Veronique Fremeaux-Bacchi

Veronique Fremeaux-Bacchi

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Veronique Fremeaux-Bacchi

Veronique Fremeaux-Bacchi

Publications by authors named "Veronique Fremeaux-Bacchi"

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Anti-Factor B Antibodies and Acute Postinfectious GN in Children.

J Am Soc Nephrol 2020 Feb 7. Epub 2020 Feb 7.

Inflammation, Complement and Cancer Team, Cordeliers Research Center, Institut National de la Santé et de la Recherche Médicale (INSERM) Unité Mixte de Recherche (UMR) S1138, Paris, France;

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http://dx.doi.org/10.1681/ASN.2019080851DOI Listing
February 2020

Analysis of protein missense alterations by combining sequence- and structure-based methods.

Mol Genet Genomic Med 2020 Feb 25:e1166. Epub 2020 Feb 25.

INSERM U973, Laboratory MTi, University Paris Diderot, Paris, France.

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http://dx.doi.org/10.1002/mgg3.1166DOI Listing
February 2020

C3 glomerulonephritis in a patient treated with anti-PD-1 antibody.

Eur J Cancer 2020 Jan 12;125:46-48. Epub 2019 Dec 12.

Institut de Transplantation Urologie Néphrologie (ITUN), CHU Nantes, Nantes, France; Centre de Recherche en Transplantation et Immunologie UMR 1064, INSERM, Université de Nantes, Nantes, France.

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http://dx.doi.org/10.1016/j.ejca.2019.11.011DOI Listing
January 2020

Complement activation in sickle cell disease: Dependence on cell density, hemolysis and modulation by hydroxyurea therapy.

Am J Hematol 2020 Jan 28. Epub 2020 Jan 28.

INSERM U955 équipe 2, Institut Mondor de Recherche Biomédicale (IMRB), Université Paris-Est-Créteil (UPEC), Créteil, France; and Laboratoire d'excellence GR-Ex, Paris, France.

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http://dx.doi.org/10.1002/ajh.25742DOI Listing
January 2020

Shiga toxin-producing Escherichia coli-associated hemolytic uremic syndrome in solid organ transplant recipients.

Kidney Int 2019 Dec;96(6):1423-1424

Centre de Recherche en Transplantation et en Immunologie UMR 1064, INSERM, Université de Nantes, Nantes, France; Department of Nephrology and Immunology, Center Hospitalier Universitaire de Nantes, Nantes, France. Electronic address:

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http://dx.doi.org/10.1016/j.kint.2019.08.024DOI Listing
December 2019

Monitoring Complement Activation: The New Conundrum in Thrombotic Microangiopathies.

Clin J Am Soc Nephrol 2019 Dec 6;14(12):1682-1683. Epub 2019 Nov 6.

Assistance Publique-Hôpitaux de Paris, Laboratory of Immunology, Hôpital Européen Georges-Pompidou, Paris, France.

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http://dx.doi.org/10.2215/CJN.12111019DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6895483PMC
December 2019

Atypical hemolytic uremic syndrome and hypertensive crisis.

Kidney Int 2019 Nov;96(5):1239

Assistance Publique-Hôpitaux de Paris, Laboratoire d'immunologie, Hôpital Européen Georges Pompidou, Paris, France; INSERM UMR S1138, Inflammation Complément et Cancer, Centre de recherche des Cordeliers, Paris, France.

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http://dx.doi.org/10.1016/j.kint.2019.07.023DOI Listing
November 2019

Glomerulonephritis With Isolated C3 Deposits as a Manifestation of Subtotal Factor I Deficiency.

Kidney Int Rep 2019 Sep 31;4(9):1354-1358. Epub 2019 May 31.

Assistance Publique des Hôpitaux de Paris (AP-HP), Groupe Hospitalier Henri-Mondor/ Albert Chenevier, Service de Néphrologie et Transplantation, Créteil, France.

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http://dx.doi.org/10.1016/j.ekir.2019.05.1156DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6732777PMC
September 2019

The authors reply.

Kidney Int 2019 Aug;96(2):517-518

Unité Mixte de Recherche 1064, Centre de Recherche en Transplantation et Immunologie, Institut National de la Santé et de la Recherche Médicale, Université de Nantes, Nantes, France; Department of Nephrology and Immunology, Center Hospitalier Universitaire de Nantes, Nantes, France. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S00852538193046
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http://dx.doi.org/10.1016/j.kint.2019.04.010DOI Listing
August 2019

Atypical and secondary hemolytic uremic syndromes have a distinct presentation and no common genetic risk factors.

