Am J Clin Dermatol 2007 ;8(1):29-36
Department of Dermatology, New York University School of Medicine, New York, NY 10016, USA.
J Am Acad Dermatol 2004 Dec;51(6):1014-7
Department of Dermatology, University Hospital of Zurich, Switzerland.
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a severe variant of pityriasis lichenoides et varioliformis acuta (PLEVA). PLEVA patients only very rarely have systemic signs; the cutaneous lesions are usually asymptomatic, but may be pruritic and may heal with scarring. FUMHD often starts out as classic PLEVA, but goes on to develop widespread ulceronecrotic lesions and is associated with a high mortality rate. Read More
J Am Acad Dermatol 2006 Oct;55(4):557-72; quiz 573-6
Minneapolis Veteran's Affairs Medical Center, USA.
Pityriasis lichenoides represents a unique group of inflammatory skin disorders that include pityriasis lichenoides et varioliformis acuta (PLEVA), febrile ulceronecrotic Mucha-Habermann disease (a subtype of PLEVA), and pityriasis lichenoides chronica. The history, epidemiology, clinical features, pathophysiology, and treatment of this group of conditions are reviewed in this manuscript. Read More
Br J Dermatol 2005 Apr;152(4):794-9
Division of Paediatric Dermatology, Department of Dermatology, University of Hamburg, Martinistr. 52, D-20246 Hamburg, Germany.
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) represents a fulminant and potentially lethal variant of pityriasis lichenoides. Only 24 cases have been described so far. We report a 9-year-old boy who initially presented with classical pityriasis lichenoides et varioliformis acuta (PLEVA) following a mild enteritis. Read More
Cutis 2016 May;97(5):345;347;358
Bay Dermatology/Largo Medical Center, Florida, USA.
Pityriasis lichenoides is an uncommon, acquired, idiopathic, self-limiting skin disease that poses a challenge to patients and clinicians to diagnose and treat. Several variants exist including pityriasis lichenoides et varioliformis acuta (PLEVA), pityriasis lichenoides chronica (PLC), and febrile ulcer-onecrotic Mucha-Habermann disease. Precise classification can be difficult due to an overlap of clinical and histologic features. Read More