Publications by authors named "Ulrich Baumann"

100Publications

Outcome of chronic granulomatous disease - conventional treatment versus stem cell transplantation.

Pediatr Allergy Immunol 2020 Oct 28. Epub 2020 Oct 28.

Department of Pediatric Hematology, Oncology and Stem Cell Transplantation, Charité Universitätsmedizin - Berlin University Hospital Center, Berlin, Germany.

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http://dx.doi.org/10.1111/pai.13402DOI Listing
October 2020

COVID-19 related reduction in pediatric emergency healthcare utilization - a concerning trend.

BMC Pediatr 2020 09 7;20(1):427. Epub 2020 Sep 7.

Department of Pediatric Pneumology, Allergology, and Neonatology, Hannover Medical School, Carl-Neuberg-Straße 1, D - 30625, Hannover, Germany.

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http://dx.doi.org/10.1186/s12887-020-02303-6DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7475725PMC
September 2020

New specific HSP47 functions in collagen subfamily chaperoning.

FASEB J 2020 Jul 27. Epub 2020 Jul 27.

Faculty of Medicine, Center for Biochemistry, University of Cologne, Cologne, Germany.

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http://dx.doi.org/10.1096/fj.202000570RDOI Listing
July 2020

An apple a day won't keep the doctor away: presentation, treatment, and outcome in pediatric apple aspirations.

Pediatr Pulmonol 2020 07 22;55(7):1697-1704. Epub 2020 May 22.

Department of Pediatric Pneumology, Allergology and Neonatology, Hannover Medical School, Hannover, Germany.

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http://dx.doi.org/10.1002/ppul.24768DOI Listing
July 2020

Endoscopic Retrograde Cholangiopancreatography in Infants: Availability Under Threat: A Survey on Availability, Need, and Clinical Practice in Europe and Israel.

J Pediatr Gastroenterol Nutr 2020 08;71(2):e54-e58

Liver Unit, Birmingham Women's and Children's Hospital, Institute of Immunology and Immunotherapy, University of Birmingham, Birmingham.

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http://dx.doi.org/10.1097/MPG.0000000000002752DOI Listing
August 2020

Hepatitis-associated Aplastic Anaemia in Children.

Klin Padiatr 2020 May 19;232(3):151-158. Epub 2020 Mar 19.

Clinic for Pediatric Nephrology, Hepatology and Metabolic Disorders, Hannover Medical School, Hannover, Germany.

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http://dx.doi.org/10.1055/a-1108-1553DOI Listing
May 2020

Human STAT1 gain-of-function iPSC line from a patient suffering from chronic mucocutaneous candidiasis.

Stem Cell Res 2020 03 17;43:101713. Epub 2020 Jan 17.

JRG Translational Hematology of Congenital Diseases, Institute of Experimental Hematology, Hannover Medical School, 30625 Hannover, Germany; REBIRTH-Cluster of Excellence, Hannover Medical School, 30625 Hannover, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.scr.2020.101713DOI Listing
March 2020

Structure-Function Relationships of the Repeat Domains of RTX Toxins.

Authors:
Ulrich Baumann

Toxins (Basel) 2019 11 12;11(11). Epub 2019 Nov 12.

Institute of Biochemistry, University of Cologne, Zülpicherstrasse 47, D-50674 Cologne, Germany.

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http://dx.doi.org/10.3390/toxins11110657DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6891781PMC
November 2019

The German National Registry of Primary Immunodeficiencies (2012-2017).

