Publications by authors named "Matthew C Kiernan"

100Publications

Spinal muscular atrophy - the dawning of a new era.

Nat Rev Neurol 2020 Sep 25. Epub 2020 Sep 25.

Brain & Mind Centre and Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1038/s41582-020-00410-7DOI Listing
September 2020

Metabolomic insights into neurodegene-rative disease.

J Neurol Neurosurg Psychiatry 2020 Sep 14. Epub 2020 Sep 14.

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia

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http://dx.doi.org/10.1136/jnnp-2020-324856DOI Listing
September 2020

Treating adults with spinal muscular atrophy with nusinersen.

J Neurol Neurosurg Psychiatry 2020 Nov 11;91(11):1139. Epub 2020 Sep 11.

Brain and Mind Centre, The University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2020-324036DOI Listing
November 2020

Isaacs syndrome: the frontier of neurology, psychiatry, immunology and cancer.

J Neurol Neurosurg Psychiatry 2020 Sep 2. Epub 2020 Sep 2.

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2020-324675DOI Listing
September 2020

Identity by descent analysis identifies founder events and links familial and sporadic ALS cases.

NPJ Genom Med 2020 7;5:32. Epub 2020 Aug 7.

Macquarie University Centre for Motor Neuron Disease Research, Department of Biological Sciences, Faculty of Medicine, Health and Human Sciences, Macquarie University, Sydney, NSW Australia.

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http://dx.doi.org/10.1038/s41525-020-00139-8DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7414871PMC
August 2020

Fatal cerebellar oedema in adult Leigh syndrome.

Pract Neurol 2020 08 17;20(4):336-337. Epub 2020 Jul 17.

Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, Australia.

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http://dx.doi.org/10.1136/practneurol-2019-002409DOI Listing
August 2020

Amyotrophic lateral sclerosis: a new diagnostic paradigm.

J Neurol Neurosurg Psychiatry 2020 Sep 23;91(9):903-904. Epub 2020 Jun 23.

Institute of Clinical Neurosciences, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2020-324006DOI Listing
September 2020

Consensus for experimental design in electromyography (CEDE) project: Amplitude normalization matrix.

J Electromyogr Kinesiol 2020 Aug 10;53:102438. Epub 2020 Jun 10.

School of Health and Rehabilitation Sciences, The University of Queensland, Brisbane, Australia; School of Biomedical Sciences, The University of Queensland, Brisbane, Australia.

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http://dx.doi.org/10.1016/j.jelekin.2020.102438DOI Listing
August 2020

Evidence for polygenic and oligogenic basis of Australian sporadic amyotrophic lateral sclerosis.

J Med Genet 2020 May 14. Epub 2020 May 14.

Macquarie University Centre for Motor Neuron Disease Research, Department of Biomedical Sciences, Faculty of Medicine and Health Sciences, Macquarie University, Sydney, New South Wales, Australia

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http://dx.doi.org/10.1136/jmedgenet-2020-106866DOI Listing
May 2020

Interrogating interneurone function using threshold tracking of the H reflex in healthy subjects and patients with motor neurone disease.

Clin Neurophysiol 2020 Aug 13;131(8):1986-1996. Epub 2020 Apr 13.

Department of Neurology, Royal Prince Alfred Hospital and The University of Sydney, N.S.W. 2006, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2020.03.028DOI Listing
August 2020

Cortical hyperexcitability evolves with disease progression in ALS.

Ann Clin Transl Neurol 2020 05 18;7(5):733-741. Epub 2020 Apr 18.

Westmead Clinical School, University of Sydney, Sydney, NSW, Australia.

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http://dx.doi.org/10.1002/acn3.51039DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7261748PMC
May 2020

Electrophysiological and phenotypic profiles of taxane-induced neuropathy.

Clin Neurophysiol 2020 Aug 2;131(8):1979-1985. Epub 2020 Apr 2.

Brain and Mind Centre, Faculty of Medicine and Health, University of Sydney, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2020.02.028DOI Listing
August 2020

Phenotypic variability in ALS-FTD and effect on survival.

Neurology 2020 05 10;94(19):e2005-e2013. Epub 2020 Apr 10.

