2,025 results match your criteria Anomalous Pulmonary Venous Return

Mixed type TAPVR-Measure twice, cut once.

J Card Surg 2021 Jun 1. Epub 2021 Jun 1.

Division of Thoracic and Cardiovascular Surgery, Department of Surgery, University of Virginia, Charlottesville, Virginia, USA.

Total anomalous pulmonary venous return (TAVR) can have varying drainage configurations. Here, we review a report by Nagulakonda et al. to the Journal of Cardiac Surgery detailing how additional computed tomography imaging revealed a mixed type presentation of TAPVR not identified on echocardiography. Read More

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VATS right apical segmentectomy for lung cancer in a patient with tracheal bronchus.

Int J Surg Case Rep 2021 May 20;83:106007. Epub 2021 May 20.

Department of Surgery, Saiseikai Fukuoka General Hospital, 1-3-46 Tenjin, Chuo-ku, Fukuoka 810-0001, Japan.

Introduction: A tracheal bronchus is rarely observed, occurring in only 1% of all patients who undergo thoracic surgeries. We rarely encounter lung cancer in a patient with a tracheal bronchus; however, it is essential to know the distinctive perioperative management strategy for patients with a tracheal bronchus.

Case Presentation: We report a 72-year-old man with lung cancer located in the right apical segment supplied by a tracheal bronchus. Read More

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Effects of universal critical CHD screening of neonates at a mid-sized California congenital cardiac surgery centre.

Cardiol Young 2021 May 24:1-8. Epub 2021 May 24.

Division of Cardiology, Loma Linda University Children's Hospital, 11234 Anderson St, Loma Linda, CA92354, USA.

Introduction: CHD affects over 1 million children in the United States. Studies show decreased mortality from CHD with newborn cardiac screening. California began a screening programme on 1 July, 2013. Read More

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Hepatic pulmonary fusion: a rare case report.

Yewei Xie

Transl Pediatr 2021 Apr;10(4):1034-1038

Department of Pediatric Cardiothoracic Surgery, Shanghai Children's Hospital, Shanghai Jiao Tong University, Shanghai, China.

Hepatic pulmonary fusion (HPF) is a very rare congenital disease which is characterized by a fibrous connection between the liver and lung tissues. It is commonly associated with congenital diaphragmatic hernia (CDH), pulmonary sequestration, congenital heart disease and other diseases. Surgical operation has been reported to be the only option for the treatment of this disease. Read More

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Scimitar Syndrome Associated With Arterial Pulmonary Hypertension. Report a Case and Literature Review.

Curr Probl Cardiol 2021 Apr 3:100855. Epub 2021 Apr 3.

Neumology Service, Pulmonary Hypertension Clinic, Hospital General de Mexico "Dr.Eduardo Liceaga", Delegacion Cuauhtemoc, Ciudad de Mexico, Mexico.

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At the forefront of congenital cardiothoracic surgery: 2020-2021.

J Thorac Cardiovasc Surg 2021 Apr 20. Epub 2021 Apr 20.

Department of Cardiothoracic Surgery, University of Louisville and Norton Children's Hospital, Louisville, Ky.

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The sword and the shunt: Scimitar syndrome.

Lung India 2021 May-Jun;38(3):288-289

Department of Radiology, University of Texas Southwestern Medical Center at Dallas, Dallas, Texas, USA.

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Diaphragmatic eventration as a first sign of Scimitar syndrome.

Cardiol Young 2021 May 4:1-3. Epub 2021 May 4.

Neonatology Department, Hospital Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisboa, Portugal.

Diaphragmatic eventration is an anomaly of the diaphragm. In Scimitar syndrome, a curved-shaped anomalous pulmonary venous drainage is seen. Association between these conditions is rare. Read More

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A unique case of unilateral pulmonary edema from partial anomalous pulmonary venous return in conjunction with superior vena cava stenosis.

Clin Imaging 2021 Apr 28;79:110-112. Epub 2021 Apr 28.

NewYork Presbyterian Weill Cornell Medical Center, Department of Radiology, Cardiothoracic Imaging Division, 1300 York Avenue, New York, NY 10065, United States of America. Electronic address:

While PAPVR is most commonly an incidental finding on chest CT, a unique case is presented where PAPVR in conjunction with SVC stenosis resulted in chronic symptomatic asymmetric pulmonary edema. The case reflects an unusual anatomic cause of unilateral edema, as a combination of both congenital and subsequently acquired anatomic anomalies. Read More

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Repair of intracardiac total anomalous pulmonary venous return.

