Patrick J McKiernan

Patrick J McKiernan

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Patrick J McKiernan

Patrick J McKiernan

Publications by authors named "Patrick J McKiernan"

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Evolving Trends in Liver Transplant for Metabolic Liver Disease in the United States.

Liver Transpl 2019 Jun 15;25(6):911-921. Epub 2019 Apr 15.

Hillman Center for Pediatric Transplantation, University of Pittsburgh, Pittsburgh, PA.

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http://dx.doi.org/10.1002/lt.25433DOI Listing
June 2019

A novel mutation in gene causing a milder ARC syndrome phenotype with prolonged survival.

JIMD Rep 2019 May 22;47(1):4-8. Epub 2019 Mar 22.

Pediatric Hepatology Children's Hospital of Pittsburgh of UPMC, University of Pittsburgh Medical Center Pittsburgh Pennsylvania.

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http://dx.doi.org/10.1002/jmd2.12027DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6498830PMC
May 2019

Hepatopulmonary Syndrome in Children: A 20-Year Review of Presenting Symptoms, Clinical Progression, and Transplant Outcome.

Liver Transpl 2018 09;24(9):1271-1279

The Liver Unit, Birmingham Women's and Children's Hospitals National Health Service Foundation Trust, Birmingham, United Kingdom.

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http://dx.doi.org/10.1002/lt.25296DOI Listing
September 2018

Transjugular Intrahepatic Portosystemic Shunt Insertion for the Management of Portal Hypertension in Children.

J Pediatr Gastroenterol Nutr 2018 08;67(2):173-179

Radiology Department, Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.

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http://Insights.ovid.com/crossref?an=00005176-201808000-0000
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http://dx.doi.org/10.1097/MPG.0000000000002006DOI Listing
August 2018

Daily variation of NTBC and its relation to succinylacetone in tyrosinemia type 1 patients comparing a single dose to two doses a day.

J Inherit Metab Dis 2018 03 23;41(2):181-186. Epub 2017 Nov 23.

Department of Metabolic Diseases, Beatrix Children's Hospital, University Medical Center Groningen, University of Groningen, Hanzeplein 1, 9700 RB, Groningen, The Netherlands.

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http://dx.doi.org/10.1007/s10545-017-0112-9DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5830494PMC
March 2018

What Is the Best Blood Sampling Time for Metabolic Control of Phenylalanine and Tyrosine Concentrations in Tyrosinemia Type 1 Patients?

JIMD Rep 2017 25;36:49-57. Epub 2017 Jan 25.

Department of Pediatrics, University of Groningen, University Medical Center Groningen, Beatrix Children's Hospital, Groningen, The Netherlands.

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http://dx.doi.org/10.1007/8904_2016_37DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5680281PMC
January 2017

Glycogen storage disease type III: diagnosis, genotype, management, clinical course and outcome.

J Inherit Metab Dis 2016 09 22;39(5):697-704. Epub 2016 Apr 22.

Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center Groningen, PO Box 30 001, 9700 RB, Groningen, The Netherlands.

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http://dx.doi.org/10.1007/s10545-016-9932-2DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4987401PMC
September 2016

Interobserver Agreement on Endoscopic Classification of Oesophageal Varices in Children.

J Pediatr Gastroenterol Nutr 2015 Aug;61(2):176-81

*Paediatric Hepatology, Gastroenterology and Transplantation, Hospital Papa Giovanni XXIII, Bergamo †Paediatric Surgery, Hospital Niguarda Ca' Granda, Milan ‡Paediatric Gastrointestinal Surgery and Endoscopy, Ospedale Pediatrico Bambino Gesù, Rome, Italy §Department of Paediatric Surgery, King's College Hospital, London ||Liver Unit, Birmingham Children's Hospital, Birmingham, UK ¶Gastroenterology Unit, Department of Paediatrics, University Hospitals, Geneva, Switzerland #Gastrointestinal Endoscopy, Hospital Papa Giovanni XXIII, Bergamo, Italy **Pediatric Gastroenterology, Hepatology and Nutrition, Istanbul University and School of Medicine ††Department of Pediatric Gastroenterology, Hepatology and Nutrition, Hospital Necker-Enfants Malades, University of Paris-René Descartes, Paris, France ‡‡Paediatric Gastroenterology and Hepatology, University Hospital for Children and Adolescents, University of Tuebingen, Germany §§Gastroenterology Diagnostics Unit, Children's Health Memorial Institute, Warsaw, Poland ||||Liver Transplantation and Hepatobiliary Medicine, Royal Free Hospital, London, UK. †Deceased.