From the Memory and Cognition Clinic, Department of Clinical Neurosciences (R.M.A., M.C.K.), Royal Prince Alfred Hospital; Central Sydney Medical School and Brain & Mind Centre (R.M.A., E.M.D., J.R.H., M.C.K.) and School of Psychology and Brain & Mind Centre (C.S.-B., O.P.), The University of Sydney; and ARC Centre of Excellence of Cognition and its Disorders (C.S.-B., O.P.), Sydney, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000009398DOI Listing
May 2020

A novel phenotype of hereditary spastic paraplegia type 7 associated with a compound heterozygous mutation in paraplegin.

Muscle Nerve 2020 07 18;62(1):E44-E45. Epub 2020 Apr 18.

Brain and Mind Centre, Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1002/mus.26882DOI Listing
July 2020

Subacute sensory neuronopathy and cancer: the identification of paraneoplastic syndromes.

J Neurol Neurosurg Psychiatry 2020 Aug 3;91(8):793-794. Epub 2020 Apr 3.

Department of Neurology, Johns Hopkins University, Baltimore, Maryland, USA.

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http://dx.doi.org/10.1136/jnnp-2020-323171DOI Listing
August 2020

Interneuronal networks mediate cortical inhibition and facilitation.

Clin Neurophysiol 2020 May 3;131(5):1000-1010. Epub 2020 Mar 3.

Westmead Clinical School, University of Sydney, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2020.02.012DOI Listing
May 2020

Health, wellbeing and lived experiences of adults with SMA: a scoping systematic review.

Orphanet J Rare Dis 2020 03 12;15(1):70. Epub 2020 Mar 12.

Discipline of Paediatrics, School of Women's and Children's Health, UNSW Medicine, UNSW Sydney, Sydney, NSW, 2031, Australia.

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http://dx.doi.org/10.1186/s13023-020-1339-3DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7068910PMC
March 2020

Queen Square: a history of the National Hospital and its Institute of Neurology.

J Neurol Neurosurg Psychiatry 2020 May 4;91(5):560-561. Epub 2020 Mar 4.

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia

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http://dx.doi.org/10.1136/jnnp-2020-322776DOI Listing
May 2020

The centenary milestone award 2020.

J Neurol Neurosurg Psychiatry 2020 Jul 2;91(7):677. Epub 2020 Mar 2.

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia

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http://dx.doi.org/10.1136/jnnp-2020-322976DOI Listing
July 2020

Regional callosal integrity and bilaterality of limb weakness in amyotrophic lateral sclerosis.

Amyotroph Lateral Scler Frontotemporal Degener 2020 08 28;21(5-6):396-402. Epub 2020 Feb 28.

Wellcome Centre for Integrative Neuroimaging, University of Oxford, Oxford, UK.

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http://dx.doi.org/10.1080/21678421.2020.1733020DOI Listing
August 2020

ALS is a multistep process in South Korean, Japanese, and Australian patients.

Neurology 2020 04 18;94(15):e1657-e1663. Epub 2020 Feb 18.

From the Westmead Clinical School (S.V., M.H., P.M.), University of Sydney, Australia; Department of Neurology (N.A.), Nagoya University Graduate School of Medicine (G.S.); The National Institute of Public Health (Y.D.), Wako-shi; Chiba University Graduate School of Medicine (S.K.), Japan; Department of Neurology (S.H.K., K.-W.O., J.P.), Hanyang University Hospital; Department of Health Sciences (I.K., E.M.K.), Hanyang University Graduate School; Department of Occupational and Environmental Medicine (I.K.), College of Medicine, Hanyang University, Seoul, Republic of Korea; Geelong Hospital (P.T.); and Brain and Mind Centre (M.C.K.), University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000009015DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7251515PMC
April 2020

Occasional essay: Upper motor neuron syndrome in amyotrophic lateral sclerosis.

J Neurol Neurosurg Psychiatry 2020 03;91(3):227-234

University of Sydney and Department of Neurology, Royal Prince Alfred Hospital, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2019-321938DOI Listing
March 2020

The impact of cognitive and behavioral impairment in amyotrophic lateral sclerosis.

