Manipal, Karnataka, India.

: Congenital pulmonary airway malformation (CPAM) is a collection of non-hereditary, developmental anomalies. Our aim was to analyze the histological profiles and prevalence of CPAMs diagnosed in our center. : A retrospective study of all CPAMs diagnosed from January 1999 to May 2018 from a general hospital pathology service was performed. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/15513815.2019.1613703DOI Listing
December 2019
2 Reads

A Missed Late Presentation of a Congenital Pulmonary Airway Malformation as a Large Infected .

Sultan Qaboos Univ Med J 2018 Nov 28;18(4):e541-e544. Epub 2019 Mar 28.

Department of Radiology, Hospital Tengku Ampuan Rahimah, Klang, Malaysia.

A congenital pulmonary airway malformation (CPAM) is a rare cystic anomaly that may occur during development of the fetal airways. The vast majority of CPAMs are detected in neonates; as such, it is unusual for diagnosis to occur in adulthood. We report a 21-year-old male patient who presented to the emergency department of the Hospital Ampang, Kuala Lumpur, Malaysia, in 2015 with chest pain, breathlessness and tachypnoea. Read More

View Article

Download full-text PDF

Source
https://journals.squ.edu.om/index.php/squmj/article/view/300
Publisher Site
http://dx.doi.org/10.18295/squmj.2018.18.04.020DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6443284PMC
November 2018
30 Reads

Lung protective ventilation during pulmonary resection in children: a prospective, single-centre, randomised controlled trial.

Br J Anaesth 2019 May 8;122(5):692-701. Epub 2019 Mar 8.

Department of Anaesthesiology and Pain Medicine, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Republic of Korea. Electronic address:

Background: Perioperative ventilatory strategies for lung protection in children are underexplored. This study evaluated the effects of lung protective ventilation (LPV) on postoperative clinical outcomes in children requiring one-lung ventilation (OLV) for pulmonary resection.

Methods: Children age ≤5 yr scheduled for video-assisted thoracoscopic lung lobectomy or segmentectomy were randomly assigned to LPV or control ventilation. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.bja.2019.02.013DOI Listing
May 2019
5 Reads

Pulmonary Infantile Hemangioma Mimicking a Congenital Cystic Adenomatoid Malformation.

Pediatr Dev Pathol 2019 Oct 26;22(5):480-485. Epub 2019 Mar 26.

Department of Pathology, Hôpital Femme Mère Enfant, CHU de Lyon, Bron, France.

Infantile hemangioma (IH) is the most common benign vascular tumor of infancy, occurring predominantly in the head and neck. It is characterized by specific endothelial expression of glucose transporter-1 (GLUT-1) and involution with time, spontaneous or on beta-blockers treatment. Although some predisposing factors are known, the exact pathogenesis remains unclear. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1177/1093526619838743DOI Listing
October 2019
6 Reads

Development of a multi-institutional registry for children with operative congenital lung malformations.

J Pediatr Surg 2019 Feb 28. Epub 2019 Feb 28.

Section of Pediatric Surgery, Department of Surgery, University of Michigan and Michigan Medicine, C.S. Mott Children's and Von Voigtlander Women's Hospital, Ann Arbor, MI, USA.

Introduction: The purpose of this study was to develop a multi-institutional registry to characterize the demographics, management, and outcomes of a contemporary cohort of children undergoing congenital lung malformation (CLM) resection.

Methods: After central reliance IRB approval, a web-based, secure database was created to capture retrospective cohort data on pathologically-confirmed CLMs performed between 2009 and 2015 within a multi-institutional research collaborative.

Results: Eleven children's hospitals contributed 506 patients. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpedsurg.2019.01.058DOI Listing
February 2019
16 Reads

Postnatally presented and spontaneously resolved congenital pulmonary airway malformation in a preterm baby.

BMJ Case Rep 2019 Mar 15;12(3). Epub 2019 Mar 15.

Paediatric Surgery, Mediclinic City Hospital, Dubai, United Arab Emirates.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1136/bcr-2019-229746DOI Listing

Microbial Evidence in Congenital Pulmonary Airway Malformations of Young Asymptomatic Infants.

J Laparoendosc Adv Surg Tech A 2019 May 13;29(5):685-687. Epub 2019 Mar 13.

Department of Pediatric and Adolescent Surgery, Medical University of Graz, Graz, Austria.

Experts of pediatric endosurgery recommend early thoracoscopic resection of congenital pulmonary airway malformations (CPAM) even in asymptomatic infants due to the risk of later infections. However, neither the rate of lower airway inflammation nor the underlying microbes and their pathogenic potential have been revealed in CPAMs yet. Using latest gene-sequencing techniques, we present the first study analyzing the pulmonary microbiome in young asymptomatic infants with CPAM. Read More

View Article

Download full-text PDF

Source
https://www.liebertpub.com/doi/10.1089/lap.2017.0456
Publisher Site
http://dx.doi.org/10.1089/lap.2017.0456DOI Listing
May 2019
12 Reads

Cervical accessory trachea with mediastinal cystic lung tissue.

Pediatr Int 2019 Mar 10;61(3):303-306. Epub 2019 Mar 10.

Department of Radiology, Kobe Children's Hospital, Kobe, Japan.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/ped.13767DOI Listing
March 2019
4 Reads

Short-term respiratory outcomes of neonates with symptomatic congenital lung malformations.

J Pediatr Surg 2019 Sep 24;54(9):1766-1770. Epub 2019 Feb 24.

Section of Pediatric Surgery, Department of Surgery, Michigan Medicine, C.S. Mott, Children's and Von Voigtlander Women's Hospital, Ann Arbor, MI, USA 48109. Electronic address:

Introduction: The purpose of this study was to evaluate short-term respiratory outcomes in neonates with symptomatic congenital lung malformations (CLM).

