3,904 results match your criteria Budd-Chiari Syndrome


Significance of malondialdehyde, superoxide dismutase and endotoxin levels in Budd-Chiari syndrome in patients and a rat model.

Exp Ther Med 2018 Dec 9;16(6):5227-5235. Epub 2018 Oct 9.

Department of Magnetic Resonance Imaging, Shandong Medical Imaging Research Institute, Shandong University, Jinan, Shandong 250021, P.R. China.

Budd-Chiari syndrome (BCS) is a rare clinical syndrome caused by the obstruction of hepatic venous outflow. In theory, hepatic congestion and hypoxia induce pathological damage and changes in the liver. However, at present, laboratory evidence supporting this theory is lacking. Read More

View Article
December 2018

Diagnostic accuracy of magnetic resonance angiography for Budd-Chiari syndrome: A meta-analysis.

Exp Ther Med 2018 Dec 19;16(6):4873-4878. Epub 2018 Sep 19.

Department of Radiology, Affiliated Hospital of Xuzhou Medical University, Xuzhou, Jiangsu 221002, P.R. China.

In recent years, the role of magnetic resonance angiography (MRA) in the diagnosis of Budd-Chiari Syndrome (BCS) has been the focus of various clinical studies. The purpose of the present study was to perform a meta-analysis of the diagnostic performance of MRA in patients with BCS by using digital subtraction angiography as a reference method. The search strategy for relevant research articles was based on the Cochrane Handbook for Systematic Reviews, and literature databases (including PubMed, Medline and China National Knowledge Infrastructure) and reference lists of retrieved studies published from 2000 to 2016 were searched. Read More

View Article
December 2018

Epidemiology of Budd-Chiari syndrome: A systematic review and meta-analysis.

Clin Res Hepatol Gastroenterol 2018 Dec 7. Epub 2018 Dec 7.

Department of Gastroenterology, Northern Theater Command General Hospital (formerly General Hospital of Shenyang Military Area), Shenyang, Liaoning Province 110840, PR China. Electronic address:

Background And Aims: The global epidemiological data of Budd-Chiari syndrome (BCS) are scant. A systemic review and meta-analysis aimed to estimate the incidence and prevalence of BCS.

Methods: PubMed, EMBASE, and Cochrane Library databases were searched. Read More

View Article
December 2018

Changes in arterial oxygenation after portal decompression in Budd-Chiari syndrome patients with hepatopulmonary syndrome.

Eur Radiol 2018 Nov 30. Epub 2018 Nov 30.

Department of Interventional Therapy, National Cancer Center/National Clinical Research Center for Cancer/Cancer Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, 17 Panjiayuan Nanli, Chaoyang District, Beijing, 100021, China.

Objectives: To evaluate the changes in arterial oxygenation after portal decompression in Budd-Chiari syndrome (BCS) patients with hepatopulmonary syndrome (HPS).

Methods: From June 2014 to June 2015, all patients with BCS who underwent balloon angioplasty or transjugular intrahepatic portosystemic shunt (TIPS) creation at our institution were eligible for inclusion in this study. Arterial blood gas analysis was performed with the patient in an upright position and breathing room air at 2-3 days and 1 and 3 months after the procedure. Read More

View Article
November 2018
6 Reads

Intravenous Lymphatic Cyst in Inferior Vena Cava - A Rare Cause of Budd-Chiari Syndrome.

Ann Vasc Surg 2018 Nov 27. Epub 2018 Nov 27.

Department of Vascular Surgery, Peking University People's Hospital, Peking University Health Science Center, Peking University, Beijing, 100044, China. Electronic address:

A case with an extremely rare intravenous cystic lesion in suprahepatic inferior vena cava was reported, which originated from the lymphatic system and had induced Budd-Chiari syndrome. To the best of our knowledge, this is the first report of a benign cystic lesion originating from the wall of suprahepatic inferior vena cava that results in Budd-Chiari syndrome. Read More

View Article
November 2018
1 Read

Vascular Behçet's syndrome: an update.

Intern Emerg Med 2018 Nov 29. Epub 2018 Nov 29.

Department of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy.

