906 results match your criteria Cheilitis Granulomatosa Miescher-Melkersson-Rosenthal Syndrome


Fatal course of clofazimine-induced pulmonary crystal deposition in a patient with Melkersson-Rosenthal syndrome
.

Int J Clin Pharmacol Ther 2020 Jun 26. Epub 2020 Jun 26.

A wide variety of drugs and substances have the potential to damage the respiratory system by different mechanisms. Clofazimine is an anti-leprosy drug that is normally only prescribed for a few years. It has a very long half-life, and crystalline deposition of the drug in various tissues has been documented. Read More

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http://dx.doi.org/10.5414/CP203784DOI Listing

The histopathological spectrum of Melkersson-Rosenthal syndrome: analysis of 47 cases.

J Cutan Pathol 2020 Jun 23. Epub 2020 Jun 23.

Department of Pathology, Dental School- University of São Paulo, Brazil.

Background: Melkersson-Rosenthal syndrome (MRS) is a rare disease characterized by the triad of recurrent orofacial edema, relapsing facial paralysis and plicated tongue. Histopathological features of MRS have not been extensively analyzed.

Methods: The present study investigated the histopathological aspects of oral lesions from 47 MRS patients. Read More

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http://dx.doi.org/10.1111/cup.13784DOI Listing

Panuveitis revealing Melkersson Rosenthal syndrome: a case report.

Tunis Med 2020 Jan;98(1):90-92

Aim: To describe a case of panuveitis revealing Melkersson Rosenthal syndrome (MRS).

Case Report:   A 35-year-old female with a history of bilateral chronic idiopathic panuveitis was referred for work up. On examination, her visual acuity was 3/10 in the right eye and limited to hand motion in the left eye. Read More

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January 2020

Management Strategies of Melkersson-Rosenthal Syndrome: A Review.

Int J Gen Med 2020 26;13:61-65. Epub 2020 Feb 26.

Pediatric Neurology Unit, Department of Pediatrics, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India.

Melkerrson-Rosenthal syndrome is a rare disorder of unknown aetiology and characterized by the triad of oro-facial edema, facial nerve palsy, and furrowing of the tongue. Two or more of the above are essential for making a clinical diagnosis. The mainstay of treatment is corticosteroids. Read More

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http://dx.doi.org/10.2147/IJGM.S186315DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7049838PMC
February 2020

A case-control study of HLA alleles in Brazilian patients with Melkersson-Rosenthal syndrome.

Eur J Med Genet 2020 Jul 8;63(7):103879. Epub 2020 Feb 8.

Department of Pathology, Dental School- University of São Paulo, Brazil.

Melkersson-Rosenthal syndrome (MRS) is a neuromucocutaneous disease that manifests by the triad of recurrent orofacial edema (frequently as cheilitis granulomatosa), relapsing facial paralysis and plicated tongue. The cause of MRS remains unknown, but genetic predisposal and a relationship with inflammatory bowel disease are suspected. The objective of this research was to compare the frequency of class I and II HLA alleles in patients with a confirmed diagnosis of MRS with those of a healthy control group. Read More

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http://dx.doi.org/10.1016/j.ejmg.2020.103879DOI Listing

Orofacial Edema and Facial Paralysis: Melkersson-Rosenthal Syndrome.

Authors:
Shengnan Yu Qin Li

J Clin Rheumatol 2020 Feb 3. Epub 2020 Feb 3.

Department of Rheumatology and Immunology, The First People's Hospital of Yunnan Province, Kunming, Yunnan, China.

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http://dx.doi.org/10.1097/RHU.0000000000001339DOI Listing
February 2020

Characteristics of the salivary microbiota in cheilitis granulomatosa.

Med Oral Patol Oral Cir Bucal 2019 Nov 1;24(6):e719-e725. Epub 2019 Nov 1.

