Pediatr Dermatol 2013 Jan-Feb;30(1):90-3. Epub 2012 Jan 26.
Division of Dermatology, Department of Internal Medicine, School of Medicine Washington University, and St. Louis Children's Hospital, St. Louis, Missouri 63110, USA.
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a severe variant of pityriasis lichenoides et varioliformis acuta (PLEVA). We report a case of FUMHD in an 11-year-old boy who subsequently developed neurologic symptoms and was found to have necrotizing vasculitis on brain biopsy. Over 5 years of follow-up, he had one biopsy-proven recurrence of his skin lesions and continued rehabilitation and treatment for residual neurologic complications. Read More