Kidney Int 2019 Jun 15;95(6):1443-1452. Epub 2019 Mar 15.

Centre de Recherche en Transplantation et Immunologie, UMR 1064, INSERM, Université de Nantes, Nantes, France; Institut de Transplantation Urologie Néphrologie, CHU Nantes, Nantes, France; Department of Nephrology and Immunology, Center Hospitalier Universitaire de Nantes, Nantes, France. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S00852538193016
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http://dx.doi.org/10.1016/j.kint.2019.01.023DOI Listing
June 2019

Haemolytic uraemic syndrome associated with non shiga toxin-producing Escherichia coli bacteraemia: a case report.

BMC Nephrol 2019 05 7;20(1):157. Epub 2019 May 7.

Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou (AP-HP), 20 rue Leblanc, 75 908, Paris, Cedex 15, France.

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http://dx.doi.org/10.1186/s12882-019-1357-3DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6505115PMC
May 2019

Successful treatment of a associated haemolytic uraemic syndrome by eculizumab.

Clin Kidney J 2019 Feb 20;12(1):106-109. Epub 2018 Mar 20.

Department of Nephrology and Kidney Transplantation, Centre Hospitalier Universitaire de Montpellier, Montpellier, France.

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http://dx.doi.org/10.1093/ckj/sfy019DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6366139PMC
February 2019

In Reply to 'Benefit of Eculizumab Compared to Standard of Care Still Unproven in C3 Glomerulopathy'.

Am J Kidney Dis 2018 12 17;72(6):906-907. Epub 2018 Sep 17.

Centre Hospitalier Universitaire de Nantes, Nantes, France.

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http://dx.doi.org/10.1053/j.ajkd.2018.08.005DOI Listing
December 2018

C4 Nephritic Factors in C3 Glomerulopathy: A Case Series.

Am J Kidney Dis 2017 Dec 24;70(6):834-843. Epub 2017 Aug 24.

Molecular Otolaryngology and Renal Research Laboratories, Carver College of Medicine, University of Iowa, Iowa City, IA; Department of Internal Medicine, Carver College of Medicine, University of Iowa, Iowa City, IA. Electronic address:

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http://dx.doi.org/10.1053/j.ajkd.2017.07.004DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5701858PMC
December 2017

Midterm Outcomes of 12 Renal Transplant Recipients Treated With Eculizumab to Prevent Atypical Hemolytic Syndrome Recurrence.

Transplantation 2017 12;101(12):2924-2930

Service de Néphrologie, Transplantation Adulte, Hôpital Necker-Enfants Malades, Université Paris Descartes, Assistance Publique-Hôpitaux de Paris, Paris, France.

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http://dx.doi.org/10.1097/TP.0000000000001909DOI Listing
December 2017

C5 nephritic factors drive the biological phenotype of C3 glomerulopathies.

Kidney Int 2017 11 14;92(5):1232-1241. Epub 2017 Jul 14.

Assistance Publique - Hopitaux de Paris, Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou, Paris, France; INSERM UMRS 1138, Cordeliers Research Center, Complement and Diseases team, Paris, France. Electronic address:

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http://dx.doi.org/10.1016/j.kint.2017.04.017DOI Listing
November 2017

A novel CFHR1-CFHR5 hybrid leads to a familial dominant C3 glomerulopathy.

Kidney Int 2017 10 18;92(4):876-887. Epub 2017 Jul 18.

Institut National de la Santé et de la Recherche Médicale, Unité Mixte de Recherche en Santé 1138, Team "Complement and Disease," Cordeliers Research Center, Paris, France; Paris Descartes University, Paris, France; Laboratoire d'Immunologie, Hôpital Européen Georges Pompidou, Assistance publique-Hôpitaux de Paris, Paris, France. Electronic address:

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http://dx.doi.org/10.1016/j.kint.2017.04.025DOI Listing
October 2017

Haemolytic uraemic syndrome.

Lancet 2017 Aug 25;390(10095):681-696. Epub 2017 Feb 25.

Assistance Publique-Hôpitaux de Paris, Department of Pediatric Nephrology, Hôpital Robert Debré, Université Paris Diderot, Sorbonne Paris Cité, Paris, France. Electronic address:

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http://dx.doi.org/10.1016/S0140-6736(17)30062-4DOI Listing
August 2017

Hemolytic Uremic Syndrome in Pregnancy and Postpartum.

Clin J Am Soc Nephrol 2017 Aug 8;12(8):1237-1247. Epub 2017 Jun 8.

Due to the number of contributing authors, the affiliations are provided in the Supplemental Material.

