1,907 results match your criteria Anomalous Pulmonary Venous Return


Mosaic Trisomy 12: Prenatal Diagnosis at Amniocentesis and Molecular Genetic Analysis on Fetal Tissues.

Fetal Pediatr Pathol 2020 Jul 1:1-7. Epub 2020 Jul 1.

Medical Genetics Laboratory, Azienda Unità Sanitaria Locale - IRCCS di Reggio Emilia, Reggio Emilia, Italy.

: Mosaic trisomy 12 is a genetic condition with few cases diagnosed prenatally and postnatally. Phenotypic variability is wide ranging from normal patients to severe congenital anomalies. A 35-year-old woman underwent amniocentesis at 17 weeks of gestation because of advanced maternal age. Read More

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http://dx.doi.org/10.1080/15513815.2020.1786199DOI Listing

A Heart Between 2 Swords.

J Cardiothorac Vasc Anesth 2020 Jun 3. Epub 2020 Jun 3.

Department of Pediatric Cardiology, National Heart Center, Royal Hospital, Muscat, Oman.

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http://dx.doi.org/10.1053/j.jvca.2020.05.037DOI Listing

Intraoperatory Diagnosis of Partial Anomalous Pulmonary Venous Return During Pulmonary Resection Surgery in a Non-Small Cell Lung Cancer Patient.

Arch Bronconeumol 2020 Jun 25. Epub 2020 Jun 25.

Servicio de Cirugía Torácica, Hospital Universitario Arnau de Vilanova, Lérida, España.

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http://dx.doi.org/10.1016/j.arbres.2020.05.023DOI Listing

Congenital extracardiac venous system anomaly in two siblings with normal karyotype and increased nuchal translucency thickness: a case report.

Oxf Med Case Reports 2020 Jun 13;2020(6):omaa034. Epub 2020 Jun 13.

Department of Obstetrics and Gynecology, Graduate School of Medicine, The University of Tokyo, Tokyo, Japan.

Previous studies have reported that congenital heart diseases (CHDs) develop in patients with genetic and environmental predisposition. Compared to CHDs, the significance of hereditary factors in the pathogenesis of congenital venous system anomalies remains unclear. Additionally, reports describing the pathogenic relationship between venous system anomalies and increased nuchal translucency (NT) are few. Read More

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http://dx.doi.org/10.1093/omcr/omaa034DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7293141PMC

Pumpless Lung Assist as a Bridge to Medical Therapy in a Teenager with Pulmonary Arterial Hypertension and Partial Anomalous Pulmonary Venous Return.

Can J Cardiol 2020 Jun 5. Epub 2020 Jun 5.

Departments of cardiac, thoracic and vascular surgery, centre de référence de l'Hypertension Artérielle Pulmonaire Sévère, groupe hospitalier Paris Saint-Joseph, hôpital Marie Lannelongue, Plessis-Robinson, Faculté de Médecine Paris-Saclay, Université Paris Sud, France; UMR-S 999, Inserm, France.

Heart failure is the main cause of death in patients with pulmonary arterial hypertension and congenital heart disease. We used an original approach in a 15-year-old girl with rapidly progressive right heart failure secondary to severe PAH and partial anomalous pulmonary venous return. After surgical CHD repair on cardiopulmonary bypass, she was weaned off bypass using a central Novalung® for 11 days then started on triple specific pulmonary vasodilator therapy. Read More

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http://dx.doi.org/10.1016/j.cjca.2020.06.001DOI Listing

Continuous real-time monitoring of pulmonary arterial pressure using a tip deflecting microcatheter in an infant with pulmonary arterial hypertension.

Cardiol Young 2020 Jun 2:1-3. Epub 2020 Jun 2.

Department of Pediatrics, Kyushu Hospital, Japan Community Healthcare Organization, Japan.

We present the case of a 3-month-old boy with pulmonary arterial hypertension after corrective repair of total anomalous pulmonary venous connection. The patient developed severe pulmonary arterial hypertension with a high mean pulmonary arterial pressure of 45 mmHg. We performed continuous monitoring of pulmonary arterial pressure using a tip deflecting microcatheter in the intensive care unit. Read More

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http://dx.doi.org/10.1017/S1047951120001286DOI Listing

Ebstein anomaly combined with unique pulmonary venous abnormality in a 9-month-old child.