Expert Rev Neurother 2020 03 14;20(3):281-293. Epub 2020 Feb 14.

Brain and Mind Centre, The University of Sydney, Sydney, Australia.

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http://dx.doi.org/10.1080/14737175.2020.1727740DOI Listing
March 2020

Primary lateral sclerosis: consensus diagnostic criteria.

J Neurol Neurosurg Psychiatry 2020 04 6;91(4):373-377. Epub 2020 Feb 6.

Neurology, Columbia University College of Physicians and Surgeons, New York City, New York, USA.

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http://dx.doi.org/10.1136/jnnp-2019-322541DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7147236PMC
April 2020

Early focality and spread of cortical dysfunction in amyotrophic lateral sclerosis: A regional study across the motor cortices.

Clin Neurophysiol 2020 Apr 23;131(4):958-966. Epub 2019 Dec 23.

Brain and Mind Centre, University of Sydney, Sydney, NSW 2050, Australia; Department of Neurology, Royal Prince Alfred Hospital, Sydney, NSW 2050, Australia.

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http://dx.doi.org/10.1016/j.clinph.2019.11.057DOI Listing
April 2020

Expanding the availability of medications for amyotrophic lateral sclerosis in Australia.

Med J Aust 2020 03 15;212(4):189-189.e1. Epub 2020 Jan 15.

Brain and Mind Centre, University of Sydney, Sydney, NSW.

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http://dx.doi.org/10.5694/mja2.50482DOI Listing
March 2020

Taxane-induced peripheral neuropathy: differences in patient report and objective assessment.

Support Care Cancer 2020 Sep 11;28(9):4459-4466. Epub 2020 Jan 11.

Brain and Mind Centre, Faculty of Medicine and Health, University of Sydney, Camperdown, NSW, 2050, Australia.

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http://dx.doi.org/10.1007/s00520-020-05299-yDOI Listing
September 2020

Characteristics and risk factors of bortezomib induced peripheral neuropathy: A systematic review of phase III trials.

Hematol Oncol 2020 Aug 27;38(3):229-243. Epub 2020 Jan 27.

Brain and Mind Centre, Faculty of Medicine and Health, The University of Sydney, Camperdown, New South Wales, Australia.

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http://dx.doi.org/10.1002/hon.2706DOI Listing
August 2020

Jewels in the crown: a century of achievement for the .

J Neurol Neurosurg Psychiatry 2020 01;91(1):1-2

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia

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http://dx.doi.org/10.1136/jnnp-2019-322443DOI Listing
January 2020

COG-01 Phenotypic variation in 
ALS-FTD and effect on survival.

Amyotroph Lateral Scler Frontotemporal Degener 2019 Nov;20(sup1):301-308

University of Sydney, Sydney, NSW, Australia.

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http://dx.doi.org/10.1080/21678421.2019.1647000DOI Listing
November 2019

Sound of the crowd: wisdom of neurologists revisited.

Pract Neurol 2019 12 24;19(6):552. Epub 2019 Oct 24.

Brain and Mind Centre, The University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/practneurol-2019-002384DOI Listing
December 2019

Inherited Neuropathies.

Semin Neurol 2019 10 22;39(5):620-639. Epub 2019 Oct 22.

Departments of Neurology, Westmead Hospital, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1055/s-0039-1693006DOI Listing
October 2019

TDP-43 levels in the brain tissue of ALS cases with and without or gene expansions.

Neurology 2019 11 16;93(19):e1748-e1755. Epub 2019 Oct 16.

From the University of Sydney (Y.Y., G.M.H., M.C.K., R.H.T.), Brain and Mind Centre and Central Clinical School, Faculty of Medicine and Health; School of Medical Sciences (G.M.H., R.H.T.), University of New South Wales; Neuroscience Research Australia (G.M.H., R.H.T.); and Department of Neurology (M.C.K.), Royal Prince Alfred Hospital, Sydney, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000008439DOI Listing
November 2019

Milestones.

J Neurol Neurosurg Psychiatry 2019 11 3;90(11):1189. Epub 2019 Oct 3.

