Stephan Ehl

Stephan Ehl

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Stephan Ehl

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Evaluating laboratory criteria for combined immunodeficiency in adult patients diagnosed with common variable immunodeficiency.

Clin Immunol 2019 Jun 17;203:59-62. Epub 2019 Apr 17.

Department for Rheumatology and Clinical Immunology and Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany; Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.clim.2019.04.001DOI Listing
June 2019

Profound immunodeficiency with severe skin disease explained by concomitant novel CARMIL2 and PLEC1 loss-of-function mutations.

Clin Immunol 2019 Jun 10. Epub 2019 Jun 10.

Institute for Immunodeficiency, Center for Chronic Immunodeficiency, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.clim.2019.06.004DOI Listing
June 2019

Disease Evolution and Response to Rapamycin in Activated Phosphoinositide 3-Kinase δ Syndrome: The European Society for Immunodeficiencies-Activated Phosphoinositide 3-Kinase δ Syndrome Registry.

Front Immunol 2018 16;9:543. Epub 2018 Mar 16.

Center for Chronic Immunodeficiency, Medical Center - University of Freiburg, Freiburg, Germany.

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http://journal.frontiersin.org/article/10.3389/fimmu.2018.00
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http://dx.doi.org/10.3389/fimmu.2018.00543DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5863269PMC
May 2019

Retroviral Gene Transfer Restores Cytotoxic Activity of T Cells Derived from Familial Hemophagocytic Lymphohistiocytosis Type 3 Patients .

Hum Gene Ther 2019 May 21. Epub 2019 May 21.

1 Institute for Transfusion Medicine and Gene Therapy, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1089/hum.2019.025DOI Listing
May 2019

Increased proportions of γδ T lymphocytes in atypical SCID associate with disease manifestations.

Clin Immunol 2019 Apr 15;201:30-34. Epub 2019 Feb 15.

Center for Chronic Immunodeficiency, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany; Center for Pediatrics and Adolescent Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.clim.2018.11.006DOI Listing
April 2019

The autoimmune targets in IPEX are dominated by gut epithelial proteins.

J Allergy Clin Immunol 2019 Apr 17. Epub 2019 Apr 17.

Center for Molecular Medicine, Department of Medicine (Solna), Karolinska Institutet, Stockholm, Sweden; Science for Life Laboratory, Department of Medical Sciences, Uppsala University, Uppsala, Sweden.

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https://linkinghub.elsevier.com/retrieve/pii/S00916749193038
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http://dx.doi.org/10.1016/j.jaci.2019.02.031DOI Listing
April 2019

The European Society for Immunodeficiencies (ESID) Registry Working Definitions for the Clinical Diagnosis of Inborn Errors of Immunity.

J Allergy Clin Immunol Pract 2019 Feb 15. Epub 2019 Feb 15.

Institute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany; Center for Pediatrics and Adolescent Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.jaip.2019.02.004DOI Listing
February 2019

Phenotype, penetrance, and treatment of 133 cytotoxic T-lymphocyte antigen 4-insufficient subjects.

J Allergy Clin Immunol 2018 Dec 4;142(6):1932-1946. Epub 2018 May 4.

Center for Chronic Immunodeficiency (CCI), Medical Center-University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany; Institute of Immunology and Transplantation, Royal Free Hospital, University College London, London, United Kingdom. Electronic address:

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http://dx.doi.org/10.1016/j.jaci.2018.02.055DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6215742PMC
December 2018

Is an infectious trigger always required for primary hemophagocytic lymphohistiocytosis? Lessons from in utero and neonatal disease.

Pediatr Blood Cancer 2018 11 1;65(11):e27344. Epub 2018 Aug 1.

Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, Freiburg, Germany.

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http://dx.doi.org/10.1002/pbc.27344DOI Listing
November 2018

T-cell gene therapy for perforin deficiency corrects cytotoxicity defects and prevents hemophagocytic lymphohistiocytosis manifestations.

J Allergy Clin Immunol 2018 Sep 31;142(3):904-913.e3. Epub 2018 Jan 31.

Infection, Immunity, Inflammation, Molecular and Cellular Immunology Section, UCL Great Ormond Street Institute of Child Health, London, United Kingdom. Electronic address:

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http://dx.doi.org/10.1016/j.jaci.2017.11.050DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6127027PMC
September 2018

CD59 deficiency presenting as polyneuropathy and Moyamoya syndrome with endothelial abnormalities of small brain vessels.