Zhongguancun Avenue South Haidian District Beijing 100081, China

Background: Cheilitis granulomatosa (CG) is a disturbing and persistent idiopathic lip swelling. The cause and treatment has not been wholly elucidated. Some reports infer that CG is mainly associated with dental infection but no firm or reliable microbiological evidence has been provided for a causative organism. Read More

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http://dx.doi.org/10.4317/medoral.23041DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6901138PMC
November 2019

Unsuccessful Treatment of Cheilitis Granulomatosa with Oral Methotrexate.

Case Rep Dermatol 2019 Sep-Dec;11(3):249-255. Epub 2019 Sep 27.

Division of Dermatology, Faculty of Medicine Ramathibodi Hospital, Mahidol University, Bangkok, Thailand.

Cheilitis granulomatosa (CG) is a rare idiopathic condition with painless lip swelling, characterized by non-necrotizing granulomatous inflammation in the absence of other identifiable causes such as Crohn's disease, sarcoidosis, foreign body reaction, or infection. CG may precede the presentation of Crohn's disease after long-term follow-up. Spontaneous remission of CG rarely occurs. Read More

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http://dx.doi.org/10.1159/000503138DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6792424PMC
September 2019
1 Read

Efficacy of vedolizumab in granulomatous cheilitis refractory to TNFα inhibitors.

Int J Dermatol 2019 Dec 9;58(12):e236-e237. Epub 2019 Sep 9.

Dermatology Department, University Hospital of Tours, University of Tours, Tours, France.

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http://dx.doi.org/10.1111/ijd.14638DOI Listing
December 2019

Melkersson-Rosenthal syndrome with coeliac and allergic diseases.

BMJ Case Rep 2019 Aug 28;12(8). Epub 2019 Aug 28.

Physical and Rehabilitation Medicine Department, Centro Hospitalar e Universitario de Coimbra EPE, Coimbra, Portugal.

A 45-year-old man presented with a 10-year history of relapsing oedema of the lips. Moreover, he exhibited recurrent facial nerve palsy since the age of 10 years, coeliac disease since the age of 12 years, atopic eczema, allergic rhinitis and asthma. Physical examination revealed lip swelling and lingua plicata. Read More

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http://dx.doi.org/10.1136/bcr-2019-229857DOI Listing
August 2019
4 Reads

Melkersson-Rosenthal syndrome: About a Tunisian family and review of the literature.

Clin Neurol Neurosurg 2019 10 5;185:105457. Epub 2019 Aug 5.

Department of Neurology, Military Hospital of Tunis, Tunisia.

Melkersson-Rosenthal (MRS) syndrome is a rare disorder defined as a triad of recurrent peripheral facial palsy, orofacial edema, and fissured tongue. The etiology of this disease is still unclear. Genetic origin has been postulated. Read More

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http://dx.doi.org/10.1016/j.clineuro.2019.105457DOI Listing
October 2019
2 Reads

Cheilitis granulomatosa and Crohn's disease : a case report.

Acta Gastroenterol Belg 2019 Apr-Jun;82(2):326-328

Universitair Ziekenhuis Brussel (UZ Brussel), Vrije Universiteit Brussel (VUB), Departement of Gastro-Enterology, Laarbeeklaan 101, 1090 Brussels, Belgium.

In this case report we describe the evolution of Cheilitis granulomatosa (GC) in a young patient with Crohn's disease during treatment with anti-TNF-alfa therapy. Read More

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July 2019
41 Reads

Hold the spice: Allergy to garlic and sulfites-Possible relevance in a patient with cheilitis granulomatosa.

Contact Dermatitis 2019 Nov 11;81(5):397-398. Epub 2019 Jul 11.

Department of Dermatology, Park Nicollet Health Services, Minneapolis, Minnesota.

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http://dx.doi.org/10.1111/cod.13345DOI Listing
November 2019
9 Reads

Successful treatment of cheilitis granulomatosa with lenalidomide.

J Eur Acad Dermatol Venereol 2019 10 20;33(10):e357-e359. Epub 2019 May 20.

Department of Dermatology and Allergology, Philipps Universität Marburg, Marburg, Germany.

