3,550 results match your criteria Cardiology in the Young[Journal]


Examining variation in interstage mortality rates across the National Pediatric Cardiology Quality Improvement Collaborative: do lower-mortality centres have lower-risk patients?

Cardiol Young 2018 Jun 21:1-6. Epub 2018 Jun 21.

1Department of Pediatrics and Communicable Diseases,Congenital Heart Center,C.S. Mott Children's Hospital,Ann Arbor,MI,USA.

Background: Although interstage mortality for infants with hypoplastic left heart syndrome has declined within the National Pediatric Cardiology Quality Improvement Collaborative, variation across centres persists. It remains unclear whether centres with lower interstage mortality have lower-risk patients or whether differences in care may explain this variation. We examined previously established risk factors across National Pediatric Cardiology Quality Improvement Collaborative centres with lower and higher interstage mortality rates. Read More

View Article

Out-of-pocket medical expenses in severe CHD.

Cardiol Young 2018 Jun 20:1-5. Epub 2018 Jun 20.

2Department of Pediatrics,Medical University of South Carolina,Charleston,SC,USA.

IntroductionFamilies of children born with CHD face added stress owing to uncertainty about the magnitude of the financial burden for medical costs they will face. This study seeks to assess the family responsibility for healthcare bills during the first 12 months of life for commercially insured children undergoing surgery for severe CHD.

Methods: The MarketScan ® database from Truven was used to identify commercially insured infants in 39 states from 2010 to 2012 with an ICD-9 diagnosis code for transposition of the great arteries, tetralogy of Fallot, or truncus arteriosus, as well as the corresponding procedure code for complete repair. Read More

View Article

Importance of transcatheter closure test for giant ventricular septal defect associated with pulmonary hypertension: a case with successful surgical repair of the defect.

Cardiol Young 2018 Jun 20:1-3. Epub 2018 Jun 20.

1Cardiovascular Surgery,Union Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan,China.

This is the first attempt to use a temporary occluder to close a giant perimembranous ventricular septal defect (32 mm), which obtains clinical evidence of good haemodynamics in patients with severe pulmonary hypertension. This may provide an alternative assessment to guide cardiac surgeons in determining a definitive treatment. Read More

View Article

Technical factors are associated with complications and repeat intervention in neonates undergoing transcatheter right ventricular decompression for pulmonary atresia and intact ventricular septum: results from the congenital catheterisation research collaborative.

Cardiol Young 2018 Jun 18:1-8. Epub 2018 Jun 18.

6Cincinnati Children's Hospital Medical Center, Cincinnati, OH,USA.

Background: Transcatheter right ventricle decompression in neonates with pulmonary atresia and intact ventricular septum is technically challenging, with risk of cardiac perforation and death. Further, despite successful right ventricle decompression, re-intervention on the pulmonary valve is common. The association between technical factors during right ventricle decompression and the risks of complications and re-intervention are not well described. Read More

View Article

Successful retrieval of a migrated neonatal ductal stent and strategies to reposition the expanded stent in the duct.

Cardiol Young 2018 Jun 18:1-3. Epub 2018 Jun 18.

Department of Pediatric Cardiology,Institute of Cardio Vascular Diseases,Madras Medical Mission,Chennai,India.

A neonatal ductal stent deployed in a straight short conical duct on second postnatal day migrated owing to inadequate ductal constriction. It was successfully retrieved using a larger balloon and redeployed in the duct again. Intravenous indomethacin prevented further stent migration. Read More

View Article

Left aortic arch with right descending aorta and severe coarctation: an unusual "vascular clamp" with airway compression.

Cardiol Young 2018 Jun 13:1-3. Epub 2018 Jun 13.

Department of Pediatric Cardiology,Madras Medical Mission,Chennai,India.

Left aortic arch with right descending aorta is a rare congenital anomaly. We describe the clinical presentation of this unusual anomaly associated with cardiorespiratory compromise from severe aortic obstruction and left main bronchus compression. The anatomical peculiarities, embryological basis, and surgical solutions are presented. Read More

View Article
June 2018
2 Reads

The REACH protocol: an innovative strategy for home management of infants with complex CHD.