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http://dx.doi.org/10.2215/CJN.00280117DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5544502PMC
August 2017

C3 glomerulopathy and eculizumab: a report on four paediatric cases.

Pediatr Nephrol 2017 06 24;32(6):1023-1028. Epub 2017 Feb 24.

Service de Néphrologie Rhumatologie Dermatologie Pédiatriques, Centre de Référence des Maladies Rénales Rares Hôpital Femme Mère Enfant, Hospices Civils de Lyon, 59 boulevard Pinel, 69677, Bron, France.

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http://dx.doi.org/10.1007/s00467-017-3619-2DOI Listing
June 2017

Anti-Factor B and Anti-C3b Autoantibodies in C3 Glomerulopathy and Ig-Associated Membranoproliferative GN.

J Am Soc Nephrol 2017 May 17;28(5):1603-1613. Epub 2017 Jan 17.

Team Complement and Diseases Cordeliers Research Center, Institut National de la Santé et de la Recherche Médicale, Unité Mixte de Recherche 1138, Paris, France;

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http://dx.doi.org/10.1681/ASN.2016030343DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5407719PMC
May 2017

Atypical hemolytic uremic syndrome and C3 glomerulopathy: conclusions from a "Kidney Disease: Improving Global Outcomes" (KDIGO) Controversies Conference.

Kidney Int 2017 03 16;91(3):539-551. Epub 2016 Dec 16.

Molecular Otolaryngology and Renal Research Laboratories, Carver College of Medicine, University of Iowa, Iowa City, Iowa, USA; Division of Nephrology, Department of Internal Medicine, Carver College of Medicine, University of Iowa, Iowa City, Iowa, USA. Electronic address:

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http://dx.doi.org/10.1016/j.kint.2016.10.005DOI Listing
March 2017

Thrombotic microangiopathy mimicking membranoproliferative glomerulonephritis.

Nephrol Dial Transplant 2017 03;32(3):584

Department of Pediatrics, Clinical Sciences Lund, Lund University, Lund, Sweden.

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http://dx.doi.org/10.1093/ndt/gfx013DOI Listing
March 2017

Atypical haemolytic uraemic syndrome and pregnancy: outcome with ongoing eculizumab.

Nephrol Dial Transplant 2016 12 1;31(12):2122-2130. Epub 2016 Sep 1.

Department of Nephrology Transplantation-Dialysis, Centre Hospitalier Universitaire de Bordeaux, Bordeaux, France.

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http://dx.doi.org/10.1093/ndt/gfw314DOI Listing
December 2016

Blockade of C5 in Severe Acute Postinfectious Glomerulonephritis Associated With Anti-Factor H Autoantibody.

Am J Kidney Dis 2016 Dec 24;68(6):944-948. Epub 2016 Sep 24.

Transplantation Center, University Hospital of Lausanne (CHUV), Lausanne, Switzerland. Electronic address:

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http://dx.doi.org/10.1053/j.ajkd.2016.06.026DOI Listing
December 2016

Long-term successful liver-kidney transplantation in a child with atypical hemolytic uremic syndrome caused by homozygous factor H deficiency.

Pediatr Nephrol 2016 12 15;31(12):2375-2378. Epub 2016 Oct 15.

Pediatric Nephrology, AP-HP Hôpital Robert-Debré, 48 Bd Sérurier, 75019, Paris, France.

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http://dx.doi.org/10.1007/s00467-016-3511-5DOI Listing
December 2016

Endothelial cells: source, barrier, and target of defensive mediators.

Immunol Rev 2016 11;274(1):307-329

INSERM UMRS 1138, Cordeliers Research Center, Université Pierre et Marie Curie (UPMC-Paris-6) and Université Paris Descartes Sorbonne Paris-Cité, Paris, France.

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http://dx.doi.org/10.1111/imr.12479DOI Listing
November 2016

A nationwide study of acquired C1-inhibitor deficiency in France: Characteristics and treatment responses in 92 patients.

Medicine (Baltimore) 2016 Aug;95(33):e4363

aInternal Medicine Department, Saint Antoine Hospital, Assistance Publique-Hôpitaux de Paris, DHU i2B, Paris 6 University, Paris bHematology Department, Pitié Salpétrière Hospital, Assistance Publique-Hôpitaux de Paris, Paris 6 University, Paris cImmunology Laboratory, University Hospital, Grenoble dCentre de Référence et d'Etude des Angioedèmes à Kinine (CREAK) , Grenoble ePublic Health Department, Tenon Hospital, Assistance Publique-Hôpitaux de Paris, Paris 6 University fImmunology Laboratory, Georges Pompidou European Hospital, Assistance Publique-Hôpitaux de Paris, Paris 5 University, Paris gJoint Unit 1036 CNRS-CEA-INSERM, University Grenoble Alpes hInternal Medicine Department, University Hospital, Grenoble iUniversité Joseph Fourier Grenoble, GREPI/AGIM CNRS FRE 3405, Grenoble jInternal Medicine Department, La Conception Hospital, AP-HM, Marseille kInternal Medicine and Clinical Immunology Department, Lille University Hospital lLIRIC, INSERM UMR 995, EA2686, Lille mDermatology Department, L'UNAM Université, University Hospital, Angers, France.

