Publications by authors named "Asghar Aghamohammadi"

100Publications

Variable Abnormalities in T and B Cell Subsets in Ataxia Telangiectasia.

J Clin Immunol 2020 Oct 14. Epub 2020 Oct 14.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-020-00881-9DOI Listing
October 2020

Protein Kinase C-Delta Defect in Autoimmune Lymphoproliferative Syndrome-Like Disease: First Case from the National Iranian Registry and Review of the Literature.

Immunol Invest 2020 Oct 13:1-12. Epub 2020 Oct 13.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences , Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2020.1829638DOI Listing
October 2020

Ataxia-telangiectasia: epidemiology, pathogenesis, clinical phenotype, diagnosis, prognosis and management.

Expert Rev Clin Immunol 2020 Oct 15:1-13. Epub 2020 Oct 15.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science , Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2020.1810570DOI Listing
October 2020

Application of Flow Cytometry in Predominantly Antibody Deficiencies.

Endocr Metab Immune Disord Drug Targets 2020 Jul 20. Epub 2020 Jul 20.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Science, Tehran. Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530320666200721013312DOI Listing
July 2020

Clinical, immunological and genetic findings in patients with UNC13D deficiency (FHL3): A systematic review.

Pediatr Allergy Immunol 2020 Jul 17. Epub 2020 Jul 17.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/pai.13323DOI Listing
July 2020

Serum sickness-like reactions in Iranian children: a registry-based study in a referral center.

Allergol Immunopathol (Madr) 2020 Sep - Oct;48(5):424-429. Epub 2020 Jul 8.

Department of Allergy and Clinical Immunology, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.aller.2019.07.012DOI Listing
July 2020

A new case of congenital ficolin-3 deficiency with primary immunodeficiency.

Expert Rev Clin Immunol 2020 Jul 11;16(7):733-738. Epub 2020 Aug 11.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences , Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2020.1792779DOI Listing
July 2020

Monogenic Primary Immunodeficiency Disorder Associated with Common Variable Immunodeficiency and Autoimmunity.

Int Arch Allergy Immunol 2020 2;181(9):706-714. Epub 2020 Jul 2.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran,

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1159/000508817DOI Listing
July 2020

Evaluation of Radiation Sensitivity in Patients with Hyper IgM Syndrome.

Immunol Invest 2020 Jun 25:1-17. Epub 2020 Jun 25.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences , Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2020.1779288DOI Listing
June 2020

Agammaglobulinemia: Epidemiology, Pathogenesis, Clinical Phenotype, Diagnosis, Prognosis and Management.

Endocr Metab Immune Disord Drug Targets 2020 May 8. Epub 2020 May 8.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran. Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530320666200508114349DOI Listing
May 2020

Characterization of the clinical and immunologic phenotype and management of 157 individuals with 56 distinct heterozygous NFKB1 mutations.

J Allergy Clin Immunol 2020 Oct 9;146(4):901-911. Epub 2020 Apr 9.

Institute for Immunodeficiency, Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany; CIBSS (Centre for Integrative Biological Signalling Studies), University of Freiburg, Freiburg, Germany; RESIST - Cluster of Excellence 2155 to Hanover Medical School, Satellite Center Freiburg, Freiburg, Germany; Institute of Immunology and Transplantation, Royal Free Hospital and University College London, London, United Kingdom; DZIF (German Center for Infection Research) Satellite Center Freiburg, Freiburg, Germany; Rheumatology and Clinical Immunology, Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaci.2019.11.051DOI Listing
October 2020

Are asthma and allergic diseases phenotypic markers for patients with common variable immunodeficiency?

Ann Allergy Asthma Immunol 2020 06 23;124(6):636. Epub 2020 Mar 23.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.anai.2020.03.019DOI Listing
June 2020

Effect of Class Switch Recombination Defect on the Phenotype of Ataxia-Telangiectasia Patients.