Cardiol Young 2018 Jul;28(7):961-967

1School of Nursing,University of Pennsylvania,Philadelphia,PA,USA.

Approximately 32,000 infants are born with CHDs each year in the United States of America. Of every 1000 live births, 2.3 require surgical or transcatheter intervention in the first year of life. Read More

View Article
July 2018
1 Read

Safety of ferumoxytol in children undergoing cardiac MRI under general anaesthesia.

Cardiol Young 2018 Jul;28(7):916-921

1Lucile Packard Children's Hospital Heart Center,Stanford University School of Medicine,Palo Alto,CA,USA.

Background: Ferumoxytol, an "off-label" contrast agent, allows for better cardiac MRI quality as compared with gadolinium-based contrast agents. However, hypotension has been reported with the use of ferumoxytol for indications other than cardiac MRI. The purpose of our investigation was to evaluate the safety of ferumoxytol in children undergoing general anaesthesia for cardiac MRI. Read More

View Article
July 2018
1 Read

Pharmacologic therapy with flecainide for asymptomatic Wolff-Parkinson-White syndrome in an infant with severe left ventricular dyssynchrony.

Cardiol Young 2018 Jul;28(7):970-973

Department of Pediatric Cardiology,Yokohama City University Hospital,Fukuura 3-9,Kanazawa-ku,Yokohama city,Kanagawa 236-0004,Japan.

Some asymptomatic patients with Wolff-Parkinson-White syndrome have severe left ventricular dyssynchrony and dysfunction. We describe a patient who was given a diagnosis of Wolff-Parkinson-White syndrome in infancy and had a complete response to pharmacologic therapy with flecainide. Our findings suggest that flecainide is a suitable resynchronisation therapy for such infants. Read More

View Article
July 2018
2 Reads

Left ventricular function and exercise capacity after arterial switch operation for transposition of the great arteries: a systematic review and meta-analysis.

Cardiol Young 2018 Jul;28(7):895-902

5Paediatric Clinical Exercise Physiology,Wilhelmina Children's Hospital,University Medical Centre Utrecht,The Netherlands.

Background: The arterial switch operation for transposition of the great arteries was initially believed to be an anatomical correction. Recent evidence shows reduced exercise capacity and left ventricular function in varying degrees in the long term after an arterial switch operation.

Objective: To perform a meta-analysis on long-term exercise capacity and left ventricular ejection fraction after an arterial switch operation. Read More

View Article
July 2018
2 Reads

Commentary on the guidelines paper by Krasemann et al.

Authors:
Robert Vincent

Cardiol Young 2018 06;28(6):795

Children's Healthcare of Atlanta Cardiology,2835 Brandywine Rd. suite 300,Atlanta,GA,USA.

View Article
June 2018
1 Read

Percutaneous pulmonary valve implantation with anomalous left anterior descending coronary artery.

Cardiol Young 2018 Jul 21;28(7):968-969. Epub 2018 May 21.

Department of Pediatric Cardiology,Children's Hospital of Georgia,Augusta University,Augusta,GA 30912,USA.

Percutaneous pulmonary valve placement in patients with an anomalous coronary artery is rare and can be complicated by coronary artery compression. We report successful implantation of a percutaneous pulmonary valve in a patient with an anomalous left anterior descending artery. Read More

View Article
July 2018
1 Read

Retrieval of large Occlutech Figula Flex septal defect occluders using a commercially available bioptome: proof of concept.

Cardiol Young 2018 Jul 21;28(7):955-960. Epub 2018 May 21.

1Department of Pediatric Cardiology and Congenital Heart Disease,German Heart Center Munich at the TU Munich,Munich,Germany.

Objectives: This study aimed to develop a method for retrieval of the new meshed nitinol atrial septal defect occluders - Ceraflex and Occlutech.

Background: The newly developed atrial septal defect occluders have potential benefits considering implantation, but concerns regarding their removal in case of embolisation have been raised.

Methods: Over 21 years, 1449 patients underwent interventional atrial septal defect occlusion in our institution. Read More

View Article
July 2018
3 Reads

DMD mutation and LTBP4 haplotype do not predict onset of left ventricular dysfunction in Duchenne muscular dystrophy.

