Primary red ear syndrome associated with cochleo-vestibular symptomatology: a paediatric case report.

Cephalalgia 2013 Nov 25;33(15):1277-80. Epub 2013 Jun 25.

Department of Paediatric Rheumatology, G Gaslini Institute, Italy.

Background: Red ear syndrome (RES), first described by Lance in 1996 in an adult series, may be primary or associated with headache syndromes, upper cervical disorders or vascular anomalies. Clinically the disease is characterised by recurrent episodes of reddening and burning pain in the auricle, usually elicited by different triggers. The prevalence of RES in the paediatric age group remains poorly understood. Several therapeutic approaches have been tried with heterogeneous clinical response.

Case Results: We report a paediatric patient suffering from primary RES associated with debilitating cochleo-vestibular symptomatology causing severe discomfort. Three years after the disease onset, the patient also developed headache, with clinical features of migraine.

Discussion: The temporal and spatial association could suggest shared pathogenetic features between neurological (cochleo-vestibular) and vascular (red and burning ear) symptomatology, likely related to trigeminal autonomic reflex activation, although further studies are required for full comprehension of RES pathogenesis.

Download full-text PDF

Source
http://dx.doi.org/10.1177/0333102413493527DOI Listing
November 2013
31 Reads

Publication Analysis

Top Keywords

cochleo-vestibular symptomatology
8
ear syndrome
8
red ear
8
ear symptomatology
4
burning pain
4
spatial association
4
pain auricle
4
auricle elicited
4
elicited triggers
4
prevalence res
4
res paediatric
4
triggers prevalence
4
red burning
4
symptomatology trigeminal
4
burning ear
4
features migrainediscussion
4
severe discomfort
4
disease characterised
4
autonomic reflex
4
clinically disease
4

Similar Publications