Cutaneous collagenous vasculopathy: a rare cause of generalised cutaneous telangiectasia.

Cristina Resende
Cristina Resende
Hospital de Braga
Goreti Catorze
Goreti Catorze
Hospital Egas Moniz
Lisboa | Portugal
Isabel Viana
Isabel Viana
Hospital Central do Funchal

BMJ Case Rep 2015 Jul 8;2015. Epub 2015 Jul 8.

Dermatology Department, Hospital Egas Moniz, Centro Hospitalar Lisboa Ocidental, Lisbon, Portugal.

Cutaneous collagenous vasculopathy is a rare cutaneous microangiopathy of unknown aetiology with only 27 cases reported to date. It is characterised clinically by generalised cutaneous telangiectasias and microscopically by dilation and marked thickening of the walls of superficial dermal blood vessels. Differential diagnosis should be performed with other causes of disseminated telangiectasias, including generalised essential telangiectasia, from which it is clinically indistinguishable. We report a new case of cutaneous collagenous vasculopathy in a 61-year-old woman presenting with a 5-year history of asymptomatic telangiectasias distributed symmetrically on her upper and lower limbs and highlight the importance of clinicopathological correlation for the diagnosis of this disease.
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July 2015
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