Cardiol Young 2018 Jul 16;28(7):910-915. Epub 2018 May 16.

2Department of Pediatrics,Division of Cardiology,University of Utah,Salt Lake City,UT,USA.

Cardiomyopathy develops in >90% of Duchenne muscular dystrophy (DMD) patients by the second decade of life. We assessed the associations between DMD gene mutations, as well as Latent transforming growth factor-beta-binding protein 4 (LTBP4) haplotypes, and age at onset of myocardial dysfunction in DMD. DMD patients with baseline normal left ventricular systolic function and genotyping between 2004 and 2013 were included. Read More

View Article
July 2018
2 Reads

Symptomatic myocardial bridging: a frequently occurring coronary variation can cause severe myocardial ischaemia in affected children with underlying cardiac conditions.

Cardiol Young 2018 Jun 16;28(6):826-831. Epub 2018 May 16.

1Department of Pediatric Cardiology and Congenital Heart Disease,Heart Center,University of Leipzig,Leipzig,Germany.

Myocardial bridging is a congenital coronary artery anomaly in which the coronary artery has a partly "tunnelled" intramyocardial course. This tunnelling leads to compression of the affected vessel segment during ventricular systole. It is considered to be a benign variation of the norm in about 25% of the population caused by an aberrancy of embryologic coronary development. Read More

View Article
June 2018
4 Reads

Giant left ventricular rhabdomyoma treated successfully with everolimus: case report and review of literature.

Cardiol Young 2018 Jul 15;28(7):903-909. Epub 2018 May 15.

2Neonatal Intensive Care Unit,Instituto Nacional de Perinatología Isidro Espinosa de los Reyes,Mexico City,Mexico.

IntroductionIntracardiac rhabdomyomas can cause severe ventricular dysfunction and outflow tract obstruction.Case reportA term newborn infant with antenatal diagnosis of giant left ventricle rhabdomyoma presented with cardiac failure and duct-dependent systemic circulation after birth. She was treated successfully with everolimus, showing decrease in tumour size and improvement in left ventricular ejection fraction. Read More

View Article
July 2018
2 Reads

Cardiac function in children with premature ventricular contractions: the effect of omega-3 polyunsaturated fatty acid supplementation.

Cardiol Young 2018 Jul 15;28(7):949-954. Epub 2018 May 15.

4Sifa University,Faculty of Medicine,Department of Pediatric Cardiology,Bornova,Izmir,Turkey.

Background: Premature ventricular contractions are accepted as benign in structurally normal hearts. However, reversible cardiomyopathy can sometimes develop. Omega-3 polyunsaturated fatty acids have anti-arrhythmic properties in animals and humans. Read More

View Article
July 2018
6 Reads

Reply to Robert Vincent.

Cardiol Young 2018 06 14;28(6):796. Epub 2018 May 14.

4Leeds Congenital Heart Unit,Leeds,UK.

View Article

Successful transcarotid transcatheter aortic valve replacement in a 34-kg patient with Schimke immuno-osseous dysplasia and severe biscuspid aortic stenosis.

Cardiol Young 2018 Jul 11;28(7):974-977. Epub 2018 May 11.

2Department of Cardiology,Mater Misericordiae University Hospital,Dublin,Ireland.

We present the case of transcatheter aortic valve replacement in a 20-year-old woman with severe bicuspid aortic stenosis and Schmike immuno-osseous dysplasia who was unfit for surgical aortic valve replacement. Meticulous pre-procedural planning and a multidisciplinary team approach can enable successful transcatheter aortic valve replacement in complex patients with genetic syndromes. Read More

View Article
July 2018
2 Reads

Efficacy of treatment with belladonna in children with severe pallid breath-holding spells.

Cardiol Young 2018 Jul 11;28(7):922-927. Epub 2018 May 11.

1Pediatric Department and Pediatric Cardiology Departments,St. Luc Hospital,Brussels,Belgium.

IntroductionPallid breath-holding spells are common and dramatic forms of recurrent syncope in infancy. They are very stressful despite their harmless nature and sometimes require treatment.