Bushell Chair of Neurology, Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia

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http://jnnp.bmj.com/lookup/doi/10.1136/jnnp-2019-321711
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http://dx.doi.org/10.1136/jnnp-2019-321711DOI Listing
November 2019

Relative contributions of diabetes and chronic kidney disease to neuropathy development in diabetic nephropathy patients.

Clin Neurophysiol 2019 11 22;130(11):2088-2095. Epub 2019 Aug 22.

Prince of Wales Clinical School, UNSW Sydney, NSW 2031, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2019.08.005DOI Listing
November 2019

Multifocal motor neuropathy: controversies and priorities.

J Neurol Neurosurg Psychiatry 2020 02 11;91(2):140-148. Epub 2019 Sep 11.

Department of Neurology, Royal Hobart Hospital, Hobart, Tasmania, Australia

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http://dx.doi.org/10.1136/jnnp-2019-321532DOI Listing
February 2020

Measurement of axonal excitability: Consensus guidelines.

Clin Neurophysiol 2020 01 2;131(1):308-323. Epub 2019 Aug 2.

Brain and Mind Centre, University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney 2006, Australia.

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http://dx.doi.org/10.1016/j.clinph.2019.07.023DOI Listing
January 2020

Neural networks associated with body composition in frontotemporal dementia.

Ann Clin Transl Neurol 2019 09 28;6(9):1707-1717. Epub 2019 Aug 28.

School of Psychology and Brain & Mind Centre, The University of Sydney, Sydney, Australia.

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http://dx.doi.org/10.1002/acn3.50869DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6764740PMC
September 2019

Regional motor cortex dysfunction in amyotrophic lateral sclerosis.

Ann Clin Transl Neurol 2019 08 28;6(8):1373-1382. Epub 2019 Jun 28.

Westmead Hospital, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1002/acn3.50819DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6689694PMC
August 2019

Quantification of Small Fiber Neuropathy in Chemotherapy-Treated Patients.

J Pain 2020 Jan - Feb;21(1-2):44-58. Epub 2019 Jul 17.

Brain and Mind Centre, Faculty of Medicine and Health, The University of Sydney, Camperdown, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.jpain.2019.06.011DOI Listing
July 2019

Neuroinflammation in frontotemporal dementia.

Nat Rev Neurol 2019 09 19;15(9):540-555. Epub 2019 Jul 19.

School of Medical Sciences, Faculty of Medicine and Health, University of Sydney, Sydney, NSW, Australia.

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http://dx.doi.org/10.1038/s41582-019-0231-zDOI Listing
September 2019

Motor neuron disease with malignancy: Clinical and pathophysiological insights.

Clin Neurophysiol 2019 09 22;130(9):1557-1561. Epub 2019 Jun 22.

Department of Neurology, Westmead Hospital, Westmead, Australia; Westmead Clinical School, University of Sydney, Westmead, New South Wales, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2019.05.026DOI Listing
September 2019

Safety and tolerability of Triumeq in amyotrophic lateral sclerosis: the Lighthouse trial.

Amyotroph Lateral Scler Frontotemporal Degener 2019 11 8;20(7-8):595-604. Epub 2019 Jul 8.

King's College London, Maurice Wohl Clinical Neuroscience Institute, Department of Basic and Clinical Neuroscience , London , United Kingdom.

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http://dx.doi.org/10.1080/21678421.2019.1632899DOI Listing
November 2019

Amyotrophic lateral sclerosis as a multi-step process: an Australia population study.

Amyotroph Lateral Scler Frontotemporal Degener 2019 11 8;20(7-8):532-537. Epub 2019 Jul 8.

Brain and Mind Centre, University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital , Sydney , Australia.

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https://www.tandfonline.com/doi/full/10.1080/21678421.2018.1
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http://dx.doi.org/10.1080/21678421.2018.1556697DOI Listing
November 2019

Amyotrophic lateral sclerosis: Origins traced to impaired balance between neural excitation and inhibition in the neonatal period.

Muscle Nerve 2019 09 5;60(3):232-235. Epub 2019 Jul 5.

Division of Neurology (Emeritus), Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.

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http://dx.doi.org/10.1002/mus.26617DOI Listing
September 2019

Marco Polo of Australian neurology.

