90 results match your criteria Angiokeratoma Circumscriptum


Linear lesions in Dermatology : a clinico-etio-pathological study.

Clin Exp Dermatol 2021 May 22. Epub 2021 May 22.

Department of Dermatology, Medical College and Hospital, Kolkata, West Bengal, India.

Background: Linear lesions are fairly common in our day to day practice. However, the appearances can be deceptive which puts dermatologists in a diagnostic dilemma.

Aims: To study the various clinical presentations, demographic profile of patients and clinico-pathological correlations of dermatoses presenting with a linear distribution. Read More

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Angiokeratoma Circumscriptum Naeviforme on Trunk.

J Cutan Med Surg 2021 May 12:12034754211016289. Epub 2021 May 12.

78595 Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi 110029, India.

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Angiokeratoma circumscriptum.

Dermatol Online J 2020 Nov 15;26(11). Epub 2020 Nov 15.

Department of Dermatology, Clinical University Hospital of Valencia, Valencia.

Angiokeratoma circumscriptum is the rarest variant of angiokeratoma. It usually affects females and it is characterized by dark-red to blue-black confluent papules or nodules on lower limbs in a segmental and unilateral distribution. We describe the clinical and histopathological findings in a patient with angiokeratoma circumscriptum and discuss the etiology, associations, diagnosis, differential diagnosis, and treatment. Read More

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November 2020

Angiokeratoma Circumscriptum on the Breast: A Case with Unusual Features.

Indian Dermatol Online J 2020 Jul-Aug;11(4):655-657. Epub 2020 Jul 13.

Department of Dermatology, Maulana Azad Medical College, Bahadur Shah Zafar Marg, Delhi, India.

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Klippel-Trenaunay Syndrome with Arterio-veno-lymphatic Malformation: A Rare Presentation.

Indian Dermatol Online J 2020 May-Jun;11(3):404-408. Epub 2020 May 10.

Department of Radiology, Government Medical College and Hospital, Nagpur, Maharashtra, India.

Klippel-Trenaunay syndrome (KTS) is a rare disorder characterized by triad of vascular malformations, varicose veins, and bony or soft tissue hypertrophy involving an extremity. Port wine stain is the most common vascular malformation associated with this syndrome. Various other rare vascular malformations described are angiokeratomas, angiokeratoma circumscriptum naeviformae, angiodermatitis, etc. Read More

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D-2-Hydroxyglutaric Aciduria with Enchondromatosis and Angiokeratoma Circumscriptum.

Cureus 2019 Nov 14;11(11):e6157. Epub 2019 Nov 14.

Dermatology, Oklahoma University Health Sciences Center, Oklahoma City, USA.

In this study, we report a four-year-old male with D-2-hydroxyglutaric aciduria (D2HA) and enchondromatosis with a prior history of hyperpigmented, segmental whorls and streaks on his abdomen who later presented with an eruption of angiokeratoma circumscriptum within a similar distribution. His condition can likely be explained by underlying somatic mosaicism; however, a unifying culprit gene mutation has not yet been identified. To date, only 10 reported cases of D2HA with enchondromatosis are available in the literature with three reported skin findings. Read More

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November 2019

A case report of adult-onset multiple angiokeratomas with zosteriform distribution.

Dermatol Online J 2018 Oct 15;24(10). Epub 2018 Oct 15.

Department of Dermatology, University of California Davis, Sacramento, California.

Angiokeratomas are benign vascular ectasias in the papillary dermis associated with epidermal changes in the form of hyperkeratosis and/or acanthosis. Clinically, angiokeratomas appear as solitary or multiple dark red to purple-black macules and/or papules, mostly with a verrucous surface. Five subtypes of angiokeratoma have been proposed - angiokeratoma corporis diffusum, angiokeratoma of Mibelli, angiokeratoma of Fordyce, angiokeratoma circumscriptum, and "solitary and multiple" angiokeratomas. Read More

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October 2018

Recurrent, nodular lesions over the vulva: A diagnostic challenge.

Indian J Sex Transm Dis AIDS 2018 Jul-Dec;39(2):124-126

Department of Dermatology, Father Muller Medical College, Mangalore, Karnataka, India.

Angiokeratomas are benign tumors characterized by proliferation and dilatation of blood vessels in the upper dermis. They are divided into widespread and localized forms. The localized forms are further classified as angiokeratoma of Fordyce, angiokeratoma circumscriptum neviforme, circumscribed angiokeratoma, and angiokeratoma of Mibelli, of which angiokeratoma of Fordyce is the most common. Read More

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January 2019

Verrucous hemangioma and histopathological differential diagnosis with angiokeratoma circumscriptum neviforme.