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http://dx.doi.org/10.1111/jdv.15654DOI Listing
October 2019
5 Reads

Persistent Upper Lip Swelling in a Young Woman: Answer.

Am J Dermatopathol 2019 May;41(5):386-387

Departments of Dermatology, and.

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http://dx.doi.org/10.1097/DAD.0000000000001048DOI Listing
May 2019
7 Reads

A 30-year follow-up study of patients with Melkersson-Rosenthal syndrome shows an association to inflammatory bowel disease.

Ann Med 2019 03 13;51(2):149-155. Epub 2019 Apr 13.

a Department of Otorhinolaryngology, Head and Neck Surgery , Helsinki University Hospital and University of Helsinki , Helsinki , Finland.

Melkersson-Rosenthal syndrome (MRS) is often classified under the term orofacial granulomatosis (OFG). A part of OFG patients eventually develop Crohn's disease (CD), but the relationship between MRS and CD is unknown. To evaluate the long-term outcomes of MRS patients, with specific interest in bowel-related symptoms. Read More

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http://dx.doi.org/10.1080/07853890.2019.1591634DOI Listing
March 2019
7 Reads

Melkersson⁻Rosenthal Syndrome in Childhood: Report of Three Paediatric Cases and a Review of the Literature.

Int J Environ Res Public Health 2019 04 10;16(7). Epub 2019 Apr 10.

Pediatric Clinic Fondazione IRCCS Policlinico San Matteo⁻V.le Golgi, 19 Pavia, Italy.

Melkersson-Rosenthal syndrome (MRS) in children is a rare condition, clinically characterised by a triad of synchronous or metachronous symptoms: recurrent peripheral facial palsy, relapsing orofacial oedema, and a fissured tongue; the most recent review published on the topic has reported 30 published patients. The aetiology of this disease is still unclear. However, genetic factors, as well as alterations in immune functions, infections, and allergic reactions have been postulated. Read More

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http://dx.doi.org/10.3390/ijerph16071289DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6479526PMC
April 2019
7 Reads

[Recurrent and alternating peripheral facial palsy in a Rehabilitation department].

Rehabilitacion (Madr) 2019 Jan - Mar;53(1):60-64. Epub 2018 Jul 18.

Servicio de Rehabilitación y Medicina Física, Hospital Clínico Universitario de Valencia, Valencia, España.

Peripheral facial palsy is a relatively frequent condition in rehabilitation departments. The most common aetiology is idiopathic, known as Bell's palsy, which usually has a good prognosis and resolves without sequels. The presence of uncommon symptoms with the facial palsy should lead to suspicion of another possible aetiology, as occurred in the case presented here. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S00487120183009
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http://dx.doi.org/10.1016/j.rh.2018.06.001DOI Listing
April 2020
19 Reads

For Whom the Bell's Toll: Recurrent Facial Nerve Paralysis, A Retrospective Study and Systematic Review of the Literature.

Otol Neurotol 2019 04;40(4):517-528

Department of Otorhinolaryngology.

Purpose: To examine the etiology, clinical course, and management of recurrent peripheral facial nerve paralysis.

Methods: Retrospective review at a single tertiary academic center and systematic review of the literature. Clinical presentation, laboratory and imaging findings, treatment and outcome for all cases of recurrent ipsilateral, recurrent contralateral, and bilateral simultaneous cases of facial paralysis are reviewed. Read More

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http://dx.doi.org/10.1097/MAO.0000000000002167DOI Listing
April 2019
35 Reads

Melkersson-Rosenthal syndrome: a case report of a rare disease with overlapping features.

Allergy Asthma Clin Immunol 2019 5;15. Epub 2019 Jan 5.

2Department of Neuroscience, Division of Dentistry, University of Padua, Via Giustiniani 2, 35128 Padua, Italy.