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http://dx.doi.org/10.1097/MPG.0000000000000822DOI Listing
August 2015

Early nitisinone treatment reduces the need for liver transplantation in children with tyrosinaemia type 1 and improves post-transplant renal function.

J Inherit Metab Dis 2014 Sep 11;37(5):745-52. Epub 2014 Feb 11.

NIHR Biomedical Research Unit and Centre for Liver Research, University of Birmingham, 5th floor IBR, Birmingham, B15 2TT, UK,

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http://dx.doi.org/10.1007/s10545-014-9683-xDOI Listing
September 2014

Population pharmacokinetic and pharmacogenetic analysis of tacrolimus in paediatric liver transplant patients.

Br J Clin Pharmacol 2014 Jan;77(1):130-40

Clinical and Practice Research Group, School of Pharmacy, Medical Biology Centre, Queen's University Belfast, Belfast, UK.

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http://dx.doi.org/10.1111/bcp.12174DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3895354PMC
January 2014

Phenotypic variation and long-term outcome in children with congenital hepatic fibrosis.

J Pediatr Gastroenterol Nutr 2013 Aug;57(2):161-6

Department of Hepatology †Department of Nephrology, Birmingham Children's Hospital, Birmingham, UK.

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http://dx.doi.org/10.1097/MPG.0b013e318291e72bDOI Listing
August 2013

Changing strategies for organ transplantation in atypical haemolytic uraemic syndrome: a tertiary case series.

Pediatr Transplant 2013 May 6;17(3):E93-9. Epub 2013 Mar 6.

Department of Nephrology, Birmingham Children's Hospital NHS Foundation Trust, Birmingham, UK.

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http://dx.doi.org/10.1111/petr.12066DOI Listing
May 2013

Plasma succinylacetone is persistently raised after liver transplantation in tyrosinaemia type 1.

J Inherit Metab Dis 2013 Jan 29;36(1):15-20. Epub 2012 Mar 29.

NIHR Biomedical Research Unit and Centre for Liver Research, University of Birmingham, 5th floor IBR, Birmingham B15 2TT, UK.

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http://dx.doi.org/10.1007/s10545-012-9482-1DOI Listing
January 2013

Long-term follow-up of children with 6-thioguanine-related chronic hepatoxicity following treatment for acute lymphoblastic leukaemia.

J Pediatr Gastroenterol Nutr 2011 Nov;53(5):478-9

Department of Hepatology, Birmingham Children's Hospital, Birmingham, UK.

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http://dx.doi.org/10.1097/MPG.0b013e31822960e9DOI Listing
November 2011

ABO-incompatible pediatric liver transplantation in very small recipients: Birmingham's experience.

Pediatr Transplant 2011 Nov 15;15(7):706-11. Epub 2011 Jul 15.

Liver Unit, Birmingham Children's Hospital, Birmingham, UK.

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http://dx.doi.org/10.1111/j.1399-3046.2011.01541.xDOI Listing
November 2011

Primary prophylaxis of variceal hemorrhage in children with portal hypertension: a framework for future research.

J Pediatr Gastroenterol Nutr 2011 Mar;52(3):254-61

Division of Gastroenterology, Hepatology & Nutrition, The Hospital for Sick Children, Toronto, Ontario, Canada.

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http://dx.doi.org/10.1097/MPG.0b013e318205993aDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3728696PMC
March 2011

Pre-emptive liver transplantation for primary hyperoxaluria (PH-I) arrests long-term renal function deterioration.