Immunol Invest 2020 Mar 2:1-15. Epub 2020 Mar 2.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2020.1723104DOI Listing
March 2020

Interleukin-1β and interleukin-6 in Common Variable Immunodeficiency and their association with subtypes of B cells and response to the Pneumovax-23 vaccine.

Eur Cytokine Netw 2019 Dec;30(4):123-129

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran, Department of Immunology, School of Public Health, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1684/ecn.2019.0435DOI Listing
December 2019

Dystonia in Ataxia Telangiectasia: A Case Report with Novel Mutations.

Oman Med J 2020 Jan 17;35(1):e93. Epub 2020 Feb 17.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.5001/omj.2020.11DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7024809PMC
January 2020

Histocompatibility Complex Status and Mendelian Randomization Analysis in Unsolved Antibody Deficiency.

Front Immunol 2020 24;11:14. Epub 2020 Jan 24.

Division of Clinical Immunology, Department of Laboratory Medicine, Karolinska Institutet at Karolinska University Hospital Huddinge, Stockholm, Sweden.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.3389/fimmu.2020.00014DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6993084PMC
January 2020

Comprehensive assessment of respiratory complications in patients with common variable immunodeficiency.

Ann Allergy Asthma Immunol 2020 05 30;124(5):505-511.e3. Epub 2020 Jan 30.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.anai.2020.01.019DOI Listing
May 2020

Primary Immunodeficiency Diseases and Bacillus Calmette-Guérin (BCG)-Vaccine-Derived Complications: A Systematic Review.

J Allergy Clin Immunol Pract 2020 Apr 30;8(4):1371-1386. Epub 2020 Jan 30.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaip.2020.01.038DOI Listing
April 2020

IL-10 induces TGF-β secretion, TGF-β receptor II upregulation, and IgA secretion in B cells.

Eur Cytokine Netw 2019 09;30(3):107-113

Tehran University of Medical Sciences, Pediatrics Center of Excellence, Children's Medical Center, Research Center for Immunodeficiencies, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1684/ecn.2019.0434DOI Listing
September 2019

Expanding Clinical Phenotype and Novel Insights into the Pathogenesis of ICOS Deficiency.

J Clin Immunol 2020 02 20;40(2):277-288. Epub 2019 Dec 20.

NIH Research-Leeds Biomedical Research Centre and Leeds Institute of Rheumatic and Musculoskeletal Medicine (LIRMM), Wellcome Trust Brenner Building, St. James's University Hospital, Beckett Street, Leeds, UK.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-019-00735-zDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7082411PMC
February 2020

Cutaneous Granulomatosis and Class Switching Defect as a Presenting Sign in Ataxia-Telangiectasia: First Case from the National Iranian Registry and Review of the Literature.

Immunol Invest 2020 Aug 25;49(6):597-610. Epub 2019 Nov 25.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran, and the University of Medical Science , Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2019.1692864DOI Listing
August 2020

The evaluation of neutropenia in common variable immune deficiency patients.

Expert Rev Clin Immunol 2019 11 15;15(11):1225-1233. Epub 2019 Oct 15.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2020.1677154DOI Listing
November 2019

Malignancy in common variable immunodeficiency: a systematic review and meta-analysis.

Expert Rev Clin Immunol 2019 10 15;15(10):1105-1113. Epub 2019 Sep 15.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2019.1658523DOI Listing
October 2019

Potential role of regulatory B cells in immunological diseases.

Immunol Lett 2019 11 20;215:48-59. Epub 2019 Aug 20.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.imlet.2019.08.004DOI Listing
November 2019

Graft versus host disease and microchimerism in a patient.

Allergy Asthma Clin Immunol 2019 22;15:47. Epub 2019 Aug 22.

1Molecular Medicine Department, Pasteur Institute of Iran, Pasteur St., 12 Farvardin Ave., Tehran, 1316943551 Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1186/s13223-019-0361-2DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6704686PMC
August 2019

Leishmaniasis and Autoimmunity in Patient with LPS-Responsive Beige-Like Anchor Protein (LRBA) Deficiency.