Objective: The objective of this study was to evaluate the efficacy of belladonna in severe breath-holding spells. Read More

View Article
July 2018
2 Reads

The development of a consensus-based nutritional pathway for infants with CHD before surgery using a modified Delphi process.

Cardiol Young 2018 Jul 29;28(7):938-948. Epub 2018 Apr 29.

7Faculty of Health Sciences,University of Southampton,Southampton,UK.

IntroductionDespite improvements in the medical and surgical management of infants with CHD, growth failure before surgery in many infants continues to be a significant concern. A nutritional pathway was developed, the aim of which was to provide a structured approach to nutritional care for infants with CHD awaiting surgery.Materials and methodsThe modified Delphi process was development of a nutritional pathway; initial stakeholder meeting to finalise draft guidelines and develop questions; round 1 anonymous online survey; round 2 online survey; regional cardiac conference and pathway revision; and final expert meeting and pathway finalisation. Read More

View Article
July 2018
2 Reads

Administrative health databases for addressing emerging issues in adults with CHD: a systematic review.

Cardiol Young 2018 Jun 29;28(6):844-853. Epub 2018 Apr 29.

1INSERM-UMRS 1138 Team 22,Cordeliers Research Center,Paris Descartes University,Paris,France.

The need for population-based studies of adults with CHD has motivated the growing use of secondary analyses of administrative health data in a variety of jurisdictions worldwide. We aimed at systematically reviewing all studies using administrative health data sources for adult CHD research from 2006 to 2016. Using PubMed and Embase (1 January, 2006 to 1 January, 2016), we identified 2217 abstracts, from which 59 studies were included in this review. Read More

View Article
June 2018
2 Reads

An unexpected case of post-operative superior caval vein syndrome.

Cardiol Young 2018 Jun 26;28(6):879-881. Epub 2018 Apr 26.

2Department of Anesthesiology,Lucile Packard Children's Hospital/Stanford University,Palo Alto,CA,USA.

Superior caval vein obstruction in children after congenital heart surgery has been more associated with thrombosis formation as result of single-ventricle palliation, infection, indwelling devices/catheters, or external compression. Many of these patients will present to the cardiac catheterisation laboratory for evaluation and possible intervention. We present an unusual case of superior caval vein obstruction in a patient after Tetralogy of Fallot repair. Read More

View Article
June 2018
1 Read

Safety of tracheal intubation in the presence of cardiac disease in paediatric ICUs.

Cardiol Young 2018 Jul 25;28(7):928-937. Epub 2018 Apr 25.

8Department of Anesthesiology and Critical Care Medicine,The Children's Hospital of Philadelphia,Philadelphia,PA,USA.

IntroductionChildren with CHD and acquired heart disease have unique, high-risk physiology. They may have a higher risk of adverse tracheal-intubation-associated events, as compared with children with non-cardiac disease.Materials and methodsWe sought to evaluate the occurrence of adverse tracheal-intubation-associated events in children with cardiac disease compared to children with non-cardiac disease. Read More

View Article
July 2018
3 Reads

Successful treatment of disseminated adenovirus infection with cidofovir and intravenous immunoglobulin in an infant following heart transplant.

Cardiol Young 2018 Jun 25;28(6):888-889. Epub 2018 Apr 25.

Pediatric Cardiology,Riley Hospital for Children,Indianapolis,IN,USA.

For most patients, adenoviruses cause few acute health concerns and are often self-limiting. Patients who are immunocompromised or immunosuppressed, however, are at risk for disseminated adenovirus and suffer high morbidity and mortality, without well-defined treatment options. We report the case of a 9-month-old boy who was successfully treated for disseminated adenovirus infection with intravenous immunoglobulin and cidofovir 3 months post heart transplant, tailored to serum adenoviral load and clinical response. Read More

View Article
June 2018
1 Read

A protocol to decrease postoperative chylous effusion duration in children.

Cardiol Young 2018 Jun 25;28(6):816-825. Epub 2018 Apr 25.

3Division of Pediatric Critical Care,University of Utah,Salt Lake City,UT,USA.