Eur J Paediatr Neurol 2018 Sep 13;22(5):870-877. Epub 2018 Apr 13.

Center for Pediatrics, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany; Center for Pediatrics, Department of Neuropediatrics and Muscle Disorders, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany.

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http://dx.doi.org/10.1016/j.ejpn.2018.04.003DOI Listing
September 2018

Recommendations for the Use of Etoposide-Based Therapy and Bone Marrow Transplantation for the Treatment of HLH: Consensus Statements by the HLH Steering Committee of the Histiocyte Society.

J Allergy Clin Immunol Pract 2018 Sep - Oct;6(5):1508-1517. Epub 2018 Jul 4.

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, and Theme of Children's and Women's Health, Karolinska University Hospital Solna, Stockholm, Sweden. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S22132198183038
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http://dx.doi.org/10.1016/j.jaip.2018.05.031DOI Listing
July 2018

T NK IL-2 Receptor γ Chain Mutation: a Challenging Diagnosis of Atypical Severe Combined Immunodeficiency.

J Clin Immunol 2018 May 9;38(4):527-536. Epub 2018 Jun 9.

Center for Chronic Immunodeficiency (CCI), University Medical Center Freiburg and Faculty of Medicine, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1007/s10875-018-0514-yDOI Listing
May 2018

Long-term follow-up of IPEX syndrome patients after different therapeutic strategies: An international multicenter retrospective study.

J Allergy Clin Immunol 2018 Mar 11;141(3):1036-1049.e5. Epub 2017 Dec 11.

Division of Stem Cell Transplantation and Regenerative Medicine, Department of Pediatrics, Stanford University School of Medicine, Stanford, Calif. Electronic address:

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http://dx.doi.org/10.1016/j.jaci.2017.10.041DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6050203PMC
March 2018

Hemophagocytic lymphohistiocytosis as presenting manifestation of profound combined immunodeficiency due to an ORAI1 mutation.

J Allergy Clin Immunol 2017 12 19;140(6):1721-1724. Epub 2017 Jun 19.

Center for Chronic Immunodeficiency, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany; Center for Pediatrics, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.jaci.2017.05.039DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5723226PMC
December 2017

Etoposide for HLH: the limits of efficacy.

Authors:
Stephan Ehl

Blood 2017 12;130(25):2692-2693

UNIVERSITY OF FREIBURG.

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http://dx.doi.org/10.1182/blood-2017-10-808543DOI Listing
December 2017

Effective Immunological Guidance of Genetic Analyses Including Exome Sequencing in Patients Evaluated for Hemophagocytic Lymphohistiocytosis.

J Clin Immunol 2017 Nov 21;37(8):770-780. Epub 2017 Sep 21.

Center for Chronic Immunodeficiency, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1007/s10875-017-0443-1DOI Listing
November 2017

IgG4-related disease in autoimmune lymphoproliferative syndrome.

Clin Immunol 2017 07 3;180:97-99. Epub 2017 May 3.

Center for Chronic Immunodeficiency, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany; Department of Rheumatology and Clinical Immunology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S15216616173004
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http://dx.doi.org/10.1016/j.clim.2017.05.003DOI Listing
July 2017

Hematopoietic stem cell transplant in patients with activated PI3K delta syndrome.

J Allergy Clin Immunol 2017 03 12;139(3):1046-1049. Epub 2016 Nov 12.

Great North Children's Hospital, Newcastle upon Tyne Hospitals NHS Foundation Trust, Newcastle upon Tyne, United Kingdom; Primary Immunodeficiency Group, Institute of Cellular Medicine, Newcastle upon Tyne University, Newcastle upon Tyne, United Kingdom.

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http://dx.doi.org/10.1016/j.jaci.2016.09.040DOI Listing
March 2017

Clinical spectrum and features of activated phosphoinositide 3-kinase δ syndrome: A large patient cohort study.

J Allergy Clin Immunol 2017 02 16;139(2):597-606.e4. Epub 2016 Jul 16.

Department of Paediatric Immunology, Newcastle upon Tyne hospitals NHS Foundation Trust, Newcastle upon Tyne, United Kingdom; Institute of Cellular Medicine, Newcastle University, Newcastle upon Tyne Hospitals NHS Trust, Newcastle upon Tyne, United Kingdom.