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http://dx.doi.org/10.1097/MD.0000000000004363DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5370791PMC
August 2016

A Familial C3GN Secondary to Defective C3 Regulation by Complement Receptor 1 and Complement Factor H.

J Am Soc Nephrol 2016 Jun 15;27(6):1665-77. Epub 2015 Oct 15.

Institut National de la Santé et de la Recherche Médicale, Unité Mixte de Recherche S1138, Complément et Maladies, Centre de Recherche des Cordeliers, Paris, France; Assistance Publique-Hôpitaux de Paris, Service d'Immunologie Biologique, Hôpital européen Georges Pompidou, Paris, France;

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http://dx.doi.org/10.1681/ASN.2015040348DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4884110PMC
June 2016

[Complement deficiencies and human diseases].

Ann Biol Clin (Paris) 2014 May-Jun;72(3):271-80

Immunologie biologique, Hôpital européen Georges-Pompidou, Assistance Publique-Hôpitaux de Paris, Paris, France, Inserm UMR_S1138, Centre de recherche des Cordeliers, Paris, France.

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http://dx.doi.org/10.1684/abc.2014.0961DOI Listing
May 2016

Defining the genetics of thrombotic microangiopathies.

Transfus Apher Sci 2016 Apr 2;54(2):212-9. Epub 2016 May 2.

Assistance Publique - Hopitaux de Paris, Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou, Paris, France; INSERM UMRS 1138, Cordeliers Research Center, Paris, France. Electronic address:

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http://dx.doi.org/10.1016/j.transci.2016.04.011DOI Listing
April 2016

aHUS associated with C3 gene mutation: a case with numerous relapses and favorable 20-year outcome.

Pediatr Nephrol 2016 Mar 16;31(3):513-7. Epub 2015 Nov 16.

Service d'Immunologie Biologique Hôpital Européen Georges Pompidou, Paris, France.

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http://dx.doi.org/10.1007/s00467-015-3267-3DOI Listing
March 2016

Complement gene variants determine the risk of immunoglobulin-associated MPGN and C3 glomerulopathy and predict long-term renal outcome.

Mol Immunol 2016 Mar 16;71:131-142. Epub 2016 Feb 16.

IRCCS-Istituto di Ricerche Farmacologiche Mario Negri, Clinical Research Center for Rare Diseases Aldo e Cele Daccò, Ranica, Bergamo, Italy; Unit of Nephrology and Dialysis, Azienda Ospedaliera Papa Giovanni XXIII, Bergamo, Italy; Department of Biomedical and Clinical Sciences, University of Milan, Milan, Italy.

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http://dx.doi.org/10.1016/j.molimm.2016.01.010DOI Listing
March 2016

Eculizumab salvage therapy for delayed hemolysis transfusion reaction in sickle cell disease patients.

Blood 2016 Feb 12;127(8):1062-4. Epub 2016 Jan 12.

Service de Médecine Interne, French Sickle Cell Referral Center, Groupe Hospitalier Henri Mondor-Albert Chenevier, Assistance Publique-Hôpitaux de Paris (APHP), and INSERM-U955, Equipe 2: Transfusion et Maladies du Globule Rouge, Laboratoire d'Excellence, GRex, Institut Mondor, Université Paris-Est Créteil, Créteil, France;

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http://dx.doi.org/10.1182/blood-2015-09-669770DOI Listing
February 2016

CFH gene mutation in a case of Shiga toxin-associated hemolytic uremic syndrome (STEC-HUS).

Pediatr Nephrol 2016 Jan 23;31(1):157-61. Epub 2015 Sep 23.

Service de Pédiatrie 1, Centre Hospitalier Universitaire de Strasbourg, Avenue Molière, 67098, Strasbourg Cedex, France.

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http://link.springer.com/content/pdf/10.1007%2Fs00467-015-32
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http://link.springer.com/10.1007/s00467-015-3207-2
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http://dx.doi.org/10.1007/s00467-015-3207-2DOI Listing
January 2016

Recurrent Hemolytic and Uremic Syndrome Induced by Escherichia Coli.