Objective: Our primary goal was to decrease time to resolution of postoperative chylothorax as demonstrated by total days of chest tube utilisation through development and implementation of a management protocol.

Methods: A chylothorax management protocol was implemented as a quality improvement project at a tertiary-care paediatric hospital in July, 2015. Retrospective analysis was completed on patients aged 0-17 years diagnosed with chylothorax within 30 days of cardiac surgery in a pre-protocol cohort (February, 2014 to June, 2015, n=20) and a post-protocol cohort (July, 2015 to March, 2016, n=22). Read More

View Article
June 2018
9 Reads

Appropriate Use Criteria for paediatric echocardiography in an outpatient practice: a validation study.

Cardiol Young 2018 Jun 25;28(6):862-867. Epub 2018 Apr 25.

1Department of Paediatrics, Johns Hopkins University,Baltimore,MD,USA.

Background: Although transthoracic echocardiography is the dominant imaging modality in CHD, optimal utilisation is unclear. We assessed whether adherence to the paediatric Appropriate Use Criteria for outpatient transthoracic echocardiography could reduce inappropriate use without missing significant cardiac disease.

Methods: Using the Appropriate Use Criteria, we determined the indication and appropriateness rating for each initial echocardiogram performed at our institution during calendar year 2014 (N=1383). Read More

View Article
June 2018
2 Reads

Deterioration of functional abilities in children surviving the Fontan operation.

Cardiol Young 2018 Jun 25;28(6):868-875. Epub 2018 Apr 25.

5Pediatric Rehabilitation,Glenrose Rehabilitation Hospital,University of Alberta,Edmonton,Canada.

Functional abilities are needed for activities of daily living. In general, these skills expand with age. We hypothesised that, in contrast to what is normally expected, children surviving the Fontan may have deterioration of functional abilities, and that peri-Fontan stroke is associated with this deterioration. Read More

View Article
June 2018
1 Read

Pulmonary atresia with intact ventricular septum and congenital left ventricular aneurysm.

Cardiol Young 2018 Jun 22;28(6):876-878. Epub 2018 Apr 22.

Johns Hopkins All Children's Hospital,Saint Petersburg,FL,USA.

Pulmonary atresia with intact ventricular septum and congenital left ventricular aneurysms are both rare, representing <1 and <0.1% of CHD, respectively. The association of left ventricular aneurysms and pulmonary atresia with intact ventricular septum has been documented in the literature, but all the previous case reports have involved children with acquired left ventricular aneurysms. Read More

View Article
June 2018
2 Reads

Three-dimensional echocardiographic evaluation of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome.

Cardiol Young 2018 Jun 22;28(6):885-887. Epub 2018 Apr 22.

3Pediatric Cardiology,Children's Hospital Colorado,University of Colorado School of Medicine,Aurora,CO,USA.

We report three-dimensional imaging of a rare finding of Ebstein's anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome, which has been previously reported only by two-dimensional echocardiography. A fetal echocardiogram was performed at 19 weeks that showed a moderately hypoplastic left ventricle, severely hypoplastic mitral valve, a severely hypoplastic aortic valve, and a dysplastic tricuspid valve. Post Caesarean delivery at 40 weeks of gestation, a transthoracic echocardiogram confirmed the findings seen on the fetal echocardiogram. Read More

View Article
June 2018
2 Reads

Left ventricular mass of persistent masked hypertension in Hong Kong Chinese adolescents: a 4-year follow-up study.

Cardiol Young 2018 Jun 22;28(6):837-843. Epub 2018 Apr 22.

1Department of Paediatrics,The Chinese University of Hong Kong,Hong Kong Special Administrative Region,Hong Kong,China.

Objective: In our previous study, the prevalence of childhood masked hypertension was 11%. This study aims to assess the left ventricular mass index of persistent masked hypertension and determine the factors of elevated left ventricular mass index in Hong Kong Chinese adolescents from a community cohort.

Design: Community prospective cohort study, follow-up of a case-control study in community. Read More

View Article
June 2018
3 Reads

Relationship between mean platelet volume-to-lymphocyte ratio and coronary artery abnormalities in Kawasaki disease.

