An Bras Dermatol 2017 Mar-Apr;92(2):235-238
Universidade Federal do Espírito Santo (Ufes) - Vitória (ES), Brazil.
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Actas Dermosifiliogr 2006 Oct;97(8):525-8
Servicio de Dermatología, Hospital Universitario Reina Sofía, Córdoba, España.
Angiosarcoma that develops on a limb with chronic lymphedema is called Stewart-Treves syndrome. This typically appears as a complication of a long course lymphedema located on the arm, after mastectomy and/or radiotherapy due to breast cancer. There are cases of Stewart-Treves syndrome in chronic lymphedema in the upper limb contralateral to the breast treated for cancer and in chronic lymphedema of the leg. Read More
Dermatol Online J 2012 Jun 15;18(6):14. Epub 2012 Jun 15.
We report a case of a Stewart-Treves syndrome of the lower limb. The tumor is best described in the upper limb following breast cancer treatment but a small number of cases have arisen in lymphedema of the lower limb. Electrochemotherapy could be useful in the palliative treatment of this lymphangiosarcoma. Read More
An Bras Dermatol 2015 May-Jun;90(3 Suppl 1):232-4
Universidade Federal do Pará, Belém, PA, BR.
Stewart-Treves syndrome is a rare cutaneous angiosarcoma that develops in long-standing chronic lymphedema. Though most commonly this angiosarcoma is a result of post mastectomy lymphoedema, it also develops in Milroy disease, idiopathic, congenital, traumatic and filarial lymphoedema. Despite the rarity of this syndrome and its poor prognosis, early diagnosis associated with radical surgery can provide improved survival. Read More
Cutis 2008 Jun;81(6):468-72
Greater Baltimore Medical Center, Maryland, USA.
Cutaneous angiosarcoma is a rare malignant vascular tumor with a poor prognosis, most commonly affecting elderly white men. Diagnosis usually is delayed because the tumor has a highly variable and often innocuous presentation. Cutaneous angiosarcoma has been associated with a number of conditions and factors, including chronic lymphedema, prior radiation therapy, exposure to chemicals, and vascular malformations. Read More