Multimed Man Cardiothorac Surg 2021 Mar 8;2021. Epub 2021 Mar 8.

Cardiology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.

Total anomalous pulmonary venous return is an uncommon congenital anomaly of the pulmonary venous system.  Excision of the common wall between the atrial septum and the coronary sinus and closure with a single patch is a popularly used technique to repair cardiac total anomalous pulmonary venous return. We have used the same approach in our patient: Our tutorial shows a simple method to divert pulmonary venous return into the mitral valve without causing damage to the internodal pathways. Read More

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Computed tomographic angiography (CTA) diagnosis of a rare meandering right pulmonary vein (MRPV).

Bruno Coulier

Surg Radiol Anat 2021 Apr 24. Epub 2021 Apr 24.

Department of Diagnostic Radiology, Clinique St Luc, Bouge, 5004, Namur, Belgium.

Meandering right pulmonary vein (MRPV) is an exceedingly rare congenital pulmonary vascular variant with less than 20 reported cases. MPVR is a tortuous aberrant venous drainage of the right pulmonary upper lobe anastomosing with the right lower pulmonary vein instead of directly joining the left atrium. The variant is benign with an orthotopic venous drainage without any kind of shunting. Read More

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Pulmonary-to-systemic venous collateral in obstructed supracardiac totally anomalous pulmonary venous connection: Blood finds a way!

J Card Surg 2021 Apr 16. Epub 2021 Apr 16.

Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.

We describe a rare variant of obstructed supracardiac totally anomalous venous connection in a 7-day-old boy where the vertical vein was occluded and the entire pulmonary venous return was draining through a large tortuous pulmonary-systemic venous collateral. The case highlights the importance of computed tomography angiography in demonstrating such complex anatomies in congenital heart diseases. Read More

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Repair technique for a rare partial anomalous pulmonary venous return associated with retroaortic innominate vein.

J Cardiothorac Surg 2021 Apr 15;16(1):83. Epub 2021 Apr 15.

Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital, Kyungpook National University School of Medicine, 41944, 130 Dongdeok-ro, Jung-gu, Daegu, Republic of Korea.

Background: Retroaortic innominate vein (RIV) is a rare vascular abnormality. Although RIV itself is asymptomatic, its presence in patients with partial anomalous pulmonary venous return (PAPVR) to the superior vena cava (SVC) is surgically challenging because a simple Warden procedure is impossible.

Case Presentation: A 16-year-old girl was diagnosed with tetralogy of Fallot, secundum, and sinus venosus atrial septal defect (ASD) at birth. Read More

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The Pulmonary Venous Return from Normal to Pathological-Clinical Correlations and Review of Literature.

Medicina (Kaunas) 2021 Mar 22;57(3). Epub 2021 Mar 22.

Department of Morpho-Functional Sciences I, Discipline of Histology, "Grigore T. Popa" University of Medicine and Pharmacy, Universității str 16, 700115 Iasi, Romania.

Pulmonary veins carry oxygenated blood from lungs to the left atrium of the heart. The anatomy of the pulmonary veins is variable with some anatomic variants. In clinical practice the difference between the normal anatomy of pulmonary veins with its variants and abnormal anatomy is very important for clinicians. Read More

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Heart transplantation in a case of scimitar syndrome.

Ann Thorac Surg 2021 Mar 29. Epub 2021 Mar 29.

Division of Congenital Heart Surgery, Texas Children's Hospital; Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX.

We present a rare clinical scenario of a patient with tetralogy of Fallot, hypertrophic cardiomyopathy, and concomitant scimitar syndrome. We created a scimitar vein cuff from a recipient heart, performed its translocation, and subsequently performed heart transplantation. This ingenuity reduces the likelihood of scimitar vein obstruction. Read More

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Multidisciplinary management of a rare case of mixed total anomalous pulmonary venous connection.

J Card Surg 2021 Jul 29;36(7):2562-2564. Epub 2021 Mar 29.

Division of Pediatric Surgery, Department of Emergencies and Organ Transplantation, University of Bari, Bari, Italy.

Introduction: Mixed total anomalous pulmonary venous connection (TAPVC) is a extremely rare congenital heart disease.

