Publications by authors named "Shanmuganathan Chandrakasan"

47Publications

Impact of autoimmune cytopenias on severity of childhood-onset systemic lupus erythematosus: A single-center retrospective cohort study.

Lupus 2020 Oct 27:961203320969806. Epub 2020 Oct 27.

Department of Pediatrics, Division of Pediatric Rheumatology, Emory University School of Medicine and Children's Healthcare of Atlanta, Georgia, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1177/0961203320969806DOI Listing
October 2020

Experience with a Reduced Toxicity Allogeneic Transplant Regimen for Non-CGD Primary Immune Deficiencies Requiring Myeloablation.

J Clin Immunol 2020 Oct 16. Epub 2020 Oct 16.

Division of Bone Marrow Transplantation and Immune Deficiency, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, MLC 7015, Cincinnati, OH, 45229, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-020-00888-2DOI Listing
October 2020

Severe Pediatric COVID-19 Presenting With Respiratory Failure and Severe Thrombocytopenia.

Pediatrics 2020 07 4;146(1). Epub 2020 May 4.

Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta and School of Medicine, Emory University, Atlanta, Georgia;

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1542/peds.2020-1437DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7329259PMC
July 2020

Lentiviral Gene Therapy for Familial Hemophagocytic Lymphohistiocytosis Type 3, Caused by Genetic Defects.

Hum Gene Ther 2020 Jun;31(11-12):626-638

Cell and Gene Therapy Program, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Atlanta, Georgia, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1089/hum.2019.329DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7310202PMC
June 2020

Early Onset Granulomatous Colitis Associated with a Mutation in NCF4 Resolved with Hematopoietic Stem Cell Transplantation.

J Pediatr 2019 07 23;210:220-225. Epub 2019 Apr 23.

Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Emory University School of Medicine, Atlanta, GA; Pediatric Institute, Children's Healthcare of Atlanta, Atlanta, GA. Electronic address:

View Article

Download full-text PDF

Source
https://linkinghub.elsevier.com/retrieve/pii/S00223476193039
Publisher Site
http://dx.doi.org/10.1016/j.jpeds.2019.03.042DOI Listing
July 2019

Outcomes and Treatment Strategies for Autoimmunity and Hyperinflammation in Patients with RAG Deficiency.

J Allergy Clin Immunol Pract 2019 Jul - Aug;7(6):1970-1985.e4. Epub 2019 Mar 12.

University of South Florida and Johns Hopkins All Children's Hospital, Saint Petersburg, Fla; Division of Allergy and Immunology, Massachusetts General Hospital for Children, Boston, Mass. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaip.2019.02.038DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6612449PMC
September 2020

Primary immune regulatory disorders for the pediatric hematologist and oncologist: A case-based review.

Pediatr Blood Cancer 2019 05 29;66(5):e27619. Epub 2019 Jan 29.

Department of Hematology, Children's Hospital of Orange County, Orange, California.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/pbc.27619DOI Listing
May 2019

Update on Advances in Hematopoietic Cell Transplantation for Primary Immunodeficiency Disorders.

Immunol Allergy Clin North Am 2019 02 1;39(1):113-128. Epub 2018 Nov 1.

Division of Bone Marrow Transplant, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, 2015 Uppergate Drive, ECC Room 418, Atlanta, GA 30030, USA. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.iac.2018.08.003DOI Listing
February 2019

Hypogammaglobulinemia with decreased class-switched B-cells and dysregulated T-follicular-helper cells in IPEX syndrome.

Clin Immunol 2018 12 24;197:219-223. Epub 2018 Oct 24.

Division of Bone Marrow Transplant, Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, Atlanta, GA, USA. Electronic address:

View Article

Download full-text PDF

Source
https://linkinghub.elsevier.com/retrieve/pii/S15216616183047
Publisher Site
http://dx.doi.org/10.1016/j.clim.2018.10.005DOI Listing
December 2018

Severe Congenital Neutropenia associated with SRP54 mutation in 22q11.2 Deletion Syndrome: Hematopoietic Stem Cell Transplantation Results in Correction of Neutropenia with Adequate Immune Reconstitution.

J Clin Immunol 2018 07 29;38(5):546-549. Epub 2018 Jun 29.

Aflac Cancer and Blood Disorders Center, Children's Healthcare of Atlanta, Emory University School of Medicine, 2015 Uppergate Drive, ECC Room 418, Atlanta, GA, 30030, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-018-0518-7DOI Listing
July 2018

Revisiting Type 1 Diabetes as a Comorbidity in Patients with Juvenile Idiopathic Arthritis.

J Pediatr 2018 01;192:6-7

Department of Pediatrics Emory University School of Medicine Children's Healthcare of Atlanta Atlanta, Georgia. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpeds.2017.09.067DOI Listing
January 2018

KIT blockade is sufficient for donor hematopoietic stem cell engraftment in Fanconi anemia mice.

Blood 2017 02 20;129(8):1048-1052. Epub 2016 Dec 20.

Division of Experimental Hematology/Cancer Biology, Cancer and Blood Institute.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1182/blood-2015-12-689083DOI Listing
February 2017

Nonclassic Inflammatory Bowel Disease in Young Infants: Immune Dysregulation, Polyendocrinopathy, Enteropathy, X-Linked Syndrome, and Other Disorders.