Background: Melkersson-Rosenthal syndrome (MRS) is a rare, neuro-mucocutaneous disease which presents as orofacial swelling, facial palsy and fissured tongue. These symptoms may occur simultaneously or, more frequently, with a oligosymptomatic or monosymptomatic pattern. Swelling, that is the most common initial finding, may mimic hereditary or acquired angioedema, a disorder caused by histamine or bradykinin-mediated plasma-leakage affecting subcutaneous and/or submucosal tissue. Read More

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https://aacijournal.biomedcentral.com/articles/10.1186/s1322
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http://dx.doi.org/10.1186/s13223-018-0316-zDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6320604PMC
January 2019
33 Reads

Teaching NeuroImages: Melkersson-Rosenthal syndrome with permanent bilateral facial weakness.

Neurology 2019 01;92(1):e81

From the Clinical Neurophysiology Laboratory (F.R.), Comprehensive Headaches Center (N.T.), Department of Neurology (N.T., E.M.R.), and Behavioral and Cognitive Center (M.H.), Orlando VA Medical Center; and Department of Neurology (F.R., M.H.), UCF Medical School, Orlando, FL.

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http://dx.doi.org/10.1212/WNL.0000000000006683DOI Listing
January 2019
5 Reads

The Light at the End of the Tunnel: A Case of Dysautonomia Associated With Melkersson-Rosenthal Syndrome

Ir Med J 2018 06 7;111(6):779. Epub 2018 Jun 7.

Department of Neurology, Galway University Hospital, Galway, Ireland.

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June 2018
8 Reads

An Unusual Cause of Recurrent Facial Nerve Palsy.

Pediatr Neurol 2019 02 25;91:68-69. Epub 2018 Oct 25.

Division of Neuroradiology and Pediatric Radiology, University of Arkansas for Medical Sciences, Little Rock, Arkansas.

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http://dx.doi.org/10.1016/j.pediatrneurol.2018.10.012DOI Listing
February 2019

[Cheilitis granulomatosa revealing Crohn's disease].

Pan Afr Med J 2018 20;30:147. Epub 2018 Jun 20.

Service d'Hépato-gastroentérologie, Faculté de Médecine et de Pharmacie de Fès, Université Sidi Mohammed Ben Abdellah, Fès, Maroc.

Many disorders of the digestive tract cause cutaneous manifestations that may be an indication of an underlying condition; hence dermatologist plays a key role in recommending that the patient see a gastroenterologist. Conversely, gastroenterologist often sees patients with mucocutaneous lesions suggesting possible association with well-known digestive disorders. Chronic inflammatory bowel diseases are the typical example of this essential collaboration between the two specialities. Read More

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http://dx.doi.org/10.11604/pamj.2018.30.147.5395DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6201612PMC
November 2018
19 Reads

Genetic Diagnostic Elucidation of a Patient With Multiorgan Granulomas, Facial Peculiarities, and Psychomotor Retardation.

Front Genet 2018 27;9:355. Epub 2018 Sep 27.

Klinik für Kinderheilkunde III, Universitätsklinikum Essen, Essen, Germany.

We report the case of a 19-years-old patient who presented with a perplexing variety of symptoms which included remarkable facial features, intellectual disability, granulomatous upper lip swelling (previously diagnosed as Melkersson-Rosenthal syndrome), Crohn's-like disease, non-productive cough, and a granulomatous mass localized in the left lung. Chronic granulomatous disease (CGD) was diagnosed using dihydrorhodamine 123 assay that showed low levels of phagocytic NADPH-oxidase. DNA sequencing revealed a heterozygous mutation in the gene on chromosome 7. Read More

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https://www.frontiersin.org/article/10.3389/fgene.2018.00355
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http://dx.doi.org/10.3389/fgene.2018.00355DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6170790PMC
September 2018
30 Reads

Idiopathic macrocheilia.

BMJ Case Rep 2018 Sep 27;2018. Epub 2018 Sep 27.

Oral and Maxillofacial Surgery, Dharmsinh Desai University Faculty of Dental Science, Nadiad, Gujarat, India.

