Robert R Montgomery

Robert R Montgomery

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Robert R Montgomery

Robert R Montgomery

Publications by authors named "Robert R Montgomery"

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How we approach: Training pediatric coagulationists.

Pediatr Blood Cancer 2019 Sep 5:e27982. Epub 2019 Sep 5.

Departments of Pediatrics and Pathology, University of Michigan, Ann Arbor, Michigan.

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http://dx.doi.org/10.1002/pbc.27982DOI Listing
September 2019

The impact of GPIbα on platelet-targeted FVIII gene therapy in hemophilia A mice with pre-existing anti-FVIII immunity.

J Thromb Haemost 2019 Mar 3;17(3):449-459. Epub 2019 Feb 3.

Blood Research Institute, BloodCenter of Wisconsin, Milwaukee, WI, USA.

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http://dx.doi.org/10.1111/jth.14379DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6397061PMC
March 2019

What have we learned from large population studies of von Willebrand disease?

Hematology Am Soc Hematol Educ Program 2016 Dec;2016(1):670-677

Blood Research Institute, BloodCenter of Wisconsin and Department of Pediatrics, Medical College of Wisconsin, Milwaukee, WI.

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http://dx.doi.org/10.1182/asheducation-2016.1.670DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5518316PMC
December 2016

Life in the shadow of a dominant partner: the FVIII-VWF association and its clinical implications for hemophilia A.

Blood 2016 10 1;128(16):2007-2016. Epub 2016 Sep 1.

Department of Pathology and Molecular Medicine, Queens University, Kingston, ON, Canada.

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http://dx.doi.org/10.1182/blood-2016-04-713289DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5073181PMC
October 2016

The immunogenicity of platelet-derived FVIII in hemophilia A mice with or without preexisting anti-FVIII immunity.

Blood 2016 Mar 14;127(10):1346-54. Epub 2015 Dec 14.

Blood Research Institute, BloodCenter of Wisconsin, Milwaukee, WI; Department of Pediatrics, Medical College of Wisconsin, Milwaukee, WI; Children's Research Institute, Children's Hospital of Wisconsin, Milwaukee, WI; and Midwest Athletes Against Childhood Cancer Research Center, Milwaukee, WI.

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http://dx.doi.org/10.1182/blood-2015-08-662916DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4786841PMC
March 2016

The heads and the tails of malaria and VWF.

Blood 2016 Mar;127(9):1081-2

BLOODCENTER OF WISCONSIN.

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http://dx.doi.org/10.1182/blood-2015-11-679878DOI Listing
March 2016

Corrigendum to "Characterization of Zebrafish von Willebrand Factor Reveals Conservation of Domain Structure, Multimerization, and Intracellular Storage".

Adv Hematol 2015 19;2015:526854. Epub 2015 Aug 19.

Department of Pediatrics, University of Michigan, Room 8301 Medical Science Research Building III, 1150 W. Medical Center Drive, Ann Arbor, MI 48109-5646, USA.

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http://dx.doi.org/10.1155/2015/526854DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4556866PMC
October 2015

Crucial role for the VWF A1 domain in binding to type IV collagen.

Blood 2015 Apr 6;125(14):2297-304. Epub 2015 Feb 6.

Department of Pediatrics, Division of Hematology/Oncology, Medical College of Wisconsin, Milwaukee, WI; Children's Research Institute, Children's Hospital of Wisconsin, Milwaukee, WI; Blood Research Institute, BloodCenter of Wisconsin, Milwaukee, WI; and.

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http://dx.doi.org/10.1182/blood-2014-11-610824DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4383803PMC
April 2015

A conditional knockout mouse model reveals endothelial cells as the principal and possibly exclusive source of plasma factor VIII.

Blood 2014 Jun 4;123(24):3706-13. Epub 2014 Apr 4.

Blood Research Institute, BloodCenter of Wisconsin, Milwaukee, WI; Medical College of Wisconsin, Milwaukee, WI; and Children's Research Institute, Children's Hospital of Wisconsin, Milwaukee, WI.

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http://dx.doi.org/10.1182/blood-2014-02-555151DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4055921PMC
June 2014

Markers of vascular perturbation correlate with airway structural change in asthma.

Am J Respir Crit Care Med 2013 Jul;188(2):167-78

Department of Biomolecular Chemistry, University of Wisconsin, 4285A Medical Sciences Center, 1300 University Avenue, Madison, WI 53706, USA.

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http://dx.doi.org/10.1164/rccm.201301-0185OCDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3778758PMC
July 2013

Collagen binding provides a sensitive screen for variant von Willebrand disease.

Clin Chem 2013 Apr 22;59(4):684-91. Epub 2013 Jan 22.

Department of Pediatrics, Division of Hematology and Oncology, Medical College of Wisconsin, Milwaukee, WI, USA.

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http://dx.doi.org/10.1373/clinchem.2012.199000DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3852672PMC
April 2013

Platelet and endothelial expression of clotting factors for the treatment of hemophilia.

Thromb Res 2012 May 14;129 Suppl 2:S46-8. Epub 2012 Mar 14.

Blood Research Institute of BloodCenter of Wisconsin and Medical College of Wisconsin, Milwaukee, WI, USA.

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http://dx.doi.org/10.1016/j.thromres.2012.02.031DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3581347PMC
May 2012

Correction of murine Bernard-Soulier syndrome by lentivirus-mediated gene therapy.

Mol Ther 2012 Mar 1;20(3):625-32. Epub 2011 Nov 1.

Blood Research Institute, Blood Center of Wisconsin, Milwaukee, Wisconsin 53226, USA.

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http://dx.doi.org/10.1038/mt.2011.231DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3293608PMC
March 2012

Von Willebrand disease in the United States: a perspective from Wisconsin.

