Matthew F Starost

Matthew F Starost

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Matthew F Starost

Matthew F Starost

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NPC1 Deficiency in Mice is Associated with Fetal Growth Restriction, Neonatal Lethality and Abnormal Lung Pathology.

J Clin Med 2019 Dec 19;9(1). Epub 2019 Dec 19.

Genomics, Development and Disease Section, Genetic Disease Research Branch, NHGRI, NIH, Bethesda, MD, 20892, USA.

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http://dx.doi.org/10.3390/jcm9010012DOI Listing
December 2019

Gene therapy prevents hepatic tumor initiation in murine glycogen storage disease type Ia at the tumor-developing stage.

J Inherit Metab Dis 2019 05 6;42(3):459-469. Epub 2019 Mar 6.

Section on Cellular Differentiation, Division of Translational Medicine, Eunice Kennedy Shriver National Institute of Child Health and Human Development, Bethesda, Maryland.

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http://dx.doi.org/10.1002/jimd.12056DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6483852PMC
May 2019

Suppression of Wnt/β-catenin signaling by EGF receptor is required for hair follicle development.

Mol Biol Cell 2018 11 6;29(22):2784-2799. Epub 2018 Sep 6.

Division of Biotechnology Review and Research IV, Office of Biotechnology Products, Office of Pharmaceutical Quality, Center for Drug Evaluation and Research, Food and Drug Administration, Silver Spring, MD 20993.

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http://dx.doi.org/10.1091/mbc.E18-08-0488DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6249831PMC
November 2018

Mouse Homolog of the Human R337H Mutation Reveals Its Role in Tumorigenesis.

Cancer Res 2018 09 24;78(18):5375-5383. Epub 2018 Jul 24.

Cardiovascular Branch, National Heart, Lung, and Blood Institute, NIH, Bethesda, Maryland.

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http://dx.doi.org/10.1158/0008-5472.CAN-18-0016DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6139041PMC
September 2018

Liver-directed gene therapy for murine glycogen storage disease type Ib.

Hum Mol Genet 2017 11;26(22):4395-4405

Section on Cellular Differentiation, Eunice Kennedy Shriver National Institute of Child Health and Human Development.

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http://dx.doi.org/10.1093/hmg/ddx325DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5886224PMC
November 2017

Glycogen storage disease type Ia mice with less than 2% of normal hepatic glucose-6-phosphatase-α activity restored are at risk of developing hepatic tumors.

Mol Genet Metab 2017 03 10;120(3):229-234. Epub 2017 Jan 10.

Section on Cellular Differentiation, Eunice Kennedy Shriver National Institute of Child Health and Human Development, United States. Electronic address:

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http://dx.doi.org/10.1016/j.ymgme.2017.01.003DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5346453PMC
March 2017

Celecoxib treatment of fibrous dysplasia (FD) in a human FD cell line and FD-like lesions in mice with protein kinase A (PKA) defects.

Mol Cell Endocrinol 2017 01 4;439:165-174. Epub 2016 Aug 4.

Section on Endocrinology and Genetics (SEGEN), Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health (NIH), Bethesda, MD 20892, USA. Electronic address:

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http://dx.doi.org/10.1016/j.mce.2016.08.004DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5123938PMC
January 2017

Studies of mice with cyclic AMP-dependent protein kinase (PKA) defects reveal the critical role of PKA's catalytic subunits in anxiety.

Behav Brain Res 2016 07 16;307:1-10. Epub 2016 Mar 16.

Section on Endocrinology and Genetics, Program in Developmental Endocrinology and Genetics, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health (NIH), Bethesda, MD 20892, United States.

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http://dx.doi.org/10.1016/j.bbr.2016.03.001DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4853257PMC
July 2016

Galnt1 is required for normal heart valve development and cardiac function.

PLoS One 2015 23;10(1):e0115861. Epub 2015 Jan 23.

Section on Biological Chemistry, National Institute of Dental and Craniofacial Research, National Institutes of Health, Bethesda, United States of America.

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http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0115861PLOS
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4304789PMC
May 2016

Celecoxib reduces glucocorticoids in vitro and in a mouse model with adrenocortical hyperplasia.

Endocr Relat Cancer 2016 Jan 5;23(1):15-25. Epub 2015 Oct 5.

Section on Endocrinology and Genetics (SEGEN)Program on Developmental Endocrinology and Genetics (PDEGEN), Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, 10 Center Drive, Building 10-Clinical Research Center, Room 1-3330, Bethesda, Maryland 20892, USAOffice of Research Services (ORS)Division of Veterinary Resources (DVR), Office of the Director (OD), National Institutes of Health, Bethesda, Maryland 20892, USACNRS UMR6247Génétique Reproduction et Développement, Clermont Université, Aubière, France.