Endocr Metab Immune Disord Drug Targets 2020 ;20(3):479-484

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530319666190807161546DOI Listing
January 2020

Disturbed Transcription of TLRs' Negative Regulators and Cytokines Secretion among TLR4- and 9-Activated PBMCs of Agammaglobulinemic Patients.

Immunol Invest 2019 Nov 11;48(8):860-874. Epub 2019 Jun 11.

Immunology Research Center (IRC), Institute of Immunology and Infectious Diseases, Iran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2019.1604742DOI Listing
November 2019

Respiratory Complications in Patients with Hyper IgM Syndrome.

J Clin Immunol 2019 08 11;39(6):557-568. Epub 2019 Jun 11.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-019-00650-3DOI Listing
August 2019

Candidiasis associated with very early onset inflammatory bowel disease: First IL10RB deficient case from the National Iranian Registry and review of the literature.

Clin Immunol 2019 08 13;205:35-42. Epub 2019 May 13.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran and the University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.clim.2019.05.007DOI Listing
August 2019

The Heterogeneous Pathogenesis of Selective Immunoglobulin A Deficiency.

Int Arch Allergy Immunol 2019 15;179(3):231-246. Epub 2019 May 15.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran,

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1159/000499044DOI Listing
August 2019

Comparison of clinical and immunological features and mortality in common variable immunodeficiency and agammaglobulinemia patients.

Immunol Lett 2019 06 3;210:55-62. Epub 2019 May 3.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.imlet.2019.05.001DOI Listing
June 2019

Clinical, Immunologic, and Molecular Spectrum of Patients with LPS-Responsive Beige-Like Anchor Protein Deficiency: A Systematic Review.

J Allergy Clin Immunol Pract 2019 Sep - Oct;7(7):2379-2386.e5. Epub 2019 Apr 14.

Non-communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaip.2019.04.011DOI Listing
October 2020

Individual Radiosensitivity Assessment of the Families of Patients by G2-Checkpoint Abrogation.

Sultan Qaboos Univ Med J 2018 Nov 28;18(4):e440-e446. Epub 2019 Mar 28.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
https://journals.squ.edu.om/index.php/squmj/article/view/298
Publisher Site
http://dx.doi.org/10.18295/squmj.2018.18.04.003DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6443281PMC
November 2018

The First Purine Nucleoside Phosphorylase Deficiency Patient Resembling IgA Deficiency and a Review of the Literature.

Immunol Invest 2019 May 19;48(4):410-430. Epub 2019 Mar 19.

a Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center , Tehran, and the University of Medical Science , Tehran , Iran.

View Article

Download full-text PDF

Source
https://www.tandfonline.com/doi/full/10.1080/08820139.2019.1
Publisher Site
http://dx.doi.org/10.1080/08820139.2019.1570249DOI Listing
May 2019

Outcomes and Treatment Strategies for Autoimmunity and Hyperinflammation in Patients with RAG Deficiency.

J Allergy Clin Immunol Pract 2019 Jul - Aug;7(6):1970-1985.e4. Epub 2019 Mar 12.

University of South Florida and Johns Hopkins All Children's Hospital, Saint Petersburg, Fla; Division of Allergy and Immunology, Massachusetts General Hospital for Children, Boston, Mass. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaip.2019.02.038DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6612449PMC
September 2020

PIK3R1 Mutation Associated with Hyper IgM (APDS2 Syndrome): A Case Report and Review of the Literature.

Endocr Metab Immune Disord Drug Targets 2019 ;19(7):941-958

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran, and the University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530319666190225114739DOI Listing
March 2020

Antagonistic Property of G2013 (α-L-Guluronic Acid) on Gene Expression of MyD88, Tollip, and NF-κB in HEK293 TLR2 and HEK293 TLR4.

Endocr Metab Immune Disord Drug Targets 2019 ;19(2):144-149

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://www.eurekaselect.com/167753/article
Publisher Site
http://dx.doi.org/10.2174/1871530319666181126153752DOI Listing
June 2019

G2-lymphocyte chromosomal radiosensitivity in patients with LPS responsive beige-like anchor protein (LRBA) deficiency.

