J Thromb Haemost 2018 Jun 19. Epub 2018 Jun 19.
Department of Clinical Chemistry and Haematology, University Medical Center Utrecht, Utrecht, the Netherlands.
The plasma contact system contributes to thrombosis in experimental models. Even though our standard blood coagulation tests are prolonged when plasma lacks contact factors, this enzyme system appears to have a minor (if any) role in haemostasis. In this review, we will explore the clinical phenotype of C1 esterase inhibitor (C1-INH) deficiency. Read More