Cardiol Young 2020 Jun 2:1-3. Epub 2020 Jun 2.

Division of Pediatric Cardiology, Department of Pediatrics, University of Arkansas for Medical Sciences and Arkansas Children's Research Institute, Little Rock, AR, USA.

Ebstein anomaly is a rare CHD known for its wide spectrum of presentation with the age of diagnosis dependent on the malformation's severity. Here, the authors describe a case of delayed diagnosis of Ebstein anomaly, secondary to lack of medical attention, which resulted in severe tricuspid regurgitation and pulmonary hypertension. Furthermore, the case was complicated by a unique pulmonary venous abnormality. Read More

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http://dx.doi.org/10.1017/S1047951120001249DOI Listing

Determination of anomalous pulmonary venous return with high-pitch low-dose computed tomography in pediatric patients.

Folia Morphol (Warsz) 2020 May 27. Epub 2020 May 27.

Background: In this study, we aimed to image pulmonary venous return anomalies and associated cardiovascular and pulmonary abnormalities by high-pitch low-dose computed tomography (CT) in children.

Materials And Methods: Forty-one patients with total or partial anomalous pulmonary venous return anomalous between May 2012 and June 2019 were retrospectively reviewed. The anomalies were determined using high-pitch low-dose CT. Read More

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http://dx.doi.org/10.5603/FM.a2020.0054DOI Listing

Sacrum agenesis and scimitar sacrum in Currarino syndrome.

Childs Nerv Syst 2020 Jul 24;36(7):1337-1338. Epub 2020 May 24.

Department of Radiology, Clínica de Diagnóstico por Imagem (CDPI)/DASA, Avenida das Américas, 4666, 302A, 303, 307, 325, 326, Barra da Tijuca, Rio de Janeiro, RJ, 2640-102, Brazil.

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http://dx.doi.org/10.1007/s00381-020-04653-zDOI Listing

Adults forms of scimitar syndrome.

J Card Surg 2020 May 22. Epub 2020 May 22.

Department of Cardiac Surgery, Mohamed 5 Military Hospital, Faculty of Medecine and Pharmacy, Rabat, Morocco.

Scimitar syndrome is a rare malformation defined as the partial or total anomalous pulmonary venous return of the right lung veins to the inferior vena cava just above or below the diaphragm. Severe forms of the disease are diagnosed in infancy and childhood. However, because of the mild form of the syndrome in adult patients, they remain asymptomatic and few cases are reported in the literature. Read More

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http://dx.doi.org/10.1111/jocs.14625DOI Listing

Pediatric Cardiology Specialist's Opinions Toward the Acceptability of Comfort Care for Congenital Heart Disease.

Pediatr Cardiol 2020 May 18. Epub 2020 May 18.

Center for Ethics, Children's Mercy Hospital, University of Missouri-Kansas City School of Medicine, Kansas City, MO, USA.

In order to evaluate physicians' willingness to seek legal action to mandate surgery when parents refuse surgery for various congenital heart lesions, we surveyed pediatric cardiologists and cardiovascular surgeons at 4 children's hospitals. We asked whether physicians would support parental refusal of surgery for specific heart defects and, if not, whether they would seek legal action to mandate surgery. We then analyzed associations between physicians' willingness to mandate surgery and national operative mortality rates for each lesion. Read More

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http://dx.doi.org/10.1007/s00246-020-02367-2DOI Listing

Scimitar Syndrome.

Eur Heart J Cardiovasc Imaging 2020 Mar 31. Epub 2020 Mar 31.

Department of Cardiovascular Medicine, Mayo Clinic, 200 1st St SW, Rochester, MN 55905, USA.

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http://dx.doi.org/10.1093/ehjci/jeaa061DOI Listing

A Very Rare Combination: two Scimitar Veins and a Myocardial Bridge.

Braz J Cardiovasc Surg 2020 Apr 1;35(2):229-231. Epub 2020 Apr 1.

Cardiovascular Associados Brasília Distrito Federal Brazil Cardiovascular Associados, Brasília, Distrito Federal, Brazil.