J Neurol Neurosurg Psychiatry 2019 06 2;90(6):627-628. Epub 2019 May 2.

Department of Neurology, Royal Prince Alfred Hospital and University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2019-320989DOI Listing
June 2019

The underacknowledged PPA-ALS: A unique clinicopathologic subtype with strong heritability.

Neurology 2019 03 15;92(12):e1354-e1366. Epub 2019 Feb 15.

From the Brain and Mind Centre and Central Clinical School (R.H.T., B.G., C.D.-S., J.B.J.K., M.C.K., J.R.H., G.M.H.) and School of Medical Sciences (J.J.K.), Faculty of Medicine and Health, and Brain and Mind Centre and School of Psychology (O.P.), The University of Sydney; School of Medical Sciences (R.H.T., C.D.-S., G.M.H.), University of New South Wales & Neuroscience Research Australia; Department of Neurology (M.C.K.), Royal Prince Alfred Hospital; ARC Centre of Excellence in Cognition and its Disorders (J.R.H., O.P.); and Division of Neuroscience (B.G.), Garvan Institute of Medical Research and St Vincent's Clinical School, UNSW Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000007146DOI Listing
March 2019

Measuring network disruption in neurodegenerative diseases: New approaches using signal analysis.

J Neurol Neurosurg Psychiatry 2019 09 13;90(9):1011-1020. Epub 2019 Feb 13.

Academic Unit of Neurology, Trinity College Dublin, the University of Dublin, Dublin, Ireland

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http://jnnp.bmj.com/lookup/doi/10.1136/jnnp-2018-319581
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http://dx.doi.org/10.1136/jnnp-2018-319581DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6820156PMC
September 2019

The effect of coil type and limb dominance in the assessment of lower-limb motor cortex excitability using TMS.

Neurosci Lett 2019 04 30;699:84-90. Epub 2019 Jan 30.

Brain and Mind Centre, University of Sydney, Sydney, NSW, 2050, Australia; Department of Neurology, Royal Prince Alfred Hospital, Sydney, NSW, 2050, Australia.

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http://dx.doi.org/10.1016/j.neulet.2019.01.050DOI Listing
April 2019

Amyotrophic lateral sclerosis diagnostic index: Toward a personalized diagnosis of ALS.

Neurology 2019 02 11;92(6):e536-e547. Epub 2019 Jan 11.

From Westmead Clinical School (N.G., P.M., M.v.d.B., S.V.), Brain and Mind Center (J.H., K.S., J.M.M., S.B.P., M.C.K.), and NHMRC Clinical Trials Centre (K.B.), University of Sydney; and Westmead Hospital (K.B.), Research and Education Network, Sydney, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000006876DOI Listing
February 2019

Clinical and neuroimaging investigations of language disturbance in frontotemporal dementia-motor neuron disease patients.

J Neurol 2019 Apr 1;266(4):921-933. Epub 2019 Feb 1.

Brain and Mind Centre, The University of Sydney, Sydney, NSW, Australia.

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http://dx.doi.org/10.1007/s00415-019-09216-0DOI Listing
April 2019

Vasculitic neuropathy: Comparison of clinical predictors with histopathological outcome.

Muscle Nerve 2019 06 23;59(6):643-649. Epub 2019 Feb 23.

Brain and Mind Centre, University of Sydney, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1002/mus.26431DOI Listing
June 2019

Cerebellar tract alterations in PLS and ALS.

Amyotroph Lateral Scler Frontotemporal Degener 2019 05 21;20(3-4):281-284. Epub 2019 Jan 21.

b Wellcome Centre for Integrative Neuroimaging , University of Oxford , Oxford , UK.

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https://www.tandfonline.com/doi/full/10.1080/21678421.2018.1
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http://dx.doi.org/10.1080/21678421.2018.1562554DOI Listing
May 2019

Functional Biomarkers for Amyotrophic Lateral Sclerosis.

Front Neurol 2018 4;9:1141. Epub 2019 Jan 4.

Brain and Mind Centre, University of Sydney, Sydney, NSW, Australia.