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http://dx.doi.org/10.1530/ERC-15-0472DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4659722PMC
January 2016

Haploinsufficiency for either one of the type-II regulatory subunits of protein kinase A improves the bone phenotype of Prkar1a+/- mice.

Hum Mol Genet 2015 Nov 5;24(21):6080-92. Epub 2015 Aug 5.

Section on Endocrinology and Genetics (SEGEN), Program on Developmental Endocrinology & Genetics (PDEGEN), Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD),

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http://dx.doi.org/10.1093/hmg/ddv320DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4599668PMC
November 2015

Hematopoietic neoplasms in Prkar2a-deficient mice.

J Exp Clin Cancer Res 2015 Nov 25;34:143. Epub 2015 Nov 25.

Section on Endocrinology and Genetics, Program on Developmental Endocrinology & Genetics (PDEGEN) & Pediatric Endocrinology Inter-institute Training Program, Eunice Kennedy Shriver National Institute of Child Health & Human Development (NICHD), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.

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http://dx.doi.org/10.1186/s13046-015-0257-zDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4660639PMC
November 2015

Late multiple organ surge in interferon-regulated target genes characterizes staphylococcal enterotoxin B lethality.

PLoS One 2014 13;9(2):e88756. Epub 2014 Feb 13.

Functional Genomics and Proteomics Facility, Critical Care Medicine Department, Clinical Research Center, National Institutes of Health, Bethesda, Maryland, United States of America.

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http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0088756PLOS
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3923834PMC
October 2014

A null mutation of mouse Kcna10 causes significant vestibular and mild hearing dysfunction.

Hear Res 2013 Jun 22;300:1-9. Epub 2013 Mar 22.

Section on Human Genetics, Laboratory of Molecular Genetics, National Institute on Deafness and Other Communication Disorders, National Institutes of Health, 5 Research Ct, 2A-19, Rockville, MD 20850, USA.

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http://dx.doi.org/10.1016/j.heares.2013.02.009DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3684051PMC
June 2013

Ambient oxygen promotes tumorigenesis.

PLoS One 2011 May 12;6(5):e19785. Epub 2011 May 12.

Center for Molecular Medicine, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, Maryland, United States of America.

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http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0019785PLOS
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3093396PMC
May 2011

Splenic angioleiomyoma in an owl monkey (Aotus nancymae).

J Med Primatol 2010 Dec;39(6):385-8

Comparative Medicine Branch, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD 20892, USA.

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http://doi.wiley.com/10.1111/j.1600-0684.2010.00425.x
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http://dx.doi.org/10.1111/j.1600-0684.2010.00425.xDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2943549PMC
December 2010

Identification of small molecules that suppress microRNA function and reverse tumorigenesis.

J Biol Chem 2010 Aug 7;285(32):24707-16. Epub 2010 Jun 7.

Molecular Virology Section, Laboratory of Molecular Microbiology, NIAID, National Institutes of Health, Bethesda, Maryland 20892, USA.

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http://dx.doi.org/10.1074/jbc.M109.062976DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2915707PMC
August 2010

Alternate protein kinase A activity identifies a unique population of stromal cells in adult bone.

Proc Natl Acad Sci U S A 2010 May 26;107(19):8683-8. Epub 2010 Apr 26.

Section on Endocrinology and Genetics, Program on Developmental Endocrinology and Genetics and Pediatric Endocrinology Inter-institute Training Program, Eunice Kennedy Shriver National Institute of Child Health and Human Development, National Institutes of Health, Bethesda, MD 20892, USA.

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http://www.pnas.org/content/107/19/8683.full.pdf
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http://www.pnas.org/cgi/doi/10.1073/pnas.1003680107
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http://dx.doi.org/10.1073/pnas.1003680107DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2889322PMC
May 2010

Mouse Prkar1a haploinsufficiency leads to an increase in tumors in the Trp53+/- or Rb1+/- backgrounds and chemically induced skin papillomas by dysregulation of the cell cycle and Wnt signaling.

Hum Mol Genet 2010 Apr 15;19(8):1387-98. Epub 2010 Jan 15.

Section on Endocrinology and Genetics, Program on Developmental Endocrinology and Genetics, Eunice KennedyShriver, National Institute of Child Health and Human Development, National Institutes of Health, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1093/hmg/ddq014DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2846157PMC
April 2010

Normoglycemia alone is insufficient to prevent long-term complications of hepatocellular adenoma in glycogen storage disease type Ib mice.

