Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) characterized by subcutaneous infiltration of pleomorphic T-cells of the alpha/beta phenotype rarely affects children. Development of hemophagocytic syndrome (HPS) leads to a poor prognosis with this otherwise indolent lymphoma. We report a case of SPTCL in a 5-year-old child complicated by HPS treated successfully with combination chemotherapy.
Pediatr Dermatol 2016 Mar-Apr;33(2):e72-6. Epub 2016 Jan 14.
Department of Dermatology and Venereology, All India Institute of Medical Sciences, New Delhi, India.
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