Scimitar syndrome is a rare congenital anomaly characterized by partial or complete anomalous pulmonary venous drainage of the right (rarely left) lung into the inferior vena cava. This anomalous vein resembles the curved Turkish sword "scimitar"[]. Only few cases were reported with two scimitar veins[]. Read More

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http://dx.doi.org/10.21470/1678-9741-2018-0240DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7199994PMC

Minimally invasive periareolar approach to repair sinus venosus atrial septal defect with partial anomalous pulmonary venous connection.

J Card Surg 2020 Apr 30. Epub 2020 Apr 30.

Division of Cardiac Surgery, Western University, London, Canada.

Background And Aim: Atrial septal defects with anomalous venous connections are commonly repaired via sternotomy, requiring careful baffle reconstruction to redirect pulmonary venous return and ensure a durable result. The cosmetically appealing periareolar incision may provide an esthetically superior alternative to the anterolateral minithoracotomy incision used in minimally invasive cardiac surgery.

Methods: We describe a patient with a sinus venosus atrial septal defect and partial anomalous pulmonary venous connection who underwent successful minimally invasive, endoscopic repair with apical vein translocation and autologous pericardial baffle reconstruction through a periareolar approach. Read More

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http://dx.doi.org/10.1111/jocs.14591DOI Listing

Early Outcomes for In-situ Pericardial Roll Repair for Distant Anomalous Pulmonary Venous Return.

Ann Thorac Surg 2020 Apr 24. Epub 2020 Apr 24.

Department of Thoracic and Cardiovascular Surgery, Cleveland Clinic Children's Hospital and Heart Vascular Institute, Cleveland Clinic Foundation, Cleveland, Ohio, USA.

Background: Repair of anomalous pulmonary venous return (APVR) when veins are remote from the left atrium (LA) is challenging, and may eventuate in a higher prevalence of pulmonary vein stenosis, superior vena cava (SVC) stenosis, or intracardiac baffle obstruction. We describe our experience in 6 patients with a technique, utilizing both anterior and posterior in-situ pericardial roll repairs, that reduce these complications.

Methods: Six patients underwent in-situ pericardial roll repair of (APVR) at Cleveland Clinic between 2018-2019. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2020.03.063DOI Listing

Meandering pulmonary veins: Two case reports.

Medicine (Baltimore) 2020 Apr;99(16):e19815

Department of Radiology, Institute of Health Sciences, Gyeongsang National University School of Medicine, Jinju.

Rationale: Meandering pulmonary vein is a rare congenital pulmonary vascular anomaly. It presents unilateral single pulmonary vein that takes a circuitous route in the lung and drains normally into the left atrium. Most cases of meandering pulmonary vein have been reported to be right-sided. Read More

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http://dx.doi.org/10.1097/MD.0000000000019815DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7220388PMC

Mustard Baffle Revision with Systemic Ventricular Assist Device Placement.

Ann Thorac Surg 2020 Apr 17. Epub 2020 Apr 17.

Duke Children's Pediatric & Congenital Heart Center, Division of Cardiovascular and Thoracic Surgery, Duke University Medical Center. Electronic address:

Patients with dextro-transposition of the great arteries (D-TGA) who have undergone atrial-level switch procedures often develop systemic right ventricle (RV) failure. An adult with D-TGA with Mustard repair in childhood presented with end-stage heart failure due to systemic RV failure, Mustard baffle leak, and unrepaired partial anomalous pulmonary venous return. She underwent device closure of the baffle leak via catheterization, followed by baffle revision and concomitant systemic ventricular assist device placement by adult and pediatric heart surgeons. Read More

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http://dx.doi.org/10.1016/j.athoracsur.2020.03.038DOI Listing

Structural and perfusion magnetic resonance imaging of congenital lung malformations.

Pediatr Radiol 2020 Jul 17;50(8):1083-1094. Epub 2020 Apr 17.

Department of Diagnostic Imaging, University Children's Hospital Zürich, Steinwiesstr. 75, CH 8032, Zürich, Switzerland.

Background: A radiation-free advanced imaging modality is desirable for investigating congenital thoracic malformations in young children.

Objective: To describe magnetic resonance imaging (MRI) findings of congenital bronchopulmonary foregut malformations and investigate the ability of lung MRI for their classification.

Materials And Methods: This is a retrospective analysis of consecutive MRI examinations performed for suspected congenital lung anomalies in 39 children (median age: 3. Read More

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http://dx.doi.org/10.1007/s00247-020-04658-5DOI Listing

Scimitar syndrome with an anomalous artery from the coeliac artery.

