Localized cutaneous fibrosing disorders.

Authors:
Aaliya Yaqub
Aaliya Yaqub
Stanford University
United States
Lorinda Chung
Lorinda Chung
Stanford University School of Medicine
United States
Kerri E Rieger
Kerri E Rieger
Stanford University School of Medicine
United States
David F Fiorentino
David F Fiorentino
Stanford University School of Medicine
United States

Rheum Dis Clin North Am 2013 May 16;39(2):347-64. Epub 2013 Mar 16.

Division of Immunology and Rheumatology, Stanford University School of Medicine, 300 Pasteur Drive, Stanford, CA 94305, USA.

This article acquaints the reader with disorders of the skin that might mimic systemic sclerosis but whose pathology is localized to the skin and/or has extracutaneous manifestations that are different than systemic sclerosis. These disorders include localized scleroderma (morphea), eosinophilic fasciitis, scleredema, scleromyxedema, nephrogenic systemic fibrosis, and chronic graft-versus-host disease. Particular emphasis is placed on clinical and histopathologic features that help the clinician differentiate between these disorders. Treatment options are briefly reviewed.

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http://dx.doi.org/10.1016/j.rdc.2013.02.013DOI Listing
May 2013
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