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https://www.frontiersin.org/article/10.3389/fneur.2018.01141
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http://dx.doi.org/10.3389/fneur.2018.01141DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6328463PMC
January 2019

Utility of threshold tracking transcranial magnetic stimulation in ALS.

Clin Neurophysiol Pract 2018 17;3:164-172. Epub 2018 Nov 17.

Brain and Mind Centre, University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, Australia.

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http://dx.doi.org/10.1016/j.cnp.2018.10.002DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6275211PMC
November 2018

Frontostriatal grey matter atrophy in amyotrophic lateral sclerosis A visual rating study.

Dement Neuropsychol 2018 Oct-Dec;12(4):388-393

Faculty of Medicine and Health Sciences, University of East Anglia, Norwich, UK.

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http://dx.doi.org/10.1590/1980-57642018dn12-040008DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6289478PMC
December 2018

Motor neurone disease.

Handb Clin Neurol 2018 ;159:345-357

Brain and Mind Centre, University of Sydney, Sydney, NSW, Australia. Electronic address:

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http://dx.doi.org/10.1016/B978-0-444-63916-5.00022-7DOI Listing
March 2019

Aerobic exercise training may improve nerve function in type 2 diabetes and pre-diabetes: A systematic review.

Diabetes Metab Res Rev 2019 02 7;35(2):e3099. Epub 2018 Dec 7.

Musculoskeletal Health Research Group, Faculty of Health Sciences, The University of Sydney, Lidcombe, NSW, Australia.

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http://dx.doi.org/10.1002/dmrr.3099DOI Listing
February 2019

The burden of apathy for caregivers of patients with amyotrophic lateral sclerosis.

Amyotroph Lateral Scler Frontotemporal Degener 2018 11 29;19(7-8):599-605. Epub 2018 Oct 29.

a Brain & Mind Centre , University of Sydney , Camperdown , NSW , Australia , and.

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http://dx.doi.org/10.1080/21678421.2018.1497659DOI Listing
November 2018

Imbalance of cortical facilitatory and inhibitory circuits underlies hyperexcitability in ALS.

Neurology 2018 10 3;91(18):e1669-e1676. Epub 2018 Oct 3.

From the Westmead Clinical School (M.A.J.V.d.B., M.H., N.G., P.M., S.V.) and Brain and Mind Center (M.C.K.), University of Sydney, Australia; and Department of Neurology (M.H.), Tokyo Metropolitan Geriatric Hospital, Japan.

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http://www.neurology.org/lookup/doi/10.1212/WNL.000000000000
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http://dx.doi.org/10.1212/WNL.0000000000006438DOI Listing
October 2018

Psychiatric disorders in kindreds: Study of 1,414 family members.

Neurology 2018 10 26;91(16):e1498-e1507. Epub 2018 Sep 26.

From the Brain and Mind Centre (E.M.D., R.M.A., G.H., O.P., M.C.K., J.R.H.), University of Sydney; Central Clinical School (E.M.D., R.M.A., M.C.K., J.R.H.), University of Sydney; and ARC Centre of Excellence in Cognition and its Disorders (E.M.D., R.M.A., O.P., J.R.H.), Sydney, Australia.

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http://dx.doi.org/10.1212/WNL.0000000000006344DOI Listing
October 2018

Potassium control in chronic kidney disease: implications for neuromuscular function.

Intern Med J 2019 07;49(7):817-825

Prince of Wales Clinical School, University of New South Wales, Sydney, New South Wales, Australia.

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July 2019

Neural correlates of changes in sexual function in frontotemporal dementia: implications for reward and physiological functioning.

J Neurol 2018 Nov 28;265(11):2562-2572. Epub 2018 Aug 28.

School of Psychology and Brain and Mind Centre, The University of Sydney, Sydney, Australia.

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http://link.springer.com/10.1007/s00415-018-9024-3
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November 2018

Anti-MAG neuropathy: Role of IgM antibodies, the paranodal junction and juxtaparanodal potassium channels.

Clin Neurophysiol 2018 10 10;129(10):2162-2169. Epub 2018 Aug 10.