Eur Heart J 2020 May;41(18):1732

Department of Pediatric Cardiology, Hokkaido Medical Center for Child Health and Rehabilitation, 1-1-240-6, Kanayama, Teine-ku, Sapporo, Hokkaido 006-0041, Japan.

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http://dx.doi.org/10.1093/eurheartj/ehaa221DOI Listing

It is not asthma! An arcane case of 'Scimitar' syndrome: A case report.

Med J Malaysia 2020 03;75(2):184-185

Institute of Respiratory Medicine, Kementerian Kesihatan Malaysia, Kuala Lumpur, Malaysia.

'Scimitar' syndrome in adulthood is usually asymptomatic. Significant structural abnormalities symptoms usually manifest early during infancy or young childhood with features of congestive heart failure from significant shunting of the anomalous pulmonary venous drainage. Diagnosis of 'Scimitar' Syndrome in adults is rare and usually an incidental finding on chest radiograph. Read More

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[Scimitar syndrome in adulthood].

Aten Primaria 2020 Apr 7. Epub 2020 Apr 7.

Unidad de Investigación del Distrito Sanitario Aljarafe-Sevilla Norte, Sevilla, España; Departamento de Citología e Histología Normal y Patológica, Facultad de Medicina, Universidad de Sevilla, Sevilla, España. Electronic address:

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http://dx.doi.org/10.1016/j.aprim.2020.02.010DOI Listing

Early prenatal diagnosis of Scimitar syndrome.

Ultrasound Obstet Gynecol 2020 Mar 20. Epub 2020 Mar 20.

Neonatal Intensive Care Unit, Carmel Medical Center, Haifa, Israel.

Scimitar venous anomaly is a rare congenital vascular anomaly characterized by partial or complete anomalous venous return and extra cardiac findings. Several studies addressed the postnatal diagnosis of this anomaly, providing specific clinical clues and radiographic findings to confirm the diagnosis. However, reaching a diagnosis prenatally remains a challenge. Read More

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http://dx.doi.org/10.1002/uog.22015DOI Listing

Modified Warden Operation With the Use of Femoral Vein Homograft for Repair of a Variant of Right-Sided Partial Anomalous Pulmonary Venous Connection.

World J Pediatr Congenit Heart Surg 2020 Mar;11(2):217-219

Department of Cardiac Surgery, Children's National Health System, Washington, DC, USA.

Surgical repair of right-sided partial anomalous pulmonary venous return (PAPVR) involves baffling the pulmonary vein across a naturally occurring or surgically created atrial septal defect without causing pulmonary venous or superior vena cava obstruction. A nine-year-old male presented to us with an unusual anatomical variant of right-sided partial anomalous pulmonary venous connection. The pulmonary veins draining the right upper and middle lobes connected to the azygous vein that drained in the usual fashion into the superior vena cava. Read More

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http://dx.doi.org/10.1177/2150135119888219DOI Listing

Unusual association of transposition of great arteries with infradiaphragmatic pulmonary venous return.

Ann Pediatr Cardiol 2020 Jan-Mar;13(1):75-77. Epub 2019 Dec 4.

Department of Pediatric Sciences, Pediatric Cardiac Surgery Unit, Giovanni XXIII Pediatric Hospital, Bari, Italy.

A 21-day-old baby with transposition of the great arteries with intact ventricular septum, infradiaphragmatic totally anomalous pulmonary venous connection, and atrial septum defect underwent combined arterial switch operation, totally anomalous venous connection repair, and atrial septum defect closure, using a right-sided approach and temporary pulmonary veins occlusion, with no postoperative and 6-months follow-up complications. Complete anatomical correction is the most conceivable treatment for this unusual pathology; right-sided approach instead lifting the heart toward the right pleural cavity to perform left atrium-to-pulmonary veins anastomosis limits heart displacement and avoids nonphysiological three-dimensional alterations; moreover, ligation and division of vertical vein allow to obtain more tissue for anastomosis; temporary occlusion of pulmonary veins while performing anastomosis is a simple procedure that allows to avoid deep hypothermic circulatory arrest or low flow systemic perfusion. Combination of these details facilitates intra- and postoperative management, especially in combined demanding cases. Read More

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http://dx.doi.org/10.4103/apc.APC_54_19DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6979011PMC
December 2019

[Different surgical approaches to Scimitar syndrome].

