A case of Hutchinson-Gilford progeria syndrome mimicking scleredema in early infancy.

Authors:
E Osma
E Osma
Dokuz Eylül University
Turkey

Dermatology 1994 ;188(4):318-21

Department of Pediatrics, Faculty of Medicine, Dokuz Eylul University, Izmir, Turkey.

We report a case of Hutchinson-Gilford progeria syndrome (HGPS). The patient showed the characteristics of scleredema at the age of 2.5 months but developed all the manifestations of HGPS gradually until 10 months old. The possibility of development of HGPS should by considered in any case of scleredema at birth or in early infancy.

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http://dx.doi.org/10.1159/000247175DOI Listing
June 1994
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