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http://dx.doi.org/10.1016/j.jaci.2016.06.021DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5292996PMC
February 2017

Primary and secondary hemophagocytic lymphohistiocytosis have different patterns of T-cell activation, differentiation and repertoire.

Eur J Immunol 2017 02 3;47(2):364-373. Epub 2017 Jan 3.

Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Germany.

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http://doi.wiley.com/10.1002/eji.201646686
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http://dx.doi.org/10.1002/eji.201646686DOI Listing
February 2017

Tyrosine kinase 2 is not limiting human antiviral type III interferon responses.

Eur J Immunol 2016 11 5;46(11):2639-2649. Epub 2016 Oct 5.

Center for Chronic Immunodeficiency, Faculty of Medicine, Medical Center-University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1002/eji.201646519DOI Listing
November 2016

Preserved effector functions of human ORAI1- and STIM1-deficient neutrophils.

J Allergy Clin Immunol 2016 05 6;137(5):1587-1591.e7. Epub 2015 Dec 6.

Center for Chronic Immunodeficiency, University Medical Center Freiburg, Freiburg, Germany; Center for Pediatrics and Adolescent Medicine, University Medical Center Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.jaci.2015.09.047DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4860117PMC
May 2016

Disturbed B-lymphocyte selection in autoimmune lymphoproliferative syndrome.

Blood 2016 05 23;127(18):2193-202. Epub 2016 Feb 23.

Center for Chronic Immunodeficiency and Clinic for Rheumatology and Clinical Immunology, University Medical Center, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1182/blood-2015-04-642488DOI Listing
May 2016

Transplantation from a symptomatic carrier sister restores host defenses but does not prevent colitis in NEMO deficiency.

Clin Immunol 2016 Mar 23;164:52-6. Epub 2016 Jan 23.

Center of Chronic Immunodeficiency, University Medical Center Freiburg, Germany; Center for Pediatrics and Adolescent Medicine, University Medical Center Freiburg, Germany. Electronic address:

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https://linkinghub.elsevier.com/retrieve/pii/S15216616163001
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http://dx.doi.org/10.1016/j.clim.2016.01.010DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6101191PMC
March 2016

SYK expression endows human ZAP70-deficient CD8 T cells with residual TCR signaling.

Clin Immunol 2015 Dec 14;161(2):103-9. Epub 2015 Jul 14.

Laboratory of Lymphocyte Activation and Susceptibility to EBV Infection, INSERM UMR1163, Institut IMAGINE, Paris, France; Paris Descartes University, Sorbonne Paris Cité, Imagine Institut, Paris, France. Electronic address:

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http://dx.doi.org/10.1016/j.clim.2015.07.002DOI Listing
December 2015

Omenn syndrome associated with a functional reversion due to a somatic second-site mutation in CARD11 deficiency.

Blood 2015 Oct 19;126(14):1658-69. Epub 2015 Aug 19.

Center for Chronic Immunodeficiency (CCI), University Medical Center and University of Freiburg, Freiburg, Germany; Center of Pediatric and Adolescent Medicine, University Medical Center and University of Freiburg, Freiburg, Germany;

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http://dx.doi.org/10.1182/blood-2015-03-631374DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4654427PMC
October 2015

Reversible pancytopenia and immunodeficiency in a patient with hereditary folate malabsorption.

Pediatr Blood Cancer 2015 Jun 11;62(6):1091-4. Epub 2014 Dec 11.

Department of Pediatrics and Adolescent Medicine, University Medical Center, Freiburg, Germany.

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http://dx.doi.org/10.1002/pbc.25364DOI Listing
June 2015

T cell expansion is the limiting factor of virus control in mice with attenuated TCR signaling: implications for human immunodeficiency.

J Immunol 2015 Mar 11;194(6):2725-34. Epub 2015 Feb 11.

Center for Chronic Immunodeficiency, University Medical Center Freiburg and University of Freiburg, 79106 Freiburg, Germany;

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http://dx.doi.org/10.4049/jimmunol.1400328DOI Listing
March 2015

Patients with T⁺/low NK⁺ IL-2 receptor γ chain deficiency have differentially-impaired cytokine signaling resulting in severe combined immunodeficiency.

Eur J Immunol 2014 Oct 28;44(10):3129-40. Epub 2014 Aug 28.

Center for Chronic Immunodeficiency (CCI), University Medical Center and University of Freiburg, Freiburg, Germany; Faculty of Biology, University of Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1002/eji.201444689DOI Listing
October 2014

Abnormally differentiated CD4+ or CD8+ T cells with phenotypic and genetic features of double negative T cells in human Fas deficiency.