Turk Kardiyol Dern Ars 2020 Jan;48(1):67-71

Department of Pediatric Cardiology, Tepecik Training and Research Hospital, İzmir, Turkey.

Scimitar syndrome is a rare congenital heart defect characterized by the combination of vascular, bronchial, and parenchymal malformations. This syndrome includes anomalous right pulmonary venous drainage to the inferior caval vein, hypoplastic right pulmonary artery, right lung hypoplasia and the presence of aortopulmonary collaterals to the right lung. In this study, we evaluate the different surgical approaches of 3 cases with Scimitar syndrome who was corrected successfully. Read More

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http://dx.doi.org/10.5543/tkda.2019.57510DOI Listing
January 2020

Percutaneous closure of an acquired and iatrogenic left ventricular-right atrium communication (Gerbode defect) with an Amplatzer Vascular Plug II.

J Cardiol Cases 2020 Jan 17;21(1):24-27. Epub 2019 Sep 17.

Pediatric Cardiology Department, Pediatric Specialties Hospital, Tuxtla Gutiérrez, Chiapas, Mexico.

Gerbode defect is defined as an abnormal left ventricle-right atrium shunting which may have congenital or acquired origin, first described by Thurman in 1838, representing 0.08% of intracardiac shunts and <1% of the congenital heart diseases. The acquired defect can be classified as iatrogenic or non-iatrogenic, with previous cardiac surgery being the most common cause. Read More

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http://dx.doi.org/10.1016/j.jccase.2019.09.008DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6951298PMC
January 2020

Unusual Course of Scimitar Syndrome Preceded by Lung Hypoplasia.

Case Rep Pediatr 2019 20;2019:8927243. Epub 2019 Dec 20.

Department of Neonatology, Ibaraki Children's Hospital, 3-3-1 Futabadai, Mito-city, Ibaraki 311-4145, Japan.

In patients with Scimitar syndrome, right pulmonary artery hypoplasia is considered to lead to right lung hypoplasia because of decrease in blood flow. However, there are no reports wherein the change was actually detected. Thus, the exact developmental mechanism of right pulmonary artery hypoplasia and right lung hypoplasia in patients with Scimitar syndrome is unclear. Read More

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http://dx.doi.org/10.1155/2019/8927243DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6939417PMC
December 2019

Airway anomalies in cases of anomalous pulmonary venous connection - A single-center experience.

Ann Card Anaesth 2020 Jan-Mar;23(1):14-19

Department of Cardiothoracic Surgery, SSSIHMS, Bengaluru, Karnataka, India.

Background: Patients with congenital heart defects may present with concomitant defects involving other organ systems. Roughly 4 percent of this nature are airway anomalies. Presence of anomalous airways summon major challenge before the anesthesiologist, surgeon, and intensivist in the perioperative management of such patients. Read More

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http://dx.doi.org/10.4103/aca.ACA_43_19DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7034199PMC
January 2020

A case report: a 22-year-old septic patient with central venous pO of 198 mmHg.

Eur Heart J Case Rep 2019 Dec 27;3(4):1-5. Epub 2019 Nov 27.

Institute of Radiology, University Hospital Zurich, Rämistrasse 100, 8091 Zurich, Switzerland.

Background: Central venous saturation and central venous pressure can be determined with central venous catheters. Therefore, the tip of the catheter should be located in the superior vena cava. The location can be monitored by electrocardiography or X-ray. Read More

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http://dx.doi.org/10.1093/ehjcr/ytz211DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6939803PMC
December 2019

Steroids as a possible effective therapy in the management of large isolated chylopericardium following open heart surgery.

Cardiol Young 2019 Dec;29(12):1426-1431

Division of Cardiology, Department of Pediatrics and Adolescent Medicine, American University of Beirut Medical Center, Beirut, Lebanon.

Background: Chylopericardium is the collection of lymph fluid inside the pericardial cavity. The incidence of chylopericardium is very low, as this diagnosis is rarely reported following cardiac procedures in children. While some reports were published worldwide on isolated chylopericardium after cardiac surgeries for diverse reasons, it has never been reported after repair for partial anomalous pulmonary venous return. Read More

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http://dx.doi.org/10.1017/S1047951119002889DOI Listing
December 2019

Corrigendum to "Pulmonary Hypertension Secondary to Partial Anomalous Pulmonary Venous Return in an Elderly Patient".