Authors:
Sabine M El-Helou Anika-Kerstin Biegner Sebastian Bode Stephan R Ehl Maximilian Heeg Maria E Maccari Henrike Ritterbusch Carsten Speckmann Stephan Rusch Raphael Scheible Klaus Warnatz Faranaz Atschekzei Renata Beider Diana Ernst Stev Gerschmann Alexandra Jablonka Gudrun Mielke Reinhold E Schmidt Gesine Schürmann Georgios Sogkas Ulrich H Baumann Christian Klemann Dorothee Viemann Horst von Bernuth Renate Krüger Leif G Hanitsch Carmen M Scheibenbogen Kirsten Wittke Michael H Albert Anna Eichinger Fabian Hauck Christoph Klein Anita Rack-Hoch Franz M Sollinger Anne Avila Michael Borte Stephan Borte Maria Fasshauer Anja Hauenherm Nils Kellner Anna H Müller Anett Ülzen Peter Bader Shahrzad Bakhtiar Jae-Yun Lee Ursula Heß Ralf Schubert Sandra Wölke Stefan Zielen Sujal Ghosh Hans-Juergen Laws Jennifer Neubert Prasad T Oommen Manfred Hönig Ansgar Schulz Sandra Steinmann Klaus Schwarz Gregor Dückers Beate Lamers Vanessa Langemeyer Tim Niehues Sonu Shai Dagmar Graf Carmen Müglich Marc T Schmalzing Eva C Schwaneck Hans-Peter Tony Johannes Dirks Gabriele Haase Johannes G Liese Henner Morbach Dirk Foell Antje Hellige Helmut Wittkowski Katja Masjosthusmann Michael Mohr Linda Geberzahn Christian M Hedrich Christiane Müller Angela Rösen-Wolff Joachim Roesler Antje Zimmermann Uta Behrends Nikolaus Rieber Uwe Schauer Rupert Handgretinger Ursula Holzer Jörg Henes Lothar Kanz Christoph Boesecke Jürgen K Rockstroh Carolynne Schwarze-Zander Jan-Christian Wasmuth Dagmar Dilloo Brigitte Hülsmann Stefan Schönberger Stefan Schreiber Rainald Zeuner Tobias Ankermann Philipp von Bismarck Hans-Iko Huppertz Petra Kaiser-Labusch Johann Greil Donate Jakoby Andreas E Kulozik Markus Metzler Nora Naumann-Bartsch Bettina Sobik Norbert Graf Sabine Heine Robin Kobbe Kai Lehmberg Ingo Müller Friedrich Herrmann Gerd Horneff Ariane Klein Joachim Peitz Nadine Schmidt Stefan Bielack Ute Groß-Wieltsch Carl F Classen Jessica Klasen Peter Deutz Dirk Kamitz Lisa Lassay Klaus Tenbrock Norbert Wagner Benedikt Bernbeck Bastian Brummel Eusebia Lara-Villacanas Esther Münstermann Dominik T Schneider Nadine Tietsch Marco Westkemper Michael Weiß Christof Kramm Ingrid Kühnle Silke Kullmann Hermann Girschick Christof Specker Elisabeth Vinnemeier-Laubenthal Henriette Haenicke Claudia Schulz Lothar Schweigerer Thomas G Müller Martina Stiefel Bernd H Belohradsky Veronika Soetedjo Gerhard Kindle Bodo Grimbacher

Front Immunol 2019 19;10:1272. Epub 2019 Jul 19.

Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.3389/fimmu.2019.01272DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6659583PMC
October 2020

Impaired polysaccharide responsiveness without agammaglobulinaemia in three patients with hypomorphic mutations in Bruton Tyrosine Kinase-No detection by newborn screening for primary immunodeficiencies.

Scand J Immunol 2020 Jan 30;91(1):e12811. Epub 2019 Oct 30.

Department of Pediatric Pneumology, Immunology and Intensive Care, Charité-Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin, Humboldt-Universität zu Berlin and Berlin Institute of Health, Berlin, Germany.

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http://dx.doi.org/10.1111/sji.12811DOI Listing
January 2020

Characterization of the pleiotropic LysR-type transcription regulator LeuO of Escherichia coli.

Nucleic Acids Res 2019 08;47(14):7363-7379

Institute for Genetics, University of Cologne, Zülpicher Str. 47a, 50674 Cologne, Germany.

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http://dx.doi.org/10.1093/nar/gkz506DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6698644PMC
August 2019

Molecular determinants of the mechanism and substrate specificity of proline-proline endopeptidase-1.

J Biol Chem 2019 07 10;294(30):11525-11535. Epub 2019 Jun 10.

Department of Chemistry, Institute of Biochemistry, University of Cologne, 50674 Cologne, Germany

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http://dx.doi.org/10.1074/jbc.RA119.009029DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6663877PMC
July 2019

Listen Carefully: The Hairy Polyp as an Unusual Cause of Neonatal Stridor.

Am J Respir Crit Care Med 2019 10;200(7):924-925

Department of Pediatrics, Allergology, and Neonatology, Hannover Medical School, Hannover, Germany.

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http://dx.doi.org/10.1164/rccm.201811-2213IMDOI Listing
October 2019

EASL Recognition Award Recipient 2019: Prof. Deirdre Kelly.