Medicine (Baltimore) 2016 Jan;95(1):e2050

From the APHP, Hôpital Tenon (MC, RK, CR, ER, AH), Urgences Néphrologiques et Transplantation Rénale, Institut Pasteur (F-XW, MG), Unité des Bactéries Pathogènes Entériques, Centre National de Référence des E coli et Shigella, Paris, VetAgro Sup (EL, AG), Campus vétérinaire de Lyon, Laboratoire d'études des microorganismes alimentaires pathogènes (LMAP), Laboratoire National de Référence pour les E coli y compris les E coli producteurs de Shiga-toxines (LNR STEC), Marcy L'Etoile, Service d'Immunologie, Hôpital Européen Georges Pompidou (VF-B); and UPMC Sorbonne Université Paris 06 (ER, AH), Paris, France.

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http://dx.doi.org/10.1097/MD.0000000000002050DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4706244PMC
January 2016

The emerging role of complement inhibitors in transplantation.

Kidney Int 2015 Nov 16;88(5):967-73. Epub 2015 Sep 16.

Service de Néphrologie-Transplantation, Hôpital Necker, AP-HP, Paris, France.

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http://dx.doi.org/10.1038/ki.2015.253DOI Listing
November 2015

Functional Characterization of Autoantibodies against Complement Component C3 in Patients with Lupus Nephritis.

J Biol Chem 2015 Oct 5;290(42):25343-55. Epub 2015 Aug 5.

INSERM, UMR_S 1138, Centre de Recherche des Cordeliers, 75006 Paris, France, the Université Paris Descartes, Sorbonne Paris Cité, UMR_S 1138, Centre de Recherche des Cordeliers, 75006 Paris, France, the Sorbonne Universités, UPMC Univ Paris 06, UMR_S 1138, Centre de Recherche des Cordeliers, 75006 Paris, France, and

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http://dx.doi.org/10.1074/jbc.M115.647008DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4646184PMC
October 2015

Use of Eculizumab in Patients With Allogeneic Stem Cell Transplant-Associated Thrombotic Microangiopathy: A Study From the SFGM-TC.

Transplantation 2015 Sep;99(9):1953-9

1 Hématologie Greffe de Moelle, Hôpital Saint Louis, APHP, Université Paris Diderot, Paris, France. 2 Service d'Hématologie Pédiatrique, Hôpital de la Timone, Marseille, France. 3 Service d'Onco-hematologie Pédiatrique, Hôpital Arnaud de Villeneuve, Centre Hospitalier Universitaire de Montpellier, Montpellier, France. 4 Service d'Hématologie, CHU de Purpan, Toulouse, France. 5 Département de Néphrologie et Transplantation d'organe, CHU de Rangueil, Toulouse, France. 6 Service d'Hématologie, Hôpital de la Pitié Salpetrière, APHP, Université Pierre et Marie Curie, Paris. 7 Service de Thérapie Cellulaire et d'Hématologie Clinique, Hôpital d'Estaing, CHU Clermont Ferrand, Université d'Auvergne, Clermont-Ferrand, France. 8 Service d'Immuno-hématologie et Rhumatologie pédiatrique, Hôpital Necker-Enfants Malades, Laboratoire INSERM U768, Institut Imagine, Université Sorbonne Paris-cité, Paris, France. 9 Centre de Néphrologie et Transplantation Rénale, Hôpital de la Conception, APHM, Université d'Aix Marseille, Marseille, France. 10 Service d'Hématologie, Hôpital Hautepierre, Hôpitaux Universitaire de Strasbourg, Strasbourg, France. 11 Département de Biostatistiques, Hôpital Saint Louis, APHP, Université Paris Diderot, Paris, France. 12 Service d'Immunologie Biologique, Hôpital Européen George Pompidou, APHP, CHU Paris Ouest, Paris, France. 13 Service d'Hématologie Biologique, Hôpital Antoine Beclère, APHP, Université Paris Sud, Clamart, France. 14 Service d'Hématologie, Centre de Référence des Microangiopathies Thrombotiques, Hôpitaux Universitaires de l'Est Parisien, APHP, Université Pierre et Marie Curie, Paris, France.

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http://dx.doi.org/10.1097/TP.0000000000000601DOI Listing
September 2015

Atypical aHUS: State of the art.

Mol Immunol 2015 Sep 3;67(1):31-42. Epub 2015 Apr 3.