Behçet's syndrome (BS) is a complex vasculitis, characterised by peculiar histological, pathogenetic and clinical features. Superficial venous thrombosis (SVT) and deep vein thrombosis (DVT) are the most frequent vascular involvements, affecting altogether 15-40% of BS patients. Atypical thrombosis is also an important clinical feature of BS, involving the vascular districts of the inferior and superior vena cava, suprahepatic veins with Budd-Chiari syndrome, portal vein, cerebral sinuses and right ventricle. Read More

View Article
November 2018
2 Reads

Anti-phospholipid Antibody Syndrome Presenting as Huge Ascites: A Case Report.

Mymensingh Med J 2018 Oct;27(4):883-887

Dr Abed Hussain Khan, Assistant Professor, Department of Internal Medicine, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Antiphospholipid Syndrome (APS) is characterized by arterial, venous or small vessel thromboses and/or pregnancy morbidity in the presence of persistently elevated titers of antiphospholipid antibodies. Since virtually any organ can be involved, the clinical presentation of APS is very varied. Abdominal manifestations are rare but may be life-threatening, and include Budd-Chiari Syndrome. Read More

View Article
October 2018
2 Reads

[Membranous occlusion of the inferior vena cava a rare cause of Budd-Chiari syndrome].

Rev Med Liege 2018 Nov;73(11):557-561

Service d'hépatologie, CHU de Liège, Belgique.

Rarely encountered in the Western countries, membranous occlusion of the inferior vena cava results from a fibrous thickening of the intima and is commonly located at the orifices of the hepatic veins. To date, two etiopathogenic hypotheses have been formulated: the first, dealing with the embryological aspect, the second, arguing for a thrombotic origin. Nevertheless, several studies are still underway to understand the exact physiopathological mechanism of this obstruction. Read More

View Article
November 2018
1 Read

Pediatric Budd-Chiari Syndrome: A Case Series.

Indian Pediatr 2018 Oct;55(10):871-873

Department of Pediatric Surgery, Lilavati Hospital and Research Centre, Mumbai, Maharashtra, India.

Objective: To study the diagnostic methods and treatment outcomes in children with Budd- Chiari syndrome.

Methods: Case records of 25 patients with Budd-Chiari syndrome were evaluated retrospectively. These patients were investigated with imaging techniques and underwent balloon angioplasty or surgical management. Read More

View Article
October 2018
8 Reads

Promising Advances in Budd-Chiari Syndrome in Children.

Indian Pediatr 2018 Oct;55(10):857-858

Department of General and Hepatobiliary Surgery, Mount Sinai Medical Center, Florida, USA.

View Article
October 2018
1 Read

Timing of Transjugular Intrahepatic Portosystemic Stent-shunt in Budd-Chiari Syndrome: A UK Hepatologist's Perspective.

J Transl Int Med 2018 Sep 9;6(3):97-104. Epub 2018 Oct 9.

Liver Unit, Queen Elizabeth Hospital, Birmingham, UK.

Budd-Chiari syndrome (BCS) is a rare but fatal disease caused by the obstruction in hepatic venous outflow tract (usually by thrombosis) and is further classified into two subtypes depending on the level of obstruction. Patients with BCS often have a combination of prothrombotic risk factors. Clinical presentation is diverse. Read More

View Article
September 2018
4 Reads

Transthoracic cholecystectomy following biliary pancreatitis arising from a thoracic herniated gallbladder.

J Visc Surg 2018 Dec 9;155(6):513-515. Epub 2018 Nov 9.

Department of HPB Surgery and Liver Transplant, Beaujon Hospital, Clichy, Université Paris VII Diderot, Assistance Publique-Hôpitaux de Paris, 100, boulevard du Général Leclerc, 92110 Clichy, Paris, France.

Asymptomatic right diaphragmatic rupture with liver and gallbladder herniation and secondary Budd-Chiari syndrome is a rare complication of abdominal trauma. In this setting, the management of gallbladder stones remains poorly described and may require a thoracic approach. Read More

View Article
December 2018
5 Reads

Excellent long-term outcomes of endovascular treatment in budd-chiari syndrome with hepatic veins involvement: A STROBE-compliant article.

Medicine (Baltimore) 2018 Oct;97(43):e12944

Department of Interventional Radiology, The First Affiliated Hospital of Zhengzhou University.