Methods: We report the initial management of a case of Mixed total anomalous pulmonary venous connection associated to right extralobar bronchopulmonary sequestration (BPS).

Results: Mixed TAPVC associated to right extra-lobar BPS was diagnosed at birth in a full-term newborn. Read More

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Tetralogy of Fallot with Scimitar Syndrome.

Radiol Cardiothorac Imaging 2020 Oct 8;2(5):e200253. Epub 2020 Oct 8.

Service of Cardiology, Hospital Nacional Dos de Mayo, Lima, Peru (D.I.K.T.); and Departments of Pediatric Cardiology (E.J.P.B.), Interventional Cardiology (J.A.G.M.), and Radiology, Service of Computed Tomography (M.J.S.), Instituto Nacional de Cardiología Ignacio Chávez, Juan Badiano 1, Col. Sección XVI, 14080 Mexico City, Mexico.

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October 2020

Surgical correction for scimitar syndrome by right thoracotomy and direct anastomosis in children.

Pediatr Investig 2021 Mar 22;5(1):46-51. Epub 2021 Mar 22.

Department of Cardiovascular Surgery II Beijing Children's Hospital Capital Medical University National Center for Children's Health Beijing China.

Importance: Scimitar syndrome (SS) is a rare type of congenital heart disease characterized by total or partial anomalous venous drainage of the right lung to the inferior vena cava. However, the surgical repair techniques for SS vary according to patients' anatomical and pathological features.

Objective: This study was performed to analyze the mid-term results of a less invasive surgical correction technique for SS in children. Read More

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A rare association of left pulmonary artery sling with Scimitar syndrome: Recurrent wheezing and respiratory distress in a pediatric patient.

Turk Gogus Kalp Damar Cerrahisi Derg 2021 Jan 13;29(1):105-109. Epub 2021 Jan 13.

Department of Cardiovascular Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.

Congenital anomalies of the heart and great vessels may lead to localized recurrent pulmonary infections through different mechanisms. Pulmonary artery sling (left pulmonary artery originating from the right pulmonary artery) and Scimitar syndrome are rare causes of wheezing in infants. An 18-month-old female infant with left pulmonary artery sling, Scimitar syndrome, and an anomalous connection of left pulmonary veins to the left atrium was admitted to our clinic. Read More

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January 2021

Rare malformations associated with partial anomalous pulmonary venous return: a cadaveric case report.

Folia Morphol (Warsz) 2021 Mar 22. Epub 2021 Mar 22.

Institute of Anatomy and Cell Biology, Paracelsus Medical University, Nuremberg, Germany.

A unique partial anomalous pulmonary venous return in combination with other rare malformations such as annular pancreas and a persistent umbilical vein was discovered in a female Caucasian cadaver during an anatomical dissection at the Paracelsus Medical University in Nuremberg, Germany. The pulmonary anomaly comprised of the aberrant left superior pulmonary vein connecting the superior lobe of the left lung with the left brachiocephalic vein resulting in a left to right shunt. An annular pancreas without any signs of probable symptom causing duodenal compression was additionally found. Read More

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Non-obstructed supracardiac total anomalous pulmonary venous connection with giant superior vena cava aneurysm.

BMC Surg 2021 Mar 17;21(1):136. Epub 2021 Mar 17.

Department of Cardiovascular Surgery, West China Hospital, Sichuan University, No.37 Guo Xue Alley, Chengdu, 610041, China.

Background: Giant superior vena cava (SVC) aneurysm in non-obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) is even more rare than in obstructed one, and this combination has not been reported.

Case Presentation: Here we reported a 29-year-old young lady with non-obstructed TAPVC complicated with a giant SVC aneurysm. Routine TAPVC correction and tricuspid valve repair were done. Read More

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Anomalous branch of right pulmonary artery supplying the left lung: A "pseudo-pulmonary sling".

J Card Surg 2021 Jun 17;36(6):2106-2107. Epub 2021 Mar 17.

Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.

We report a case of a 9-month-old boy with supracardiac total anomalous pulmonary venous connection showing a small aberrant vessel arising from the right pulmonary artery and traversing below the left main bronchus to supply the anteromedial segment of the left lower lobe. Read More

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Intravascular Ultrasound for Pulmonary Vein Stenosis Interventions in Congenital Heart Disease.

J Invasive Cardiol 2021 Apr 3;33(4):E259-E262. Epub 2021 Mar 3.