Case Rep Cardiol 2019;2019:2347179. Epub 2019 Nov 21.

University of Arizona, Tucson, AZ 85714, USA.

[This corrects the article DOI: 10.1155/2016/8609282.]. Read More

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http://dx.doi.org/10.1155/2019/2347179DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6906838PMC
November 2019

Total absence of the pericardium associated with hypogammaglobulinemia and bronchiectasis in a girl.

Pediatr Rep 2019 Dec 2;11(4):8250. Epub 2019 Dec 2.

Department of Pediatrics, Divisions of Pediatric Cardiology and Pulmonology, University Hospital Liège.

We report the case of an 8-years-old girl with recurrent pulmonary infections and wheezing since infancy, in whom asthma and immunoglobulin-G deficiency were diagnosed at the age of 7 months. Since then, the patient was treated for asthma without any satisfactory control of the disease. Cardiomegaly was finally diagnosed radiologically that led to cardiac assessment. Read More

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http://dx.doi.org/10.4081/pr.2019.8250DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6908960PMC
December 2019

Outcomes of the Warden Procedure for Partial Anomalous Pulmonary Venous Drainage.

Pediatr Cardiol 2020 Jan 6;41(1):134-140. Epub 2019 Dec 6.

Fuwai Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, No. 167, North Lishi Street, Xicheng District, Beijing, 100037, China.

Partial anomalous pulmonary venous drainage (PAPVD) is a common congenital heart disease. If the insertion of an anomalous pulmonary vein (PV) is high into the superior vena cava (SVC), the traditional 1-patch or 2-patch surgical repair might be challenging. Unlike patch procedures, the cavoatrial anastomosis technique (Warden procedure) theoretically reduces complications such as sinus node dysfunction and venous obstruction. Read More

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http://dx.doi.org/10.1007/s00246-019-02235-8DOI Listing
January 2020

Sinus Venosus Atrial Septal Defect: A Challenging Diagnosis.

Cureus 2019 Oct 17;11(10):e5936. Epub 2019 Oct 17.

Cardiology, Saint Mary's Hospital, Waterbury, USA.

Sinus venosus atrial septal defect (SVASD) is a rare adult congenital heart disease which permits shunting of blood from the systemic to the pulmonary circulation and is commonly associated with anomalous pulmonary venous return. We report a case of a 27-year-old man with a history of premature birth and unilateral cryptorchidism who was admitted for syncope. Electrocardiogram (ECG) demonstrated atrial fibrillation (AF)and S1Q3T3 pattern along with an incomplete right bundle branch block. Read More

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http://dx.doi.org/10.7759/cureus.5936DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6858266PMC
October 2019

Partial anomalous pulmonary venous connection detected during right pneumonectomy.

Interact Cardiovasc Thorac Surg 2020 03;30(3):497-498

Thoracic Surgery Department, Ankara University School of Medicine, Ankara, Turkey.

Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital anomaly. Generally, it is seen on the right side and is associated with an atrial septal defect. Herein, we present a case of a 50-year-old male patient with a supracardiac type PAPVC detected during pneumonectomy for a right hilar mass. Read More

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http://dx.doi.org/10.1093/icvts/ivz282DOI Listing

Currarino Triad: Importance of Preoperative Magnetic Resonance Imaging.

European J Pediatr Surg Rep 2019 Jan 22;7(1):e86-e89. Epub 2019 Nov 22.

Genetics Unit, Department of Pediatrics, Ain Shams University, Cairo, Egypt.

Currarino triad is a rare syndrome that may be occasionally encountered during managing cases of anorectal anomalies. The triad consists of anorectal anomaly, sacral bony defect, and a presacral mass. It may be familial or sporadic, with a reported female predominance. Read More

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http://dx.doi.org/10.1055/s-0039-3399533DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6874504PMC
January 2019

Trends in Infant Mortality After TAPVR Repair over 18 Years in Texas and Impact of Hospital Surgical Volume.

Pediatr Cardiol 2020 Jan 22;41(1):77-87. Epub 2019 Nov 22.

Division of Pediatric Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, Houston, TX, USA.