Authors:
Ulrich Baumann

J Hepatol 2019 05;70(5):822-823

Paediatric Gastroenterology and Hepatology, Hannover Medical School, Hannover, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.jhep.2019.01.002DOI Listing
May 2019

Psychosocial outcome and resilience after paediatric liver transplantation in young adults.

Clin Res Hepatol Gastroenterol 2019 04 5;43(2):155-160. Epub 2019 Feb 5.

Division for Paediatric Gastroenterology and Hepatology, Centre for Paediatric and Adolescent Medicine, Department of Paediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.clinre.2018.08.017DOI Listing
April 2019

Pharmacokinetics of tacrolimus granules in pediatric de novo liver, kidney, and heart transplantation: The OPTION study.

Pediatr Transplant 2019 02 21;23(1):e13328. Epub 2019 Jan 21.

Astellas Pharma EMEA, Chertsey, Surrey, UK.

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http://dx.doi.org/10.1111/petr.13328DOI Listing
February 2019

Impact of Immunosuppression on Executive Functioning After Pediatric Liver Transplantation: An Observational Cohort Study.

J Pediatr Gastroenterol Nutr 2019 04;68(4):480-487

Department of Paediatric Gastroenterology and Hepatology, Hannover Medical School, Hannover.

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http://dx.doi.org/10.1097/MPG.0000000000002274DOI Listing
April 2019

Health-related quality of life in pre-adolescent liver transplant recipients with biliary atresia: A cross-sectional study.

Clin Res Hepatol Gastroenterol 2019 08 6;43(4):427-435. Epub 2018 Dec 6.

Transplant and regenerative medicine centre, division of pediatric gastroenterology, hepatology and nutrition, the hospital for sick children, university of Toronto, Toronto, Ontario, Canada. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S22107401183023
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http://dx.doi.org/10.1016/j.clinre.2018.10.018DOI Listing
August 2019

Steps Forward in the Management of Familial Cholestasis.

J Pediatr Gastroenterol Nutr 2019 02;68(2):155-156

Birmingham Women's and Children's Hospital, NHS Foundation Trust, University of Birmingham, Institute for Immunology and Immunotherapy, Consulting Agreements for Albireo Pharma and Shire Pharma, Birmingham, UK.

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http://dx.doi.org/10.1097/MPG.0000000000002201DOI Listing
February 2019

European paediatric non-alcoholic fatty liver disease registry (EU-PNAFLD): Design and rationale.

Contemp Clin Trials 2018 12 5;75:67-71. Epub 2018 Nov 5.

Institute of Cellular Medicine, Faculty of Medical Sciences, Newcastle University, Newcastle Upon Tyne, United Kingdom; Liver Unit, Newcastle Upon Tyne Hospitals NHS Foundation Trust, Freeman Hospital, Newcastle upon Tyne, United Kingdom.

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https://www.journals.elsevier.com/contemporary-clinical-tria
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https://linkinghub.elsevier.com/retrieve/pii/S15517144183042
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http://dx.doi.org/10.1016/j.cct.2018.11.003DOI Listing
December 2018

The Lung in Primary Immunodeficiencies: New Concepts in Infection and Inflammation.

Front Immunol 2018 8;9:1837. Epub 2018 Aug 8.

Immunodeficiency Centre for Wales, University Hospital of Wales, Cardiff, United Kingdom.

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http://dx.doi.org/10.3389/fimmu.2018.01837DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6096054PMC
September 2019

Conformational flexibility of pore loop-1 gives insights into substrate translocation by the AAA protease FtsH.

J Struct Biol 2018 11 14;204(2):199-206. Epub 2018 Aug 14.

Institute of Biochemistry, University of Cologne, Zuelpicher Str. 47, Cologne, North Rhine-Westphalia 50674, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.jsb.2018.08.009DOI Listing
November 2018

Side effects and efficacy of renal sparing immunosuppression in pediatric liver transplantation-A single center matched cohort study.

Pediatr Transplant 2018 08 5;22(5):e13207. Epub 2018 May 5.

Division of Pediatric Gastroenterology and Hepatology, Department of Pediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany.

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http://doi.wiley.com/10.1111/petr.13207
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http://dx.doi.org/10.1111/petr.13207DOI Listing
August 2018

Improved protein-crystal identification by using 2,2,2-trichloroethanol as a fluorescence enhancer.