University of Arizona, Department of Pediatrics (Cardiology), 1501 N. Campbell Ave, P.O. Box 245073, Tucson AZ, 85724 USA.

Objective: Pulmonary vein stenosis (PVS) is aggressive, with high morbidity and mortality. Surgical and catheter interventions yield modest success, at best. Refinements in catheter interventions could potentially improve outcomes in this patient population. Read More

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The Lugones Procedure for Surgical Repair of Scimitar Syndrome: Preserved Growth in a Young Infant.

World J Pediatr Congenit Heart Surg 2021 Mar;12(2):284-285

Congenital Cardiac Surgery, Timone Hospital, 369900Assistance Publique-Hôpitaux de Marseille, France.

Surgical repair of Scimitar syndrome is challenging, especially in small patients. Our images demonstrate that the pericardial tunnel technique is feasible even in low-weight patient and that it provides a good growth potential. Read More

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Recurrent fibrovascular granulation on PhotoFix® bovine pericardium causing systemic and pulmonary venous obstruction after repair of scimitar syndrome.

Cardiol Young 2021 May 8;31(5):829-830. Epub 2021 Mar 8.

Division of Pediatric Cardiology, Department of Pediatrics, Stanford University School of Medicine, Palo Alto, CA, USA.

A young adult with late diagnosis of scimitar syndrome underwent infradiaphragmatic baffling of the scimitar vein to left atrium through an intra-atrial tunnel using PhotoFix® bovine pericardium with recurrent extensive fibrovascular granulation of the patch causing pulmonary and systemic venous obstruction leading to eventual explantation of the bovine pericardium. Read More

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A Rare Case of an Unroofed Coronary Sinus With a Persistent Left Superior Vena Cava Diagnosed by Two-Dimensional Transthoracic Echocardiography.

Cureus 2021 Jan 31;13(1):e13041. Epub 2021 Jan 31.

Cardiology, Smt. Nathiba Hargovandas Lakhmichand (NHL) Municipal Medical College, Ahmedabad, IND.

An unroofed coronary sinus is a rare congenital anomaly in the roof of the coronary sinus causing a communication between the coronary sinus and the left atrium leading to a left to right shunt. It is often associated with a persistent left superior vena cava and other complex congenital lesions like anomalous pulmonary venous return and heterotaxy. Since it is a deep-seated defect, it is seldom diagnosed by transthoracic two-dimensional (2D) echocardiography and requires multimodal imaging for a diagnosis. Read More

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January 2021

Multi-Modality Imaging Approach in a Challenging Case of Surgically Corrected Partial Anomalous Pulmonary Venous Return and Atrial Tachycardia Treated With Radiofrequency Ablation.

Cureus 2021 Jan 30;13(1):e13009. Epub 2021 Jan 30.

Radiology, Sant'Andrea Hospital - Sapienza University of Rome, Roma, ITA.

Pulmonary anomalous venous return (PAPVR) is defined as a congenital anomaly in which at least one but not all of the pulmonary veins abnormally drain into a systemic vein or directly into the right atrium. Signs and symptoms related to this condition are due to the hemodynamic abnormalities secondary to left-to-right shunt and the possible presence of other associated cardiac anomalies (e.g. Read More

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January 2021

Right mini-thoracotomy approach for grown-up congenital heart disease.

J Card Surg 2021 Jun 26;36(6):1917-1921. Epub 2021 Feb 26.

Department of Cardiovascular and Thoracic Surgery, Città della Salute e della Scienza, University of Turin, Torino, Italy.

Background: Right mini-thoracotomy cardiac surgery has been recognized as a safe and effective procedure, with remarkable early and long-terms outcomes. However, most of the literature is focused on mitral valve surgery and few studies report on the minimally invasive approach applied to congenital disease. Aim of this study was to review our experience on patients with grown-up congenital heart (GUCH) undergoing right mini-thoracotomy cardiac surgery. Read More

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Rev Esp Enferm Dig 2021 Feb 25. Epub 2021 Feb 25.

Aparato Digestivo, Hosptal Universitario Cruces.

Scimitar syndrome is a congenital malformation that usually associates hypoplasia of the right lung with abnormal blood supply to it by direct branches of the aorta. This branches normally require embolization. We present a case of a sixteen year old man with Scimitar syndrome. Read More

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February 2021