This study aimed to evaluate the long-term efficacy and safety of percutaneous transhepatic balloon angioplasty (PTBA) and transjugular intrahepatic portosystemic stent-shunt (TIPSS) in the treatment of Budd-Chiari syndrome (BCS) with hepatic veins involvement. Between June 2008 and August 2016, a total of 60 BCS patients with hepatic vein involvement in our department were enrolled in this study. Thirty-three cases underwent hepatic vein balloon angioplasty in PTBA Group and 27 cases underwent TIPSS. Read More

View Article
October 2018
4 Reads

Outcomes of endovascular interventional therapy for primary Budd-Chiari syndrome caused by hepatic venous obstruction.

Exp Ther Med 2018 Nov 7;16(5):4141-4149. Epub 2018 Sep 7.

Shandong Medical Imaging Research Institute, Shandong University, Jinan, Shandong 250021, P.R. China.

To date, interventional therapy for patients with Budd-Chiari syndrome (BCS) due to hepatic vein obstruction (HVO) has not been standardized in China. In Western countries, BCS primarily occurs due to thrombosis and the majority of patients receive thrombolysis. In China, BCS is mostly caused by the membranous occlusion of the HV or IVC. Read More

View Article
November 2018
1 Read

Use of Computed Tomography Volumetry to Assess Liver Weight in Patients With Cirrhosis During Evaluation Before Living-Donor Liver Transplant.

Exp Clin Transplant 2018 Nov 6. Epub 2018 Nov 6.

From the Department of Radiology, Baskent University Faculty of Medicine, Ankara, Turkey.

Objectives: Computed tomography liver volumetry has been widely used to detect total and segmental liver volume in living-donor liver transplantation. However, use of this technique to evaluate the cirrhotic liver remains unclear. In this study, we evaluated the accuracy of freehand computed tomography volumetry to assess total liver volume by comparing weights of total hepatectomy specimens in patients with cirrhosis. Read More

View Article
November 2018
6 Reads

Dilated abdominal veins from Budd-Chiari syndrome and caval obstruction.

Lancet Gastroenterol Hepatol 2018 Nov;3(11):812

Department of Gastroenterology and Liver Transplant Unit, Austin Health, Melbourne, VIC, Australia; Department of Medicine, University of Melbourne, Melbourne, VIC, Australia.

View Article
November 2018
1 Read

Radical surgical treatment of Budd-Chiari syndrome through entire exposure of hepatic inferior vena cava.

J Vasc Surg Venous Lymphat Disord 2018 Oct 16. Epub 2018 Oct 16.

Department of Vascular Surgery, Peking University People's Hospital, Beijing, China. Electronic address:

Objective: Therapies for Budd-Chiari syndrome (BCS) can be divided into three main categories: medical, endovascular, and surgical. Surgery is applicable to the disease when other therapeutic options have failed. We introduce a surgical method of recanalization through exposure of the entire hepatic inferior vena cava (IVC) and hepatic vein (HV) outflow tract for BCS and investigate the long-term outcomes. Read More

View Article
October 2018
4 Reads

Effects of low-dose energy spectrum scanning combined with adaptive statistical iterative reconstruction on the quality of imaging in Budd-Chiari syndrome.

PLoS One 2018 18;13(10):e0204797. Epub 2018 Oct 18.

Department of Radiology, First Affiliated Hospital of Zhengzhou University, Zhengzhou, Henan Province, China.

Objective: To assess the quality and diagnostic accuracy of monochromatic images combined with adaptive statistical iterative reconstruction (ASIR) performed via spectral computed tomography (CT) in patients with Budd-Chiari syndrome (BCS).

Methods: Sixty-two patients with BCS underwent pectral CT with upper abdominal two-phase contrast-enhanced scanning to generate a 60keV monochromatic energy level combined with ASIR (ranging from 0% -100%) during the portal venous phase (PVP) and the hepatic venous phase (HVP). One-way ANOVA was used to compare vessel-to-liver contrast-to-noise ratio (CNR) for the portal vein (PV), hepatic vein (HV), and inferior vena cava (IVC). Read More

View Article
October 2018
5 Reads

Spider's web sign: Budd-Chiari syndrome.

J Med Imaging Radiat Oncol 2018 Oct;62 Suppl 1:110

Department of Radiology, Concord Repatriation General Hospital, Concord, New South Wales, Australia.

View Article
October 2018
2 Reads

Hepatic Involvement in Systemic Sarcoidosis.

Am J Case Rep 2018 Oct 11;19:1212-1215. Epub 2018 Oct 11.

