Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature.

Authors:
Dr. Waseem Hajjar, MD. MS. FRCS. FCCP.
Dr. Waseem Hajjar, MD. MS. FRCS. FCCP.
King Saud University, College of Medicine.
Associate professor and Consultant Thoracic Surgeon
Thoracic Surgery
Riyadh, Riyadh | Saudi Arabia

Ann Thorac Med 2018 Oct-Dec;13(4):254-256

Department of Medicine, Alfaisal University, Riyadh, Saudi Arabia.

Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tube insertion and then he was treated surgically with bilateral staged thoracoscopy, apical bullectomy, and pleurodesis with full uneventful recovery.

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Source
http://dx.doi.org/10.4103/atm.ATM_402_17DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6196669PMC

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November 2018
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