Acta Crystallogr F Struct Biol Commun 2018 05 24;74(Pt 5):307-314. Epub 2018 Apr 24.

Institute of Biochemistry, University of Cologne, Zülpicher Strasse 47, 50674 Cologne, Germany.

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http://dx.doi.org/10.1107/S2053230X18005253DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5931144PMC
May 2018

A family of unconventional deubiquitinases with modular chain specificity determinants.

Nat Commun 2018 02 23;9(1):799. Epub 2018 Feb 23.

Institute for Genetics, University of Cologne, Zülpicher Str. 47a, 50674, Cologne, Germany.

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http://dx.doi.org/10.1038/s41467-018-03148-5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5824887PMC
February 2018

Impact of Arginine to Cysteine Mutations in Collagen II on Protein Secretion and Cell Survival.

Int J Mol Sci 2018 Feb 11;19(2). Epub 2018 Feb 11.

Center for Biochemistry, Medical Faculty, University of Cologne, 50931 Cologne, Germany.

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http://dx.doi.org/10.3390/ijms19020541DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5855763PMC
February 2018

Noninvasive Assessment of Intra-Abdominal Pressure Using Ultrasound-Guided Tonometry: A Proof-of-Concept Study.

Shock 2018 12;50(6):684-688

Department of Intensive Care Medicine, Inselspital, Bern University Hospital, University of Bern, Bern, Switzerland.

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http://dx.doi.org/10.1097/SHK.0000000000001085DOI Listing
December 2018

Impaired IFNγ-Signaling and Mycobacterial Clearance in IFNγR1-Deficient Human iPSC-Derived Macrophages.

Stem Cell Reports 2018 01 14;10(1):7-16. Epub 2017 Dec 14.

Institute of Experimental Hematology, Hannover Medical School, Carl-Neuberg-Strasse 1, 30625 Hannover, Germany; REBIRTH Cluster of Excellence, Hannover Medical School, 30625 Hannover, Germany. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S22136711173051
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http://dx.doi.org/10.1016/j.stemcr.2017.11.011DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5768914PMC
January 2018

A CK1 FRET biosensor reveals that DDX3X is an essential activator of CK1ε.

J Cell Sci 2018 01 4;131(1). Epub 2018 Jan 4.

Institute of Cell Biology, Department of Biology, University of Bern, Baltzerstrasse 4, 3012 Bern, Switzerland

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http://dx.doi.org/10.1242/jcs.207316DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5818060PMC
January 2018

Cystic Fibrosis-related Liver Disease: Research Challenges and Future Perspectives.

J Pediatr Gastroenterol Nutr 2017 10;65(4):443-448

*Pediatric Hepatology Unit, APHP-Hôpital Necker and UPMC Univ Paris 06, INSERM, UMR_S 938, Centre de Recherche Saint-Antoine, Paris, France †Digestive Health Institute, Children's Hospital Colorado and Section of Pediatric Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, University of Colorado School of Medicine Aurora, CO ‡Pediatric Gastroenterology and Hepatology, Department Pediatrics, Beatrix Children's Hospital/University Medical Center Groningen, University of Groningen, Groningen, The Netherlands §CF Center, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy ||Sorbonne Universités, UPMC Univ Paris 06, INSERM, UMR_S 938, Centre de Recherche Saint-Antoine, Institute of Cardiometabolism and Nutrition, Institut Hospitalo-Universitaire & Assistance Publique-Hôpitaux de Paris, Hôpital Saint-Antoine, Centre de Référence Maladies Rares des Maladies Inflammatoires des Voies Biliaires, Service d'Hépatologie, Paris, France ¶Department of Gastroenterology & Hepatology, Erasmus University Medical Center, Rotterdam #Center for Liver, Digestive and Metabolic Diseases, Department of Pediatrics, University of Groningen, University Medical Center Groningen, Groningen, The Netherlands **The Liver Unit, Birmingham Children's Hospital, Birmingham, UK ††Division of Gastroenterology, Hepatology & Nutrition, The Hospital for Sick Children, Department of Paediatrics, University of Toronto, Toronto, Ontario, Canada ‡‡Sorbonne Universités, UPMC Univ Paris 06, INSERM, UMR_S 938, Centre de Recherche Saint-Antoine, Institute of Cardiometabolism and Nutrition, Institut Hospitalo-Universitaire & Assistance Publique-Hôpitaux de Paris, Hôpital Pitié-Salpêtrière §§Paris-Descartes, Sorbonne Paris-Cité University, INSERM U-1223 - Pasteur Institute, and Hepatology Unit, Assistance Publique-Hôpitaux de Paris, Cochin Hospital, Paris, France ||||Division of Gastroenterology and Hepatology, Department of Internal Medicine III, Medical University of Vienna, Vienna, Austria ¶¶Department of Paediatric Gastroenterology, Hepatology and Nutrition University Hospitals Leuven, Leuven, Belgium ##Department of Paediatric Kidney, Liver and Metabolic Diseases, Division of Paediatric Gastroenterology and Hepatology, Hannover Medical School, Hannover, Germany ***Pediatric Gastroenterology, Hadassah Hebrew University Medical Center, Jerusalem, Israel.