Molecular Otolaryngology and Renal Research Laboratories, Carver College of Medicine, University of Iowa, Iowa City, IA, USA; Division of Nephrology, Stead Family Department of Pediatrics, Department of Internal Medicine, Carver College of Medicine, University of Iowa, Iowa City, IA, USA. Electronic address:

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http://dx.doi.org/10.1016/j.molimm.2015.03.246DOI Listing
September 2015

The role of complement in C3 glomerulopathy.

Mol Immunol 2015 Sep 28;67(1):21-30. Epub 2015 Apr 28.

University of Iowa Carver College of Medicine, Otolaryngology, Iowa City, IA 52242, USA.

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http://dx.doi.org/10.1016/j.molimm.2015.03.012DOI Listing
September 2015

Distal Angiopathy and Atypical Hemolytic Uremic Syndrome: Clinical and Functional Properties of an Anti-Factor H IgAλ Antibody.

Am J Kidney Dis 2015 Aug 23;66(2):331-6. Epub 2015 May 23.

Service de Néphrologie Transplantation Dialyse, Centre Hospitalier Universitaire de Bordeaux, Bordeaux, France; INSERM U1026, Université de Bordeaux, Bordeaux, France.

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http://dx.doi.org/10.1053/j.ajkd.2015.03.039DOI Listing
August 2015

Current Understanding of the Role of Complement in IgA Nephropathy.

J Am Soc Nephrol 2015 Jul 18;26(7):1503-12. Epub 2015 Feb 18.

University of Alabama at Birmingham, Departments of Microbiology and Medicine, Birmingham, Alabama;

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http://dx.doi.org/10.1681/ASN.2014101000DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4483595PMC
July 2015

A case of C3 glomerulonephritis successfully treated with eculizumab.

Pediatr Nephrol 2015 Jun 22;30(6):1033-7. Epub 2015 Mar 22.

Department of Pediatrics, Division of Nephrology, CHU Sainte Justine and University of Montreal, 3175 Côte Sainte Catherine, H3T1C5, Montreal, QC, Canada.

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http://link.springer.com/content/pdf/10.1007%2Fs00467-015-30
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http://link.springer.com/10.1007/s00467-015-3061-2
Publisher Site
http://dx.doi.org/10.1007/s00467-015-3061-2DOI Listing
June 2015

Anti-factor H autoantibodies in C3 glomerulopathies and in atypical hemolytic uremic syndrome: one target, two diseases.

J Immunol 2015 Jun 27;194(11):5129-38. Epub 2015 Apr 27.

INSERM Unité Mixte de Recherche S1138, "Complément et Maladies" Équipe 10, Centre de Recherche des Cordeliers, Université Pierre et Marie Curie, 75006 Paris, France; Service de Néphrologie, Hôpital Tenon, Assistance Publique-Hôpitaux de Paris, 75970 Paris Cedex 20, France; Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou, Assistance Publique-Hôpitaux de Paris, 75908 Paris, France

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http://dx.doi.org/10.4049/jimmunol.1402770DOI Listing
June 2015

Complement System Part II: Role in Immunity.

Front Immunol 2015 26;6:257. Epub 2015 May 26.

UMRS 1138, Centre de Recherche des Cordeliers, INSERM , Paris , France ; UMRS 1138, Centre de Recherche des Cordeliers, Sorbonne Paris Cité, Université Paris Descartes , Paris , France ; UMRS 1138, Centre de Recherche des Cordeliers, Sorbonne Universités, UPMC Université Paris 06 , Paris , France.

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http://dx.doi.org/10.3389/fimmu.2015.00257DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4443744PMC
June 2015

Complement System Part I - Molecular Mechanisms of Activation and Regulation.

Front Immunol 2015 2;6:262. Epub 2015 Jun 2.

UMR_S 1138, Cordeliers Research Center, Complement and Diseases Team, INSERM , Paris , France ; UMR_S 1138, Centre de Recherche des Cordeliers, Sorbonne Paris Cité, Université Paris Descartes , Paris , France ; UMR_S 1138, Centre de Recherche des Cordeliers, Sorbonne Universités, Université Pierre et Marie Curie-Paris , Paris , France.

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http://dx.doi.org/10.3389/fimmu.2015.00262DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4451739PMC
June 2015

Mapping interactions between complement C3 and regulators using mutations in atypical hemolytic uremic syndrome.

Blood 2015 Apr 21;125(15):2359-69. Epub 2015 Jan 21.

INSERM UMRS 1138, Cordeliers Research Center, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie, Paris, France; Assistance Publique-Hôpitaux de Paris, Service d'Immunologie Biologique, Hôpital Européen Georges Pompidou, Paris, France.