For some congenital heart lesions, higher institutional surgical volume has been associated with better survival than in lower volume centers. The relationship between institutional surgical volume and mortality in infants after total anomalous pulmonary vein return (TAPVR) repair has not been well explored. The Texas Inpatient Public Use Data File was queried for hospitalizations including TAPVR repair in infants between January 1, 1999 and December 31, 2016. Read More

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http://dx.doi.org/10.1007/s00246-019-02224-xDOI Listing
January 2020

Outcomes of hypoplastic left heart syndrome: analysis of National Inpatient Sample Database 1998-2004 versus 2005-2014.

Eur J Pediatr 2020 Feb 18;179(2):309-316. Epub 2019 Nov 18.

Department of Pediatric Critical Care, Cleveland Clinic Children's, 9500 Euclid Ave. M14, Cleveland, OH, 44195, USA.

Neonates with hypoplastic left heart syndrome (HLHS) were identified from the National Inpatient Sample dataset for the years 1998-2014. These patients were stratified into two chronological groups, past group (1998-2005) and recent group (2006-2014). A total of 20,649 neonates with HLHS were identified. Read More

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http://dx.doi.org/10.1007/s00431-019-03508-3DOI Listing
February 2020

Anesthetic Management of Right Single-lung Ventilation in a Patient with Anomalous Left Superior Pulmonary Venous Return for Left Pulmonary Lobectomy.

Cureus 2019 Sep 27;11(9):e5780. Epub 2019 Sep 27.

Anesthesiology, H. Lee Moffitt Cancer Center and Research Institute, Tampa, USA.

Partial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly in which one or more of the pulmonary veins are connected to the right atrium or to the systemic venous system. One lung ventilation (OLV) is required for a number of thoracic procedures. When switching to OLV, right-to-left shunt fraction increases, oxygenation is impaired, and hypoxemia may occur. Read More

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http://dx.doi.org/10.7759/cureus.5780DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6825499PMC
September 2019

Bronchopulmonary and vascular anomalies are frequent in children with oesophageal atresia.

Acta Paediatr 2020 Jun 11;109(6):1221-1228. Epub 2019 Dec 11.

Pediatric Pulmonology and Allergy Department, Pole Enfant, Jeanne de Flandre Hospital, CHU Lille, Univ. Lille, Lille, France.

Aim: Oesophageal atresia is frequently associated with other malformations, and our aim was to use computed tomography (CT) to explore intrathoracic malformations in patients with this condition.

Method: This was retrospective study of children aged 0-16 with oesophageal atresia who were born in 1996-2013 and followed up at the French reference centre for rare oesophageal diseases at the University of Lille. Computed tomography scans were available for 48 of the 234 patients during follow-up visits, and these were reviewed by a thoracic radiologist. Read More

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http://dx.doi.org/10.1111/apa.15086DOI Listing

Scimitar Syndrome: An Incidental Finding.

Indian J Pediatr 2020 02 9;87(2):165-166. Epub 2019 Nov 9.

Department of Pediatrics, Chacha Nehru Bal Chikitsalya, New Delhi, India.

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http://dx.doi.org/10.1007/s12098-019-03083-3DOI Listing
February 2020

Macrophage activation syndrome and pulmonary arterial hypertension in a patient with adult-onset Still disease: A case report.

Medicine (Baltimore) 2019 Nov;98(44):e17427

Department of Rheumatology and Immunology, Xiangya Hospital, The Institution of Rheumatology and Immunology.

Introduction: Macrophage activation syndrome (MAS) and pulmonary arterial hypertension (PAH) are rare and life-threatening complications of adult-onset Still disease (AOSD).

Patient Concerns: We reported an interesting case of a 25-year-old AOSD patient with MAS and PAH, and the patient was found to have right anomalous pulmonary venous connection accompanied by an atrial septal defect.

Diagnosis: MAS was diagnosed as a complication of AOSD. Read More

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http://dx.doi.org/10.1097/MD.0000000000017427DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6946370PMC
November 2019

Myocardial overexpression of ANKRD1 causes sinus venosus defects and progressive diastolic dysfunction.

Cardiovasc Res 2020 Jul;116(8):1458-1472

Department of Biomedical Sciences, University of Padua, 35121 Padua, Italy.