Int J Radiat Biol 2019 06 13;95(6):680-690. Epub 2019 Feb 13.

b Research Center for Immunodeficiencies, Children's Medical Center , Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/09553002.2019.1577570DOI Listing
June 2019

Toll-like receptors pathway in common variable immune deficiency (CVID) and X-linked agammaglobulinemia (XLA).

Eur Cytokine Netw 2018 Nov;29(4):153-158

Department of Immunology, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran, Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran, Network of Immunity in Infection, Malignancy and Autoimmunity (NIIMA), Universal Scientific Education and Research Network (USERN), Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1684/ecn.2018.0420DOI Listing
November 2018

Ataxia-telangiectasia: A review of clinical features and molecular pathology.

Pediatr Allergy Immunol 2019 05 20;30(3):277-288. Epub 2019 Mar 20.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1111/pai.13020DOI Listing
May 2019

The hyper IgM syndromes: Epidemiology, pathogenesis, clinical manifestations, diagnosis and management.

Clin Immunol 2019 01 13;198:19-30. Epub 2018 Nov 13.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
https://linkinghub.elsevier.com/retrieve/pii/S15216616183063
Publisher Site
http://dx.doi.org/10.1016/j.clim.2018.11.007DOI Listing
January 2019

Fourth Update on the Iranian National Registry of Primary Immunodeficiencies: Integration of Molecular Diagnosis.

J Clin Immunol 2018 10 9;38(7):816-832. Epub 2018 Oct 9.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://link.springer.com/10.1007/s10875-018-0556-1
Publisher Site
http://dx.doi.org/10.1007/s10875-018-0556-1DOI Listing
October 2018

Comparison of Common Monogenic Defects in a Large Predominantly Antibody Deficiency Cohort.

Authors:
Reza Yazdani Hassan Abolhassani Fatemeh Kiaee Sima Habibi Gholamreza Azizi Marzieh Tavakol Zahra Chavoshzadeh Seyed Alireza Mahdaviani Tooba Momen Mohammad Gharagozlou Masoud Movahedi Amir Ali Hamidieh Nasrin Behniafard Mohammamd Nabavi Mohammad Hassan Bemanian Saba Arshi Rasol Molatefi Roya Sherkat Afshin Shirkani Reza Amin Soheila Aleyasin Reza Faridhosseini Farahzad Jabbari-Azad Iraj Mohammadzadeh Javad Ghaffari Alireza Shafiei Arash Kalantari Mahboubeh Mansouri Mehrnaz Mesdaghi Delara Babaie Hamid Ahanchian Maryam Khoshkhui Habib Soheili Mohammad Hossein Eslamian Taher Cheraghi Abbas Dabbaghzadeh Mahmoud Tavassoli Rasoul Nasiri Kalmarzi Seyed Hamidreza Mortazavi Sara Kashef Hossein Esmaeilzadeh Javad Tafaroji Abbas Khalili Fariborz Zandieh Mahnaz Sadeghi-Shabestari Sepideh Darougar Fatemeh Behmanesh Hedayat Akbari Mohammadreza Zandkarimi Farhad Abolnezhadian Abbas Fayezi Mojgan Moghtaderi Akefeh Ahmadiafshar Behzad Shakerian Vahid Sajedi Behrang Taghvaei Mojgan Safari Marzieh Heidarzadeh Babak Ghalebaghi Seyed Mohammad Fathi Behzad Darabi Saeed Bazregari Nasrin Bazargan Morteza Fallahpour Alireza Khayatzadeh Naser Javahertrash Bahram Bashardoust Mohammadali Zamani Azam Mohsenzadeh Sarehsadat Ebrahimi Samin Sharafian Ahmad Vosughimotlagh Mitra Tafakoridelbari Maziar Rahim Parisa Ashournia Anahita Razaghian Arezou Rezaei Ashraf Samavat Setareh Mamishi Hossein Ali Khazaei Javad Mohammadi Babak Negahdari Nima Parvaneh Nima Rezaei Vassilios Lougaris Silvia Giliani Alessandro Plebani Hans D Ochs Lennart Hammarström Asghar Aghamohammadi

J Allergy Clin Immunol Pract 2019 03 19;7(3):864-878.e9. Epub 2018 Sep 19.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Iranian Primary Immunodeficiencies Network (IPIN), Tehran University of Medical Sciences, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaip.2018.09.004DOI Listing
March 2019

chromosomal radiosensitivity in patients with common variable immunodeficiency.