Semin Thromb Hemost 2011 Jul 18;37(5):528-34. Epub 2011 Nov 18.

Division of Hematology/Oncology, Department of Pediatrics, Medical College of Wisconsin, Wisconsin 53201-2178, USA.

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http://dx.doi.org/10.1055/s-0031-1281039DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3807766PMC
July 2011

Alternative strategies for gene therapy of hemophilia.

Hematology Am Soc Hematol Educ Program 2010 ;2010:197-202

Blood Research Institute, BloodCenter of Wisconsin, Milwaukee, WI, USA.

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http://dx.doi.org/10.1182/asheducation-2010.1.197DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3383974PMC
April 2011

Platelets as delivery systems for disease treatments.

Adv Drug Deliv Rev 2010 Sep 7;62(12):1196-203. Epub 2010 Jul 7.

Blood Research Institute, BloodCenter of Wisconsin, Departments of Pediatrics, Medical College of Wisconsin, Children's Hospital of Wisconsin, Milwaukee, USA.

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http://dx.doi.org/10.1016/j.addr.2010.06.007DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2991519PMC
September 2010

Clinical and laboratory diagnosis of von Willebrand disease: a synopsis of the 2008 NHLBI/NIH guidelines.

Am J Hematol 2009 Jun;84(6):366-70

Department of Laboratory Medicine and Pathology, Division of Hematopathology, Special Coagulation Laboratory, College of Medicine, Mayo Clinic, Rochester, Minnesota 55905, USA.

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http://dx.doi.org/10.1002/ajh.21405DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5592788PMC
June 2009

At least type VWD2B is a discrete variant of VWD, isn't it?

Blood 2009 Jan;113(3):501

Bloodcenter of Wisconsin, USA.

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http://dx.doi.org/10.1182/blood-2008-11-184531DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2628358PMC
January 2009

Factor VIII ectopically targeted to platelets is therapeutic in hemophilia A with high-titer inhibitory antibodies.

J Clin Invest 2006 Jul;116(7):1974-82

Blood Research Institute, BloodCenter of Wisconsin, Department of Pediatrics, Medical College of Wisconsin, and Children's Research Institute, Children's Hospital of Wisconsin, Milwaukee, Wisconsin 53226, USA.

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http://dx.doi.org/10.1172/JCI28416DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1483176PMC
July 2006

Intracellular interaction of von Willebrand factor and factor VIII depends on cellular context: lessons from platelet-expressed factor VIII.

Blood 2005 Jun 24;105(12):4674-6. Epub 2005 Feb 24.

Department of Pediatrics, Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.

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http://www.bloodjournal.org/cgi/doi/10.1182/blood-2004-12-47
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http://dx.doi.org/10.1182/blood-2004-12-4701DOI Listing
June 2005

von Willebrand factor: the new treatment paradigm--introduction.

Blood Coagul Fibrinolysis 2005 Apr;16 Suppl 1:S1-2

Haemophilia Centre and Haemostasis Unit, Royal Free Hospital, London, UK.

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http://dx.doi.org/10.1097/01.mbc.0000167655.00391.caDOI Listing
April 2005

Re-establishment of VWF-dependent Weibel-Palade bodies in VWD endothelial cells.

Blood 2005 Jan 26;105(1):145-52. Epub 2004 Aug 26.

Department of Pediatrics, Medical College of Wisconsin, Milwaukee 53226, USA.

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http://dx.doi.org/10.1182/blood-2004-02-0464DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3938105PMC
January 2005

Factor VIII ectopically expressed in platelets: efficacy in hemophilia A treatment.

Blood 2003 Dec 24;102(12):4006-13. Epub 2003 Jul 24.

The Children's Hospital of Philadelphia, 1 Civic Center, ARC, Rm 317, Philadelphia, PA 19104, USA.

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http://dx.doi.org/10.1182/blood-2003-05-1519DOI Listing
December 2003

PECAM-1 negatively regulates GPIb/V/IX signaling in murine platelets.

Blood 2003 Nov 31;102(10):3658-64. Epub 2003 Jul 31.

Blood Research Institute, The Blood Center of Southeastern Wisconsin, PO Box 2178, 638 N 18th St, Milwaukee, WI 53201, USA.

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http://dx.doi.org/10.1182/blood-2003-06-1888DOI Listing
November 2003

Critical independent regions in the VWF propeptide and mature VWF that enable normal VWF storage.

Blood 2003 Feb 10;101(4):1384-91. Epub 2002 Oct 10.

Department of Pediatrics, Medical College of Wisconsin, Milwaukee 53226, USA.

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http://dx.doi.org/10.1182/blood-2002-07-2281DOI Listing
February 2003

The role of the D1 domain of the von Willebrand factor propeptide in multimerization of VWF.

Blood 2002 Sep;100(5):1699-706

Blood Research Institute, The Blood Center of Southeastern Wisconsin, Milwaukee, USA.

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http://dx.doi.org/10.1182/blood-2002-03-0789DOI Listing
September 2002

The cysteine knot of platelet glycoprotein Ib beta (GPIb beta) is critical for the interaction of GPIb beta with GPIX.

Blood 2002 Jun;99(12):4428-33

Blood Research Institute, the Blood Center of Southeastern Wisconsin, Milwaukee, 53226-0509, USA.

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http://dx.doi.org/10.1182/blood.v99.12.4428DOI Listing
June 2002

The von Willebrand factor propeptide (VWFpp) traffics an unrelated protein to storage.

Arterioscler Thromb Vasc Biol 2002 Jun;22(6):921-6

Blood Research Institute, The Blood Center of Southeastern Wisconsin, Milwaukee, USA.

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http://dx.doi.org/10.1161/01.atv.0000017063.36768.87DOI Listing
June 2002