Aims: Increased Ankyrin Repeat Domain 1 (ANKRD1) levels linked to gain of function mutations have been associated to total anomalous pulmonary venous return and adult cardiomyopathy occurrence in humans. The link between increased ANKRD1 level and cardiac structural and functional disease is not understood. To get insight into this problem, we have generated a gain of function ANKRD1 mouse model by overexpressing ANKRD1 in the myocardium. Read More

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http://dx.doi.org/10.1093/cvr/cvz291DOI Listing

Abnormal arterial anatomy and an unexpected intracranial haemorrhage.

Authors:
Kieran Bannerman

Arch Dis Child Educ Pract Ed 2019 Oct 30. Epub 2019 Oct 30.

Neonatal Unit, Leeds General Infirmary, Leeds, UK

A baby boy was born at term by spontaneous vaginal delivery to non-consanguineous parents following an unremarkable pregnancy. He was admitted to his local neonatal intensive care unit shortly after birth following several episodes of eye-rolling, colour change and apnoea. He had bilateral parieto-occipital cephalohaematomata, scattered petechiae and intermittent hypotonia. Read More

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http://dx.doi.org/10.1136/archdischild-2019-317834DOI Listing
October 2019
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A situs solitus transposition of great arteries with obstructed sub-diaphragmatic totally anomalous pulmonary venous connection: a rare case treated with anatomical repair.

Cardiol Young 2019 Dec 30;29(12):1536-1538. Epub 2019 Oct 30.

Department of Paediatric Cardiology, Giovanni XXIII Paediatric Hospital, Bari, Italy.

Transposition of the great arteries combined with totally anomalous pulmonary venous connection is extremely rare outside of heterotaxy syndrome. Most reported cases have been treated by a modified atrial switch operation. We report the successful treatment of a neonate with this rare association, repaired by arterial switch operation and connection of the pulmonary venous return to the left atrium. Read More

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http://dx.doi.org/10.1017/S1047951119002415DOI Listing
December 2019

The Hypogenetic Lung (Scimitar) Syndrome.

Radiology 2019 12 29;293(3):522. Epub 2019 Oct 29.

From the Washington University School of Medicine in Saint Louis, Mallinckrodt Institute of Radiology, Campus Box 8131, 510 S Kingshighway Blvd, St Louis, MO 63110.

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http://dx.doi.org/10.1148/radiol.2019191540DOI Listing
December 2019

L-looped Transposition of the Great Arteries in a Patient with Marfanoid Habitus: First Reported Case in Literature.

Cureus 2019 Aug 18;11(8):e5416. Epub 2019 Aug 18.

Internal Medicine, Dow University of Health Sciences, Karachi, PAK.

L-looped transposition of great arteries (L-TGA) is an extremely rare heart condition. It is associated with physiologically corrected transposition of great vessels, leading to the normal return of deoxygenated systemic venous blood to the heart and transport of oxygenated pulmonary venous blood to the main systemic circulation. Anatomic discordancy and anomalous coronary artery distribution predispose the right ventricle to excessive workload and eventual heart failure. Read More

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http://dx.doi.org/10.7759/cureus.5416DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6795352PMC

Assessing the recently noted surgical outcome of isolated total anomalous pulmonary venous connection repair: A single-secondary center experience.

J Card Surg 2019 Dec 15;34(12):1526-1532. Epub 2019 Oct 15.

Department of Pediatrics, College of Medicine, Kangwon National University, Gangwon-do, Republic of Korea.

Background And Aim Of The Study: Total anomalous pulmonary venous connection (TAPVC) is a rare cyanotic congenital heart defect. This study aimed to evaluate the outcome of isolated TAPVC repairs and the prognoses of affected patients in the last 12 years at a single center.

Methods: We retrospectively analyzed the medical records of 51 patients who underwent isolated TAPVC repair from 2007 to 2018. Read More

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http://dx.doi.org/10.1111/jocs.14284DOI Listing
December 2019

Type A3 truncus arteriosus with infracardiac total anomalous pulmonary venous return and single ventricle physiology: A triad of tribulations.

J Cardiovasc Comput Tomogr 2019 Sep 23. Epub 2019 Sep 23.

Department of Cardiovascular Radiology & Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, 110029, India. Electronic address:

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http://dx.doi.org/10.1016/j.jcct.2019.09.006DOI Listing
September 2019
1 Read