Department of Endocrinology, Springfield Clinic, Springfield, IL, USA.

BACKGROUND Sarcoidosis is a systemic disease that can affect any organ, including the liver. It is manifested by the presence of non-caseating granulomas within involved organs, most commonly the pulmonary, lymphatic, and hepatic system. Unlike pulmonary or lymphatic involvement, hepatic involvement is usually asymptomatic and it is underdiagnosed. Read More

View Article
October 2018
6 Reads

Budd-Chiari syndrome: a focussed and collaborative approach.

Hepatol Int 2018 Nov 8;12(6):483-486. Epub 2018 Oct 8.

Department of Hepatology, Institute of Liver and Biliary Sciences, D-1, Vasant Kunj, New Delhi, 110070, India.

View Article
November 2018
2 Reads

Liver transplantation for inferior vena cava leiomyosarcoma: from a Maslow's hammer to the Occam's razor.

BMJ Case Rep 2018 Sep 28;2018. Epub 2018 Sep 28.

Institute of Liver Disease & Transplantation, Gleneagles Global Health City, Chennai, Tamil Nadu, India.

Leiomyosarcoma (LMS) of primary vascular origin is a rare entity with only potentially curative option being complete surgical resection; despite which the prognosis remains dismal. Tumour recurrence is very common, and the benefits of adjuvant therapy are undefined. A 39-year-old woman presented with 6 months' history of abdominal pain, abdominal distension and pedal oedema. Read More

View Article
September 2018
3 Reads

Doppler ultrasound surveillance of TIPS-patency in the era of covered stents - retrospective analysis of a large single-center cohort.

Z Gastroenterol 2018 09 17;56(9):1053-1062. Epub 2018 Sep 17.

Medizinische Klinik I, Klinikum Ludwigsburg, Germany.

Purpose: The purpose of this study was to determine accuracy and necessity of long-term Doppler ultrasound (DU) surveillance of transjugular intrahepatic portosystemic shunt (TIPS) patency after implantation of an ePTFE-covered stent-graft (Viatorr).

Methods: This single-center retrospective study includes 228 consecutive cirrhotic patients with TIPS implantation due to portal hypertensive complications. Standardized DU surveillance was scheduled 3 - 5 days, 3 months, and 6 months after TIPS implantation and every 6 months thereafter. Read More

View Article
September 2018
2 Reads

Direct Intrahepatic Portosystemic Shunt in Budd-Chiari Syndrome: A Case Report and Review of the Literature.

Case Rep Radiol 2018 23;2018:9261268. Epub 2018 Aug 23.

Department of Radiology, Rutgers New Jersey Medical School, Newark, NJ, USA.

Transjugular intrahepatic portosystemic shunt (TIPS) is an alternative interventional procedure used to manage refractory Budd-Chiari syndrome (BCS) when conservative medical therapy has failed. However, TIPS is not always technically successful because of hepatic vein thrombosis and inability to catheterize the hepatic veins. In these situations, direct intrahepatic portosystemic shunt (DIPS) with access to the portal vein from the IVC has been shown to be a viable alternative that may ameliorate portal hypertension in these patients. Read More

View Article
August 2018
2 Reads

Thromboembolic disease in females and males aged 10 to 39 years in Germany.

Vasa 2018 Oct 11;47(6):483-489. Epub 2018 Sep 11.

1 Department of Angiology, Helios Klinikum Krefeld, Germany.

Background: We analysed differences in hospitalization rates for venous diseases such as pulmonary embolism (PE), deep vein thrombosis (DVT), sinus vein thrombosis (SVT), portal vein thrombosis (PVT), and Budd-Chiari syndrome (BCS) as well as for arterial diseases such as myocardial infarction (MI) and embolic stroke (ES) in females and males aged 10 to 39 years.

Patients And Methods: Detailed lists of hospitalizations with the principal and additional diagnoses for PE (ICD-code I26.0 + I26. Read More

View Article
October 2018
8 Reads

Efficacy of anti-TNF alpha in severe and refractory major vessel involvement of Behcet's disease: A multicenter observational study of 18 patients.

Clin Immunol 2018 Dec 18;197:54-59. Epub 2018 Aug 18.