Cent Eur J Immunol 2018 30;43(2):155-161. Epub 2018 Jun 30.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.5114/ceji.2018.77385DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6102621PMC
June 2018

Monogenic polyautoimmunity in primary immunodeficiency diseases.

Autoimmun Rev 2018 Oct 11;17(10):1028-1039. Epub 2018 Aug 11.

Center for Autoimmune Diseases Research (CREA), School of Medicine and Health Sciences, Universidad del Rosario, Bogota, Colombia. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.autrev.2018.05.001DOI Listing
October 2018

Clearing Vaccine-Derived Poliovirus Infection Following Hematopoietic Stem Cell Transplantation: a Case Report and Review of Literature.

J Clin Immunol 2018 07 14;38(5):610-616. Epub 2018 Jun 14.

Research Center for Immunodeficiencies, Children's Medical Center Hospital, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-018-0521-zDOI Listing
July 2018

Clinical implications of systematic phenotyping and exome sequencing in patients with primary antibody deficiency.

Genet Med 2019 01 19;21(1):243-251. Epub 2018 Jun 19.

Division of Clinical Immunology, Department of Laboratory Medicine, Karolinska Institutet at Karolinska University Hospital Huddinge, Stockholm, Sweden.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1038/s41436-018-0012-xDOI Listing
January 2019

The imbalance of circulating T helper subsets and regulatory T cells in patients with LRBA deficiency: Correlation with disease severity.

J Cell Physiol 2018 11 28;233(11):8767-8777. Epub 2018 May 28.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1002/jcp.26772DOI Listing
November 2018

The Profile of Toll-like Receptor 2 (TLR2), TLR4 and Their Cytosolic Downstream Signaling Pathway in Common Variable Immunodeficiency (CVID) Patients.

Iran J Allergy Asthma Immunol 2018 Apr;17(2):188-200

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran AND Department of Immunology, School of Public Health, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
April 2018

Efficacy of an Attachment-Based Intervention Model on Health Indices in Children with Chronic Disease and Their Mothers.

Adm Policy Ment Health 2018 11;45(6):900-910

Pediatric Medical Center Hospital, Tehran University of Medical Science, Dr Gharib Street, Tehran, Iran.

View Article

Download full-text PDF

Source
http://link.springer.com/10.1007/s10488-018-0873-y
Publisher Site
http://dx.doi.org/10.1007/s10488-018-0873-yDOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6208895PMC
November 2018

The Clinical and Immunological Features of Patients with Primary Antibody Deficiencies.

Endocr Metab Immune Disord Drug Targets 2018 ;18(5):537-545

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530318666180413110216DOI Listing
January 2019

Evaluation of the TLR negative regulatory network in CVID patients.

Genes Immun 2019 03 5;20(3):198-206. Epub 2018 Apr 5.

Immunology Research Center (IRC), Institute of Immunology and Infectious Diseases, Iran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://www.nature.com/articles/s41435-018-0022-3
Publisher Site
http://dx.doi.org/10.1038/s41435-018-0022-3DOI Listing
March 2019

Disease Evolution and Response to Rapamycin in Activated Phosphoinositide 3-Kinase δ Syndrome: The European Society for Immunodeficiencies-Activated Phosphoinositide 3-Kinase δ Syndrome Registry.

Front Immunol 2018 16;9:543. Epub 2018 Mar 16.

Center for Chronic Immunodeficiency, Medical Center - University of Freiburg, Freiburg, Germany.