Brain and Mind Centre, Sydney Medical School, The University of Sydney, 94 Mallett St, Camperdown, NSW 2050, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2018.07.021DOI Listing
October 2018

Fasciculation intensity and disease progression in amyotrophic lateral sclerosis.

Clin Neurophysiol 2018 10 2;129(10):2149-2154. Epub 2018 Aug 2.

Brain and Mind Centre, Sydney Medical School, University of Sydney, Sydney, Australia; Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2018.07.015DOI Listing
October 2018

Regional thalamic MRI as a marker of widespread cortical pathology and progressive frontotemporal involvement in amyotrophic lateral sclerosis.

J Neurol Neurosurg Psychiatry 2018 12 26;89(12):1250-1258. Epub 2018 Jul 26.

Wellcome Centre for Integrative Neuroimaging, University of Oxford, Oxford, UK

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http://dx.doi.org/10.1136/jnnp-2018-318625DOI Listing
December 2018

Comparison of cross-sectional areas and distal-proximal nerve ratios in amyotrophic lateral sclerosis.

Muscle Nerve 2018 12 15;58(6):777-783. Epub 2018 Oct 15.

Brain and Mind Centre, Sydney Medical School, University of Sydney, 94 Mallett Street, Camperdown, Sydney, New South Wales, 2040, Australia.

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http://doi.wiley.com/10.1002/mus.26301
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December 2018

Cortical excitability varies across different muscles.

J Neurophysiol 2018 09 5;120(3):1397-1403. Epub 2018 Jul 5.

Western Clinical School, University of Sydney , Sydney , Australia.

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https://www.physiology.org/doi/10.1152/jn.00148.2018
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September 2018

Inflammatory neuropathies: all shapes and sizes.

J Neurol Neurosurg Psychiatry 2018 11 26;89(11):1128. Epub 2018 Jun 26.

Brain and Mind Centre, Sydney Medical School, The University of Sydney, Sydney, New South Wales, Australia.

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November 2018

A unified model of the excitability of mouse sensory and motor axons.

J Peripher Nerv Syst 2018 09 15;23(3):159-173. Epub 2018 Jul 15.

Brain and Mind Centre, The University of Sydney, Sydney, Australia.

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http://dx.doi.org/10.1111/jns.12278DOI Listing
September 2018

Interrogating cortical function with transcranial magnetic stimulation: insights from neurodegenerative disease and stroke.

J Neurol Neurosurg Psychiatry 2019 01 4;90(1):47-57. Epub 2018 Jun 4.

Brain and Mind Centre, University of Sydney, and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1136/jnnp-2017-317371DOI Listing
January 2019

Correlation between markers of peripheral nerve function and structure in type 1 diabetes.

Diabetes Metab Res Rev 2018 10 3;34(7):e3028. Epub 2018 Jul 3.

University of New South Wales, Prince of Wales Clinical School, Sydney, New South Wales, Australia.

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http://dx.doi.org/10.1002/dmrr.3028DOI Listing
October 2018

Paradox of amyotrophic lateral sclerosis and energy metabolism.

J Neurol Neurosurg Psychiatry 2018 10 7;89(10):1013-1014. Epub 2018 May 7.

Memory and Cognition Clinic, Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, New South Wales, Australia.

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October 2018

Implications of structural and functional brain changes in amyotrophic lateral sclerosis.

Expert Rev Neurother 2018 05 19;18(5):407-419. Epub 2018 Apr 19.

a Brain and Mind Centre , The University of Sydney , Sydney , Australia.

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https://www.tandfonline.com/doi/full/10.1080/14737175.2018.1
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May 2018

Human cerebral evolution and the clinical syndrome of amyotrophic lateral sclerosis.

J Neurol Neurosurg Psychiatry 2019 05 17;90(5):570-575. Epub 2018 Apr 17.

Division of Neurology Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6581076PMC
May 2019

Excitability of sensory axons in amyotrophic lateral sclerosis.

Clin Neurophysiol 2018 07 2;129(7):1472-1478. Epub 2018 Apr 2.

Brain and Mind Centre, University of Sydney, Sydney, NSW 2050, Australia; Sydney Medical School, University of Sydney, Sydney, NSW 2006, Australia; Department of Neurology, Royal Prince Alfred Hospital, Sydney, NSW 2050, Australia.