Methods: Consecutive newborns who underwent surgical resection of a CLM were retrospectively reviewed. Demographic, prenatal, and outcomes data were analyzed as appropriate (p < 0. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpedsurg.2019.01.056DOI Listing
September 2019
3 Reads

Manifestation of congenital pulmonary airway malformation in a 26-year-old adult, requiring surgery.

Interact Cardiovasc Thorac Surg 2019 07;29(1):154-156

Department of Thoracic Surgery, Kyoto University Hospital, Kyoto, Japan.

This is a case of type 1 congenital pulmonary airway malformation in the left lower lobe of a 26-year-old male. At the age of 1 year, he developed a pulmonary cystic lesion, which was considered to be bronchopulmonary sequestration. He grew up healthy and showed no impairment during exercise; however, giant bullous lesion development along with compressed left upper lobe and mediastinum was recently noted; consequently, the patient was referred to our hospital for further examination. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1093/icvts/ivz032DOI Listing
July 2019
8 Reads

Cystic and pseudocystic pulmonary malformations in children: Clinico-pathological correlation.

Ann Diagn Pathol 2019 Apr 16;39:78-85. Epub 2019 Feb 16.

Unidad de Investigación Médica en Enfermedades Respiratorias, Unidad Médica de Alta Especialidad, Hospital de Pediatría Silvestre Frenk Freund, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, Ciudad de México, Mexico.

Pulmonary malformations are rare disorders, with cystic and pseudocystic pulmonary malformations (CPPM) the most frequent, and constitute the first cause of lobectomy in children <1 year of age. Morphological overlap of congenital cystic pulmonary lesions might correspond to a spectrum of lesions in which bronchial atresia is a common etiopathogenetic mechanism. We aimed to report the frequency of CPPM resected in a tertiary-level hospital and to evaluate the degree of agreement between presurgical and anatomopathological diagnoses. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.anndiagpath.2019.02.005DOI Listing
April 2019
11 Reads

Agreement between magnetic resonance imaging and computed tomography in the postnatal evaluation of congenital lung malformations: a pilot study.

Eur Radiol 2019 Sep 22;29(9):4544-4554. Epub 2019 Feb 22.

Pediatric Radiology and Neuroradiology, ASST Fatebenefratelli-Sacco Milano, Children's Hospital V. Buzzi, Via Castelvetro 32, 20154, Milan, Italy.

Objectives: To compare postnatal magnetic resonance imaging (MRI) with the reference standard computed tomography (CT) in the identification of the key features for diagnosing different types of congenital lung malformation (CLM).

Methods: Respiratory-triggered T2-weighted single-shot turbo spin echo (ss-TSE), respiratory-triggered T1-weighted turbo field echo (TFE), balanced fast field echo (BFFE), and T2-weighted MultiVane sequences were performed at 1.5 T on 20 patients prospectively enrolled. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00330-019-06042-wDOI Listing
September 2019
9 Reads

In prenatally diagnosed CPAM, does the affected lobe influence the timing of symptom onset?

Pediatr Surg Int 2019 May 16;35(5):559-563. Epub 2019 Feb 16.

Department of Pediatric General and Urogenital Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, 113-8421, Tokyo, Japan.

Purpose: We investigated the relationship between the affected lobe and symptom onset in prenatally diagnosed congenital pulmonary airway malformation (CPAM).

Methods: 53 CPAM patients diagnosed prenatally were reviewed retrospectively by creating 2 groups according to symptom onset. Group Sneo: (symptomatic during the neonatal period; n = 13) and group S > neo: (symptomatic after the neonatal period; n = 40) were compared for type of CPAM, affected lobes, types of symptoms/infections, treatment, duration of follow-up, and histopathology. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00383-019-04460-xDOI Listing
May 2019
4 Reads

Thoracoscopic Pulmonary Lobectomy for Densely Fused Pulmonary Lobes in Children with Congenital Pulmonary Airway Malformation: Technical Tips.

J Laparoendosc Adv Surg Tech A 2019 Mar 8;29(3):415-419. Epub 2019 Feb 8.

1 Department of Pediatric General and Urogenital Surgery, Juntendo University School of Medicine, Tokyo, Japan.

Aim: Thoracoscopic pulmonary lobectomy (TPL) is extremely challenging in cases where severe incomplete fissure causes densely fused pulmonary lobes (DFPL) since pulmonary arteries (PAs) are buried and completely concealed by DFPL. We describe TPL for DFPL including a technical tip to prevent pitfalls.

Materials And Methods: Four congenital pulmonary airway malformation (CPAM) and DFPL (left-upper: 2, left-lower: 1, right-middle: 1) were treated. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1089/lap.2018.0168DOI Listing
March 2019
12 Reads

[Asymmetric auscultation: What the truth hides].

An Pediatr (Barc) 2019 Nov 1;91(5):353-354. Epub 2019 Feb 1.

Servicio de Neumología Infantil, Cátedra de Pediatría UMA, Hospital Regional Universitario, Málaga, España.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.anpedi.2018.09.008DOI Listing
November 2019

Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration: a 12-year 3-center experience in China.

Sci Rep 2019 01 30;9(1):943. Epub 2019 Jan 30.

Department of Ultrasound Diagnosis, The Second Xiangya Hospital, Central South University, Changsha, Hunan, 410011, China.

To provide useful information for diagnosing and predicting fetal intraabdominal extralobar pulmonary sequestration (IEPS), a retrospective review of diagnostic approaches was conducted. Ultrasonography was performed serially in 21 fetuses with IEPS from 2005 to 2017. Prenatal sonographic features, treatment, and outcomes of each case were evaluated and collected. Read More

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1038/s41598-018-37268-1DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6353922PMC
January 2019
12 Reads