IgG4-Related Skin Disease Presenting as a Pseudolymphoma in a White Adolescent Girl.

Am J Dermatopathol 2019 Feb 26. Epub 2019 Feb 26.

Department of Pathology, University of Virginia School of Medicine, Charlottesville, VA.

Immunoglobulin gamma (Ig) type 4-related disease (IgG4-RD) is a chronic immunologic systemic disorder that has gained worldwide recognition in the past decade. This entity can affect almost every organ system, and its characteristic lesions have been found in a variety of organs such as lacrimal and salivary glands, pancreas, liver, bile ducts, lungs, kidneys, retroperitoneum, breast, aorta, thyroid, and prostate. This case reports a very rare case of IgG4-RD presenting with a cutaneous lesion in a young female patient mimicking a lymphoproliferative disorder. IgG4-RD affecting the skin is a rare entity and has mostly been reported in Japanese men of middle to older age. IgG4-RD with cutaneous involvement should be in the differential of non-neoplastic, lymphomas, autoimmune, and infectious disorders of the skin.

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http://Insights.ovid.com/crossref?an=00000372-900000000-9818
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http://dx.doi.org/10.1097/DAD.0000000000001401DOI Listing

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February 2019
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