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http://dx.doi.org/10.1097/MPG.0000000000001676DOI Listing
October 2017

Microstructure dependent binding of pigment epithelium derived factor (PEDF) to type I collagen fibrils.

J Struct Biol 2017 08 12;199(2):132-139. Epub 2017 Jun 12.

Department of Chemistry, University of Michigan, Ann Arbor, MI 48109, United States; Program in Macromolecular Science and Engineering, University of Michigan, Ann Arbor, MI 48109, United States; Department of Biomedical Engineering, University of Michigan, Ann Arbor, MI 48109, United States. Electronic address:

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http://dx.doi.org/10.1016/j.jsb.2017.06.001DOI Listing
August 2017

Inflammatory bowel disease caused by primary immunodeficiencies-Clinical presentations, review of literature, and proposal of a rational diagnostic algorithm.

Pediatr Allergy Immunol 2017 08;28(5):412-429

Department of Pediatrics and Adolescent Medicine, Faculty of Medicine, Medical Center, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1111/pai.12734DOI Listing
August 2017

Crystallographic and biochemical characterization of the dimeric architecture of site-2 protease.

Biochim Biophys Acta Biomembr 2017 Oct 11;1859(10):1859-1871. Epub 2017 May 11.

Institute of Biochemistry, University of Cologne, Otto-Fischer-Str. 14, 50674 Cologne, Germany.

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http://dx.doi.org/10.1016/j.bbamem.2017.05.006DOI Listing
October 2017

Long-term challenges and perspectives of pre-adolescent liver disease.

Lancet Gastroenterol Hepatol 2017 06;2(6):435-445

Hepatometabolic Unit, Bambino Gesù Children's Hospital, Rome, Italy. Electronic address:

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http://dx.doi.org/10.1016/S2468-1253(16)30160-1DOI Listing
June 2017

Transition after pediatric liver transplantation - Perceptions of adults, adolescents and parents.

World J Gastroenterol 2017 Apr;23(13):2365-2375

Norman Junge, Katarina Migal, Imeke Goldschmidt, Ulrich Baumann, Department of Pediatric Gastroenterology and Hepatology, Hannover Medical School, 30625 Hannover, Germany.

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http://dx.doi.org/10.3748/wjg.v23.i13.2365DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5385403PMC
April 2017

Early and Late Factors Impacting Patient and Graft Outcome in Pediatric Liver Transplantation: Summary of an ESPGHAN Monothematic Conference.