A 13-year-boy presented with painless swelling of upper and lower lips accompanied with gingival enlargement. The aetiology for these symptoms included vast pathological varieties but none of them could fit in. Clinical features were similar to orofacial graulomatosis but histopathological examination revealed chronic non-specific infection. Read More

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http://dx.doi.org/10.1136/bcr-2018-225682DOI Listing
September 2018
33 Reads

Clinical and genetic heterogeneity in Melkersson-Rosenthal Syndrome.

Eur J Med Genet 2019 Jun 11;62(6):103536. Epub 2018 Sep 11.

Manchester Centre for Genomic Medicine, Evolution and Genomic Sciences, University of Manchester, Manchester, UK; Manchester Centre for Genomic Medicine, St. Mary's Hospital, Manchester University NHS Foundation Trust, Manchester, UK. Electronic address:

Melkersson Rosenthal syndromes (MRS) is a rare autosomal dominantly inherited neurocutaneous syndrome characterised by a triad of facial (seventh cranial) nerve palsy, recurrent orofacial swelling and fissuring of the tongue. A recent report implicated a heterozygous missense variant in SLC27A1 (FATP1) as the cause of this condition in members of an affected Chinese family. We undertook Sanger sequencing of this gene in 14 affected unrelated individuals affected by MRS. Read More

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https://linkinghub.elsevier.com/retrieve/pii/S17697212183039
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http://dx.doi.org/10.1016/j.ejmg.2018.09.003DOI Listing
June 2019
17 Reads

Facial nerve palsy in children: A retrospective study of 124 cases.

J Paediatr Child Health 2019 Mar 24;55(3):299-304. Epub 2018 Aug 24.

1st Academic ENT Department, Aristotle University of Thessaloniki, AHEPA Hospital, Thessaloniki, Greece.

Aim: To report the causes and clinical evaluation of children with facial nerve palsy (FNP) admitted to an affiliated university hospital during a 5-year period (2011-2015).

Methods: A total of 124 children were retrospectively categorised into two groups: idiopathic Bell's palsy (109 patients) and the second group into other FNP aetiologies (15 patients). All children received a standardised work-up and follow-up. Read More

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http://dx.doi.org/10.1111/jpc.14190DOI Listing
March 2019
45 Reads

Facial nerve decompression.

Curr Opin Otolaryngol Head Neck Surg 2018 Oct;26(5):280-285

Department of Otolaryngology - Head and Neck Surgery.

Purpose Of Review: Facial nerve paralysis is a debilitating condition. Bell's palsy and temporal bone trauma are common causes of acute facial palsy, with recurrent idiopathic paralysis and Melkersson-Rosenthal syndrome accounting for a smaller subset of cases. Properly selected patients may benefit from facial nerve decompression. Read More

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http://dx.doi.org/10.1097/MOO.0000000000000478DOI Listing
October 2018
42 Reads

Intravenous immunoglobulins in Melkersson-Rosenthal syndrome: A clinical and neuroimaging study.

Pediatr Allergy Immunol 2018 12 15;29(8):881-883. Epub 2018 Oct 15.

UOC Pediatria, Fondazione Policlinico Universitario A. Gemelli IRCCS, Roma - Università Cattolica del Sacro Cuore, Roma, Italy.

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http://dx.doi.org/10.1111/pai.12970DOI Listing
December 2018
29 Reads

One of the Faces of Facial Swelling: Melkersson-Rosenthal Syndrome.

J Investig Allergol Clin Immunol 2018 Aug;28(4):265-267

Allergy Department, Hospital General Universitario Gregorio Marañón, Madrid, Spain.

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http://dx.doi.org/10.18176/jiaci.0255DOI Listing
August 2018
5 Reads

Melkersson-Rosenthal Syndrome: A Rare Cause of Recurrent Facial Nerve Palsy and Acute Respiratory Distress Syndrome.

Case Rep Neurol Med 2018 10;2018:1373581. Epub 2018 Jun 10.

Ankara University School of Medicine, Department of Anesthesiology and Reanimation, Division of Intensive Care Unit, Turkey.