View Article

Download full-text PDF

Source
http://journal.frontiersin.org/article/10.3389/fimmu.2018.00
Publisher Site
http://dx.doi.org/10.3389/fimmu.2018.00543DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5863269PMC
May 2019

Inflammation, a significant player of Ataxia-Telangiectasia pathogenesis?

Inflamm Res 2018 Jul 26;67(7):559-570. Epub 2018 Mar 26.

Research Center for Immunodeficiencies, Children's Medical Center Hospital, Tehran University of Medical Science, 62 Qarib St., Keshavarz Blvd., Tehran, 14194, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00011-018-1142-yDOI Listing
July 2018

Polyautoimmunity in Patients with LPS-Responsive Beige-Like Anchor (LRBA) Deficiency.

Immunol Invest 2018 Jul 12;47(5):457-467. Epub 2018 Mar 12.

b Research Center for Immunodeficiencies, Children's Medical Center , Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2018.1446978DOI Listing
July 2018

Evaluation of infectious and non-infectious complications in patients with primary immunodeficiency.

Cent Eur J Immunol 2017 30;42(4):336-341. Epub 2017 Dec 30.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.5114/ceji.2017.72825DOI Listing
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5820987PMC
December 2017

New insights into physiopathology of immunodeficiency-associated vaccine-derived poliovirus infection; systematic review of over 5 decades of data.

Vaccine 2018 03 23;36(13):1711-1719. Epub 2018 Feb 23.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.vaccine.2018.02.059DOI Listing
March 2018

Ataxia telangiectasia syndrome: moonlighting ATM.

Expert Rev Clin Immunol 2017 12 20;13(12):1155-1172. Epub 2017 Oct 20.

b Research Center for Immunodeficiencies, Children's Medical Center , Tehran University of Medical Science , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2017.1392856DOI Listing
December 2017

Autoimmunity in a cohort of 471 patients with primary antibody deficiencies.

Expert Rev Clin Immunol 2017 11 11;13(11):1099-1106. Epub 2017 Oct 11.

c Research Center for Immunodeficiencies, Children's Medical Center , Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2017.1384312DOI Listing
November 2017

Role of Apoptosis in the Pathogenesis of Common Variable Immunodeficiency (CVID).

Endocr Metab Immune Disord Drug Targets 2017 Nov;17(4):332-340

bResearch Center for Immunodeficiencies, Pediatrics Center of Excellence, Children`s Medical Center, Tehran University of Medical Science, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530317666170919120245DOI Listing
November 2017

Clinical, immunologic, and genetic spectrum of 696 patients with combined immunodeficiency.

J Allergy Clin Immunol 2018 04 12;141(4):1450-1458. Epub 2017 Sep 12.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran, and the University of Medical Science, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jaci.2017.06.049DOI Listing
April 2018

Cernunnos deficiency associated with BCG adenitis and autoimmunity: First case from the national Iranian registry and review of the literature.

Clin Immunol 2017 10 17;183:201-206. Epub 2017 Jul 17.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.clim.2017.07.007DOI Listing
October 2017

A Review on Defects of Dendritic Cells in Common Variable Immunodeficiency.

Endocr Metab Immune Disord Drug Targets 2017 ;17(2):100-113

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran. Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530317666170613125009DOI Listing
June 2018

Comparison of Bone Mineral Density in Common Variable Immunodeficiency and X-Linked Agammaglobulinaemia Patients.

Endocr Metab Immune Disord Drug Targets 2017 ;17(2):134-140

Research Center for Immunodeficiencies, Children's Medical Center, Pediatric Center of Excellence, Tehran University of Medical Sciences, Tehran. Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1871530317666170612093906DOI Listing
June 2018

Immunomodulatory Effect of G2013 (α-L-Guluronic Acid) on the TLR2 and TLR4 in Human Mononuclear Cells.

Curr Drug Discov Technol 2018 ;15(2):123-131

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.2174/1570163814666170605111331DOI Listing
June 2019

Developing Inference Model to Diagnosis of Primary Immunodeficiency Diseases in Protégé.