J Pediatr Gastroenterol Nutr 2017 09;65(3):e53-e59

*Swiss Center for Liver Disease in Children, University Hospitals Geneva, Geneva, Switzerland †Division of Infectious Diseases and the Transplant and Regenerative Medicine Centre, Hospital for Sick Children, University of Toronto, Toronto, Canada ‡Pediatric Nephrology, Imagine Institute, Necker-Enfants Malades Hospital, APHP, Paris Descartes University-Sorbonne Paris Cité, Paris, France §Pediatric Liver Care Center, Cincinnati Children's Hospital, Cincinnati, OH ||Department of Surgery, Ospedale Papa Giovanni XXIII, Bergamo, Italy ¶Faculté de Médecine, University de Nantes, Nantes, France #Pediatric Hepatology, Gastroenterology and Transplantation, Ospedale Papa Giovanni XXIII, Bergamo, Italy **Pediatric Hepatology Unit, Necker Enfants Malades Hospital, Paris, France ††First Department of Pediatrics, Semmelweis University, Budapest, Hungary ‡‡University Tor Vergata, Rome, Italy §§Pediatric Liver GI and Nutrition Centre, King's College Hospital, London, UK ||||Faculty of Medicine, Istanbul University, Istanbul, Turkey ¶¶Institute of Transplant Immunology, FIB-Tx, Hannover Medical School, Germany ##Abdominal Transplant Surgery, University of California San Francisco, San Francisco, CA ***Department of Pediatrics, Karolinska University Hospital, CLINTEC Karolinska Institutet, Stockholm, Sweden †††Pediatric Radiology Department, Hôpital Bicêtre, Hôpitaux Universitaires Paris Sud- Assistance Publique Hôpitaux de Paris, Le Kremlin-Bicêtre, France ‡‡‡Pediatric Hepatology and Liver Transplantation, Hospital Universitario Infantil La Paz, Madrid, Spain §§§Department of Pediatrics, University Children's Hospital Bonn, Bonn, Germany ||||||Center for Cell and Gene Therapy and Texas Children's Cancer Center, Texas Children's Hospital, Houston Methodist Hospital, Baylor College of Medicine, Houston, TX ¶¶¶Pediatric Liver GI and Nutrition Centre, King's College, London, UK ###Seattle Children's Hospital and University of Washington, Seattle, WA ****School of Cancer Sciences ††††Department of Cellular Pathology, Queen Elizabeth Hospital, University of Birmingham, Birmingham, UK ‡‡‡‡The European Transplant Registry, APHP Paul Brousse Hospital, Villejuif, France §§§§Liver Unit, Birmingham Children's Hospital, Birmingham, UK ||||||||Department of Pediatric Hematology/Oncology and Integrated Research and Treatment Center for Transplantation, Hannover Medical School, Germany ¶¶¶¶Hillman Center for Pediatric Transplantation, Children's Hospital of Pittsburgh, Pittsburgh, PA ####Department of Medicine, Surgery and Dentistry "Scuola Medica Salernitana", Section of Pediatrics, University of Salerno, Baronissi, Italy *****Bambino Gesu Children's Hospital, Rome, Italy †††††Department of Pediatric Gastroenterology, Hepatology, and Nutrition, Ege University, Izmir, Turkey ‡‡‡‡‡Pediatric Surgery and Transplantation Unit, Cliniques Universitaires de Saint-Luc, Université Catholique de Louvain, Brussels, Belgium §§§§§ISMETT, University of Pittsburgh Medical Center, Palermo, Italy ||||||||||The Children's Memorial Health Institute, Warsaw, Poland ¶¶¶¶¶Divisions of Abdominal and Transplant Surgery, Faculty of Medicine and University Hospitals Geneva, Geneva, Switzerland #####University of Salerno, Baronissi, Italy ******King's College Hospital, Institute of Liver Studies, London, UK ††††††Department for Pediatric Kidney, Liver and Metabolic Disease, Division of Pediatric Gastroenterology and Hepatology, Hannover Medical School, Hannover, Germany.

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http://dx.doi.org/10.1097/MPG.0000000000001564DOI Listing
September 2017

Attempt to Determine the Prevalence of Two Inborn Errors of Primary Bile Acid Synthesis: Results of a European Survey.

J Pediatr Gastroenterol Nutr 2017 06;64(6):864-868

*Department of Paediatrics and Adolescent Medicine, Medical University of Graz, Graz, Austria †Department of Paediatrics, CLINTEC, Karolinska University Hospital, Stockholm, Sweden ‡Paediatric Hepatology, Gastroenterology and Transplantation, Hospital Papa Giovanni XXIII, Bergamo, Italy §Pediatric Hepatology Unit, Hôpital Necker-Enfants-Malades, Paris, France ||First Department of Paediatrics, Semmelweis University, Budapest, Hungary ¶Division of Neuropediatrics and Metabolic Medicine, University Children's Hospital Heidelberg, Heidelberg, Germany #Paediatric Centre for Hepatology, Gastroenterology and Nutrition, King's College Hospital, London, UK **Pediatric Hepatology and Liver Transplantation Unit, Hôpital Bicêtre, Reference Centre for Pediatric Liver Diseases-DHU Hepatinov, Assistance Publique-Hôpitaux de Paris and INSERM UMR-S 1174, Université Paris-Sud 11, Le Kremlin-Bicêtre ††Pediatric Hepatology and Gastroenterology Unit, University Children's Hospital, Bordeaux, France ‡‡Department of Medical Sciences, Paediatric Section, University Hospital Arcispedale Sant'Anna, University of Ferrara, Ferrara, Italy §§Division of Gastroenterology/Hepatology/Nutrition, Children's Hospital of Pittsburgh of UPMC, University of Pittsburgh, Pittsburgh, PA ||||Department of Pediatrics, Pediatric Gastroenterology Unit, Azienda Ospedaliera-Universitaria Citta[Combining Grave Accent] della Salute e della Scienza di Torino, University of Torino, Torino, Italy ¶¶Department of Paediatrics, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands ##Paediatric Hepatology Service, Hospital Infantil Universitario "La Paz," Madrid, Spain ***Paediatric Gastroenterology Unit, Department of Pediatrics, University Hospitals Geneva, Geneva, Switzerland †††Division of Paediatric Gastroenterology and Hepatology, Department of Paediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany.