Melkersson-Rosenthal Syndrome (MRS) is a rare disease characterized by persistent or recurrent orofacial oedema, relapsing peripheral facial paralysis, and furrowed tongue. Pathologically, granulomatosis is responsible for oedema of face, labia, oral cavity, and facial nerve. We present a patient with MRS admitted to our hospital with acute respiratory distress syndrome (ARDS). Read More

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http://dx.doi.org/10.1155/2018/1373581DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6015706PMC
June 2018
17 Reads

[Dermatopathology histoseminar. Case 4].

Authors:
Eric Frouin

Ann Pathol 2018 Aug 12;38(4):230-235. Epub 2018 Jun 12.

Service d'anatomie et de cytologie pathologiques, CHU de Poitiers, 2, rue de la Milétrie, 86021 Poitiers cedex, France. Electronic address:

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http://dx.doi.org/10.1016/j.annpat.2018.05.006DOI Listing
August 2018
4 Reads

[Miescher's granulomatous vulvitis].

Ann Dermatol Venereol 2018 Aug - Sep;145(8-9):492-499. Epub 2018 Jun 6.

Service de pathologie, hôpital Cochin, 27, rue du faubourg Saint-Jacques, 75014 Paris, France.

Background: Miescher's cheilitis, whether occurring alone or as part of Melkersson-Rosenthal syndrome, is a rare type of granulomatous inflammation of unknown cause with an even rarer genital equivalent. Herein, we describe a case of the latter condition developing over a 12-year period.

Patients And Methods: A 27-year-old woman presented episodes of unilateral vulvar oedema, which initially regressed but resulted over time in permanent vulvar and perineal tumefaction. Read More

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http://dx.doi.org/10.1016/j.annder.2018.02.017DOI Listing
February 2019
21 Reads

Melkersson-Rosenthal Syndrome: the possible role of comorbidities in the etiopathogenesis.

G Ital Dermatol Venereol 2019 Jun 16;154(3):347-351. Epub 2018 May 16.

Department of Dermatology and Venereology, Soroka Medical Center, Faculty of Health Sciences, Ben-Gurion University of the Negev, Beer-Sheva, Israel.

Background: Melkersson-Rosenthal Syndrome (MRS) is a rare syndrome. Recently, possible association between MRS and psoriasis was reported. Our objective is to evaluate the presence of comorbidities in MRS with a focus on psoriasis-related morbidities. Read More

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https://www.minervamedica.it/index2.php?show=R23Y9999N00A180
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http://dx.doi.org/10.23736/S0392-0488.18.05810-8DOI Listing
June 2019
8 Reads

A Systematic Review of the Literature of the Three Related Disease Entities Cheilitis Granulomatosa, Orofacial Granulomatosis and Melkersson - Rosenthal Syndrome.

Curr Pediatr Rev 2018 ;14(3):196-203

Department of Pediatrics, Hospital Ostallgau-Kaufbeuren, Kaufbeuren, Germany.

Background And Objective: Melkersson Rosenthal syndrome (MRS) is a rare disorder of unknown etiology and comprises the triad: orofacial edema, recurrent facial paralysis and lingua plicata. In the current literature confusing heterogeneity exists, mixing together the historically grown terms cheilitis granulomatosa or granulomatous cheilitis, Melkersson Rosenthal syndrome and the umbrella term Orofacial Granulomatosis (OFG).

Methods: We provide a systematic review comprising all three disease entities of orofacial granulomatosis using the computerized database "Pubmed Medline" entering the keywords "orofacial granulomatosis" (141 references), "Melkersson-Rosenthal syndrome" (207 references), "granulomatous cheilitis" or "cheilitis granulomatosa" (102 references) back to 1956. Read More

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http://dx.doi.org/10.2174/1573396314666180515113941DOI Listing
December 2018
9 Reads

Allergic and Immunologic Perspectives of Inflammatory Bowel Disease.

Clin Rev Allergy Immunol 2019 Oct;57(2):179-193

Division of Gastroenterology and Hepatology, Penn State Milton S Hershey Medical Center, 500 University Dr, Hershey, PA, 17033, USA.

