Autoimmune myocarditis in systemic sclerosis: an unusual form of scleroderma heart disease presentation.

Authors:
Ana Rita Ramalho
Ana Rita Ramalho
Associate Editor of AMP-Student. Student at Faculdade de Medicina da Universidade do Porto. Porto. Portugal
Susana Costa
Susana Costa
Laboratório de Química Aplicada
Portugal
Francisco Silva
Francisco Silva
Universitat de València
Spain
Paulo Donato
Paulo Donato
Coimbra Hospital and University Centre
Fatima Franco
Fatima Franco
University of Texas Southwestern Medical Center
United States

ESC Heart Fail 2017 Aug 22;4(3):365-370. Epub 2017 Apr 22.

Coimbra Hospital and University Center, Cardiology Department, Coimbra, Portugal.

Primary cardiac involvement in systemic sclerosis is common, often subclinical, and is associated with significant mortality. We report the case of a patient who developed autoimmune myocarditis at an early stage of systemic sclerosis, who completely recovered from cardiac dysfunction under optimal medical therapy for heart failure and immunosuppression. This challenging case aims at increasing awareness around the fact that the heart is a target organ of scleroderma disease. It also highlights the importance of screening and early diagnosis of cardiac involvement, because a timely treatment may impact the quality of life of these patients and improve their prognosis.
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http://dx.doi.org/10.1002/ehf2.12139DOI ListingPossible
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5542725PMCFound
August 2017
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