APHP, Service de Médecine Interne et Immunologie clinique, Groupe Hospitalier Pitié Salpétrière Paris, France; DHU Inflammation, Immunopathologie, Biothérapie, Université Pierre et Marie Curie, Paris VI, France. Electronic address:

Objective: To describe the outcome and tolerance in patients treated with anti-TNFα in severe and refractory major vessel disease in Behçet's disease (BD).

Methods: A multicenter study evaluating 18 refractory BD patients with major vessel involvement [pulmonary artery (n = 4), aorta (n = 4) or peripheral artery aneurysm (n = 1) and/or pulmonary artery (n = 7), inferior vena cava (n = 5), or intra-cardiac (n = 3) thrombosis or Budd Chiari Syndrome (n = 2)] treated with anti-TNFα agents.

Results: Vascular remission was achieved in 16 (89%) patients. Read More

View Article
December 2018
3 Reads

A report on three patients with Echinococcus multilocularis: Lessons learned.

Indian J Gastroenterol 2018 Jul 18;37(4):353-358. Epub 2018 Aug 18.

Fortis Escorts Heart Institute, Okhla Road, New Delhi, 110 025, India.

Echinococcus multilocularis (EM) is the most virulent species of the genus Echinococcus. It causes a highly lethal helminthic disease in humans. The disease may present as hepatic mass mimicking a malignant neoplasm. Read More

View Article
July 2018
14 Reads

Clinical Efficacy of Spectral Computed Tomography for Evaluating Liver Function in Patients with Budd-Chiari Syndrome.

Acad Radiol 2018 Aug 9. Epub 2018 Aug 9.

Department of Radiology, The First Affiliated Hospital of Zhengzhou University, No.1, East Jianshe Road, Zhengzhou, Henan Province 450052, China. Electronic address:

Rationale And Objectives: To analyze the clinical relevance of quantitative spectral parameters in evaluating the treatment of patients with Budd-Chiari syndrome (BCS) with different classes of liver function by comparing normalized iodine concentration (NIC) before and after BCS treatment.

Materials And Methods: Angiographic data were obtained from 41 patients with confirmed BCS between December 2015 and March 2017. All patients underwent spectral computed tomography (CT) before and after BCS treatment; the average interval between scans was 2-4 months. Read More

View Article
August 2018
2 Reads

Surgical Techniques and Long-term Outcomes of Living-donor Liver Transplantation With Inferior Vena Cava Replacement Using Atriocaval Synthetic Interposition Graft for Budd-Chiari Syndrome.

Ann Surg 2018 Aug 3. Epub 2018 Aug 3.

Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Republic of Korea.

Objective: We aimed to describe our living-donor liver transplantation (LDLT) surgical technique and its long-term patency for patients with Budd-Chiari syndrome (BCS) and retrohepatic inferior vena cava (IVC) obstruction that extends up to the atrium.

Background: From a technical perspective, LDLT for BCS with an IVC obstruction up to the right atrium is one of the most challenging surgical procedures. Consequently, the optimal surgical technique for patients with BCS has not yet been elucidated. Read More

View Article
August 2018
5 Reads

Ultrasonography in Liver Vascular Disease.

Ultraschall Med 2018 Aug 2;39(4):382-405. Epub 2018 Aug 2.

Servicio de Radiodiagnóstico, Hospital Clinic, Barcelona, Spain.

Vascular liver diseases include a heterogeneous group of disorders affecting the micro- and the macro-circulation of the liver. Thrombosis and obstruction of the inflow (portal vein) and/or outflow venous system (Budd-Chiari syndrome), spontaneous porto-systemic shunts, diseases affecting the sinusoids, and hepatic vascular malformations are the most important vascular liver diseases. Thrombosis of the portal venous system and of the hepatic venous system occur most commonly and are potentially life-threatening conditions, while congenital and acquired pro-thrombotic diseases are major causal factors, together with local factors triggering thrombotic events. Read More

View Article
August 2018
2 Reads

Transjugular Intrahepatic Portosystemic Shunt (TIPS): Pathophysiologic Basics, Actual Indications and Results with Review of the Literature.

Rofo 2018 08 25;190(8):701-711. Epub 2018 Jul 25.

Department of Radiology, Medical School & Hospital, University of Bonn, Germany.

Background: Transjugular intrahepatic portosystemic shunt (TIPS) is a non-selective portosystemic shunt created using endovascular techniques. During recent years technical improvements and new insights into pathophysiology have modified indications for TIPS placement. In this article we therefore want to discuss current knowledge. Read More

View Article
August 2018
3 Reads

Long-term Outcomes of Endoluminal Sharp Recanalization of Occluded Inferior Vena Cava in Budd-Chiari Syndrome.