Nephrol Dial Transplant 2011 Jan 23;26(1):354-9. Epub 2010 Jun 23.

Liver Unit, Birmingham Children’s Hospital NHS Foundation Trust, Birmingham B4 6NH, UK.

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http://dx.doi.org/10.1093/ndt/gfq353DOI Listing
January 2011

Gallbladder dysfunction in cholesterol ester storage disease.

J Pediatr Gastroenterol Nutr 2010 May;50(5):555-8

Birmingham Children's Hospital, Liver Unit, Birmingham, UK.

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http://dx.doi.org/10.1097/MPG.0b013e31819f659bDOI Listing
May 2010

Childhood autoimmune liver disease: indications and outcome of liver transplantation.

J Pediatr Gastroenterol Nutr 2010 Mar;50(3):295-302

Department of Paediatrics, University of Malaya Medical Centre, Kuala Lumpur, Malaysia.

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http://dx.doi.org/10.1097/MPG.0b013e3181bf0ef7DOI Listing
March 2010

Influence of ABCB1 polymorphisms and haplotypes on tacrolimus nephrotoxicity and dosage requirements in children with liver transplant.

Br J Clin Pharmacol 2009 Sep;68(3):413-21

Clinical and Practice Research Group, School of Pharmacy, Medical Biology Centre, Queen's University Belfast, 97 Lisburn Road, BT97BL Belfast, UK.

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http://dx.doi.org/10.1111/j.1365-2125.2009.03461.xDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2766481PMC
September 2009

Improved outcomes of combined liver and kidney transplants in small children (<15 kg).

Transplantation 2009 Sep;88(5):711-5

The Liver Unit, University Hospital Birmingham NHS Trust, Queen Elizabeth Hospital, Edgbaston, Birmingham, United Kingdom.

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http://dx.doi.org/10.1097/TP.0b013e3181b29f0cDOI Listing
September 2009

Renal function recovery in children undergoing combined liver kidney transplants.

Transplantation 2009 May;87(10):1584-9

The Liver Unit, University Hospital Birmingham NHS Trust, Queen Elizabeth Hospital, Edgbaston, Birmingham, United Kingdom.

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http://dx.doi.org/10.1097/TP.0b013e3181a4e710DOI Listing
May 2009

The role of endoscopic ultrasound for evaluating portal hypertension in children being assessed for intestinal transplantation.

Transplantation 2008 Nov;86(10):1470-3

Liver Unit, Birmingham Children's Hospital, Birmingham, United Kingdom.

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https://insights.ovid.com/crossref?an=00007890-200811270-000
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http://dx.doi.org/10.1097/TP.0b013e3181891d63DOI Listing
November 2008

Neonatal classical galactosaemia presenting as citrin deficiency.

J Hepatol 2008 Sep 9;49(3):463; author reply 464. Epub 2008 Jul 9.

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http://dx.doi.org/10.1016/j.jhep.2008.06.014DOI Listing
September 2008

Paediatric Hepatology Dependency score (PHD score): an audit tool.

J Pediatr Gastroenterol Nutr 2007 Jan;44(1):108-15

The Liver Unit, The Institute of Child Health, Birmingham Children's Hospital, Birmingham, UK.

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http://dx.doi.org/10.1097/01.mpg.0000243427.86345.25DOI Listing
January 2007

Immunosuppression in infants with short bowel syndrome undergoing isolated liver transplantation.

Pediatr Transplant 2006 Sep;10(6):677-81

The Liver Unit, Birmingham Children's Hospital (BCH), Birmingham, UK.

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http://dx.doi.org/10.1111/j.1399-3046.2006.00504.xDOI Listing
September 2006

Visual loss and idiopathic intracranial hypertension in children with Alagille syndrome.

J Pediatr Gastroenterol Nutr 2006 Sep;43(3):348-52

Liver Unit, Birmingham Children's Hospital, Birmingham, UK.

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http://dx.doi.org/10.1097/01.mpg.0000221895.51748.44DOI Listing
September 2006

Nitisinone in the treatment of hereditary tyrosinaemia type 1.