Blood 2014 Aug 3;124(6):851-60. Epub 2014 Jun 3.

Center for Chronic Immunodeficiency, University Medical Center Freiburg and University of Freiburg, Freiburg, Germany; Center for Paediatrics and Adolescent Medicine, University Medical Center, University of Freiburg, Freiburg, Germany;

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http://dx.doi.org/10.1182/blood-2014-03-564286DOI Listing
August 2014

XIAP deficiency is a mendelian cause of late-onset IBD.

Gut 2014 Jun 10;63(6):1031-2. Epub 2013 Dec 10.

Center for Chronic Immunodeficiency, University of Freiburg, , Freiburg, Germany.

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http://dx.doi.org/10.1136/gutjnl-2013-306474DOI Listing
June 2014

Translating the genomic revolution - targeted genome editing in primates.

N Engl J Med 2014 Jun;370(24):2342-5

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http://dx.doi.org/10.1056/NEJMcibr1403629DOI Listing
June 2014

Lesson from hypomorphic recombination-activating gene (RAG) mutations: Why asymptomatic siblings should also be tested.

J Allergy Clin Immunol 2014 Apr 10;133(4):1211-5. Epub 2013 Dec 10.

Institute for Transfusion Medicine, University of Ulm, Ulm, Germany; Institute for Clinical Transfusion Medicine and Immunogenetics Ulm, German Red Cross Blood Service, Baden-Württemberg-Hessen, Germany.

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http://dx.doi.org/10.1016/j.jaci.2013.10.021DOI Listing
April 2014

Severe eczema and Hyper-IgE in Loeys-Dietz-syndrome - contribution to new findings of immune dysregulation in connective tissue disorders.

Clin Immunol 2014 Jan 19;150(1):43-50. Epub 2013 Nov 19.

Center of Chronic Immunodeficiency, University Hospital Freiburg, Freiburg, Germany. Electronic address:

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http://dx.doi.org/10.1016/j.clim.2013.11.008DOI Listing
January 2014

Deficiency of innate and acquired immunity caused by an IKBKB mutation.

N Engl J Med 2013 Dec;369(26):2504-14

From the Institute for Transfusion Medicine, University Hospital Ulm (U.P., C.L., H.S., K.S.), the Institute of Physiological Chemistry (B.B., T.W.), the Center for Biomedical Research, Genomics Core Facility (K. Holzmann), University of Ulm, and the Institute for Clinical Transfusion Medicine and Immunogenetics Ulm, German Red Cross Blood Service Baden-Wuerttemberg-Hessen (E.-M.R., H.S., K.S.), Ulm; the Center of Chronic Immunodeficiency, University Medical Center Freiburg (S.F., P.H., A.R.-E., K. Hese, M.R., A.J., M.S., S.E.), the Faculty of Biology, University of Freiburg (S.F.), the Center for Pediatrics and Adolescent Medicine (P.H., S.E.), and the Department of Rheumatology and Clinical Immunology (M.S.), University Hospital Freiburg, Freiburg; and the Translational Center for Regenerative Medicine, University of Leipzig, Leipzig (S.B.) - all in Germany; the Division of Clinical Immunology and Transfusion Medicine, Department of Laboratory Medicine, Karolinska Institute, Karolinska University Hospital Huddinge, Stockholm (S.B.); and the Department of Pediatrics, University of Saskatchewan, Saskatoon (A.R.), and the Departments of Biochemistry and Medical Genetics (T.Z.) and Pediatrics and Child Health (T.Z., M.L.S.), University of Manitoba, Winnipeg - both in Canada.

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http://dx.doi.org/10.1056/NEJMoa1309199DOI Listing
December 2013

Graded defects in cytotoxicity determine severity of hemophagocytic lymphohistiocytosis in humans and mice.

Front Immunol 2013 16;4:448. Epub 2013 Dec 16.

Centre of Chronic Immunodeficiency, University Medical Center Freiburg, University of Freiburg , Freiburg , Germany.

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http://dx.doi.org/10.3389/fimmu.2013.00448DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3864253PMC
December 2013

Syntaxin binding mechanism and disease-causing mutations in Munc18-2.

Proc Natl Acad Sci U S A 2013 Nov 5;110(47):E4482-91. Epub 2013 Nov 5.

