Idiopathic pleuroparenchymal fibroelastosis: The first case to be managed with a successful lung transplant at King Faisal Specialist Hospital and Research Center, Riyadh.

Ann Thorac Med 2019 Jan-Mar;14(1):94-98

Section of Pulmonary Medicine, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia.

Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, managed successfully by bilateral lung transplant performed on a 26 year old Saudi male.

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Source
http://www.thoracicmedicine.org/text.asp?2019/14/1/94/249797
Publisher Site
http://dx.doi.org/10.4103/atm.ATM_106_18DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6341862PMC
February 2019
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