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    A case of Hutchinson-Gilford progeria syndrome mimicking scleredema in early infancy.
    Dermatology 1994 ;188(4):318-21
    Department of Pediatrics, Faculty of Medicine, Dokuz Eylul University, Izmir, Turkey.
    We report a case of Hutchinson-Gilford progeria syndrome (HGPS). The patient showed the characteristics of scleredema at the age of 2.5 months but developed all the manifestations of HGPS gradually until 10 months old. The possibility of development of HGPS should by considered in any case of scleredema at birth or in early infancy.

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    Department of Pathology, University of South Florida and Tampa General Hospital, Florida 33601, USA.
    Hutchinson-Gilford progeria syndrome is an extremely rare condition with features of premature and accelerated aging. The pattern of inheritance if unclear, although both autosomal recessive and autosomal dominant modes have been proposed. The children usually present in late infancy and early childhood with a characteristic phenotype of alopecia; short stature; abnormal skin, teeth, and nails; beaked nose; loss of subcutaneous fat; and failure to thrive. Read More
    The Hutchinson-Gilford Progeria Syndrome: a case report.
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