J Laparoendosc Adv Surg Tech A 2018 Jul 23. Epub 2018 Jul 23.

Department of Interventional Radiology, The First Affiliated Hospital of Zhengzhou University , Zhengzhou, China .

Purpose: To report the long-term results of endoluminal sharp recanalization of occluded inferior vena cava (IVC) in patients with the Budd-Chiari syndrome (BCS).

Patients And Methods: Seventy-two consecutive patients with BCS and IVC occlusion underwent endoluminal recanalization of the IVC occlusion during a 6-year period. BCS with occlusive IVC was detected by reviewing patient history and color Doppler ultrasonography. Read More

View Article
July 2018
2 Reads

Surgical Treatment of Pulmonary Complications in Behçet's Syndrome.

Semin Thorac Cardiovasc Surg 2018 Autumn;30(3):369-378. Epub 2018 Jul 19.

Division of Rheumatology, Department of Medicine, Cerrahpasa Medical Faculty, University of Istanbul, Istanbul, Turkey.

We described disease characteristics, management and outcome of a group of Behçet's syndrome (BS) patients who underwent pulmonary lobectomy, segmentectomy or various pleura interventions for complications due to pulmonary artery or descending aorta involvement. There were 9 patients with BS (8 M/1 F; mean age: 24.8 ± 7. Read More

View Article
July 2018
8 Reads

Hepatic vein stenting in a 7 week/old infant with Budd-Chiari syndrome using an anterograde approach from the inferior accessory hepatic vein.

Dig Liver Dis 2018 Nov 18;50(11):1246. Epub 2018 Jun 18.

Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IRCCS-ISMETT), Palermo, Italy.

View Article
November 2018

Transplant-free Survival in Chronic Liver Disease Presenting as Acute Liver Failure in Childhood.

Transplantation 2018 Jul 19. Epub 2018 Jul 19.

Paediatric Hepatology, Gastroenterology and Transplantation, Hospital Papa Giovanni XXIII Bergamo, Italy.

Background: in adults, the absence of a preexisting chronic liver disease (CLD) is required to diagnose acute liver failure (ALF). The paediatric classification does not considered this aspect, thus previous studies pooled together children with ALF and children with unknown CLD presenting with acute hepatic decompensation (ALF-CLD). We aimed to compare prevalence, features and outcome of children with ALF-CLD to those with a proper ALF. Read More

View Article
July 2018
10 Reads

Transjugular Intrahepatic Portosystemic Shunt Through the Strut of a Previously Placed Stent: Technical Feasibility and Long-Term Follow-Up Results.

Cardiovasc Intervent Radiol 2018 Nov 16;41(11):1794-1798. Epub 2018 Jul 16.

Department of Hepatology, Christian Medical College, Vellore, 632004, India.

Aims And Objectives: To evaluate technical feasibility, long-term primary patency and clinical outcome of the transjugular intrahepatic portosystemic shunt (TIPS) through the struts of the previously placed stents.

Materials And Methods: Retrospective evaluation of seven consecutive patients (three male and four female, age range 13-65 years, median 28) out of a total 95 patients, who underwent TIPS through the strut of the previously placed stents of hepatic vein (HV), inferior vena cava (IVC) or TIPS in a single tertiary care hospital. Six of the patients were diagnosed with Budd-Chiari syndrome (BCS) and one with alcohol-induced chronic liver disease (CLD). Read More

View Article
November 2018
3 Reads
1.970 Impact Factor

Budd-Chiari syndrome: imaging review.

Br J Radiol 2018 Dec 24;91(1092):20180441. Epub 2018 Jul 24.

2 Deapartment of Gastroenterology, Postgraduate Institue of Medical Education and Research , Chandigarh , India.

Budd-Chiari syndrome (BCS), also known as hepatic venous outflow tract obstruction includes a group of conditions characterized by obstruction to the outflow of blood from the liver secondary to involvement of one or more hepatic veins (HVs), inferior vena cava (IVC) or the right atrium. There are a number of conditions that lead to BCS-ranging from hypercoagulable states to malignancies. In up to 25% patients, no underlying disorder is identified. Read More

View Article
December 2018
5 Reads

Hypoxia-inducible Factor may Induce the Development of Liver Fibrosis in Budd-Chiari Syndrome by Regulating CD248/endosialin Expression: A Hypothesis.