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http://dx.doi.org/10.1182/blood-2014-10-609073DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4392009PMC
April 2015

Eculizumab for treatment of rapidly progressive C3 glomerulopathy.

Am J Kidney Dis 2015 Mar 17;65(3):484-9. Epub 2014 Dec 17.

INSERM, UMR-S 1064, and Department of Nephrology and Immunology, CHU de Nantes, Nantes, France. Electronic address:

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http://dx.doi.org/10.1053/j.ajkd.2014.09.025DOI Listing
March 2015

Atypical Hemolytic Uremic Syndrome Recurrence after Renal Transplantation: C3-Glomerulonephritis as an Initial Presentation.

Transplant Direct 2015 Mar 26;1(2):e9. Epub 2015 Mar 26.

Division of Nephrology, Geneva University Hospitals, Geneva, Switzerland.; Division of Transplantation, Geneva University Hospitals, Geneva, Switzerland.

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http://dx.doi.org/10.1097/TXD.0000000000000518DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4946455PMC
March 2015

Detection of C3d-binding donor-specific anti-HLA antibodies at diagnosis of humoral rejection predicts renal graft loss.

J Am Soc Nephrol 2015 Feb 14;26(2):457-67. Epub 2014 Aug 14.

Hospices Civils de Lyon, Hôpital Edouard Herriot, Service de Transplantation, Néphrologie et Immunologie Clinique, Lyon, France; Institut National de la Santé et de la Recherche Médicale U1111, Lyon, France; Unité de Formation et de Recherche Lyon Est, Université de Lyon, Lyon, France;

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http://dx.doi.org/10.1681/ASN.2013101144DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4310653PMC
February 2015

C3 nephritic factor can be associated with membranous glomerulonephritis.

Pediatr Nephrol 2015 Feb 14;30(2):353-5. Epub 2014 Nov 14.

Inserm U1091, Genetics of Renal Development and Diseases, UNS Université Nice Sophia Antipolis, 28, avenue de Valrose, 06000, Nice, France,

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http://dx.doi.org/10.1007/s00467-014-3004-3DOI Listing
February 2015

Loss of DGKε induces endothelial cell activation and death independently of complement activation.

Blood 2015 Feb 10;125(6):1038-46. Epub 2014 Dec 10.

INSERM Unité Mixte de Recherche S-1064, Institut de Transplantation Urologie-Nephrologie, Centre Hospitalier Universitaire de Nantes, University of Nantes, Nantes, France;

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http://dx.doi.org/10.1182/blood-2014-06-579953DOI Listing
February 2015

Assessing complement blockade in patients with paroxysmal nocturnal hemoglobinuria receiving eculizumab.

Blood 2015 Jan 4;125(5):775-83. Epub 2014 Dec 4.

Service d'Hématologie Greffe, Assistance Publique-Hôpitaux de Paris, Hôpital Saint Louis, Paris, France; Université Paris Diderot, Paris, France; and Institut National de la Santé et de la Recherche Médicale U1160, Paris, France.

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http://dx.doi.org/10.1182/blood-2014-03-560540DOI Listing
January 2015

Heterogeneous histologic and clinical evolution in 3 cases of dense deposit disease with long-term follow-up.

Hum Pathol 2014 Nov 16;45(11):2326-33. Epub 2014 Aug 16.

Paris Descartes University, Paris, France 75006; Department of Nephrology, Hôpital Necker, AP-HP, Paris, France 75015. Electronic address:

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http://dx.doi.org/10.1016/j.humpath.2014.07.021DOI Listing
November 2014

Complement factor B mutations in atypical hemolytic uremic syndrome-disease-relevant or benign?

J Am Soc Nephrol 2014 Sep 20;25(9):2053-65. Epub 2014 Mar 20.

Institut National de la Santé et de la Recherche Médicale UMRS 1138, Cordeliers Research Center, Complement and Diseases Team, Paris, France; Université Paris Descartes Sorbonne Paris-Cité, Paris, France; Université Pierre et Marie Curie (Paris-6), Paris, France;

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http://dx.doi.org/10.1681/ASN.2013070796DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4147975PMC
September 2014

Malignancy and thrombotic microangiopathy or atypical haemolytic and uraemic syndrome?

Br J Haematol 2014 Sep 21;166(5):802-5. Epub 2014 Apr 21.

Department of nephrology, CHU de Nice, Nice, France; Aging and Diabetes Team, IRCAN, UMR-INSERM 1081, Nice, France.

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http://dx.doi.org/10.1111/bjh.12907DOI Listing
September 2014

Deciphering complement interference in anti-human leukocyte antigen antibody detection with flow beads assays.