An Bras Dermatol 2018 Sep-Oct;93(5):712-715

Dermatology Department and Public Health Dermatology Outpatient Clinic, Porto Alegre, Rio Grande do Sul State Health Department, Porto Alegre (RS), Brazil.

Verrucous hemangioma is a rare vascular skin disorder with an immune profile similar to vascular neoplasms, but with behavior and evolution of vascular malformations. Its main differential diagnosis is angiokeratoma circumscriptum neviforme, with an almost indistinguishable clinical presentation because both diseases appear as erythematous patches that evolve to violaceous plaques, becoming scaly and even verrucous, most commonly affecting the lower limbs. Histopathology is crucial for the correct diagnosis: while in angiokeratoma the vascular alterations are limited to the papillary dermis, verrucous hemangioma extends deep into the dermis, reaching the subcutaneous tissue. Read More

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October 2018

[Angiokeratoma circumscriptum neviforme].

Ann Dermatol Venereol 2018 Aug - Sep;145(8-9):552-553. Epub 2018 Jul 21.

Service de dermatologie, GHR Mulhouse Sud-Alsace, 20, avenue Dr René-Laennec, 68100 Mulhouse, France.

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February 2019

Blaschko-linear "Congenital Mixed Hemato-lymphangio-keratoma Serpiginosum" Naeviforme: A New Hybrid Entity or Various Morphological Reflections of the Two Different Vascular Abnormalities?

J Clin Aesthet Dermatol 2018 May 1;11(5):43-47. Epub 2018 May 1.

Dr. Tas is with the Health Sciences University, Istanbul Bagcilar Research and Training Hospital, Department of Dermatology in Istanbul, Turkey.

We present the case of a 15-year-old girl who presented with an unusual grouping of lesions on her upper left leg. The lesions had been present since birth. The patient had five different types of lesions: 1) transparent grouped or scattered yellowish vesicles; 2) keratotic-surfaced, grouped dark-yellowish papules; 3) bright-red grouped papules; 4) keratotic-surfaced grouped dark-red papules; and 5) patchy, punctate, and erythematous red macules. Read More

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Multiple Verrucous Hemangiomas: A Case Report with New Therapeutic Insight.

Indian Dermatol Online J 2017 Jul-Aug;8(4):254-256

Department of Dermatology, Venereology and Leprosy, Post Graduate Institute of Medical Education and Research (PGIMER) and Dr. Ram Manohar Lohia Hospital, New Delhi, India.

Verrucous hemangioma is an uncommon congenital vascular malformation, which may clinically masquerade angiokeratoma, lymphangioma circumscriptum, or malignant melanoma. Differentiation is essential owing to varied therapeutic and prognostic implications. We present a rare case of multiple verrucous hemangiomas in a teenage girl who presented with multiple warty lesions over the dorsal aspect of the left foot since birth. Read More

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Utility and tolerability of the long-pulsed 1064-nm neodymium:yttrium-aluminum-garnet (LP Nd:YAG) laser for treatment of symptomatic or disfiguring vascular malformations in children and adolescents.

J Am Acad Dermatol 2017 Sep 1;77(3):473-479. Epub 2017 Jun 1.

Department of Dermatology, University of California, San Francisco, California. Electronic address:

Background: Vascular malformations manifest with pain, bleeding, disability, and disfigurement in a subset of children. There are scant data available on the utility and tolerability of laser surgery for symptomatic or disfiguring non-port-wine stain vascular malformations in children.

Objective: The objective of this study was to determine the utility and tolerability of the 1064-nm long-pulsed neodymium:yttrium-aluminum-garnet (LP Nd:YAG) laser for treatment of symptomatic or disfiguring vascular malformations in children. Read More

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September 2017

Sodium Tetradecyl Sulfate: A Review of Clinical Uses.

Dermatol Surg 2017 Nov;43(11):1313-1320

*University of Texas McGovern Medical School at Houston, Houston, Texas; †Department of Dermatology, University of Texas McGovern Medical School at Houston, Houston, Texas.

Background: Sodium tetradecyl sulfate (STS) is Food and Drug Administration approved for treatment of varicose veins, but numerous other off-label applications have been reported.

Objective: To describe the clinical uses of STS, as well as efficacy and adverse effects.

Methods: Review of studies searchable on PubMed from 1938 to 2016 describing clinical uses of STS to determine efficacy and adverse effects associated with various applications. Read More

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November 2017

Nonconventional Use of Flash-Lamp Pulsed-Dye Laser in Dermatology.

Biomed Res Int 2016 18;2016:7981640. Epub 2016 Aug 18.

Laser in Dermatology Unit, University of Rome "Tor Vergata", Rome, Italy.

