Relapsing cerebral amyloid angiopathy-related inflammation: the wax and the wane.

Pract Neurol 2017 Oct 24;17(5):392-395. Epub 2017 Jun 24.

Department of Neurology, Greater Manchester Neurosciences Centre, Salford Royal NHS Trust, Salford, UK.

Cerebral amyloid angiopathy-related inflammation (CAA-I) is a rare variant of cerebral amyloid angiopathy (CAA). Its precise pathophysiology remains uncertain and we currently have limited evidence on which immunosuppressive agents are the most effective in its treatment. The disease course of CAA-I disorders can vary from an isolated clinical event to recurrent episodes. We present a case of biopsy-confirmed CAA-I that gives insight into its potential relapsing nature and the challenges of its long-term management.

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http://pn.bmj.com/lookup/doi/10.1136/practneurol-2017-001599
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http://dx.doi.org/10.1136/practneurol-2017-001599DOI Listing
October 2017
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References

(Supplied by CrossRef)
Genetics of cerebral amyloid angiopathy: systematic review and meta-analysis
Rannikmäe et al.
J Neurol Neurosurg Psychiatry 2013

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