Pediatr Clin North Am 2017 Feb;64(1):139-160

Department of Pediatrics, Children's Health Care of Atlanta, Emory University School of Medicine, Atlanta, GA, USA; Division of Gastroenterology, Emory University School of Medicine, Atlanta, GA, USA. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.pcl.2016.08.010DOI Listing
February 2017

Atypical haemolytic uraemic syndrome in a patient with sickle cell disease, successfully treated with eculizumab.

Br J Haematol 2016 11 21;175(4):744-747. Epub 2015 Dec 21.

Division of Haematology, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/bjh.13884DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5545798PMC
November 2016

Outcome of patients with NEMO deficiency following allogeneic hematopoietic cell transplant.

J Allergy Clin Immunol 2017 03 12;139(3):1040-1043.e2. Epub 2016 Oct 12.

Division of Bone Marrow Transplantation and Immune Deficiency, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaci.2016.08.039DOI Listing
March 2017

Pathogenesis of Hemophagocytic Lymphohistiocytosis.

Hematol Oncol Clin North Am 2015 Oct 21;29(5):895-902. Epub 2015 Aug 21.

Immunodeficiency and Histiocytosis Program, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Avenue, Cincinnati, OH 45229-3039, USA. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.hoc.2015.06.007DOI Listing
October 2015

The use of a Berlin Heart EXCOR LVAD in a child receiving chemotherapy for Castleman's disease.

Pediatr Transplant 2015 Feb 1;19(1):E15-8. Epub 2014 Dec 1.

The Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/petr.12398DOI Listing
February 2015

Reduced-intensity conditioning hematopoietic cell transplantation is an effective treatment for patients with SLAM-associated protein deficiency/X-linked lymphoproliferative disease type 1.

Biol Blood Marrow Transplant 2014 Oct 9;20(10):1641-5. Epub 2014 Jun 9.

Division of Bone Marrow Transplantation and Immune Deficiency, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital, Cincinnati, Ohio.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.bbmt.2014.06.003DOI Listing
October 2014

Gene therapy for hemoglobinopathies: the state of the field and the future.

Hematol Oncol Clin North Am 2014 Apr;28(2):199-216

Division of Experimental Hematology/Cancer Biology, Cincinnati Children's Research Foundation, Cancer and Blood Institute (CBDI), Cincinnati Children's Hospital Medical Center (CCHMC), 3333 Burnet Avenue, Cincinnati, OH 45229, USA; Division of Hematology, Cincinnati Children's Research Foundation, Cancer and Blood Institute (CBDI), Cincinnati Children's Hospital Medical Center (CCHMC), 3333 Burnet Avenue, Cincinnati, OH 45229, USA. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.hoc.2013.12.003DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4167426PMC
April 2014

Iron-refractory microcytic anemia as the presenting feature of unicentric Castleman disease in children.

J Pediatr 2014 Apr 22;164(4):928-30. Epub 2013 Dec 22.

Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpeds.2013.11.026DOI Listing
April 2014

Hemophagocytic lymphohistiocytosis: advances in pathophysiology, diagnosis, and treatment.

J Pediatr 2013 Nov 15;163(5):1253-9. Epub 2013 Aug 15.

Division of Bone Marrow Transplantation and Immune Deficiency Cincinnati Children's Hospital Medical Center, Cincinnati, OH. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jpeds.2013.06.053DOI Listing
November 2013

Granulomatosis with polyangiitis presenting as Henoch-Schönlein purpura in children.

J Clin Rheumatol 2013 Jun;19(4):199-202

Pediatric Residency Program, Wayne State University School of Medicine, Children's Hospital of Michigan, Detroit, MI, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1097/RHU.0b013e318293aff5DOI Listing
June 2013

Risk factors and management of deep venous thrombosis in children following post-surgical hypopituitarism in craniopharyngioma.

Pediatr Blood Cancer 2011 Jul 10;57(1):175-7. Epub 2011 Feb 10.

Carman and Ann Adams Department of Pediatrics, Children's Hospital of Michigan, Wayne State University, Detroit, Michigan, USA.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/pbc.22937DOI Listing
July 2011

Malignant fibrous histiocytoma two years after autologous stem cell transplant for Hodgkin lymphoma: evidence for genomic instability.

Pediatr Blood Cancer 2011 Jul 18;56(7):1143-5. Epub 2011 Feb 18.

Division of Pediatric Hematology Oncology, Children's Hospital of Michigan, Wayne State University, Detroit, Michigan.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/pbc.22929DOI Listing
July 2011

Wiskott-Aldrich syndrome presenting with early onset recurrent acute hemorrhagic edema and hyperostosis.

Pediatr Blood Cancer 2011 Jul 23;56(7):1130-2. Epub 2011 Feb 23.

Division of Pediatric Allergy and Immunology, Department of Pediatrics, Postgraduate Institute of Medical Education and Research, Chandigarh, India.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/pbc.22888DOI Listing
July 2011

Macrophage activation syndrome in children with systemic onset juvenile idiopathic arthritis: clinical experience from northwest India.

Rheumatol Int 2012 Apr 11;32(4):881-6. Epub 2011 Jan 11.

Pediatric Allergy Immunology Unit, Department of Pediatrics, Advanced Pediatrics Centre, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00296-010-1711-zDOI Listing
April 2012

Anasarca as the presenting manifestation of parvovirus B19 associated juvenile dermatomyositis.

Rheumatol Int 2009 Mar 20;29(5):565-7. Epub 2008 Sep 20.

Postgraduate Institute of Medical Education and Research, Chandigarh, India.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00296-008-0702-9DOI Listing
March 2009