J Hepatol 2009 Nov 5;51(5):909-17. Epub 2009 Feb 5.

Section on Cellular Differentiation, Program on Developmental Endocrinology and Genetics, National Institute of Child Health and Human Development, Bethesda, MD 20892-1830, USA.

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http://dx.doi.org/10.1016/j.jhep.2008.11.026DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2762018PMC
November 2009

Adenomyofibroma of the fimbria in a cynomolgus monkey (Macaca fascicularis).

J Vet Diagn Invest 2009 Nov;21(6):892-4

National Institutes of Health, Division of Veterinary Resources, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1177/104063870902100624DOI Listing
November 2009

Neuronal M3 muscarinic acetylcholine receptors are essential for somatotroph proliferation and normal somatic growth.

Proc Natl Acad Sci U S A 2009 Apr 30;106(15):6398-403. Epub 2009 Mar 30.

Molecular Signaling Section, Laboratory of Bioorganic Chemistry, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1073/pnas.0900977106DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2662962PMC
April 2009

Ring expanded nucleoside analogues inhibit RNA helicase and intracellular human immunodeficiency virus type 1 replication.

J Med Chem 2008 Aug 5;51(16):5043-51. Epub 2008 Aug 5.

Molecular Virology Section, Laboratory of Molecular Microbiology, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, Maryland 20892, USA.

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http://dx.doi.org/10.1021/jm800332mDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2537995PMC
August 2008

Acalculous and clostridial cholecystitis in a pig.

J Vet Diagn Invest 2008 Jul;20(4):527-30

Division of Veterinary Resources, National Institutes of Health, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1177/104063870802000422DOI Listing
July 2008

Necrotic foci, elevated chemokines and infiltrating neutrophils in the liver of glycogen storage disease type Ia.

J Hepatol 2008 Mar 28;48(3):479-85. Epub 2007 Dec 28.

Section on Cellular Differentiation, National Institute of Child Health and Human Development, NIH, Bethesda, MD 20892-1830, USA.

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http://linkinghub.elsevier.com/retrieve/pii/S016882780700644
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http://dx.doi.org/10.1016/j.jhep.2007.11.014DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2744599PMC
March 2008

Inflammatory cardiac valvulitis in TAX1BP1-deficient mice through selective NF-kappaB activation.

EMBO J 2008 Feb 31;27(4):629-41. Epub 2008 Jan 31.

Laboratory of Molecular Microbiology, Molecular Virology Section, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD 20892-0460, USA.

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http://dx.doi.org/10.1038/emboj.2008.5DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2262037PMC
February 2008

Deafness and stria vascularis defects in S1P2 receptor-null mice.

J Biol Chem 2007 Apr 6;282(14):10690-6. Epub 2007 Feb 6.

Genetics of Development and Disease Branch, NIDDK, National Institutes of Health, Bethesda, Maryland 20892-1821, USA.

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http://dx.doi.org/10.1074/jbc.M700370200DOI Listing
April 2007

Selenoprotein expression is essential in endothelial cell development and cardiac muscle function.

Neuromuscul Disord 2007 Feb 4;17(2):135-42. Epub 2006 Dec 4.

Molecular Biology of Selenium Section, Laboratory of Cancer Prevention, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1016/j.nmd.2006.10.006DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1894657PMC
February 2007

TEL-AML1 transgenic zebrafish model of precursor B cell acute lymphoblastic leukemia.

Proc Natl Acad Sci U S A 2006 Oct 2;103(41):15166-71. Epub 2006 Oct 2.

Experimental Transplantation and Immunology Branch, Center for Cancer Research, National Cancer Institute, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1073/pnas.0603349103DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1622794PMC
October 2006

Reproductive capability in dogs with canine leukocyte adhesion deficiency treated with nonmyeloablative conditioning prior to allogeneic hematopoietic stem cell transplantation.

Blood 2006 Sep 27;108(5):1767-9. Epub 2006 Apr 27.

Division of Veterinary Resources, Office of Research Services, National Institutes of Health, 9000 Rockville Pike, Bldg 28, Rm 104, Bethesda, MD 20892-0001, USA.

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http://dx.doi.org/10.1182/blood-2006-02-005645DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1553182PMC
September 2006

Runx1 deficiency predisposes mice to T-lymphoblastic lymphoma.

Blood 2005 Nov 28;106(10):3621-4. Epub 2005 Jul 28.

Genetics and Molecular Biology Branch and Genetic Diseases Research Branch, National Human Genome Research Institute, National Institutes of Health, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1182/blood-2005-04-1447DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1459843PMC
November 2005

First description of a new species of Demodex (Acari: Demodecidae) from rhesus monkey.

