Search our Database of Scientific Publications and Authors

I’m looking for a
    Giant pancreatic solid cystic desmoid tumor with two ectopic adrenal tissues.
    Turk J Gastroenterol 2017 Sep 9;28(5):401-404. Epub 2017 Aug 9.
    Department of Pathology, İzmir Katip Çelebi University Atatürk Training and Research Hospital, İzmir, Turkey.
    A 19-year-old woman presented with painless swelling of the abdomen. During surgery, a giant mass measuring 37 cm×26 cm×12 cm within the distal pancreas invading the spleen was noted. The clinical diagnosis of a solid cystic pseudopapillary tumor of the pancreas was suspected. Distal pancreatectomy, splenectomy, and debulking surgery were performed. Histological examination showed that the tumor infiltrated the spleen and pancreatic parenchyma, and sections of the solid areas revealed a proliferation of spindle-shaped or stellate cells growing in fascicular and storiform patterns within a myxoid intercellular matrix. Cystic areas were representing the entrapped excretory pancreatic ductules. Interestingly, there were two ectopic adrenal tissues found incidentally in the peripheral portion of the tumor. The histopathologic and immunohistochemical features were consistent with a solid cystic desmoid tumor of the pancreas. Desmoid tumors of the pancreas are very rare, and if they present as a solid cystic lesion, their diagnosis may be difficult. We report the case for its rarity and huge size and to emphasize a regular follow-up because the long-term prognosis is currently unknown.

    Similar Publications

    Desmoid tumor of the pancreas: a case report.
    J Med Case Rep 2015 May 6;9:104. Epub 2015 May 6.
    Department of Pediatric Surgery, Medical University of Warsaw, Marszałkowska 24, Warsaw, 00-576, Poland.
    Introduction: Desmoid tumor is a rare, benign, usually asymptomatic fibromatous lesion. The etiology is unknown and the diagnosis is based on histopathological examination. The treatment is complete resection of the tumor. Read More
    Solid cystic pseudopapillary tumor of pancreas with splenic metastasis: Case report and review of literature.
    Int J Surg Case Rep 2015 21;14:50-2. Epub 2015 Jul 21.
    Department of Surgery, Gazi Yasargil Teaching and Research Hospital, Diyarbakır, Turkey.
    Introduction: Solid-cystic pseudopapillary tumor of the pancreas is rare and most commonly seen in young women. We present a young women with solid-cystic pseudopapillary tumor of the pancreas and discuss the literature.

    Presentation Of Case: Thirty nine years old female patient with a mass about 12cm in the pancreas with splenic invasion seen in our clinic. Read More
    Isolated desmoid tumor of pancreatic tail with cyst formation diagnosed by beta-catenin immunostaining: a rare case report with review of literature.
    JOP 2013 May 10;14(3):296-301. Epub 2013 May 10.
    Department of Pathology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, UP, India.
    Context: Isolated pancreatic desmoid tumors with cyst formation are uncommon benign mesenchymal soft tissue tumors, characterized by the dense fibroblastic proliferations with abundant extra-cellular collagen matrix. Intra-abdominal desmoid tumor usually involve the mesentery and retroperitoneum and mostly occur in association of familial adenomatous polyposis or Gardner's syndrome. While desmoid tumors do not metastasize, their advancement can be life threatening due to aggressive local invasion, such as mesentery involvement. Read More
    [Solid pseudopapillary tumors of the pancreas: a pediatric case report].
    Tunis Med 2008 Oct;86(10):928-31
    Laboratoire d'Anatomie et de Cytologie Pathologiques, Hôpital Charles Nicolle, Tunis, Tunisie.
    Background: Solid pseudopapillary tumors of the pancreas are extremely rare and mostly seen in young females. It is often diagnosed incidentally or during investigations of gastrointestinal complaints.

    Aim: Report of a pediatric case of this tumor. Read More