J Transl Int Med 2018 06 26;6(2):66-69. Epub 2018 Jun 26.

Department of Gastroenterology, General Hospital of Shenyang Military Area, Shenyang, Liaoning Province, China.

Budd-Chiari syndrome (BCS) leads to the development of liver fibrosis in most of the cases. However, the mechanism of BCS-related liver fibrosis is unclear, and it may be largely different from that induced by chronic viral hepatitis. Hepatic stellate cell (HSC) and its specific marker CD248/endosialin are known to play an important regulatory role in the development of liver fibrosis. Read More

View Article
June 2018
4 Reads

Budd-Chiari syndrome has different presentations and disease severity during adolescence.

Hepatol Int 2018 Nov 3;12(6):560-566. Epub 2018 Jul 3.

Department of Gastroenterology, KEM Hospital and Seth GS Medical College, Multistory Building, 11th floor, Parel, Mumbai, Maharashtra, 400012, India.

There are limited data on clinical profile of adolescent patients with Budd-Chiari syndrome (BCS). We studied clinical, radiological, thrombophilia profile and treatment outcomes in adolescent patients with BCS.

Methods: Forty-three consecutive patients of BCS with onset of symptoms during adolescence (10-19 years) were enrolled in the study. Read More

View Article
November 2018
10 Reads

A Case of Live Donor Liver Transplantation in Acute-on-Chronic Liver Failure with Budd-Chiari Syndrome: Donor and Recipient with Antiphospholipid Antibody Syndrome.

Am J Case Rep 2018 Jun 30;19:767-772. Epub 2018 Jun 30.

Department of Hepatology, Gastroenterology and Hepatobiliary/Transplant Unit, Jordan Hospital, Amman, Jordan.

BACKGROUND Acute-on-chronic liver failure was first defined within the last 10 years as acute decompensation of chronic liver disease accompanied by multiorgan failure and poor outcome. Budd-Chiari syndrome is a rare and potentially deadly hepatic condition. To the best of our knowledge, this is the first case report of a live liver donor recipient with antiphospholipid antibody syndrome. Read More

View Article
June 2018
11 Reads

Pattern of Vascular Involvement in Egyptian Patients with Budd-Chiari Syndrome: Relation to Etiology and Impact on Clinical Presentation.

Ann Hepatol 2018 July - August ,;17(4):638-644

Department of Radiodiagnosis and Interventional Radiology, Ain Shams University, Cairo, Abbasia, Egypt.

Introduction And Aim: Budd-Chiari syndrome (BCS) is caused by hepatic venous outflow obstruction. This work aims to analyze the pattern of vascular involvement in Egyptian patients with BCS, demonstrates its relation to etiology and shows its impact on clinical presentation.

Material And Methods: The current retrospective study was conducted at The Tropical Medicine Department, Ain Shams University on one hundred Egyptian patients with confirmed diagnosis of primary BCS who were presented to the Budd-Chiari Study Group (BCSG) from April 2014 to May 2016 by collecting clinical, laboratory and radiological data from their medical records. Read More

View Article
June 2018
7 Reads

Transjugular intrahepatic portosystemic shunt for alveolar echinococcosis of the liver and Budd-Chiari syndrome.

Clin Res Hepatol Gastroenterol 2018 Sep 8;42(4):e61-e62. Epub 2018 Jun 8.

Claude-Bernard Lyon 1 university, Lyon, France; Department of digestive radiology, Edouard-Herriot hospital, Hospices civils de Lyon, Lyon, France.

View Article
September 2018
6 Reads

Pancreatic Cancer in Pregnancy Presenting with Thromboembolic Events: Case Report and Review of the Literature.

Gynecol Obstet Invest 2018 8;83(4):404-409. Epub 2018 Jun 8.

Division of Maternal Fetal Medicine, Department of Obstetrics and Gynecology, University of Colorado School of Medicine, Aurora, Colorado, USA.

Stroke and hepatic vein thrombosis are highly associated with neoplasia but are extremely rare events in young, pregnant women. Rare and recurrent thrombotic events in pregnancy increase the suspicion for occult malignancy. We describe the case of a healthy 31-year-old G2P1 who presented with visual changes and dysarthria during pregnancy. Read More

View Article
October 2018
15 Reads

Chronic Budd-Chiari syndrome.