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http://dx.doi.org/10.1097/MPG.0000000000001546DOI Listing
June 2017

The Benefit of Sleeve Gastrectomy in Obese Adolescents on Nonalcoholic Steatohepatitis and Hepatic Fibrosis.

J Pediatr 2017 01 30;180:31-37.e2. Epub 2016 Sep 30.

Hepatometabolic Unit, Bambino Gesù Children's Hospital, Rome, Italy; Liver Research Unit, Bambino Gesù Children's Hospital, Rome, Italy. Electronic address:

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http://dx.doi.org/10.1016/j.jpeds.2016.08.101DOI Listing
January 2017

Matched-pair analysis: identification of factors with independent influence on the development of PTLD after kidney or liver transplantation.

Transplant Res 2016 2;5. Epub 2016 Aug 2.

Core Facility Quality Management & Health Technology Assessment in Transplantation, Integrated Research and Treatment Center Transplantation (IFB-Tx), Hannover Medical School, Hannover, Germany ; General, Visceral and Transplant Surgery, Hannover Medical School, Carl-Neuberg-Str. 1, 30625 Hannover, Germany.

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http://dx.doi.org/10.1186/s13737-016-0036-1DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4970231PMC
August 2016

Guideline for the Evaluation of Cholestatic Jaundice in Infants: Joint Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition and the European Society for Pediatric Gastroenterology, Hepatology, and Nutrition.

J Pediatr Gastroenterol Nutr 2017 01;64(1):154-168

*Division of Gastroenterology, Hepatology and Nutrition, Boston Children's Hospital, Harvard Medical School, Boston, MA †Division of Paediatric Gastroenterology and Hepatology, Department of Paediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany ‡Yale New Haven Hospital Transplantation Center, Yale University School of Medicine, New Haven, CT §Department of Pediatrics, Karolinska University Hospital, CLINTEC, Karolinska Institute, Stockholm, Sweden ||Paediatric Centre for Hepatology, Gastroenterology and Nutrition King's College Hospital, London, UK ¶Section of Pediatric Gastroenterology, Hepatology and Nutrition, Children's Hospital Colorado, University of Colorado School of Medicine, Aurora, CO #Swiss Center for Liver Disease in Children, University Hospitals Geneva, Geneva, Switzerland **Indiana University School of Medicine/Riley Hospital for Children, Indianapolis, IN ††Division of Pediatric Gastroenterology, Hepatology and Nutrition, Hasbro Children's Hospital, The Warren Alpert School of Medicine at Brown University, Providence, RI ‡‡Division of Pediatric Gastroenterology, Hepatology and Nutrition, The Hospital for Sick Children, University of Toronto, Toronto, Canada §§Department of Pediatrics, Emory University School of Medicine/Children's Healthcare of Atlanta, Atlanta, GA.

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http://dx.doi.org/10.1097/MPG.0000000000001334DOI Listing
January 2017

Oral Tocofersolan Corrects or Prevents Vitamin E Deficiency in Children With Chronic Cholestasis.