Acta Med Iran 2017 04;55(4):280-281

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran. AND Primary Immunodeficiency Diseases Network (PIDNeT), Universal Scientific Education and Research Network (USERN), Tehran, Iran.

View Article

Download full-text PDF

Source
April 2017

Clinical, immunologic, molecular analyses and outcomes of iranian patients with LRBA deficiency: A longitudinal study.

Pediatr Allergy Immunol 2017 08 19;28(5):478-484. Epub 2017 Jun 19.

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://doi.wiley.com/10.1111/pai.12735
Publisher Site
http://dx.doi.org/10.1111/pai.12735DOI Listing
August 2017

Costs of Hospital Admission on Primary Immunodeficiency Diseases.

Iran J Public Health 2017 Mar;46(3):342-350

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5395530PMC
March 2017

Measurement of Health-Related Quality of Life in Primary Antibody-Deficient Patients.

Immunol Invest 2017 May 30;46(4):329-340. Epub 2017 Mar 30.

a Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center , Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2016.1258710DOI Listing
May 2017

Preference of Genetic Diagnosis of CXCR4 Mutation Compared with Clinical Diagnosis of WHIM Syndrome.

J Clin Immunol 2017 04 28;37(3):282-286. Epub 2017 Mar 28.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, 62 Qarib St., Keshavarz Blvd., Tehran, 14194, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1007/s10875-017-0387-5DOI Listing
April 2017

Abnormality of regulatory T cells in common variable immunodeficiency.

Cell Immunol 2017 05 29;315:11-17. Epub 2016 Dec 29.

Department of Immunology, School of Public Health, Tehran University of Medical Sciences, Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.cellimm.2016.12.007DOI Listing
May 2017

The clinical significance of complete class switching defect in Ataxia telangiectasia patients.

Expert Rev Clin Immunol 2017 05 15;13(5):499-505. Epub 2017 Feb 15.

a Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center , Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/1744666X.2017.1292131DOI Listing
May 2017

Autoimmunity in Primary Antibody Deficiencies.

Int Arch Allergy Immunol 2016 24;171(3-4):180-193. Epub 2016 Dec 24.

Department of Laboratory Medicine, Imam Hassan Mojtaba Hospital, Alborz University of Medical Sciences, Karaj, Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1159/000453263DOI Listing
February 2017

Impact of IgE-mediated Food Allergy on Parental Quality of Life in Iranian Patients.

Iran J Allergy Asthma Immunol 2016 Oct;15(5):372-380

Department of Allergy and Clinical Immunology, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

View Article

Download full-text PDF

Source
October 2016

LPS-Responsive Beige-Like Anchor Gene Mutation Associated With Possible Bronchiolitis Obliterans Organizing Pneumonia Associated With Hypogammaglobulinemia and Normal IgM Phenotype and Low Number of B Cells.

Acta Med Iran 2016 Oct;54(10):620-623

Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran. AND Department of Immunology, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran. AND Network of Immunity in Infection, Malignancy and Autoimmunity (NIIMA), Universal Scientific Education and Research Network (USERN), Boston, MA, USA.

View Article

Download full-text PDF

Source
October 2016

Novel Mutation of ZAP-70-related Combined Immunodeficiency: First Case from the National Iranian Registry and Review of the Literature.

Immunol Invest 2017 Jan 19;46(1):70-79. Epub 2016 Oct 19.

e Research Center for Immunodeficiencies, Pediatrics Center of Excellence , Children's Medical Center, Tehran University of Medical Sciences , Tehran , Iran.

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1080/08820139.2016.1214962DOI Listing
January 2017

Impaired Akt phosphorylation in B-cells of patients with common variable immunodeficiency.

Clin Immunol 2017 02 21;175:124-132. Epub 2016 Sep 21.

Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran; Primary Immunodeficiency Disease Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address:

View Article

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.clim.2016.09.009DOI Listing
February 2017