CMAJ 2018 Jun;190(22):E689

Department of Cardiology (Singh), Dayanand Medical College and Hospital, Ludhiana, Punjab, India; Department of Cardiology (Srinivas), Sri Jayadeva Institute of Cardiovascular Sciences and Research, Bangalore, India.

View Article

Endovascular treatment for hepatic vein-type Budd-Chiari syndrome: effectiveness and long-term outcome.

Radiol Med 2018 Oct 31;123(10):799-807. Epub 2018 May 31.

Department of Radiology, Xuzhou Central Hospital, 199 South Jiefang Road, Xuzhou, Jiangsu, China.

Purpose: To determine the clinical effectiveness and long-term outcomes of endovascular treatment for hepatic vein (HV)-type Budd-Chiari syndrome (BCS).

Materials And Methods: From June 2011 to August 2016, 68 consecutive patients with symptomatic HV-type BCS underwent endovascular treatment in our center. Data on the baseline characteristics, technical success, clinical success, and long-term outcomes were collected and analyzed retrospectively. Read More

View Article
October 2018
2 Reads
1.370 Impact Factor

Doppler ultrasound in the diagnosis of Budd-Chiari syndrome in children after split liver transplantation.

Diagn Interv Imaging 2018 Oct 28;99(10):663-668. Epub 2018 May 28.

Department of Pediatric Radiology, Hôpital Timone-Enfants, 264, rue Saint-Pierre, 13005 Marseille, France.

Purpose: To assess the capabilities of a velocity ratio>3 for the diagnosis of Budd-Chiari syndrome (BCS) in children after split liver transplantation using Doppler ultrasonography (DUS).

Materials And Methods: A total of 28 children who underwent liver transplantation using a split procedure were included. There were 11boys and 17girls with a mean age of 3. Read More

View Article
October 2018

Percutaneous Transhepatic Hepatic Vein Angioplasty in Budd-Chiari Syndrome After Transvenous Failure.

J Laparoendosc Adv Surg Tech A 2018 Nov 31;28(11):1346-1351. Epub 2018 May 31.

1 Department of Interventional Radiology, The First Affiliated Hospital of Zhengzhou University , Zhengzhou, China .

Purpose: To evaluate the safety and efficacy of percutaneous transhepatic route creation for hepatic vein (HV) angioplasty in Budd-Chiari syndrome (BCS).

Patients And Methods: Between April 2012 and August 2016, a total of 19 BCS patients underwent percutaneous transhepatic route creation for HV angioplasty after transvenous catheterization failure in this study. Color Doppler ultrasonography was required in all patients after admission and during follow-up. Read More

View Article
November 2018
2 Reads

Comparison of retrievable stents and permanent stents for Budd-Chiari syndrome due to obstructive inferior vena cava.

J Gastroenterol Hepatol 2018 Dec 19;33(12):2015-2021. Epub 2018 Jun 19.

Department of Interventional Radiology, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, China.

Background And Aim: The aim of this study is to compare long-term outcomes of retrievable stents (RSs) and permanent stents (PSs) for Budd-Chiari syndrome (BCS) due to long-segment obstructive inferior vena cava (IVC).

Methods: Between July 2000 and August 2016, 42 patients with BCS due to long-segment obstructive IVC were treated with RSs, and 41 patients were treated with PSs. The RSs were removed eventually after thrombus disappeared. Read More

View Article
December 2018
5 Reads

Real-time shear wave elastography (SWE) assessment of short- and long-term treatment outcome in Budd-Chiari syndrome: A pilot study.

PLoS One 2018 30;13(5):e0197550. Epub 2018 May 30.

Department of Ultrasound, Chinese PLA General Hospital, Beijing, China.

Purpose: The first aim of this study was to analyze the relationships between liver stiffness measurement, hepatic venous pressure and liver fibrosis. The second aim was to demonstrate the utility of real-time shear wave elastography for evaluation of Budd-Chiari syndrome patients before and after balloon hepatic venous angioplasty.

Materials And Methods: A total of 32 patients with Budd-Chiari syndrome slated for successful balloon angioplasty met the inclusion and exclusion criteria. Read More

View Article
December 2018
4 Reads