Cambridge Institute for Medical Research, University of Cambridge Biomedical Campus, University of Cambridge, Cambridge CB2 0XY, United Kingdom.

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http://dx.doi.org/10.1073/pnas.1313474110DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3839780PMC
November 2013

Platelet secretion defect in a patient with stromal interaction molecule 1 deficiency.

Blood 2013 Nov;122(22):3696-8

Department of Pediatrics and Adolescent Medicine, University Medical Center Freiburg, Freiburg, Germany.

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http://dx.doi.org/10.1182/blood-2013-08-522037DOI Listing
November 2013

In situ evolution of virus-specific cytotoxic T cell responses in the lung.

J Virol 2013 Oct 14;87(20):11267-75. Epub 2013 Aug 14.

Centre of Chronic Immunodeficiency, University Medical Center Freiburg, Freiburg, Germany.

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http://jvi.asm.org/content/early/2013/08/08/JVI.00255-13.ful
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http://jvi.asm.org/cgi/doi/10.1128/JVI.00255-13
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http://dx.doi.org/10.1128/JVI.00255-13DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3807307PMC
October 2013

Disease-causing mutations in the XIAP BIR2 domain impair NOD2-dependent immune signalling.

EMBO Mol Med 2013 Aug 1;5(8):1278-95. Epub 2013 Jul 1.

Department of Disease Biology, Novo Nordisk Foundation Center for Protein Research, University of Copenhagen, Copenhagen, Denmark.

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http://dx.doi.org/10.1002/emmm.201303090DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3944466PMC
August 2013

Diagnostic evaluation of patients with suspected haemophagocytic lymphohistiocytosis.

Br J Haematol 2013 Feb 4;160(3):275-87. Epub 2012 Dec 4.

Department of Paediatric Haematology and Oncology, University Medical Centre, Hamburg, Germany.

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http://doi.wiley.com/10.1111/bjh.12138
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http://dx.doi.org/10.1111/bjh.12138DOI Listing
February 2013

Hemophagocytic lymphohistiocytosis in syntaxin-11-deficient mice: T-cell exhaustion limits fatal disease.

Blood 2013 Jan 27;121(4):604-13. Epub 2012 Nov 27.

Institute for Medical Microbiology and Hygiene, Department of Immunology, University of Freiburg, Freiburg, Germany.

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http://www.bloodjournal.org/cgi/doi/10.1182/blood-2012-07-44
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http://dx.doi.org/10.1182/blood-2012-07-441139DOI Listing
January 2013

Semi-automatic determination of cell surface areas used in systems biology.

Front Biosci (Elite Ed) 2013 Jan 1;5:533-45. Epub 2013 Jan 1.

BIOSS Centre for Biological Signaling Studies, University of Freiburg, Germany.

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January 2013

Massive monoclonal expansion of CD4 T-cells specific for a Mycobacterium tuberculosis ESAT-6 peptide.

Eur Respir J 2012 Jul 20;40(1):152-60. Epub 2012 Jan 20.

Dept of Transplant and Infection Immunology, Saarland University, Homburg, Germany.

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http://dx.doi.org/10.1183/09031936.00175611DOI Listing
July 2012

Recent advances in the diagnosis and treatment of hemophagocytic lymphohistiocytosis.

Arthritis Res Ther 2012 Jun 8;14(3):213. Epub 2012 Jun 8.

Centre of Chronic Immunodeficiency, University Medical Center Freiburg, D-79106 Freiburg, Germany.

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http://arthritis-research.biomedcentral.com/articles/10.1186
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http://dx.doi.org/10.1186/ar3843DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3446494PMC
June 2012

Clinical and immunological manifestations of patients with atypical severe combined immunodeficiency.

Clin Immunol 2011 Oct 30;141(1):73-82. Epub 2011 May 30.

Centre of Chronic Immunodeficiency, University Hospital Freiburg, Breisacher Str. 117, D-79106 Freiburg, Germany.

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http://dx.doi.org/10.1016/j.clim.2011.05.007DOI Listing
October 2011

A novel single point mutation of the LYST gene in two siblings with different phenotypic features of Chediak Higashi syndrome.

Pediatr Blood Cancer 2011 Jul 4;56(7):1136-9. Epub 2011 Feb 4.

Pediatric Hematology Unit of the Department of Pediatrics, Medical School of Gazi University, Ankara, Turkey.

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http://dx.doi.org/10.1002/pbc.22878DOI Listing
July 2011