J Med Entomol 2005 Nov;42(6):948-52

National Institutes of Health, Division of Veterinary Resources, Health Surveillance, Parasitology, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1093/jmedent/42.6.948DOI Listing
November 2005

Nonmyeloablative conditioning with busulfan before matched littermate bone marrow transplantation results in reversal of the disease phenotype in canine leukocyte adhesion deficiency.

Biol Blood Marrow Transplant 2005 Oct;11(10):755-63

Experimental Transplantation and Immunology Branch, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Bethesda, Maryland 20892, USA.

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http://dx.doi.org/10.1016/j.bbmt.2005.07.011DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1351378PMC
October 2005

Demodex spp. in the hair follicles of rhesus macaques (Macaca mulatta).

J Med Primatol 2005 Aug;34(4):215-8

National Institutes of Health, division of Veterinary Resources, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1111/j.1600-0684.2005.00112.xDOI Listing
August 2005

Nonmyeloablative hematopoietic stem cell transplantation corrects the disease phenotype in the canine model of leukocyte adhesion deficiency.

Exp Hematol 2005 Jun;33(6):706-12

Experimental Transplantation and Immunology Branch, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Bethesda, MD 20892-1203, USA.

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http://dx.doi.org/10.1016/j.exphem.2005.03.010DOI Listing
June 2005

IDEC-131 (anti-CD154), sirolimus and donor-specific transfusion facilitate operational tolerance in non-human primates.

Am J Transplant 2005 May;5(5):1032-41

Transplantation Branch, National Institute of Diabetes, Digestive and Kidney Diseases, National Institutes of Health, Department of Health and Human Services, Bethesda, Maryland, USA.

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http://dx.doi.org/10.1111/j.1600-6143.2005.00796.xDOI Listing
May 2005

Identification and characterization of SSTK, a serine/threonine protein kinase essential for male fertility.

Mol Cell Biol 2005 May;25(10):4250-61

Division of Therapeutic Proteins, Center for Drug Evaluation and Research, Food and Drug Administration, HFD-122, Bldg. 29A, Rm. 3B-20, 8800 Rockville Pike, Bethesda, Maryland 20892, USA.

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http://mcb.asm.org/cgi/doi/10.1128/MCB.25.10.4250-4261.2005
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http://dx.doi.org/10.1128/MCB.25.10.4250-4261.2005DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1087724PMC
May 2005

Xanthine oxidoreductase is an endogenous regulator of cyclooxygenase-2.

Circ Res 2004 Nov 4;95(11):1118-24. Epub 2004 Nov 4.

Cardiovascular Branch, National Heart, Lung, and Blood Institute, NIH, Bethesda, Md 20892-1622, USA.

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http://dx.doi.org/10.1161/01.RES.0000149571.96304.36DOI Listing
November 2004

The genetic immunodeficiency disease, leukocyte adhesion deficiency, in humans, dogs, cattle, and mice.

Comp Med 2004 Aug;54(4):363-72

Experimental Transplantation and Immunology, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Bethesda, Maryland 20892, USA.

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August 2004

Canine leukocyte adhesion deficiency colony for investigation of novel hematopoietic therapies.

Vet Immunol Immunopathol 2003 Jul;94(1-2):11-22

Experimental Transplantation and Immunology Branch, Center for Cancer Research, National Cancer Institute, National Institutes of Health, Building 10, Rm 12C-116, 10 Center Drive, Bethesda, MD 20892, USA.

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http://dx.doi.org/10.1016/s0165-2427(03)00057-6DOI Listing
July 2003

Oral administration of the citrus coumarin, isopimpinellin, blocks DNA adduct formation and skin tumor initiation by 7,12-dimethylbenz[a]anthracene in SENCAR mice.

Carcinogenesis 2002 Oct;23(10):1667-75

University of Texas M.D. Anderson Cancer Center, Science Park-Research Division, Department of Carcinogenesis, PO Box 389, Smithville, TX 78957, USA.

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http://dx.doi.org/10.1093/carcin/23.10.1667DOI Listing
October 2002

Adenoma of the gallbladder in a chimpanzee (Pan troglodytes).

J Zoo Wildl Med 2002 Jun;33(2):176-7

Department of Veterinary Sciences, The University of Texas M. D. Anderson Cancer Center, Bastrop 78602, USA.

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http://www.bioone.org/doi/abs/10.1638/1042-7260(2002)033%5B0
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http://dx.doi.org/10.1638/1042-7260(2002)033[0176:AOTGIA]2.0.CO;2DOI Listing
June 2002