Transplantation 2014 Sep;98(6):625-31

1 Laboratoire d'Immunologie et Immunogénétique, Hôpital Pellegrin, CHU de Bordeaux, Bordeaux, France. 2 UMR CNRS 5164, Université de Bordeaux, Talence, France. 3 Assistance Publique-Hôpitaux de Paris, Hôpital Européen Georges Pompidou, Laboratoire d'immunologie biologique, Paris, France. 4 Service des Maladies Respiratoires, Hôpital Haut-Lévêque, CHU de Bordeaux, Pessac, France. 5 Service de Chirurgie Cardiaque, Hôpital Haut-Lévêque, CHU de Bordeaux, Pessac, France. 6 Service de Transplantation Hépatique, Hôpital Pellegrin, CHU de Bordeaux, Bordeaux, France. 7 Address correspondence to: Jean-Luc Taupin, Pharm. D., Ph.D., Laboratoire d'Immunologie et Immunogénétique, Hôpital Pellegrin, CHU de Bordeaux, Place Amélie Raba Léon, 33076 Bordeaux Cedex, France.

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http://dx.doi.org/10.1097/TP.0000000000000315DOI Listing
September 2014

Phenotypic expansion of DGKE-associated diseases.

J Am Soc Nephrol 2014 Jul 7;25(7):1408-14. Epub 2014 Feb 7.

Division of Nephrology, Department of Medicine, Columbia University College of Physicians and Surgeons, New York, New York;

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http://dx.doi.org/10.1681/ASN.2013080886DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4073436PMC
July 2014

Invasive pneumococcal disease in children can reveal a primary immunodeficiency.

Clin Infect Dis 2014 Jul 23;59(2):244-51. Epub 2014 Apr 23.

Laboratory of Human Genetics of Infectious Diseases, Necker Branch, Institut National de la Santé et de la Recherche Médicale UMR1163 University Paris Descartes, Sorbonne Paris Cité, Imagine Institute, Paris, France Pediatric Hematology-Immunology Unit, Necker-Enfants Malades Hospital, Paris, France Center for the Study of Primary Immunodeficiencies, APHP, Necker Hospital, Paris, France.

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http://dx.doi.org/10.1093/cid/ciu274DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4102913PMC
July 2014

Functional evaluation of factor H genetic and acquired abnormalities: application for atypical hemolytic uremic syndrome (aHUS).

Methods Mol Biol 2014 ;1100:237-47

Cordeliers Research Center, INSERM UMRS 872, Université Pierre et Marie Curie, and Université Paris Descartes, Paris, France.

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http://dx.doi.org/10.1007/978-1-62703-724-2_19DOI Listing
June 2014

Anti-factor H autoantibodies assay.

Methods Mol Biol 2014 ;1100:249-56

Cordeliers Research Center, INSERM UMRS 872, Paris, France.

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http://dx.doi.org/10.1007/978-1-62703-724-2_20DOI Listing
June 2014

Spectrum of complement-mediated thrombotic microangiopathies: pathogenetic insights identifying novel treatment approaches.

Semin Thromb Hemost 2014 Jun 9;40(4):444-64. Epub 2014 Jun 9.

Division of Nephrology, The Hospital for Sick Children, Toronto, Ontario, Canada.

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http://dx.doi.org/10.1055/s-0034-1376153DOI Listing
June 2014

Anti-factor H autoantibody-associated hemolytic uremic syndrome: the earlier diagnosed and treated, the better.

Kidney Int 2014 May;85(5):1019-22

1] Laboratory of Immunology, Hôpital Européen Georges Pompidou, Assistance Publique-Hôpitaux de Paris, Paris, France [2] INSERM Unité Mixte de Recherche en Santé 872, Paris, France.

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http://dx.doi.org/10.1038/ki.2013.447DOI Listing
May 2014

[C3 glomerulopathy].

Nephrol Ther 2014 Apr 4;10(2):78-85. Epub 2014 Feb 4.

Laboratoire d'immunologie, hôpital Georges-Pompidou, 20, rue Leblanc, 75015 Paris, France.

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http://dx.doi.org/10.1016/j.nephro.2013.09.007DOI Listing
April 2014

Blockade of alternative complement pathway in dense deposit disease.

Case Rep Nephrol 2014 6;2014:201568. Epub 2014 Feb 6.

Service de Néphrologie Pédiatrique, Hôpital Robert Debré, 48 boulevard Sérurier, 75019 Paris, France.

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http://dx.doi.org/10.1155/2014/201568DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3932839PMC
March 2014