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    Hydroa vacciniforme-like lymphoma: a case report from India.
    J Pediatr Hematol Oncol 2015 May;37(4):e223-6
    Department of *Pediatrics †Dermatology ‡Pathology, Christian Medical College, Vellore, India.
    We report a 14-year-old Indian boy who presented with a history of weight loss, fever, facial edema, and a relapsing papulovesicular eruption on the face and limbs for 1 year. Histopathology of the skin showed dense lymphoid infiltrate from dermis to subcutaneous fat. Immunohistochemistry of this lymphoid infiltrate was CD3, CD8, CD56, CD57, Granzyme B, TIA, and Epstein Barr virus LMP1. The histopathology and immunohistochemistry were consistent with the diagnosis of hydroa vacciniforme-like T-cell lymphoma. The child responded remarkably to oral steroids but relapsed on tapering doses. CHOP (Cyclophosphamide, Adriamycin, Vincristine, and Prednisolone) chemotherapy was initiated in view of systemic involvement to which he showed some response, however, the disease relapsed again. He then had a rapidly progressive disease and ultimately succumbed to his illness. This is the first case of hydroa vacciniforme-like T-cell lymphoma being reported from this subcontinent.

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    Epstein-Barr virus-associated hydroa vacciniforme-like cutaneous lymphoma in seven Chinese children.
    Pediatr Dermatol 2010 Sep-Oct;27(5):463-9
    Department of Dermatology, Beijing Children's Hospital, Capital Medical University, Beijing, China.
    Hydroa vacciniforme-like cutaneous lymphoma is a rare type of Epstein-Barr virus-associated lymphoma. We analyze clinicopathologic features of seven Chinese child patients with hydroa vacciniforme-like cutaneous lymphoma and determine the pathogenic association of Epstein-Barr virus with this disorder. Clinical, histologic, and immunohistochemical features were reviewed. Read More
    [Hydroa vacciniforme-like cutaneous T cell lymphoma: a case report and literature review].
    Zhongguo Dang Dai Er Ke Za Zhi 2009 Jul;11(7):596-8
    Department of Pediatrics, First Teaching Hospital of Zhengzhou University, Zhengzhou 450052, China.
    Objective: To study the clinical features, diagnosis and therapy of hydroa vacciniforme-like cutaneous T cell lymphoma.

    Methods: The clinical presentations and the findings of laboratory examinations and skin biopsy of affected tissue in a child with hydroa vacciniforme-like cutaneous T cell lymphoma were retrospectively reviewed.

    Results: The child manifested as rash, fever and lymph node intumesce. Read More
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    Int J Surg Pathol 2013 Apr 17;21(2):161-8. Epub 2012 Jul 17.
    The First Affiliated Hospital, Sun Yat-sen University, Guangzhou, China.
    Primary cutaneous hydroa vacciniforme (HV)-like lymphoma is a rare, Epstein-Barr virus-associated cutaneous neoplasm characterized by photosensitive papulovesicular eruption and usually associated with poor prognosis. This report presents 2 cases of primary cutaneous HV-like lymphoma with unusual indolent clinical course and favorable prognosis during the follow-up periods of 2 and 3 years, respectively. Both patients presented with erythema, papulovesicles, scars, ulcerations, and edema on the face and extremities. Read More
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    Am J Dermatopathol 2015 Jan;37(1):20-5
    *Department of Pathology, Division of Dermatopathology, Medical College of Wisconsin, Milwaukee, WI; and †Department of Pathology and Dermatology, Division of Dermatopathology, Hospital Obrero, La Paz, Bolivia.
    Hydroa vacciniforme-like lymphoma (HVL) is a rare cutaneous T-cell lymphoma that is usually seen in children of Hispanic or Asian origin. Association between chronic latent Epstein-Barr virus infection in both hydroa vacciniforme (HV) and HVL has been demonstrated and has recently been categorized by the World Health Organization as one of the Epstein Barr virus-positive lymphoproliferative disorders of childhood. Patients with HVL present with a cutaneous rash characterized by edema, blisters, ulcers, and scars mainly seen on the face and extremities that mimic HV; however, unlike in HV, the lesions tend to be extensive and deeper and are associated with severe scarring, necrosis, and systemic manifestations. Read More