J Pediatr Gastroenterol Nutr 2016 12;63(6):610-615

*Pediatric Hepatology and Pediatric Liver Transplantation Unit, National Reference Centre for biliary atresia, Assistance Publique-Hôpitaux de Paris, Université Paris Sud, Hepatinov, Le Kremlin-Bicêtre, France †Center for Inherited metabolic Diseases, Karolinska University Hospital Solna, Stockholm, Sweden ‡Medical Department, Orphan Europe, Puteaux, France §Beatrix Childrens Hospital, University Medical Center Groningen, Groningen, The Netherlands ||Division of Paediatric Gastroenterology and Hepatology, Children's Hospital, Hannover Medical School, Hannover, Germany ¶Department of Paediatric Gastroenterology and Hepatology, Academisch Medisch Centrum, Amsterdam, The Netherlands #Department of Pediatric Gastroenterology and Hepatology, CHRU de Lille, Hôpital Jeanne de Flandre, Lille, France **Wilhelmina Childrens Hospital, University Medical Center Utrecht, Utrecht, The Netherlands ††INSERM U1174, Université Paris-Sud, Orsay, France.

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http://dx.doi.org/10.1097/MPG.0000000000001331DOI Listing
December 2016

Insights into Lysine Deacetylation of Natively Folded Substrate Proteins by Sirtuins.

J Biol Chem 2016 Jul 18;291(28):14677-94. Epub 2016 May 18.

From the Institute for Genetics and Cologne Excellence Cluster on Cellular Stress Responses in Aging-associated Diseases (CECAD), Joseph-Stelzmann-Strasse 26, University of Cologne, 50931 Cologne and

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http://www.jbc.org/lookup/doi/10.1074/jbc.M116.726307
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http://dx.doi.org/10.1074/jbc.M116.726307DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4938187PMC
July 2016

The pH-dependent Client Release from the Collagen-specific Chaperone HSP47 Is Triggered by a Tandem Histidine Pair.

J Biol Chem 2016 Jun 19;291(24):12612-26. Epub 2016 Apr 19.

From the Institute of Biochemistry, University of Cologne, Otto-Fischer-Strasse 12-14, D-50674 Cologne, Germany,

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http://dx.doi.org/10.1074/jbc.M115.706069DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4933464PMC
June 2016

Hepatitis E in Children: A Position Paper by the ESPGHAN Hepatology Committee.

J Pediatr Gastroenterol Nutr 2016 08;63(2):288-94

*Department of Paediatrics, CLINTEC, Karolinska Institute, Karolinska University Hospital, Stockholm, Sweden †Division of Paediatric Gastroenterology and Hepatology, Department of Paediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany ‡First Department of Paediatrics, Semmelweis University, Budapest, Hungary §Paediatric Centre for Hepatology, Gastroenterology and Nutrition, King's College Hospital, London, UK ||Paediatric Hepatology Service, Hospital Infantil Universitario "La Paz," Madrid, Spain ¶Department of Paediatrics and Adolescent Medicine, Medical University of Graz, Austria #Paediatric Gastroenterology Unit, Department of Pediatrics, University Hospitals Geneva, Switzerland **Hepatometabolic Unit, Bambino Gesu Children's Hospital, Rome, Italy ††Pediatric Gastroenterology and Hepatology Unit, IREC, Cliniques Universitaires Saint-Luc, Université Catholique de Louvain, Brussels, Belgium ‡‡Department of Paediatrics, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands §§Pediatric Hepatology Unit, Hôpital NECKER-APHP, Paris, France.

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http://dx.doi.org/10.1097/MPG.0000000000001231DOI Listing
August 2016

Circulating miR-21 and miR-29a as Markers of Disease Severity and Etiology in Cholestatic Pediatric Liver Disease.

J Clin Med 2016 Feb 25;5(3). Epub 2016 Feb 25.

Department of Paediatric Hepatology and Gastroenterology, Hannover Medical School, Carl-Neuberg-Strasse 1, Hannover 30625, Germany.

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http://dx.doi.org/10.3390/jcm5030028DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4810099PMC
February 2016

Feeding Anthrax: The Crystal Structure of Bacillus anthracis InhA Protease.

Structure 2016 Jan;24(1):1-2

Institute of Biochemistry, University of Cologne, 50674 Cologne, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.str.2015.12.002DOI Listing
January 2016

Structural and Mechanistic Insights into the Regulation of the Fundamental Rho Regulator RhoGDIα by Lysine Acetylation.

J Biol Chem 2016 Mar 30;291(11):5484-99. Epub 2015 Dec 30.

From the Institute for Genetics and Cologne Excellence Cluster on Cellular Stress Responses in Aging-associated Diseases (CECAD), Joseph-Stelzmann-Strasse 26, University of Cologne, 50931 Cologne, Germany,

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http://dx.doi.org/10.1074/jbc.M115.707091DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4786691PMC
March 2016