Cardiol Young 2018 Jun 16;28(6):832-836. Epub 2018 Apr 16.

1Department of Pediatrics,University of Mersin Faculty of Medicine,Mersin,Turkey.

Objectives: Recently, mean platelet volume-to-lymphocyte ratio has emerged as a novel parameter of inflammation. No study has investigated the role of mean platelet volume-to-lymphocyte ratio in children with Kawasaki disease. We aimed to evaluate the relationship between mean platelet volume-to-lymphocyte ratio and coronary artery abnormalities in Kawasaki disease. Read More

View Article
June 2018
2 Reads

Large right ventricular sinusoids in an infant with aorta-left ventricular tunnel and proximal right coronary artery atresia.

Cardiol Young 2018 Jul 16;28(7):978-980. Epub 2018 Apr 16.

1Department of Congenital Heart Surgery,Texas Children's Hospital,Baylor School of Medicine,Houston,TX 77030,USA.

We report a 1-month-old infant diagnosed with an aorta-left ventricular tunnel, ventricular septal defect, and right coronary atresia with right ventricular sinusoids. The patient's anatomy and physiology did not indicate right-ventricular-dependent coronary circulation, and therefore right ventricular decompression could be performed without compromising coronary perfusion during surgical correction. A detailed understanding of the coronary anatomy is critical in managing this defect when coronary anomalies are present. Read More

View Article
July 2018
3 Reads

Radiofrequency catheter ablation for ventricular tachycardia in ischaemic cardiomyopathy due to Kawasaki disease.

Cardiol Young 2018 Jun 16;28(6):890-893. Epub 2018 Apr 16.

Department of Cardiology,Gifu University Graduate School of Medicine,Gifu,Japan.

In some patients with Kawasaki disease, a prior myocardial infarction causes ventricular tachycardia in the chronic post-myocardial infarction phase. We report the case of a 41-year-old man with symptomatic and haemodynamically unstable ventricular tachycardia in whom substrate ablation was performed for the ventricular tachycardia before insertion of an implantable cardioverter-defibrillator. Read More

View Article
June 2018
3 Reads

The Pediatric Heart Network Scholar Award programme: a unique mentored award embedded within a multicentre network.

Cardiol Young 2018 Jun 16;28(6):854-861. Epub 2018 Apr 16.

11Children's Hospital of Atlanta,Atlanta,GA,USA.

Background: The Pediatric Heart Network designed a career development award to train the next generation of clinician scientists in paediatric-cardiology-related research, a historically underfunded area. We sought to identify the strengths/weaknesses of the programme and describe the scholars' academic achievements and the network's return on investment.

Methods: Survey questions designed to evaluate the programme were sent to applicants - 13 funded and 19 unfunded applicants - and 20 mentors and/or principal investigators. Read More

View Article
June 2018
3 Reads

Quantitative assessment of the association between IL-10 -592 A/C polymorphism and Kawasaki disease risk in Chinese population: evidence from a meta-analysis.

Cardiol Young 2018 Jun 16;28(6):811-815. Epub 2018 Apr 16.

2Department of Clinical Laboratory,First Affiliated Hospital of Soochow University,Suzhou,People's Republic of China.

Background: IL-10, as a proinflammatory and anti-inflammatory cytokine, has been thought to have an important role in the development of Kawasaki disease. Variation in the IL-10 gene might lead to altered protein production, which may result in Kawasaki disease. Several studies have been performed to investigate the IL-10 -592 A/C polymorphism and Kawasaki disease risk. Read More

View Article
June 2018
3 Reads

Cardiac deformation parameters and rotational mechanics by cardiac magnetic resonance feature tracking in pre-adolescent male soccer players.

Cardiol Young 2018 Jun 21;28(6):882-884. Epub 2018 Mar 21.

2Department of Pediatric Radiology,Medical University of Warsaw,Warsaw,Poland.