Flash-lamp pulsed-dye laser (FPDL) is a nonablative technology, typically used in vascular malformation therapy due to its specificity for hemoglobin. FPDL treatments were performed in a large group of patients with persistent and/or recalcitrant different dermatological lesions with cutaneous microvessel involvement. In particular, 149 patients (73 males and 76 females) were treated. Read More

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February 2017

Successful treatment of angiokeratoma circumscriptum naeviforme with long pulse alexandrite laser.

J Eur Acad Dermatol Venereol 2017 Apr 26;31(4):e186-e187. Epub 2016 Aug 26.

Department of Dermatology, University Hospital of Nice, Nice, France.

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Breast Cancer Metastasis Misdiagnosed as an Angiokeratomatous Eruption. An Infrequent Presentation. Case Report.

Am J Dermatopathol 2016 Apr;38(4):302-4

*Dermatology Department, Faculty of Medicine, Pontificia Universidad Católica de Chile; †Dermatology Department, Sótero del Río Hospital Santiago, Chile; and ‡Pathology Department, Faculty of Medicine, Pontificia Universidad Católica de Chile.

Introduction: Cutaneous metastases represent 2% of all metastases. Breast cancer is the most common cause of skin metastases. Schwartz described 8 types of cutaneous breast metastases; one uncommon form is carcinoma telangiectodes (CT), which may resemble angiosarcoma or lymphangioma circumscriptum. Read More

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Extensive angiokeratoma circumscriptum - successful treatment with 595-nm variable-pulse pulsed dye laser and 755-nm long-pulse pulsed alexandrite laser.

J Cosmet Laser Ther 2016 Jun 8;18(3):134-7. Epub 2016 Mar 8.

c Institute of Pathological Anatomy, Commenius University , Bratislava , Slovak Republic.

Angiokeratomas are rare vascular mucocutaneous lesions characterized by small-vessel ectasias in the upper dermis with reactive epidermal changes. Angiokeratoma circumscriptum (AC) is the rarest among the five types in the current classification of angiokeratoma. We present a case of an extensive AC in 19-year-old women with Fitzpatrick skin type I of the left lower extremity, characterized by a significant morphological heterogeneity of the lesions, intermittent bleeding, and negative psychological impact. Read More

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Angiokeratomas Scroti Associated with Angiokeratomas of the Eyelids: Coincidence or One Entity? A Case Report and Review of the Literature.

Dermatology 2015 24;231(3):213-6. Epub 2015 Jul 24.

Department of Dermatology, University Hospital of Basel, Basel, Switzerland.

We describe a unique patient with multiple angiokeratomas on both upper eyelids and on the scrotum. We review the literature and discuss the pathogenetic relationship. Angiokeratomas are described as vascular lesions, which are defined histologically as one or several dilated blood vessel(s) covered by a keratotic layer. Read More

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Capillary malformations: a classification using specific names for specific skin disorders.

Authors:
R Happle

J Eur Acad Dermatol Venereol 2015 Dec 10;29(12):2295-305. Epub 2015 Apr 10.

Department of Dermatology, Freiburg University Medical Center, Freiburg, Germany.

The name capillary malformation has caused much confusion because it is presently used to designate numerous quite different disorders such as naevus flammeus, the salmon patch, the vascular naevus of the hereditary 'megalencephaly-capillary malformation syndrome' and the skin lesions of non-hereditary traits such as 'capillary malformation-arteriovenous malformation' and 'microcephaly-capillary malformation'. To avoid such bewilderment, the present review describes the distinguishing clinical and genetic criteria of 20 different capillary malformations, and a specific name is given to all of them. The group of capillary naevi includes naevus flammeus, port-wine naevus of the Proteus type, port-wine naevus of the CLOVES type, naevus roseus, rhodoid naevus, cutis marmorata telangiectatica congenita, congenital livedo reticularis, segmental angioma serpiginosum, naevus anaemicus, naevus vascularis mixtus and angiokeratoma circumscriptum. Read More

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December 2015

Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?

Indian Dermatol Online J 2014 Dec;5(Suppl 2):S109-12

Department of Radiology, Government Medical College and Hospital, Nagpur, Maharashtra, India.

Klippel-Trenaunay syndrome (KTS) is a cutaneous capillary malformation on a limb in association with soft tissue swelling with or without bony hypertrophy and atypical varicosity. The capillary malformation associated with KTS is port wine stain. Angiokeratoma circumscriptum naeviforme (ACN) is a congenital variant of angiokeratoma commonly present on the lower limb as a hyperkeratotic plaque. Read More

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December 2014

Angiokeratoma circumscriptum neviforme: An entity, few and far between.

Indian Dermatol Online J 2014 Oct;5(4):472-4

Department of Dermatology, Medical College and Hospital, Kolkata, West Bengal, India.

