Cutaneous angiosarcoma: report of three different and typical cases admitted in a unique dermatology clinic.

Authors:
Karina Bittencourt Medeiros
Karina Bittencourt Medeiros
Universidade Federal do Espírito Santo (UFES) - Vitória (ES)
Lucia Martins Diniz
Lucia Martins Diniz
Santa Casa de Misericordia Hospital - Vitoria (ES)
Brazil

An Bras Dermatol 2017 Mar-Apr;92(2):235-238

Universidade Federal do Espírito Santo (Ufes) - Vitória (ES), Brazil.

Angiosarcoma is a rare and aggressive tumor with high rates of metastasis and relapse. It shows a particular predilection for the skin and superficial soft tissues. We report three distinct and typical cases of angiosarcoma that were diagnosed in a single dermatology clinic over the course of less than a year: i) Angiosarcoma in lower limb affected by chronic lymphedema, featuring Stewart-Treves syndrome; ii) a case of the most common type of angiosarcoma loated in the scalp and face of elderly man and; iii) a skin Angiosarcoma in previously irradiated breast. All lesions presented characteristic histopathological findings: irregular vascular proliferation that dissects the collagen bundles with atypical endothelial nuclei projection toward the lumen.

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Source
http://dx.doi.org/10.1590/abd1806-4841.20175326DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5429112PMC
October 2017
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