Aggressive fibromatosis of the oral cavity in a 5 year old boy: a rare case report.

Authors:
Keerthi Krishnankutty Nair
Keerthi Krishnankutty Nair
Bapuji Dental College and Hospital
Kanad Chaudhuri
Kanad Chaudhuri
Bapuji Dental College and Hospital
Davanagere | India
Ashok Lingappa
Ashok Lingappa
Al Margeb University
Ranjani Shetty
Ranjani Shetty
Department of Oral Medicine and Radiology Bapuji Dental College and Hospital MCC B Block
Pramod Gujjar Vittobarao
Pramod Gujjar Vittobarao
Department of Oral Medicine and Radiology Bapuji Dental College and Hospital MCC B Block

Pan Afr Med J 2017 18;27:47. Epub 2017 May 18.

Department of Oral Medicine and Radiology Bapuji Dental College and Hospital MCC B Block, Davangere, Karnataka, India.

Fibrous tissue proliferations express a wide spectrum of histologic and morphologic variation in both infants and adults. This ranges from hypertrophic scar formation at one end to malignant fibrosarcoma at the other end of the spectrum. Aggressive fibromatosis is an intermediate tumor which is in proximity to fibrosarcomas. These are locally invasive and often recur after excision, but do not metastasize. Histologically, they are characterized by proliferating fibroblasts with little mitotic activity. Aggressive fibromatosis in the head and neck region is not common, and very sporadically occurs in the oral cavity or jaw bones. Here we report a rare case of aggressive fibromatosis occurring in a 5 year old boy.

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Source
http://dx.doi.org/10.11604/pamj.2017.27.47.11739DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5554660PMC
September 2017
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