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http://dx.doi.org/10.1016/j.clinph.2018.03.014DOI Listing
July 2018

Selective Spatiotemporal Vulnerability of Central Nervous System Neurons to Pathologic TAR DNA-Binding Protein 43 in Aged Transgenic Mice.

Am J Pathol 2018 06 22;188(6):1447-1456. Epub 2018 Mar 22.

Motor Neuron Disease Unit, Department of Anatomy, School of Medical Sciences, Faculty of Medicine, University of New South Wales, Sydney, New South Wales, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.ajpath.2018.03.002DOI Listing
June 2018

Physiological changes in neurodegeneration - mechanistic insights and clinical utility.

Nat Rev Neurol 2018 05 23;14(5):259-271. Epub 2018 Mar 23.

Brain and Mind Centre, Sydney Medical School, The University of Sydney, Sydney, Australia.

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http://dx.doi.org/10.1038/nrneurol.2018.23DOI Listing
May 2018

Ectopic impulse generation in peripheral nerve hyperexcitability syndromes and amyotrophic lateral sclerosis.

Clin Neurophysiol 2018 05 10;129(5):974-980. Epub 2018 Feb 10.

Brain and Mind Centre, Sydney Medical School, University of Sydney, Sydney, NSW, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2018.01.061DOI Listing
May 2018

The utility of the Total Neuropathy Score as an instrument to assess neuropathy severity in chronic kidney disease: A validation study.

Clin Neurophysiol 2018 05 6;129(5):889-894. Epub 2018 Mar 6.

Prince of Wales Clinical School, UNSW Sydney, NSW 2031, Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2018.02.120DOI Listing
May 2018

Riluzole, disease stage and survival in ALS.

Lancet Neurol 2018 05 7;17(5):385-386. Epub 2018 Mar 7.

Brain and Mind Centre, University of Sydney and Institute of Clinical Neurosciences, Royal Prince Alfred Hospital, Sydney, NSW 2040, Australia. Electronic address:

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http://dx.doi.org/10.1016/S1474-4422(18)30091-7DOI Listing
May 2018

Inter-session reliability of short-interval intracortical inhibition measured by threshold tracking TMS.

Neurosci Lett 2018 05 1;674:18-23. Epub 2018 Mar 1.

Brain and Mind Centre, University of Sydney, Sydney, NSW 2050, Australia; Sydney Medical School, University of Sydney, Sydney, NSW 2006, Australia; Department of Neurology, Royal Prince Alfred Hospital, Sydney, NSW 2050, Australia.

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http://dx.doi.org/10.1016/j.neulet.2018.02.065DOI Listing
May 2018

Tracking small sensory nerve action potentials in human axonal excitability studies.

J Neurosci Methods 2018 03 11;298:45-53. Epub 2018 Feb 11.

Department of Neurology, Royal Prince Alfred Hospital and the University of Sydney, Sydney, Australia.

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http://dx.doi.org/10.1016/j.jneumeth.2018.02.003DOI Listing
March 2018

Structural and functional papez circuit integrity in amyotrophic lateral sclerosis.

Brain Imaging Behav 2018 Dec;12(6):1622-1630

Center of Mathematics, Computation and Cognition, Universidade Federal do ABC, Santo André, Brazil.

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http://dx.doi.org/10.1007/s11682-018-9825-0DOI Listing
December 2018

Motor neuron disease in 2017: Progress towards therapy in motor neuron disease.

Nat Rev Neurol 2018 Feb 19;14(2):65-66. Epub 2018 Jan 19.

Brain and Mind Centre, University of Sydney, New South Wales 2040, Australia.

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http://dx.doi.org/10.1038/nrneurol.2017.186DOI Listing
February 2018

Oxaliplatin and neuropathy: A role for sodium channels.

Clin Neurophysiol 2018 03 28;129(3):670-671. Epub 2017 Dec 28.

Brain and Mind Centre, Sydney Medical School, University of Sydney, 94 Mallett Street Camperdown, NSW 2050 Australia. Electronic address:

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http://dx.doi.org/10.1016/j.clinph.2017.12.028DOI Listing
March 2018