The purpose of the study was to analyse whether prolonged and regular physical training in children leads to changes in myocardial systolic deformation and rotational mechanics. For that purpose, cardiac MRI feature tracking was performed retrospectively in 35 pre-adolescent male soccer players and 20 matched controls. There were no changes in global strain, but left ventricular twist and apical rotation were greater in soccer players, which adds to the features of paediatric athlete's heart. Read More

View Article
June 2018
3 Reads

Unmasking the borderline coarctation: the utility of isoproterenol in the paediatric cardiac catheterisation laboratory.

Cardiol Young 2018 Jun 14;28(6):804-810. Epub 2018 Mar 14.

3Divison of Pediatric Cardiology,University of California Davis Children's Hospital,Sacramento,CA,USA.

Background: One indication for intervention in coarctation of the aorta is a peak-to-peak gradient >20 mmHg. Gradients may be masked in patients under general anaesthesia and may be higher during exercise. Isoproterenol was given during cardiac catheterisation to simulate a more active physiologic state. Read More

View Article
June 2018
3 Reads

Recommendations for the configuration of a cardiac catheterisation laboratory for the treatment of children with CHD.

Cardiol Young 2018 Jun 9;28(6):791-794. Epub 2018 Mar 9.

4Leeds Congenital Heart Unit,Leeds,UK.

A modern catheter laboratory for the treatment of children with CHD should be in close proximity to the paediatric ICU, operating theatres, and imaging facilities. Space requirements and equipment for an up-to-date catheter laboratory are discussed. The document was endorsed by the council of the Association of European Paediatric and Congenital Cardiologists. Read More

View Article
June 2018
4 Reads

Validation of the Brief Developmental Assessment in pre-school children with heart disease.

Cardiol Young 2018 Apr;28(4):571-581

1Charles West Division,NHS Foundation Trust,Great Ormond Street Hospital,Great Ormond Street,London,United Kingdom.

Introduction The objective of this study was to prospectively validate the "Brief Developmental Assessment", which is a new early recognition tool for neurodevelopmental abnormalities in children with heart disease that was developed for use by cardiac teams.

Methods: This was a prospective validation study among a representative sample of 960 pre-school children with heart disease from three United Kingdom tertiary cardiac centres who were analysed grouped into five separate age bands.

Results: The "Brief Developmental Assessment" was successfully validated in the older four age bands, but not in the youngest representing infants under the age of 4 months, as pre-set validation thresholds were met - lower 95% confidence limit for the correlation coefficient above 0. Read More

View Article
April 2018
3 Reads

Rare presentation of Candida albicans: infective endocarditis and a pulmonary coin lesion.

Cardiol Young 2018 Apr;28(4):602-604

1Department of Pediatric Cardiology,Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital,Istanbul,Turkey.

We present a case of a rare association of infective endocarditis and a coin lesion in the lung caused by Candida albicans. The lesion disappeared after 6 weeks of treatment with 5 mg/kg/day amphotericin B. Read More

View Article
April 2018
2 Reads

Disopyramide use in infants and children with hypertrophic cardiomyopathy.

Cardiol Young 2018 Apr;28(4):530-535

Division of Cardiology,The Children's Hospital of Philadelphia,University of Pennsylvania Perelman School of Medicine,Philadelphia,PA,United States of America.

Hypertrophic cardiomyopathy has a range of clinical severity in children. Treatment options are limited, mainly on account of small patient size. Disopyramide is a sodium channel blocker with negative inotropic properties that effectively reduces left ventricular outflow tract gradients in adults with hypertrophic cardiomyopathy, but its efficacy in children is uncertain. Read More

View Article
April 2018
2 Reads

Transcatheter closure of ventricular septal defect with Occlutech Duct Occluder.

Cardiol Young 2018 Apr;28(4):598-601

Department of Pediatric Cardiology,Istanbul University Cerrahpaşa Medical Faculty,Istanbul,Turkey.

Patent ductus arteriosus occluders are used for transcatheter closure of ventricular septal defects, as well as for closure of patent ductus arteriosus. The Occlutech Duct Occluder is a newly introduced device for transcatheter closure of patent ductus arteriosus. Here, we present a case in which the Occlutech Duct Occluder was successfully used on a patient for the closure of a perimembraneous ventricular septal defect. Read More

View Article
April 2018
2 Reads

Involvement of patients and parents in research generated by the Australian and New Zealand Fontan Registry.

