Giant pancreatic solid cystic desmoid tumor with two ectopic adrenal tissues.

Authors:
Nese Ekinci
Nese Ekinci
Ataturk Training and Research Hospital
Turkey
Arzu Avci
Arzu Avci
Atatürk Research and Education Hospital
Turkey
Oguzhan Ozsay
Oguzhan Ozsay
Yuksek Ihtisas Hospital

Turk J Gastroenterol 2017 Sep 9;28(5):401-404. Epub 2017 Aug 9.

Department of Pathology, İzmir Katip Çelebi University Atatürk Training and Research Hospital, İzmir, Turkey.

A 19-year-old woman presented with painless swelling of the abdomen. During surgery, a giant mass measuring 37 cm×26 cm×12 cm within the distal pancreas invading the spleen was noted. The clinical diagnosis of a solid cystic pseudopapillary tumor of the pancreas was suspected. Distal pancreatectomy, splenectomy, and debulking surgery were performed. Histological examination showed that the tumor infiltrated the spleen and pancreatic parenchyma, and sections of the solid areas revealed a proliferation of spindle-shaped or stellate cells growing in fascicular and storiform patterns within a myxoid intercellular matrix. Cystic areas were representing the entrapped excretory pancreatic ductules. Interestingly, there were two ectopic adrenal tissues found incidentally in the peripheral portion of the tumor. The histopathologic and immunohistochemical features were consistent with a solid cystic desmoid tumor of the pancreas. Desmoid tumors of the pancreas are very rare, and if they present as a solid cystic lesion, their diagnosis may be difficult. We report the case for its rarity and huge size and to emphasize a regular follow-up because the long-term prognosis is currently unknown.

Download full-text PDF

Source
http://dx.doi.org/10.5152/tjg.2017.17208DOI Listing

Still can't find the full text of the article?

Sign up to send a request to the authors directly.
September 2017
28 Reads

Publication Analysis

Top Keywords

solid cystic
16
adrenal tissues
8
cystic desmoid
8
tumor pancreas
8
ectopic adrenal
8
desmoid tumor
8
tumor
5
cystic
5
solid
5
revealed proliferation
4
solid areas
4
parenchyma sections
4
sections solid
4
areas revealed
4
lesion diagnosis
4
cystic lesion
4
cells growing
4
stellate cells
4
difficult report
4
proliferation spindle-shaped
4

Similar Publications