Drugs 2006 ;66(6):743-50

Liver Unit, Children's Hospital NHS Trust, Birmingham, UK.

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http://dx.doi.org/10.2165/00003495-200666060-00002DOI Listing
August 2006

Lectin-reactive alpha-fetoprotein in patients with tyrosinemia type I and hepatocellular carcinoma.

J Pediatr Gastroenterol Nutr 2006 Jul;43(1):77-82

Children's Hospital, University of Essen, Essen, Germany.

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http://dx.doi.org/10.1097/01.mpg.0000228112.29359.f8DOI Listing
July 2006

The trouble with biopsies...

J Pediatr Gastroenterol Nutr 2006 Jul;43(1):122

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http://dx.doi.org/10.1097/01.mpg.0000226375.18494.5dDOI Listing
July 2006

Progressive histological damage in liver allografts following pediatric liver transplantation.

Hepatology 2006 May;43(5):1109-17

Liver Unit, Birmingham Children's Hospital, Birmingham, United Kingdom.

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http://dx.doi.org/10.1002/hep.21152DOI Listing
May 2006

Requirement of VPS33B, a member of the Sec1/Munc18 protein family, in megakaryocyte and platelet alpha-granule biogenesis.

Blood 2005 Dec 25;106(13):4159-66. Epub 2005 Aug 25.

Department of Paediatrics, Division of Clinical and Metabolic Genetics, Programme in Cell Biology, The Hospital for Sick Children, University of Toronto, 555 University Ave, Toronto, ON, M5G 1X8, Canada.

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http://www.bloodjournal.org/cgi/doi/10.1182/blood-2005-04-13
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http://dx.doi.org/10.1182/blood-2005-04-1356DOI Listing
December 2005

Portal vein cavernoma associated with goldenhar syndrome.

J Pediatr Gastroenterol Nutr 2005 Sep;41(3):368-70

Children's Liver and GI Unit, St James's University Hospital, Leeds, United Kingdom.

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http://dx.doi.org/10.1097/01.mpg.0000174333.85463.4fDOI Listing
September 2005

Mycophenolate mofetil for renal dysfunction after pediatric liver transplantation.

Transplantation 2005 Jun;79(11):1575-80

The Liver Unit, Birmingham Children's Hospital, Birmingham B4 6NH, UK.

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http://dx.doi.org/10.1097/01.tp.0000163504.29054.3fDOI Listing
June 2005

Histiocytic sarcoma with interdigitating dendritic cell differentiation.

J Pediatr Hematol Oncol 2004 Dec;26(12):827-30

Liver Unit, Birmingham Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.

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December 2004

Safety and efficacy of octreotide in the immediate control of oesophageal variceal bleeding.

J Pediatr Gastroenterol Nutr 2004 Oct;39(4):437-8; author reply 438

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http://dx.doi.org/10.1097/00005176-200410000-00029DOI Listing
October 2004

Acute fatty liver disease after suprasellar tumor resection.

J Pediatr Gastroenterol Nutr 2004 Sep;39(3):288-91

The Liver Unit, Birmingham Children's Hospital, The Royal Hospital for Sick Children, Bristol, UK.

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http://dx.doi.org/10.1097/00005176-200409000-00012DOI Listing
September 2004

Difficult management choices for infants with short bowel syndrome and liver failure.

J Pediatr Gastroenterol Nutr 2002 Aug;35(2):216-9

The Liver Unit, Birmingham Childrens Hospital NHS Trust, United Kingdom.

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http://dx.doi.org/10.1097/00005176-200208000-00022DOI Listing
August 2002

A prospective study of endoscopic esophageal variceal ligation using a multiband ligator.

J Pediatr Gastroenterol Nutr 2002 Feb;34(2):207-11

Liver Unit, Birmingham Children's Hospital National Health Service Trust, Birmingham, United Kingdom.

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http://dx.doi.org/10.1097/00005176-200202000-00019DOI Listing
February 2002