Cardiol Young 2018 04;28(4):522

Johns Hopkins All Children's Hospital,St. Petersburg,Florida,United States of America.

View Article
April 2018
5 Reads

Right ventricular pressure response to exercise in adults with isolated ventricular septal defect closed in early childhood.

Cardiol Young 2018 Jun 6;28(6):797-803. Epub 2018 Mar 6.

1Department of Paediatric Cardiology,Oslo University Hospital,Oslo,Norway.

We previously demonstrated an abnormally high right ventricular systolic pressure response to exercise in 50% of adolescents operated on for isolated ventricular septal defect. The present study investigated the prevalence of abnormal right ventricular systolic pressure response in 20 adult (age 30-45 years) patients who underwent surgery for early ventricular septal defect closure and its association with impaired ventricular function, pulmonary function, or exercise capacity. The patients underwent cardiopulmonary tests, including exercise stress echocardiography. Read More

View Article
June 2018
4 Reads

Cost-effectiveness of digoxin, pacing, and direct current cardioversion for conversion of atrial flutter in neonates.

Cardiol Young 2018 May 6;28(5):725-729. Epub 2018 Mar 6.

1Division of Pediatric Cardiology,The Congenital Heart Collaborative,UH Rainbow Babies and Children's Hospital,Cleveland,OH,USA.

IntroductionNewborn atrial flutter can be treated by medications, pacing, or direct current cardioversion. The purpose is to compare the cost-effectiveness of digoxin, pacing, and direct current cardioversion for the treatment of atrial flutter in neonates.Materials and methodsA decision tree model was developed comparing the efficacy and cost of digoxin, pacing, and direct current cardioversion based on a meta-analysis of published studies of success rates of cardioversion of neonatal atrial flutter (age<2 months). Read More

View Article
May 2018
4 Reads

Rationalising the use of cardiac catheterisation before Glenn completion.

Cardiol Young 2018 May 6;28(5):719-724. Epub 2018 Mar 6.

Pediatric Cardiology,Department of Pediatrics,UT Southwestern Children's Medical Center,Dallas,TX,USA.

Previous studies have shown that cardiac MRI can be used to evaluate the suitability for infants to undergo the Glenn operation after having undergone the Norwood procedure. We sought to analyse our institutional data retrospectively to identify whether such a policy would be advisable in the current era. We reviewed patients who underwent the Norwood procedure between 1 January, 2006 and 1 January, 2016. Read More

View Article
May 2018
5 Reads

Early childhood onset of high-grade atrioventricular block in Hunter syndrome.

Cardiol Young 2018 May 6;28(5):786-787. Epub 2018 Mar 6.

1Department of Pediatric Cardiology,Children's Mercy,Kansas City,MO,USA.

Cardiac involvement has been reported in various mucopolysaccharidoses syndromes. Cardiac valve pathology is the most prominent cardiac manifestation of patients with these syndromes. To date, there have been no reports of early childhood onset of high-grade atrioventricular block in patients with Hunter syndrome. Read More

View Article
May 2018
3 Reads

Coronary occlusion in a child masquerading as dilated cardiomyopathy: the sequelae of missed Kawasaki disease.

Cardiol Young 2018 May 5;28(5):773-775. Epub 2018 Mar 5.

Department of Pediatrics,Division of Pediatric Cardiology,College of Physicians & Surgeons,Columbia University Medical Center,New York,NY,USA.

If coronary artery sequelae are the only suggestive signs of previous Kawasaki disease, the diagnosis may easily be missed. We describe a rare case of a child with severe occlusive coronary disease likely owing to missed Kawasaki disease. This diagnosis was not initially considered given the age and absence of suggestive history. Read More

View Article
May 2018
6 Reads

Francis Fontan: an appreciation.

Cardiol Young 2018 05 1;28(5):788-789. Epub 2018 Mar 1.

Institute of Genetic Medicine,Newcastle University,Newcastle upon Tyne,UK.

View Article
May 2018
2 Reads