Angiokeratomas are a group of vascular ectasias that involve the papillary dermis and may produce papillomatosis, acanthosis and hyperkeratosis of the epidermis. Angiokeratoma circumscriptum is the least common variant among many types. Angiokeratoma circumscriptum neviforme is a still rarer variety of angiokeratoma, which is classically seen at birth. Read More

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October 2014

Angiokeratoma circumscriptum of the buccal mucosa: a case report and literature review.

J Korean Assoc Oral Maxillofac Surg 2014 Oct 24;40(5):240-5. Epub 2014 Oct 24.

Department of Oral and Maxillofacial Surgery, Gyeongsang National University School of Medicine, Jinju, Korea.

Angiokeratoma is a benign cutaneous lesion of the capillaries, presenting as dilated vessels in the upper part of the dermis. Although this disorder is classified into various types and has been occasionally reported in the skin of the scrotum or extremities, the involvement of the oral cavity mucosa has been rarely reported. The present study reports a case of angiokeratoma circumscriptum in the buccal mucosa. Read More

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October 2014

Late onset palmar angiokeratoma circumscriptum: An unusual presentation.

Indian Dermatol Online J 2014 Jul;5(3):320-2

Department of Dermatology, Venereology and Leprosy, Mahatma Gandhi Mission's Medical College, Navi Mumbai, India.

Angiokeratomas (AK) are a group of capillary vascular malformations encompassing several unrelated conditions, predominantly seen on the lower extremities. AK can be classified into localized and diffuse forms. The diffuse forms comprise Fabry's disease, which is the result of α-galactosidase deficiency. Read More

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Angiokeratoma circumscriptum: dilemma in diagnosis.

Indian J Pathol Microbiol 2014 Apr-Jun;57(2):350-1

Department of Dermatology, Dr. Panjabrao Deshmukh Memorial Medical College, Amravati, Maharashtra, India.

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Lymphangioma circumscriptum, angiokeratoma, or superficial vascular ectasia with epithelial hyperplasia?

Oral Surg Oral Med Oral Pathol Oral Radiol 2014 Aug 6;118(2):e53-7. Epub 2013 Dec 6.

Professor, Department of Oral Pathology, Faculty of Dentistry, National and Kapodistrian University of Athens, Athens, Greece.

We report a case of lymphangioma circumscriptum (cavernous lymphangioma with epithelial hyperplasia) in a 12-year-old girl, presenting as a papillary tumor on the right dorsal side of her tongue. Microscopic examination found cavernous vascular channels lined by a single layer of CD31(+), podoplanin-positive, CD34(-) endothelial cells that occupied the papillary lamina propria and were accompanied by epithelial hyperplasia. A review of the literature on oral vascular tumors with epithelial hyperplasia, namely, lymphangioma circumscriptum and angiokeratoma, provided information that draws into question the use of these terms. Read More

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Angiokeratoma circumscriptum in a young male.

Indian J Dermatol 2014 Jan;59(1):85-7

Department of Surgery, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.

A 20-year-old male presented with multiple eruptions on his right leg since birth; these bled and were painful on trivial trauma. Examination revealed dark brown, hyperkeratotic, indurated, verrucous linear plaques with irregular borders. Histopathological evidence of hyperkeratosis, acanthosis, and extensive vascular proliferation in papillary dermis confirmed clinical suspicion of angiokeratoma circumscriptum (AKC). Read More

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January 2014

Development of hemangioma in a tongue harboring long-standing angiokeratoma circumscriptum.

Ear Nose Throat J 2012 Nov;91(11):E7-E10

Division of Head and Neck Oncology, Jewish General Hospital, 3755 Cote Ste. Catherine Rd., Montreal, QC H3T 1E2, Canada.

Angiokeratoma is a very rare vascular lesion of the papillary dermis. It is characterized by vascular ectasia with overlying epidermal hyperkeratosis. The systemic form of angiokeratoma is associated with Fabry disease and fucosidosis. Read More

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November 2012

[A new location of angiokeratoma circumscriptum].

Ann Dermatol Venereol 2012 Nov 31;139(11):732-5. Epub 2012 Aug 31.

Service de dermatologie, faculté de médecine et de pharmacie, université Mohammed V, Souissi, Maroc.

Background: Angiokeratomas are papular telangiectasias having a common histology of ectasia of the superficial dermal vessels surmounted by a hyperkeratotic epidermis.

Patients And Methods: The patient was a 9-year-old girl born of non-consanguineous parents after a well-followed pregnancy with problem-free delivery at term. From birth, she had a tumefaction of the left side of the nose and the left half of the upper lip that gradually increased in size without obstructing the nasal orifice and bled easily. Read More

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November 2012