Inflammatory bowel disease (IBD) is a chronic immune-mediated inflammatory condition primarily involving the gastrointestinal tract. It includes Crohn's disease (CD), ulcerative colitis (UC), and a less common phenotype-indeterminate colitis. It is thought to result from a complex interplay of environmental, microbial, and host factors including genetic factors, although the exact mechanism is not known. Read More

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http://link.springer.com/10.1007/s12016-018-8690-3
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http://dx.doi.org/10.1007/s12016-018-8690-3DOI Listing
October 2019
17 Reads

Metronidazole as a monotherapy in the management of granulomatous cheilitis.

Indian J Dermatol Venereol Leprol 2018 Jul-Aug;84(4):491-495

Department of Dermatology, MGM Medical College and Hospital, Mumbai, Maharashtra, India.

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http://dx.doi.org/10.4103/ijdvl.IJDVL_1169_16DOI Listing
November 2018
3 Reads

Selected presentations of lip enlargement: clinical manifestation and differentiation.

Postepy Dermatol Alergol 2018 Feb 20;35(1):18-25. Epub 2018 Feb 20.

Department of Oral Surgery, Poznan University of Medical Sciences, Poznan, Poland.

Lip enlargement may be an important symptom of either systemic or local diseases. On the basis of selected age-matched clinical cases we present the possible causes of lip swelling. We describe the most representative symptoms and recommend treatment of these pathologies. Read More

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http://dx.doi.org/10.5114/ada.2018.73160DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5872243PMC
February 2018
9 Reads

Melkersson-Rosenthal syndrome successfully treated with adalimumab.

Cutis 2018 Feb;101(2):122-124

Department of Dermatology, Icahn School of Medicine at Mount Sinai, New York, New York, USA.

Melkersson-Rosenthal syndrome (MRS) is a rare syndrome of facial nerve palsy, facial edema, and lingua plicata that can be difficult to treat. We observed a patient with MRS of 4 years' duration that was unsuccessfully treated with multiple therapies. After a variety of diagnoses were considered at outside institutions, including Bell palsy, we diagnosed the patient with MRS based on clinical presentation of the classic triad. Read More

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February 2018
10 Reads

A favorable response to omalizumab in a patient with cheilitis granulomatosa.

J Allergy Clin Immunol Pract 2018 Jul - Aug;6(4):1425-1426. Epub 2018 Feb 6.

Department of Biomedical Sciences and Human Oncology Unit of Internal Medicine "G. Baccelli", "Aldo Moro" University of Bari Medical School, Policlinico, Bari, Italy.

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http://dx.doi.org/10.1016/j.jaip.2017.12.013DOI Listing
November 2019
5 Reads

Granulomatous diseases: Kids are not just little people.

Clin Dermatol 2017 Nov - Dec;35(6):555-565. Epub 2017 Aug 4.

Department of Dermatology, University of Connecticut Health Center, Farmington, CT.

Granulomatous diseases represent a heterogeneous group of conditions characterized by histiocytic inflammation that affect patients of any age. These diseases differ widely in their pathogenesis and include infectious and noninfectious conditions. This review focuses on noninfectious granulomatous conditions, with particular emphasis on age-related differences in the onset, epidemiology, clinical manifestations, prognosis, and age-specific management of specific granulomatous disorders. Read More

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http://dx.doi.org/10.1016/j.clindermatol.2017.08.006DOI Listing
July 2018
10 Reads

Melkersson-Rosenthal syndrome.

QJM 2018 Mar;111(3):199

Department of Dermatology, Venerology and Allergology, University School of Medicine Essen-Duisburg, Hufelandstrasse 55, 45122 Essen, Germany.

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https://academic.oup.com/qjmed/article/111/3/199/4568571
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http://dx.doi.org/10.1093/qjmed/hcx210DOI Listing
March 2018
8 Reads

Treatment of orofacial granulomatosis: a case report.

J Med Case Rep 2017 Oct 25;11(1):300. Epub 2017 Oct 25.

Department of Gastroenterology and Hepatology, University of Illinois Peoria Campus, OSF Saint Francis Medical Center, Peoria, IL, 61637, USA.

Background: Orofacial granulomatosis is a relatively recent term coined by Wiesenfield et al. in 1985 to define granulomatous lesions of oral mucosa without intestinal involvement. When it presents in a triad encompassing facial nerve palsy, lip swelling, and fissured or furrowed tongue it is called Melkersson-Rosenthal syndrome while monosymptomatic or oligosymptomatic forms are referred to as granulomatous cheilitis. Read More

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http://jmedicalcasereports.biomedcentral.com/articles/10.118
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http://dx.doi.org/10.1186/s13256-017-1455-4DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5655806PMC
October 2017
39 Reads

[An unusual presentation of mantle cell lymphoma].

Ann Dermatol Venereol 2018 Mar 6;145(3):187-188. Epub 2017 Oct 6.

Service de dermatologie, CHIC Laënnec, 14, avenue Yves-Thépot, 29000 Quimper, France.

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http://dx.doi.org/10.1016/j.annder.2017.08.013DOI Listing
March 2018
9 Reads

Successful treatment of childhood cheilitis granulomatosa with infliximab.

J Dtsch Dermatol Ges 2017 Dec 6;15(12):1241-1243. Epub 2017 Oct 6.

Department of Dermatology and Allergy, Charité - Universitätsmedizin Berlin, Berlin, Germany.

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http://dx.doi.org/10.1111/ddg.13348DOI Listing
December 2017
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Melkersson-rosenthal syndrome: a case report.

J Istanb Univ Fac Dent 2017 2;51(1):42-45. Epub 2017 Jan 2.

Department of Dentomaxillofacial Radiology, Gazi University Faculty of Dentistry Turkey.

Melkersson-Rosenthal Syndrome (MRS) is a rare disorder consisting of a triad of persistent or recurrent orofacial edema, relapsing facial paralysis and fissured tongue. It is rarely possible to observe all aspects of the classical triad at the same time, since these symptoms may appear in different times of life cycle. The most common symptom is orofacial edema. Read More

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http://dx.doi.org/10.17096/jiufd.96279DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5573494PMC
January 2017
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Orofacial granulomatosis in a 12-year-old girl successfully treated with intravenous pulse corticosteroid therapy and chloroquine.

Pediatr Dermatol 2017 Nov 21;34(6):e324-e327. Epub 2017 Sep 21.

Division of Pediatric Dermatology, Clinic of Dermatovenereology, Clinical Center of Serbia, Belgrade, Serbia.

Orofacial granulomatosis, a rare disease in childhood, is characterized by orofacial swelling in the absence of systemic disease. We report the case of a 12-year-old girl with asymptomatic erythematous infiltration of her upper lip, cheeks, and chin that had persisted for more than 2 years; biopsy confirmed granuloma formation. Because a large area was affected, intralesional corticosteroids were inappropriate and six cycles of 3-day intravenous pulse corticosteroid therapy (dexamethasone 1. Read More

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http://dx.doi.org/10.1111/pde.13279DOI Listing
November 2017
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Effectiveness of surgical treatment of severe macrocheilia in a patient with orofacial granulomatosis.

Clin Exp Dermatol 2017 Dec 27;42(8):887-889. Epub 2017 Jul 27.

Department of Clinical-Surgical, Diagnostic and Pediatric Science, Institute of Dermatology, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy.

Orofacial granulomatosis (OFG) is the term given to a group of diseases characterized by the presence of non-necrotizing granulomatous inflammation affecting the soft tissues of the orofacial region. Treatment of OFG is often challenging and unsatisfactory. We report on a 32-year-old man with a 2-year history of oedema and swelling of the upper lip without systemic symptoms. Read More

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http://dx.doi.org/10.1111/ced.13201DOI Listing
December 2017
9 Reads